KEGG   DISEASE: H01007Help
Entry
H01007                      Disease                                

Name
Choroid plexus papilloma
Description
Choroid plexus tumors (CPTs) are rare intraventricular papillary neoplasms of neuroectodermal origin, accounting for less than 1% of all intracranial tumors and 2-4% of pediatric brain tumors. CPTs are categorized by three distinct histologies; choroid plexus papilloma, atypical choroid plexus papilloma, and the malignant choroid plexus carcinoma. Choroid plexus papillomas outnumber choroid plexus carcinomas and are composed of a single layer of cuboidal-to-columnar cells, resting on a basement membrane overlying papillary and vascularized connective tissue.
Category
Cancer; Nervous system disease
Brite
Human diseases [BR:br08402]
 Nervous system diseases
  Other nervous and sensory system diseases
   H01007  Choroid plexus papilloma
Human diseases in ICD-10 classification [BR:br08403]
 2. Neoplasms (C00-D48)
  D10-D36  Benign neoplasms
   D33  Benign neoplasm of brain and other parts of central nervous system
    H01007  Choroid plexus papilloma
BRITE hierarchy
Pathway
MAPK signaling pathway
Cell cycle
p53 signaling pathway
Apoptosis
Wnt signaling pathway
Neurotrophin signaling pathway
Pathways in cancer
Gene
p53 [HSA:7157] [KO:K04451]
Other DBs
ICD-10: 
MeSH: 
OMIM: 
Reference
PMID:3217283 (description)
  Authors
Tomita T, McLone DG, Flannery AM
  Title
Choroid plexus papillomas of neonates, infants and children.
  Journal
Pediatr Neurosci 14:23-30 (1988)
Reference
PMID:21990040 (description, gene)
  Authors
Gozali AE, Britt B, Shane L, Gonzalez I, Gilles F, McComb JG, Krieger MD, Lavey RS, Shlien A, Villablanca JG, Erdreich-Epstein A, Dhall G, Jubran R, Tabori U, Malkin D, Finlay JL
  Title
Choroid plexus tumors; management, outcome, and association with the Li-Fraumeni  syndrome: the Children's Hospital Los Angeles (CHLA) experience, 1991-2010.
  Journal
Pediatr Blood Cancer 58:905-9 (2012)
Reference
PMID:21970783 (description)
  Authors
Ogiwara H, Dipatri AJ, Alden TD, Bowman RM, Tomita T
  Title
Choroid plexus tumors in pediatric patients.
  Journal
Br J Neurosurg 26:32-7 (2012)
Reference
PMID:11135453 (description)
  Authors
Rickert CH, Paulus W
  Title
Tumors of the choroid plexus.
  Journal
Microsc Res Tech 52:104-11 (2001)
Reference
PMID:22059144 (description)
  Authors
Imai M, Tominaga J, Matsumae M
  Title
Choroid plexus papilloma originating from the cerebrum parenchyma.
  Journal
Surg Neurol Int 2:151 (2011)

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