KEGG   DISEASE: H01007Help
Entry
H01007                      Disease                                

Name
Choroid plexus papilloma
Description
Choroid plexus tumors (CPTs) are rare intraventricular papillary neoplasms of neuroectodermal origin, accounting for less than 1% of all intracranial tumors and 2-4% of pediatric brain tumors. CPTs are categorized by three distinct histologies; choroid plexus papilloma, atypical choroid plexus papilloma, and the malignant choroid plexus carcinoma. Choroid plexus papillomas outnumber choroid plexus carcinomas and are composed of a single layer of cuboidal-to-columnar cells, resting on a basement membrane overlying papillary and vascularized connective tissue.
Category
Cancer; Nervous system disease
BRITE hierarchy
Pathway
MAPK signaling pathway
Cell cycle
p53 signaling pathway
Apoptosis
Wnt signaling pathway
Neurotrophin signaling pathway
Pathways in cancer
Gene
p53 [HSA:7157] [KO:K04451]
Other DBs
ICD-10: 
MeSH: 
OMIM: 
Reference
PMID:3217283 (description)
  Authors
Tomita T, McLone DG, Flannery AM
  Title
Choroid plexus papillomas of neonates, infants and children.
  Journal
Pediatr Neurosci 14:23-30 (1988)
Reference
PMID:21990040 (description, gene)
  Authors
Gozali AE, Britt B, Shane L, Gonzalez I, Gilles F, McComb JG, Krieger MD, Lavey RS, Shlien A, Villablanca JG, Erdreich-Epstein A, Dhall G, Jubran R, Tabori U, Malkin D, Finlay JL
  Title
Choroid plexus tumors; management, outcome, and association with the Li-Fraumeni  syndrome: the Children's Hospital Los Angeles (CHLA) experience, 1991-2010.
  Journal
Pediatr Blood Cancer 58:905-9 (2012)
Reference
PMID:21970783 (description)
  Authors
Ogiwara H, Dipatri AJ, Alden TD, Bowman RM, Tomita T
  Title
Choroid plexus tumors in pediatric patients.
  Journal
Br J Neurosurg 26:32-7 (2012)
Reference
PMID:11135453 (description)
  Authors
Rickert CH, Paulus W
  Title
Tumors of the choroid plexus.
  Journal
Microsc Res Tech 52:104-11 (2001)
Reference
PMID:22059144 (description)
  Authors
Imai M, Tominaga J, Matsumae M
  Title
Choroid plexus papilloma originating from the cerebrum parenchyma.
  Journal
Surg Neurol Int 2:151 (2011)

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