| Entry |
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| Gene name |
SUCLA2, A-BETA, MTDPS5, SCS-betaA
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| Definition |
succinate-CoA ligase, ADP-forming, beta subunit (EC:6.2.1.5)
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| Orthology |
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| Organism |
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| Pathway |
| Citrate cycle (TCA cycle) | | Propanoate metabolism | | Metabolic pathways |
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| Module |
| Citrate cycle, second carbon oxidation, 2-oxoglutarate => oxaloacetate |
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| Disease |
| Mitochondrial DNA depletion syndrome (MDS) |
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| Class |
Metabolism; Carbohydrate metabolism; Citrate cycle (TCA cycle) [PATH: hsa00020]
Metabolism; Carbohydrate metabolism; Propanoate metabolism [PATH: hsa00640]
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| SSDB |
   |
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| Motif |
 |
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| Other DBs |
NCBI-GI: NCBI-GeneID: OMIM: HGNC: HPRD: Ensembl: Vega: UniProt: |
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| Position |
13q12.2-q13.3
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| AA seq |
463 aa  
MAASMFYGRLVAVATLRNHRPRTAQRAAAQVLGSSGLFNNHGLQVQQQQQRNLSLHEYMS
MELLQEAGVSVPKGYVAKSPDEAYAIAKKLGSKDVVIKAQVLAGGRGKGTFESGLKGGVK
IVFSPEEAKAVSSQMIGKKLFTKQTGEKGRICNQVLVCERKYPRREYYFAITMERSFQGP
VLIGSSHGGVNIEDVAAESPEAIIKEPIDIEEGIKKEQALQLAQKMGFPPNIVESAAENM
VKLYSLFLKYDATMIEINPMVEDSDGAVLCMDAKINFDSNSAYRQKKIFDLQDWTQEDER
DKDAAKANLNYIGLDGNIGCLVNGAGLAMATMDIIKLHGGTPANFLDVGGGATVHQVTEA
FKLITSDKKVLAILVNIFGGIMRCDVIAQGIVMAVKDLEIKIPVVVRLQGTRVDDAKALI
ADSGLKILACDDLDEAARMVVKLSEIVTLAKQAHVDVKFQLPI |
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| NT seq |
1392 nt  +upstreamnt +downstreamnt
atggcggcctccatgttctacggcaggctagtggccgtggccacccttcggaaccaccgg
cctcggacggcccagcgggctgctgctcaggttctgggaagttctggattgtttaataac
catggactccaagtacagcagcaacagcaaaggaatctctcactacatgaatacatgagt
atggaattattgcaagaagctggtgtctccgttcccaaaggatatgtggcaaagtcacca
gatgaagcttatgcaattgccaaaaaattaggttcaaaagatgtcgtgataaaggcacag
gttttagctggtggtagaggaaaaggaacatttgaaagtggcctcaaaggaggagtgaag
atagttttctctccagaagaagcaaaagctgtttcttcacaaatgattgggaaaaaattg
tttaccaagcaaacgggagaaaagggcagaatatgcaatcaagtattggtctgtgagcga
aaatatcccaggagagaatactactttgcaataacaatggaaaggtcatttcaaggtcct
gtattaataggaagttcacatggtggtgtcaacattgaagatgttgctgctgagtctcct
gaagcaataattaaagaacctattgatattgaagaaggcatcaaaaaggaacaagctctc
cagcttgcacagaagatgggatttccacctaatattgtggaatcagcagcagaaaacatg
gtcaagctttacagcctttttctgaaatacgatgcaaccatgatagaaataaatccaatg
gtggaagattcagatggagctgtattgtgtatggatgcaaagatcaattttgactctaat
tcagcctatcgccaaaagaaaatctttgatctacaggactggacccaggaagatgaaagg
gacaaagatgctgctaaggcaaatctcaactacattggcctcgatggaaatataggctgc
ctagtaaatggtgctggtttggctatggccacaatggatataataaaacttcatggaggg
actccagccaacttccttgatgttggtggtggtgctacagtccatcaagtaacagaagca
tttaagcttatcacttcagataaaaaggtactggctattctggtcaacatttttggagga
atcatgcgctgtgatgttattgcacagggtatagtcatggcagtaaaagacttggaaatt
aaaatacctgttgtggtacggttacaaggtacacgagtcgatgatgctaaggcactgata
gcggacagtggacttaaaatacttgcttgtgatgacttggatgaagctgctagaatggtt
gtaaagctctctgaaatagtgaccttagcgaagcaagcacatgtggatgtgaaatttcag
ttgccaatatga |
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