KEGG   ORTHOLOGY: K01158
Entry
K01158                      KO                                     
Symbol
DNASE2
Name
deoxyribonuclease II [EC:3.1.22.1]
Pathway
map04142  Lysosome
map04623  Cytosolic DNA-sensing pathway
Disease
H02608  Autoinflammatory-pancytopenia syndrome
Brite
KEGG Orthology (KO) [BR:ko00001]
 09140 Cellular Processes
  09141 Transport and catabolism
   04142 Lysosome
    K01158  DNASE2; deoxyribonuclease II
 09150 Organismal Systems
  09151 Immune system
   04623 Cytosolic DNA-sensing pathway
    K01158  DNASE2; deoxyribonuclease II
Enzymes [BR:ko01000]
 3. Hydrolases
  3.1  Acting on ester bonds
   3.1.22  Endodeoxyribonucleases producing 3'-phosphomonoesters
    3.1.22.1  deoxyribonuclease II
     K01158  DNASE2; deoxyribonuclease II
Other DBs
GO: 0004531
Genes
HSA: 1777(DNASE2) 58511(DNASE2B)
PTR: 469369(DNASE2B) 747576(DNASE2)
PPS: 100971929(DNASE2B) 100983965(DNASE2)
GGO: 101138006(DNASE2B) 101145943(DNASE2)
PON: 100171654(DNASE2) 100453264(DNASE2B)
NLE: 100586795(DNASE2B) 100599185(DNASE2)
HMH: 116468391(DNASE2B) 116478544(DNASE2)
MCC: 710197(DNASE2B) 716802(DNASE2)
MCF: 102116438(DNASE2B) 102117817(DNASE2)
MTHB: 126942671 126963620
MNI: 105465513(DNASE2) 105482745(DNASE2B)
CSAB: 103224537(DNASE2B) 103234370(DNASE2)
CATY: 105593566(DNASE2B) 105601540(DNASE2)
PANU: 101004076(DNASE2) 101026845(DNASE2B)
TGE: 112613025(DNASE2) 112635027(DNASE2B)
MLEU: 105550066(DNASE2)
RRO: 104661085(DNASE2) 104677492(DNASE2B)
RBB: 108527686(DNASE2B) 108544114(DNASE2)
TFN: 117076672(DNASE2) 117092166(DNASE2B)
PTEH: 111523870(DNASE2) 111540345(DNASE2B)
CANG: 105520791(DNASE2) 105521803(DNASE2B)
CJC: 100388793(DNASE2) 100409153(DNASE2B)
SBQ: 101044247(DNASE2) 101046560(DNASE2B)
CIMI: 108282012(DNASE2)
CSYR: 103249401(DNASE2) 103267184(DNASE2B)
MMUR: 105861794(DNASE2B) 105885498(DNASE2)
LCAT: 123635473(DNASE2B) 123637263(DNASE2)
PCOQ: 105807868(DNASE2) 105823818(DNASE2B)
OGA: 100953706(DNASE2)
MMU: 13423(Dnase2a) 56629(Dnase2b)
MCAL: 110291255(Dnase2b) 110299623(Dnase2)
MPAH: 110320532(Dnase2b) 110337216(Dnase2)
RNO: 171575(Dnase2) 59296(Dnase2b)
MCOC: 116069736(Dnase2) 116094385(Dnase2b)
ANU: 117707048(Dnase2b) 117723044(Dnase2)
MUN: 110545826(Dnase2)
CGE: 100763100(Dnase2) 100767962(Dnase2b)
MAUA: 101839257(Dnase2) 101842103(Dnase2b)
PROB: 127229871(Dnase2b) 127229906(Dnase2)
PLEU: 114687631(Dnase2) 114698267(Dnase2b)
MORG: 121446792(Dnase2) 121450476(Dnase2b)
AAMP: 119801353(Dnase2b) 119802059(Dnase2)
NGI: 103728126(Dnase2b) 103751880(Dnase2)
HGL: 101716162(Dnase2) 101719320(Dnase2b)
CPOC: 100728975(Dnase2) 100732795(Dnase2b)
CCAN: 109681258(Dnase2) 109688704(Dnase2b)
DORD: 105987045(Dnase2b) 105999245(Dnase2)
DSP: 122100303(Dnase2) 122103676(Dnase2b)
PLOP: 125348831(Dnase2) 125354410(Dnase2b)
MMMA: 107145243(Dnase2) 107158291(Dnase2b)
OPI: 101522904(DNASE2) 101526550(DNASE2B)
TUP: 102489174(DNASE2) 102500832(DNASE2B)
GVR: 103585640(DNASE2)
CFA: 476697(DNASE2) 479973(DNASE2B)
CLUD: 112640982(DNASE2B) 112666582(DNASE2)
VVP: 112908182(DNASE2)
VLG: 121487811(DNASE2B) 121495935(DNASE2)
NPO: 129520276(DNASE2B) 129521935(DNASE2)
AML: 100478733(DNASE2)
UMR: 103663110(DNASE2B) 103682150(DNASE2)
UAH: 113247207(DNASE2)
UAR: 123777738(DNASE2) 123794903(DNASE2B)
MPUF: 101678832(DNASE2) 101691763(DNASE2B)
MNP: 132001065(DNASE2B) 132011038(DNASE2)
MLK: 131809765(DNASE2B) 131823591(DNASE2)
NVS: 122899139(DNASE2B) 122909679(DNASE2)
ORO: 101365858(DNASE2B) 101372958(DNASE2)
EJU: 114197773(DNASE2) 114208504(DNASE2B)
ZCA: 113917273(DNASE2) 113935929(DNASE2B)
MLX: 118005335(DNASE2) 118020190(DNASE2B)
NSU: 110580483(DNASE2B) 110593930(DNASE2)
LWW: 102732185(DNASE2B) 102738650(DNASE2)
FCA: 101086631(DNASE2)
PYU: 121014046(DNASE2) 121027380(DNASE2B)
PCOO: 112852996(DNASE2) 112864154(DNASE2B)
PBG: 122480699(DNASE2B) 122486939(DNASE2)
PTG: 102955307(DNASE2) 102971388(DNASE2B)
PPAD: 109246178(DNASE2B) 109254029(DNASE2)
PUC: 125929035
HHV: 120241650(DNASE2B) 120245286(DNASE2)
BTA: 282218(DNASE2) 525117(DNASE2B)
BOM: 102267450(DNASE2B) 102274104(DNASE2)
BIU: 109556135(DNASE2B) 109561533(DNASE2)
BBUB: 102409788(DNASE2B) 123466185(DNASE2)
BBIS: 104999847(DNASE2) 105003255(DNASE2B)
CHX: 102180029(DNASE2) 102191199(DNASE2B)
OAS: 101105493(DNASE2) 101110100(DNASE2B)
BTAX: 128045111(DNASE2B) 128051394(DNASE2)
ODA: 120856551(DNASE2B) 120864042(DNASE2)
CCAD: 122436766(DNASE2B) 122440503(DNASE2)
MBEZ: 129541765(DNASE2B) 129559610(DNASE2)
SSC: 100620625(DNASE2B) 397398(DNASE2)
CFR: 102504882(DNASE2B) 102515557(DNASE2)
CBAI: 105068330(DNASE2) 105075494(DNASE2B)
CDK: 105095039(DNASE2B) 105100754(DNASE2)
VPC: 102526800(DNASE2B) 102541728(DNASE2)
BACU: 103004369(DNASE2) 103010260(DNASE2B)
LVE: 103068859(DNASE2) 103070741(DNASE2B)
OOR: 101275963(DNASE2B) 101280767(DNASE2)
DLE: 111166547(DNASE2) 111178376(DNASE2B)
PCAD: 102982017(DNASE2B) 102994956(DNASE2)
PSIU: 116751226(DNASE2) 116764604(DNASE2B)
NASI: 112414935(DNASE2) 112415089(DNASE2B)
ECB: 100064895(DNASE2B) 100147278(DNASE2)
EPZ: 103540639(DNASE2) 103557287(DNASE2B)
EAI: 106824010(DNASE2B) 106844341(DNASE2)
MYB: 102242953(DNASE2B) 102244884(DNASE2)
MYD: 102751727(DNASE2) 102752051(DNASE2B)
MMYO: 118652577(DNASE2) 118677531(DNASE2B)
MLF: 102436632(DNASE2) 102440779(DNASE2B)
MNA: 107541541(DNASE2) 107543180(DNASE2B)
PKL: 118710376(DNASE2) 118722344(DNASE2B)
EFUS: 103284160(DNASE2B) 103301011(DNASE2)
HAI: 109385434(DNASE2B) 109394275(DNASE2)
DRO: 112301522(DNASE2) 112309366(DNASE2B)
SHON: 118984123(DNASE2) 118997367(DNASE2B)
AJM: 119049659(DNASE2) 119062891(DNASE2B)
PDIC: 114497842(DNASE2B) 114502585(DNASE2)
PHAS: 123816505(DNASE2B) 123828611(DNASE2)
MMF: 118616200(DNASE2) 118626580(DNASE2B)
RFQ: 117027825(DNASE2B) 117037824(DNASE2)
PPAM: 129062559(DNASE2) 129065606(DNASE2B)
PALE: 102878930(DNASE2B) 102880783(DNASE2)
PGIG: 120583273(DNASE2B) 120618529(DNASE2)
PVP: 105289067(DNASE2B) 105307170(DNASE2)
RAY: 107511586(DNASE2B) 107519410(DNASE2)
MJV: 108386576(DNASE2B) 108399655(DNASE2)
TOD: 119235498(DNASE2B) 119241004(DNASE2)
LAV: 100657160(DNASE2) 100668172(DNASE2B)
ETF: 101649457(DNASE2B) 101657478(DNASE2)
DNM: 101419597(DNASE2B) 101439635(DNASE2)
MDO: 100012881(DNASE2B) 100027525(DNASE2)
GAS: 123232086(DNASE2) 123245348(DNASE2B)
SHR: 100917174(DNASE2B) 100927318(DNASE2)
PCW: 110210015(DNASE2B) 110214186(DNASE2)
OAA: 100075769(DNASE2)
GGA: 424540(DNASE2B)
PCOC: 116233339(DNASE2B)
MGP: 100548401(DNASE2B)
CJO: 107317541(DNASE2B)
TPAI: 128072335(DNASE2B)
LMUT: 125693270(DNASE2B)
NMEL: 110402303(DNASE2B)
APLA: 101792648(DNASE2B)
ACYG: 106034063(DNASE2B)
CATA: 118243729(DNASE2B)
AFUL: 116492033(DNASE2B)
TGU: 100231880(DNASE2B)
LSR: 110468792(DNASE2B)
SCAN: 103814925(DNASE2B)
PMOA: 120510817(DNASE2B)
OTC: 121345139(DNASE2B)
PRUF: 121362121(DNASE2B)
GFR: 102040552(DNASE2B)
FAB: 107603307(DNASE2B)
OMA: 130256089(DNASE2B)
PHI: 102112417(DNASE2B)
PMAJ: 107208238(DNASE2B)
CCAE: 111932858(DNASE2B)
CCW: 104695301(DNASE2B)
CBRC: 103612623(DNASE2B)
ETL: 114064917(DNASE2B)
ZAB: 102068431(DNASE2B)
ACHL: 103804862(DNASE2B)
SVG: 106857412(DNASE2B)
MMEA: 130578596(DNASE2B)
HRT: 120756480(DNASE2B)
FPG: 101917930(DNASE2B)
FCH: 102059822(DNASE2B)
CLV: 102094785(DNASE2B)
EGZ: 104122907(DNASE2B)
NNI: 104015463(DNASE2B)
PCRI: 104028065(DNASE2B)
PLET: 104623199(DNASE2B)
EHS: 104515606(DNASE2B)
PCAO: 104045647(DNASE2B)
ACUN: 113483166(DNASE2B)
TALA: 104362339(DNASE2B)
PADL: 103925148(DNASE2B)
AFOR: 103894708(DNASE2B)
ACHC: 115349365(DNASE2B)
HALD: 104325203(DNASE2B)
HLE: 104841116(DNASE2B)
AGEN: 126042139
GCL: 127019102
CCRI: 104168243(DNASE2B)
CSTI: 104553164(DNASE2B)
CMAC: 104487560(DNASE2B)
MUI: 104545039(DNASE2B)
BREG: 104630507(DNASE2B)
FGA: 104078856(DNASE2B)
GSTE: 104262263(DNASE2B)
LDI: 104348208(DNASE2B)
MNB: 103768847(DNASE2B)
OHA: 104338850(DNASE2B)
NNT: 104408381(DNASE2B)
SHAB: 115611454(DNASE2B)
DPUB: 104300111(DNASE2B)
PGUU: 104457941(DNASE2B)
ACAR: 104524349(DNASE2B)
CPEA: 104396833(DNASE2B)
AVIT: 104281461(DNASE2B)
CVF: 104286300(DNASE2B)
RTD: 128913519(DNASE2B)
CUCA: 104055207(DNASE2B)
TEO: 104378014(DNASE2B)
BRHI: 104488817(DNASE2B)
AAM: 106499687(DNASE2B)
AROW: 112961920(DNASE2B)
NPD: 112946254(DNASE2B)
TGT: 104565321(DNASE2B)
DNE: 112993125(DNASE2B)
SCAM: 104143002(DNASE2B)
ASN: 102373654(DNASE2B) 102378453(DNASE2)
AMJ: 102569684(DNASE2) 102571694(DNASE2B)
CPOO: 109307345(DNASE2B)
GGN: 109286785(DNASE2B)
PSS: 102453737(DNASE2B)
CMY: 102943737(DNASE2B)
CCAY: 125627716(DNASE2) 125641906(DNASE2B)
DCC: 119846005(DNASE2) 119860347(DNASE2B)
CPIC: 101933598(DNASE2) 101936999(DNASE2B)
TST: 117882029(DNASE2B)
CABI: 116830802(DNASE2) 116835759(DNASE2B)
MRV: 120370464(DNASE2B) 120391489(DNASE2)
ACS: 100552794(dnase2b)
ASAO: 132767915(DNASE2) 132774079(DNASE2B)
PVT: 110078007(DNASE2) 110079740(DNASE2B)
SUND: 121920659(DNASE2) 121929999(DNASE2B)
PBI: 103065325(DNASE2)
PMUR: 107285126(DNASE2)
TSR: 106543317
PGUT: 117675621(DNASE2)
APRI: 131190644(DNASE2)
PTEX: 113446931(DNASE2)
NSS: 113419933(DNASE2)
VKO: 123024488(DNASE2B) 123030071(DNASE2)
PMUA: 114587682(DNASE2) 114598813(DNASE2B)
PRAF: 128404857(DNASE2) 128415088(DNASE2B)
ZVI: 118088818(DNASE2B) 118097587(DNASE2)
HCG: 128324008(DNASE2B) 128348304(DNASE2)
GJA: 107112001(DNASE2) 107117303(DNASE2B)
STOW: 125429965(DNASE2)
EMC: 129331100(DNASE2B) 129346347(DNASE2)
XLA: 108715496(dnase2b.S) 446506(dnase2.L)
XTR: 496759(dnase2b) 733868(dnase2)
NPR: 108791376(DNASE2B) 108799819(DNASE2)
RTEM: 120933354(DNASE2) 120945979(DNASE2B)
BBUF: 120979287(DNASE2B) 120986449(DNASE2)
BGAR: 122927267(DNASE2) 122943159(DNASE2B)
MUO: 115464901(DNASE2) 115471880(DNASE2B)
GSH: 117346927(DNASE2B) 117350419(DNASE2)
DRE: 100000399(dnase2) 562996(dnase2b)
SRX: 107726682(dnase2) 107742910(dnase2b) 107745346
CAUA: 113069363(dnase2b) 113115741(dnase2)
PTET: 122353559(dnase2b) 122360993(dnase2)
LROH: 127172872(dnase2b) 127178396(dnase2)
OMC: 131521703(dnase2) 131549822(dnase2b)
PPRM: 120464254(dnase2b) 120488413 120488437
RKG: 130078099(dnase2b)
MAMB: 125243188(dnase2) 125256681(dnase2b)
CIDE: 127496815
TROS: 130557515(dnase2) 130571505(dnase2b)
TDW: 130410423(dnase2b) 130433308(dnase2)
MANU: 129427097(dnase2b) 129448799(dnase2)
IPU: 108256294(dnase2) 108270716
IFU: 128599632(dnase2) 128613451(dnase2b)
PHYP: 113529157(dnase2b) 113533098(dnase2)
SMEO: 124375631(dnase2) 124391088(dnase2b)
TFD: 113649708(dnase2) 113651605(dnase2b)
TVC: 132840544(dnase2) 132853701(dnase2b)
AMEX: 103028211 103030372(dnase2b)
CMAO: 118798902(dnase2) 118819498(dnase2b)
EEE: 113571916 113581922(dnase2b)
TFS: 130517325 130528159(dnase2b) 130531992(dnase2)
NCC: 104941343 104941344(dnase2b) 104964581(dnase2)
EFO: 125892827(dnase2) 125896273(dnase2b) 125896391
PLEP: 121945982(dnase2) 121961968(dnase2b)
ECRA: 117945680(dnase2) 117950658(dnase2b) 117950659 117958878
PPUG: 119197947(dnase2) 119216131(dnase2b) 119216449
AFB: 129094080 129094081(dnase2b) 129102718 129109312(dnase2)
CLUM: 117727984(dnase2) 117730103(dnase2b)
SCHU: 122865831 122877467(dnase2b) 122877868 122881512(dnase2)
OML: 112136612(dnase2) 112150546(dnase2b) 112150737
PPRL: 129351093 129370945(dnase2) 129371418 129371429(dnase2b)
NWH: 119407777 119409812(dnase2) 119430794(dnase2b)
MCEP: 125008932(dnase2b) 125008933 125016106(dnase2)
CSEM: 103388950(dnase2) 103392263(dnase2b)
SLAL: 111655669(dnase2) 111658493(dnase2b) 111658505
XGL: 120783568(dnase2) 120790333(dnase2b) 120790334
HCQ: 109512201(dnase2) 109522037(dnase2b)
SBIA: 133501455(dnase2) 133504135(dnase2b)
PEE: 133401859(dnase2) 133406216(dnase2b)
PTAO: 133479847(dnase2) 133481440(dnase2b)
MALB: 109958175(dnase2b) 109965583(dnase2)
OTW: 112222995 112229709(dnase2)
SNH: 120031287
CCLU: 121559687(dnase2) 121566465
ELS: 105021861(dnase2)
PKI: 111838477(dnase2) 111860507(dnase2b)
LOC: 102689536(dnase2b)
PSPA: 121304319(dnase2) 121330468
PSEX: 120514320(dnase2b) 120514811 120539136(dnase2)
CMK: 103173520 103174707(dnase2b)
CPLA: 122552455 122554113(dnase2b)
HOC: 132818861(dnase2b) 132836011(dnase2)
LERI: 129700698(dnase2b) 129714346
PMRN: 116943714
LRJ: 133346524
AJC: 117118905
SKO: 102807747
DME: Dmel_CG7780(DNaseII)
DER: 6552004
DSE: 6616669
DSI: Dsimw501_GD19194(Dsim_GD19194)
DAN: 6499544
DSR: 110191008
DPO: 4803163
DPE: 6594082
DMN: 108154950
DWI: 6647557
DGR: 6568142
DAZ: 108621276
DNV: 115563651
DHE: 111601331
DVI: 6629613
CCAT: 101453982
BOD: 106615437
BDR: 105223550
RZE: 108362430
AOQ: 129237506
TDA: 119690283
MDE: 101890173
SCAC: 106087861
LCQ: 111691068
LSQ: 119601532
GFS: 119645048
ECOE: 129948055
CLON: 129609794
HIS: 119654496
AGA: 1279761
ACOZ: 120950753
AARA: 120903834
ASTE: 118502761
AFUN: 125762227
AMOU: 128298054
AALI: 118456642
AAG: 5576264
CPII: 120417540
CNS: 116339476
BCOO: 119079451
AME: 413489
ACER: 107997036
ALAB: 122716380
ADR: 102681239
AFLR: 100864814
BIM: 100742638
BBIF: 117205882
BVK: 117233141
BVAN: 117153871
BTER: 100651072
BAFF: 126916272
BPYO: 122565729
BPAS: 132905218
FVI: 122537300
CCAL: 108625258
OBB: 114880714
OLG: 117605160
MGEN: 117220758
NMEA: 116432062
CGIG: 122398165
SOC: 105198320
MPHA: 105837554
AEC: 105147236
ACEP: 105619618
PBAR: 105426743
VEM: 105564192
HST: 105190511
DQU: 106745292
CFO: 105249606
FEX: 115235254
LHU: 105668384
PGC: 109858774
OBO: 105284110
PCF: 106787764
PFUC: 122522918
VPS: 122629442
VCRB: 124423707
VVE: 124949871
NVI: 100123791
CSOL: 105368581
LHT: 122502005
LBD: 127280001
MDL: 103570972
CGLO: 123273302
DAM: 107038895
AGIF: 122857070
VCAN: 122410716
CCIN: 107268475
DSM: 124407002
NPT: 124215042
NFB: 124178672
NLO: 107222798
NVG: 124300953
AROA: 105692360
TCA: 103312693
DPA: 109542049
SOY: 115888114
AGRG: 126735361
ATD: 109595018
AGB: 108917377
LDC: 111517648
NVL: 108561966
PPYR: 116168823
OTU: 111423733
BMOR: 101746575
MSEX: 115441803
VCD: 124535805
MCIX: 123660790
PMAC: 106710810
PPOT: 106104391
PXU: 106121814
PRAP: 110996932
ZCE: 119833067
LSIN: 126968067
HAW: 110380895
TNL: 113496237
CCRN: 123292910
API: 100161890
DNX: 107173444
AGS: 114128000
RMD: 113551002
ACOO: 126838128
DVT: 126903335
BTAB: 109039880
DCI: 113471832
CLEC: 106662821
HHAL: 106685126
NLU: 111048316
HVI: 124360592
FOC: 113207935
TPAL: 117642367
ZNE: 110836613
CSEC: 111864727
IEL: 124165755
DMK: 116918615
DPZ: 124343265
PVM: 113829943
PJA: 122253597
PCHN: 125032429
PMOO: 119596526
HAME: 121869640
PCLA: 123769860
CQD: 128699878
PTRU: 123501441
ESN: 127005230
EAF: 111708673
LSM: 121119752
TCF: 131884676
DPTE: 113799111
CSCU: 111614735
UDV: 129219672
SDM: 118196847
CEL: CELE_C07B5.5(nuc-1) CELE_F09G8.2(crn-7) CELE_K04H4.6(crn-6)
CBR: CBG_10104(Cbr-crn-6) CBG_16650(Cbr-crn-7)
BMY: BM_BM4822(Bma-crn-6)
PCAN: 112575747
BGT: 106077106
GAE: 121384809
PMAX: 117317724
MCAF: 127729238
MMER: 123561497
OBI: 106880775
OSN: 115223215
EGL: EGR_00642
DGT: 114528359
XEN: 124446389
HMG: 100214979
DDI: DDB_G0290577(dnase2)
DFA: DFA_07386(dnase2)
BPS: BPSS1983
BPSE: BDL_5397
BPSM: BBQ_4145
BPSU: BBN_5451
BPSD: BBX_4563
BPK: BBK_4726
BPSH: DR55_5746
BPSA: BBU_4025
BPSO: X996_5549
BUT: X994_5109
BTQ: BTQ_3681
BTJ: BTJ_4714
BTZ: BTL_5501
BTD: BTI_5010
BTV: BTHA_4702
BTHE: BTN_5171
BTHM: BTRA_5440
BTHA: DR62_5301
BTHL: BG87_5513
BOK: DM82_6277
BOC: BG90_4391
BSAV: WS86_29130
BUL: BW21_4547
 » show all
Reference
  Authors
Shiokawa D, Tanuma SI
  Title
Isolation and characterization of the DLAD/Dlad genes, which lie head-to-head with the genes for urate oxidase.
  Journal
Biochem Biophys Res Commun 288:1119-28 (2001)
DOI:10.1006/bbrc.2001.5894
  Sequence
[hsa:58511]

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