KEGG   ORTHOLOGY: K01948Help
Entry
K01948                      KO                                     

Name
CPS1
Definition
carbamoyl-phosphate synthase (ammonia) [EC:6.3.4.16]
Pathway
Arginine biosynthesis
Alanine, aspartate and glutamate metabolism
Nitrogen metabolism
Metabolic pathways
Microbial metabolism in diverse environments
Carbon metabolism
Biosynthesis of amino acids
Module
M00029  
Urea cycle
Disease
H00164  
Carbamoyl phosphate synthetase I deficiency
H01398  
Primary hyperammonemic disorders (Urea cycle disorders)
Brite
KEGG Orthology (KO) [BR:ko00001]
 Metabolism
  Energy metabolism
   00910 Nitrogen metabolism
    K01948  CPS1; carbamoyl-phosphate synthase (ammonia)
  Amino acid metabolism
   00250 Alanine, aspartate and glutamate metabolism
    K01948  CPS1; carbamoyl-phosphate synthase (ammonia)
   00220 Arginine biosynthesis
    K01948  CPS1; carbamoyl-phosphate synthase (ammonia)
KEGG modules [BR:ko00002]
 Pathway module
  Nucleotide and amino acid metabolism
   Arginine and proline metabolism
    M00029  Urea cycle
     K01948  CPS1; carbamoyl-phosphate synthase (ammonia)
Enzymes [BR:ko01000]
 6. Ligases
  6.3  Forming carbon-nitrogen bonds
   6.3.4  Other carbon-nitrogen ligases
    6.3.4.16  carbamoyl-phosphate synthase (ammonia)
     K01948  CPS1; carbamoyl-phosphate synthase (ammonia)
Peptidases [BR:ko01002]
 Cysteine Peptidases
  Family C26: gamma-glutamyl hydrolase family
   K01948  CPS1; carbamoyl-phosphate synthase (ammonia)
BRITE hierarchy
Other DBs
RN: 
GO: 
Genes
HSA: 
1373(CPS1)
PTR: 
738670(CPS1)
PPS: 
100984596(CPS1)
GGO: 
101130709(CPS1)
PON: 
100442727(CPS1)
NLE: 
100596216(CPS1)
MCC: 
711806(CPS1)
MCF: 
102139369(CPS1)
CSAB: 
103217763(CPS1)
RRO: 
104655495(CPS1)
RBB: 
108540334(CPS1)
CJC: 
100402602(CPS1)
SBQ: 
101050943(CPS1)
MMU: 
227231(Cps1)
RNO: 
497840(Cps1)
CGE: 
100760467(Cps1)
NGI: 
103744467(Cps1)
HGL: 
101696508(Cps1)
CCAN: 
109699651(Cps1)
OCU: 
100303765(CPS1)
TUP: 
102491899(CPS1)
CFA: 
488506(CPS1)
AML: 
100466842(CPS1)
UMR: 
103659822(CPS1)
FCA: 
101099824(CPS1)
PTG: 
102968283(CPS1)
AJU: 
106984775(CPS1)
BTA: 
510506(CPS1)
BOM: 
102267831(CPS1)
BIU: 
109570387(CPS1)
PHD: 
102342950(CPS1)
CHX: 
102179612(CPS1)
OAS: 
101107584(CPS1)
SSC: 
100157716(CPS1)
CFR: 
CDK: 
105101586(CPS1)
BACU: 
103003987(CPS1)
LVE: 
103079188(CPS1)
ECB: 
100050116(CPS1)
EPZ: 
103554808(CPS1)
EAI: 
106843053(CPS1)
MYB: 
102262103(CPS1)
MYD: 
102756563(CPS1)
HAI: 
109390430(CPS1)
RSS: 
109445055(CPS1)
PALE: 
102895317(CPS1)
LAV: 
100669826(CPS1)
MDO: 
100015090(CPS1)
SHR: 
100929825(CPS1)
OAA: 
100077228(CPS1)
GGA: 
428994(CPS1)
MGP: 
100539661(CPS1)
CJO: 
107316483(CPS1)
APLA: 
101797791(CPS1)
ACYG: 
106034508(CPS1)
TGU: 
100221389(CPS1)
GFR: 
102044867(CPS1)
FAB: 
101816308(CPS1)
PHI: 
102105821(CPS1)
PMAJ: 
107207199(CPS1)
CCW: 
104694540(CPS1)
FPG: 
101910440(CPS1)
FCH: 
102046837(CPS1)
CLV: 
102091543(CPS1)
AAM: 
106492382(CPS1)
ASN: 
102386005(CPS1)
AMJ: 
106736782(CPS1)
PSS: 
102462440(CPS1)
CMY: 
102943091(CPS1)
CPIC: 
101942404(CPS1)
ACS: 
100562333(cps1)
PVT: 
110072386(CPS1)
PBI: 
103061484(CPS1)
GJA: 
XLA: 
733340(cps1.L)
XTR: 
100158506(cps1)
NPR: 
DRE: 
555623(cps1)
SRX: 
SANH: 
SGH: 
IPU: 
108266807(cps1)
AMEX: 
103026142(cps1)
TRU: 
101074466(cps1)
TNG: 
LCO: 
104929821(cps1)
NCC: 
MZE: 
101479159(cps1)
OLA: 
101164854(cps1)
XMA: 
102232024(cps1)
CSEM: 
103392237(cps1)
LCF: 
HCQ: 
109531202(cps1)
BPEC: 
110156044(cps1)
SASA: 
106586447(cps1)
ELS: 
105008497(cps1)
SFM: 
108922278(cps1)
LCM: 
102363877(CPS1)
CMK: 
103182939(cps1)
BFO: 
SPU: 
APLC: 
SKO: 
LGI: 
OBI: 
LAK: 
ADF: 
PTI: 
FCY: 
TPS: 
AAF: 
PIF: 
PSOJ: 
SPAR: 
 » show all
TaxonomyKoalaUniProt
Reference
PMID:1840546
  Authors
Haraguchi Y, Uchino T, Takiguchi M, Endo F, Mori M, Matsuda I
  Title
Cloning and sequence of a cDNA encoding human carbamyl phosphate synthetase I: molecular analysis of hyperammonemia.
  Journal
Gene 107:335-40 (1991)
DOI:10.1016/0378-1119(91)90336-A

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