KEGG   PATHWAY: ko00340Help
Entry
ko00340                     Pathway                                

Name
Histidine metabolism
Class
Metabolism; Amino acid metabolism
BRITE hierarchy
Pathway map
Histidine metabolism
ko00340

All organismsOrtholog table
Module
M00026  
Histidine biosynthesis, PRPP => histidine [PATH:ko00340]
M00045  
Histidine degradation, histidine => N-formiminoglutamate => glutamate [PATH:ko00340]
Disease
H00171  
Histidinemia
H00548  
Brunner syndrome
H00862  
Tourette syndrome
H01233  
Urocanase deficiency
H01262  
Formiminotransferase deficiency
Drug
D02922  
Amodiaquine  (USAN/INN)
Other DBs
BSID: 
GO: 
Orthology
K00765  
ATP phosphoribosyltransferase [EC:2.4.2.17]
K02502  
ATP phosphoribosyltransferase regulatory subunit
K01523  
phosphoribosyl-ATP pyrophosphohydrolase [EC:3.6.1.31]
K01496  
phosphoribosyl-AMP cyclohydrolase [EC:3.5.4.19]
K11755  
phosphoribosyl-ATP pyrophosphohydrolase / phosphoribosyl-AMP cyclohydrolase [EC:3.5.4.19 3.6.1.31]
K14152  
phosphoribosyl-ATP pyrophosphohydrolase / phosphoribosyl-AMP cyclohydrolase / histidinol dehydrogenase [EC:1.1.1.23 3.5.4.19 3.6.1.31]
K01814  
phosphoribosylformimino-5-aminoimidazole carboxamide ribotide isomerase [EC:5.3.1.16]
K02501  
glutamine amidotransferase [EC:2.4.2.-]
K02500  
cyclase [EC:4.1.3.-]
K01663  
glutamine amidotransferase / cyclase [EC:4.1.3.- 2.4.2.-]
K01693  
imidazoleglycerol-phosphate dehydratase [EC:4.2.1.19]
K00817  
histidinol-phosphate aminotransferase [EC:2.6.1.9]
K05602  
histidinol-phosphatase [EC:3.1.3.15]
K01089  
imidazoleglycerol-phosphate dehydratase / histidinol-phosphatase [EC:3.1.3.15 4.2.1.19]
K04486  
histidinol-phosphatase (PHP family) [EC:3.1.3.15]
K00013  
histidinol dehydrogenase [EC:1.1.1.23]
K01745  
histidine ammonia-lyase [EC:4.3.1.3]
K01712  
urocanate hydratase [EC:4.2.1.49]
K01468  
imidazolonepropionase [EC:3.5.2.7]
K01479  
formiminoglutamase [EC:3.5.3.8]
K00603  
glutamate formiminotransferase [EC:2.1.2.5]
K13990  
glutamate formiminotransferase / formiminotetrahydrofolate cyclodeaminase [EC:4.3.1.4 2.1.2.5]
K05603  
formimidoylglutamate deiminase [EC:3.5.3.13]
K01458  
N-formylglutamate deformylase [EC:3.5.1.68]
K00492  
[EC:1.14.13.-]
K01590  
histidine decarboxylase [EC:4.1.1.22]
K01593  
aromatic-L-amino-acid decarboxylase [EC:4.1.1.28]
K11182  
diamine oxidase [EC:1.4.3.22]
K00128  
aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085  
aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.3 1.2.1.8 1.2.1.31]
K00149  
aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.3 1.2.1.47]
K01437  
aspartoacylase [EC:3.5.1.15]
K00546  
histamine N-methyltransferase [EC:2.1.1.8]
K00274  
monoamine oxidase [EC:1.4.3.4]
K00129  
aldehyde dehydrogenase (NAD(P)+) [EC:1.2.1.5]
K14755  
carnosine synthase [EC:6.3.2.11]
K08660  
cytosolic nonspecific dipeptidase [EC:3.4.13.18]
K05604  
beta-Ala-His dipeptidase [EC:3.4.13.20]
K00599  
[EC:2.1.1.-]
Compound
C00025  
L-Glutamate
C00026  
2-Oxoglutarate
C00049  
L-Aspartate
C00119  
5-Phospho-alpha-D-ribose 1-diphosphate
C00135  
L-Histidine
C00386  
Carnosine
C00388  
Histamine
C00439  
N-Formimino-L-glutamate
C00785  
Urocanate
C00860  
L-Histidinol
C01044  
N-Formyl-L-aspartate
C01045  
N-Formyl-L-glutamate
C01100  
L-Histidinol phosphate
C01152  
N(pi)-Methyl-L-histidine
C01262  
beta-Alanyl-N(pi)-methyl-L-histidine
C01267  
3-(Imidazol-4-yl)-2-oxopropyl phosphate
C01929  
L-Histidinal
C02739  
1-(5-Phospho-D-ribosyl)-ATP
C02741  
Phosphoribosyl-AMP
C02835  
Imidazole-4-acetate
C03277  
Imidazol-5-yl-pyruvate
C03409  
N-Formimino-L-aspartate
C03680  
4-Imidazolone-5-propanoate
C04437  
1-(5-Phosphoribosyl)imidazole-4-acetate
C04666  
D-erythro-1-(Imidazol-4-yl)glycerol 3-phosphate
C04677  
1-(5'-Phosphoribosyl)-5-amino-4-imidazolecarboxamide
C04896  
5-(5-Phospho-D-ribosylaminoformimino)-1-(5-phosphoribosyl)-imidazole-4-carboxamide
C04916  
N-(5'-Phospho-D-1'-ribulosylformimino)-5-amino-1-(5''-phospho-D-ribosyl)-4-imidazolecarboxamide
C05127  
N-Methylhistamine
C05130  
Imidazole-4-acetaldehyde
C05131  
(1-Ribosylimidazole)-4-acetate
C05133  
4-Imidazolone-5-acetate
C05135  
4-(beta-Acetylaminoethyl)imidazole
C05565  
Hydantoin-5-propionate
C05568  
Imidazole lactate
C05570  
Ergothioneine
C05571  
Thiourocanic acid
C05572  
4-Oxoglutaramate
C05575  
Hercynine
C05827  
Methylimidazole acetaldehyde
C05828  
Methylimidazoleacetic acid
C05829  
N-Carbamyl-L-glutamate
C16673  
Isoglutamine
C16674  
Formylisoglutamine

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