KEGG   PATHWAY: ko00531Help
Entry
ko00531                     Pathway                                

Name
Glycosaminoglycan degradation
Class
Metabolism; Glycan biosynthesis and metabolism
BRITE hierarchy
Pathway map
Glycosaminoglycan degradation
ko00531

All organismsOrtholog table
Module
M00076  
Dermatan sulfate degradation [PATH:ko00531]
M00077  
Chondroitin sulfate degradation [PATH:ko00531]
M00078  
Heparan sulfate degradation [PATH:ko00531]
M00079  
Keratan sulfate degradation [PATH:ko00531]
Disease
H00123  
Mucopolysaccharidosis type IV (MPS4)
H00124  
GM2 gangliosidoses
H00128  
Mucopolysaccharidosis type I (MPS1)
H00129  
Mucopolysaccharidosis type II (MPS2)
H00130  
Mucopolysaccharidosis type III (MPS3)
H00131  
Mucopolysaccharidosis type VI (MPS6)
H00132  
Mucopolysaccharidosis type VII (MPS7)
H00133  
Mucopolysaccharidosis type IX (MPS9)
H00281  
GM1 gangliosidosis
H00753  
Urofacial syndrome
Orthology
K01136  
iduronate 2-sulfatase [EC:3.1.6.13]
K01217  
L-iduronidase [EC:3.2.1.76]
K01135  
arylsulfatase B [EC:3.1.6.12]
K01197  
hyaluronoglucosaminidase [EC:3.2.1.35]
K01195  
beta-glucuronidase [EC:3.2.1.31]
K07964  
heparanase 1 [EC:3.2.1.166]
K07965  
heparanase 2 [EC:3.2.1.-]
K01565  
N-sulfoglucosamine sulfohydrolase [EC:3.10.1.1]
K10532  
heparan-alpha-glucosaminide N-acetyltransferase [EC:2.3.1.78]
K01205  
alpha-N-acetylglucosaminidase [EC:3.2.1.50]
K01132  
N-acetylgalactosamine-6-sulfatase [EC:3.1.6.4]
K12309  
beta-galactosidase [EC:3.2.1.23]
K01137  
N-acetylglucosamine-6-sulfatase [EC:3.1.6.14]
K12373  
hexosaminidase [EC:3.2.1.52]
Compound
C00426  
Dermatan sulfate
C00573  
Keratan sulfate
C00634  
Chondroitin 4-sulfate
C00925  
Heparan sulfate
G00872  
DWA-2
G02632  
 
G06780  
 
G08421  
 
G09660  
 
G12336  
 
G13031  
 
G13032  
 
G13033  
 
G13034  
 
G13035  
 
G13036  
 
G13037  
 
G13038  
 
G13039  
 
G13040  
 
G13041  
 
G13042  
 
G13043  
 

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