KEGG   ORTHOLOGY: K12309Help
Entry
K12309                      KO                                     

Name
GLB1, ELNR1
Definition
beta-galactosidase [EC:3.2.1.23]
Pathway
Galactose metabolism
Other glycan degradation
Glycosaminoglycan degradation
Sphingolipid metabolism
Glycosphingolipid biosynthesis - ganglio series
Lysosome
Module
M00079  
Keratan sulfate degradation
Disease
H00123  
Mucopolysaccharidosis type IV (MPS4)
H00276  
Galactosialidosis
H00281  
GM1 gangliosidosis
Brite
KEGG Orthology (KO) [BR:ko00001]
 Metabolism
  Carbohydrate metabolism
   00052 Galactose metabolism
    K12309  GLB1, ELNR1; beta-galactosidase
  Lipid metabolism
   00600 Sphingolipid metabolism
    K12309  GLB1, ELNR1; beta-galactosidase
  Glycan biosynthesis and metabolism
   00531 Glycosaminoglycan degradation
    K12309  GLB1, ELNR1; beta-galactosidase
   00604 Glycosphingolipid biosynthesis - ganglio series
    K12309  GLB1, ELNR1; beta-galactosidase
   00511 Other glycan degradation
    K12309  GLB1, ELNR1; beta-galactosidase
 Cellular Processes
  Transport and catabolism
   04142 Lysosome
    K12309  GLB1, ELNR1; beta-galactosidase
KEGG pathway modules [BR:ko00002]
 Pathway module
  Carbohydrate and lipid metabolism
   Glycosaminoglycan metabolism
    M00079  Keratan sulfate degradation
     K12309  GLB1, ELNR1; beta-galactosidase
Enzymes [BR:ko01000]
 3. Hydrolases
  3.2  Glycosylases
   3.2.1  Glycosidases, i.e. enzymes that hydrolyse O- and S-glycosyl compounds
    3.2.1.23  beta-galactosidase
     K12309  GLB1, ELNR1; beta-galactosidase
BRITE hierarchy
Other DBs
Genes
HSA: 
2720(GLB1)
PTR: 
460254(GLB1)
PPS: 
100978745(GLB1)
GGO: 
101125280(GLB1)
PON: 
100173272(GLB1)
MCC: 
MMU: 
12091(Glb1)
RNO: 
316033(Glb1)
CFA: 
403873(GLB1)
AML: 
FCA: 
493927(GLB1)
BTA: 
507188(GLB1)
ECB: 
MDO: 
SHR: 
100921364(GLB1)
OAA: 
GGA: 
420720(GLB1)
MGP: 
TGU: 
100226450(GLB1)
ACS: 
XLA: 
100158367(glb1l)
XTR: 
548712(glb1l)
DRE: 
548343(glb1)
TRU: 
OLA: 
BFO: 
SPU: 
DME: 
DPO: 
DAN: 
DER: 
DPE: 
DSE: 
DSI: 
DWI: 
DYA: 
DGR: 
DMO: 
DVI: 
AGA: 
AAG: 
CQU: 
AME: 
NVI: 
100119157(NV18425) 100119373(NV18427)
API: 
PHU: 
ISC: 
CEL: 
CELE_T19B10.3(T19B10.3)
CBR: 
TSP: 
SMM: 
NVE: 
HMG: 
AQU: 
ATH: 
AT1G72990(BGAL17) AT3G52840(BGAL2)
ALY: 
GMX: 
MTR: 
CSV: 
RCU: 
POP: 
VVI: 
OSA: 
DOSA: 
Os05t0539400-01(Os05g0539400)
BDI: 
SBI: 
SORBI_09g026870(SORBIDRAFT_09g026870)
ZMA: 
SMO: 
PPP: 
DDI: 
 » show all
TaxonomyKoalaUniProt
Reference
  Authors
Ohto U, Usui K, Ochi T, Yuki K, Satow Y, Shimizu T
  Title
Crystal structure of human beta-galactosidase: structural basis of Gm1 gangliosidosis and morquio B diseases.
  Journal
J Biol Chem 287:1801-12 (2012)

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