KEGG   Nomascus leucogenys (northern white-cheeked gibbon): 100590008
Entry
100590008         CDS       T03265                                 
Symbol
MCCC1
Name
(RefSeq) methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X1
  KO
K01968  3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
Organism
nle  Nomascus leucogenys (northern white-cheeked gibbon)
Pathway
nle00280  Valine, leucine and isoleucine degradation
nle01100  Metabolic pathways
Module
nle_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:nle00001]
 09100 Metabolism
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    100590008 (MCCC1)
Enzymes [BR:nle01000]
 6. Ligases
  6.4  Forming carbon-carbon bonds
   6.4.1  Ligases that form carbon-carbon bonds (only sub-subclass identified to date)
    6.4.1.4  methylcrotonoyl-CoA carboxylase
     100590008 (MCCC1)
SSDB
Motif
Pfam: CPSase_L_D2 Biotin_carb_N Biotin_carb_C Biotin_lipoyl Dala_Dala_lig_C ATP-grasp Biotin_lipoyl_2 RimK ATP-grasp_3 ATPgrasp_ST GARS_A ATP-grasp_4 RnfC_N 2OG-FeII_Oxy_2 NQRA
Other DBs
NCBI-GeneID: 100590008
NCBI-ProteinID: XP_012366215
Ensembl: ENSNLEG00000005989
Position
11:complement(104209177..104300386)
AA seq 725 aa
MAAASAVSVLLVAAERNRWHRLPSLLLPPRTWVWRQRTMKYTTTTGRNITKVLIANRGEI
ACRVMRTAKKLGVQTVAVYSEADRNSMHVDMADEAYSIGPAPCQQSYLSMEKIIQVAKAS
AAQAIHPGYGFLSENMEFAELCKQEGIIFIGPPPSAIRDMGIKSTSKSIMAAAGVPVVEG
YHGEDQSDQCLKEHAGRIGYPVMIKAVRGGGGKGMRIVRSEQEFQEQLESVRREAKKSFN
DDAVLIEKFVDTPRHVEVQVFGDHHGNAVYLFERDCSVQRRHQKIIEEAPAPGIKPEVRK
KLGEAAVRAAKAVNYVGAGTVEFIMDSKHNFYFMEMNTRLQVEHPVTEMITGTDLVEWQL
RIAAGEKIPLSQEEITLQGHAFEARIYAEDPSNNFMPGAGPLVHLSTPRADPSTRIETGV
RQGDEVSVHYDPMIAKLVVWAADRQAALTKLRYSLRQYNIVGLHTNIDFLLNLSGHPEFE
AGNVHTDFIPQHHKQLLLSRKAAAKESLCQAALGLILKEKAVTDTFALQAHDQFSPFSSS
SGRRLNISYTRNVTLKDGKNNVAIAVTYNRDGSYSMQIEDKTFQVLGDLYSEGDCTYLKC
SVNGVASKAKLIILENTIYLFSKEGSIEIDIPVPKYLSSVSLQGTQGGPLAPMTGTIEKV
FVKAGDKVKAGDFLMVMIAMKMEHTIKAPKDGTIKKVFYREGAQADRHTPLVEFEEEESD
KRESE
NT seq 2178 nt   +upstreamnt  +downstreamnt
atggcggcggcctctgcggtgtcggtgctgctggtggcggcagagaggaaccggtggcat
cgtctcccgagcctgctcctgccgccgaggacatgggtgtggaggcaaagaaccatgaag
tacacaacaaccacaggaagaaacattaccaaggtcctcattgcaaacagaggagaaatt
gcctgcagggtgatgcgcacagccaaaaaactgggtgtacagactgtggcggtttatagt
gaggctgacagaaattccatgcatgtagatatggcagatgaagcatattccatcggcccc
gctccctgccagcagagctacctatctatggagaaaatcattcaagtggccaaggcctct
gctgcacaggctatccatccaggatatggttttctttcagaaaacatggaatttgctgaa
ctttgtaagcaagaaggaattatttttataggccctcctccatctgcaattagagacatg
ggtataaagagcacatccaaatccataatggctgctgctggagtacctgttgtggagggt
tatcatggtgaggaccaatcagaccagtgcctgaaggaacacgccgggagaattggctat
cctgtcatgattaaagctgtccggggtggaggaggaaaaggaatgaggattgttagatca
gaacaagaatttcaagaacagttagagtcagtgcggagagaagctaagaagtctttcaat
gatgatgctgtgttgatcgagaagtttgtagacacaccgaggcatgtagaagtccaggtg
tttggtgatcaccatggcaatgctgtgtacttgtttgaaagagactgtagtgtgcagagg
cgacatcagaagatcattgaggaggccccagcgcctggtattaaacctgaagtaagaaaa
aagctgggagaagctgcagtcagagctgctaaagctgtaaattatgttggagcagggact
gtggagtttattatggactcaaaacataatttctatttcatggagatgaatacaaggctg
caagtggaacatcctgttactgagatgatcacaggaactgacttggtggagtggcagctt
agaattgcagcaggagagaagattcctttgagccaggaagaaataactctgcagggccat
gccttcgaagctagaatatatgcagaagatcctagcaataacttcatgcctggggctggc
ccattagtgcacctctctactcctcgagcagacccttccaccaggattgaaactggagta
cggcaaggagacgaagtttccgtgcattatgaccccatgattgcgaagctggtcgtgtgg
gctgcagatcgccaggcggcattgacaaaactgaggtacagccttcgtcagtacaatatt
gttggactacacaccaacattgacttcttactcaacctgtctggccacccagagtttgaa
gctgggaacgtgcacaccgatttcatccctcaacatcacaaacagttgttgctcagtcgg
aaggctgcagccaaagagtctttatgccaggcagccctgggtctcatcctcaaggagaaa
gccgtgactgacacttttgctcttcaggcacatgatcaattctctccattttcgtctagc
agtggaagaagactgaatatctcttataccagaaacgtgactcttaaagatggtaaaaac
aatgtagccatagctgtaacgtataaccgtgatgggtcttatagcatgcagattgaagat
aaaactttccaagtccttggtgatctttacagcgagggagactgcacttacctgaaatgt
tctgttaatggagttgctagtaaagcgaagctgattatcctggaaaacactatttaccta
ttttccaaggaaggaagtattgagattgacattccagtccccaagtacttatcttctgtg
agcttacaaggaactcagggaggccccttagctcctatgactggaaccattgaaaaggtg
tttgtcaaagctggagacaaagtgaaagcgggagatttcctcatggttatgatcgccatg
aagatggagcataccataaaggctccaaaggatggcacaataaagaaagtgttctacaga
gaaggtgctcaggctgacagacacactcctttagtggagtttgaggaggaagaatcagac
aaaagggaatcggaataa

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