KEGG   PATHWAY: hsa00500Help
Entry
hsa00500                    Pathway                                

Name
Starch and sucrose metabolism - Homo sapiens (human)
Class
Metabolism; Carbohydrate metabolism
BRITE hierarchy
Pathway map
Starch and sucrose metabolism
hsa00500

All organismsOrtholog table
Disease
H00069  
Glycogen storage diseases (GSD)
H00115  
Congenital sucrase-isomaltase deficiency
H01002  
Generalized arterial calcification of infancy
H01193  
Familial tumoral calcinosis (FTC)
H01394  
Cole disease
H01760  
Hepatic glycogen storage disease
H01762  
Muscle glycogen storage disease
Drug
D00216  
Acarbose (JAN/USAN/INN)
D00625  
Miglitol (JP17/USAN/INN)
D01665  
Voglibose (JP17/USAN/INN)
D04537  
Ingliforib (USAN/INN)
Other DBs
BSID: 
GO: 
Organism
Homo sapiens (human) [GN:hsa]
Gene
8972  
MGAM; maltase-glucoamylase [KO:K12047] [EC:3.2.1.3 3.2.1.20]
93432  
MGAM2; maltase-glucoamylase 2 (putative) [KO:K12047] [EC:3.2.1.3 3.2.1.20]
2548  
GAA; glucosidase alpha, acid [KO:K12316] [EC:3.2.1.20]
2595  
GANC; glucosidase alpha, neutral C [KO:K12317] [EC:3.2.1.20]
6476  
SI; sucrase-isomaltase [KO:K01203] [EC:3.2.1.10 3.2.1.48]
7360  
UGP2; UDP-glucose pyrophosphorylase 2 [KO:K00963] [EC:2.7.7.9]
5167  
ENPP1; ectonucleotide pyrophosphatase/phosphodiesterase 1 [KO:K01513] [EC:3.6.1.9 3.1.4.1]
5169  
ENPP3; ectonucleotide pyrophosphatase/phosphodiesterase 3 [KO:K01513] [EC:3.6.1.9 3.1.4.1]
57733  
GBA3; glucosylceramidase beta 3 (gene/pseudogene) [KO:K05350] [EC:3.2.1.21]
2998  
GYS2; glycogen synthase 2 [KO:K00693] [EC:2.4.1.11]
2997  
GYS1; glycogen synthase 1 [KO:K00693] [EC:2.4.1.11]
2992  
GYG1; glycogenin 1 [KO:K00750] [EC:2.4.1.186]
8908  
GYG2; glycogenin 2 [KO:K00750] [EC:2.4.1.186]
2632  
GBE1; 1,4-alpha-glucan branching enzyme 1 [KO:K00700] [EC:2.4.1.18]
5836  
PYGL; glycogen phosphorylase L [KO:K00688] [EC:2.4.1.1]
5837  
PYGM; glycogen phosphorylase, muscle associated [KO:K00688] [EC:2.4.1.1]
5834  
PYGB; glycogen phosphorylase B [KO:K00688] [EC:2.4.1.1]
178  
AGL; amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase [KO:K01196] [EC:3.2.1.33 2.4.1.25]
278  
AMY1C; amylase, alpha 1C (salivary) [KO:K01176] [EC:3.2.1.1]
279  
AMY2A; amylase, alpha 2A (pancreatic) [KO:K01176] [EC:3.2.1.1]
276  
AMY1A; amylase, alpha 1A (salivary) [KO:K01176] [EC:3.2.1.1]
280  
AMY2B; amylase, alpha 2B (pancreatic) [KO:K01176] [EC:3.2.1.1]
277  
AMY1B; amylase, alpha 1B (salivary) [KO:K01176] [EC:3.2.1.1]
11181  
TREH; trehalase [KO:K01194] [EC:3.2.1.28]
5236  
PGM1; phosphoglucomutase 1 [KO:K01835] [EC:5.4.2.2]
55276  
PGM2; phosphoglucomutase 2 [KO:K15779] [EC:5.4.2.7 5.4.2.2]
3101  
HK3; hexokinase 3 [KO:K00844] [EC:2.7.1.1]
3098  
HK1; hexokinase 1 [KO:K00844] [EC:2.7.1.1]
3099  
HK2; hexokinase 2 [KO:K00844] [EC:2.7.1.1]
80201  
HKDC1; hexokinase domain containing 1 [KO:K00844] [EC:2.7.1.1]
2645  
GCK; glucokinase [KO:K12407] [EC:2.7.1.2]
2538  
G6PC; glucose-6-phosphatase catalytic subunit [KO:K01084] [EC:3.1.3.9]
57818  
G6PC2; glucose-6-phosphatase catalytic subunit 2 [KO:K01084] [EC:3.1.3.9]
92579  
G6PC3; glucose-6-phosphatase catalytic subunit 3 [KO:K01084] [EC:3.1.3.9]
283209  
PGM2L1; phosphoglucomutase 2 like 1 [KO:K11809] [EC:2.7.1.106]
2821  
GPI; glucose-6-phosphate isomerase [KO:K01810] [EC:5.3.1.9]
Compound
C00029  
UDP-glucose
C00031  
D-Glucose
C00085  
D-Fructose 6-phosphate
C00089  
Sucrose
C00092  
D-Glucose 6-phosphate
C00095  
D-Fructose
C00103  
D-Glucose 1-phosphate
C00185  
Cellobiose
C00208  
Maltose
C00252  
Isomaltose
C00369  
Starch
C00372  
Dextran
C00394  
GDP-glucose
C00498  
ADP-glucose
C00501  
CDP-glucose
C00663  
beta-D-Glucose 1-phosphate
C00689  
alpha,alpha'-Trehalose 6-phosphate
C00718  
Amylose
C00721  
Dextrin
C00760  
Cellulose
C00963  
beta-D-Glucoside
C00965  
1,3-beta-D-Glucan
C00973  
Cyclomaltodextrin
C01083  
alpha,alpha-Trehalose
C01231  
alpha-D-Glucose 1,6-bisphosphate
C01725  
Levanbiose
C01898  
Cellodextrin
C01935  
Maltodextrin
C02591  
Sucrose 6'-phosphate
C02995  
Maltose 6'-phosphate
C03323  
(2,1-beta-D-Fructosyl)n
C04534  
6-Phospho-beta-D-glucosyl-(1,4)-D-glucose
C05731  
3-Ketosucrose
C06215  
Levan
C06400  
1-alpha-D-[(1->4)-alpha-D-Glucosyl](n-1)-alpha-D-glucopyranoside
C16688  
Sucrose 6-phosphate
C20237  
alpha-Maltose 1-phosphate
KO pathway
 

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