KEGG   PATHWAY: hsa00500Help
Entry
hsa00500                    Pathway                                

Name
Starch and sucrose metabolism - Homo sapiens (human)
Class
Metabolism; Carbohydrate metabolism
BRITE hierarchy
Pathway map
Starch and sucrose metabolism
hsa00500

All organismsOrtholog table
Disease
H00069  
Glycogen storage diseases (GSD)
H00115  
Congenital sucrase-isomaltase deficiency
H01002  
Generalized arterial calcification of infancy
H01193  
Familial tumoral calcinosis (FTC)
H01394  
Cole disease
H01760  
Hepatic glycogen storage disease
H01762  
Muscle glycogen storage disease
H01941  
Glycogen storage disease type III
H01942  
Glycogen storage disease type IV
H01943  
Glycogen storage disease type V
H01944  
Glycogen storage disease type VI
H01949  
Glycogen storage disease type 0b
H01950  
Glycogen storage disease type 0a
H01954  
Glycogen storage disease type XIV
H01955  
Glycogen storage disease type XV
Drug
D00216  
Acarbose (JAN/USAN/INN)
D00625  
Miglitol (JP17/USAN/INN)
D01665  
Voglibose (JP17/USAN/INN)
D04537  
Ingliforib (USAN/INN)
Other DBs
BSID: 
GO: 
Organism
Homo sapiens (human) [GN:hsa]
Gene
8972  
MGAM; maltase-glucoamylase [KO:K12047] [EC:3.2.1.3 3.2.1.20]
93432  
MGAM2; maltase-glucoamylase 2 (putative) [KO:K12047] [EC:3.2.1.3 3.2.1.20]
2548  
GAA; glucosidase alpha, acid [KO:K12316] [EC:3.2.1.20]
2595  
GANC; glucosidase alpha, neutral C [KO:K12317] [EC:3.2.1.20]
6476  
SI; sucrase-isomaltase [KO:K01203] [EC:3.2.1.10 3.2.1.48]
7360  
UGP2; UDP-glucose pyrophosphorylase 2 [KO:K00963] [EC:2.7.7.9]
5167  
ENPP1; ectonucleotide pyrophosphatase/phosphodiesterase 1 [KO:K01513] [EC:3.6.1.9 3.1.4.1]
5169  
ENPP3; ectonucleotide pyrophosphatase/phosphodiesterase 3 [KO:K01513] [EC:3.6.1.9 3.1.4.1]
57733  
GBA3; glucosylceramidase beta 3 (gene/pseudogene) [KO:K05350] [EC:3.2.1.21]
2998  
GYS2; glycogen synthase 2 [KO:K00693] [EC:2.4.1.11]
2997  
GYS1; glycogen synthase 1 [KO:K00693] [EC:2.4.1.11]
2992  
GYG1; glycogenin 1 [KO:K00750] [EC:2.4.1.186]
8908  
GYG2; glycogenin 2 [KO:K00750] [EC:2.4.1.186]
2632  
GBE1; 1,4-alpha-glucan branching enzyme 1 [KO:K00700] [EC:2.4.1.18]
5836  
PYGL; glycogen phosphorylase L [KO:K00688] [EC:2.4.1.1]
5837  
PYGM; glycogen phosphorylase, muscle associated [KO:K00688] [EC:2.4.1.1]
5834  
PYGB; glycogen phosphorylase B [KO:K00688] [EC:2.4.1.1]
178  
AGL; amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase [KO:K01196] [EC:3.2.1.33 2.4.1.25]
278  
AMY1C; amylase, alpha 1C (salivary) [KO:K01176] [EC:3.2.1.1]
279  
AMY2A; amylase, alpha 2A (pancreatic) [KO:K01176] [EC:3.2.1.1]
276  
AMY1A; amylase, alpha 1A (salivary) [KO:K01176] [EC:3.2.1.1]
280  
AMY2B; amylase, alpha 2B (pancreatic) [KO:K01176] [EC:3.2.1.1]
277  
AMY1B; amylase, alpha 1B (salivary) [KO:K01176] [EC:3.2.1.1]
11181  
TREH; trehalase [KO:K01194] [EC:3.2.1.28]
5236  
PGM1; phosphoglucomutase 1 [KO:K01835] [EC:5.4.2.2]
55276  
PGM2; phosphoglucomutase 2 [KO:K15779] [EC:5.4.2.7 5.4.2.2]
3101  
HK3; hexokinase 3 [KO:K00844] [EC:2.7.1.1]
3098  
HK1; hexokinase 1 [KO:K00844] [EC:2.7.1.1]
3099  
HK2; hexokinase 2 [KO:K00844] [EC:2.7.1.1]
80201  
HKDC1; hexokinase domain containing 1 [KO:K00844] [EC:2.7.1.1]
2645  
GCK; glucokinase [KO:K12407] [EC:2.7.1.2]
2538  
G6PC; glucose-6-phosphatase catalytic subunit [KO:K01084] [EC:3.1.3.9]
57818  
G6PC2; glucose-6-phosphatase catalytic subunit 2 [KO:K01084] [EC:3.1.3.9]
92579  
G6PC3; glucose-6-phosphatase catalytic subunit 3 [KO:K01084] [EC:3.1.3.9]
283209  
PGM2L1; phosphoglucomutase 2 like 1 [KO:K11809] [EC:2.7.1.106]
2821  
GPI; glucose-6-phosphate isomerase [KO:K01810] [EC:5.3.1.9]
Compound
C00029  
UDP-glucose
C00031  
D-Glucose
C00085  
D-Fructose 6-phosphate
C00089  
Sucrose
C00092  
D-Glucose 6-phosphate
C00095  
D-Fructose
C00103  
D-Glucose 1-phosphate
C00185  
Cellobiose
C00208  
Maltose
C00252  
Isomaltose
C00369  
Starch
C00372  
Dextran
C00394  
GDP-glucose
C00498  
ADP-glucose
C00501  
CDP-glucose
C00663  
beta-D-Glucose 1-phosphate
C00689  
alpha,alpha'-Trehalose 6-phosphate
C00718  
Amylose
C00721  
Dextrin
C00760  
Cellulose
C00963  
beta-D-Glucoside
C00965  
1,3-beta-D-Glucan
C00973  
Cyclomaltodextrin
C01083  
alpha,alpha-Trehalose
C01231  
alpha-D-Glucose 1,6-bisphosphate
C01725  
Levanbiose
C01898  
Cellodextrin
C01935  
Maltodextrin
C02591  
Sucrose 6'-phosphate
C02995  
Maltose 6'-phosphate
C03323  
(2,1-beta-D-Fructosyl)n
C04534  
6-Phospho-beta-D-glucosyl-(1,4)-D-glucose
C05731  
3-Ketosucrose
C06215  
Levan
C06400  
1-alpha-D-[(1->4)-alpha-D-Glucosyl](n-1)-alpha-D-glucopyranoside
C16688  
Sucrose 6-phosphate
C20237  
alpha-Maltose 1-phosphate
KO pathway
 

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