KEGG   PATHWAY: hsa00601Help
Entry
hsa00601                    Pathway                                

Name
Glycosphingolipid biosynthesis - lacto and neolacto series - Homo sapiens (human)
Class
Metabolism; Glycan biosynthesis and metabolism
BRITE hierarchy
Pathway map
Glycosphingolipid biosynthesis - lacto and neolacto series
hsa00601

All organismsOrtholog table
Module
Glycosphingolipid biosynthesis, lacto-series, LacCer => Lc4Cer [PATH:hsa00601]
Glycosphingolipid biosynthesis, neolacto-series, LacCer => nLc4Cer [PATH:hsa00601]
Disease
H00606  
Early infantile epileptic encephalopathy
H00768  
Nonsyndromic autosomal recessive mental retardation (NS-ARMR)
H01013  
Adult i phenotype
H01202  
Cataract
H01460  
West syndrome
Organism
Homo sapiens (human) [GN:hsa]
Gene
84002  
B3GNT5; UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 5 [KO:K03766] [EC:2.4.1.206]
8708  
B3GALT1; beta-1,3-galactosyltransferase 1 [KO:K07819] [EC:2.4.1.-]
8707  
B3GALT2; beta-1,3-galactosyltransferase 2 [KO:K07820] [EC:2.4.1.-]
10317  
B3GALT5; beta-1,3-galactosyltransferase 5 [KO:K03877] [EC:2.4.1.-]
2523  
FUT1; fucosyltransferase 1 (H blood group) [KO:K00718] [EC:2.4.1.69]
2524  
FUT2; fucosyltransferase 2 [KO:K00718] [EC:2.4.1.69]
2525  
FUT3; fucosyltransferase 3 (Lewis blood group) [KO:K00716] [EC:2.4.1.65]
6487  
ST3GAL3; ST3 beta-galactoside alpha-2,3-sialyltransferase 3 [KO:K00781] [EC:2.4.99.6]
6484  
ST3GAL4; ST3 beta-galactoside alpha-2,3-sialyltransferase 4 [KO:K03494] [EC:2.4.99.4]
28  
ABO; ABO blood group (transferase A, alpha 1-3-N-acetylgalactosaminyltransferase [KO:K00709] [EC:2.4.1.37 2.4.1.40]
2683  
B4GALT1; beta-1,4-galactosyltransferase 1 [KO:K07966] [EC:2.4.1.- 2.4.1.38 2.4.1.90 2.4.1.22]
8704  
B4GALT2; beta-1,4-galactosyltransferase 2 [KO:K07967] [EC:2.4.1.- 2.4.1.38 2.4.1.90 2.4.1.22]
8703  
B4GALT3; beta-1,4-galactosyltransferase 3 [KO:K07968] [EC:2.4.1.- 2.4.1.38 2.4.1.90]
8702  
B4GALT4; beta-1,4-galactosyltransferase 4 [KO:K07969] [EC:2.4.1.- 2.4.1.275 2.4.1.90]
10690  
FUT9; fucosyltransferase 9 [KO:K03663] [EC:2.4.1.152]
2526  
FUT4; fucosyltransferase 4 [KO:K07632] [EC:2.4.1.-]
2527  
FUT5; fucosyltransferase 5 [KO:K07633] [EC:2.4.1.65]
2528  
FUT6; fucosyltransferase 6 [KO:K07634] [EC:2.4.1.65]
2529  
FUT7; fucosyltransferase 7 [KO:K07635] [EC:2.4.1.-]
10402  
ST3GAL6; ST3 beta-galactoside alpha-2,3-sialyltransferase 6 [KO:K03792] [EC:2.4.99.10]
6489  
ST8SIA1; ST8 alpha-N-acetyl-neuraminide alpha-2,8-sialyltransferase 1 [KO:K03371] [EC:2.4.99.8]
10678  
B3GNT2; UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 2 [KO:K00741] [EC:2.4.1.149]
11041  
B4GAT1; beta-1,4-glucuronyltransferase 1 [KO:K00741] [EC:2.4.1.149]
10331  
B3GNT3; UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 3 [KO:K07970] [EC:2.4.1.-]
79369  
B3GNT4; UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 4 [KO:K07971] [EC:2.4.1.-]
2651  
GCNT2; glucosaminyl (N-acetyl) transferase 2, I-branching enzyme (I blood group) [KO:K00742] [EC:2.4.1.150]
Compound
G00036  
Lc3Cer
G00037  
Lc4Cer
G00038  
 
G00039  
Type IB glycolipid
G00040  
 
G00042  
Type IA glycolipid
G00043  
 
G00044  
IV2Fuc-Lc4Cer
G00045  
IV2Fuc,III4Fuc-Lc4Cer
G00046  
Fuc-Lc4Cer
G00047  
3'-isoLM1
G00048  
Fuc-3'-isoLM1
G00050  
Paragloboside
G00051  
nLc5Cer
G00052  
Type II B antigen
G00054  
Type II A antigen
G00055  
IV2Fuc-nLc4Cer
G00056  
III3,IV2Fuc-nLc4Cer
G00057  
 
G00058  
Type IIIH glycolipid
G00059  
Type IIIA glycolipid
G00060  
III3Fuc-nLc4Cer
G00061  
Sialyl-6-paragloboside
G00062  
Sialyl-3-paragloboside
G00063  
IV3NeuAc,III3Fuc-nLc4Cer
G00064  
3',8'-LD1
G00066  
nLc5Cer
G00067  
nLc6Cer
G00068  
nLc7Cer
G00069  
nLc8Cer
G00071  
VI2Fuc-nLc6
G00072  
 
G00073  
 
G00074  
 
G00075  
Type IIIAb
G00076  
III3Fuc-nLc6Cer
G00077  
 
G00078  
iso-nLc8Cer
G00079  
 
G00080  
 
G00081  
 
G00082  
 
G00083  
 
G00084  
 
G00085  
 
G00086  
 
G00087  
VI6NeuAc-nLc6Cer
G00088  
VI3NeuAc-nLc6Cer
G00089  
V3Fuc-nLc6Cer
G00090  
V3Fuc,III3Fuc-nLc6Cer
G00091  
 
G00092  
Lactosylceramide
KO pathway
 

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