| Acetyl-CoA |
| Thiamin diphosphate |
| Succinyl-CoA |
| Propanoyl-CoA |
| L-Leucine |
| 3-Methyl-2-oxobutanoic acid |
| Acetoacetate |
| L-Valine |
| 4-Methyl-2-oxopentanoate |
| Acetoacetyl-CoA |
| (S)-3-Hydroxy-3-methylglutaryl-CoA |
| L-Isoleucine |
| 2-Methylpropanoyl-CoA |
| (S)-3-Methyl-2-oxopentanoic acid |
| (S)-Methylmalonyl-CoA |
| (R)-Methylmalonyl-CoA |
| Methylmalonate |
| (3R)-beta-Leucine |
| 3-Methylbutanoyl-CoA |
| 3-Methylcrotonyl-CoA |
| 3-Methylglutaconyl-CoA |
| L-3-Amino-isobutanoate |
| 2-Methylacetoacetyl-CoA |
| 2-Methylbut-2-enoyl-CoA |
| 2-Methylprop-2-enoyl-CoA |
| beta-Ketoisocaproate |
| (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA |
| Branched chain fatty acid |
| 3-Hydroxyisovaleryl-CoA |
| (S)-3-Hydroxyisobutyryl-CoA |
| (S)-3-Hydroxyisobutyrate |
| (S)-Methylmalonate semialdehyde |
| Enzyme N6-(lipoyl)lysine |
| Enzyme N6-(dihydrolipoyl)lysine |
| 3-Methyl-1-hydroxybutyl-ThPP |
| [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine |
| 2-Methyl-1-hydroxypropyl-ThPP |
| [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine |
| 2-Methyl-1-hydroxybutyl-ThPP |
| [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine |
| (S)-2-Methylbutanoyl-CoA |