KEGG   Pongo abelii (Sumatran orangutan): 100437483
Entry
100437483         CDS       T01416                                 
Symbol
MCCC1
Name
(RefSeq) methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
  KO
K01968  3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
Organism
pon  Pongo abelii (Sumatran orangutan)
Pathway
pon00280  Valine, leucine and isoleucine degradation
pon01100  Metabolic pathways
Module
pon_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:pon00001]
 09100 Metabolism
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    100437483 (MCCC1)
Enzymes [BR:pon01000]
 6. Ligases
  6.4  Forming carbon-carbon bonds
   6.4.1  Ligases that form carbon-carbon bonds (only sub-subclass identified to date)
    6.4.1.4  methylcrotonoyl-CoA carboxylase
     100437483 (MCCC1)
SSDB
Motif
Pfam: CPSase_L_D2 Biotin_carb_N Biotin_carb_C Biotin_lipoyl Dala_Dala_lig_C ATP-grasp Biotin_lipoyl_2 RimK ATP-grasp_3 ATPgrasp_ST ATP-grasp_4 GARS_A RnfC_N MCCA_BT NQRA 2OG-FeII_Oxy_2
Other DBs
NCBI-GeneID: 100437483
NCBI-ProteinID: XP_002814381
Ensembl: ENSPPYG00000014331
UniProt: H2PC45
Position
3:complement(180709655..180784868)
AA seq 725 aa
MAAASAVSVLLVAAERNRWHRLPSLLLPPRTWVWRQRTMKYPTTTGRNITKVLIANRGEI
ACRVMRTAKKLGVQTVAVYSEADRNSMHVDMADEAYSIGPAPSQQSYLSMEKIIQVAKTS
AAQAIHPGYGFLSENMEFAELCKQEGIIFIGPPPSAIRDMGIKSTSKSIMAAAGVPVVEG
YHGEDQSDQCLKEHAGRIGYPVMIKAVRGGGGKGMRIVRSEQEFQEQLESARREAKKSFN
DDAMLIEKFVDTPRHVEVQVFGDHHGNAVYLFERDCSVQRRHQKIIEEAPAPGIKPEVRK
KLGEAAVRAARAVNYVGAGTVEFIMDSKHNFYFMEMNTRLQVEHPVTEMITGTDLVEWQL
RIAAGEKIPLSQEEITLQGHAFEARIYAEDPGNNFMPGAGPLVHLSTPRADPSTRIETGV
RQGDEVSVHYDPMIAKLVVWAADRQAALTKLRYSLLQYNIVGLHTNIDFLLNLSGHPEFE
AGNVHTDFIPQHHKQLLLSQKAATKESLCQAALGLILKEKAMTDAFTLQAHDQFSPFSSS
SGRRLNISYTRNMTLKDGKNNVAIAVTYNHDGSYSMQIEDKTFQVLGDLYSEGDCTYLKC
SVNGVASKVKLIILENTIYLFSKEGSTEIDIPVPKYLSSVSSQGTQGGPLAPMTGTIEKV
FVKAGDKVKAGDSLMVMIAMKMEHTIKAPKDGTIKKVFYREGAQADRHTPLVEFEEEESD
KRESE
NT seq 2178 nt   +upstreamnt  +downstreamnt
atggcagcggcctctgcggtgtcggtgctgctagtggcggcggagaggaaccggtggcat
cgtctcccgagcctgcttctgccgccgaggacatgggtgtggaggcaaagaaccatgaag
tacccaacaaccacaggaagaaacattaccaaggtcctcattgcaaacagaggagaaatt
gcctgcagggtgatgcgcacagccaaaaaactgggtgtacagactgtggcggtttatagt
gaggctgacagaaattccatgcatgtagatatggcagatgaagcatattccatcggcccc
gctccctcccagcagagctacctatctatggagaaaatcattcaagtggccaagacatct
gctgcacaggctatccatccaggatatggttttctttcagaaaacatggaatttgctgaa
ctttgtaagcaagaaggaattatttttataggccctcctccatctgcaattagagacatg
ggtataaagagcacatccaaatccataatggctgctgctggagtacctgttgtggagggt
tatcatggtgaggaccaatcagatcagtgcctgaaggaacacgccgggagaattggctat
cctgtcatgattaaagccgtccggggtggaggaggaaaaggaatgaggattgttagatca
gaacaagaatttcaagaacagttagagtcagcgcggagagaagctaagaagtctttcaat
gatgatgctatgctgatcgagaagtttgtagacacaccgaggcatgtagaagtccaggtg
tttggtgatcaccatggcaatgctgtgtacttgtttgaaagagactgtagtgtgcagagg
cgacatcagaagatcattgaggaggccccagcgcctggtattaaacctgaagtaagaaaa
aagctgggagaagctgcagtcagagctgctagagctgtaaattatgttggagcagggact
gtggagtttattatggactcgaaacataatttctatttcatggagatgaatacaaggctg
caagtggaacatcctgttactgagatgatcacaggaactgacttggtggagtggcagctt
agaattgcagcaggagagaagattcctttgagccaggaagaaataactctgcagggccat
gccttcgaagctagaatatacgcagaagatcctggcaataacttcatgcctggggctggc
ccattagtgcacctctctactcctcgagcagacccttccaccaggattgaaactggagta
cggcaaggagacgaagtttccgtgcattatgaccccatgattgcgaagctggtcgtgtgg
gctgcagatcgccaggcggcattgacaaaactgaggtacagccttcttcagtacaatatt
gttggactgcacaccaacattgacttcttactcaacctgtctggccacccagagtttgaa
gctgggaacgtgcacactgatttcatccctcaacaccacaaacagttgttgctcagtcag
aaggctgcaaccaaagagtctttatgccaggcagccctgggtctcatcctcaaggagaaa
gccatgaccgacgctttcactcttcaggcacacgatcaattctctccattttcatctagc
agtggaagaagactgaatatctcttataccagaaacatgactcttaaagatggtaaaaac
aatgtagccatagctgtaacatataaccatgatgggtcttatagcatgcagattgaagat
aaaactttccaagtccttggtgatctttacagcgagggagactgcacttacctgaaatgt
tctgttaatggagttgctagtaaagtgaagctgattatcctggaaaacactatttaccta
ttttccaaggaaggaagtactgagattgacattccagtccccaaatacttatcttctgtg
agctcacaaggaactcagggaggccccttagctcctatgactggaaccattgaaaaggtg
tttgtcaaagctggagacaaagtgaaagcgggagattccctcatggttatgatcgccatg
aagatggagcataccataaaggctccaaaggatggcacaataaagaaagtgttctacaga
gagggtgctcaggccgacagacacactcctttagtcgagtttgaggaggaagaatcagac
aaaagggaatcggaataa

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