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KO |
09100 Metabolism
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09101 Carbohydrate metabolism
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09102 Energy metabolism
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09103 Lipid metabolism
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00061 Fatty acid biosynthesis [PATH:hsa00061]
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00062 Fatty acid elongation [PATH:hsa00062]
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10449 ACAA2; acetyl-CoA acyltransferase 2
3032 HADHB; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
3033 HADH; hydroxyacyl-CoA dehydrogenase
3030 HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
1892 ECHS1; enoyl-CoA hydratase, short chain 1
51102 MECR; mitochondrial trans-2-enoyl-CoA reductase
5538 PPT1; palmitoyl-protein thioesterase 1
9374 PPT2; palmitoyl-protein thioesterase 2
64834 ELOVL1; ELOVL fatty acid elongase 1
54898 ELOVL2; ELOVL fatty acid elongase 2
83401 ELOVL3; ELOVL fatty acid elongase 3
6785 ELOVL4; ELOVL fatty acid elongase 4
60481 ELOVL5; ELOVL fatty acid elongase 5
79071 ELOVL6; ELOVL fatty acid elongase 6
79993 ELOVL7; ELOVL fatty acid elongase 7
51144 HSD17B12; hydroxysteroid 17-beta dehydrogenase 12
201562 HACD2; 3-hydroxyacyl-CoA dehydratase 2
9200 HACD1; 3-hydroxyacyl-CoA dehydratase 1
401494 HACD4; 3-hydroxyacyl-CoA dehydratase 4
51495 HACD3; 3-hydroxyacyl-CoA dehydratase 3
9524 TECR; trans-2,3-enoyl-CoA reductase
122970 ACOT4; acyl-CoA thioesterase 4
10965 ACOT2; acyl-CoA thioesterase 2
641371 ACOT1; acyl-CoA thioesterase 1
11332 ACOT7; acyl-CoA thioesterase 7
117145 THEM4; thioesterase superfamily member 4
284486 THEM5; thioesterase superfamily member 5
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K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K07512 MECR; mitochondrial enoyl-[acyl-carrier protein] reductase / trans-2-enoyl-CoA reductase [EC:1.3.1.- 1.3.1.38]
K01074 PPT; palmitoyl-protein thioesterase [EC:3.1.2.22]
K01074 PPT; palmitoyl-protein thioesterase [EC:3.1.2.22]
K10247 ELOVL1; elongation of very long chain fatty acids protein 1 [EC:2.3.1.199]
K10205 ELOVL2; elongation of very long chain fatty acids protein 2 [EC:2.3.1.199]
K10248 ELOVL3; elongation of very long chain fatty acids protein 3 [EC:2.3.1.199]
K10249 ELOVL4; elongation of very long chain fatty acids protein 4 [EC:2.3.1.199]
K10244 ELOVL5; elongation of very long chain fatty acids protein 5 [EC:2.3.1.199]
K10203 ELOVL6; elongation of very long chain fatty acids protein 6 [EC:2.3.1.199]
K10250 ELOVL7; elongation of very long chain fatty acids protein 7 [EC:2.3.1.199]
K10251 HSD17B12; 17beta-estradiol 17-dehydrogenase / very-long-chain 3-oxoacyl-CoA reductase [EC:1.1.1.62 1.1.1.330]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10258 TER; very-long-chain enoyl-CoA reductase [EC:1.3.1.93]
K01068 ACOT1_2_4; acyl-coenzyme A thioesterase 1/2/4 [EC:3.1.2.2]
K01068 ACOT1_2_4; acyl-coenzyme A thioesterase 1/2/4 [EC:3.1.2.2]
K01068 ACOT1_2_4; acyl-coenzyme A thioesterase 1/2/4 [EC:3.1.2.2]
K17360 ACOT7; acyl-coenzyme A thioesterase 7 [EC:3.1.2.2]
K16339 THEM4; acyl-coenzyme A thioesterase THEM4 [EC:3.1.2.2]
K22554 THEM5; acyl-coenzyme A thioesterase THEM5 [EC:3.1.2.2]
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00071 Fatty acid degradation [PATH:hsa00071]
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39 ACAT2; acetyl-CoA acetyltransferase 2
38 ACAT1; acetyl-CoA acetyltransferase 1
30 ACAA1; acetyl-CoA acyltransferase 1
10449 ACAA2; acetyl-CoA acyltransferase 2
3032 HADHB; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
3033 HADH; hydroxyacyl-CoA dehydrogenase
3030 HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
1962 EHHADH; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
1892 ECHS1; enoyl-CoA hydratase, short chain 1
8310 ACOX3; acyl-CoA oxidase 3, pristanoyl
51 ACOX1; acyl-CoA oxidase 1
35 ACADS; acyl-CoA dehydrogenase short chain
34 ACADM; acyl-CoA dehydrogenase medium chain
33 ACADL; acyl-CoA dehydrogenase long chain
36 ACADSB; acyl-CoA dehydrogenase short/branched chain
37 ACADVL; acyl-CoA dehydrogenase very long chain
2639 GCDH; glutaryl-CoA dehydrogenase
23305 ACSL6; acyl-CoA synthetase long chain family member 6
2182 ACSL4; acyl-CoA synthetase long chain family member 4
2180 ACSL1; acyl-CoA synthetase long chain family member 1
51703 ACSL5; acyl-CoA synthetase long chain family member 5
2181 ACSL3; acyl-CoA synthetase long chain family member 3
23205 ACSBG1; acyl-CoA synthetase bubblegum family member 1
81616 ACSBG2; acyl-CoA synthetase bubblegum family member 2
1374 CPT1A; carnitine palmitoyltransferase 1A
1375 CPT1B; carnitine palmitoyltransferase 1B
126129 CPT1C; carnitine palmitoyltransferase 1C
1376 CPT2; carnitine palmitoyltransferase 2
1632 ECI1; enoyl-CoA delta isomerase 1
10455 ECI2; enoyl-CoA delta isomerase 2
113612 CYP2U1; cytochrome P450 family 2 subfamily U member 1
124 ADH1A; alcohol dehydrogenase 1A (class I), alpha polypeptide
125 ADH1B; alcohol dehydrogenase 1B (class I), beta polypeptide
126 ADH1C; alcohol dehydrogenase 1C (class I), gamma polypeptide
131 ADH7; alcohol dehydrogenase 7 (class IV), mu or sigma polypeptide
127 ADH4; alcohol dehydrogenase 4 (class II), pi polypeptide
128 ADH5; alcohol dehydrogenase 5 (class III), chi polypeptide
130 ADH6; alcohol dehydrogenase 6 (class V)
217 ALDH2; aldehyde dehydrogenase 2 family member
224 ALDH3A2; aldehyde dehydrogenase 3 family member A2
219 ALDH1B1; aldehyde dehydrogenase 1 family member B1
501 ALDH7A1; aldehyde dehydrogenase 7 family member A1
223 ALDH9A1; aldehyde dehydrogenase 9 family member A1
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K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00255 ACADL; long-chain-acyl-CoA dehydrogenase [EC:1.3.8.8]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K09479 ACADVL; very long chain acyl-CoA dehydrogenase [EC:1.3.8.9]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K15013 ACSBG; long-chain-fatty-acid--CoA ligase ACSBG [EC:6.2.1.3]
K15013 ACSBG; long-chain-fatty-acid--CoA ligase ACSBG [EC:6.2.1.3]
K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
K08766 CPT2; carnitine O-palmitoyltransferase 2 [EC:2.3.1.21]
K13238 ECI1; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K13239 ECI2; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K07422 CYP2U1; long-chain fatty acid omega-monooxygenase [EC:1.14.14.80]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13980 ADH4; alcohol dehydrogenase 4 [EC:1.1.1.1]
K00121 frmA; S-(hydroxymethyl)glutathione dehydrogenase / alcohol dehydrogenase [EC:1.1.1.284 1.1.1.1]
K13952 ADH6; alcohol dehydrogenase 6 [EC:1.1.1.1]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
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00073 Cutin, suberine and wax biosynthesis
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00100 Steroid biosynthesis [PATH:hsa00100]
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00120 Primary bile acid biosynthesis [PATH:hsa00120]
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00121 Secondary bile acid biosynthesis
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00140 Steroid hormone biosynthesis [PATH:hsa00140]
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00561 Glycerolipid metabolism [PATH:hsa00561]
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00564 Glycerophospholipid metabolism [PATH:hsa00564]
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00565 Ether lipid metabolism [PATH:hsa00565]
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00600 Sphingolipid metabolism [PATH:hsa00600]
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00590 Arachidonic acid metabolism [PATH:hsa00590]
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00591 Linoleic acid metabolism [PATH:hsa00591]
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00592 alpha-Linolenic acid metabolism [PATH:hsa00592]
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01040 Biosynthesis of unsaturated fatty acids [PATH:hsa01040]
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09104 Nucleotide metabolism
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09105 Amino acid metabolism
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00250 Alanine, aspartate and glutamate metabolism [PATH:hsa00250]
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00260 Glycine, serine and threonine metabolism [PATH:hsa00260]
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00270 Cysteine and methionine metabolism [PATH:hsa00270]
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00280 Valine, leucine and isoleucine degradation [PATH:hsa00280]
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587 BCAT2; branched chain amino acid transaminase 2
586 BCAT1; branched chain amino acid transaminase 1
259307 IL4I1; interleukin 4 induced 1
593 BCKDHA; branched chain keto acid dehydrogenase E1 subunit alpha
594 BCKDHB; branched chain keto acid dehydrogenase E1 subunit beta
1629 DBT; dihydrolipoamide branched chain transacylase E2
1738 DLD; dihydrolipoamide dehydrogenase
35 ACADS; acyl-CoA dehydrogenase short chain
34 ACADM; acyl-CoA dehydrogenase medium chain
3712 IVD; isovaleryl-CoA dehydrogenase
36 ACADSB; acyl-CoA dehydrogenase short/branched chain
27034 ACAD8; acyl-CoA dehydrogenase family member 8
3030 HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
1962 EHHADH; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
1892 ECHS1; enoyl-CoA hydratase, short chain 1
3033 HADH; hydroxyacyl-CoA dehydrogenase
3028 HSD17B10; hydroxysteroid 17-beta dehydrogenase 10
30 ACAA1; acetyl-CoA acyltransferase 1
10449 ACAA2; acetyl-CoA acyltransferase 2
3032 HADHB; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
5095 PCCA; propionyl-CoA carboxylase subunit alpha
5096 PCCB; propionyl-CoA carboxylase subunit beta
84693 MCEE; methylmalonyl-CoA epimerase
4594 MMUT; methylmalonyl-CoA mutase
26275 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase
11112 HIBADH; 3-hydroxyisobutyrate dehydrogenase
4329 ALDH6A1; aldehyde dehydrogenase 6 family member A1
217 ALDH2; aldehyde dehydrogenase 2 family member
224 ALDH3A2; aldehyde dehydrogenase 3 family member A2
219 ALDH1B1; aldehyde dehydrogenase 1 family member B1
501 ALDH7A1; aldehyde dehydrogenase 7 family member A1
223 ALDH9A1; aldehyde dehydrogenase 9 family member A1
316 AOX1; aldehyde oxidase 1
197322 ACSF3; acyl-CoA synthetase family member 3
18 ABAT; 4-aminobutyrate aminotransferase
64902 AGXT2; alanine--glyoxylate aminotransferase 2
56922 MCCC1; methylcrotonyl-CoA carboxylase subunit 1
64087 MCCC2; methylcrotonyl-CoA carboxylase subunit 2
549 AUH; AU RNA binding methylglutaconyl-CoA hydratase
3155 HMGCL; 3-hydroxy-3-methylglutaryl-CoA lyase
54511 HMGCLL1; 3-hydroxy-3-methylglutaryl-CoA lyase like 1
5019 OXCT1; 3-oxoacid CoA-transferase 1
64064 OXCT2; 3-oxoacid CoA-transferase 2
65985 AACS; acetoacetyl-CoA synthetase
39 ACAT2; acetyl-CoA acetyltransferase 2
38 ACAT1; acetyl-CoA acetyltransferase 1
3157 HMGCS1; 3-hydroxy-3-methylglutaryl-CoA synthase 1
3158 HMGCS2; 3-hydroxy-3-methylglutaryl-CoA synthase 2
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K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2]
K00166 BCKDHA; 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00253 IVD; isovaleryl-CoA dehydrogenase [EC:1.3.8.4]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K11538 ACAD8; isobutyryl-CoA dehydrogenase [EC:1.3.99.-]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K01965 PCCA; propionyl-CoA carboxylase alpha chain [EC:6.4.1.3]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K05606 MCEE; methylmalonyl-CoA/ethylmalonyl-CoA epimerase [EC:5.1.99.1]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K00020 HIBADH; 3-hydroxyisobutyrate dehydrogenase [EC:1.1.1.31]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K18660 ACSF3; malonyl-CoA/methylmalonyl-CoA synthetase [EC:6.2.1.76 6.2.1.-]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00827 AGXT2; alanine-glyoxylate transaminase / (R)-3-amino-2-methylpropionate-pyruvate transaminase [EC:2.6.1.44 2.6.1.40]
K01968 MCCC1; 3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
K01969 MCCC2; 3-methylcrotonyl-CoA carboxylase beta subunit [EC:6.4.1.4]
K05607 AUH; methylglutaconyl-CoA hydratase [EC:4.2.1.18]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01907 AACS; acetoacetyl-CoA synthetase [EC:6.2.1.16]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
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00290 Valine, leucine and isoleucine biosynthesis [PATH:hsa00290]
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00300 Lysine biosynthesis
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00310 Lysine degradation [PATH:hsa00310]
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00220 Arginine biosynthesis [PATH:hsa00220]
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00330 Arginine and proline metabolism [PATH:hsa00330]
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00340 Histidine metabolism [PATH:hsa00340]
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00350 Tyrosine metabolism [PATH:hsa00350]
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00360 Phenylalanine metabolism [PATH:hsa00360]
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00380 Tryptophan metabolism [PATH:hsa00380]
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00400 Phenylalanine, tyrosine and tryptophan biosynthesis [PATH:hsa00400]
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09106 Metabolism of other amino acids
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09107 Glycan biosynthesis and metabolism
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09108 Metabolism of cofactors and vitamins
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09109 Metabolism of terpenoids and polyketides
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09110 Biosynthesis of other secondary metabolites
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09111 Xenobiotics biodegradation and metabolism
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09112 Not included in regular maps
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09120 Genetic Information Processing
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09130 Environmental Information Processing
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09140 Cellular Processes
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09150 Organismal Systems
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09160 Human Diseases
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09180 Brite Hierarchies
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09190 Not Included in Pathway or Brite
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