KEGG Orthology (KO) - Homo sapiens (human)

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     KO
 09100 Metabolism
 
   09101 Carbohydrate metabolism
 
   09102 Energy metabolism
 
   09103 Lipid metabolism
     00061 Fatty acid biosynthesis [PATH:hsa00061]
     00062 Fatty acid elongation [PATH:hsa00062]
       10449 ACAA2; acetyl-CoA acyltransferase 2
       3032 HADHB; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
       3033 HADH; hydroxyacyl-CoA dehydrogenase
       3030 HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
       1892 ECHS1; enoyl-CoA hydratase, short chain 1
       51102 MECR; mitochondrial trans-2-enoyl-CoA reductase
       5538 PPT1; palmitoyl-protein thioesterase 1
       9374 PPT2; palmitoyl-protein thioesterase 2
       64834 ELOVL1; ELOVL fatty acid elongase 1
       54898 ELOVL2; ELOVL fatty acid elongase 2
       83401 ELOVL3; ELOVL fatty acid elongase 3
       6785 ELOVL4; ELOVL fatty acid elongase 4
       60481 ELOVL5; ELOVL fatty acid elongase 5
       79071 ELOVL6; ELOVL fatty acid elongase 6
       79993 ELOVL7; ELOVL fatty acid elongase 7
       51144 HSD17B12; hydroxysteroid 17-beta dehydrogenase 12
       201562 HACD2; 3-hydroxyacyl-CoA dehydratase 2
       9200 HACD1; 3-hydroxyacyl-CoA dehydratase 1
       401494 HACD4; 3-hydroxyacyl-CoA dehydratase 4
       51495 HACD3; 3-hydroxyacyl-CoA dehydratase 3
       9524 TECR; trans-2,3-enoyl-CoA reductase
       122970 ACOT4; acyl-CoA thioesterase 4
       10965 ACOT2; acyl-CoA thioesterase 2
       641371 ACOT1; acyl-CoA thioesterase 1
       11332 ACOT7; acyl-CoA thioesterase 7
       117145 THEM4; thioesterase superfamily member 4
       284486 THEM5; thioesterase superfamily member 5
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K07512 MECR; mitochondrial enoyl-[acyl-carrier protein] reductase / trans-2-enoyl-CoA reductase [EC:1.3.1.- 1.3.1.38]
K01074 PPT; palmitoyl-protein thioesterase [EC:3.1.2.22]
K01074 PPT; palmitoyl-protein thioesterase [EC:3.1.2.22]
K10247 ELOVL1; elongation of very long chain fatty acids protein 1 [EC:2.3.1.199]
K10205 ELOVL2; elongation of very long chain fatty acids protein 2 [EC:2.3.1.199]
K10248 ELOVL3; elongation of very long chain fatty acids protein 3 [EC:2.3.1.199]
K10249 ELOVL4; elongation of very long chain fatty acids protein 4 [EC:2.3.1.199]
K10244 ELOVL5; elongation of very long chain fatty acids protein 5 [EC:2.3.1.199]
K10203 ELOVL6; elongation of very long chain fatty acids protein 6 [EC:2.3.1.199]
K10250 ELOVL7; elongation of very long chain fatty acids protein 7 [EC:2.3.1.199]
K10251 HSD17B12; 17beta-estradiol 17-dehydrogenase / very-long-chain 3-oxoacyl-CoA reductase [EC:1.1.1.62 1.1.1.330]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10258 TER; very-long-chain enoyl-CoA reductase [EC:1.3.1.93]
K01068 ACOT1_2_4; acyl-coenzyme A thioesterase 1/2/4 [EC:3.1.2.2]
K01068 ACOT1_2_4; acyl-coenzyme A thioesterase 1/2/4 [EC:3.1.2.2]
K01068 ACOT1_2_4; acyl-coenzyme A thioesterase 1/2/4 [EC:3.1.2.2]
K17360 ACOT7; acyl-coenzyme A thioesterase 7 [EC:3.1.2.2]
K16339 THEM4; acyl-coenzyme A thioesterase THEM4 [EC:3.1.2.2]
K22554 THEM5; acyl-coenzyme A thioesterase THEM5 [EC:3.1.2.2]
     00071 Fatty acid degradation [PATH:hsa00071]
       39 ACAT2; acetyl-CoA acetyltransferase 2
       38 ACAT1; acetyl-CoA acetyltransferase 1
       30 ACAA1; acetyl-CoA acyltransferase 1
       10449 ACAA2; acetyl-CoA acyltransferase 2
       3032 HADHB; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
       3033 HADH; hydroxyacyl-CoA dehydrogenase
       3030 HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
       1962 EHHADH; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
       1892 ECHS1; enoyl-CoA hydratase, short chain 1
       8310 ACOX3; acyl-CoA oxidase 3, pristanoyl
       51 ACOX1; acyl-CoA oxidase 1
       35 ACADS; acyl-CoA dehydrogenase short chain
       34 ACADM; acyl-CoA dehydrogenase medium chain
       33 ACADL; acyl-CoA dehydrogenase long chain
       36 ACADSB; acyl-CoA dehydrogenase short/branched chain
       37 ACADVL; acyl-CoA dehydrogenase very long chain
       2639 GCDH; glutaryl-CoA dehydrogenase
       23305 ACSL6; acyl-CoA synthetase long chain family member 6
       2182 ACSL4; acyl-CoA synthetase long chain family member 4
       2180 ACSL1; acyl-CoA synthetase long chain family member 1
       51703 ACSL5; acyl-CoA synthetase long chain family member 5
       2181 ACSL3; acyl-CoA synthetase long chain family member 3
       23205 ACSBG1; acyl-CoA synthetase bubblegum family member 1
       81616 ACSBG2; acyl-CoA synthetase bubblegum family member 2
       1374 CPT1A; carnitine palmitoyltransferase 1A
       1375 CPT1B; carnitine palmitoyltransferase 1B
       126129 CPT1C; carnitine palmitoyltransferase 1C
       1376 CPT2; carnitine palmitoyltransferase 2
       1632 ECI1; enoyl-CoA delta isomerase 1
       10455 ECI2; enoyl-CoA delta isomerase 2
       113612 CYP2U1; cytochrome P450 family 2 subfamily U member 1
       124 ADH1A; alcohol dehydrogenase 1A (class I), alpha polypeptide
       125 ADH1B; alcohol dehydrogenase 1B (class I), beta polypeptide
       126 ADH1C; alcohol dehydrogenase 1C (class I), gamma polypeptide
       131 ADH7; alcohol dehydrogenase 7 (class IV), mu or sigma polypeptide
       127 ADH4; alcohol dehydrogenase 4 (class II), pi polypeptide
       128 ADH5; alcohol dehydrogenase 5 (class III), chi polypeptide
       130 ADH6; alcohol dehydrogenase 6 (class V)
       217 ALDH2; aldehyde dehydrogenase 2 family member
       224 ALDH3A2; aldehyde dehydrogenase 3 family member A2
       219 ALDH1B1; aldehyde dehydrogenase 1 family member B1
       501 ALDH7A1; aldehyde dehydrogenase 7 family member A1
       223 ALDH9A1; aldehyde dehydrogenase 9 family member A1
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00255 ACADL; long-chain-acyl-CoA dehydrogenase [EC:1.3.8.8]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K09479 ACADVL; very long chain acyl-CoA dehydrogenase [EC:1.3.8.9]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K15013 ACSBG; long-chain-fatty-acid--CoA ligase ACSBG [EC:6.2.1.3]
K15013 ACSBG; long-chain-fatty-acid--CoA ligase ACSBG [EC:6.2.1.3]
K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
K08766 CPT2; carnitine O-palmitoyltransferase 2 [EC:2.3.1.21]
K13238 ECI1; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K13239 ECI2; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K07422 CYP2U1; long-chain fatty acid omega-monooxygenase [EC:1.14.14.80]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13980 ADH4; alcohol dehydrogenase 4 [EC:1.1.1.1]
K00121 frmA; S-(hydroxymethyl)glutathione dehydrogenase / alcohol dehydrogenase [EC:1.1.1.284 1.1.1.1]
K13952 ADH6; alcohol dehydrogenase 6 [EC:1.1.1.1]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
     00073 Cutin, suberine and wax biosynthesis
     00100 Steroid biosynthesis [PATH:hsa00100]
     00120 Primary bile acid biosynthesis [PATH:hsa00120]
     00121 Secondary bile acid biosynthesis
     00140 Steroid hormone biosynthesis [PATH:hsa00140]
     00561 Glycerolipid metabolism [PATH:hsa00561]
     00564 Glycerophospholipid metabolism [PATH:hsa00564]
     00565 Ether lipid metabolism [PATH:hsa00565]
     00600 Sphingolipid metabolism [PATH:hsa00600]
     00590 Arachidonic acid metabolism [PATH:hsa00590]
     00591 Linoleic acid metabolism [PATH:hsa00591]
     00592 alpha-Linolenic acid metabolism [PATH:hsa00592]
     01040 Biosynthesis of unsaturated fatty acids [PATH:hsa01040]
 
   09104 Nucleotide metabolism
 
   09105 Amino acid metabolism
     00250 Alanine, aspartate and glutamate metabolism [PATH:hsa00250]
     00260 Glycine, serine and threonine metabolism [PATH:hsa00260]
     00270 Cysteine and methionine metabolism [PATH:hsa00270]
     00280 Valine, leucine and isoleucine degradation [PATH:hsa00280]
       587 BCAT2; branched chain amino acid transaminase 2
       586 BCAT1; branched chain amino acid transaminase 1
       259307 IL4I1; interleukin 4 induced 1
       593 BCKDHA; branched chain keto acid dehydrogenase E1 subunit alpha
       594 BCKDHB; branched chain keto acid dehydrogenase E1 subunit beta
       1629 DBT; dihydrolipoamide branched chain transacylase E2
       1738 DLD; dihydrolipoamide dehydrogenase
       35 ACADS; acyl-CoA dehydrogenase short chain
       34 ACADM; acyl-CoA dehydrogenase medium chain
       3712 IVD; isovaleryl-CoA dehydrogenase
       36 ACADSB; acyl-CoA dehydrogenase short/branched chain
       27034 ACAD8; acyl-CoA dehydrogenase family member 8
       3030 HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
       1962 EHHADH; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
       1892 ECHS1; enoyl-CoA hydratase, short chain 1
       3033 HADH; hydroxyacyl-CoA dehydrogenase
       3028 HSD17B10; hydroxysteroid 17-beta dehydrogenase 10
       30 ACAA1; acetyl-CoA acyltransferase 1
       10449 ACAA2; acetyl-CoA acyltransferase 2
       3032 HADHB; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
       5095 PCCA; propionyl-CoA carboxylase subunit alpha
       5096 PCCB; propionyl-CoA carboxylase subunit beta
       84693 MCEE; methylmalonyl-CoA epimerase
       4594 MMUT; methylmalonyl-CoA mutase
       26275 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase
       11112 HIBADH; 3-hydroxyisobutyrate dehydrogenase
       4329 ALDH6A1; aldehyde dehydrogenase 6 family member A1
       217 ALDH2; aldehyde dehydrogenase 2 family member
       224 ALDH3A2; aldehyde dehydrogenase 3 family member A2
       219 ALDH1B1; aldehyde dehydrogenase 1 family member B1
       501 ALDH7A1; aldehyde dehydrogenase 7 family member A1
       223 ALDH9A1; aldehyde dehydrogenase 9 family member A1
       316 AOX1; aldehyde oxidase 1
       197322 ACSF3; acyl-CoA synthetase family member 3
       18 ABAT; 4-aminobutyrate aminotransferase
       64902 AGXT2; alanine--glyoxylate aminotransferase 2
       56922 MCCC1; methylcrotonyl-CoA carboxylase subunit 1
       64087 MCCC2; methylcrotonyl-CoA carboxylase subunit 2
       549 AUH; AU RNA binding methylglutaconyl-CoA hydratase
       3155 HMGCL; 3-hydroxy-3-methylglutaryl-CoA lyase
       54511 HMGCLL1; 3-hydroxy-3-methylglutaryl-CoA lyase like 1
       5019 OXCT1; 3-oxoacid CoA-transferase 1
       64064 OXCT2; 3-oxoacid CoA-transferase 2
       65985 AACS; acetoacetyl-CoA synthetase
       39 ACAT2; acetyl-CoA acetyltransferase 2
       38 ACAT1; acetyl-CoA acetyltransferase 1
       3157 HMGCS1; 3-hydroxy-3-methylglutaryl-CoA synthase 1
       3158 HMGCS2; 3-hydroxy-3-methylglutaryl-CoA synthase 2
K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2]
K00166 BCKDHA; 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00253 IVD; isovaleryl-CoA dehydrogenase [EC:1.3.8.4]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K11538 ACAD8; isobutyryl-CoA dehydrogenase [EC:1.3.99.-]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K01965 PCCA; propionyl-CoA carboxylase alpha chain [EC:6.4.1.3]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K05606 MCEE; methylmalonyl-CoA/ethylmalonyl-CoA epimerase [EC:5.1.99.1]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K00020 HIBADH; 3-hydroxyisobutyrate dehydrogenase [EC:1.1.1.31]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K18660 ACSF3; malonyl-CoA/methylmalonyl-CoA synthetase [EC:6.2.1.76 6.2.1.-]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00827 AGXT2; alanine-glyoxylate transaminase / (R)-3-amino-2-methylpropionate-pyruvate transaminase [EC:2.6.1.44 2.6.1.40]
K01968 MCCC1; 3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
K01969 MCCC2; 3-methylcrotonyl-CoA carboxylase beta subunit [EC:6.4.1.4]
K05607 AUH; methylglutaconyl-CoA hydratase [EC:4.2.1.18]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01907 AACS; acetoacetyl-CoA synthetase [EC:6.2.1.16]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
     00290 Valine, leucine and isoleucine biosynthesis [PATH:hsa00290]
     00300 Lysine biosynthesis
     00310 Lysine degradation [PATH:hsa00310]
     00220 Arginine biosynthesis [PATH:hsa00220]
     00330 Arginine and proline metabolism [PATH:hsa00330]
     00340 Histidine metabolism [PATH:hsa00340]
     00350 Tyrosine metabolism [PATH:hsa00350]
     00360 Phenylalanine metabolism [PATH:hsa00360]
     00380 Tryptophan metabolism [PATH:hsa00380]
     00400 Phenylalanine, tyrosine and tryptophan biosynthesis [PATH:hsa00400]
 
   09106 Metabolism of other amino acids
 
   09107 Glycan biosynthesis and metabolism
 
   09108 Metabolism of cofactors and vitamins
 
   09109 Metabolism of terpenoids and polyketides
 
   09110 Biosynthesis of other secondary metabolites
 
   09111 Xenobiotics biodegradation and metabolism
 
   09112 Not included in regular maps
 
 09120 Genetic Information Processing
 
 09130 Environmental Information Processing
 
 09140 Cellular Processes
 
 09150 Organismal Systems
 
 09160 Human Diseases
 
 09180 Brite Hierarchies
 
 09190 Not Included in Pathway or Brite

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Last updated: April 17, 2024