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KO |
09100 Metabolism
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09101 Carbohydrate metabolism
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00010 Glycolysis / Gluconeogenesis [PATH:hsa00010]
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00020 Citrate cycle (TCA cycle) [PATH:hsa00020]
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1431 CS; citrate synthase
47 ACLY; ATP citrate lyase
50 ACO2; aconitase 2
48 ACO1; aconitase 1
3417 IDH1; isocitrate dehydrogenase (NADP(+)) 1
3418 IDH2; isocitrate dehydrogenase (NADP(+)) 2
3420 IDH3B; isocitrate dehydrogenase (NAD(+)) 3 non-catalytic subunit beta
3421 IDH3G; isocitrate dehydrogenase (NAD(+)) 3 non-catalytic subunit gamma
3419 IDH3A; isocitrate dehydrogenase (NAD(+)) 3 catalytic subunit alpha
55753 OGDHL; oxoglutarate dehydrogenase L
4967 OGDH; oxoglutarate dehydrogenase
1743 DLST; dihydrolipoamide S-succinyltransferase
1738 DLD; dihydrolipoamide dehydrogenase
8802 SUCLG1; succinate-CoA ligase GDP/ADP-forming subunit alpha
8801 SUCLG2; succinate-CoA ligase GDP-forming subunit beta
8803 SUCLA2; succinate-CoA ligase ADP-forming subunit beta
6389 SDHA; succinate dehydrogenase complex flavoprotein subunit A
6390 SDHB; succinate dehydrogenase complex iron sulfur subunit B
6391 SDHC; succinate dehydrogenase complex subunit C
6392 SDHD; succinate dehydrogenase complex subunit D
2271 FH; fumarate hydratase
4190 MDH1; malate dehydrogenase 1
4191 MDH2; malate dehydrogenase 2
5091 PC; pyruvate carboxylase
5105 PCK1; phosphoenolpyruvate carboxykinase 1
5106 PCK2; phosphoenolpyruvate carboxykinase 2, mitochondrial
5161 PDHA2; pyruvate dehydrogenase E1 subunit alpha 2
5160 PDHA1; pyruvate dehydrogenase E1 subunit alpha 1
5162 PDHB; pyruvate dehydrogenase E1 subunit beta
1737 DLAT; dihydrolipoamide S-acetyltransferase
8050 PDHX; pyruvate dehydrogenase complex component X
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K01647 CS; citrate synthase [EC:2.3.3.1]
K01648 ACLY; ATP citrate (pro-S)-lyase [EC:2.3.3.8]
K01681 ACO; aconitate hydratase [EC:4.2.1.3]
K01681 ACO; aconitate hydratase [EC:4.2.1.3]
K00031 IDH1; isocitrate dehydrogenase [EC:1.1.1.42]
K00031 IDH1; isocitrate dehydrogenase [EC:1.1.1.42]
K00030 IDH3; isocitrate dehydrogenase (NAD+) [EC:1.1.1.41]
K00030 IDH3; isocitrate dehydrogenase (NAD+) [EC:1.1.1.41]
K00030 IDH3; isocitrate dehydrogenase (NAD+) [EC:1.1.1.41]
K00164 OGDH; 2-oxoglutarate dehydrogenase E1 component [EC:1.2.4.2]
K00164 OGDH; 2-oxoglutarate dehydrogenase E1 component [EC:1.2.4.2]
K00658 DLST; 2-oxoglutarate dehydrogenase E2 component (dihydrolipoamide succinyltransferase) [EC:2.3.1.61]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K01899 LSC1; succinyl-CoA synthetase alpha subunit [EC:6.2.1.4 6.2.1.5]
K01900 LSC2; succinyl-CoA synthetase beta subunit [EC:6.2.1.4 6.2.1.5]
K01900 LSC2; succinyl-CoA synthetase beta subunit [EC:6.2.1.4 6.2.1.5]
K00234 SDHA; succinate dehydrogenase (ubiquinone) flavoprotein subunit [EC:1.3.5.1]
K00235 SDHB; succinate dehydrogenase (ubiquinone) iron-sulfur subunit [EC:1.3.5.1]
K00236 SDHC; succinate dehydrogenase (ubiquinone) cytochrome b560 subunit
K00237 SDHD; succinate dehydrogenase (ubiquinone) membrane anchor subunit
K01679 E4.2.1.2B; fumarate hydratase, class II [EC:4.2.1.2]
K00025 MDH1; malate dehydrogenase [EC:1.1.1.37]
K00026 MDH2; malate dehydrogenase [EC:1.1.1.37]
K01958 PC; pyruvate carboxylase [EC:6.4.1.1]
K01596 E4.1.1.32; phosphoenolpyruvate carboxykinase (GTP) [EC:4.1.1.32]
K01596 E4.1.1.32; phosphoenolpyruvate carboxykinase (GTP) [EC:4.1.1.32]
K00161 PDHA; pyruvate dehydrogenase E1 component subunit alpha [EC:1.2.4.1]
K00161 PDHA; pyruvate dehydrogenase E1 component subunit alpha [EC:1.2.4.1]
K00162 PDHB; pyruvate dehydrogenase E1 component subunit beta [EC:1.2.4.1]
K00627 DLAT; pyruvate dehydrogenase E2 component (dihydrolipoyllysine-residue acetyltransferase) [EC:2.3.1.12]
K13997 PDHX; dihydrolipoamide dehydrogenase-binding protein of pyruvate dehydrogenase complex
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00030 Pentose phosphate pathway [PATH:hsa00030]
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00040 Pentose and glucuronate interconversions [PATH:hsa00040]
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00051 Fructose and mannose metabolism [PATH:hsa00051]
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00052 Galactose metabolism [PATH:hsa00052]
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00053 Ascorbate and aldarate metabolism [PATH:hsa00053]
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00500 Starch and sucrose metabolism [PATH:hsa00500]
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00520 Amino sugar and nucleotide sugar metabolism [PATH:hsa00520]
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00620 Pyruvate metabolism [PATH:hsa00620]
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84532 ACSS1; acyl-CoA synthetase short chain family member 1
55902 ACSS2; acyl-CoA synthetase short chain family member 2
5161 PDHA2; pyruvate dehydrogenase E1 subunit alpha 2
5160 PDHA1; pyruvate dehydrogenase E1 subunit alpha 1
5162 PDHB; pyruvate dehydrogenase E1 subunit beta
1737 DLAT; dihydrolipoamide S-acetyltransferase
1738 DLD; dihydrolipoamide dehydrogenase
8050 PDHX; pyruvate dehydrogenase complex component X
124 ADH1A; alcohol dehydrogenase 1A (class I), alpha polypeptide
125 ADH1B; alcohol dehydrogenase 1B (class I), beta polypeptide
126 ADH1C; alcohol dehydrogenase 1C (class I), gamma polypeptide
131 ADH7; alcohol dehydrogenase 7 (class IV), mu or sigma polypeptide
127 ADH4; alcohol dehydrogenase 4 (class II), pi polypeptide
130 ADH6; alcohol dehydrogenase 6 (class V)
128 ADH5; alcohol dehydrogenase 5 (class III), chi polypeptide
10327 AKR1A1; aldo-keto reductase family 1 member A1
5315 PKM; pyruvate kinase M1/2
5313 PKLR; pyruvate kinase L/R
31 ACACA; acetyl-CoA carboxylase alpha
32 ACACB; acetyl-CoA carboxylase beta
98 ACYP2; acylphosphatase 2
97 ACYP1; acylphosphatase 1
217 ALDH2; aldehyde dehydrogenase 2 family member
224 ALDH3A2; aldehyde dehydrogenase 3 family member A2
219 ALDH1B1; aldehyde dehydrogenase 1 family member B1
501 ALDH7A1; aldehyde dehydrogenase 7 family member A1
223 ALDH9A1; aldehyde dehydrogenase 9 family member A1
134526 ACOT12; acyl-CoA thioesterase 12
160287 LDHAL6A; lactate dehydrogenase A like 6A
92483 LDHAL6B; lactate dehydrogenase A like 6B
3939 LDHA; lactate dehydrogenase A
3945 LDHB; lactate dehydrogenase B
3948 LDHC; lactate dehydrogenase C
197257 LDHD; lactate dehydrogenase D
2739 GLO1; glyoxalase I
3029 HAGH; hydroxyacylglutathione hydrolase
9380 GRHPR; glyoxylate and hydroxypyruvate reductase
4200 ME2; malic enzyme 2
10873 ME3; malic enzyme 3
4199 ME1; malic enzyme 1
5091 PC; pyruvate carboxylase
4190 MDH1; malate dehydrogenase 1
4191 MDH2; malate dehydrogenase 2
2271 FH; fumarate hydratase
5105 PCK1; phosphoenolpyruvate carboxykinase 1
5106 PCK2; phosphoenolpyruvate carboxykinase 2, mitochondrial
39 ACAT2; acetyl-CoA acetyltransferase 2
38 ACAT1; acetyl-CoA acetyltransferase 1
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K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K00161 PDHA; pyruvate dehydrogenase E1 component subunit alpha [EC:1.2.4.1]
K00161 PDHA; pyruvate dehydrogenase E1 component subunit alpha [EC:1.2.4.1]
K00162 PDHB; pyruvate dehydrogenase E1 component subunit beta [EC:1.2.4.1]
K00627 DLAT; pyruvate dehydrogenase E2 component (dihydrolipoyllysine-residue acetyltransferase) [EC:2.3.1.12]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K13997 PDHX; dihydrolipoamide dehydrogenase-binding protein of pyruvate dehydrogenase complex
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13980 ADH4; alcohol dehydrogenase 4 [EC:1.1.1.1]
K13952 ADH6; alcohol dehydrogenase 6 [EC:1.1.1.1]
K00121 frmA; S-(hydroxymethyl)glutathione dehydrogenase / alcohol dehydrogenase [EC:1.1.1.284 1.1.1.1]
K00002 AKR1A1; alcohol dehydrogenase (NADP+) [EC:1.1.1.2]
K00873 PK; pyruvate kinase [EC:2.7.1.40]
K12406 PKLR; pyruvate kinase isozymes R/L [EC:2.7.1.40]
K11262 ACACA; acetyl-CoA carboxylase / biotin carboxylase 1 [EC:6.4.1.2 6.3.4.14 2.1.3.15]
K01946 ACACB; acetyl-CoA carboxylase / biotin carboxylase 2 [EC:6.4.1.2 6.3.4.14 2.1.3.15]
K01512 acyP; acylphosphatase [EC:3.6.1.7]
K01512 acyP; acylphosphatase [EC:3.6.1.7]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K01067 E3.1.2.1; acetyl-CoA hydrolase [EC:3.1.2.1]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00102 LDHD; D-lactate dehydrogenase (cytochrome) [EC:1.1.2.4]
K01759 GLO1; lactoylglutathione lyase [EC:4.4.1.5]
K01069 gloB; hydroxyacylglutathione hydrolase [EC:3.1.2.6]
K00049 GRHPR; glyoxylate/hydroxypyruvate reductase [EC:1.1.1.79 1.1.1.81]
K00027 ME2; malate dehydrogenase (oxaloacetate-decarboxylating) [EC:1.1.1.38]
K00029 maeB; malate dehydrogenase (oxaloacetate-decarboxylating)(NADP+) [EC:1.1.1.40]
K00029 maeB; malate dehydrogenase (oxaloacetate-decarboxylating)(NADP+) [EC:1.1.1.40]
K01958 PC; pyruvate carboxylase [EC:6.4.1.1]
K00025 MDH1; malate dehydrogenase [EC:1.1.1.37]
K00026 MDH2; malate dehydrogenase [EC:1.1.1.37]
K01679 E4.2.1.2B; fumarate hydratase, class II [EC:4.2.1.2]
K01596 E4.1.1.32; phosphoenolpyruvate carboxykinase (GTP) [EC:4.1.1.32]
K01596 E4.1.1.32; phosphoenolpyruvate carboxykinase (GTP) [EC:4.1.1.32]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
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00630 Glyoxylate and dicarboxylate metabolism [PATH:hsa00630]
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84532 ACSS1; acyl-CoA synthetase short chain family member 1
55902 ACSS2; acyl-CoA synthetase short chain family member 2
4190 MDH1; malate dehydrogenase 1
4191 MDH2; malate dehydrogenase 2
1431 CS; citrate synthase
50 ACO2; aconitase 2
48 ACO1; aconitase 1
39 ACAT2; acetyl-CoA acetyltransferase 2
38 ACAT1; acetyl-CoA acetyltransferase 1
84693 MCEE; methylmalonyl-CoA epimerase
5095 PCCA; propionyl-CoA carboxylase subunit alpha
5096 PCCB; propionyl-CoA carboxylase subunit beta
4594 MMUT; methylmalonyl-CoA mutase
51179 HAO2; hydroxyacid oxidase 2
54363 HAO1; hydroxyacid oxidase 1
847 CAT; catalase
9380 GRHPR; glyoxylate and hydroxypyruvate reductase
283871 PGP; phosphoglycolate phosphatase
189 AGXT; alanine--glyoxylate aminotransferase
2752 GLUL; glutamate-ammonia ligase
6472 SHMT2; serine hydroxymethyltransferase 2
6470 SHMT1; serine hydroxymethyltransferase 1
2731 GLDC; glycine decarboxylase
275 AMT; aminomethyltransferase
1738 DLD; dihydrolipoamide dehydrogenase
2653 GCSH; glycine cleavage system protein H
81888 HYI; hydroxypyruvate isomerase (putative)
132158 GLYCTK; glycerate kinase
112817 HOGA1; 4-hydroxy-2-oxoglutarate aldolase 1
125061 AFMID; arylformamidase
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K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K00025 MDH1; malate dehydrogenase [EC:1.1.1.37]
K00026 MDH2; malate dehydrogenase [EC:1.1.1.37]
K01647 CS; citrate synthase [EC:2.3.3.1]
K01681 ACO; aconitate hydratase [EC:4.2.1.3]
K01681 ACO; aconitate hydratase [EC:4.2.1.3]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K05606 MCEE; methylmalonyl-CoA/ethylmalonyl-CoA epimerase [EC:5.1.99.1]
K01965 PCCA; propionyl-CoA carboxylase alpha chain [EC:6.4.1.3]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K11517 HAO; (S)-2-hydroxy-acid oxidase [EC:1.1.3.15]
K11517 HAO; (S)-2-hydroxy-acid oxidase [EC:1.1.3.15]
K03781 katE; catalase [EC:1.11.1.6]
K00049 GRHPR; glyoxylate/hydroxypyruvate reductase [EC:1.1.1.79 1.1.1.81]
K19269 PGP; phosphoglycolate phosphatase [EC:3.1.3.18 3.1.3.48]
K00830 AGXT; alanine-glyoxylate transaminase / serine-glyoxylate transaminase / serine-pyruvate transaminase [EC:2.6.1.44 2.6.1.45 2.6.1.51]
K01915 glnA; glutamine synthetase [EC:6.3.1.2]
K00600 glyA; glycine hydroxymethyltransferase [EC:2.1.2.1]
K00600 glyA; glycine hydroxymethyltransferase [EC:2.1.2.1]
K00281 GLDC; glycine cleavage system P protein (glycine dehydrogenase) [EC:1.4.4.2]
K00605 gcvT; glycine cleavage system T protein (aminomethyltransferase) [EC:2.1.2.10]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K02437 gcvH; glycine cleavage system H protein
K01816 hyi; hydroxypyruvate isomerase [EC:5.3.1.22]
K11529 gck; glycerate 2-kinase [EC:2.7.1.165]
K18123 HOGA1; 4-hydroxy-2-oxoglutarate aldolase [EC:4.1.3.16]
K01432 AFMID; arylformamidase [EC:3.5.1.9]
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00640 Propanoate metabolism [PATH:hsa00640]
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00650 Butanoate metabolism [PATH:hsa00650]
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00660 C5-Branched dibasic acid metabolism
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00562 Inositol phosphate metabolism [PATH:hsa00562]
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09102 Energy metabolism
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09103 Lipid metabolism
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09104 Nucleotide metabolism
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09105 Amino acid metabolism
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00250 Alanine, aspartate and glutamate metabolism [PATH:hsa00250]
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00260 Glycine, serine and threonine metabolism [PATH:hsa00260]
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00270 Cysteine and methionine metabolism [PATH:hsa00270]
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1491 CTH; cystathionine gamma-lyase
56267 KYAT3; kynurenine aminotransferase 3
883 KYAT1; kynurenine aminotransferase 1
875 CBS; cystathionine beta-synthase
102724560 CBS; cystathionine beta-synthase like
635 BHMT; betaine--homocysteine S-methyltransferase
23743 BHMT2; betaine--homocysteine S-methyltransferase 2
4548 MTR; 5-methyltetrahydrofolate-homocysteine methyltransferase
27430 MAT2B; methionine adenosyltransferase 2 non-catalytic beta subunit
4143 MAT1A; methionine adenosyltransferase 1A
4144 MAT2A; methionine adenosyltransferase 2A
262 AMD1; adenosylmethionine decarboxylase 1
6723 SRM; spermidine synthase
6611 SMS; spermine synthase
4507 MTAP; methylthioadenosine phosphorylase
144811 LACC1; laccase domain containing 1
84245 MRI1; methylthioribose-1-phosphate isomerase 1
51074 APIP; APAF1 interacting protein
58478 ENOPH1; enolase-phosphatase 1
55256 ADI1; acireductone dioxygenase 1
6898 TAT; tyrosine aminotransferase
259307 IL4I1; interleukin 4 induced 1
27232 GNMT; glycine N-methyltransferase
1786 DNMT1; DNA methyltransferase 1
1788 DNMT3A; DNA methyltransferase 3 alpha
1789 DNMT3B; DNA methyltransferase 3 beta
23382 AHCYL2; adenosylhomocysteinase like 2
10768 AHCYL1; adenosylhomocysteinase like 1
191 AHCY; adenosylhomocysteinase
587 BCAT2; branched chain amino acid transaminase 2
586 BCAT1; branched chain amino acid transaminase 1
64902 AGXT2; alanine--glyoxylate aminotransferase 2
2729 GCLC; glutamate-cysteine ligase catalytic subunit
2730 GCLM; glutamate-cysteine ligase modifier subunit
2937 GSS; glutathione synthetase
1036 CDO1; cysteine dioxygenase type 1
2805 GOT1; glutamic-oxaloacetic transaminase 1
137362 GOT1L1; glutamic-oxaloacetic transaminase 1 like 1
2806 GOT2; glutamic-oxaloacetic transaminase 2
4357 MPST; mercaptopyruvate sulfurtransferase
7263 TST; thiosulfate sulfurtransferase
160287 LDHAL6A; lactate dehydrogenase A like 6A
92483 LDHAL6B; lactate dehydrogenase A like 6B
3939 LDHA; lactate dehydrogenase A
3945 LDHB; lactate dehydrogenase B
3948 LDHC; lactate dehydrogenase C
4190 MDH1; malate dehydrogenase 1
4191 MDH2; malate dehydrogenase 2
10993 SDS; serine dehydratase
113675 SDSL; serine dehydratase like
26227 PHGDH; phosphoglycerate dehydrogenase
29968 PSAT1; phosphoserine aminotransferase 1
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K01758 CTH; cystathionine gamma-lyase [EC:4.4.1.1]
K00816 CCBL; kynurenine---oxoglutarate transaminase / cysteine-S-conjugate beta-lyase / glutamine---phenylpyruvate transaminase [EC:2.6.1.7 4.4.1.13 2.6.1.64]
K00816 CCBL; kynurenine---oxoglutarate transaminase / cysteine-S-conjugate beta-lyase / glutamine---phenylpyruvate transaminase [EC:2.6.1.7 4.4.1.13 2.6.1.64]
K01697 CBS; cystathionine beta-synthase [EC:4.2.1.22]
K01697 CBS; cystathionine beta-synthase [EC:4.2.1.22]
K00544 BHMT; betaine-homocysteine S-methyltransferase [EC:2.1.1.5]
K00547 mmuM; homocysteine S-methyltransferase [EC:2.1.1.10]
K00548 metH; 5-methyltetrahydrofolate--homocysteine methyltransferase [EC:2.1.1.13]
K00789 metK; S-adenosylmethionine synthetase [EC:2.5.1.6]
K00789 metK; S-adenosylmethionine synthetase [EC:2.5.1.6]
K00789 metK; S-adenosylmethionine synthetase [EC:2.5.1.6]
K01611 speD; S-adenosylmethionine decarboxylase [EC:4.1.1.50]
K00797 speE; spermidine synthase [EC:2.5.1.16]
K00802 SMS; spermine synthase [EC:2.5.1.22]
K00772 mtaP; 5'-methylthioadenosine phosphorylase [EC:2.4.2.28]
K05810 LACC1; purine-nucleoside/S-methyl-5'-thioadenosine phosphorylase / adenosine deaminase [EC:2.4.2.1 2.4.2.28 3.5.4.4]
K08963 mtnA; methylthioribose-1-phosphate isomerase [EC:5.3.1.23]
K08964 mtnB; methylthioribulose-1-phosphate dehydratase [EC:4.2.1.109]
K09880 mtnC; enolase-phosphatase E1 [EC:3.1.3.77]
K08967 mtnD; 1,2-dihydroxy-3-keto-5-methylthiopentene dioxygenase [EC:1.13.11.53 1.13.11.54]
K00815 TAT; tyrosine aminotransferase [EC:2.6.1.5]
K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2]
K00552 GNMT; glycine N-methyltransferase [EC:2.1.1.20]
K00558 DNMT1; DNA (cytosine-5)-methyltransferase 1 [EC:2.1.1.37]
K17398 DNMT3A; DNA (cytosine-5)-methyltransferase 3A [EC:2.1.1.37]
K17399 DNMT3B; DNA (cytosine-5)-methyltransferase 3B [EC:2.1.1.37]
K01251 AHCY; adenosylhomocysteinase [EC:3.13.2.1]
K01251 AHCY; adenosylhomocysteinase [EC:3.13.2.1]
K01251 AHCY; adenosylhomocysteinase [EC:3.13.2.1]
K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K00827 AGXT2; alanine-glyoxylate transaminase / (R)-3-amino-2-methylpropionate-pyruvate transaminase [EC:2.6.1.44 2.6.1.40]
K11204 GCLC; glutamate--cysteine ligase catalytic subunit [EC:6.3.2.2]
K11205 GCLM; glutamate--cysteine ligase regulatory subunit
K21456 GSS; glutathione synthase [EC:6.3.2.3]
K00456 CDO1; cysteine dioxygenase [EC:1.13.11.20]
K14454 GOT1; aspartate aminotransferase, cytoplasmic [EC:2.6.1.1]
K14454 GOT1; aspartate aminotransferase, cytoplasmic [EC:2.6.1.1]
K14455 GOT2; aspartate aminotransferase, mitochondrial [EC:2.6.1.1]
K01011 TST; thiosulfate/3-mercaptopyruvate sulfurtransferase [EC:2.8.1.1 2.8.1.2]
K01011 TST; thiosulfate/3-mercaptopyruvate sulfurtransferase [EC:2.8.1.1 2.8.1.2]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00025 MDH1; malate dehydrogenase [EC:1.1.1.37]
K00026 MDH2; malate dehydrogenase [EC:1.1.1.37]
K17989 SDS; L-serine/L-threonine ammonia-lyase [EC:4.3.1.17 4.3.1.19]
K17989 SDS; L-serine/L-threonine ammonia-lyase [EC:4.3.1.17 4.3.1.19]
K00058 serA; D-3-phosphoglycerate dehydrogenase / 2-oxoglutarate reductase [EC:1.1.1.95 1.1.1.399]
K00831 serC; phosphoserine aminotransferase [EC:2.6.1.52]
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00280 Valine, leucine and isoleucine degradation [PATH:hsa00280]
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00290 Valine, leucine and isoleucine biosynthesis [PATH:hsa00290]
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00300 Lysine biosynthesis
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00310 Lysine degradation [PATH:hsa00310]
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00220 Arginine biosynthesis [PATH:hsa00220]
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00330 Arginine and proline metabolism [PATH:hsa00330]
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00340 Histidine metabolism [PATH:hsa00340]
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00350 Tyrosine metabolism [PATH:hsa00350]
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00360 Phenylalanine metabolism [PATH:hsa00360]
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00380 Tryptophan metabolism [PATH:hsa00380]
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00400 Phenylalanine, tyrosine and tryptophan biosynthesis [PATH:hsa00400]
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09106 Metabolism of other amino acids
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09107 Glycan biosynthesis and metabolism
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09108 Metabolism of cofactors and vitamins
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09109 Metabolism of terpenoids and polyketides
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09110 Biosynthesis of other secondary metabolites
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09111 Xenobiotics biodegradation and metabolism
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09112 Not included in regular maps
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09120 Genetic Information Processing
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09130 Environmental Information Processing
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09140 Cellular Processes
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09150 Organismal Systems
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09151 Immune system
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09152 Endocrine system
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09153 Circulatory system
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09154 Digestive system
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09155 Excretory system
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04962 Vasopressin-regulated water reabsorption [PATH:hsa04962]
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04960 Aldosterone-regulated sodium reabsorption [PATH:hsa04960]
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04961 Endocrine and other factor-regulated calcium reabsorption [PATH:hsa04961]
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04964 Proximal tubule bicarbonate reclamation [PATH:hsa04964]
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6550 SLC9A3; solute carrier family 9 member A3
762 CA4; carbonic anhydrase 4
358 AQP1; aquaporin 1 (Colton blood group)
760 CA2; carbonic anhydrase 2
8671 SLC4A4; solute carrier family 4 member 4
476 ATP1A1; ATPase Na+/K+ transporting subunit alpha 1
477 ATP1A2; ATPase Na+/K+ transporting subunit alpha 2
478 ATP1A3; ATPase Na+/K+ transporting subunit alpha 3
480 ATP1A4; ATPase Na+/K+ transporting subunit alpha 4
23439 ATP1B4; ATPase Na+/K+ transporting family member beta 4
481 ATP1B1; ATPase Na+/K+ transporting subunit beta 1
482 ATP1B2; ATPase Na+/K+ transporting subunit beta 2
483 ATP1B3; ATPase Na+/K+ transporting subunit beta 3
486 FXYD2; FXYD domain containing ion transport regulator 2
10991 SLC38A3; solute carrier family 38 member 3
27165 GLS2; glutaminase 2
2744 GLS; glutaminase
2747 GLUD2; glutamate dehydrogenase 2
2746 GLUD1; glutamate dehydrogenase 1
1468 SLC25A10; solute carrier family 25 member 10
4190 MDH1; malate dehydrogenase 1
5105 PCK1; phosphoenolpyruvate carboxykinase 1
5106 PCK2; phosphoenolpyruvate carboxykinase 2, mitochondrial
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K12040 SLC9A3; solute carrier family 9 (sodium/hydrogen exchanger), member 3
K18246 CA4; carbonic anhydrase 4 [EC:4.2.1.1]
K09864 AQP1; aquaporin-1
K18245 CA2; carbonic anhydrase 2 [EC:4.2.1.1]
K13575 SLC4A4; solute carrier family 4 (sodium bicarbonate cotransporter), member 4
K01539 ATP1A; sodium/potassium-transporting ATPase subunit alpha [EC:7.2.2.13]
K01539 ATP1A; sodium/potassium-transporting ATPase subunit alpha [EC:7.2.2.13]
K01539 ATP1A; sodium/potassium-transporting ATPase subunit alpha [EC:7.2.2.13]
K01539 ATP1A; sodium/potassium-transporting ATPase subunit alpha [EC:7.2.2.13]
K01540 ATP1B; sodium/potassium-transporting ATPase subunit beta
K01540 ATP1B; sodium/potassium-transporting ATPase subunit beta
K01540 ATP1B; sodium/potassium-transporting ATPase subunit beta
K01540 ATP1B; sodium/potassium-transporting ATPase subunit beta
K01538 FXYD2; sodium/potassium-transporting ATPase subunit gamma (FXYD domain-containing ion transport regulator 2)
K13576 SLC38A3; solute carrier family 38 (sodium-coupled neutral amino acid transporter), member 3
K01425 glsA; glutaminase [EC:3.5.1.2]
K01425 glsA; glutaminase [EC:3.5.1.2]
K00261 GLUD1_2; glutamate dehydrogenase (NAD(P)+) [EC:1.4.1.3]
K00261 GLUD1_2; glutamate dehydrogenase (NAD(P)+) [EC:1.4.1.3]
K13577 SLC25A10; solute carrier family 25 (mitochondrial dicarboxylate transporter), member 10
K00025 MDH1; malate dehydrogenase [EC:1.1.1.37]
K01596 E4.1.1.32; phosphoenolpyruvate carboxykinase (GTP) [EC:4.1.1.32]
K01596 E4.1.1.32; phosphoenolpyruvate carboxykinase (GTP) [EC:4.1.1.32]
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04966 Collecting duct acid secretion [PATH:hsa04966]
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09156 Nervous system
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09157 Sensory system
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09158 Development and regeneration
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09149 Aging
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09159 Environmental adaptation
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09160 Human Diseases
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09180 Brite Hierarchies
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09190 Not Included in Pathway or Brite
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