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KO |
09100 Metabolism
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09101 Carbohydrate metabolism
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00010 Glycolysis / Gluconeogenesis [PATH:mgp00010]
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00020 Citrate cycle (TCA cycle) [PATH:mgp00020]
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00030 Pentose phosphate pathway [PATH:mgp00030]
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00040 Pentose and glucuronate interconversions [PATH:mgp00040]
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00051 Fructose and mannose metabolism [PATH:mgp00051]
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00052 Galactose metabolism [PATH:mgp00052]
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00053 Ascorbate and aldarate metabolism [PATH:mgp00053]
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00500 Starch and sucrose metabolism [PATH:mgp00500]
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00520 Amino sugar and nucleotide sugar metabolism [PATH:mgp00520]
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00620 Pyruvate metabolism [PATH:mgp00620]
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00630 Glyoxylate and dicarboxylate metabolism [PATH:mgp00630]
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00640 Propanoate metabolism [PATH:mgp00640]
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100538464 ACSS1; acetyl-coenzyme A synthetase 2-like, mitochondrial
100542964 ACSS2; acetyl-coenzyme A synthetase, cytoplasmic isoform X1
100541607 acetyl-coenzyme A synthetase 2-like, mitochondrial
100540880 ACSS3; LOW QUALITY PROTEIN: acyl-CoA synthetase short-chain family member 3, mitochondrial
100546491 BCKDHB; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
100550654 DBT; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
100548628 DLD; dihydrolipoyl dehydrogenase, mitochondrial
100541626 ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial
100540963 ACOX1; peroxisomal acyl-coenzyme A oxidase 1 isoform X1
100538886 ACOX3; peroxisomal acyl-coenzyme A oxidase 3 isoform X1
100548080 HADHA; trifunctional enzyme subunit alpha, mitochondrial
100551164 EHHADH; peroxisomal bifunctional enzyme
100541406 ECHS1; enoyl-CoA hydratase, mitochondrial
100544087 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
100539060 ACACB; acetyl-CoA carboxylase 2 isoform X1
100539312 MLYCD; malonyl-CoA decarboxylase, mitochondrial isoform X1
100549381 ABAT; 4-aminobutyrate aminotransferase, mitochondrial
100550247 PCCB; propionyl-CoA carboxylase beta chain, mitochondrial
100546546 ethylmalonyl-CoA decarboxylase isoform X1
104909791 ethylmalonyl-CoA decarboxylase-like
100542286 MCEE; methylmalonyl-CoA epimerase, mitochondrial
100549048 MMUT; methylmalonyl-CoA mutase, mitochondrial
100538831 SUCLG1; succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial
100548125 SUCLA2; succinate--CoA ligase [ADP-forming] subunit beta, mitochondrial
100550609 SUCLG2; succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial
100541149 ALDH6A1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
100547460 LDHB; L-lactate dehydrogenase B chain isoform X2
100550282 L-lactate dehydrogenase A chain-like
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K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01908 ACSS3; propionyl-CoA synthetase [EC:6.2.1.17]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K01946 ACACB; acetyl-CoA carboxylase / biotin carboxylase 2 [EC:6.4.1.2 6.3.4.14 2.1.3.15]
K01578 MLYCD; malonyl-CoA decarboxylase [EC:4.1.1.9]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K18426 ECHDC1; ethylmalonyl-CoA/methylmalonyl-CoA decarboxylase [EC:4.1.1.94 4.1.1.-]
K18426 ECHDC1; ethylmalonyl-CoA/methylmalonyl-CoA decarboxylase [EC:4.1.1.94 4.1.1.-]
K05606 MCEE; methylmalonyl-CoA/ethylmalonyl-CoA epimerase [EC:5.1.99.1]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K01899 LSC1; succinyl-CoA synthetase alpha subunit [EC:6.2.1.4 6.2.1.5]
K01900 LSC2; succinyl-CoA synthetase beta subunit [EC:6.2.1.4 6.2.1.5]
K01900 LSC2; succinyl-CoA synthetase beta subunit [EC:6.2.1.4 6.2.1.5]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
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00650 Butanoate metabolism [PATH:mgp00650]
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100550534 ACAT2; acetyl-CoA acetyltransferase, cytosolic
109365384 ACAT1; acetyl-CoA acetyltransferase, mitochondrial isoform X1
100542994 HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial
100548080 HADHA; trifunctional enzyme subunit alpha, mitochondrial
100551164 EHHADH; peroxisomal bifunctional enzyme
100541406 ECHS1; enoyl-CoA hydratase, mitochondrial
100541626 ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial
100540035 acyl-coenzyme A synthetase ACSM4, mitochondrial
100540188 acyl-coenzyme A synthetase ACSM3, mitochondrial-like isoform X1
100540655 ACSM3; acyl-coenzyme A synthetase ACSM3, mitochondrial isoform X1
100540849 L2HGDH; L-2-hydroxyglutarate dehydrogenase, mitochondrial
100542323 GAD2; glutamate decarboxylase 2
100541203 glutamate decarboxylase 1
104911775 glutamate decarboxylase 1-like
100549381 ABAT; 4-aminobutyrate aminotransferase, mitochondrial
100546241 ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial
100547858 HMGCS1; hydroxymethylglutaryl-CoA synthase, cytoplasmic
100540645 HMGCS2; hydroxymethylglutaryl-CoA synthase, mitochondrial
100539267 HMGCL; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1
100542783 HMGCLL1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic isoform X3
100546776 OXCT1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial isoform X1
100550304 AACS; acetoacetyl-CoA synthetase
100544505 BDH1; D-beta-hydroxybutyrate dehydrogenase, mitochondrial
100545437 D-beta-hydroxybutyrate dehydrogenase, mitochondrial-like
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K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K01896 ACSM; medium-chain acyl-CoA synthetase [EC:6.2.1.2]
K01896 ACSM; medium-chain acyl-CoA synthetase [EC:6.2.1.2]
K01896 ACSM; medium-chain acyl-CoA synthetase [EC:6.2.1.2]
K00109 L2HGDH; 2-hydroxyglutarate dehydrogenase [EC:1.1.99.2]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00139 ALDH5A1; succinate-semialdehyde dehydrogenase [EC:1.2.1.24]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01907 AACS; acetoacetyl-CoA synthetase [EC:6.2.1.16]
K00019 BDH1; 3-hydroxybutyrate dehydrogenase [EC:1.1.1.30]
K00019 BDH1; 3-hydroxybutyrate dehydrogenase [EC:1.1.1.30]
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00660 C5-Branched dibasic acid metabolism
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00562 Inositol phosphate metabolism [PATH:mgp00562]
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09102 Energy metabolism
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09103 Lipid metabolism
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00061 Fatty acid biosynthesis [PATH:mgp00061]
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00062 Fatty acid elongation [PATH:mgp00062]
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100543276 ACAA2; 3-ketoacyl-CoA thiolase, mitochondrial
100548234 HADHB; trifunctional enzyme subunit beta, mitochondrial isoform X2
100542994 HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial
100548080 HADHA; trifunctional enzyme subunit alpha, mitochondrial
100541406 ECHS1; enoyl-CoA hydratase, mitochondrial
100550872 MECR; enoyl-[acyl-carrier-protein] reductase, mitochondrial
100540149 PPT1; palmitoyl-protein thioesterase 1
104915837 PPT2; lysosomal thioesterase PPT2
100539668 ELOVL1; elongation of very long chain fatty acids protein 1
100538879 ELOVL2; elongation of very long chain fatty acids protein 2
100546793 ELOVL4; elongation of very long chain fatty acids protein 4
100540425 ELOVL5; elongation of very long chain fatty acids protein 5
100542840 ELOVL6; elongation of very long chain fatty acids protein 6
100539665 ELOVL3; elongation of very long chain fatty acids protein 3
104914910 ELOVL7; elongation of very long chain fatty acids protein 7
104911119 HSD17B12; very-long-chain 3-oxoacyl-CoA reductase
104911129 very-long-chain 3-oxoacyl-CoA reductase-like
100548753 HACD2; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase 2
100547269 HACD1; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase 1 isoform X2
100542802 HACD3; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase 3
104915048 HACD4; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase 4
100545685 TECR; very-long-chain enoyl-CoA reductase isoform X1
100545577 acyl-coenzyme A thioesterase 1-like isoform X2
100542633 acyl-coenzyme A thioesterase 1-like
100545422 acyl-coenzyme A thioesterase 5-like
100547443 ACOT7; cytosolic acyl coenzyme A thioester hydrolase
104915960 LOW QUALITY PROTEIN: acyl-coenzyme A thioesterase THEM4-like
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K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K07512 MECR; mitochondrial enoyl-[acyl-carrier protein] reductase / trans-2-enoyl-CoA reductase [EC:1.3.1.- 1.3.1.38]
K01074 PPT; palmitoyl-protein thioesterase [EC:3.1.2.22]
K01074 PPT; palmitoyl-protein thioesterase [EC:3.1.2.22]
K10247 ELOVL1; elongation of very long chain fatty acids protein 1 [EC:2.3.1.199]
K10205 ELOVL2; elongation of very long chain fatty acids protein 2 [EC:2.3.1.199]
K10249 ELOVL4; elongation of very long chain fatty acids protein 4 [EC:2.3.1.199]
K10244 ELOVL5; elongation of very long chain fatty acids protein 5 [EC:2.3.1.199]
K10203 ELOVL6; elongation of very long chain fatty acids protein 6 [EC:2.3.1.199]
K10203 ELOVL6; elongation of very long chain fatty acids protein 6 [EC:2.3.1.199]
K10250 ELOVL7; elongation of very long chain fatty acids protein 7 [EC:2.3.1.199]
K10251 HSD17B12; 17beta-estradiol 17-dehydrogenase / very-long-chain 3-oxoacyl-CoA reductase [EC:1.1.1.62 1.1.1.330]
K10251 HSD17B12; 17beta-estradiol 17-dehydrogenase / very-long-chain 3-oxoacyl-CoA reductase [EC:1.1.1.62 1.1.1.330]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10258 TER; very-long-chain enoyl-CoA reductase [EC:1.3.1.93]
K01068 ACOT1_2_4; acyl-coenzyme A thioesterase 1/2/4 [EC:3.1.2.2]
K01068 ACOT1_2_4; acyl-coenzyme A thioesterase 1/2/4 [EC:3.1.2.2]
K01068 ACOT1_2_4; acyl-coenzyme A thioesterase 1/2/4 [EC:3.1.2.2]
K17360 ACOT7; acyl-coenzyme A thioesterase 7 [EC:3.1.2.2]
K16339 THEM4; acyl-coenzyme A thioesterase THEM4 [EC:3.1.2.2]
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00071 Fatty acid degradation [PATH:mgp00071]
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100550534 ACAT2; acetyl-CoA acetyltransferase, cytosolic
109365384 ACAT1; acetyl-CoA acetyltransferase, mitochondrial isoform X1
100542533 ACAA1; 3-ketoacyl-CoA thiolase, peroxisomal
100543276 ACAA2; 3-ketoacyl-CoA thiolase, mitochondrial
100548234 HADHB; trifunctional enzyme subunit beta, mitochondrial isoform X2
100542994 HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial
100548080 HADHA; trifunctional enzyme subunit alpha, mitochondrial
100551164 EHHADH; peroxisomal bifunctional enzyme
100541406 ECHS1; enoyl-CoA hydratase, mitochondrial
100540963 ACOX1; peroxisomal acyl-coenzyme A oxidase 1 isoform X1
100538886 ACOX3; peroxisomal acyl-coenzyme A oxidase 3 isoform X1
100541626 ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial
104917156 ACADM; medium-chain specific acyl-CoA dehydrogenase, mitochondrial
100540388 ACADL; long-chain specific acyl-CoA dehydrogenase, mitochondrial
100542282 ACADSB; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
104915954 glutaryl-CoA dehydrogenase, mitochondrial-like
104916895 glutaryl-CoA dehydrogenase, mitochondrial-like
100539925 ACSL4; long-chain-fatty-acid--CoA ligase 4
100546186 ACSL1; long-chain-fatty-acid--CoA ligase 1 isoform X2
100548195 ACSL5; long-chain-fatty-acid--CoA ligase 5
100548919 ACSL6; long-chain-fatty-acid--CoA ligase 6 isoform X1
100549940 long-chain-fatty-acid--CoA ligase 3-like
100551321 ACSBG1; long-chain-fatty-acid--CoA ligase ACSBG1 isoform X1
100542721 ACSBG2; long-chain-fatty-acid--CoA ligase ACSBG2 isoform X1
100549362 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform isoform X1
100540756 CPT2; carnitine O-palmitoyltransferase 2, mitochondrial
100540710 ECI1; enoyl-CoA delta isomerase 1, mitochondrial
100541809 ECI2; enoyl-CoA delta isomerase 2, mitochondrial isoform X1
100543147 cytochrome P450 2U1
100545163 alcohol dehydrogenase 1
104910746 alcohol dehydrogenase 1-like
104915446 alcohol dehydrogenase 1-like
100544708 alcohol dehydrogenase class-3
100548356 ALDH2; aldehyde dehydrogenase, mitochondrial
100547956 ALDH3A2; LOW QUALITY PROTEIN: aldehyde dehydrogenase family 3 member A2
104915364 ALDH7A1; LOW QUALITY PROTEIN: alpha-aminoadipic semialdehyde dehydrogenase
100546048 ALDH9A1; 4-trimethylaminobutyraldehyde dehydrogenase
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K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00255 ACADL; long-chain-acyl-CoA dehydrogenase [EC:1.3.8.8]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K15013 ACSBG; long-chain-fatty-acid--CoA ligase ACSBG [EC:6.2.1.3]
K15013 ACSBG; long-chain-fatty-acid--CoA ligase ACSBG [EC:6.2.1.3]
K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
K08766 CPT2; carnitine O-palmitoyltransferase 2 [EC:2.3.1.21]
K13238 ECI1; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K13239 ECI2; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K07422 CYP2U1; long-chain fatty acid omega-monooxygenase [EC:1.14.14.80]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K13951 ADH1_7; alcohol dehydrogenase 1/7 [EC:1.1.1.1]
K00121 frmA; S-(hydroxymethyl)glutathione dehydrogenase / alcohol dehydrogenase [EC:1.1.1.284 1.1.1.1]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
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00073 Cutin, suberine and wax biosynthesis
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00100 Steroid biosynthesis [PATH:mgp00100]
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00120 Primary bile acid biosynthesis [PATH:mgp00120]
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00121 Secondary bile acid biosynthesis
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00140 Steroid hormone biosynthesis [PATH:mgp00140]
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00561 Glycerolipid metabolism [PATH:mgp00561]
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00564 Glycerophospholipid metabolism [PATH:mgp00564]
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00565 Ether lipid metabolism [PATH:mgp00565]
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00600 Sphingolipid metabolism [PATH:mgp00600]
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00590 Arachidonic acid metabolism [PATH:mgp00590]
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00591 Linoleic acid metabolism [PATH:mgp00591]
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00592 alpha-Linolenic acid metabolism [PATH:mgp00592]
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01040 Biosynthesis of unsaturated fatty acids [PATH:mgp01040]
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09104 Nucleotide metabolism
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09105 Amino acid metabolism
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00250 Alanine, aspartate and glutamate metabolism [PATH:mgp00250]
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00260 Glycine, serine and threonine metabolism [PATH:mgp00260]
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00270 Cysteine and methionine metabolism [PATH:mgp00270]
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00280 Valine, leucine and isoleucine degradation [PATH:mgp00280]
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100539235 BCAT1; branched-chain-amino-acid aminotransferase, cytosolic
100540143 IL4I1; L-amino-acid oxidase
100546491 BCKDHB; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
100550654 DBT; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
100548628 DLD; dihydrolipoyl dehydrogenase, mitochondrial
100541626 ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial
104917156 ACADM; medium-chain specific acyl-CoA dehydrogenase, mitochondrial
100546033 IVD; isovaleryl-CoA dehydrogenase, mitochondrial
100542282 ACADSB; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
100540043 ACAD8; isobutyryl-CoA dehydrogenase, mitochondrial
100548080 HADHA; trifunctional enzyme subunit alpha, mitochondrial
100551164 EHHADH; peroxisomal bifunctional enzyme
100541406 ECHS1; enoyl-CoA hydratase, mitochondrial
100542994 HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial
100540780 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2
100542533 ACAA1; 3-ketoacyl-CoA thiolase, peroxisomal
100543276 ACAA2; 3-ketoacyl-CoA thiolase, mitochondrial
100548234 HADHB; trifunctional enzyme subunit beta, mitochondrial isoform X2
100550247 PCCB; propionyl-CoA carboxylase beta chain, mitochondrial
100542286 MCEE; methylmalonyl-CoA epimerase, mitochondrial
100549048 MMUT; methylmalonyl-CoA mutase, mitochondrial
100544087 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
100539611 HIBADH; 3-hydroxyisobutyrate dehydrogenase, mitochondrial isoform X1
100541149 ALDH6A1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
100548356 ALDH2; aldehyde dehydrogenase, mitochondrial
100547956 ALDH3A2; LOW QUALITY PROTEIN: aldehyde dehydrogenase family 3 member A2
104915364 ALDH7A1; LOW QUALITY PROTEIN: alpha-aminoadipic semialdehyde dehydrogenase
100546048 ALDH9A1; 4-trimethylaminobutyraldehyde dehydrogenase
100548803 AOX1; aldehyde oxidase
100549268 aldehyde oxidase 2-like
104913064 ACSF3; malonate--CoA ligase ACSF3, mitochondrial
100549381 ABAT; 4-aminobutyrate aminotransferase, mitochondrial
100541842 AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1
104912682 MCCC1; methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
100539364 methylcrotonoyl-CoA carboxylase beta chain, mitochondrial-like
100549392 AUH; methylglutaconyl-CoA hydratase, mitochondrial
100539267 HMGCL; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1
100542783 HMGCLL1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic isoform X3
100546776 OXCT1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial isoform X1
100550304 AACS; acetoacetyl-CoA synthetase
100550534 ACAT2; acetyl-CoA acetyltransferase, cytosolic
109365384 ACAT1; acetyl-CoA acetyltransferase, mitochondrial isoform X1
100547858 HMGCS1; hydroxymethylglutaryl-CoA synthase, cytoplasmic
100540645 HMGCS2; hydroxymethylglutaryl-CoA synthase, mitochondrial
|
K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00253 IVD; isovaleryl-CoA dehydrogenase [EC:1.3.8.4]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K11538 ACAD8; isobutyryl-CoA dehydrogenase [EC:1.3.99.-]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K05606 MCEE; methylmalonyl-CoA/ethylmalonyl-CoA epimerase [EC:5.1.99.1]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K00020 HIBADH; 3-hydroxyisobutyrate dehydrogenase [EC:1.1.1.31]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K18660 ACSF3; malonyl-CoA/methylmalonyl-CoA synthetase [EC:6.2.1.76 6.2.1.-]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00827 AGXT2; alanine-glyoxylate transaminase / (R)-3-amino-2-methylpropionate-pyruvate transaminase [EC:2.6.1.44 2.6.1.40]
K01968 MCCC1; 3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
K01969 MCCC2; 3-methylcrotonyl-CoA carboxylase beta subunit [EC:6.4.1.4]
K05607 AUH; methylglutaconyl-CoA hydratase [EC:4.2.1.18]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01907 AACS; acetoacetyl-CoA synthetase [EC:6.2.1.16]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
|
00290 Valine, leucine and isoleucine biosynthesis [PATH:mgp00290]
|
00300 Lysine biosynthesis
|
00310 Lysine degradation [PATH:mgp00310]
|
100543809 AASS; alpha-aminoadipic semialdehyde synthase, mitochondrial
104915364 ALDH7A1; LOW QUALITY PROTEIN: alpha-aminoadipic semialdehyde dehydrogenase
100539859 AADAT; kynurenine/alpha-aminoadipate aminotransferase, mitochondrial isoform X1
100540782 DHTKD1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial isoform X1
100542845 DLST; dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial
100548628 DLD; dihydrolipoyl dehydrogenase, mitochondrial
104915954 glutaryl-CoA dehydrogenase, mitochondrial-like
104916895 glutaryl-CoA dehydrogenase, mitochondrial-like
100548080 HADHA; trifunctional enzyme subunit alpha, mitochondrial
100551164 EHHADH; peroxisomal bifunctional enzyme
100541406 ECHS1; enoyl-CoA hydratase, mitochondrial
100542994 HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial
100550534 ACAT2; acetyl-CoA acetyltransferase, cytosolic
109365384 ACAT1; acetyl-CoA acetyltransferase, mitochondrial isoform X1
104912798 HYKK; hydroxylysine kinase
100538852 5-phosphohydroxy-L-lysine phospho-lyase
100540414 PIPOX; peroxisomal sarcosine oxidase isoform X1
100547619 CAMKMT; calmodulin-lysine N-methyltransferase isoform X1
100540662 KMT2A; histone-lysine N-methyltransferase 2A
104915798 LOW QUALITY PROTEIN: histone-lysine N-methyltransferase 2D-like
100545169 KMT2C; histone-lysine N-methyltransferase 2C isoform X2
100545555 KMT2E; inactive histone-lysine N-methyltransferase 2E
100544670 SETD1B; histone-lysine N-methyltransferase SETD1B
100541967 SETD7; histone-lysine N-methyltransferase SETD7
100539732 ASH1L; histone-lysine N-methyltransferase ASH1L isoform X1
100548953 SMYD1; histone-lysine N-methyltransferase SMYD1 isoform X1
104909329 histone-lysine N-methyltransferase SMYD3-like
100538978 SMYD2; N-lysine methyltransferase SMYD2
100539540 SUV39H2; histone-lysine N-methyltransferase SUV39H2
100548070 histone-lysine N-methyltransferase SUV39H1-like
104916314 histone-lysine N-methyltransferase SUV39H1-like
100538392 EHMT1; histone-lysine N-methyltransferase EHMT1 isoform X5
100542346 SETDB1; LOW QUALITY PROTEIN: histone-lysine N-methyltransferase SETDB1
100550682 LOW QUALITY PROTEIN: histone-lysine N-methyltransferase SETDB2
104914188 LOW QUALITY PROTEIN: PR domain zinc finger protein 2
100541270 LOW QUALITY PROTEIN: PR domain zinc finger protein 2-like
100547448 EZH1; histone-lysine N-methyltransferase EZH1
100540374 EZH2; histone-lysine N-methyltransferase EZH2 isoform X1
100542442 histone-lysine N-methyltransferase SETMAR
100538695 NSD1; LOW QUALITY PROTEIN: histone-lysine N-methyltransferase, H3 lysine-36 and H4 lysine-20 specific
100543303 histone-lysine N-methyltransferase NSD2
100550821 NSD3; histone-lysine N-methyltransferase NSD3 isoform X1
100539457 SETD2; histone-lysine N-methyltransferase SETD2
100546682 DOT1L; histone-lysine N-methyltransferase, H3 lysine-79 specific isoform X4
100540244 KMT5A; N-lysine methyltransferase KMT5A
100547012 KMT5B; histone-lysine N-methyltransferase KMT5B isoform X1
116217397 histone-lysine N-methyltransferase KMT5C-like
100541414 MECOM; histone-lysine N-methyltransferase MECOM isoform X1
100549442 PRDM16; LOW QUALITY PROTEIN: histone-lysine N-methyltransferase PRDM16
100544092 TMLHE; trimethyllysine dioxygenase, mitochondrial
100548356 ALDH2; aldehyde dehydrogenase, mitochondrial
100547956 ALDH3A2; LOW QUALITY PROTEIN: aldehyde dehydrogenase family 3 member A2
100546048 ALDH9A1; 4-trimethylaminobutyraldehyde dehydrogenase
100548089 BBOX1; gamma-butyrobetaine dioxygenase
100542606 PLOD1; procollagen-lysine,2-oxoglutarate 5-dioxygenase 1
100544189 PLOD2; procollagen-lysine,2-oxoglutarate 5-dioxygenase 2 isoform X1
100540024 COLGALT2; procollagen galactosyltransferase 2
100546534 procollagen galactosyltransferase 1-like
|
K14157 AASS; alpha-aminoadipic semialdehyde synthase [EC:1.5.1.8 1.5.1.9]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00825 AADAT; kynurenine/2-aminoadipate aminotransferase [EC:2.6.1.7 2.6.1.39]
K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
K00658 DLST; 2-oxoglutarate dehydrogenase E2 component (dihydrolipoamide succinyltransferase) [EC:2.3.1.61]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K18201 AGPHD1; hydroxylysine kinase [EC:2.7.1.81]
K18202 AGXT2L2; 5-phosphonooxy-L-lysine phospho-lyase [EC:4.2.3.134]
K00306 PIPOX; sarcosine oxidase / L-pipecolate oxidase [EC:1.5.3.1 1.5.3.7]
K18826 CAMKMT; calmodulin-lysine N-methyltransferase [EC:2.1.1.60]
K09186 MLL1; [histone H3]-lysine4 N-trimethyltransferase MLL1 [EC:2.1.1.354]
K09187 MLL2; [histone H3]-lysine4 N-trimethyltransferase MLL2 [EC:2.1.1.354]
K09188 MLL3; [histone H3]-lysine4 N-trimethyltransferase MLL3 [EC:2.1.1.354]
K09189 MLL5; [histone H3]-lysine4 N-trimethyltransferase MLL5 [EC:2.1.1.354]
K11422 SETD1; [histone H3]-lysine4 N-trimethyltransferase SETD1 [EC:2.1.1.354]
K11431 SETD7; [histone H3]-lysine4 N-methyltransferase [EC:2.1.1.364]
K06101 ASH1L; [histone H3]-lysine4 N-trimethyltransferase ASH1L [EC:2.1.1.354]
K11426 SMYD; [histone H3]-lysine4/36 N-trimethyltransferase SMYD [EC:2.1.1.354 2.1.1.357]
K11426 SMYD; [histone H3]-lysine4/36 N-trimethyltransferase SMYD [EC:2.1.1.354 2.1.1.357]
K11426 SMYD; [histone H3]-lysine4/36 N-trimethyltransferase SMYD [EC:2.1.1.354 2.1.1.357]
K11419 SUV39H; [histone H3]-lysine9 N-trimethyltransferase SUV39H [EC:2.1.1.355]
K11419 SUV39H; [histone H3]-lysine9 N-trimethyltransferase SUV39H [EC:2.1.1.355]
K11419 SUV39H; [histone H3]-lysine9 N-trimethyltransferase SUV39H [EC:2.1.1.355]
K11420 EHMT; [histone H3]-lysine9 N-trimethyltransferase EHMT [EC:2.1.1.355]
K11421 SETDB1; [histone H3]-N6,N6-dimethyl-lysine9 N-methyltransferase [EC:2.1.1.366]
K18494 SETDB2; [histone H3]-lysine9 N-trimethyltransferase SETDB2 [EC:2.1.1.355]
K11432 PRDM2; [histone H3]-lysine9 N-trimethyltransferase PRDM2 [EC:2.1.1.355]
K11432 PRDM2; [histone H3]-lysine9 N-trimethyltransferase PRDM2 [EC:2.1.1.355]
K17451 EZH1; [histone H3]-lysine27 N-trimethyltransferase EZH1 [EC:2.1.1.356]
K11430 EZH2; [histone H3]-lysine27 N-trimethyltransferase EZH2 [EC:2.1.1.356]
K11433 SETMAR; [histone H3]-lysine36 N-dimethyltransferase SETMAR [EC:2.1.1.357]
K15588 NSD1; [histone H3]-lysine36 N-dimethyltransferase NSD1 [EC:2.1.1.357]
K11424 WHSC1; [histone H3]-lysine36 N-dimethyltransferase NSD2 [EC:2.1.1.357]
K11425 WHSC1L1; [histone H3]-lysine4 N-dimethyltransferase / [histone H3]-lysine27 N-dimethyltransferase [EC:2.1.1.370 2.1.1.371]
K11423 SETD2; [histone H3]-lysine36 N-trimethyltransferase [EC:2.1.1.359]
K11427 DOT1L; [histone H3]-lysine79 N-trimethyltransferase [EC:2.1.1.360]
K11428 SETD8; [histone H4]-lysine20 N-methyltransferase SETD8 [EC:2.1.1.361]
K11429 SUV420H; [histone H4]-N-methyl-L-lysine20 N-methyltransferase [EC:2.1.1.362]
K11429 SUV420H; [histone H4]-N-methyl-L-lysine20 N-methyltransferase [EC:2.1.1.362]
K04462 MECOM; [histone H3]-lysine9 N-methyltransferase (ecotropic virus integration site 1 protein) [EC:2.1.1.367]
K22410 PRDM16; [histone H3]-lysine9 N-methyltransferase [EC:2.1.1.367]
K00474 TMLHE; trimethyllysine dioxygenase [EC:1.14.11.8]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K00471 BBOX1; gamma-butyrobetaine dioxygenase [EC:1.14.11.1]
K00473 PLOD1; procollagen-lysine,2-oxoglutarate 5-dioxygenase 1 [EC:1.14.11.4]
K13645 PLOD2; procollagen-lysine,2-oxoglutarate 5-dioxygenase 2 [EC:1.14.11.4]
K11703 GLT25D; collagen beta-1,O-galactosyltransferase [EC:2.4.1.50]
K11703 GLT25D; collagen beta-1,O-galactosyltransferase [EC:2.4.1.50]
|
00220 Arginine biosynthesis [PATH:mgp00220]
|
00330 Arginine and proline metabolism [PATH:mgp00330]
|
00340 Histidine metabolism [PATH:mgp00340]
|
00350 Tyrosine metabolism [PATH:mgp00350]
|
00360 Phenylalanine metabolism [PATH:mgp00360]
|
00380 Tryptophan metabolism [PATH:mgp00380]
|
100547674 TDO2; tryptophan 2,3-dioxygenase
100548413 IDO2; indoleamine 2,3-dioxygenase 2 isoform X1
100547285 AFMID; kynurenine formamidase
100543720 KMO; kynurenine 3-monooxygenase isoform X1
100543523 kynureninase isoform X1
104911834 kynureninase-like
100543137 HAAO; 3-hydroxyanthranilate 3,4-dioxygenase isoform X1
100540076 ACMSD; 2-amino-3-carboxymuconate-6-semialdehyde decarboxylase isoform X1
100538722 ALDH8A1; 2-aminomuconic semialdehyde dehydrogenase
100540782 DHTKD1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial isoform X1
100542845 DLST; dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial
100548628 DLD; dihydrolipoyl dehydrogenase, mitochondrial
104915954 glutaryl-CoA dehydrogenase, mitochondrial-like
104916895 glutaryl-CoA dehydrogenase, mitochondrial-like
100548080 HADHA; trifunctional enzyme subunit alpha, mitochondrial
100551164 EHHADH; peroxisomal bifunctional enzyme
100541406 ECHS1; enoyl-CoA hydratase, mitochondrial
100542994 HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial
100550534 ACAT2; acetyl-CoA acetyltransferase, cytosolic
109365384 ACAT1; acetyl-CoA acetyltransferase, mitochondrial isoform X1
100545698 KYAT1; kynurenine--oxoglutarate transaminase 1 isoform X1
100546759 KYAT3; kynurenine--oxoglutarate transaminase 3 isoform X3
100539859 AADAT; kynurenine/alpha-aminoadipate aminotransferase, mitochondrial isoform X1
100303678 TPH2; tryptophan 5-hydroxylase 2
100549515 TPH1; tryptophan 5-hydroxylase 1
100542576 DDC; aromatic-L-amino-acid decarboxylase
100540365 amine oxidase [flavin-containing] A-like
100540209 amine oxidase [flavin-containing] B-like
100548356 ALDH2; aldehyde dehydrogenase, mitochondrial
100547956 ALDH3A2; LOW QUALITY PROTEIN: aldehyde dehydrogenase family 3 member A2
104915364 ALDH7A1; LOW QUALITY PROTEIN: alpha-aminoadipic semialdehyde dehydrogenase
100546048 ALDH9A1; 4-trimethylaminobutyraldehyde dehydrogenase
100548803 AOX1; aldehyde oxidase
100549268 aldehyde oxidase 2-like
100547251 acetylserotonin O-methyltransferase
100549848 AANAT; serotonin N-acetyltransferase
100542888 cytochrome P450 1B1
100540143 IL4I1; L-amino-acid oxidase
100541757 CAT; catalase
|
K00453 TDO2; tryptophan 2,3-dioxygenase [EC:1.13.11.11]
K00463 IDO; indoleamine 2,3-dioxygenase [EC:1.13.11.52]
K01432 AFMID; arylformamidase [EC:3.5.1.9]
K00486 KMO; kynurenine 3-monooxygenase [EC:1.14.13.9]
K01556 KYNU; kynureninase [EC:3.7.1.3]
K01556 KYNU; kynureninase [EC:3.7.1.3]
K00452 HAAO; 3-hydroxyanthranilate 3,4-dioxygenase [EC:1.13.11.6]
K03392 ACMSD; aminocarboxymuconate-semialdehyde decarboxylase [EC:4.1.1.45]
K23234 ALDH8A1; aminomuconate-semialdehyde dehydrogenase [EC:1.2.1.32]
K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
K00658 DLST; 2-oxoglutarate dehydrogenase E2 component (dihydrolipoamide succinyltransferase) [EC:2.3.1.61]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00816 CCBL; kynurenine---oxoglutarate transaminase / cysteine-S-conjugate beta-lyase / glutamine---phenylpyruvate transaminase [EC:2.6.1.7 4.4.1.13 2.6.1.64]
K00816 CCBL; kynurenine---oxoglutarate transaminase / cysteine-S-conjugate beta-lyase / glutamine---phenylpyruvate transaminase [EC:2.6.1.7 4.4.1.13 2.6.1.64]
K00825 AADAT; kynurenine/2-aminoadipate aminotransferase [EC:2.6.1.7 2.6.1.39]
K00502 TPH1_2; tryptophan 5-monooxygenase [EC:1.14.16.4]
K00502 TPH1_2; tryptophan 5-monooxygenase [EC:1.14.16.4]
K01593 DDC; aromatic-L-amino-acid/L-tryptophan decarboxylase [EC:4.1.1.28 4.1.1.105]
K00274 MAO; monoamine oxidase [EC:1.4.3.4]
K00274 MAO; monoamine oxidase [EC:1.4.3.4]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K00543 ASMT; acetylserotonin O-methyltransferase [EC:2.1.1.4]
K00669 AANAT; arylalkylamine N-acetyltransferase [EC:2.3.1.87]
K07410 CYP1B1; cytochrome P450 family 1 subfamily B1 [EC:1.14.14.1]
K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2]
K03781 katE; catalase [EC:1.11.1.6]
|
00400 Phenylalanine, tyrosine and tryptophan biosynthesis [PATH:mgp00400]
|
|
|
09106 Metabolism of other amino acids
|
00410 beta-Alanine metabolism [PATH:mgp00410]
|
100547015 GADL1; acidic amino acid decarboxylase GADL1
100547396 CSAD; cysteine sulfinic acid decarboxylase isoform X2
100542323 GAD2; glutamate decarboxylase 2
100541203 glutamate decarboxylase 1
104911775 glutamate decarboxylase 1-like
100541194 CNDP1; beta-Ala-His dipeptidase
100548525 CARNS1; LOW QUALITY PROTEIN: carnosine synthase 1
100541349 CNDP2; cytosolic non-specific dipeptidase
100549381 ABAT; 4-aminobutyrate aminotransferase, mitochondrial
100540689 SMOX; spermine oxidase
100548064 LOW QUALITY PROTEIN: membrane primary amine oxidase-like
100548356 ALDH2; aldehyde dehydrogenase, mitochondrial
100547956 ALDH3A2; LOW QUALITY PROTEIN: aldehyde dehydrogenase family 3 member A2
104915364 ALDH7A1; LOW QUALITY PROTEIN: alpha-aminoadipic semialdehyde dehydrogenase
100546048 ALDH9A1; 4-trimethylaminobutyraldehyde dehydrogenase
100548954 aldehyde dehydrogenase family 3 member B1
100548799 aldehyde dehydrogenase family 3 member B1-like
100549110 aldehyde dehydrogenase family 3 member B1-like isoform X1
100538897 dihydropyrimidine dehydrogenase [NADP(+)]
100551410 DPYS; dihydropyrimidinase
100546726 UPB1; beta-ureidopropionase
100544087 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
100548080 HADHA; trifunctional enzyme subunit alpha, mitochondrial
100551164 EHHADH; peroxisomal bifunctional enzyme
100541406 ECHS1; enoyl-CoA hydratase, mitochondrial
100541626 ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial
100540963 ACOX1; peroxisomal acyl-coenzyme A oxidase 1 isoform X1
100538886 ACOX3; peroxisomal acyl-coenzyme A oxidase 3 isoform X1
100539312 MLYCD; malonyl-CoA decarboxylase, mitochondrial isoform X1
100541149 ALDH6A1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
|
K18966 GADL1; sulfinoalanine decarboxylase / aspartate 1-decarboxylase [EC:4.1.1.29 4.1.1.11]
K18966 GADL1; sulfinoalanine decarboxylase / aspartate 1-decarboxylase [EC:4.1.1.29 4.1.1.11]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K05604 CNDP1; beta-Ala-His dipeptidase [EC:3.4.13.20]
K14755 CRNS1; carnosine synthase [EC:6.3.2.11]
K08660 CNDP2; cytosolic nonspecific dipeptidase [EC:3.4.13.18]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K12259 SMOX; spermine oxidase [EC:1.5.3.16 1.5.3.-]
K00276 AOC3; primary-amine oxidase [EC:1.4.3.21]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K00129 ALDH3; aldehyde dehydrogenase (NAD(P)+) [EC:1.2.1.5]
K00129 ALDH3; aldehyde dehydrogenase (NAD(P)+) [EC:1.2.1.5]
K00129 ALDH3; aldehyde dehydrogenase (NAD(P)+) [EC:1.2.1.5]
K00207 DPYD; dihydropyrimidine dehydrogenase (NADP+) [EC:1.3.1.2]
K01464 DPYS; dihydropyrimidinase [EC:3.5.2.2]
K01431 UPB1; beta-ureidopropionase [EC:3.5.1.6]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K01578 MLYCD; malonyl-CoA decarboxylase [EC:4.1.1.9]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
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00430 Taurine and hypotaurine metabolism [PATH:mgp00430]
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00440 Phosphonate and phosphinate metabolism [PATH:mgp00440]
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00450 Selenocompound metabolism [PATH:mgp00450]
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00460 Cyanoamino acid metabolism
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00470 D-Amino acid metabolism [PATH:mgp00470]
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00480 Glutathione metabolism [PATH:mgp00480]
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09107 Glycan biosynthesis and metabolism
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09108 Metabolism of cofactors and vitamins
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09109 Metabolism of terpenoids and polyketides
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09110 Biosynthesis of other secondary metabolites
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09111 Xenobiotics biodegradation and metabolism
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09112 Not included in regular maps
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09120 Genetic Information Processing
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09130 Environmental Information Processing
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09140 Cellular Processes
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09150 Organismal Systems
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09160 Human Diseases
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09180 Brite Hierarchies
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09190 Not Included in Pathway or Brite
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