Human diseases in ICD-11 classification [BR:br08403] 05 Endocrine, nutritional or metabolic diseases Metabolic disorders Inborn errors of metabolism 5C52 Inborn errors of lipid metabolism H00151 Cerebrotendinous xanthomatosis Pathway-based classification of diseases [BR:br08402] Lipid/glycolipid metabolism nt06022 Bile acid biosynthesis H00151 Cerebrotendinous xanthomatosis