KEGG   ORTHOLOGY: K01204
Entry
K01204                      KO                                     
Symbol
NAGA
Name
alpha-N-acetylgalactosaminidase [EC:3.2.1.49]
Pathway
map00603  Glycosphingolipid biosynthesis - globo and isoglobo series
map01100  Metabolic pathways
map04142  Lysosome
Reaction
R05966  
Disease
H00146  Alpha-N-acetylgalactosaminidase deficiency
H00422  Glycoproteinoses
Brite
KEGG Orthology (KO) [BR:ko00001]
 09100 Metabolism
  09107 Glycan biosynthesis and metabolism
   00603 Glycosphingolipid biosynthesis - globo and isoglobo series
    K01204  NAGA; alpha-N-acetylgalactosaminidase
 09140 Cellular Processes
  09141 Transport and catabolism
   04142 Lysosome
    K01204  NAGA; alpha-N-acetylgalactosaminidase
Enzymes [BR:ko01000]
 3. Hydrolases
  3.2  Glycosylases
   3.2.1  Glycosidases, i.e. enzymes that hydrolyse O- and S-glycosyl compounds
    3.2.1.49  alpha-N-acetylgalactosaminidase
     K01204  NAGA; alpha-N-acetylgalactosaminidase
Other DBs
GO: 0008456
Genes
HSA: 4668(NAGA)
PTR: 470279(NAGA)
PPS: 100991597(NAGA)
GGO: 101132690(NAGA)
PON: 100450338(NAGA)
PPYG: 129023331(NAGA)
NLE: 100605546(NAGA)
HMH: 116458803(NAGA)
SSYN: 129468048(NAGA)
MCC: 713068(NAGA)
MCF: 102145379(NAGA)
MTHB: 126963611
MNI: 105464355(NAGA)
CSAB: 103223407(NAGA)
CATY: 105572167(NAGA)
PANU: 101016466(NAGA)
TGE: 112633355(NAGA)
MLEU: 105538807(NAGA)
RRO: 104670530(NAGA)
RBB: 108543578(NAGA)
TFN: 117096393(NAGA)
PTEH: 111548936(NAGA)
CANG: 105514017(NAGA)
CJC: 100397642(NAGA)
SBQ: 101052589(NAGA)
CIMI: 108290476(NAGA)
CSYR: 103264351(NAGA)
MMUR: 105858599(NAGA)
LCAT: 123640287(NAGA)
PCOQ: 105805270(NAGA)
OGA: 100954557(NAGA)
MMU: 17939(Naga)
MCAL: 110310380(Naga)
MPAH: 110334850(Naga)
RNO: 315165(Naga)
MCOC: 116076661(Naga)
ANU: 117719166(Naga)
ASYL: 127668213(Naga)
MUN: 110554096(Naga)
CGE: 100751670(Naga)
MAUA: 101840437(Naga)
PROB: 127225858(Naga)
PLEU: 114694320(Naga)
MORG: 121461193(Naga)
MFOT: 126515716
AAMP: 119823607(Naga)
NGI: 103743459(Naga)
HGL: 101726122(Naga)
CPOC: 100719787(Naga)
CCAN: 109689379(Naga)
DORD: 105992105(Naga)
DSP: 122123599(Naga)
DMER: 138811810(Naga) 138829787
PLOP: 125357570(Naga)
NCAR: 124982310
MMMA: 107155833(Naga)
ITI: 101959382(Naga)
OCU: 100350048
OPI: 101536106(NAGA)
TUP: 102490461(NAGA)
GVR: 103591795(NAGA)
CFA: 481226(NAGA)
CLUD: 112666708(NAGA)
VVP: 112934013(NAGA)
VLG: 121492200(NAGA)
NPO: 129512102(NAGA)
AML: 100471467(NAGA)
UMR: 103674070(NAGA)
UAH: 113241706(NAGA)
UAR: 123780544(NAGA)
ELK: 111157598
LLV: 125106372
MPUF: 101673551(NAGA)
MNP: 132019160(NAGA)
MLK: 131839557(NAGA)
NVS: 122892575(NAGA)
ORO: 101381151(NAGA)
EJU: 114218390(NAGA)
ZCA: 113922578(NAGA)
MLX: 117998614(NAGA)
NSU: 110578239(NAGA)
LWW: 102738869(NAGA)
FCA: 101083277(NAGA)
PYU: 121040244(NAGA)
PCOO: 112863480(NAGA)
PBG: 122472839(NAGA)
PVIV: 125171045(NAGA)
LRUF: 124502033
LGF: 123590449(NAGA)
AJU: 106979923
PTG: 102963636(NAGA)
PPAD: 109265652(NAGA)
PUC: 125920377
PLEZ: 122225203(NAGA)
HHV: 120235028(NAGA)
BTA: 533357(NAGA)
BOM: 102280167(NAGA)
BIU: 109559874(NAGA)
BBUB: 102404704(NAGA)
BBIS: 104991253(NAGA)
CHX: 102170679(NAGA)
OAS: 100145858(NAGA)
BTAX: 128047737(NAGA)
CSUM: 138078008(NAGA)
ODA: 120857579(NAGA)
CCAD: 122423544(NAGA)
MREE: 136174649(NAGA)
OVR: 110127013(NAGA)
MBEZ: 129536613(NAGA)
SSC: 100142667(NAGA)
CFR: 102511662(NAGA)
CBAI: 105073060(NAGA)
CDK: 105091882(NAGA)
VPC: 102541563(NAGA)
BACU: 103005673(NAGA)
BMUS: 118901630(NAGA)
LVE: 103072389(NAGA)
OOR: 101272207(NAGA)
LALB: 132528992(NAGA)
GMF: 115852722(NAGA)
DDP: 132434125(NAGA)
DLE: 111186345(NAGA)
PCAD: 102973583(NAGA)
PSIU: 116760277(NAGA)
PPHC: 136130641(NAGA)
NASI: 112394634(NAGA)
ECB: 100070793(NAGA)
EPZ: 103541990(NAGA)
EAI: 106848492(NAGA)
MYB: 102258282(NAGA)
MYD: 102754122(NAGA)
MMYO: 118651848(NAGA)
MLF: 102422016(NAGA)
MDT: 132225822(NAGA)
MYUM: 139007621(NAGA)
PKL: 118712063(NAGA)
EFUS: 103288815(NAGA)
MNA: 107534967(NAGA)
DRO: 112321929(NAGA)
SHON: 119002460(NAGA)
AJM: 119060491(NAGA)
PDIC: 114513182(NAGA)
PHAS: 123816241(NAGA)
MMF: 118624061(NAGA)
PPAM: 129077872(NAGA)
HAI: 109371486(NAGA)
RFQ: 117028886(NAGA)
PALE: 102887437(NAGA)
PVP: 105298028(NAGA)
RAY: 107505567(NAGA)
MJV: 108387109(NAGA)
TOD: 119247191(NAGA)
SARA: 101552815(NAGA)
SFUM: 130044862(NAGA)
LAV: 100657188(NAGA)
TMU: 101340834
ETF: 101658442(NAGA)
DNM: 101412227(NAGA)
MDO: 100018362(NAGA)
GAS: 123248507(NAGA)
SHR: 100925898(NAGA)
AFZ: 127538467
PCW: 110205858(NAGA)
TVP: 118852026(NAGA)
PBRV: 138156593(NAGA)
MLAO: 141515468(NAGA)
OAA: 100086854(NAGA)
TACU: 119936895(NAGA)
GGA: 396547(NAGA)
PCOC: 116233406(NAGA)
MGP: 100548783(NAGA)
CJO: 107313216(NAGA)
TPAI: 128073495(NAGA)
LMUT: 125703241(NAGA)
NMEL: 110391010(NAGA)
APLA: 101792497(NAGA)
ACYG: 106045224(NAGA)
CATA: 118246877(NAGA)
AFUL: 116501933(NAGA)
TGU: 100229129(NAGA)
LSR: 110483094(NAGA)
SCAN: 103813308(NAGA)
PMOA: 120510061(NAGA)
OTC: 121342303(NAGA)
PRUF: 121361071(NAGA)
ATRC: 139588081(NAGA)
GFR: 102040040(NAGA)
FAB: 101821644(NAGA)
OMA: 130262263(NAGA)
PHI: 102103812(NAGA)
PMAJ: 107204588(NAGA)
CCAE: 111934375(NAGA)
CCW: 104696358(NAGA)
CBRC: 103618258(NAGA)
ACOE: 138103930(NAGA)
ETL: 114058038(NAGA)
ZAB: 102070897(NAGA)
ZLE: 135442460(NAGA)
ACHL: 103802046(NAGA)
SVG: 106856926(NAGA)
MMEA: 130588313(NAGA)
HRT: 120751502(NAGA)
SATI: 136361706(NAGA)
CCIC: 134043645(NAGA)
FPG: 101922362(NAGA)
FCH: 102047533(NAGA)
CCRI: 104162967(NAGA)
NNT: 104407874(NAGA)
SHAB: 115605354(NAGA)
ACUN: 113491563(NAGA)
TALA: 104366462(NAGA)
ACHC: 115352699(NAGA)
HALD: 104323585(NAGA)
HLE: 104834577(NAGA)
AGEN: 126047855
HHAR: 128142721(NAGA)
GCL: 127013473
CSTI: 104560837(NAGA)
LDI: 104352511(NAGA)
MNB: 103774977(NAGA)
DPUB: 104301984(NAGA)
PPUS: 135181767(NAGA)
AVIT: 104277587(NAGA)
BRHI: 104499058(NAGA)
EGZ: 104134264(NAGA)
NNI: 104021651(NAGA)
PCRI: 104030655(NAGA)
PADL: 103915835(NAGA)
AFOR: 103907788(NAGA)
FGA: 104078318(NAGA)
GSTE: 104255667(NAGA)
CBOY: 140654526(NAGA)
CLV: 102085181
CNIC: 135993021(NAGA)
MUI: 104535829(NAGA)
PGUU: 104468446(NAGA)
PLET: 104621952(NAGA)
EHS: 104514134(NAGA)
CMAC: 104483227(NAGA)
CUCA: 104055484(NAGA)
TEO: 104383723(NAGA)
BREG: 104631008(NAGA)
OHA: 104329835(NAGA)
ACAR: 104524204
CPEA: 104387592(NAGA)
CVF: 104295511(NAGA)
RTD: 128913046(NAGA)
CRID: 134509897(NAGA)
AAM: 106488675(NAGA)
AROW: 112967690(NAGA)
NPD: 112946458(NAGA)
TGT: 104577045(NAGA)
DNE: 112984590(NAGA)
SCAM: 104137914(NAGA)
ASN: 102387946(NAGA)
AMJ: 102561061(NAGA)
CPOO: 109316752(NAGA)
GGN: 109295927(NAGA)
PSS: 102457826 102463470(NAGA)
CMY: 102938681 102948025(NAGA)
CCAY: 125629944(NAGA) 125644183
DCC: 119843756(NAGA) 119862015
CPIC: 101940500 101949244(NAGA)
TST: 117879763(NAGA) 117884012
CABI: 116824402 116828655(NAGA)
MRV: 120372978 120388241(NAGA)
ACS: 100558544(naga) 100561397
ASAO: 132776001(NAGA)
PVT: 110076094(NAGA) 110087036
SUND: 121914721 121930837(NAGA)
PBI: 103050555(NAGA) 103062412
PMUR: 107284005 107285348(NAGA)
CTIG: 120304707(NAGA) 120319293
TSR: 106537803(NAGA) 106551524
PGUT: 117655846(NAGA) 117679480
PCAE: 139319180(NAGA) 139325253
APRI: 131185380 131202690(NAGA)
PTEX: 113434142(NAGA) 113438874
NSS: 113422414 113432676(NAGA)
VKO: 123024956 123036014(NAGA)
PMUA: 114584858 114605424(NAGA)
PRAF: 128401326 128422534(NAGA)
ZVI: 118090684(NAGA) 118092720
HCG: 128326235(NAGA) 128336771
GJA: 107109285 107124086(NAGA)
STOW: 125431786 125434385(NAGA)
EMC: 129335837(NAGA) 129340610
XLA: 443592(naga.S) 443753(naga.L)
XTR: 779501(naga)
NPR: 108791730(NAGA)
RTEM: 120943521(NAGA)
ACAT: 141101771(NAGA)
BBUF: 121007375(NAGA)
BGAR: 122945688(NAGA)
DTC: 141047669(NAGA)
PWL: 138261408 138292521(NAGA)
MUO: 115475613(NAGA)
GSH: 117369301(NAGA)
DRE: 560778(naga)
SRX: 107758144(naga)
SANH: 107669032(naga)
PTET: 122333199(naga)
LROH: 127164070(naga)
GRF: 141333142(naga) 141333393
OMC: 131539690(naga)
PPRM: 120471042(naga)
RKG: 130077474(naga)
MAMB: 125245754(naga)
CIDE: 127510944
CERY: 137023731(naga)
MASI: 127435206
TROS: 130547930(naga)
TDW: 130420602(naga)
MANU: 129432337(naga)
PDAB: 135745894(naga)
IPU: 108279976
IFU: 128623414(naga)
PHYP: 113532108(naga)
SMEO: 124401815(naga)
TFD: 113645809(naga)
TVC: 132859198(naga)
NGRA: 132869569(naga)
TRN: 134313346(naga)
AMEX: 103026015(naga) 103035758
CMAO: 118797201 118812294(naga)
EEE: 113578116(naga)
CHAR: 105897611 105899535(naga)
TRU: 101073468(naga)
TFS: 130515965(naga)
PPUG: 119194579(naga) 119197929
CLUM: 117727298(naga) 117728260
CUD: 121521601(naga)
ASTR: 137613261(naga)
ONL: 100703787(naga)
OAU: 116309574(naga)
OLA: 101155483(naga)
OML: 112158553(naga)
CSAI: 133418324(naga)
XMA: 102234608(naga)
XCO: 114159062(naga)
XHE: 116734632(naga)
PRET: 103457699(naga)
PFOR: 103144121(naga)
PLAI: 106957335(naga)
PMEI: 106920818(naga)
GAF: 122825137(naga)
PPRL: 129369266(naga)
CVG: 107094481(naga)
CTUL: 119777585(naga)
GMU: 124882107(naga)
NFU: 107378045(naga)
KMR: 108247662(naga)
ALIM: 106520049(naga)
NWH: 119418143(naga)
AOCE: 111578929(naga)
EJA: 138203488(naga)
BFRE: 138636036(naga)
MCEP: 124999552(nagA)
POV: 109632473(naga)
SSEN: 122775154 122783991(naga)
SSOE: 131443876(naga) 131471437
HHIP: 117758879(naga)
HSP: 118099815(naga)
PPLT: 128460233(naga)
SMAU: 118290430(naga)
HCQ: 109523497(naga)
SSCV: 125990555(naga)
SBIA: 133496433(naga)
PEE: 133416974(naga)
PTAO: 133468203(naga)
BSPL: 114850166(naga)
SASA: 100195244(nagab) 106605016(NAGAB)
ELS: 105017628
SFM: 108929235(naga)
PKI: 111851557(naga)
LOC: 102689279(naga)
ARUT: 117418220(naga)
PSEX: 120537041(naga) 120542618
RTP: 109912737 109918425(naga)
CPLA: 122542330(naga) 122560453
LERI: 129707010 129713764(naga)
HAKA: 140719095(naga)
PMRN: 116946153(NAGA)
LRJ: 133353489(NAGA)
BFO: 118419659
BBEL: 109470720
CIN: 100182270
DME: Dmel_CG5731(CG5731) Dmel_CG7997(CG7997)
DSI: Dsimw501_GD22296(Dsim_GD22296) Dsimw501_GD25544(Dsim_GD25544)
DAN: 6496959
DPO: 6903316
DPE: 6589878
DMN: 108164177
DWI: 6642168
DGR: 6567052
DAZ: 108610423
DNV: 115563046
DHE: 111603988
DVI: 6634139
CCAT: 101452734
RZE: 108353938
AOQ: 129246425
ALUD: 128868204
MDE: 101892706
SCAC: 106085202
CVJ: 135961847
GFS: 119633318
CLON: 129608206
AGA: 1278996
ACOZ: 120960109
AARA: 120900627
ASTE: 118511646
AMAP: 126564697
AFUN: 125762438
AMOU: 128301223
AMRS: 128715895
AALI: 118457870
ACOS: 131266062
AAG: 5566514
ASUA: 134212433
CPII: 120416306
CBRI: 134829296
CNS: 116340507
BCOO: 119075334
AME: 725899
ACER: 107998803
ALAB: 122715262
ADR: 102670862
AFLR: 100868815
BIM: 100749267
BBIF: 117207441
BVK: 117241661
BVAN: 117158270
BHUN: 126870876
BTER: 100650051
BAFF: 126920854
BPYO: 122573707
BPAS: 132913296
FVI: 122534920
CCAL: 108629032
OBB: 114877136
OLG: 117609141
NMEA: 116424449
CGIG: 122395648
MPHA: 105839861
AEC: 105145873
ACEP: 105618932
ACOC: 108690135
MZT: 108726694
CCOA: 108778045
PBAR: 105432733
VEM: 105562785
COBS: 139106861
TLN: 139819087
HST: 105189481
DQU: 106748903
CFO: 105249395
FEX: 115236284
PMEC: 138936863
LHU: 105673165
PGC: 109855212
OBO: 105274738
PCF: 106786516
PFUC: 122520278
VPS: 122635643
VCRB: 124428864
VVE: 124955606
NVI: 100117222
CSOL: 105365441
TPRE: 106653074
LHT: 122498484
LBD: 127280474
MDL: 103570227
CGLO: 123262809
CTYP: 141537538
FAS: 105263599
DAM: 107042922
AGIF: 122854841
CINS: 118072878
VCAN: 122408559
CCIN: 107271861
DSM: 124412630
NPT: 124221427
NFB: 124185637
NLO: 107222644
NVG: 124308024
AROA: 105694104
TCA: 663249
TMOL: 138133381
DPA: 109533489
ESIM: 136412826
EFOR: 136343627
SOY: 115880959
AGRG: 126737000
ATD: 109601137
CSET: 123309972
HAXR: 123683960
AGB: 108903557
LDC: 111518252
DVV: 114326855
NVL: 108564677
DCOR: 135791518
APLN: 108736374
PPYR: 116168065
OTU: 111416168
BMOR: 101736031
BMAN: 114246283
MSEX: 115446055
BANY: 112054114
MJU: 123876246
NIQ: 126776831
VCD: 124537942
MCIX: 123662670
PMAC: 106720851
PPOT: 106111620
PXU: 106120756
BPHI: 137923865
PRAP: 110997336
PBX: 123711249
PNAP: 125051849
ZCE: 119837506
CCRC: 123701484
LSIN: 126970994
AAGE: 121726535
HAW: 110376691
HZE: 124635683
TNL: 113499879
SLIU: 111354373
OFU: 114351665
ONU: 135081132
ATRA: 106135541
GMW: 113512055
PXY: 105386672
PGW: 126375504
CSTB: 134747240
CFUM: 141435752
BTAB: 109031143
DCI: 103524481
CLEC: 106667230
HHAL: 106686038
MQU: 128985577
FOC: 113209723
TPAL: 117644394
FCD: 110857972
AFRA: 136038709
ISC: 8028507
VDE: 111244156
VJA: 111266613
DPTE: 113795622
DFR: 124499487
CEL: CELE_R07B7.11(gana-1)
CBR: CBG_23373(Cbr-gana-1)
BMY: BM_BM5269(Bma-gana-1)
OBI: 106872822
OSN: 115213936
LLON: 135494181
DGT: 114529372
XEN: 124453811
HMG: 100204126
HSY: 130631130
RES: 135687378
AQU: 100636085
DFA: DFA_08734
AG: BAB08149(nagA)
 » show all
Reference
PMID:9741689
  Authors
Asfaw B, Schindler D, Ledvinova J, Cerny B, Smid F, Conzelmann E
  Title
Degradation of blood group A glycolipid A-6-2 by normal and mutant human skin fibroblasts.
  Journal
J Lipid Res 39:1768-80 (1998)
  Sequence
[hsa:4668]

KEGG   ENZYME: 3.2.1.49
Entry
EC 3.2.1.49                 Enzyme                                 
Name
alpha-N-acetylgalactosaminidase;
alpha-acetylgalactosaminidase;
N-acetyl-alpha-D-galactosaminidase;
N-acetyl-alpha-galactosaminidase;
alpha-NAGAL;
alpha-NAGA;
alpha-GalNAcase
Class
Hydrolases;
Glycosylases;
Glycosidases, i.e. enzymes that hydrolyse O- and S-glycosyl compounds
Sysname
alpha-N-acetyl-D-galactosaminide N-acetylgalactosaminohydrolase
Reaction(IUBMB)
Cleavage of non-reducing alpha-(1->3)-N-acetylgalactosamine residues from human blood group A and AB mucin glycoproteins, Forssman hapten and blood group A lacto series glycolipids
Reaction(KEGG)
(other) R04183 R05966(G)
Comment
The human lysosomal enzyme is involved in the degradation of blood type A epitope.
History
EC 3.2.1.49 created 1972, modified 2011
Pathway
ec00603  Glycosphingolipid biosynthesis - globo and isoglobo series
ec01100  Metabolic pathways
Orthology
K01204  alpha-N-acetylgalactosaminidase
Genes
HSA4668(NAGA)
PTR470279(NAGA)
PPS100991597(NAGA)
GGO101132690(NAGA)
PON100450338(NAGA)
PPYG129023331(NAGA)
NLE100605546(NAGA)
HMH116458803(NAGA)
SSYN129468048(NAGA)
MCC713068(NAGA)
MCF102145379(NAGA)
MTHB126963611
MNI105464355(NAGA)
CSAB103223407(NAGA)
CATY105572167(NAGA)
PANU101016466(NAGA)
TGE112633355(NAGA)
MLEU105538807(NAGA)
RRO104670530(NAGA)
RBB108543578(NAGA)
TFN117096393(NAGA)
PTEH111548936(NAGA)
CANG105514017(NAGA)
CJC100397642(NAGA)
SBQ101052589(NAGA)
CIMI108290476(NAGA)
ANAN105733965(NAGA) 135268078 135271262
CSYR103264351(NAGA)
MMUR105858599(NAGA)
LCAT123640287(NAGA)
PCOQ105805270(NAGA)
OGA100954557(NAGA)
MMU17939(Naga)
MCAL110310380(Naga)
MPAH110334850(Naga)
RNO315165(Naga)
MCOC116076661(Naga)
ANU117719166(Naga)
ASYL127668213(Naga)
MUN110554096(Naga)
CGE100751670(Naga)
MAUA101840437(Naga)
PROB127225858(Naga)
PLEU114694320(Naga)
MORG121461193(Naga)
MFOT126515716
AAMP119823607(Naga)
NGI103743459(Naga)
HGL101726122(Naga)
CPOC100719787(Naga)
CCAN109689379(Naga)
DORD105992105(Naga)
DSP122123599(Naga)
DMER138811810(Naga) 138829787
PLOP125357570(Naga)
NCAR124982310
MMMA107155833(Naga)
ITI101959382(Naga)
OCU100350048
OPI101536106(NAGA)
TUP102490461(NAGA)
GVR103591795(NAGA)
CFA481226(NAGA)
CLUD112666708(NAGA)
VVP112934013(NAGA)
VLG121492200(NAGA)
NPO129512102(NAGA)
AML100471467(NAGA)
UMR103674070(NAGA)
UAH113241706(NAGA)
UAR123780544(NAGA)
ELK111157598
LLV125106372
MPUF101673551(NAGA)
MNP132019160(NAGA)
MLK131839557(NAGA)
NVS122892575(NAGA)
ORO101381151(NAGA)
EJU114218390(NAGA)
ZCA113922578(NAGA)
MLX117998614(NAGA)
NSU110578239(NAGA)
LWW102738869(NAGA)
FCA101083277(NAGA)
PYU121040244(NAGA)
PCOO112863480(NAGA)
PBG122472839(NAGA)
PVIV125171045(NAGA)
LRUF124502033
LGF123590449(NAGA)
AJU106979923
PTG102963636(NAGA)
PPAD109265652(NAGA)
PUC125920377
PLEZ122225203(NAGA)
HHV120235028(NAGA)
BTA533357(NAGA)
BOM102280167(NAGA)
BIU109559874(NAGA)
BBUB102404704(NAGA)
BBIS104991253(NAGA)
CHX102170679(NAGA)
OAS100145858(NAGA)
BTAX128047737(NAGA)
CSUM138078008(NAGA)
ODA120857579(NAGA)
CCAD122423544(NAGA)
MREE136174649(NAGA)
OVR110127013(NAGA)
MBEZ129536613(NAGA)
SSC100142667(NAGA)
CFR102511662(NAGA)
CBAI105073060(NAGA)
CDK105091882(NAGA)
VPC102541563(NAGA)
BACU103005673(NAGA)
BMUS118901630(NAGA)
LVE103072389(NAGA)
OOR101272207(NAGA)
LALB132528992(NAGA)
GMF115852722(NAGA)
DDP132434125(NAGA)
DLE111186345(NAGA)
PCAD102973583(NAGA)
PSIU116760277(NAGA)
PPHC136130641(NAGA)
NASI112394634(NAGA)
ECB100070793(NAGA)
EPZ103541990(NAGA)
EAI106848492(NAGA)
MYB102258282(NAGA)
MYD102754122(NAGA)
MMYO118651848(NAGA)
MLF102422016(NAGA)
MDT132225822(NAGA)
MYUM139007621(NAGA)
PKL118712063(NAGA)
EFUS103288815(NAGA)
MNA107534967(NAGA)
DRO112321929(NAGA)
SHON119002460(NAGA)
AJM119060491(NAGA)
PDIC114513182(NAGA)
PHAS123816241(NAGA)
MMF118624061(NAGA)
PPAM129077872(NAGA)
HAI109371486(NAGA)
RFQ117028886(NAGA)
PALE102887437(NAGA)
PVP105298028(NAGA)
RAY107505567(NAGA)
MJV108387109(NAGA)
TOD119247191(NAGA)
SARA101552815(NAGA)
SFUM130044862(NAGA)
SETR126006265 126006909 126006910
LAV100657188(NAGA)
TMU101340834
ETF101658442(NAGA)
DNM101412227(NAGA)
MDO100018362(NAGA)
GAS123248507(NAGA)
SHR100925898(NAGA)
AFZ127538467
PCW110205858(NAGA)
TVP118852026(NAGA)
PBRV138156593(NAGA)
MLAO141515468(NAGA)
OAA100086854(NAGA)
TACU119936895(NAGA)
GGA396547(NAGA)
PCOC116233406(NAGA)
MGP100548783(NAGA)
CJO107313216(NAGA)
TPAI128073495(NAGA)
LMUT125703241(NAGA)
NMEL110391010(NAGA)
APLA101792497(NAGA)
ACYG106045224(NAGA)
CATA118246877(NAGA)
AFUL116501933(NAGA)
TGU100229129(NAGA)
LSR110483094(NAGA)
SCAN103813308(NAGA)
PMOA120510061(NAGA)
OTC121342303(NAGA)
PRUF121361071(NAGA)
ATRC139588081(NAGA)
GFR102040040(NAGA)
FAB101821644(NAGA)
OMA130262263(NAGA)
PHI102103812(NAGA)
PMAJ107204588(NAGA)
CCAE111934375(NAGA)
CCW104696358(NAGA)
CBRC103618258(NAGA)
ACOE138103930(NAGA)
ETL114058038(NAGA)
ZAB102070897(NAGA)
ZLE135442460(NAGA)
ACHL103802046(NAGA)
SVG106856926(NAGA)
MMEA130588313(NAGA)
HRT120751502(NAGA)
SATI136361706(NAGA)
CCIC134043645(NAGA)
FPG101922362(NAGA)
FCH102047533(NAGA)
CCRI104162967(NAGA)
NNT104407874(NAGA)
SHAB115605354(NAGA)
ACUN113491563(NAGA)
TALA104366462(NAGA)
ACHC115352699(NAGA)
HALD104323585(NAGA)
HLE104834577(NAGA)
AGEN126047855
HHAR128142721(NAGA)
GCL127013473
CSTI104560837(NAGA)
LDI104352511(NAGA)
MNB103774977(NAGA)
DPUB104301984(NAGA)
PPUS135181767(NAGA)
AVIT104277587(NAGA)
BRHI104499058(NAGA)
EGZ104134264(NAGA)
NNI104021651(NAGA)
PCRI104030655(NAGA)
PADL103915835(NAGA)
AFOR103907788(NAGA)
FGA104078318(NAGA)
GSTE104255667(NAGA)
CBOY140654526(NAGA)
CLV102085181
CNIC135993021(NAGA)
MUI104535829(NAGA)
PGUU104468446(NAGA)
PLET104621952(NAGA)
EHS104514134(NAGA)
CMAC104483227(NAGA)
CUCA104055484(NAGA)
TEO104383723(NAGA)
BREG104631008(NAGA)
OHA104329835(NAGA)
ACAR104524204
CPEA104387592(NAGA)
CVF104295511(NAGA)
RTD128913046(NAGA)
CRID134509897(NAGA)
AAM106488675(NAGA)
AROW112967690(NAGA)
NPD112946458(NAGA)
TGT104577045(NAGA)
DNE112984590(NAGA)
SCAM104137914(NAGA)
ASN102387946(NAGA)
AMJ102561061(NAGA)
CPOO109316752(NAGA)
GGN109295927(NAGA)
PSS102457826 102463470(NAGA)
CMY102938681 102948025(NAGA)
CCAY125629944(NAGA) 125644183
DCC119843756(NAGA) 119862015
CPIC101940500 101949244(NAGA)
TST117879763(NAGA) 117884012
CABI116824402 116828655(NAGA)
MRV120372978 120388241(NAGA)
ACS100558544(naga) 100561397
ASAO132776001(NAGA)
PVT110076094(NAGA) 110087036
SUND121914721 121930837(NAGA)
PBI103050555(NAGA) 103062412
PMUR107284005 107285348(NAGA)
CTIG120304707(NAGA) 120319293
TSR106537803(NAGA) 106551524
PGUT117655846(NAGA) 117679480
PCAE139319180(NAGA) 139325253
APRI131185380 131202690(NAGA)
PTEX113434142(NAGA) 113438874
NSS113422414 113432676(NAGA)
VKO123024956 123036014(NAGA)
PMUA114584858 114605424(NAGA)
PRAF128401326 128422534(NAGA)
ZVI118090684(NAGA) 118092720
HCG128326235(NAGA) 128336771
GJA107109285 107124086(NAGA)
STOW125431786 125434385(NAGA)
EMC129335837(NAGA) 129340610
XLA443592(naga.S) 443753(naga.L)
XTR779501(naga)
NPR108791730(NAGA)
RTEM120943521(NAGA)
ACAT141101771(NAGA)
BBUF121007375(NAGA)
BGAR122945688(NAGA)
DTC141047669(NAGA)
PWL138261408 138292521(NAGA)
MUO115475613(NAGA)
GSH117369301(NAGA)
DRE560778(naga)
SRX107758144(naga)
SANH107669032(naga)
SGH107572590 107577412
CCAR109044975 109044979
CAUA113048520 113048521 113064738
CGIB127956248 127979701 128028905
PTET122333199(naga)
LROH127164070(naga)
GRF141333142(naga) 141333393
OMC131539690(naga)
PPRM120471042(naga)
RKG130077474(naga)
MAMB125245754(naga)
CIDE127510944
CERY137023731(naga)
MASI127435206
TROS130547930(naga)
TDW130420602(naga)
MANU129432337(naga)
PDAB135745894(naga)
IPU108279976
IFU128623414(naga)
PHYP113532108(naga)
SMEO124401815(naga)
TFD113645809(naga)
TVC132859198(naga)
CGAR128534111 128534294
NGRA132869569(naga)
TRN134313346(naga)
AMEX103026015(naga) 103035758
CMAO118797201 118812294(naga)
EEE113578116(naga)
CHAR105897611 105899535(naga)
SPIL134082471 134098139
TRU101073468(naga)
TFS130515965(naga)
TNGGSTEN00012743G001
LCO104925622 104939011
NCC104944830 104959892
TBEN117470771 117492290
CGOB115004066 115021387
PGEO117440179 117460966
GACU117538563 117555312
EMAC134861971 134876459
ELY117266424 117271065
EFO125892867 125896852
PLEP121946152 121955894
SLUC116064585 116066291
ECRA117946601 117961153
ESP116699433 116706565
PFLV114557187 114572938
GAT120808355 120810359
PPUG119194579(naga) 119197929
AFB129106998 129110261
CLUM117727298(naga) 117728260
PSWI130202419 130206474
CANA137780942 137785617
CVE137871174 137891583
MSAM119887973 119898153 119909038
SCHU122863353 122881650
CUD121521601(naga)
SPUL138584327 138584367
LMIX132983311 132985078
ALAT119005321 119012882
ASTR137613261(naga)
MZE101471811 105940732
ONL100703787(naga)
OAU116309574(naga)
OLA101155483(naga)
OML112158553(naga)
CSAI133418324(naga)
XMA102234608(naga)
XCO114159062(naga)
XHE116734632(naga)
PRET103457699(naga)
PFOR103144121(naga)
PLAI106957335(naga)
PMEI106920818(naga)
GAF122825137(naga)
PPRL129369266(naga)
CVG107094481(naga)
CTUL119777585(naga)
GMU124882107(naga)
NFU107378045(naga)
KMR108247662(naga)
ALIM106520049(naga)
NWH119418143(naga)
AOCE111578929(naga)
EJA138203488(naga)
BFRE138636036(naga)
MCEP124999552(nagA)
CSEM103380792 103388750
POV109632473(naga)
SSEN122775154 122783991(naga)
SSOE131443876(naga) 131471437
HHIP117758879(naga)
HSP118099815(naga)
PPLT128460233(naga)
SMAU118290430(naga)
LCF108886088 108896867
SDU111227730 111239406
SLAL111664120 111672770
XGL120784719 120789171 120789172
HCQ109523497(naga)
SSCV125990555(naga)
SBIA133496433(naga)
PEE133416974(naga)
PTAO133468203(naga)
BPEC110159082 110170156
ENY140356414 140374477
MALB109973040 109973819
BSPL114850166(naga)
SJO128365748 128376941
SSCO133983718 133997511
GMH115534579 115553883
SASA100195244(nagab) 106605016(NAGAB)
STRU115174693 115175520
OTW112223180 112250394
OMY110490166 110529695
OGO123991645 123997615
ONE115107842 115141424
OKI109900822 109902229
OKE118364173 118367570 118398576
OMM135505886 135521214 135522508
OCLA139367320 139405971 139415614
SALP111954345 111965311
SNH120024125 120047526
CCLU121542471 121552400 121585419
ELS105017628
OEP134024016 134025185
SFM108929235(naga)
PKI111851557(naga)
AANG118220561 118230805
AROT135256901 135258500
CCOG133128569 133135397
LOC102689279(naga)
PSPA121300536 121306145(naga) 121330809
ARUT117418220(naga)
PSEX120537041(naga) 120542618
LCM102361487 102366389
RTP109912737 109918425(naga)
CPLA122542330(naga) 122560453
HOC132825571 132831162
LERI129707010 129713764(naga)
HAKA140719095(naga)
PMRN116946153(NAGA)
LRJ133353489(NAGA)
BFO118419659
BBEL109470720
CIN100182270
SCLV120335584 120335840 120335841 120336669 120336670 120336671
SPU581755 587840
LPIC129260745 129260747
AJJ139979989 139980030
APLC110979801 110983724 110983725 110983726
ARUN117293333 117293334 117293335 117305520
AAMU139935746 139935948 139935950 139935951
AFIL140161127 140161128 140161129 140161130
AJC117108823 117108824
SKO100372870 100373018 100374673
PFLL139121080 139121081
DMEDmel_CG5731(CG5731) Dmel_CG7997(CG7997)
DER6543326 6548681
DSE6609435 6611926
DSIDsimw501_GD22296(Dsim_GD22296) Dsimw501_GD25544(Dsim_GD25544)
DYADyak_GE14068 Dyak_GE26351
DAN6496959
DSR110181534 110183385
DPO6903316
DPE6589878
DMN108164177
DWI6642168
DGR6567052
DMODmoj_GI17617
DAZ108610423
DNV115563046
DHE111603988
DVI6634139
CCAT101452734
RZE108353938
AOQ129246425
ALUD128868204
TDA119662124 119679041
MDE101892706
SCAC106085202
CVJ135961847
GFS119633318
ECOE129948874 129950991
CLON129608206
HIS119659042 119660415
AGA1278996
ACOZ120960109
AARA120900627
AMER121597641 121601729
ASTE118511646
AMAP126564697
AFUN125762438
AMOU128301223
AMRS128715895
AALI118457870
ACOS131266062
AAG5566514
AALB109409620 109413741
ASUA134212433
CQUCpipJ_CPIJ005600
CPII120416306
CBRI134829296
CNS116340507
BCOO119075334
LLL129789909 129791058
PPAP129805710 129808275
AME725899
ACER107998803
ALAB122715262
ADR102670862
AFLR100868815
BIM100749267
BBIF117207441
BVK117241661
BVAN117158270
BHUN126870876
BTER100650051
BAFF126920854
BPYO122573707
BPAS132913296
FVI122534920
CCAL108629032
OBB114877136
OLG117609141
MGEN117220488 117228319
NMEA116424449
CGIG122395648
SOC105208200 105208212
MPHA105839861
AEC105145873
ACEP105618932
ACOC108690135
MZT108726694
CCOA108778045
PBAR105432733
VEM105562785
COBS139106861
TLN139819087
HST105189481
DQU106748903
CFO105249395
FEX115236284
PMEC138936863
LHU105673165
PGC109855212
OBO105274738
PCF106786516
PFUC122520278
VPS122635643
VCRB124428864
VVE124955606
NVI100117222
CSOL105365441
TPRE106653074
LHT122498484
LBD127280474
MDL103570227
CGLO123262809
CTYP141537538
FAS105263599
DAM107042922
AGIF122854841
CINS118072878
VCAN122408559
CCIN107271861
DSM124412630
NPT124221427
NFB124185637
NLO107222644
NVG124308024
AROA105694104
TCA663249
TMOL138133381
DPA109533489
ESIM136412826
EFOR136343627
SOY115880959
AGRG126737000
ATD109601137
CSET123309972
HAXR123683960
AGB108903557
LDC111518252
DVV114326855
NVL108564677
DCOR135791518
APLN108736374
PPYR116168065
OTU111416168
BMOR101736031
BMAN114246283
MSEX115446055
DPLKGM_213240
BANY112054114
MJU123876246
NIQ126776831
VCD124537942
MCIX123662670
PMAC106720851
PPOT106111620
PXU106120756
BPHI137923865
PRAP110997336
PBX123711249
PNAP125051849
ZCE119837506
CCRC123701484
LSIN126970994
AAGE121726535
HAW110376691
HZE124635683
TNL113499879
SLIU111354373
OFU114351665
ONU135081132
ATRA106135541
GMW113512055
PXY105386672
PGW126375504
CSTB134747240
CFUM141435752
CFEL113377030 113387868 113387869 113388479 113388482
CCRN123291385 123297787 123299189
API100161159 100161679 100163871 100168844
DNX107163389 107166489 107170563 107171670
AGS114123152 114129670 114129775
RMD113550049 113550417 113555041
ACOO126838058 126841779 126846159
DVT126896684 126902618 126908660 126909271
BTAB109031143
DCI103524481
CLEC106667230
HHAL106686038
NLU111052906 111059935
HVI124357487 124357508
MQU128985577
PHUPhum_PHUM061380 Phum_PHUM476700 Phum_PHUM476710
FOC113209723
TPAL117644394
ZNE110833303 110833336
CSEC111868046 111869442
PAME138698397 138698400
SGRE126281182 126281183
BROR134534230 134534231
IEL124162004 124162418
HAMR139697665 139697811
FCD110857972
DPXDAPPUDRAFT_309394 DAPPUDRAFT_309434
DMK116924432 116931840
DPZ124347915 124349292
AFRA136038709
PVM113810366 113821065
PJA122251463 122266112
PCHN125044678 125044716
PMOO119582586 119582834
HAME121859550 121870400
PCLA123745643 123757610
CQD128697416 128697418
PTRU123500089 123513846
ESN127004553 127007411
MNZ135208396 135212602 135219552 135225671
MRJ136832568 136848155
PORN139745672 139767417
HAZT108666989 108666993
EAF111696100 111702601
LSM121117202 121132043
TCF131878514 131888348
PPOI119090892 119090896 119092962
ISC8028507
DSV119448283 119449552 119449553 119449557 119449859
RSAN119382560 119382561 119382562 119382563 119382759
RMP119170107 119179705 119179714 119179725 119179740
VDE111244156
VJA111266613
GOE100897761 100898048 100902273
TUT107359742 107371157
DPTE113795622
DFR124499487
CSCU111637616 111637617 111639968
CVS136975082 136988730
PTEP107442827 107457045
ABRU129958128 129960516 129961831
UDV129218094 129224581 129231582
SDM118184115 118192968 118202592
LPOL106460381 106472165
PMEO129584925 129597038
CELCELE_R07B7.11(gana-1)
CBRCBG_23373(Cbr-gana-1)
CRQGCK72_018182
NAINECAME_03019
BMYBM_BM5269(Bma-gana-1)
LOALOAG_00060
TSPTsp_02508 Tsp_02909
HROHELRODRAFT_111560 HELRODRAFT_182706
LGILOTGIDRAFT_158234 LOTGIDRAFT_178842 LOTGIDRAFT_209340 LOTGIDRAFT_235899
PVUL126828049 126829285 126830080 126830191 126830438 126830492
PCAN112559739 112560249 112560712 112560713 112560714 112560715
LSAX138968248 138968693 138968760 138968795 138968888 138969313 138969314 138969315
BGT106057326 106057369 106057370
GAE121374342 121374920 121376150 121376283 121376303
HRF124119945 124129757 124139615 124139616 124139617 124139618 124143661 124148129 124148132 124148942 124148995 124148997 124148998 125371717
HRJ124256424 124256433 124256435 124256437 124256447 124256448 124256450 124280219 124280221 124280222 124280223 124280224 124280226 124283107 124283108 124283138 124283487
HASI137272553 137272556 137272558 137272559 137272844 137274254 137274255 137274256 137274259 137274411 137274604 137274605
HCRA139449344 139449545 139449560 139449587 139449798 139449799 139449845 139451099 139472979 139472989 139472990 139472991 139473042
CRG105326821 105331657 105339434
CANU128157076 128184593 128192440
CVN111104087 111104138 111125097 111125814
OED125673347 125682476
MYI110454106 110454114 110459235 110465170
PMAX117328990 117328994 117329669
AIRR138304654 138328120 138328427 138328429
MCAF127714304 127716492 127726257 127732872
MMER123556288 123556509 123556588 123557012 123557021 123557150 123557151 123557964
RPHI132717197 132717447 132721887 132721890 132722113 132729233 132731067 132731918 132738372 132753260
DPOL127842635 127878981
MAEA128225607 128226390 128227368 128227597 128228203 128228670
OBI106872822
OSN115213936
LJP135471010 135471544 135472197 135473091 135473408
LAK106173465 106177951
SMMSmp_170830 Smp_179260
LLON135494181
NVE116608331 5498815 5501245 5508946 5513905
EPA110243080 110243193
ATEN116299918 116299920 116299921
ADF107330554 107331315 107334325 107334332
AMIL114958680 114958713 114968339 114968344
MCAZ138038485 138038590 138038593 138038594 138038632
MFOO137992174 137992278 137992280 137992281 137992305
PDAM113672638 113672725 113681613 113681615
SPIS111321754 111340747 111340767
DGT114529372
XEN124453811
HMG100204126
HSY130631130
RES135687378
TADTRIADDRAFT_23253
AQU100636085
DDIDDB_G0291524
DPPDICPUDRAFT_58841
DFADFA_08734
ACANACA1_257940
TETTTHERM_00136050
EHXEMIHUDRAFT_205415 EMIHUDRAFT_460708
 » show all
Reference
1  [PMID:9741689]
  Authors
Asfaw B, Schindler D, Ledvinova J, Cerny B, Smid F, Conzelmann E
  Title
Degradation of blood group A glycolipid A-6-2 by normal and mutant human skin fibroblasts.
  Journal
J Lipid Res 39:1768-80 (1998)
  Sequence
[hsa:4668]
Reference
2  [PMID:8954893]
  Authors
Zhu A, Monahan C, Wang ZK, Goldstein J
  Title
Expression, purification, and characterization of recombinant alpha-N-acetylgalactosaminidase produced in the yeast Pichia pastoris.
  Journal
Protein Expr Purif 8:456-62 (1996)
DOI:10.1006/prep.1996.0124
Reference
3  [PMID:19683538]
  Authors
Clark NE, Garman SC
  Title
The 1.9 a structure of human alpha-N-acetylgalactosaminidase: The molecular basis of Schindler and Kanzaki diseases.
  Journal
J Mol Biol 393:435-47 (2009)
DOI:10.1016/j.jmb.2009.08.021
  Sequence
[hsa:4668]
Reference
4  [PMID:9065462]
  Authors
Hoskins LC, Boulding ET, Larson G
  Title
Purification and characterization of blood group A-degrading isoforms of alpha-N-acetylgalactosaminidase from Ruminococcus torques strain IX-70.
  Journal
J Biol Chem 272:7932-9 (1997)
DOI:10.1074/jbc.272.12.7932
Reference
5  [PMID:20139603]
  Authors
Harun-Or-Rashid M, Matsuzawa T, Satoh Y, Shiraishi T, Ando M, Sadik G, Uda Y
  Title
Purification and characterization of alpha-N-acetylgalactosaminidases I and II from the starfish Asterina amurensis.
  Journal
Biosci Biotechnol Biochem 74:256-61 (2010)
DOI:10.1271/bbb.90178
Reference
6  [PMID:18443780]
  Authors
Weignerova L, Filipi T, Manglova D, Kren V
  Title
Induction, purification and characterization of alpha-N-acetylgalactosaminidase from Aspergillus Niger.
  Journal
Appl Microbiol Biotechnol 79:769-74 (2008)
DOI:10.1007/s00253-008-1485-3
Reference
7  [PMID:11368317]
  Authors
Ashida H, Tamaki H, Fujimoto T, Yamamoto K, Kumagai H
  Title
Molecular cloning of cDNA encoding alpha-N-acetylgalactosaminidase from Acremonium sp. and its expression in yeast.
  Journal
Arch Biochem Biophys 384:305-10 (2000)
DOI:10.1006/abbi.2000.2114
  Sequence
Other DBs
ExplorEnz - The Enzyme Database: 3.2.1.49
IUBMB Enzyme Nomenclature: 3.2.1.49
ExPASy - ENZYME nomenclature database: 3.2.1.49
BRENDA, the Enzyme Database: 3.2.1.49
CAS: 9075-63-2

KEGG   REACTION: R05966
Entry
R05966                      Reaction                               
Definition
H2O + Forssman antigen <=> N-Acetyl-D-galactosamine + Globoside
Equation
Remark
Same as: R04183
Enzyme
Pathway
rn00603  Glycosphingolipid biosynthesis - globo and isoglobo series
rn01100  Metabolic pathways
Brite
Enzymatic reactions [BR:br08201]
 3. Hydrolase reactions
  3.2  Glycosylases
   3.2.1  Glycosidases, i.e. enzymes that hydrolyse O- and S-glycosyl compounds
    3.2.1.49
     R05966  H2O + Forssman antigen <=> N-Acetyl-D-galactosamine + Globoside
Orthology
K01204  alpha-N-acetylgalactosaminidase [EC:3.2.1.49]

  All links  
No link information was found.   
DBGET integrated database retrieval system