KEGG   NETWORK: N00856
Entry
N00856                      Network                                
Name
Isoleucine degradation
Definition
2-MB-CoA -- (ACADS,ACADSB,ACADM) >> (ECHS1,HADHA) >> (HSD17B10,HADH) >> (ACAA1/2,HADHB) -> Propanoyl-CoA
  Expanded
C15980 -- (35,36,34) >> (1892,3030) >> (3028,3033) >> (30,10449,3032) -> C00100
Class
nt06024 Valine, leucine and isoleucine degradation
Type
Reference
Pathway
hsa00280  Valine, leucine and isoleucine degradation
Gene
35  ACADS; acyl-CoA dehydrogenase short chain
36  ACADSB; acyl-CoA dehydrogenase short/branched chain
34  ACADM; acyl-CoA dehydrogenase medium chain
1892  ECHS1; enoyl-CoA hydratase, short chain 1
3030  HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
3028  HSD17B10; hydroxysteroid 17-beta dehydrogenase 10
3033  HADH; hydroxyacyl-CoA dehydrogenase
30  ACAA1; acetyl-CoA acyltransferase 1
10449  ACAA2; acetyl-CoA acyltransferase 2
3032  HADHB; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
Metabolite
C15980  (S)-2-Methylbutanoyl-CoA
C00100  Propanoyl-CoA

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