Infantile hepatic hemangioma (IHH), although rare, is the most common benign hepatic vascular tumor in the first year of age. They are sub-classified in focal, multiple and diffuse lesions, based on degree of unaffected liver parenchyma. Most lesions are clinically silent and self-limiting, whereas others can become symptomatic, manifesting as cardiac failure, fulminant hepatic failure and abdominal compartment syndrome. The term IHH is preferred to "hemangioendothelioma" because the clinical and biologic behavior is similar to infantile hemangiomas [DS:H01482] that affect the skin and other parts of the body.
Category
Neoplasm
Brite
Human diseases in ICD-11 classification [BR:br08403]
02 Neoplasms
Benign neoplasms, except of lymphoid, haematopoietic, central nervous system or related tissues
Benign mesenchymal neoplasms
2E81 Benign vascular neoplasms
H01875 Infantile hepatic hemangioma
