Entry
Name
N-acetylglucosaminyl-proteoglycan 4-beta-glucuronosyltransferase;
N-acetylglucosaminylproteoglycan beta-1,4-glucuronyltransferase;
heparan glucuronyltransferase II
Class
Transferases;
Glycosyltransferases;
Hexosyltransferases
BRITE hierarchy
Sysname
UDP-alpha-D-glucuronate:N-acetyl-alpha-D-glucosaminyl-(1->4)-beta-D-glucuronosyl-proteoglycan 4-beta-glucuronosyltransferase
Reaction(IUBMB)
UDP-alpha-D-glucuronate + N-acetyl-alpha-D-glucosaminyl-(1->4)-beta-D-glucuronosyl-proteoglycan = UDP + beta-D-glucuronosyl-(1->4)-N-acetyl-alpha-D-glucosaminyl-(1->4)-beta-D-glucuronosyl-proteoglycan [RN:
R07335 ]
Reaction(KEGG)
Substrate
UDP-alpha-D-glucuronate [CPD:
C00167 ];
N-acetyl-alpha-D-glucosaminyl-(1->4)-beta-D-glucuronosyl-proteoglycan
Product
UDP [CPD:
C00015 ];
beta-D-glucuronosyl-(1->4)-N-acetyl-alpha-D-glucosaminyl-(1->4)-beta-D-glucuronosyl-proteoglycan
Comment
Involved in the biosynthesis of heparin and heparan sulfate. Some forms of the human enzyme (particularly the enzyme complex encoded by the EXT1 and EXT2 genes) act as bifunctional glycosyltransferases, which also have the glucuronosyl-N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase (EC
2.4.1.224 ) activity required for the synthesis of the heparan sulfate disaccharide repeats.
History
EC 2.4.1.225 created 2002
Pathway
ec00534 Glycosaminoglycan biosynthesis - heparan sulfate / heparin
Orthology
K02366 glucuronyl/N-acetylglucosaminyl transferase EXT1
K02367 glucuronyl/N-acetylglucosaminyl transferase EXT2
Genes
HSA : 2131(EXT1) 2132(EXT2)
PTR : 107976420(EXT1) 451140(EXT2)
PPS : 100975712(EXT2) 100985695(EXT1)
GGO : 101130563(EXT2) 109025298(EXT1)
PON : 100172450(EXT1) 100436160(EXT2)
NLE : 100597702(EXT1) 100604250(EXT2)
HMH : 116476325 116813541(EXT1)
MCC : 701488(EXT1) 715975(EXT2)
MCF : 101926231(EXT1) 102136104(EXT2)
MTHB : 126936267 126961556
MNI : 105468540(EXT1) 105471617(EXT2)
CSAB : 103236980 103237338(EXT1)
CATY : 105584539(EXT1) 105586840(EXT2)
PANU : 100137439(EXT1) 101019229(EXT2) 116272456 116272614
TGE : 112606187(EXT2) 112629920(EXT1)
MLEU : 105529083 105554777(EXT2)
RRO : 104658897(EXT1) 104673882(EXT2)
RBB : 108519255(EXT2) 108536176(EXT1)
TFN : 117079472(EXT1) 117081393(EXT2)
PTEH : 111544934(EXT2) 111551020(EXT1)
CANG : 105511053(EXT1) 105527086(EXT2)
CJC : 100386964(EXT1) 100400679(EXT2)
SBQ : 101039408(EXT2) 101053444(EXT1)
CIMI : 108304907(EXT2) 108305915(EXT1)
CSYR : 103260803 103263660 103264178 103272774
MMUR : 105863703(EXT1) 105885490(EXT2)
LCAT : 123642622(EXT2) 123645168(EXT1)
PCOQ : 105812176(EXT1) 105819145(EXT2)
OGA : 100943601(EXT1) 100949922(EXT2)
MMU : 14042(Ext1) 14043(Ext2)
MCAL : 110310432(Ext1) 110311448(Ext2)
MPAH : 110317782(Ext2) 110334870(Ext1)
RNO : 299907(Ext1) 311215(Ext2)
MCOC : 116082489(Ext1) 116090518(Ext2)
MUN : 110540376(Ext2) 110559447 110559448
CGE : 100689334(Ext1) 100751585(Ext2)
MAUA : 101826524(Ext1) 101842118(Ext2)
PROB : 127222213(Ext2) 127235391(Ext1)
PLEU : 114694845(Ext1) 114699729(Ext2)
MORG : 121440558(Ext2) 121461166(Ext1)
MFOT : 126491860 126504517
AAMP : 119814179(Ext2) 119822782(Ext1)
NGI : 103738135(Ext1) 103751554(Ext2)
HGL : 101706257(Ext1) 101715817(Ext2)
CPOC : 100712625(Ext2) 100716132(Ext1)
CCAN : 109686418 109702003
DORD : 105996073(Ext2) 105997725(Ext1)
DSP : 122100734(Ext2) 122102360(Ext1)
NCAR : 124960112 124981119
OPI : 101535829(EXT1) 101536088(EXT2)
TUP : 102467803(EXT1) 102487057(EXT2)
GVR : 103591115(EXT1) 103596582(EXT2)
CFA : 475989(EXT2) 482024(EXT1)
CLUD : 112662087(EXT1) 112663258(EXT2)
VVP : 112915941(EXT1) 112924118(EXT2)
VLG : 121498758(EXT1) 121501521(EXT2)
AML : 100465258(EXT1) 105242037(EXT2)
UMR : 103661582(EXT1) 103672344(EXT2)
UAH : 113252791(EXT1) 113265011(EXT2)
UAR : 123797768(EXT1) 123799595(EXT2)
MPUF : 101672930(EXT2) 101691546(EXT1)
NVS : 122904351(EXT1) 122912861(EXT2)
ORO : 101366478(EXT2) 101382133(EXT1)
EJU : 114199089(EXT1) 114215287(EXT2)
ZCA : 113914556(EXT2) 113931105(EXT1)
MLX : 118015150(EXT1) 118015783(EXT2)
NSU : 110576283(EXT2) 110579220(EXT1)
LWW : 102741200(EXT1) 102744900(EXT2)
FCA : 101081362(EXT1) 101083620(EXT2)
PYU : 121042894(EXT1) 121043515(EXT2)
PCOO : 112859477(EXT1) 112865217(EXT2)
PBG : 122483728(EXT2) 122495739(EXT1)
LRUF : 124504734 124507771
PTG : 102964333(EXT2) 102968916(EXT1)
PPAD : 109273237(EXT1) 109279210 109279211(EXT2)
AJU : 106975536(EXT1) 106978049(EXT2)
HHV : 120228461(EXT2) 120228668(EXT1)
BTA : 281151(EXT2) 538602(EXT1)
BOM : 102275740(EXT2) 102280308(EXT1)
BIU : 109568471(EXT1) 109569634(EXT2)
BBUB : 102389161(EXT2) 102407802(EXT1)
BBIS : 104982778(EXT2) 105005436(EXT1)
CHX : 102182243(EXT2) 102182809(EXT1)
OAS : 101110867(EXT2) 101114877(EXT1)
ODA : 120860718 120876908(EXT2) 120878901(EXT1)
CCAD : 122449196(EXT2) 122450981(EXT1)
SSC : 100157655(EXT1) 100522362(EXT2)
CFR : 102508456(EXT1) 102514905(EXT2)
CBAI : 105076487(EXT2) 105082972(EXT1)
CDK : 105096148(EXT1) 105106838(EXT2)
VPC : 102535018(EXT1) 102542570(EXT2)
BACU : 102999728(EXT2) 103019432(EXT1)
LVE : 103078738(EXT1) 103091009(EXT2)
OOR : 101280958(EXT2) 101286251(EXT1)
DLE : 111165183(EXT1) 111184011(EXT2)
PCAD : 102979294 102980097(EXT1)
PSIU : 116742524(EXT1) 116758175(EXT2)
NASI : 112397180(EXT1) 112402430(EXT2)
ECB : 100055879(EXT2) 100056983(EXT1)
EPZ : 103549478(EXT1) 103556459(EXT2)
EAI : 106839736(EXT1) 106843971(EXT2)
MYB : 102238781(EXT2) 102244714(EXT1)
MYD : 102765321(EXT1) 102767712(EXT2)
MMYO : 118665109(EXT2) 118670761(EXT1)
MLF : 102422014(EXT2) 102441376(EXT1)
MNA : 107525491(EXT2) 107533185(EXT1)
PKL : 118712503 118718227(EXT1)
HAI : 109382533 109391972(EXT2)
DRO : 112303473(EXT2) 112315333(EXT1)
SHON : 118988619(EXT1) 119002984(EXT2)
AJM : 119051826(EXT1) 119064418(EXT2)
PDIC : 114499874(EXT2) 114514407(EXT1)
PHAS : 123810129(EXT2) 123833269(EXT1)
MMF : 118627865(EXT2) 118631561(EXT1)
RFQ : 117029882(EXT2) 117033795(EXT1)
PALE : 102890634(EXT2) 102891150(EXT1)
PGIG : 120595391(EXT1) 120606317
PVP : 105290068(EXT2) 105292239(EXT1)
RAY : 107507149(EXT1) 107511887(EXT2)
MJV : 108386769 108394755(EXT2) 108399086(EXT1) 108399399
TOD : 119238592 119255341(EXT2)
SARA : 101538625(EXT1) 101551336(EXT2)
LAV : 100656016(EXT2) 100657623(EXT1)
ETF : 101661672(EXT1) 101662457(EXT2)
DNM : 101436351(EXT1) 101436915(EXT2)
MDO : 100010947(EXT2) 100025396(EXT1)
GAS : 123241026(EXTL1) 123241182(EXT1) 123252570 123252571
SHR : 100929895(EXT1) 105750949(EXT2)
AFZ : 127541352 127544392 127555663
PCW : 110200303(EXT1) 110223945(EXT2)
OAA : 100078206(EXT1) 100079286(EXT2)
GGA : 100858205(EXT1) 100859367(EXTL1) 425859(EXT2)
PCOC : 116227694(EXT1) 116229130(EXT2) 116230047(EXTL1)
MGP : 100542119(EXT1) 100545109 100551486(EXTL1)
CJO : 107310492(EXT1) 107314816(EXT2) 107324063(EXTL1)
NMEL : 110387476(EXTL1) 110395119(EXT1) 110401311(EXT2)
APLA : 101790687(EXT2) 101792373(EXT1)
ACYG : 106037911(EXTL1) 106038456(EXT1) 106044125(EXT2)
AFUL : 116485915(EXT1) 116489660(EXT2) 116498028(EXTL1)
TGU : 100227900(EXT1) 100231605(EXT2) 115498288(EXTL1)
LSR : 110472037(EXT2) 110472893(EXTL1) 110479282(EXT1)
SCAN : 103814231(EXT1) 103823579(EXTL1) 103826716(EXT2)
PMOA : 120505159(EXT1) 120512558(EXT2) 120513889(EXTL1)
OTC : 121333361(EXT2) 121337462(EXT1) 121342741(EXTL1)
PRUF : 121349516(EXT2) 121351215(EXTL1) 121355356(EXT1)
GFR : 102035022(EXTL1) 102040196(EXT2) 102043948(EXT1)
FAB : 101814666(EXT2) 101816822(EXT1) 101818678(EXTL1)
PHI : 102099981(EXT1) 102107359(EXT2) 102111356(EXTL1)
PMAJ : 107200137(EXT1) 107205846(EXT2) 107213996(EXTL1)
CCAE : 111925064(EXT1) 111930141(EXT2)
CCW : 104692676(EXT1) 104695274(EXT2)
CBRC : 103616910(EXTL1) 103620718(EXT2) 103623522(EXT1)
ETL : 114057979(EXT1) 114064860(EXT2) 114070342(EXTL1)
ZAB : 102062154(EXT2) 102067827(EXT1)
SVG : 106849477(EXT1) 106851532(EXT2) 106861906(EXTL1)
FPG : 101919384(EXT1) 101922176(EXTL1) 101923547(EXT2)
FCH : 102049940(EXT1) 102054426(EXT2) 102056866(EXTL1)
CLV : 102084082(EXTL1) 102085197(EXT2) 102091811(EXT1)
EGZ : 104123693(EXT1) 104134053(EXT2) 104134955(EXTL1)
NNI : 104017847(EXTL1) 104018021(EXT1) 104019563(EXT2)
PLET : 104618170 104619405(EXT2)
PCRI : 104037223(EXT2) 104037444
PCAO : 104039550(EXT2) 104049419
ACUN : 113476897(EXT1) 113480641(EXT2) 113488189(EXTL1)
TALA : 104365235(EXT1) 104367927(EXT2) 116964263(EXTL1)
PADL : 103914958(EXT1) 103921685(EXT2)
AFOR : 103896426(EXTL1) 103897223(EXT1) 103897455(EXT2)
ACHC : 115333408(EXT2) 115340329(EXT1) 115351760(EXTL1)
HLE : 104837180(EXTL1) 104837692(EXT1) 104839720(EXT2)
AGEN : 126047399 126049009 126049243
GCL : 127012556 127017427 127025047
CCRI : 104157610(EXT2) 104162814(EXT1)
CSTI : 104550813(EXT2) 104555699 104561130
EHS : 104506250(EXT2) 104510203(EXT1)
CMAC : 104481663 104482061
MUI : 104538279(EXT2) 104542233 104542281(EXTL1)
FGA : 104079754(EXT2) 104080655(EXT1)
LDI : 104342773(EXT2) 104349538(EXT1)
OHA : 104330168(EXT2) 104332486(EXT1)
NNT : 104403804(EXT1) 104409474(EXT2)
SHAB : 115606439(EXT2) 115609772(EXT1) 115615978(EXTL1)
DPUB : 104297238(EXT1) 104297453(EXT2) 104307496(EXTL1)
CPEA : 104386715(EXT1) 104390387(EXT2) 104394116(EXTL1)
AVIT : 104275926(EXT2) 104279093(EXT1)
CVF : 104282894(EXT1) 104283937(EXTL1) 104295831(EXT2)
CUCA : 104061521(EXTL1) 104066187(EXT1) 104067268(EXT2)
TEO : 104372233 104374413(EXT2)
BRHI : 104494174(EXT2) 104496894(EXT1)
AAM : 106485009 106496271(EXT1) 106498294(EXT2) 106499622
AROW : 112960952(EXT1) 112964418(EXTL1) 112972955 112978433(EXT2)
NPD : 112943491(EXT2) 112948502(EXT1) 112950897(EXTL1)
TGT : 104565017(EXT2) 104573294
DNE : 112979229(EXT2) 112982032(EXTL1) 112989149(EXT1)
SCAM : 104149258(EXT2) 104150074(EXT1)
ASN : 102370729(EXT1) 102376854(EXTL1) 102379048(EXT2)
AMJ : 102560415(EXT1) 102562202(EXT2) 102575942(EXTL1)
CPOO : 109318544(EXTL1) 109321140(EXT2) 109321481(EXT1)
GGN : 109294162(EXTL1) 109298936(EXT2) 109299004(EXT1)
PSS : 102444477(EXT1) 102446763(EXT2)
CMY : 102929859(EXTL1) 102938478(EXT2) 102939595(EXT1)
CPIC : 101946173(EXT1) 101949276(EXT2) 101953823(EXTL1) 103307378
TST : 117868243(EXTL1) 117873767(EXT1) 117876973(EXT2)
CABI : 116818811(EXT1) 116830766(EXT2) 116837997(EXTL1)
MRV : 120389310(EXTL1) 120398808(EXT1) 120404543(EXT2)
ACS : 100553800(extl1) 100555771(ext2) 100567014(ext1)
PVT : 110076972(EXT1) 110081549(EXT2) 110084159(EXTL1)
SUND : 121915625(EXTL1) 121928875(EXT1) 121933481(EXT2)
PBI : 103048904 103054708 103062807(EXT2) 103067611(EXTL1)
PMUR : 107292260 107295666(EXTL1) 107302595(EXT2)
CTIG : 120307392(EXT1) 120307969(EXT2) 120314310(EXTL1)
TSR : 106538947 106539688(EXTL1) 106545012(EXT2)
PGUT : 117663388(EXTL1) 117665492(EXT2) 117668371(EXT1)
VKO : 123019173(EXT1) 123025901(EXTL1) 123026241(EXT2)
PMUA : 114596253(EXT2) 114601312(EXT1) 114601546(EXTL1)
ZVI : 118085381(EXT2) 118086449(EXTL1) 118089708(EXT1)
HCG : 128323737(EXT1) 128333382(EXTL1) 128334415(EXT2)
GJA : 107110827(EXTL1) 107113379 107122615(EXT2)
STOW : 125426333(EXT2) 125434955(EXTL1) 125439498(EXT1)
XLA : 380140(ext2.L) 398214(ext1.L) 398750(ext2.S) 399115(ext1.S)
XTR : 100151709(ext2) 448393(ext1)
NPR : 108786158(EXT2) 108790563(EXT1)
RTEM : 120917049(EXT2) 120941479(EXT1)
BBUF : 120980295(EXT2) 121001066(EXT1)
BGAR : 122920720(EXT2) 122938154(EXT1)
DRE : 101885478 493780(ext2) 497279(ext1a) 497280(ext1b) 497281(ext1c)
SRX : 107706235(extl1) 107706241 107711539 107715577 107727350 107733302 107750554 107754264 107754269 107754691
SANH : 107654722 107654729 107659874 107671371 107671458 107683605 107685778 107688159(ext2) 107688215 107688378 107696533
SGH : 107558762 107562300 107586005 107592048(extl1) 107592050 107592164 107592487 107592940 107592945 107593432
CCAR : 109050531 109056569 109059721 109072430 109074535(ext2) 109075419 109075422 109093562 109106263 109109198 109109965 109111718
CAUA : 113052033 113062235 113062294 113062301 113063437 113073234 113083119 113105758 113115689 113119245 113119254 113121224
CGIB : 127935072 127935393 127938411 127962006 127975010 127978542 127979490 127983603 128017046 128030806
PPRM : 120468007(ext2) 120469966(ext1c) 120479262(ext1b) 120491188(ext1a) 120493730
MAMB : 125243241(ext1a) 125264629(ext2) 125275117(ext1b) 125275126 125278978
CIDE : 127497257 127497324 127500934 127501221 127502442 127515571
MASI : 127420630 127420631 127425512 127425513 127453101 127454129 127454839
IPU : 108256617(ext1a) 108257122(ext1b) 108257140 108271344(ext2) 108275270
PHYP : 113529295 113532714 113535947 113535988 113536365(ext2)
SMEO : 124375785(ext1b) 124375938 124390802(ext2) 124401370 124403868(ext1a)
TFD : 113643961(ext1c) 113649722(ext1a) 113654795 113661608(ext1b) 113663258(ext2)
AMEX : 103026919 103031914 103040053 103046596(ext2) 103047171 111197650
EEE : 113575759(ext2) 113578814 113588018(ext1) 113591568 113591687
TRU : 101065654 101066048(ext2) 101072426 101072822 101075972
TNG : GSTEN00017827G001 GSTEN00032917G001 GSTEN00032935G001 GSTEN00035381G001 GSTEN00038113G001
LCO : 104919199(ext2) 104926220 104931682 104932462 104937142
NCC : 104945394 104949435 104961795(ext1) 104963025(ext2)
CGOB : 115003439 115006327(ext2) 115015568 115016180 115021154
ELY : 117258719(ext2) 117263289(ext1b) 117263650 117265950 117270842
EFO : 125881736(ext2) 125893291 125897583 125904485 125904491(ext1b)
PLEP : 121945585 121955317 121958010(ext1b) 121958038 121960250(ext2)
SLUC : 116034014(ext2) 116035281 116047237(ext1c) 116047249(ext1b) 116066120
ECRA : 117943850(ext2) 117946948 117956425(ext1b) 117956791 117961813 117961814
ESP : 116688651(ext2) 116690738 116701186 116701221 116706523
PFLV : 114553112(ext2) 114557177 114567744 114567814 114572953
GAT : 120807940 120808600(ext2) 120810156 120826358(ext1b) 120826673(ext1c)
PPUG : 119195167 119197352 119219177(ext1b) 119219200 119229335(ext2)
MSAM : 119890106(ext2) 119897919 119907162 119907458(ext1b) 119908630 119909485
CUD : 121513315 121513674(ext2) 121521338 121523384(ext1b) 121524170
ALAT : 119005988 119012419 119016449(ext1b) 119017160 119017615(ext2)
MZE : 101464589 101473582(ext2) 101479111 101482519 101486492
ONL : 100695641(ext2) 100700775 100705583 100707723 109194193
OAU : 116309414 116318909 116318948(ext1b) 116322583 116327190(ext2)
OLA : 101163398(ext2) 101164181 101167217 101169374
OML : 112143494 112160904(ext2) 112162700(ext1b) 112162739(ext1c)
XMA : 102217307 102217354 102230266 102234444(ext2) 102237506
XCO : 114141516 114142777(ext2) 114155469 114156156 114159116
XHE : 116716748 116718349(ext2) 116731149 116731796 116734657
PRET : 103457265 103462432(ext2) 103472886(ext1) 103473086 103478346
PFOR : 103131421 103135121 103139431(ext2) 103151922 103154987 103155379(ext1)
PLAI : 106951280 106953583(ext1) 106958190(ext2) 106961006 106964918
PMEI : 106907411 106923397(ext1) 106926106(ext2) 106928852
GAF : 122821865(ext2) 122825094 122831600 122843906(ext1b) 122844227(ext1c)
CVG : 107082854 107085591(ext2) 107086154 107089629(ext1) 107094248 107094935
CTUL : 119772289(ext1c) 119775297 119777081 119778046(ext1b) 119782724(ext2)
GMU : 124865747 124866743(ext2) 124879655(ext1c) 124879738(ext1b) 124881887
NFU : 107377760 107378775 107381443(ext2) 107394502 107394966
KMR : 108228674(ext2) 108232308 108243943(ext1b) 108244864 108250176(ext1c)
ALIM : 106511501 106514225(ext1) 106527530 106530767(ext2) 106532427 106535689
NWH : 119418618 119425471 119425560(ext1c) 119427822(ext2)
AOCE : 111563665 111564587 111574611(ext2) 111580481 111589114(ext1)
MCEP : 125005111(ext2) 125016650 125019553(ext1b) 125019586
CSEM : 103378751(ext2) 103381137 103388612(ext1) 103393992 103394040
POV : 109632177(ext1) 109636768(ext2) 109639984 109642456 109643173 109644500
SSEN : 122772353(ext2) 122774807 122784514 122786453 122786792
HHIP : 117758031 117758296(ext2) 117770077 117770079(ext1b) 117776501
HSP : 118099670 118109144(ext2) 118113668 118124559 118124711(ext1b)
LCF : 108888686 108889564(ext1b) 108889565 108889668 108889677 108891202
SDU : 111222995 111223271 111227735 111237872 111238419(ext2)
SLAL : 111654812(ext2) 111658101 111671857 111671874 111672565
XGL : 120784183 120786451(ext1b) 120786592(ext1c) 120788958 120794269(ext2)
HCQ : 109514394(ext2) 109518055 109518060 109523479 109529689(ext1)
SSCV : 125967040 125975194 125986591 125986799 125990392
BPEC : 110153759 110156338 110171534 110172856(ext2) 110173279
MALB : 109952487 109958190 109958643 109958685 109965798(ext2) 109968834
BSPL : 114843138 114849466 114852235(ext2) 114865978(ext1b) 114866303(ext1c)
SASA : 100306779(ext1c) 100380322(ext2) 106570050 106571404 106588496 106588504 106594121 106597672 106607809
STRU : 115167097(ext2) 115173416 115173427 115174806 115175988 115175999 115187873 115187874 115192831
OTW : 112217339 112229926 112229932 112247034 112250171 112264222 112264884 112264892 121844920
OMY : 110487634 110488385 110496112(ext1b) 110496808(ext1c) 110506669 110511734 110522229 110526537 110529611
OGO : 123990750 123995089 124012587 124012858(ext1b) 124017649 124033638 124035622 124043635 124043639
ONE : 115107751 115112435(ext2) 115128292 115128299 115131708 115131715 115139415
SALP : 111954432 111955132 111955294 111955814 111955850 111969484 111972462
SNH : 120019504 120022446 120022523 120024563 120027266 120027289 120040883 120049131
CCLU : 121542569 121548927 121552579 121571473 121571482 121585943 121586367(ext1b) 121586374(ext1c) 123484405 123484718
ELS : 105005807 105017786 105022258(ext2) 105023503 105027867
SFM : 108922050(ext1) 108928562 108931808 108934682(ext2) 108940524
PKI : 111836091 111840708(ext2) 111843930 111843931 111844061 111854291
AANG : 118215430(ext2) 118226079 118230580 118233246(ext1c) 118233844
LOC : 102688650 102688999(ext1) 102689027(ext2) 102698389
PSPA : 121294359 121303296 121308213 121313281 121314898 121315561 121317487 121329636
ARUT : 117394872 117400267 117402503 117411447 117412720 117414200 117432282 117435140 117964062
PSEX : 120516821(ext1b) 120517016(ext2) 120517779 120526106
LCM : 102353460(EXT1) 102354369 102354854(EXTL1) 102363354(EXT2)
CMK : 103174976(ext2) 103179627 103184956 103185802
RTP : 109910890(ext2) 109930524 109932300
CPLA : 122549339 122558076(ext2) 122563602
BBEL : 109479557 109480278
SCLV : 120335452 120335699
SPU : 100893938 115918716 577995
APLC : 110981069 110986223
SKO : 100313593 100372539 102809744
DME : Dmel_CG10117(ttv) Dmel_CG8433(sotv)
DSI : Dsimw501_GD11060(Dsim_GD11060) Dsimw501_GD25567(Dsim_GD25567)
DYA : Dyak_GE13596 Dyak_GE14097
DMN : 108159562 108159662 117190510
DMO : Dmoj_GI20737 Dmoj_GI20872
DNV : 108652943 115564114 115564922
CCAT : 101453656 101460876
MDE : 101888783 101894872 101901385
SCAC : 106082419 106091369
AGA : AgaP_AGAP000081 AgaP_AGAP010388
ACOZ : 120952216 120956752
AARA : 120901724 120906198
AMER : 121593113 121599408
ASTE : 118503312 118509916
AALB : 109397881 109411435 109416900 109428863 115254192
CQU : CpipJ_CPIJ009765 CpipJ_CPIJ012734
CPII : 120424304 120429091
BCOO : 119078978 119081884
ACER : 107997927 107999513
ALAB : 122711993 122714818
BBIF : 117211962 117214192
BVAN : 117156137 117166073
BTER : 100643223 100650849
BPYO : 122571366 122577021
CCAL : 108622677 108627221
OBB : 114871565 114871663 114880970
MGEN : 117220187 117224160
NMEA : 116429461 116432549
CGIG : 122399622 122404430
MPHA : 105835292 105839250
ACEP : 105619491 105627211
PBAR : 105425236 105427034
PFUC : 122518599 122523426
CSOL : 105364815 105366129
CGLO : 123268665 123275072
AGIF : 122851929 122854354
CINS : 118067431 118074555
CCIN : 107262845 107267679
CSET : 123316160 123321334
NVL : 108557086 108557670 108558174
APLN : 108740927 108743766
PPYR : 116163081 116164508 116166831
BMOR : 101736061 101741346
BMAN : 114247002 114249440
MSEX : 115440710 115448364
DPL : KGM_203672 KGM_214517
BANY : 112046889 112047335
PMAC : 106708978 106709701
PPOT : 106100685 106105805
PRAP : 110993283 111003256
PNAP : 125049662 125056161
CCRC : 123696746 123705704
SLIU : 111353115 111357626
PXY : 105389344 105394758 105394780
CFEL : 113365782 113366316 113369841 113369842
BTAB : 109034604 109035894
CLEC : 106673227 106674189
HHAL : 106678975 106681771
PHU : Phum_PHUM455050 Phum_PHUM488440
TPAL : 117652175 117652466
CSEC : 111866884 111872464
SGRE : 126297625 126352265
DPX : DAPPUDRAFT_304945 DAPPUDRAFT_307216
DPZ : 124328499 124337515 124340498
PVM : 113802032 113819966 113824640
PCHN : 125032085 125036743
PMOO : 119592442 119596794
HAME : 121864489 121869478
PCLA : 123758376 123769944
PTRU : 123501535 123501664
ESN : 126984445 127005043 127005282
HAZT : 108671440 108677950
PPOI : 119094444 119094445 119102599
ISC : IscW_ISCW000326 IscW_ISCW021392
RSAN : 119374094 119402119
TUT : 107361403 107367244 107371591 107371607
DPTE : 113789732 113796479
CSCU : 111630346 111639960
PTEP : 107437365 107450714
BMY : BM_BM10349(Bma-rib-2) BM_BM3322(Bma-rib-1)
LOA : LOAG_05822 LOAG_08703
NAI : NECAME_01875 NECAME_04728
HRO : HELRODRAFT_119925 HELRODRAFT_186788
LGI : LOTGIDRAFT_124977 LOTGIDRAFT_199269
PCAN : 112561913 112565643
HRJ : 124270731 124276925 124282773
CRG : 105324710 105325442 117690299
PMAX : 117317139 117326975
MCAF : 127725165 127732091
MMER : 123539606 123552181
DPOL : 127850329 127857791
LAK : 106155252 106175986 106181741
SMM : Smp_146320.1 Smp_172060
SHX : MS3_00006818(EXT2_1)
OVI : T265_05866 T265_05932
EPA : 110240280 110241454 110241460
ATEN : 116298104 116307177
ADF : 107336652 107336815 107358713
AMIL : 114957442 114961284
PDAM : 113666284 113669827
SPIS : 111326534 111336973
TAD : TRIADDRAFT_1026 TRIADDRAFT_24279
SMO : SELMODRAFT_23945 SELMODRAFT_24030
PPP : 112279610 112280248 112280650 112281934 112282628 112290993 112294684
SRE : PTSG_07269 PTSG_10121
ACAN : ACA1_335890 ACA1_393390
FCY : FRACYDRAFT_160829 FRACYDRAFT_234481
» show all
Taxonomy
Reference
Authors
Senay C, Lind T, Muguruma K, Tone Y, Kitagawa H, Sugahara K, Lidholt K, Lindahl U, Kusche-Gullberg M.
Title
The EXT1/EXT2 tumor suppressors: catalytic activities and role in heparan sulfate biosynthesis.
Journal
Sequence
Reference
Authors
Lind T, Tufaro F, McCormick C, Lindahl U, Lidholt K
Title
The putative tumor suppressors EXT1 and EXT2 are glycosyltransferases required for the biosynthesis of heparan sulfate.
Journal
Sequence
Other DBs
ExPASy - ENZYME nomenclature database: 2.4.1.225