Entry
Name
N-acetyl-beta-glucosaminyl-glycoprotein 4-beta-N-acetylgalactosaminyltransferase;
beta1,4-N-acetylgalactosaminyltransferase III;
beta4GalNAc-T3;
beta1,4-N-acetylgalactosaminyltransferase IV;
beta4GalNAc-T4;
UDP-N-acetyl-D-galactosamine:N-acetyl-D-glucosaminyl-group beta-1,4-N-acetylgalactosaminyltransferase;
UDP-N-acetyl-D-galactosamine:N-acetyl-beta-D-glucosaminyl-group 4-beta-N-acetylgalactosaminyltransferase
Class
Transferases;
Glycosyltransferases;
Hexosyltransferases
BRITE hierarchy
Sysname
UDP-N-acetyl-alpha-D-galactosamine:N-acetyl-beta-D-glucosaminyl-group 4-beta-N-acetylgalactosaminyltransferase
Reaction(IUBMB)
UDP-N-acetyl-alpha-D-galactosamine + N-acetyl-beta-D-glucosaminyl group = UDP + N-acetyl-beta-D-galactosaminyl-(1->4)-N-acetyl-beta-D-glucosaminyl group
Reaction(KEGG)
Substrate
UDP-N-acetyl-alpha-D-galactosamine [CPD:
C00203 ];
N-acetyl-beta-D-glucosaminyl group
Product
UDP [CPD:
C00015 ];
N-acetyl-beta-D-galactosaminyl-(1->4)-N-acetyl-beta-D-glucosaminyl group
Comment
The enzyme from human can transfer N-acetyl-D-galactosamine (GalNAc) to N-glycan and O-glycan substrates that have N-acetyl-D-glucosamine (GlcNAc) but not D-glucuronic acid (GlcUA) at their non-reducing end. The N-acetyl-beta-D-glucosaminyl group is normally on a core oligosaccharide although benzyl glycosides have been used in enzyme-characterization experiments. Some glycohormones, e.g. lutropin and thyrotropin contain the N-glycan structure containing the N-acetyl-beta-D-galactosaminyl-(1->4)-N-acetyl-beta-D-glucosaminyl group.
History
EC 2.4.1.244 created 2006
Pathway
ec00513 Various types of N-glycan biosynthesis
Orthology
K09656 beta-1,4-N-acetylgalactosaminyltransferase 3
K09657 beta-1,4-N-acetylgalactosaminyltransferase 4
Genes
HSA : 283358(B4GALNT3) 338707(B4GALNT4)
PTR : 450920(B4GALNT4) 451738(B4GALNT3)
PPS : 100976376(B4GALNT4) 100989611(B4GALNT3)
PON : 100435319(B4GALNT3) 100457244(B4GALNT4)
NLE : 100602613(B4GALNT4) 105738882(B4GALNT3)
HMH : 116466564(B4GALNT4) 116472508(B4GALNT3)
MCC : 114669831(B4GALNT4) 706259(B4GALNT3) 720768
MCF : 102115389(B4GALNT4) 102145263(B4GALNT3)
MTHB : 126930231 126936566
MNI : 105463809(B4GALNT3) 105494128(B4GALNT4)
CSAB : 103218358(B4GALNT3) 103239139(B4GALNT4)
CATY : 105577189(B4GALNT4) 105582943(B4GALNT3)
PANU : 101000778(B4GALNT4)
TGE : 112606611(B4GALNT4) 112634023(B4GALNT3)
MLEU : 105529907(B4GALNT3)
RRO : 104656676 104662541(B4GALNT3) 115893542(B4GALNT4)
RBB : 108519516(B4GALNT3) 108543532(B4GALNT4)
TFN : 117080293(B4GALNT4) 117090732(B4GALNT3)
PTEH : 111520323(B4GALNT3) 111520629(B4GALNT4)
CANG : 105503272(B4GALNT4) 105522580(B4GALNT3)
CJC : 100407822(B4GALNT3) 100413834(B4GALNT4)
SBQ : 101037149(B4GALNT4) 101054201(B4GALNT3)
CIMI : 108288801(B4GALNT4) 108315833(B4GALNT3)
CSYR : 103266186(B4GALNT3)
MMUR : 105862186(B4GALNT3) 105874069(B4GALNT4)
LCAT : 123640206(B4GALNT3) 123642981(B4GALNT4)
PCOQ : 105812899(B4GALNT3) 105816516(B4GALNT4)
OGA : 100944061(B4GALNT4) 100961561(B4GALNT3)
MMU : 330406(B4galnt3) 330671(B4galnt4)
MCAL : 110296670(B4galnt3) 110297886
MPAH : 110316578(B4galnt3) 110318245(B4galnt4)
RNO : 309105(B4galnt4) 500306(B4galnt3)
MCOC : 116099504(B4galnt3) 116103201(B4galnt4)
ANU : 117706236(B4galnt4) 117715281(B4galnt3)
MUN : 110546049(B4galnt3) 110553927(B4galnt4)
CGE : 100756528(B4galnt3) 100758404(B4galnt4)
MAUA : 101831193(B4galnt3) 101836962(B4galnt4)
PROB : 127228519(B4galnt4) 127236255(B4galnt3)
PLEU : 114693511(B4galnt4) 114700747(B4galnt3)
MORG : 121440001(B4galnt3) 121458064(B4galnt4)
MFOT : 126498373 126505562
AAMP : 119799909(B4galnt4) 119807981(B4galnt3)
NGI : 103739368(B4galnt3) 103751068(B4galnt4)
HGL : 101702463(B4galnt3) 101720559(B4galnt4)
CPOC : 100712778(B4galnt4) 100730678(B4galnt3)
CCAN : 109694620(B4galnt3) 109698146(B4galnt4)
DORD : 105991056(B4galnt3) 105998569(B4galnt4)
DSP : 122095036(B4galnt4) 122099585
OPI : 101516966(B4GALNT4) 101534838(B4GALNT3)
TUP : 102476308(B4GALNT4) 102477252(B4GALNT3)
GVR : 103594688(B4GALNT3) 103606188(B4GALNT4)
CFA : 483398(B4GALNT4) 486751(B4GALNT3)
CLUD : 112663544(B4GALNT4) 112669004(B4GALNT3)
VVP : 112914603(B4GALNT4) 112917410(B4GALNT3)
VLG : 121480290(B4GALNT3) 121501378(B4GALNT4)
AML : 100474848(B4GALNT4) 100481474(B4GALNT3)
UMR : 103671083(B4GALNT4) 103675765(B4GALNT3)
UAH : 113248774(B4GALNT4) 113258033(B4GALNT3)
UAR : 123775533(B4GALNT4) 123777720(B4GALNT3)
MPUF : 101671138(B4GALNT4) 101673160(B4GALNT3)
NVS : 122891063(B4GALNT3) 122913210(B4GALNT4)
ORO : 101362933(B4GALNT4) 101376959(B4GALNT3)
EJU : 114201512(B4GALNT4) 114222591(B4GALNT3)
ZCA : 113914397(B4GALNT4) 113923158(B4GALNT3)
MLX : 118015665(B4GALNT4) 118025451(B4GALNT3)
NSU : 110580881(B4GALNT3) 110582238(B4GALNT4)
LWW : 102734637(B4GALNT4) 102741875
FCA : 101086091(B4GALNT4) 101097324(B4GALNT3)
PYU : 121022074(B4GALNT3) 121022812(B4GALNT4)
PCOO : 112867382(B4GALNT3)
PBG : 122473889(B4GALNT3) 122484185(B4GALNT4)
LRUF : 124502560 124527523
PTG : 102950331(B4GALNT4) 102953154(B4GALNT3)
PPAD : 109259799(B4GALNT4) 109276235(B4GALNT3)
AJU : 106965465(B4GALNT3) 106987942(B4GALNT4)
HHV : 120223395(B4GALNT4) 120234496(B4GALNT3)
BTA : 100137759(B4GALNT4) 527026(B4GALNT3)
BOM : 102275891(B4GALNT3) 102283950(B4GALNT4)
BBUB : 102394198(B4GALNT3) 102409676(B4GALNT4)
BBIS : 104992352(B4GALNT3)
CHX : 102172522(B4GALNT3) 102188023
OAS : 101105615(B4GALNT4) 101115274(B4GALNT3)
ODA : 120857852(B4GALNT3) 120874219(B4GALNT4)
CCAD : 122423417(B4GALNT3) 122430574(B4GALNT4)
SSC : 100623649(B4GALNT4) 110260758(B4GALNT3)
CFR : 102522276(B4GALNT4) 102523640(B4GALNT3)
CBAI : 105062438(B4GALNT4) 105076667(B4GALNT3)
CDK : 105102955(B4GALNT3) 105106170(B4GALNT4)
VPC : 102535991(B4GALNT4) 102539840(B4GALNT3)
BACU : 103000329(B4GALNT4) 103019272(B4GALNT3)
LVE : 103071788(B4GALNT4) 103084199(B4GALNT3)
OOR : 101269577(B4GALNT3) 101279166(B4GALNT4)
DLE : 111170320(B4GALNT4) 111176612(B4GALNT3)
PCAD : 102994651(B4GALNT4)
PSIU : 116757325(B4GALNT4) 116761376(B4GALNT3)
NASI : 112391623(B4GALNT3) 112402186(B4GALNT4)
ECB : 100054676(B4GALNT4) 100056854(B4GALNT3)
EPZ : 103561349(B4GALNT4) 103565631(B4GALNT3)
EAI : 106825357(B4GALNT4) 106831525(B4GALNT3)
MYB : 102246590(B4GALNT4) 102254875(B4GALNT3)
MMYO : 118649013(B4GALNT4) 118651139(B4GALNT3)
MNA : 107542329(B4GALNT4) 107546417(B4GALNT3)
PKL : 118717962(B4GALNT4) 118729258(B4GALNT3)
HAI : 109375626(B4GALNT4) 109388940(B4GALNT3)
DRO : 112311132(B4GALNT3) 112317448(B4GALNT4)
SHON : 118982226(B4GALNT4) 119000001(B4GALNT3)
AJM : 119045231(B4GALNT3) 119062225(B4GALNT4)
PDIC : 114499180(B4GALNT4) 114513177(B4GALNT3)
PHAS : 123807341(B4GALNT4) 123813561(B4GALNT3)
MMF : 118624292(B4GALNT3) 118643193(B4GALNT4)
RFQ : 117029209(B4GALNT3) 117031317(B4GALNT4)
PALE : 102884317(B4GALNT4) 102884875(B4GALNT3)
PGIG : 120584649(B4GALNT4) 120607341(B4GALNT3)
PVP : 105297302(B4GALNT3) 105305950(B4GALNT4)
RAY : 107506918(B4GALNT3) 107506949(B4GALNT4)
MJV : 108386186(B4GALNT3) 108401884(B4GALNT4)
TOD : 119247842(B4GALNT3) 119248775(B4GALNT4)
SARA : 101546179(B4GALNT3) 101551635(B4GALNT4)
LAV : 100656658(B4GALNT4) 100665318(B4GALNT3)
ETF : 101644547(B4GALNT4) 101663950(B4GALNT3)
DNM : 101415099(B4GALNT3) 101445790(B4GALNT4)
SHR : 100918044(B4GALNT3) 100921988(B4GALNT4)
PCW : 110202986(B4GALNT4) 110204330 110218701(B4GALNT3)
OAA : 100080104(B4GALNT3) 100088024(B4GALNT4)
GGA : 418150(B4GALNT3) 770601(B4GALNT4)
PCOC : 116226858(B4GALNT3) 116237913(B4GALNT4)
MGP : 100539296(B4GALNT4) 100543657(B4GALNT3)
CJO : 107314272(B4GALNT4) 107315358(B4GALNT3)
NMEL : 110395311(B4GALNT3) 110401603(B4GALNT4)
APLA : 101794410(B4GALNT3) 101795425(B4GALNT4)
ACYG : 106031042(B4GALNT3) 106047061(B4GALNT4)
AFUL : 116487230(B4GALNT3) 116489412(B4GALNT4)
TGU : 100218099(B4GALNT4) 100221161(B4GALNT3)
LSR : 110472973(B4GALNT3) 110484970(B4GALNT4)
SCAN : 103820514(B4GALNT3) 103827051(B4GALNT4)
PMOA : 120501032(B4GALNT4) 120501516(B4GALNT3)
OTC : 121332794(B4GALNT3) 121334773(B4GALNT4)
PRUF : 121352308(B4GALNT4) 121362663(B4GALNT3)
GFR : 102034690(B4GALNT4) 102036024(B4GALNT3)
FAB : 101806677(B4GALNT4) 101814333(B4GALNT3)
PHI : 102109686(B4GALNT3) 102112024(B4GALNT4)
PMAJ : 107204887(B4GALNT3) 107206466(B4GALNT4)
CCAE : 111928420(B4GALNT3) 111930586(B4GALNT4) 111944590
CCW : 104684539(B4GALNT4) 104692236(B4GALNT3)
CBRC : 103614579(B4GALNT4) 103624718(B4GALNT3)
ETL : 114063268(B4GALNT4) 114068768(B4GALNT3)
ZAB : 102067994(B4GALNT4) 102069046(B4GALNT3)
ACHL : 103800365(B4GALNT4)
SVG : 106849352(B4GALNT3) 106854721(B4GALNT4)
FPG : 101919553(B4GALNT4) 101920197(B4GALNT3)
FCH : 102051612(B4GALNT4) 102055264(B4GALNT3)
CLV : 102088828(B4GALNT4) 102090270(B4GALNT3)
EGZ : 104127888(B4GALNT4) 104129759(B4GALNT3)
NNI : 104011411(B4GALNT4) 104020250(B4GALNT3)
PLET : 104625129(B4GALNT3) 104625881
PCRI : 104035242(B4GALNT3)
ACUN : 113481121(B4GALNT4) 113487437(B4GALNT3)
TALA : 104357006(B4GALNT3) 116961597(B4GALNT4)
PADL : 103924499(B4GALNT3) 103925356(B4GALNT4)
AFOR : 103906292(B4GALNT4) 103906477(B4GALNT3)
ACHC : 115351887(B4GALNT4) 115352766(B4GALNT3)
HALD : 104321236(B4GALNT3)
HLE : 104831025(B4GALNT3) 104832094(B4GALNT4)
AGEN : 126047330 126048108
CSTI : 104563214(B4GALNT3)
CMAC : 104482300(B4GALNT3)
MUI : 104541194(B4GALNT3) 104546704(B4GALNT4)
FGA : 104073318(B4GALNT4) 104076689(B4GALNT3)
GSTE : 104263353(B4GALNT3)
OHA : 104326525(B4GALNT4) 104330276(B4GALNT3)
SHAB : 115605642(B4GALNT3) 115607582(B4GALNT4)
DPUB : 104297523(B4GALNT4) 104310227(B4GALNT3)
PGUU : 104463140(B4GALNT3)
ACAR : 104520411(B4GALNT4) 104527370(B4GALNT3)
CPEA : 104386596(B4GALNT3) 104392119(B4GALNT4)
AVIT : 104276245(B4GALNT3)
CVF : 104281700(B4GALNT3) 104282480(B4GALNT4)
CUCA : 104055923(B4GALNT3) 104057239(B4GALNT4)
BRHI : 104500014(B4GALNT3) 104501662(B4GALNT4)
AAM : 106488281(B4GALNT3) 106489126(B4GALNT4)
AROW : 112968267(B4GALNT3) 112973777(B4GALNT4)
NPD : 112948021(B4GALNT4) 112958331(B4GALNT3)
TGT : 104574676(B4GALNT4) 104575866(B4GALNT3)
DNE : 112991580(B4GALNT4) 112993372(B4GALNT3)
SCAM : 104147385(B4GALNT3) 104149792(B4GALNT4)
AMJ : 102563895(B4GALNT3) 102569972(B4GALNT4)
CPOO : 109315923(B4GALNT3) 109318171(B4GALNT4)
GGN : 109296220(B4GALNT3) 109299254(B4GALNT4)
PSS : 102450592(B4GALNT3) 102454912(B4GALNT4)
CMY : 102944252(B4GALNT3) 102948034(B4GALNT4)
CPIC : 101946283(B4GALNT3) 101950465(B4GALNT4)
TST : 117877383(B4GALNT4) 117882408(B4GALNT3)
CABI : 116820558(B4GALNT4) 116834553(B4GALNT3)
MRV : 120395802(B4GALNT3) 120403836(B4GALNT4)
ACS : 100552264(b4galnt3) 100568220(b4galnt4)
SUND : 121919039(B4GALNT4) 121930897(B4GALNT3)
PBI : 103050876(B4GALNT3) 103061436(B4GALNT4)
PMUR : 107291100(B4GALNT4)
CTIG : 120312477(B4GALNT4) 120313153(B4GALNT3)
PGUT : 117655634(B4GALNT3) 117665151(B4GALNT4)
VKO : 123016517(B4GALNT3) 123021256(B4GALNT4)
PMUA : 114600280(B4GALNT4) 114605389(B4GALNT3)
HCG : 128325760(B4GALNT3) 128329804(B4GALNT4)
STOW : 125425864(B4GALNT4) 125435322(B4GALNT3)
XLA : 108704576(b4galnt3.L) 108712580(b4galnt3.S) 108713824(b4galnt4.L) 108715202(b4galnt4.S)
XTR : 100036642(b4galnt4) 100488678(b4galnt3)
RTEM : 120917276(B4GALNT4) 120932697(B4GALNT3)
BBUF : 120980929(B4GALNT4) 121004272(B4GALNT3)
BGAR : 122920474(B4GALNT4) 122928496(B4GALNT3)
DRE : 553524(b4galnt3b) 559305(b4galnt4b) 565184(b4galnt4a)
SRX : 107705801 107707534 107709930 107730265
SANH : 107675269 107686572 107688567 107696636
SGH : 107558306 107562842 107564911 107596444 107600469
CCAR : 109045851 109054019 109083500 109097386
CAUA : 113043593 113067112 113100338 113106233 113118141
CGIB : 127934737 127946721 127962637 127977241 128014322
PPRM : 120464776(b4galnt3b) 120469310(b4galnt4b) 120473350(b4galnt4a)
MAMB : 125247077(b4galnt4a) 125253862(b4galnt3b) 125265129(b4galnt4b)
CIDE : 127499502 127507655 127516407
MASI : 127435661 127437087 127440030 127452144
IPU : 108259196(b4galnt4b) 108264151(b4galnt3b) 108275076(b4galnt4a)
PHYP : 113529844(b4galnt4) 113540814
SMEO : 124380028(b4galnt4b) 124392673(b4galnt4a) 124395851(b4galnt3b)
TFD : 113636656(b4galnt4b) 113657294(b4galnt3b) 113659872(b4galnt4a)
AMEX : 103022890 103037724(b4galnt4) 103040627
EEE : 113570817 113579684 113581322(b4galnt4)
TRU : 101067924 101067926(b4galnt4)
LCO : 104918138 104920486(b4galnt4)
NCC : 104957600(b4galnt3) 104967977(b4galnt4)
CGOB : 115009853(b4galnt4) 115010263
ELY : 117262120(b4galnt3b) 117262290(b4galnt4a)
EFO : 125887637(b4galnt3b) 125887737(b4galnt4a)
PLEP : 121949667(b4galnt4a) 121950026(b4galnt3b)
SLUC : 116038542(b4galnt4a) 116045686(b4galnt3b)
ECRA : 117949490(b4galnt4a) 117949521(b4galnt3b)
ESP : 116694153 116694547(b4galnt4)
PFLV : 114559669(b4galnt4) 114560215
GAT : 120808958 120809787(b4galnt3b) 120812247
PPUG : 119195585(b4galnt4a) 119196592(b4galnt3b)
MSAM : 119893562(b4galnt3b) 119894206(b4galnt4a)
CUD : 121514681(b4galnt3b) 121515700(b4galnt4a)
ALAT : 119023889(b4galnt3b) 119025002(b4galnt4a)
MZE : 101471802(b4galnt4) 101485737
ONL : 100704589(b4galnt4) 100709042
OAU : 116313492(b4galnt3b) 116333275(b4galnt4a)
OLA : 101163791(b4galnt4) 101164306
OML : 112151753(b4galnt4a) 112152134(b4galnt3b)
XMA : 102221073(b4galnt4) 102223638
XHE : 116734070(b4galnt4) 116735786
PRET : 103466150(b4galnt4) 103466673
PFOR : 103133797 103151601
PLAI : 106936817 106954927
PMEI : 106915345 106933230
GAF : 122835285(b4galnt4a) 122835521(b4galnt3b)
CVG : 107085425(b4galnt4) 107090556
CTUL : 119772420(b4galnt3b) 119776920(b4galnt4a)
GMU : 124855303(b4galnt4a) 124860987(b4galnt3b)
NFU : 107388842 107389008(b4galnt4)
KMR : 108230205(b4galnt3b) 108239976(b4galnt4a)
ALIM : 106514300(b4galnt3) 106515656(b4galnt4)
NWH : 119415703(b4galnt3b) 119416009(b4galnt4a)
AOCE : 111571948 111578077
MCEP : 125014775(b4galnt3b) 125014914(b4galnt4a)
CSEM : 103380088 103380379(b4galnt4)
SSEN : 122775446(b4galnt3b) 122775936(b4galnt4a)
HHIP : 117762992(b4galnt4a) 117763192
HSP : 118109172(b4galnt4a) 118109451
LCF : 108875136(b4galnt3b) 108875398(b4galnt4a)
SDU : 111228500 111228650(b4galnt4)
SLAL : 111653356 111661820(b4galnt4)
XGL : 120792688(b4galnt3b) 120793655(b4galnt4a)
HCQ : 109528077 109530471(b4galnt4)
BPEC : 110165926(b4galnt4)
MALB : 109967709 109973574
BSPL : 114857636(b4galnt4a) 114857690(b4galnt3b)
SASA : 106560716(b4galnt4) 106561254(b4galnt3)
STRU : 115196693 115197182(b4galnt4)
OTW : 112218977(b4galnt3b) 112219203(b4galnt4a) 112252461
OMY : 110490617(b4galnt4a) 110496319 110521711
OGO : 124001623 124036033 124040915(b4galnt4a)
ONE : 115109478 115134198 115134636(b4galnt4)
SALP : 111961981(b4galnt4) 111962535
SNH : 120065861(b4galnt3b) 120066544(b4galnt4a)
CCLU : 121531187(b4galnt4a)
ELS : 105006820(b4galnt4) 105022210
SFM : 108934528 108936581 108942180(b4galnt4)
PKI : 111841532 111859463(b4galnt4)
AANG : 118215602(b4galnt4a) 118219072(b4galnt3b) 118228416 118231854
LOC : 102683937(b4galnt3) 102689842(b4galnt4)
PSPA : 121294830 121318539(b4galnt3b) 121320154 121330341
ARUT : 117416081 117420048(b4galnt3b) 117432458
PSEX : 120516713(b4galnt4a)
LCM : 102348774(B4GALNT3) 102349555(B4GALNT4)
CMK : 103181837(b4galnt3b) 103186017
RTP : 109911271 109919635 109930789
EPA : 110236390 110236544 110241297 110246555 110249064
ATEN : 116301396 116301860 116303567 116305195 116305287
ADF : 107326871 107341393 107342115 107344974
AMIL : 114947641 114967932 114967936 114973417
PDAM : 113667731 113669909 113672594 113682024 113685757
SPIS : 111320861 111321881 111323356 111335085 111336369
HMG : 100206963 100210795 100214956
SRE : PTSG_03250 PTSG_05319
» show all
Taxonomy
Reference
Authors
Sato T, Gotoh M, Kiyohara K, Kameyama A, Kubota T, Kikuchi N, Ishizuka Y, Iwasaki H, Togayachi A, Kudo T, Ohkura T, Nakanishi H, Narimatsu H
Title
Molecular cloning and characterization of a novel human beta 1,4-N-acetylgalactosaminyltransferase, beta 4GalNAc-T3, responsible for the synthesis of N,N'-diacetyllactosediamine, galNAc beta 1-4GlcNAc.
Journal
Sequence
Reference
Authors
Gotoh M, Sato T, Kiyohara K, Kameyama A, Kikuchi N, Kwon YD, Ishizuka Y, Iwai T, Nakanishi H, Narimatsu H
Title
Molecular cloning and characterization of beta1,4-N-acetylgalactosaminyltransferases IV synthesizing N,N'-diacetyllactosediamine.
Journal
Sequence
Other DBs
ExPASy - ENZYME nomenclature database: 2.4.1.244