KEGG   ENZYME: 4.1.2.63
Entry
EC 4.1.2.63                 Enzyme                                 
Name
2-hydroxyacyl-CoA lyase;
HACL1 (gene name);
2-hydroxyphytanoyl-CoA lyase;
2-HPCL
Class
Lyases;
Carbon-carbon lyases;
Aldehyde-lyases
Sysname
2-hydroxy-3-methyl fatty-CoA formyl-CoA lyase (2-methyl branched fatty aldehyde-forming)
Reaction(IUBMB)
(1) a 2-hydroxy-3-methyl-Cn-fatty-acyl-CoA = a 2-methyl-branched Cn-1-fatty aldehyde + formyl-CoA [RN:R12799];
(2) a (2R)-2-hydroxy-Cn-long-chain fatty acyl-CoA = a Cn-1-long-chain fatty aldehyde + formyl-CoA [RN:R12800]
Reaction(KEGG)
R12799 R12800
Substrate
2-hydroxy-3-methyl-Cn-fatty-acyl-CoA;
(2R)-2-hydroxy-Cn-long-chain fatty acyl-CoA
Product
2-methyl-branched Cn-1-fatty aldehyde;
formyl-CoA [CPD:C00798];
Cn-1-long-chain fatty aldehyde
Comment
Requires Mg2+ and thiamine diphosphate. This peroxisomal enzyme, found in animals, is involved in the alpha-oxidation of 3-methyl-branched fatty acids like phytanic acid and the shortening of 2-hydroxy long-chain fatty acids.
History
EC 4.1.2.63 created 2021
Orthology
K12261  2-hydroxyacyl-CoA lyase
Genes
HSA26061(HACL1)
PTR743738(HACL1)
PPS100982158(HACL1)
GGO101130205(HACL1)
PON100457302(HACL1)
PPYG129033966(HACL1)
NLE100589385(HACL1)
HMH116462043(HACL1)
SSYN129491329(HACL1)
MCC694261(HACL1)
MCF102130550(HACL1)
MTHB126946855
MNI105490407(HACL1)
CSAB103241708(HACL1)
CATY105578325(HACL1)
PANU101016987(HACL1)
TGE112617609(HACL1)
MLEU105538148(HACL1)
RRO104656450(HACL1)
RBB108535627(HACL1)
TFN117084204(HACL1)
PTEH111539503(HACL1)
CANG105505757(HACL1)
CJC100385052(HACL1)
SBQ101042137(HACL1)
CIMI108299907(HACL1)
ANAN105727097(HACL1)
CSYR103249270(HACL1)
MMUR105872704(HACL1)
LCAT123628571(HACL1)
PCOQ105826259(HACL1)
OGA100942962(HACL1)
MMU56794(Hacl1)
MCAL110309041(Hacl1)
MPAH110325771(Hacl1)
RNO85255(Hacl1)
MCOC116084402(Hacl1)
ANU117706255(Hacl1)
ASYL127690588(Hacl1)
MUN110551269(Hacl1)
CGE100767514(Hacl1)
MAUA101844934(Hacl1)
PROB127217007(Hacl1)
PLEU114708165(Hacl1)
MORG121455236(Hacl1)
MFOT126499145
AAMP119827425(Hacl1)
NGI103747520(Hacl1)
HGL101706829(Hacl1)
CPOC100731806(Hacl1)
CCAN109694810(Hacl1)
DORD105989902(Hacl1)
DSP122107948(Hacl1)
DMER138824648(Hacl1)
PLOP125358624(Hacl1)
NCAR124968501
MMMA107149652(Hacl1)
ITI101961946(Hacl1)
OCU100342558
OPI101524332(HACL1)
TUP102488706(HACL1)
GVR103595212(HACL1)
CFA608697
CLUD112660940(COLQ)
VVP112925619(HACL1)
VLG121478711(HACL1)
NPO129507342(HACL1)
AML100483076(HACL1)
UMR103679362(HACL1)
UAH113253912(HACL1)
UAR123788357(HACL1)
ELK111155096
LLV125104689
MPUF101679744(HACL1)
MNP132011775(HACL1)
MLK131824518(HACL1)
NVS122908996(HACL1)
ORO101380715(HACL1)
EJU114205724(HACL1)
ZCA113915823(HACL1)
MLX118003367(HACL1)
NSU110570751(HACL1)
LWW102734410(HACL1)
FCA101093708(HACL1)
PYU121033647(HACL1)
PCOO112849332(HACL1)
PBG122492011(HACL1)
PVIV125175574(HACL1)
LRUF124526159
LGF123611588(HACL1)
AJU106971590
PTG102951290(HACL1)
PPAD109258811(HACL1)
PUC125921333
PLEZ122229710(HACL1)
HHV120238469(HACL1)
BTA512676(HACL1)
BOM102283180(HACL1)
BIU109561790(HACL1)
BBUB102399404(HACL1)
BBIS105000735(HACL1)
CHX102182450(HACL1)
OAS101119009(HACL1)
BTAX128046078(HACL1)
CSUM138078184(HACL1)
ODA120880360(HACL1)
CCAD122445507(HACL1)
MREE136173630(HACL1)
MBEZ129549457(HACL1)
SSC100518218(HACL1)
CFR102508961(HACL1)
CBAI105077623(HACL1)
CDK105096613(HACL1)
VPC102525121(HACL1)
BACU103005299(HACL1)
BMUS118893900(HACL1)
LVE103081479(HACL1)
OOR101278567(HACL1)
LALB132520839(HACL1)
GMF115863478(HACL1)
DLE111168157(HACL1)
PCAD102980162(HACL1)
PSIU116753296(HACL1)
PPHC136122525(HACL1)
NASI112401406(HACL1)
ECB100063920(HACL1)
EPZ103561485(HACL1)
EAI106842763(HACL1)
MYB102259094(HACL1)
MYD102760568(HACL1)
MMYO118668201(HACL1)
MLF102419042(HACL1)
MDT132215583(HACL1)
MYUM139022336(HACL1)
PKL118715364(HACL1)
EFUS103296694(HACL1)
MNA107542410(HACL1)
DRO112309688(HACL1)
SHON118997591(HACL1)
AJM119048308(HACL1)
PDIC114501580(HACL1)
PHAS123830654(HACL1)
MMF118633385(HACL1)
PPAM129088236(HACL1)
HAI109395823(HACL1)
RFQ117037187(HACL1)
PALE102884140(HACL1)
PGIG120582055(HACL1)
PVP105288363(HACL1)
RAY107508452(HACL1)
MJV108390849(HACL1)
TOD119256849(HACL1)
SARA101543974(HACL1)
SFUM130037739(HACL1)
SETR125997954(HACL1)
LAV100667352(HACL1)
TMU101354112
ETF101648042(HACL1)
DNM101437479(HACL1)
MDO100030500(HACL1)
GAS123250584(HACL1)
SHR100916928(HACL1)
AFZ127539116
PCW110209056(HACL1)
TVP118850418(HACL1)
PBRV138161655(HACL1)
MLAO141494504(HACL1)
OAA100084023(HACL1)
TACU119921985(HACL1)
GGA420638(HACL1)
PCOC116227085(HACL1)
MGP100542074(HACL1)
CJO107309164(HACL1)
TPAI128086214(HACL1)
LMUT125696480(HACL1)
NMEL110394950(HACL1)
APLA101798319(HACL1)
ACYG106030248(HACL1)
CATA118252779(HACL1)
AFUL116486217(HACL1)
TGU100232217(HACL1)
LSR110474620(HACL1)
SCAN103812914(HACL1)
PMOA120502665(HACL1)
OTC121339586(HACL1)
PRUF121352912(HACL1)
ATRC139591096(HACL1)
GFR102037543(HACL1)
FAB101821112(HACL1)
OMA130249060(HACL1)
PHI102104383(HACL1)
PMAJ107199916(HACL1)
CCAE111923442(HACL1)
CCW104689075(HACL1)
CBRC103614161(HACL1)
ACOE138106516(HACL1)
ETL114055681(HACL1)
ZAB102070040(HACL1)
ZLE135443843(HACL1)
ACHL103801685(HACL1)
SVG106864264(HACL1)
MMEA130573229(HACL1)
HRT120760589(HACL1)
SATI136361502(HACL1)
CCIC134045937(HACL1)
FPG101915302(HACL1)
FCH102057939(HACL1)
CCRI104160177
NNT104408971(HACL1)
SHAB115618352(HACL1)
ACUN113476794(HACL1)
TALA104358157(HACL1)
ACHC115339770(HACL1)
HALD104313638(HACL1)
HLE104843120(HACL1)
AGEN126038077
HHAR128146956(HACL1)
GCL127013652
LDI104349001
MNB103771331(HACL1)
DPUB104307537(HACL1)
PPUS135187986(HACL1)
AVIT104275262(HACL1)
BRHI104498511(HACL1)
EGZ104126084(HACL1)
NNI104013970(HACL1)
PCRI104032401(HACL1)
PCAO104050212(HACL1)
PADL103918430(HACL1)
AFOR103906681(HACL1)
FGA104074755(HACL1)
GSTE104257112(HACL1)
CBOY140648273(HACL1)
CLV102085572(HACL1)
CNIC135984837(HACL1)
MUI104539747(HACL1)
PGUU104461122(HACL1)
PLET104616668(HACL1)
EHS104510634(HACL1)
CMAC104473038(HACL1)
CUCA104059184(HACL1)
TEO104375456(HACL1)
BREG104637546
OHA104333338(HACL1)
ACAR104518009(HACL1)
CPEA104397634(HACL1)
CVF104289911(HACL1)
RTD128905283(HACL1)
CRID134511338(HACL1)
AAM106483474(HACL1)
AROW112977277(HACL1)
NPD112957212(HACL1)
TGT104568401(HACL1)
DNE112985274(HACL1)
SCAM104145126(HACL1)
ASN102372627(HACL1)
AMJ102569780(HACL1)
CPOO109310399(HACL1)
GGN109291599(HACL1)
PSS102457478(HACL1)
CMY102946745(HACL1)
CCAY125631589(HACL1)
DCC119850377(HACL1)
CPIC101939557(HACL1)
TST117872359(HACL1)
CABI116837022(HACL1)
MRV120398934(HACL1)
ACS100557174(hacl1)
ASAO132778718(HACL1)
PVT110072147(HACL1)
SUND121934086(HACL1)
PBI103048759(HACL1)
PMUR107282910(HACL1)
CTIG120307310(HACL1)
TSR106545060(HACL1)
PGUT117655106(HACL1)
APRI131196703(HACL1)
PTEX113441307(HACL1)
NSS113415958(HACL1)
VKO123033833(HACL1)
PMUA114607097(HACL1)
PRAF128398463(HACL1)
ZVI118092350(HACL1)
HCG128330448(HACL1)
GJA107126170(HACL1)
STOW125441283(HACL1)
EMC129337493(HACL1)
XLA446657(hacl1.L)
XTR550086(hacl1)
NPR108802925(HACL1)
ACAT141144469(HACL1)
BBUF121002206(HACL1)
BGAR122938311(HACL1)
DTC141053688(HACL1)
PWL138262234(HACL1)
MUO115469822(HACL1)
GSH117354009(HACL1)
DRE406358(hacl1)
SRX107743162 107745383
SANH107684560 107685543
SGH107550801 107596724(hacl1)
CCAR109106433(hacl1)
CAUA113116276(hacl1)
CGIB127975224
PTET122360337(hacl1)
LROH127178744(hacl1)
GRF141342399(hacl1)
OMC131521729(hacl1)
PPRM120495103(hacl1)
RKG130070141(hacl1)
MAMB125243141(hacl1)
CIDE127496887
CERY137031336(hacl1)
MASI127454326
TROS130557861(hacl1)
TDW130433557(hacl1)
MANU129448009(hacl1)
PDAB135743551(hacl1)
IPU108267388
IFU128609235(hacl1)
PHYP113542549(hacl1)
SMEO124385334(hacl1)
TFD113644391(hacl1)
TVC132846001(hacl1)
CGAR128520941(hacl1)
NGRA132886755(hacl1)
TRN134310734(hacl1)
AMEX125802460(hacl1)
CMAO118816486(hacl1)
EEE113571243(hacl1)
CHAR105891974(hacl1)
SPIL134082386(hacl1)
TRU101061718(hacl1)
TFS130532614(hacl1)
TNGGSTEN00034133G001
LCO104927751(hacl1)
NCC104944968(hacl1)
TBEN117480344(hacl1)
CGOB115021252(hacl1)
PGEO117461424(hacl1)
GACU117554061(hacl1)
EMAC134861315(hacl1)
ELY117265388(hacl1)
EFO125893706(hacl1)
PLEP121945760(hacl1)
SLUC116049391(hacl1)
ECRA117946488(hacl1)
ESP116691366(hacl1)
PFLV114557200(hacl1)
GAT120811025(hacl1)
PPUG119198104(hacl1)
AFB129109251(hacl1)
CLUM117745899(hacl1)
PSWI130212618(hacl1)
CANA137781607(hacl1)
CVE137891523(hacl1)
MSAM119897754(hacl1)
SCHU122881383(hacl1)
CUD121513857(hacl1)
SPUL138584351(hacl1)
LMIX132984104(hacl1)
ALAT119006461(hacl1)
ASTR137601971(hacl1)
MZE101465513(hacl1)
ONL100690060(hacl1)
OAU116325395(hacl1)
OLA101156193(hacl1)
OML112143126(hacl1)
CSAI133429710(hacl1)
XMA102223303(hacl1)
XCO114142081(hacl1)
XHE116717578(hacl1)
PRET103478561(hacl1)
PFOR103150389 103150392
PLAI106941218 106955235
PMEI106922205(hacl1)
GAF122831424
PPRL129371152(hacl1)
CVG107103875(hacl1)
CTUL119772782(hacl1)
GMU124865949(hacl1)
NFU107378691(hacl1)
KMR108241945(hacl1)
ALIM106517744(hacl1)
NWH119409454(hacl1)
AOCE111588844(hacl1)
EJA138194334(hacl1)
BFRE138619584(hacl1)
MCEP125015938(hacl1)
CSEM103388412(hacl1)
POV109633118(hacl1)
SSEN122774464(hacl1)
SSOE131471501(hacl1)
HHIP117777286(hacl1)
HSP118114372(hacl1)
PPLT128449439(hacl1)
SMAU118313967(hacl1)
LCF108891319
SDU111238787(hacl1)
SLAL111652800(hacl1)
XGL120784806(hacl1)
HCQ109525685(hacl1)
SSCV125975603(hacl1)
SBIA133501329(hacl1)
PEE133401696(hacl1)
PTAO133479457(hacl1)
BPEC110171659(hacl1)
ENY140346043 140374245(hacl1) 140375886
MALB109967232(hacl1)
BSPL114843450(hacl1)
SJO128366484(hacl1)
SSCO133983063(hacl1)
GMH115554133(hacl1)
SASA106592607(hacl1) 106596819
STRU115187725 115187759
OTW112225223(hacl1)
OMY110505030(hacl1) 110515045 118936608
OGO124019490 124023920
OKI109876961 116365063
OKE118380248(hacl1)
OMM135538528(hacl1)
OCLA139387186 139404897 139404925
SALP111971452(hacl1)
SNH120038022 120040290
CCLU121577404 121586943(hacl1)
ELS105018820(hacl1)
OEP134024211(hacl1)
SFM108927371(hacl1)
PKI111839032(hacl1)
AANG118212187(hacl1)
AROT135261805(hacl1)
CCOG133133750(hacl1)
LOC102687234(hacl1)
PSPA121315127(hacl1)
ARUT117394717(hacl1)
PSEX120515400(hacl1)
LCM102362798(HACL1)
CMK103181261(hacl1)
RTP109933345(hacl1)
CPLA122549928(hacl1)
HOC132816078(hacl1)
LERI129710056(hacl1)
HAKA140732166(hacl1)
PMRN116948202(HACL1)
LRJ133345175(HACL1)
BFO118407296
BBEL109468963
CIN100178631
SCLV120341709
SPU586415
LPIC129274217
AJJ139958863
APLC110973383
ARUN117299838
AAMU139948701
AFIL140151434 140151587
AJC117104185
SKO100370616(HACL1)
PFLL139148198
DMEDmel_CG11208(Hacl)
DER6547754
DSE6610038
DSIDsimw501_GD25296(Dsim_GD25296)
DYADyak_GE13819
DAN6496000
DSR110183103
DPO4805546
DPE6600980
DMN108160101 117192789
DWI6640896
DGR6568724
DMODmoj_GI18529
DAZ108616686
DNV108654972
DHE111594678
DVI6625321(Hacl)
CCAT101448871
BOD106624777
BDR105224676
RZE108367644
AOQ129244539
ALUD128868517
TDA119680124 119685324
SCAC106096256
LCQ111684644
LSQ119608012
CVJ135960208(Hacl)
GFS119641353
ECOE129950059
CLON129614126
HIS119654366
AGA1272675
ACOZ120956444
AARA120902070
AMER121599382 121602677
ASTE118506300
AMAP126557577
AFUN125771062
AMOU128299765
AMRS128710177
AALI118465009
ACOS131271185
AAG5565030 5572369
AALB109398509
ASUA134220414
CQUCpipJ_CPIJ014172 CpipJ_CPIJ017705
CPII120417246
CBRI134827298 134836448
CNS116340071
BCOO119066566
LLL129797288
PPAP129799177
AME552738
ACER107995125
ALAB122717988
ADR102673058
AFLR100867800
BIM100744016
BBIF117207092
BVK117237409
BVAN117160978
BHUN126863363
BTER100644973
BAFF126917186
BPYO122572768
BPAS132906822
FVI122535468
CCAL108629887
OBB114878797
OLG117602462
MGEN117229721
NMEA116434819
CGIG122404927
SOC105194976
MPHA105836739
AEC105154992
ACEP105626893
ACOC108688382
MZT108729186(Hacl)
PBAR105426340
VEM105566829
COBS139104639(Hacl)
TLN139814446(Hacl)
HST105189078
DQU106750369
CFO105255983
FEX115243773
PMEC138942410(Hacl)
LHU105669841(Hacl)
PGC109857866
OBO105282994
PCF106784580
PFUC122516260
VPS122627482
VCRB124422523
VVE124947528
NVI100123260
CSOL105361881
TPRE106658765
LHT122501395
LBD127283454
MDL103573582
CGLO123270220
CTYP141533596(Hacl)
FAS105272077
DAM107038575
AGIF122855352
CINS118066738 118066746 118069709
VCAN122408023
CCIN107263840
DSM124415425
NPT124215150(Hacl)
NFB124178108
NLO107219405
NVG124300342
AROA105684491
TCA664029
TMOL138138240(Hacl)
DPA109536893
ESIM136416833(Hacl)
EFOR136347411(Hacl)
SOY115884215
AGRG126737969
ATD109596968
CSET123317367
HAXR123683509
AGB108903720
LDC111511260
DVV126888127
NVL108560626
APLN108742675
PPYR116180506
OTU111426368
BMOR692884
BMAN114245011
MSEX115455821
DPLKGM_216038
BANY112045363
MJU123874087
NIQ126771840
VCD124536716
MCIX123660708
PMAC106707335 106712100
PPOT106110820
PXU106126854
BPHI137918623(Hacl)
PRAP110998130
PBX123713017
PNAP125060876
ZCE119839860
CCRC123697728
LSIN126966229
AAGE121735380
HAW110380221
HZE124638887
TNL113492403
SLIU111353800
OFU114354508
ONU135078882
ATRA106142233
GMW113515963
PXY105381789
PGW126373626
LGLY125230822
CSTB134746602
CFUM141441005(Hacl)
CFEL113377167
CCRN123300906
API100165444
DNX107163705
AGS114132285
RMD113551822
ACOO126847115
DVT126895664
BTAB109042181
DCI103515657
CLEC106674218
HHAL106686454(Hacl)
NLU111047026
HVI124362007
MQU128990225
PHUPhum_PHUM529400
FOC113211311
TPAL117654372
ZNE110831053
CSEC111868986
PAME138700261 138700262
SGRE126335352
BROR134542661
IEL124164359
HAMR139696717 139698310
FCD110848423
DPXDAPPUDRAFT_253560 DAPPUDRAFT_306512
DMK116930937
DPZ124348925
AFRA136026541
PVM113829823(Hacl)
PJA122259379
PCHN125032303
PMOO119597108
HAME121861697
PCLA123761322
CQD128689615(Hacl)
PTRU123499102
ESN127009089
MNZ135207748
MRJ136830645(Hacl)
PORN139756546
EAF111696878
TCF131884062
PPOI119105814 119106411
DSV119442762
RSAN119387927 119387928
RMP119188213
VDE111248283
VJA111271184
GOE100905806
CSCU111629264
CVS136976171(Hacl)
PTEP107455176
ABRU129956781
UDV129223799
SDM118180287 118202574
LPOL106471573
CELCELE_B0334.3(hacl-1)
CBRCBG_02874
CRQGCK72_005332
NAINECAME_12882
LGILOTGIDRAFT_207618
PVUL126831466
PCAN112564745
LSAX138981704
BGT106078649
GAE121382197
HRF124141592
HRJ124281687
HASI137256559
HCRA139470023
CRG105325181
CANU128189203
CVN111106696
MYI110449719
PMAX117343704
AIRR138314297
MCAF127728519
MMER123531889 128546649
RPHI132760561
DPOL127855304
MAEA128241824 128244020
OBI106872707
OSN115212767
LJP135478224
LAK106162962 106178375
LLON135500469
NVE5509052
EPA110232378 110241064 110251089
ATEN116307823
ADF107339514 107349360
AMIL114965786
PDAM113664752
SPIS111333468
DGT114536270
HSY130621646
RES135691295
AQU100641768
ATHAT5G17380
ALY9309892
CRB17882398
CSAT104706028 104735774 104770038
EUSEUTSA_v10013104mg
BRP103833165
BNA106445967 106445973
BOE106318756
RSZ108817706
THJ104820853
CPAP110807471
CIT102621022
CICCICLE_v10011371mg CICLE_v10011616mg
PVY116111220
MINC123197953 123225748
TCC18601969
GRA105803616
GHI107912763 107912909
GAB108453368
HSYR120139211 120196639
DZI111305773 111314659
EGR104449677
RARG115738757
GMX100778257 100781584
GSJ114384324 114397553
PVU137823603
VRA106765165
VAR108338133
VUN114195378
VUM124842392
CCAJ109796119
APRC113847006
MTR25495093
TPRA123906672
CAM101501749
PSAT127118840
VVO131652686
LJA130739156
ADU107489982
AIP107644561
AHF112751450 112801899
LANG109347251
PCIN129322071
QSAO6P43_005651 O6P43_009312
FVE101306541
AANS126787447
RCN112195257
PPER18784460
PMUM103328654
PAVI110764468
PDUL117621238
MDM103405762 103421889
MSYL126583168 126609676
PXB103936009 103948272
PCOX137708055 137739411
ZJU107409054
MNT21409733
CSAV115722296
CSV101218890
CMO103487508
BHJ120082736
MCHA111024979
CMAX111492838
CMOS111452318 111457768
CPEP111788701 111790346
RCU8265016
MEAN126678086
JCU105638783
HBR110659002
MESC110631370
POP7477453
PEU105133039
PALZ118055950
PNZ133699221
JRE108988141
CILL122302852
CAVE132182769
AGLU133859324
QSU112028189
QLO115975759
TWL119995081 119998680
VVI100232933
VRI117930698
SLY101264774
SPEN107011723
SOT102604551
SSTN125846875
SDUL129872273
CANN107860091
LBB132623613
NTA107781829 107825460
NSY104211662 138886522
NTO104096832
NAU109243823
INI109154528
ITR116016327
SIND105176140
OEU111401032
EGT105961104
SSPL121746641 121750258 121779556 121783055
SMIL131014698
SHIS125214766 125214936
APAN127242133
HPUM140894613
PHUA140969312 140974313
PEBU140803430 140806074
HAN110868206
ECAD122603179
LSV111903096
CCAV112501516
DCR108196317
CSIN114315157
RVL131302583
AEW130769124
DLT127810071
BVG104906480
SOE110801650
CQI110703946 110720354
ATRI130802255
MOF131146019
NNU104613342
MING122068615
TSS122645871 122650155
PSOM113282348 113341018 113355684
OSA4324491(2-HPCL)
OBR102721129
OGL127773731
BDI100829473
ATS109738743
TDC119270248 119278317
TAES123063247 123072164 123080437
TUA125545867
LPER127308411
LRD124691323 124691726
SBI8056536
ZMA100191888
MFLO136461640
SITA101779082
SVS117857218
PVIR120672655 120705520
PHAI112895441
PAUA133888168
TANG140773897
PDA103705628 103715163
EGU105047067 105047158
MUS103992223
ZOF122002304 122006560 122026853 122028908
DCT110114604 114579507
PEQ110035637
AOF109829098
MSIN131234684
ACAK137936921
NCOL116248481
ATR18428183
CJF131075395
SMOSELMODRAFT_178690 SELMODRAFT_179619
PPP112279961
CSLCOCSUDRAFT_18867
APROF751_4156
GSLGasu_12440
SCEYEL020C(PXP1)
SEUBDI49_1382
SPAOSPAR_E00510
AGOAGOS_AEL055C
ERCEcym_1360
LTHKLTH0H14102g
VPOKpol_1061p50
ZROZYRO0E03454g
CGR2891496(GVI51_M03113)
NCSNCAS_0G03960(NCAS0G03960)
NDINDAI_0G00520(NDAI0G00520)
TPFTPHA_0B03940(TPHA0B03940)
TBLTBLA_0C01560(TBLA0C01560)
TGBHG536_0G03620
TDLTDEL_0B05520(TDEL0B05520)
KAFKAFR_0H02890(KAFR0H02890)
KNGKNAG_0H01580(KNAG0H01580)
ZMKHG535_0B03790
SLUDSCDLUD_003407
PPAPAS_chr1-1_0394
OPAHPODL_00543
YLI2912435(YALI2_E01615g)
SLBAWJ20_180
SSLSS1G_07774
BFUBCIN_15g01860
MBEMBM_05575
PSCOLY89DRAFT_234715
GLZGLAREA_03030
ANIANIA_10214
AFMAFUA_8G05230
ACTACLA_058670
NFINFIA_097990
AORAO090005000624
ANGAn16g07490
AFVAFLA_003432
ALUCAKAW2_70591S
ACHEACHE_60592S
APUUAPUU_21693S
CIMCIMG_04305
CPW9697376(D8B26_003681)
UREUREG_01556
ABEARB_06558
TVETRV_04424
PBLPAAG_11932(PAAG_04811)
PBNPADG_11446
AJEHCAG_02805
BGHBDBG_04203
ZTRMYCGRDRAFT_100226
PFJMYCFIDRAFT_158085
CBETCB0940_11906
NPAUCRNP2_5114
TMLGSTUM_00003438001
SPO2541142(hac1)
SOMSOMG_01328(hac1)
RIEOCT59_019746
DDIDDB_G0292402
DPPDICPUDRAFT_156484
DFADFA_00674
ACANACA1_369090
TETTTHERM_00503839
PTMGSPATT00010458001
METRBSY238_2193
TBHTbon_01510
TFLAO0235_12075(oxc)
 » show all
Reference
1  [PMID:10468558]
  Authors
Foulon V, Antonenkov VD, Croes K, Waelkens E, Mannaerts GP, Van Veldhoven PP, Casteels M
  Title
Purification, molecular cloning, and expression of 2-hydroxyphytanoyl-CoA lyase, a peroxisomal thiamine pyrophosphate-dependent enzyme that catalyzes the carbon-carbon bond cleavage during alpha-oxidation of 3-methyl-branched fatty acids.
  Journal
Proc Natl Acad Sci U S A 96:10039-44 (1999)
DOI:10.1073/pnas.96.18.10039
  Sequence
[hsa:26061]
Reference
2  [PMID:15644336]
  Authors
Foulon V, Sniekers M, Huysmans E, Asselberghs S, Mahieu V, Mannaerts GP, Van Veldhoven PP, Casteels M.
  Title
Breakdown of 2-hydroxylated straight chain fatty acids via peroxisomal 2-hydroxyphytanoyl-CoA lyase: a revised pathway for the alpha-oxidation of straight chain fatty acids.
  Journal
J Biol Chem 280:9802-12 (2005)
DOI:10.1074/jbc.M413362200
Reference
3  [PMID:17956236]
  Authors
Casteels M, Sniekers M, Fraccascia P, Mannaerts GP, Van Veldhoven PP
  Title
The role of 2-hydroxyacyl-CoA lyase, a thiamin pyrophosphate-dependent enzyme, in the peroxisomal metabolism of 3-methyl-branched fatty acids and 2-hydroxy straight-chain fatty acids.
  Journal
Biochem Soc Trans 35:876-80 (2007)
DOI:10.1042/BST0350876
Other DBs
ExplorEnz - The Enzyme Database: 4.1.2.63
IUBMB Enzyme Nomenclature: 4.1.2.63
ExPASy - ENZYME nomenclature database: 4.1.2.63
BRENDA, the Enzyme Database: 4.1.2.63

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