Entry
Name
methylmalonyl-CoA epimerase;
methylmalonyl-CoA racemase;
methylmalonyl coenzyme A racemase;
DL-methylmalonyl-CoA racemase;
2-methyl-3-oxopropanoyl-CoA 2-epimerase [incorrect]
Class
Isomerases;
Racemases and epimerases;
Acting on other compounds
BRITE hierarchy
Sysname
methylmalonyl-CoA 2-epimerase
Reaction(IUBMB)
(R)-methylmalonyl-CoA = (S)-methylmalonyl-CoA [RN:
R02765 ]
Reaction(KEGG)
Substrate
(R)-methylmalonyl-CoA [CPD:
C01213 ]
Product
(S)-methylmalonyl-CoA [CPD:
C00683 ]
History
EC 5.1.99.1 created 1965, modified 1981
Pathway
ec00280 Valine, leucine and isoleucine degradation
ec00630 Glyoxylate and dicarboxylate metabolism
ec00720 Other carbon fixation pathways
ec01120 Microbial metabolism in diverse environments
Orthology
K05606 methylmalonyl-CoA/ethylmalonyl-CoA epimerase
Genes
PPYG : 129014590 129030270(MCEE)
MCC : 106997075 704094(MCEE)
MNI : 105465241(MCEE) 105468152
CATY : 105576556(MCEE) 105579993
NCAR : 124962107 124977182
BTAX : 128066855 128066857
SARA : 101552491(MCEE) 101554909
SETR : 125999473 126021848(MCEE)
SRX : 107736368 107750491 107755054
SANH : 107670763 107700438
PTET : 122347862(mcee) 122349504
MASI : 127409749 127438841
CSAI : 133420478 133461298
SASA : 106562156(mcee) 106587249
STRU : 115167359 115202993
OTW : 112235776 112249131(mcee)
OMY : 110506431 110526316(mcee)
OGO : 124033139(mcee) 124035806
OKI : 109886769(mcee) 109895448
SALP : 111974749(mcee) 112067775
SNH : 120025160 120056032(mcee)
CCLU : 121559311 121560434
PSPA : 121294856 121299281
ARUT : 117428198 117429709
PPOI : 119090436 119090529
RSAN : 119378672 119394121
CBR : CBG_11959(Cbr-mce-1)
CRQ : GCK72_000089 GCK72_000972
PMAX : 117319022 117319023 117333859
AQU : 100637435 100641619 100641874 100641999
GSL : Gasu_25180 Gasu_44010
MBRN : 26241232(G6M90_00g095210)
LMAT : 92514043(LSCM1_04005)
LOI : 92360895(LSCM4_04986)
LEIS : 94180410(GH5_04999)
LENR : 94170986(CUR178_03747)
LEIN : 94188563(JIQ42_04915)
TVA : TVAG_2v0965190 TVAG_2v0983900
OSG : BST96_07520 BST96_11065 BST96_19455
HJA : BST95_12165 BST95_13460
HALC : EY643_01215 EY643_10235(mce) EY643_12830
PAQM : E0F26_01840 E0F26_08820(mce)
MESU : LHFGNBLO_003296(mce)
SAME : SAMCFNEI73_Ch1397 SAMCFNEI73_pB0192
ASAL : CFBP5507_21105(mce)
RPUS : CFBP5875_16775(mce)
ALEG : CFBP4996_17470(mce)
RLT : Rleg2_1277 Rleg2_6135
RTR : RTCIAT899_CH06970(mce)
RLW : RlegWSM1455_06870(mce)
BCAN : BcanWSM471_21890(mce)
MAQU : Maq22A_c02915(gloA)
NOH : G5V57_27800(mce) G5V57_31105
BVIT : JIP62_01480(mce) JIP62_11345
TSV : DSM104635_02066 DSM104635_03083
RLI : RLO149_c035990(mcee)
AHT : ANTHELSMS3_01403 ANTHELSMS3_01735
BOO : E2K80_03725 E2K80_10395(mce)
PPRU : FDP22_09700(mce) FDP22_22010
HDH : G5B40_03340(mce) G5B40_16005
GCE : KYE46_03160 KYE46_06820(mce)
GYJ : AADW23_00620 AADW23_09615(mce)
RHOC : QTA57_09820(mce) QTA57_11435
FAQ : G5B39_12545(mce) G5B39_18500
NRE : BES08_02160 BES08_26595
NDR : HT578_04340(mce) HT578_04345
SPHD : HY78_11030 HY78_26585
RDI : CMV14_01115(mce) CMV14_05495
SSAN : NX02_10695 NX02_28100
SPAN : AWL63_08310 AWL63_13060
SPKC : KC8_05295 KC8_06365 KC8_14110
SLAN : GV829_01820 GV829_12120(mce)
SBIN : SBA_ch1_24740 SBA_ch2_0720
SCH : Sphch_0763 Sphch_3630
SYB : TZ53_05610 TZ53_18340 TZ53_19025
SBD : ATN00_13160 ATN00_17600
SPHT : K426_09225 K426_23979
SHYD : CJD35_12960(mce) CJD35_15615
SYA : A6768_08935(mce) A6768_12290
SUFL : FIL70_06710 FIL70_07765(mce) FIL70_22025
SBAR : H5V43_05865(mce) H5V43_18935
SPAG : sphantq_03340(epi) sphantq_03850
SPCA : GL174_04795(mce) GL174_05755
CIJ : WG74_06130 WG74_11515
SFLA : SPHFLASMR4Y_00818(cetB)
BLAS : BSY18_1006(mce) BSY18_2487
CMAN : A9D14_02385 A9D14_14725
PHZ : CHX26_05375 CHX26_09915(mce)
NTD : EGO55_02015(mce) EGO55_04835
CAEN : K5X80_11450(mce) K5X80_13735
TMK : QGN29_04075 QGN29_12645(mce)
DAV : DESACE_02170 DESACE_06800
GBN : GEOBRER4_05640(mceE)
DLM : DPPLL_19890 DPPLL_38280
ECOM : QTN59_09375(mce) QTN59_19325
DTO : TOL2_C04730 TOL2_C32210 TOL2_C41550
DOV : DSCO28_10390 DSCO28_18580 DSCO28_39210 DSCO28_49000 DSCO28_56480
DALK : DSCA_12240 DSCA_43860 DSCA_54220
DML : Dmul_24350 Dmul_34090(mce)
DLI : dnl_16550(mce) dnl_16800
DMM : dnm_019390 dnm_047430(mce)
SAT : SYN_00683 SYN_01971 SYN_02418
DTI : Desti_1826 Desti_2972 Desti_3852
DMP : FAK_08210 FAK_18690 FAK_23500(mceE) FAK_34510
MRM : A7982_04983 A7982_10444
ABIW : Abiwalacus_17050(mceE)
SMAM : Mal15_36340 Mal15_48420
SNEP : Enr13x_12880 Enr13x_31610
CCOP : Mal65_01300 Mal65_39180
ABA : Acid345_2364 Acid345_3022
PSPC : Strain318_001046(mce)
MGOD : E7746_00055(mce) E7746_02540(mce)
CFAS : Cfast33896_24610(mce)
SCN : Solca_0781 Solca_3069
FCR : HYN56_03245(mce) HYN56_16435
FAZ : M0M57_13400(mce) M0M57_15165(mce)
FCS : TRV642_0656 TRV642_1570
FPEC : Q1W71_15605(mce) Q1W71_19965
ZLA : Q5W13_06490 Q5W13_08180(mce)
PUN : NQP51_01855(mce) NQP51_13440(mce)
PHG : KCTC32516_01044(fosB_1)
POLQ : JOP69_02795(mce) JOP69_13595(mce)
SZE : AW14_01735 AW14_04950
MLIL : QLS71_007205(mce) QLS71_009750(mce)
SPON : HME9304_01467(mceE)
FBE : FF125_16430(mce) FF125_19345(mce)
SAHN : JRG66_07650(mce) JRG66_07950(mce)
SAZS : VS868_06660(mce) VS868_07975(mce)
LUY : QZH61_03030(mce) QZH61_13240(mce)
MANG : RBH95_01130(mce) RBH95_08085(mce)
PTAN : CRYO30217_03364(epi)
BAZ : BAMTA208_12275(yqjC)
BAE : BATR1942_10275 BATR1942_17580
BTF : YBT020_09930 YBT020_25650
BIF : N288_11180 N288_17660
BWH : A9C19_06830 A9C19_08750
BHAI : KJK41_11775 KJK41_14835(mce)
PPSR : I6J18_21065(mce) I6J18_23000
PSYO : PB01_11155(mce) PB01_16780
PSYB : KD050_00750 KD050_01560(mce)
NCM : QNK12_20615(mce) QNK12_22560(mce)
MEKU : HUW50_00100(mce) HUW50_23490 HUW50_24625
MLIT : KDJ21_013970(mce) KDJ21_016950
AIA : AWH56_020525(mce) AWH56_025865(mce)
BLEN : NCTC4824_01787(mce)
RAZ : U9J35_05215(mce) U9J35_14800(mce)
ROSS : V2W31_05260(mce) V2W31_14720(mce)
GAJ : MY490_08040(mce) MY490_10780(mce)
PCAL : BV455_03065(gloA_2)
ANEU : PP175_01385 PP175_08535(mce)
PMAR : B0X71_08035 B0X71_09820 B0X71_09885
SPSY : AZE41_10795 AZE41_12305
SOW : QWT69_07350(mce) QWT69_14255
SJT : PGH26_06635(mce) PGH26_07005
PANC : E2636_07395(mce) E2636_09005
CPRF : K7H06_13580 K7H06_17015(mce)
FWA : DCMF_05750 DCMF_07175
DGI : Desgi_1108 Desgi_1958
IBU : IB211_00599c IB211_02984c
TTE : TTE1219(GloA2) TTE2386(GloA3)
DBC : MFMK1_002302(mce) MFMK1_003572
SELM : TAMA11512_20960(mce)
SSID : SPSIL_019720(epi_1) SPSIL_057090(epi_2)
SACV : SPACI_012060(epi_1) SPACI_019510(epi_2)
EUZ : DVS28_a3736 DVS28_a4273
MMAE : MMARE11_38850(gloA_1)
MHEK : JMUB5695_01717(mce)
MARZ : MARA_48140 MARA_57020(mce)
MCEE : MCEL_03730 MCEL_46850(mce)
MTER : 4434518_01248(gloA_1)
COI : CPCIP5297_04455(mce)
NNO : NONO_c12700 NONO_c27420
NSL : BOX37_12990 BOX37_25235
NSPU : IFM12276_51660(mce)
RRZ : CS378_00025(mce) CS378_11495 CS378_16830
RHOD : AOT96_29940 AOT96_31935
RANT : RHODO2019_03965(mce)
RHOP : D8W71_11290 D8W71_11360 D8W71_21455(mce)
RHOU : KZJ41_04920 KZJ41_11470(mce)
RHOW : A4U64_14355 A4U64_20175
RFA : A3L23_03567 A3L23_04987
SCZ : ABE83_10595 ABE83_21730
SLE : sle_22570(sle_22570)
SGV : B1H19_27645 B1H19_35565
SGD : ELQ87_12680(mce) ELQ87_34855
SCHA : CP983_13765(mce) CP983_20520
SACT : DMT42_22445 DMT42_26775(mce)
SGOB : test1122_19475(mce)
SARG : HKX69_08155 HKX69_10775(mce)
SCYN : N8I84_01000 N8I84_27290(mce)
SARM : DVA86_07185 DVA86_20860(mce)
STSD : HEP87_00840 HEP87_35560(mce)
STRH : GXP74_28575 GXP74_33925(mce)
LYK : FLP23_04925 FLP23_05430
ACIT : HPK19_01830(mce) HPK19_05225(mce)
DCO : SAMEA4475696_0976(gloA)
PAK : HMPREF0675_4166(mce)
PPC : HMPREF9154_1431(mce)
NPC : KUV85_07780(mce) KUV85_14555
AEZ : C3E78_02975 C3E78_12360(mce)
KSL : OG809_31335 OG809_40915(mce)
THAO : NI17_008820 NI17_014830(mce)
TALX : FOF52_05350 FOF52_12180(mce)
AGRA : AGRA3207_002630(mce)
SPIQ : OHA34_06745 OHA34_16615(mce)
ACTQ : OG417_09910(mce) OG417_32020
NOA : BKM31_36335 BKM31_56820
NOW : GBF35_08755(mce) GBF35_39460
NCX : Nocox_08120 Nocox_32370
NGN : LCN96_09095(mce) LCN96_44050
NFS : OIE67_05135 OIE67_37745(mce)
MHAI : OHB01_00770 OHB01_20005(mce)
FSY : FsymDg_1625 FsymDg_3823
FRI : FraEuI1c_3572 FraEuI1c_4196
AJA : AJAP_07620 AJAP_19560
PBRO : HOP40_06080 HOP40_14630(mce)
PSDS : K1T35_40625(mce) K1T35_45235
PMAD : BAY61_24420 BAY61_24640 BAY61_24655 BAY61_24680
ACTY : OG774_11680(mce) OG774_14220
MSAG : GCM10017556_13540(mce)
MCHL : PVK74_09670(mce) PVK74_15770(mce)
MICF : QQG74_01300 QQG74_26155(mce)
ACTR : Asp14428_59940(mce)
PLK : CIK06_16835 CIK06_23025(mce)
PSUU : Psuf_011770 Psuf_047000(mce)
DAUR : Daura_06960(mce) Daura_21160(mce)
BSOL : FSW04_03150(mce) FSW04_25115 FSW04_25240
BALA : DSM104299_05732(epi)
PARQ : DSM112329_05251(epi)
SBAE : DSM104329_01238 DSM104329_05660(epi)
AQZ : KSP35_14100(mce) KSP35_14105
IAM : HC251_09965(mce) HC251_22960(mce)
LEPV : J4558_09290 J4558_18925
TBH : Tbon_11650(mce) Tbon_11660
TFLA : O0235_00700 O0235_00705 O0235_00710(mce)
AST : Asulf_00337 Asulf_00513
HDL : HALDL1_04620 HALDL1_06515
HLU : LT972_10420(mce) LT972_12140
HALX : M0R89_10935(mce) M0R89_15740
HAXZ : M0R88_11175(mce) M0R88_16095
HAXY : NGM07_01235 NGM07_16995(mce)
HMA : rrnAC0635(gloA2) rrnB0232
HHI : HAH_1293(gloA1) HAH_4349
HHN : HISP_06625 HISP_16970
HAB : SG26_00610 SG26_14485
HTA : BVU17_06310 BVU17_15195
HALJ : G9465_08365(mce) G9465_24105
HSIN : KDQ40_07000(mce) KDQ40_16915
NHO : HWV23_00340 HWV23_12745(mce)
NSAL : HWV07_08920 HWV07_14055(mce)
HALE : G3A49_05695 G3A49_10085(mce)
HLN : SVXHx_1342(mce) SVXHx_4113(gloa2)
HME : HFX_1453(gloA) HFX_6362(gloA)
HGI : ABY42_06745 ABY42_17410
HLS : KU306_11680(mce) KU306_18740
HAER : DU502_10980(mce) DU502_17035
HALP : DOS48_05595(mce) DOS48_13860
HEZZ : EO776_07345(mce) EO776_16250
HALQ : Hrr1229_000110(mce)
HSAL : JMJ58_14065 JMJ58_19005(mce) JMJ58_22935
NAY : HYG81_02440(mce) HYG81_24775
HALY : HYG82_05550(mce) HYG82_20200
HJT : DVR14_18605(mce) DVR14_22740(mce)
HRU : Halru_1810 Halru_2428
SAWL : NGM29_08980 NGM29_13830(mce) NGM29_18775 NGM29_18785 NGM29_18825
HALV : NGM15_01135 NGM15_05110(mce)
HLR : HALLA_02585 HALLA_12720
HLC : CHINAEXTREME02570 CHINAEXTREME13325
NAJ : B1756_07145 B1756_14235
NAS : GCU68_14420(mce) GCU68_16840
NBV : T478_0162 T478_0629(mce)
» show all
Taxonomy
Reference
Authors
MAZUMDER R, SASAKAWA T, KAZIRO Y, OCHOA S.
Title
Metabolism of propionic acid in animal tissues. IX. Methylmalonyl coenzyme A racemase.
Journal
J Biol Chem 237:3065-8 (1962)
Reference
Authors
OVERATH P, KELLERMAN GM, LYNEN F, FRITZ HP, KELLER HJ.
Title
[On the mechanism of the rearrangement of methylmalonyl-Co A into succinyl-Co A. II. Experiments on the mechanism of action of methylmalonyl-Co A isomerase and methylmalonyl-Co A racemase.]
Journal
Biochem Z 335:500-18 (1962)
Other DBs
ExplorEnz - The Enzyme Database: 5.1.99.1
ExPASy - ENZYME nomenclature database: 5.1.99.1