KEGG ORTHOLOGY: K18165

ORTHOLOGY: K18165

Entry

K18165                      KO

Symbol

TMEM126B

Name

complex I assembly factor TMEM126B

Disease

H00473

Mitochondrial complex I deficiency

Brite

KEGG Orthology (KO) [BR:ko00001]
09180 Brite Hierarchies
  09182 Protein families: genetic information processing
   03029 Mitochondrial biogenesis
    K18165  TMEM126B; complex I assembly factor TMEM126B
Mitochondrial biogenesis [BR:ko03029]
Mitochondrial quality control factors
  Mitochondrial respiratory chain complex assembly factors
   Complex-I assembly factors
    K18165  TMEM126B; complex I assembly factor TMEM126B

Genes

HSA:	55863(TMEM126B)

PTR:	749051(TMEM126B)

PPS:	100977453(TMEM126B) 100985422

GGO:	101130565(TMEM126B)

PON:	100440737(TMEM126B)

NLE:	100587654(TMEM126B)

HMH:	116477259(TMEM126B)

MCC:	702719(TMEM126B)

MCF:	101865616(TMEM126B)

MTHB:

126934925

MNI:	105468950(TMEM126B)

CSAB:

103248136(TMEM126B)

CATY:

105592927(TMEM126B)

PANU:

101005907(TMEM126B)

TGE:	112605704(TMEM126B)

MLEU:

105543149(TMEM126B)

RRO:	104660699(TMEM126B)

RBB:	108514592(TMEM126B)

TFN:	117072787 117081461(TMEM126B)

PTEH:

111540773(TMEM126B)

CANG:

105509324(TMEM126B)

CJC:	100414191(TMEM126B)

SBQ:	101034557(TMEM126B)

CIMI:

108290755(TMEM126B)

CSYR:

103258016(TMEM126B)

MMUR:

105856799(TMEM126B)

LCAT:

123641158(TMEM126B)

PCOQ:

105808223(TMEM126B)

OGA:	100942426(TMEM126B)

MMU:	68472(Tmem126b)

MCAL:

110298671(Tmem126b)

MPAH:

110318983(Tmem126b)

RNO:	293114(Tmem126b)

MCOC:

116102562(Tmem126b)

ANU:	117724223(Tmem126b)

MUN:	110552590(Tmem126b)

CGE:	100760417(Tmem126b)

MAUA:

101839828(Tmem126b)

PROB:

127227897(Tmem126b)

PLEU:

114695936(Tmem126b)

MORG:

121448292(Tmem126b)

MFOT:

126508909

AAMP:

119802631(Tmem126b)

HGL:	101706998 101711031(Tmem126b) 106007788

CPOC:

100732563(Tmem126b)

CCAN:

109697159(Tmem126b)

DORD:

105983862(Tmem126b)

DSP:	122116811(Tmem126b)

PLOP:

125345350 125362096(Tmem126b) 125363012

NCAR:

124958964

MMMA:

107135455(Tmem126b)

OCU:	100343876 100345213 100355385

OPI:	101521489(TMEM126B)

TUP:	102469243(TMEM126B)

GVR:	103590129(TMEM126B)

CFA:	485156(TMEM126B)

CLUD:

112642082(TMEM126B)

VVP:	112932317(TMEM126B)

VLG:	121475958(TMEM126B)

NPO:	129506549(TMEM126B) 129515849

AML:	100467564(TMEM126B)

UMR:	103675340(TMEM126B)

UAH:	113269388(TMEM126B)

UAR:	123803849(TMEM126B)

ELK:	111151039 111154428

LLV:	125078431 125091674 125104835

MPUF:

101692289(TMEM126B)

MNP:	132012020(TMEM126B)

MLK:	131839918(TMEM126B)

NVS:	122912529(TMEM126B)

ORO:	101370905(TMEM126B)

EJU:	114226591(TMEM126B)

ZCA:	113913520(TMEM126B)

MLX:	118004279(TMEM126B)

NSU:	110577233(TMEM126B)

LWW:	102726882 102727407(TMEM126B)

FCA:	101097665(TMEM126B)

PYU:	121039478(TMEM126B)

PCOO:

112865489(TMEM126B)

PBG:	122483268(TMEM126B)

PVIV:

125176234(TMEM126B)

LRUF:

124505855

PTG:	102972639(TMEM126B)

PPAD:

109267287(TMEM126B)

PUC:

125914676

AJU:

106977375

HHV:	120220055(TMEM126B) 120230516

BTA:	504229(TMEM126B)

BOM:	102267354(TMEM126B)

BIU:	109554633(TMEM126B)

BBUB:

102392402(TMEM126B)

BBIS:

104998148(TMEM126B)

CHX:	102189833(TMEM126B)

OAS:	101104615(TMEM126B)

BTAX:

128069005(TMEM126B)

ODA:	120874252(TMEM126B)

CCAD:

122430678(TMEM126B) 122444287

MBEZ:

129549061(TMEM126B)

SSC:	100626990(TMEM126B)

CFR:	102508867(TMEM126B)

CBAI:

105083540(TMEM126B)

CDK:	105097732(TMEM126B)

VPC:	102537852(TMEM126B)

BACU:

103008205(TMEM126B)

BMUS:

118900102(TMEM126B)

LVE:	103080541(TMEM126B)

OOR:	101273200(TMEM126B)

DLE:	111184934(TMEM126B)

PCAD:

102980790(TMEM126B)

PSIU:

116757969(TMEM126B)

NASI:

112412115(TMEM126B)

ECB:	100061424(TMEM126B)

EPZ:	103564297(TMEM126B)

EAI:	106848255(TMEM126B)

MYB:	102251021(TMEM126B)

MYD:	102769263(TMEM126B)

MMYO:

118664565(TMEM126B)

MLF:	102439130(TMEM126B)

PKL:	118712988(TMEM126B)

EFUS:

103297011(TMEM126B)

MNA:	107532463(TMEM126B)

DRO:	112316053(TMEM126B)

SHON:

118984732(TMEM126B)

AJM:	119065554(TMEM126B)

PDIC:

114499857(TMEM126B) 114504872

PHAS:

123805649(TMEM126B)

MMF:	118628297(TMEM126B)

PPAM:

129072800(TMEM126B)

HAI:	109383235(TMEM126B)

RFQ:	117029858(TMEM126B)

PALE:

102887566(TMEM126B)

PGIG:

120590428(TMEM126B)

PVP:	105294173(TMEM126B)

RAY:	107518568(TMEM126B)

MJV:	108398152(TMEM126B)

TOD:	119232693 119255685(TMEM126B)

SARA:

101540082(TMEM126B)

SETR:

126017976(TMEM126B)

LAV:	100665437(TMEM126B)

TMU:

101354365

ETF:	101652536(TMEM126B)

DNM:	101418981 101422581(TMEM126B)

MDO:	100026199(TMEM126B)

GAS:	123238800(TMEM126B)

SHR:	100923243(TMEM126B)

AFZ:

127555142

OAA:	114805880(TMEM126B)

» show all

Reference

PMID:24191001

Authors

Andrews B, Carroll J, Ding S, Fearnley IM, Walker JE

Title

Assembly factors for the membrane arm of human complex I.

Journal

Proc Natl Acad Sci U S A 110:18934-9 (2013)
DOI:10.1073/pnas.1319247110

Sequence

[hsa:55863]

Reference

PMID:22982022

Authors

Heide H, Bleier L, Steger M, Ackermann J, Drose S, Schwamb B, Zornig M, Reichert AS, Koch I, Wittig I, Brandt U

Title

Complexome profiling identifies TMEM126B as a component of the mitochondrial complex I assembly complex.

Journal

Cell Metab 16:538-49 (2012)
DOI:10.1016/j.cmet.2012.08.009

Sequence

[hsa:55863]

All links

Ontology (2)   
   KEGG BRITE (2)   
Disease (1)   
   KEGG DISEASE (1)   
Gene (175)   
   KEGG GENES (164)   
   KEGG MGENES (6)   
   RefGene (4)   
   OC (1)   
Literature (2)   
   PubMed (2)   
All databases (180)   

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