KEGG   ORTHOLOGY: K05626
Entry
K05626                      KO                                     
Symbol
DRPLA
Name
atrophin-1 (dentatorubral-pallidoluysian atrophy protein)
Disease
H00060  Dentatorubropallidoluysian atrophy (DRPLA)
Brite
KEGG Orthology (KO) [BR:ko00001]
 09190 Not Included in Pathway or Brite
  09193 Unclassified: signaling and cellular processes
   99995 Signaling proteins
    K05626  DRPLA; atrophin-1 (dentatorubral-pallidoluysian atrophy protein)
Genes
HSA: 1822(ATN1)
PTR: 451803(ATN1)
PPS: 100994844(ATN1)
GGO: 109029059(ATN1)
PON: 100448818(ATN1)
NLE: 100599977(ATN1)
HMH: 116472604(ATN1)
MCC: 722114(ATN1)
MCF: 102132888(ATN1)
MTHB: 126930428
MNI: 105484213(ATN1)
CSAB: 103218489(ATN1)
CATY: 105583044(ATN1)
PANU: 101000537(ATN1)
TGE: 112635579(ATN1)
MLEU: 105541819(ATN1)
RRO: 104680087(ATN1)
RBB: 108542022(ATN1)
TFN: 117090603(ATN1)
PTEH: 111555914(ATN1)
CANG: 105519107(ATN1)
CJC: 100409521(ATN1)
SBQ: 101033589(ATN1)
CIMI: 108294987(ATN1)
MMUR: 105868992(ATN1)
LCAT: 123640093(ATN1)
PCOQ: 105805038(ATN1)
OGA: 100948851(ATN1)
MMU: 13498(Atn1)
MCAL: 110296416(Atn1)
MPAH: 110316180(Atn1)
RNO: 29515(Atn1)
MCOC: 116099570(Atn1)
ANU: 117714767(Atn1)
MUN: 110548580(Atn1)
CGE: 100767627(Atn1)
MAUA: 101844714(Atn1)
PROB: 127213038(Atn1)
PLEU: 114708784(Atn1)
MORG: 121434794(Atn1)
MFOT: 126514834
AAMP: 119807646(Atn1)
NGI: 103727494(Atn1)
HGL: 101723354(Atn1)
CPOC: 100733654(Atn1)
CCAN: 109682812(Atn1)
DSP: 122101948(Atn1)
NCAR: 124983059
MMMA: 107154933(Atn1)
OCU: 100349239
OPI: 101517352(ATN1)
TUP: 102488708(ATN1)
GVR: 103586400(ATN1)
CFA: 611607(ATN1)
CLUD: 112675366(ATN1)
VVP: 112917326(ATN1)
VLG: 121479997(ATN1)
NPO: 129503478(ATN1)
AML: 100474046(ATN1)
UMR: 103656222(ATN1)
UAH: 113257949(ATN1)
UAR: 123781555(ATN1)
ELK: 111159799
LLV: 125106085
MPUF: 101678310(ATN1)
MNP: 132019903(ATN1)
MLK: 131838461(ATN1)
NVS: 122892660(ATN1)
ORO: 101374271(ATN1)
EJU: 114222535(ATN1)
ZCA: 113921840(ATN1)
MLX: 118025719(ATN1)
NSU: 110581056(ATN1)
LWW: 102735092(ATN1)
FCA: 101093617(ATN1)
PYU: 121021912(ATN1)
PBG: 122472387(ATN1)
PVIV: 125170379(ATN1)
LRUF: 124501430
PTG: 102955053(ATN1)
PPAD: 109276097(ATN1)
AJU: 106965439
HHV: 120220430(ATN1)
BTA: 513125(ATN1)
BOM: 102288144(ATN1)
BIU: 109558912(ATN1)
BBUB: 102389691(ATN1)
BBIS: 104992332(ATN1)
CHX: 102187302(ATN1)
OAS: 101108302(ATN1)
BTAX: 128047423(ATN1)
ODA: 120858744(ATN1)
CCAD: 122423268(ATN1)
MBEZ: 129536437(ATN1)
SSC: 100153709(ATN1)
CFR: 102515605(ATN1)
CBAI: 105071205(ATN1)
CDK: 105098195(ATN1)
VPC: 102532627(ATN1)
BACU: 103006159(ATN1)
BMUS: 118901758(ATN1)
LVE: 103087983(ATN1)
OOR: 101288757(ATN1)
DLE: 111176701(ATN1)
PCAD: 102985049(ATN1)
PSIU: 116760534(ATN1)
NASI: 112391699(ATN1)
ECB: 100060226(ATN1)
EPZ: 103547025(ATN1)
EAI: 106847313(ATN1)
MYB: 102257828(ATN1)
MYD: 102754400(ATN1)
MMYO: 118649838(ATN1)
PKL: 118720253 118730174(ATN1)
EFUS: 103289034(ATN1)
MNA: 107544061(ATN1)
DRO: 112321721(ATN1)
SHON: 119002401(ATN1)
AJM: 119065686(ATN1)
PDIC: 114513334(ATN1)
PHAS: 123810563(ATN1)
MMF: 118624349(ATN1)
PPAM: 129085051(ATN1) 129085058
HAI: 109373663(ATN1)
RFQ: 117028001(ATN1)
PALE: 102895411(ATN1)
PGIG: 120611672(ATN1)
PVP: 105295944(ATN1)
RAY: 107519827(ATN1)
MJV: 108384834(ATN1)
TOD: 119247765(ATN1)
SARA: 101546293(ATN1)
SETR: 126006510(ATN1)
LAV: 100676703(ATN1)
TMU: 101357414
ETF: 101639976(ATN1)
DNM: 101440463(ATN1)
MDO: 100033075(ATN1)
GAS: 123248544(ATN1)
AFZ: 127539229
PCW: 110213781(ATN1)
OAA: 103169606(ATN1)
GGA: 427946(ATN1)
PCOC: 116239991(ATN1)
CJO: 107318623(ATN1)
TPAI: 128089877(ATN1)
LMUT: 125685186(ATN1)
NMEL: 110398296(ATN1)
APLA: 101795518(ATN1)
ACYG: 106047825(ATN1)
CATA: 118247631(ATN1)
AFUL: 116498796(ATN1)
TGU: 100229755(ATN1)
LSR: 110480839(ATN1)
SCAN: 103812465(ATN1)
PMOA: 120506453(ATN1)
OTC: 121339340(ATN1)
PRUF: 121351689(ATN1)
GFR: 102040712(ATN1)
FAB: 101813001(ATN1)
OMA: 130253991(ATN1)
PHI: 102110702(ATN1)
PMAJ: 107211589(ATN1)
CCAE: 111945169(ATN1)
CCW: 104687226(ATN1)
CBRC: 103614066(ATN1)
ETL: 114058139(ATN1)
ZAB: 102063014(ATN1)
SVG: 106857892(ATN1)
MMEA: 130574781(ATN1)
HRT: 120749107(ATN1)
FPG: 101914391(ATN1)
FCH: 102055471(ATN1)
CLV: 102085150(ATN1)
EGZ: 104126603(ATN1)
NNI: 104009743(ATN1)
ACUN: 113479393(ATN1)
TALA: 116962317(ATN1)
PADL: 103921920(ATN1)
AFOR: 103905504(ATN1)
ACHC: 115343910(ATN1)
HLE: 104831777(ATN1)
AGEN: 126049041
GCL: 127021638
SHAB: 115601656(ATN1)
DPUB: 104299506(ATN1)
CPEA: 104389853(ATN1)
RTD: 128904216(ATN1)
CUCA: 104064396(ATN1)
AAM: 106497248(ATN1)
AROW: 112973022(ATN1)
NPD: 112960146(ATN1)
TGT: 104565676(ATN1)
DNE: 112991065(ATN1)
SCAM: 104150752(ATN1)
ASN: 102375019(ATN1)
AMJ: 102569960(ATN1)
CPOO: 109319379(ATN1)
GGN: 109304427(ATN1)
PSS: 102450875(ATN1)
CMY: 102932251(ATN1)
CCAY: 125622620(ATN1)
DCC: 119849859(ATN1)
CPIC: 101940262(ATN1)
TST: 117885672(ATN1)
CABI: 116821046(ATN1)
MRV: 120372519(ATN1)
ACS: 100567809(atn1)
ASAO: 132767529(ATN1)
PVT: 110084629(ATN1)
SUND: 121922414(ATN1)
PBI: 103067127(ATN1)
PMUR: 107285776(ATN1)
CTIG: 120306106(ATN1)
TSR: 106552514(ATN1)
PGUT: 117661825(ATN1)
APRI: 131190847(ATN1)
PTEX: 113444559(ATN1)
NSS: 113424527(ATN1)
VKO: 123033216(ATN1)
PMUA: 114587354(ATN1)
PRAF: 128405252(ATN1)
ZVI: 118097465(ATN1)
HCG: 128342811(ATN1)
GJA: 107116795(ATN1)
STOW: 125436160(ATN1)
EMC: 129345324(ATN1)
XLA: 108696045(atn1.L) 108697336(atn1.S)
XTR: 100486351(atn1)
NPR: 108784408(ATN1)
RTEM: 120946622(ATN1)
BBUF: 121004037(ATN1)
BGAR: 122941598(ATN1)
MUO: 115456949(ATN1)
GSH: 117350141(ATN1)
LCM: 102351834(ATN1)
 » show all
Reference
  Authors
Ellerby LM, Andrusiak RL, Wellington CL, Hackam AS, Propp SS, Wood JD, Sharp AH, Margolis RL, Ross CA, Salvesen GS, Hayden MR, Bredesen DE
  Title
Cleavage of atrophin-1 at caspase site aspartic acid 109 modulates cytotoxicity.
  Journal
J Biol Chem 274:8730-6 (1999)
DOI:10.1074/jbc.274.13.8730
  Sequence
[hsa:1822]

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