KEGG   Maylandia zebra (zebra mbuna): 101474711
Entry
101474711         CDS       T02814                                 
Symbol
bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
mze  Maylandia zebra (zebra mbuna)
Pathway
mze00280  Valine, leucine and isoleucine degradation
mze00640  Propanoate metabolism
mze00785  Lipoic acid metabolism
mze01100  Metabolic pathways
mze01210  2-Oxocarboxylic acid metabolism
Module
mze_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:mze00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    101474711 (bckdha)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    101474711 (bckdha)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    101474711 (bckdha)
Enzymes [BR:mze01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     101474711 (bckdha)
SSDB
Motif
Pfam: E1_dh DXP_synthase_N TPP_enzyme_C bCoV_NSP1
Other DBs
NCBI-GeneID: 101474711
NCBI-ProteinID: XP_004560526
UniProt: A0A3P9DEA2
Position
LG14:complement(31265972..31273291)
AA seq 446 aa
MAAVSSMSKMYGLCFRAVRQTAGLKAYRLLQRRGFRVTVLQLQQTFDSSLEKPQFPGASA
EFVDQLEFIQPNVISGIPVYRVMDRQGNIINPSQDPQLSKETVLNFYQKMTMLNTMDRIL
YESQRQGRISFYMTNYGEEGTHIGSAAALDPNDLVFGQYREAGVLMYRGFPLDHFMAQCY
ANADDLGKGRQMPVHYGSKDLNFVTISSPLATQIPQAAGAAYAVKRENTNRAVICYFGEG
AASEGDAHAGFNFSATLECPLIFFCRNNGYAISTPTNEQYRGDGIAARGPGYGMLSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYMTARGWWSEDDERSWRKQSRKTVMEAFERAERRLKPNPELLFTDVYQEMIPS
LNKQRESLWRHVQQYKENYPLDLYEK
NT seq 1341 nt   +upstreamnt  +downstreamnt
atggcagctgtgagcagcatgagcaaaatgtatgggctctgtttccgcgctgtccgtcag
acagcaggactgaaggcatatcgactgcttcagcgcagaggcttcagggtaactgttctt
cagctgcagcagacctttgactcttcgctggaaaagccccagtttccaggagcctcggcc
gagtttgtggatcagctcgagttcatccagcccaatgtcatctctgggatcccagtgtac
cgcgtgatggacaggcagggaaatatcatcaacccctctcaagaccctcagctctccaaa
gagacagttttgaacttttatcagaagatgacgatgctgaacacaatggaccgcattctt
tatgagtctcaaagacagggtcggatctccttctacatgactaactatggtgaggagggg
acacacatcggcagtgctgctgctctggatccaaacgatctggtttttgggcaatacaga
gaagctggagtgctgatgtaccgaggctttcctctggatcacttcatggctcagtgttac
gccaatgctgatgacctcggaaagggccggcagatgcccgtccactatggctccaaagat
ctgaactttgtcaccatctcatctcctctggccacacagattcctcaggcggctggagct
gcgtatgcagtcaagagagagaacacaaaccgtgccgtcatttgctattttggagaagga
gcagctagcgaaggggatgcacacgccggcttcaacttctctgccacccttgagtgccca
ctgatatttttttgccgcaacaatggctacgccatctctacccctacaaacgaacagtat
agaggtgatggcatcgctgctcgtggtcctggttatggcatgttgtccattcgtgttgat
ggtaatgatgtgtttgctgtgtacaacgctacaaaggaagcgaggcgcagggctgtggct
gagaaccagccattcctcattgaggcaatgacctacagaattggccaccacagcaccagc
gatgacagctcggcgtaccgttcagtggatgaagtgaactattgggacaaacaggaccat
cccatttccaggctgagacattacatgacagcccgcggatggtggagtgaagatgacgag
aggagctggcgaaaacaatcgcgcaagacggtgatggaggcgtttgagagggctgaaagg
cggctcaaacccaatcctgaactgttgttcacagacgtgtaccaggagatgatacccagc
ctgaacaagcagagagagtccctgtggagacatgtgcagcagtacaaagagaactaccca
ctagacttgtatgaaaaataa

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