KEGG   NETWORK: N00852
Entry
N00852                      Network                                
Name
Valine degradation
Definition
IB-CoA -- (ACADS,ACAD8,ACADM) >> (ECHS1,HADHA) >> HIBCH >> HIBADH >> ALDH6A1 -> Propanoyl-CoA
  Expanded
C00630 -- (35,27034,34) >> (1892,3030) >> 26275 >> 11112 >> 4329 -> C00100
Class
nt06024 Valine, leucine and isoleucine degradation
Type
Reference
Pathway
hsa00280  Valine, leucine and isoleucine degradation
Gene
35  ACADS; acyl-CoA dehydrogenase short chain
27034  ACAD8; acyl-CoA dehydrogenase family member 8
34  ACADM; acyl-CoA dehydrogenase medium chain
1892  ECHS1; enoyl-CoA hydratase, short chain 1
3030  HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
26275  HIBCH; 3-hydroxyisobutyryl-CoA hydrolase
11112  HIBADH; 3-hydroxyisobutyrate dehydrogenase
4329  ALDH6A1; aldehyde dehydrogenase 6 family member A1
Metabolite
C00630  Isobutyryl-CoA
C00100  Propanoyl-CoA

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