KEGG   PATHWAY: map00280Help
Entry
map00280                    Pathway                                

Name
Valine, leucine and isoleucine degradation
Class
09100 Metabolism; 09105 Amino acid metabolism
BRITE hierarchy
Pathway map
map00280  Valine, leucine and isoleucine degradation
map00280

Ortholog table
Module
M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:map00280]
M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:map00280]
Disease
H00172  Maple syrup urine disease (MSUD)
H00173  Isovaleric acidemia (IVA)
H00174  Methylmalonic aciduria (MMA)
H00175  Propionic acidemia
H00179  3-Hydroxy-3-methylglutaryl-CoA lyase deficiency
H00181  3-Methylcrotonylglycinuria
H00375  SBCAD deficiency
H00754  3-Methylglutaconic aciduria (MGCA)
H00925  2-Methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiency
H01076  Alpha-methylacetoacetic aciduria
H01121  Succinyl CoA:3-oxoacid CoA transferase (SCOT) deficiency
H01123  HMG-CoA synthase (HMGCS) deficiency
H01279  Isobutyryl-CoA dehydrogenase (IBD) deficiency
H01349  Methacrylic aciduria
H01364  3-Hydroxyacyl-CoA dehydrogenase deficiency
H01400  Secondary hyperammonemia
H02109  Combined malonic and methylmalonic aciduria
Other DBs
GO: 0006550 0006552 0006574
KO pathway
ko00280   

  All links  
Pathway (2)   
   KEGG MODULE (2)   
Disease (17)   
   KEGG DISEASE (17)   
Chemical substance (42)   
   KEGG COMPOUND (42)   
Chemical reaction (87)   
   KEGG ENZYME (36)   
   KEGG REACTION (51)   
Gene (405841)   
   KEGG ORTHOLOGY (69)   
   RefGene (405772)   
All databases (405989)   

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