KEGG   PATHWAY: map00280Help
Entry
map00280                    Pathway                                

Name
Valine, leucine and isoleucine degradation
Class
09100 Metabolism; 09105 Amino acid metabolism
BRITE hierarchy
Pathway map
map00280  Valine, leucine and isoleucine degradation
map00280

Ortholog table
Module
M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:map00280]
M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:map00280]
Disease
H00172  Maple syrup urine disease (MSUD)
H00173  Isovaleric acidemia (IVA)
H00174  Methylmalonic aciduria (MMA)
H00175  Propionic acidemia
H00179  3-Hydroxy-3-methylglutaryl-CoA lyase deficiency
H00181  3-Methylcrotonylglycinuria
H00375  SBCAD deficiency
H00754  3-Methylglutaconic aciduria (MGCA)
H00925  2-Methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiency
H01076  Alpha-methylacetoacetic aciduria
H01121  Succinyl CoA:3-oxoacid CoA transferase (SCOT) deficiency
H01123  HMG-CoA synthase (HMGCS) deficiency
H01279  Isobutyryl-CoA dehydrogenase (IBD) deficiency
H01349  Methacrylic aciduria
H01364  3-Hydroxyacyl-CoA dehydrogenase deficiency
H01400  Secondary hyperammonemia
H02109  Combined malonic and methylmalonic aciduria
Other DBs
GO: 0006550 0006552 0006574
KO pathway
ko00280   

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