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KO |
09100 Metabolism
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09101 Carbohydrate metabolism
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00010 Glycolysis / Gluconeogenesis [PATH:ame00010]
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00020 Citrate cycle (TCA cycle) [PATH:ame00020]
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00030 Pentose phosphate pathway [PATH:ame00030]
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00040 Pentose and glucuronate interconversions [PATH:ame00040]
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00051 Fructose and mannose metabolism [PATH:ame00051]
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00052 Galactose metabolism [PATH:ame00052]
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00053 Ascorbate and aldarate metabolism [PATH:ame00053]
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00500 Starch and sucrose metabolism [PATH:ame00500]
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00520 Amino sugar and nucleotide sugar metabolism [PATH:ame00520]
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00620 Pyruvate metabolism [PATH:ame00620]
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00630 Glyoxylate and dicarboxylate metabolism [PATH:ame00630]
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00640 Propanoate metabolism [PATH:ame00640]
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409624 acetyl-coenzyme A synthetase
413942 acyl-CoA synthetase short-chain family member 3, mitochondrial isoform X2
412548 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
409306 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
552557 lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
551039 dihydrolipoyl dehydrogenase, mitochondrial
102655391 dihydrolipoyl dehydrogenase, mitochondrial
411697 short-chain specific acyl-CoA dehydrogenase, mitochondrial
412020 peroxisomal acyl-coenzyme A oxidase 3
552757 probable peroxisomal acyl-coenzyme A oxidase 1
410325 trifunctional enzyme subunit alpha, mitochondrial
409150 probable enoyl-CoA hydratase, mitochondrial
724838 uncharacterized protein LOC724838
412796 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X1
551208 3-hydroxyisobutyrate dehydrogenase, mitochondrial isoform X1
552286 acetyl-CoA carboxylase isoform X3
552823 malonyl-CoA decarboxylase, mitochondrial isoform X1
408955 4-aminobutyrate aminotransferase, mitochondrial isoform X3
412177 4-aminobutyrate aminotransferase, mitochondrial isoform X1
551403 succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial isoform X2
551958 uncharacterized protein LOC551958
409736 probable methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X2
411188 L-lactate dehydrogenase isoform X2
725482 L-lactate dehydrogenase A-like 6A isoform X2
411187 L-lactate dehydrogenase
411189 L-lactate dehydrogenase A-like 6A
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K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01908 ACSS3; propionyl-CoA synthetase [EC:6.2.1.17]
K00166 BCKDHA; 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K14729 FOX2; multifunctional beta-oxidation protein [EC:4.2.1.- 1.1.1.-]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K23146 HPD1; 3-hydroxyisobutyrate/3-hydroxypropionate dehydrogenase [EC:1.1.1.31 1.1.1.59]
K11262 ACACA; acetyl-CoA carboxylase / biotin carboxylase 1 [EC:6.4.1.2 6.3.4.14 2.1.3.15]
K01578 MLYCD; malonyl-CoA decarboxylase [EC:4.1.1.9]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K01899 LSC1; succinyl-CoA synthetase alpha subunit [EC:6.2.1.4 6.2.1.5]
K01900 LSC2; succinyl-CoA synthetase beta subunit [EC:6.2.1.4 6.2.1.5]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
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00650 Butanoate metabolism [PATH:ame00650]
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726218 acetyl-CoA acetyltransferase, mitochondrial
551395 acetyl-CoA acetyltransferase, cytosolic
410325 trifunctional enzyme subunit alpha, mitochondrial
409150 probable enoyl-CoA hydratase, mitochondrial
411697 short-chain specific acyl-CoA dehydrogenase, mitochondrial
410999 L-2-hydroxyglutarate dehydrogenase, mitochondrial isoform X1
408432 glutamate decarboxylase isoform X2
408955 4-aminobutyrate aminotransferase, mitochondrial isoform X3
412177 4-aminobutyrate aminotransferase, mitochondrial isoform X1
412305 succinate-semialdehyde dehydrogenase, mitochondrial
413763 hydroxymethylglutaryl-CoA synthase 1 isoform X1
726494 hydroxymethylglutaryl-CoA lyase, mitochondrial
409157 succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial
409087 D-beta-hydroxybutyrate dehydrogenase, mitochondrial isoform X2
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K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00109 L2HGDH; 2-hydroxyglutarate dehydrogenase [EC:1.1.99.2]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00139 ALDH5A1; succinate-semialdehyde dehydrogenase [EC:1.2.1.24]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K00019 BDH1; 3-hydroxybutyrate dehydrogenase [EC:1.1.1.30]
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00660 C5-Branched dibasic acid metabolism
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00562 Inositol phosphate metabolism [PATH:ame00562]
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09102 Energy metabolism
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09103 Lipid metabolism
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00061 Fatty acid biosynthesis [PATH:ame00061]
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00062 Fatty acid elongation [PATH:ame00062]
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408291 3-ketoacyl-CoA thiolase, mitochondrial
551775 trifunctional enzyme subunit beta, mitochondrial
410325 trifunctional enzyme subunit alpha, mitochondrial
409150 probable enoyl-CoA hydratase, mitochondrial
411662 enoyl-[acyl-carrier-protein] reductase, mitochondrial
408426 lysosomal thioesterase PPT2 homolog isoform X2
551664 palmitoyl-protein thioesterase 1
411692 elongation of very long chain fatty acids protein 4
725842 elongation of very long chain fatty acids protein 6-like
113219003 elongation of very long chain fatty acids protein 6-like
113219005 elongation of very long chain fatty acids protein 6-like
725031 elongation of very long chain fatty acids protein 6
724552 elongation of very long chain fatty acids protein AAEL008004
409638 elongation of very long chain fatty acids protein AAEL008004 isoform X1
551938 elongation of very long chain fatty acids protein AAEL008004 isoform X1
413789 elongation of very long chain fatty acids protein AAEL008004
550828 elongation of very long chain fatty acids protein AAEL008004
100578829 elongation of very long chain fatty acids protein 1
725258 very-long-chain 3-oxoacyl-CoA reductase
100577192 very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase hpo-8
413078 very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase isoform X1
725146 very-long-chain enoyl-CoA reductase isoform X1
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K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K07512 MECR; mitochondrial enoyl-[acyl-carrier protein] reductase / trans-2-enoyl-CoA reductase [EC:1.3.1.- 1.3.1.38]
K01074 PPT; palmitoyl-protein thioesterase [EC:3.1.2.22]
K01074 PPT; palmitoyl-protein thioesterase [EC:3.1.2.22]
K10249 ELOVL4; elongation of very long chain fatty acids protein 4 [EC:2.3.1.199]
K10203 ELOVL6; elongation of very long chain fatty acids protein 6 [EC:2.3.1.199]
K10203 ELOVL6; elongation of very long chain fatty acids protein 6 [EC:2.3.1.199]
K10203 ELOVL6; elongation of very long chain fatty acids protein 6 [EC:2.3.1.199]
K10203 ELOVL6; elongation of very long chain fatty acids protein 6 [EC:2.3.1.199]
K10250 ELOVL7; elongation of very long chain fatty acids protein 7 [EC:2.3.1.199]
K10250 ELOVL7; elongation of very long chain fatty acids protein 7 [EC:2.3.1.199]
K10250 ELOVL7; elongation of very long chain fatty acids protein 7 [EC:2.3.1.199]
K10250 ELOVL7; elongation of very long chain fatty acids protein 7 [EC:2.3.1.199]
K10250 ELOVL7; elongation of very long chain fatty acids protein 7 [EC:2.3.1.199]
K10250 ELOVL7; elongation of very long chain fatty acids protein 7 [EC:2.3.1.199]
K10251 HSD17B12; 17beta-estradiol 17-dehydrogenase / very-long-chain 3-oxoacyl-CoA reductase [EC:1.1.1.62 1.1.1.330]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10703 HACD; very-long-chain (3R)-3-hydroxyacyl-CoA dehydratase [EC:4.2.1.134]
K10258 TER; very-long-chain enoyl-CoA reductase [EC:1.3.1.93]
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00071 Fatty acid degradation [PATH:ame00071]
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726218 acetyl-CoA acetyltransferase, mitochondrial
551395 acetyl-CoA acetyltransferase, cytosolic
408291 3-ketoacyl-CoA thiolase, mitochondrial
551775 trifunctional enzyme subunit beta, mitochondrial
410325 trifunctional enzyme subunit alpha, mitochondrial
409150 probable enoyl-CoA hydratase, mitochondrial
412020 peroxisomal acyl-coenzyme A oxidase 3
552757 probable peroxisomal acyl-coenzyme A oxidase 1
411697 short-chain specific acyl-CoA dehydrogenase, mitochondrial
408567 probable medium-chain specific acyl-CoA dehydrogenase, mitochondrial
409712 short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
412025 very long-chain specific acyl-CoA dehydrogenase, mitochondrial
410254 glutaryl-CoA dehydrogenase, mitochondrial
409515 long-chain-fatty-acid--CoA ligase 4 isoform X1
412541 long-chain-fatty-acid--CoA ligase 1 isoform X3
551837 very long-chain-fatty-acid--CoA ligase bubblegum isoform X1
550695 carnitine O-palmitoyltransferase 1, liver isoform isoform X1
411473 carnitine O-palmitoyltransferase 2, mitochondrial
552000 enoyl-CoA delta isomerase 1, mitochondrial
552143 enoyl-CoA delta isomerase 3, peroxisomal
409773 alcohol dehydrogenase class-3
550687 aldehyde dehydrogenase, mitochondrial
408559 retinal dehydrogenase 1
411140 putative aldehyde dehydrogenase family 7 member A1 homolog
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K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K09479 ACADVL; very long chain acyl-CoA dehydrogenase [EC:1.3.8.9]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K01897 ACSL; long-chain acyl-CoA synthetase [EC:6.2.1.3]
K15013 ACSBG; long-chain-fatty-acid--CoA ligase ACSBG [EC:6.2.1.3]
K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
K08766 CPT2; carnitine O-palmitoyltransferase 2 [EC:2.3.1.21]
K13238 ECI1; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K13239 ECI2; Delta3-Delta2-enoyl-CoA isomerase [EC:5.3.3.8]
K00121 frmA; S-(hydroxymethyl)glutathione dehydrogenase / alcohol dehydrogenase [EC:1.1.1.284 1.1.1.1]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
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00073 Cutin, suberine and wax biosynthesis
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00100 Steroid biosynthesis [PATH:ame00100]
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00120 Primary bile acid biosynthesis
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00121 Secondary bile acid biosynthesis
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00140 Steroid hormone biosynthesis
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00561 Glycerolipid metabolism [PATH:ame00561]
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00564 Glycerophospholipid metabolism [PATH:ame00564]
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00565 Ether lipid metabolism [PATH:ame00565]
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00600 Sphingolipid metabolism [PATH:ame00600]
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00590 Arachidonic acid metabolism [PATH:ame00590]
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00591 Linoleic acid metabolism
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00592 alpha-Linolenic acid metabolism [PATH:ame00592]
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01040 Biosynthesis of unsaturated fatty acids [PATH:ame01040]
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09104 Nucleotide metabolism
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09105 Amino acid metabolism
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00250 Alanine, aspartate and glutamate metabolism [PATH:ame00250]
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00260 Glycine, serine and threonine metabolism [PATH:ame00260]
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00270 Cysteine and methionine metabolism [PATH:ame00270]
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00280 Valine, leucine and isoleucine degradation [PATH:ame00280]
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412889 branched-chain-amino-acid aminotransferase, cytosolic
412548 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
409306 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
552557 lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
551039 dihydrolipoyl dehydrogenase, mitochondrial
102655391 dihydrolipoyl dehydrogenase, mitochondrial
411697 short-chain specific acyl-CoA dehydrogenase, mitochondrial
408567 probable medium-chain specific acyl-CoA dehydrogenase, mitochondrial
408288 isovaleryl-CoA dehydrogenase, mitochondrial
409712 short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
410325 trifunctional enzyme subunit alpha, mitochondrial
409150 probable enoyl-CoA hydratase, mitochondrial
725274 3-hydroxyacyl-CoA dehydrogenase type-2
726590 3-hydroxyacyl-CoA dehydrogenase type-2
408291 3-ketoacyl-CoA thiolase, mitochondrial
551775 trifunctional enzyme subunit beta, mitochondrial
412796 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X1
551208 3-hydroxyisobutyrate dehydrogenase, mitochondrial isoform X1
409736 probable methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X2
550687 aldehyde dehydrogenase, mitochondrial
408559 retinal dehydrogenase 1
411140 putative aldehyde dehydrogenase family 7 member A1 homolog
408955 4-aminobutyrate aminotransferase, mitochondrial isoform X3
412177 4-aminobutyrate aminotransferase, mitochondrial isoform X1
100576186 alanine--glyoxylate aminotransferase 2, mitochondrial
413233 methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
410554 methylcrotonoyl-CoA carboxylase beta chain, mitochondrial
409494 methylglutaconyl-CoA hydratase, mitochondrial
726494 hydroxymethylglutaryl-CoA lyase, mitochondrial
409157 succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial
726218 acetyl-CoA acetyltransferase, mitochondrial
551395 acetyl-CoA acetyltransferase, cytosolic
413763 hydroxymethylglutaryl-CoA synthase 1 isoform X1
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K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K00166 BCKDHA; 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00253 IVD; isovaleryl-CoA dehydrogenase [EC:1.3.8.4]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K23146 HPD1; 3-hydroxyisobutyrate/3-hydroxypropionate dehydrogenase [EC:1.1.1.31 1.1.1.59]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00827 AGXT2; alanine-glyoxylate transaminase / (R)-3-amino-2-methylpropionate-pyruvate transaminase [EC:2.6.1.44 2.6.1.40]
K01968 MCCC1; 3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
K01969 MCCC2; 3-methylcrotonyl-CoA carboxylase beta subunit [EC:6.4.1.4]
K05607 AUH; methylglutaconyl-CoA hydratase [EC:4.2.1.18]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
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00290 Valine, leucine and isoleucine biosynthesis [PATH:ame00290]
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00300 Lysine biosynthesis
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00310 Lysine degradation [PATH:ame00310]
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552130 alpha-aminoadipic semialdehyde synthase, mitochondrial
411140 putative aldehyde dehydrogenase family 7 member A1 homolog
724239 kynurenine/alpha-aminoadipate aminotransferase, mitochondrial
725529 kynurenine/alpha-aminoadipate aminotransferase, mitochondrial isoform X1
412569 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial isoform X2
409155 dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial isoform X2
551039 dihydrolipoyl dehydrogenase, mitochondrial
102655391 dihydrolipoyl dehydrogenase, mitochondrial
410254 glutaryl-CoA dehydrogenase, mitochondrial
410325 trifunctional enzyme subunit alpha, mitochondrial
409150 probable enoyl-CoA hydratase, mitochondrial
726218 acetyl-CoA acetyltransferase, mitochondrial
551395 acetyl-CoA acetyltransferase, cytosolic
725458 hydroxylysine kinase
107964319 calmodulin-lysine N-methyltransferase
408716 histone-lysine N-methyltransferase trithorax isoform X1
411466 histone-lysine N-methyltransferase 2C isoform X1
100577280 uncharacterized protein LOC100577280
411985 histone-lysine N-methyltransferase SETD1
727238 histone-lysine N-methyltransferase ash1 isoform X1
412195 histone-lysine N-methyltransferase SMYD3 isoform X1
413388 histone-lysine N-methyltransferase EHMT2 isoform X1
409098 histone-lysine N-methyltransferase eggless
552235 histone-lysine N-methyltransferase E(z) isoform X3
102653839 probable histone-lysine N-methyltransferase set-23
727429 histone-lysine N-methyltransferase SETMAR-like
102655244 histone-lysine N-methyltransferase NSD2 isoform X1
100578450 histone-lysine N-methyltransferase SETD2 isoform X1
411070 histone-lysine N-methyltransferase, H3 lysine-79 specific
412027 histone-lysine N-methyltransferase PR-Set7
411906 histone-lysine N-methyltransferase KMT5B-B-like
725792 transcription factor hamlet-like isoform X1
550687 aldehyde dehydrogenase, mitochondrial
408559 retinal dehydrogenase 1
100578909 procollagen-lysine,2-oxoglutarate 5-dioxygenase 3 isoform X1
413713 glycosyltransferase 25 family member
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K14157 AASS; alpha-aminoadipic semialdehyde synthase [EC:1.5.1.8 1.5.1.9]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00825 AADAT; kynurenine/2-aminoadipate aminotransferase [EC:2.6.1.7 2.6.1.39]
K00825 AADAT; kynurenine/2-aminoadipate aminotransferase [EC:2.6.1.7 2.6.1.39]
K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
K00658 DLST; 2-oxoglutarate dehydrogenase E2 component (dihydrolipoamide succinyltransferase) [EC:2.3.1.61]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K18201 AGPHD1; hydroxylysine kinase [EC:2.7.1.81]
K18826 CAMKMT; calmodulin-lysine N-methyltransferase [EC:2.1.1.60]
K09186 MLL1; [histone H3]-lysine4 N-trimethyltransferase MLL1 [EC:2.1.1.354]
K09188 MLL3; [histone H3]-lysine4 N-trimethyltransferase MLL3 [EC:2.1.1.354]
K09189 MLL5; [histone H3]-lysine4 N-trimethyltransferase MLL5 [EC:2.1.1.354]
K11422 SETD1; [histone H3]-lysine4 N-trimethyltransferase SETD1 [EC:2.1.1.354]
K06101 ASH1L; [histone H3]-lysine4 N-trimethyltransferase ASH1L [EC:2.1.1.354]
K11426 SMYD; [histone H3]-lysine4/36 N-trimethyltransferase SMYD [EC:2.1.1.354 2.1.1.357]
K11420 EHMT; [histone H3]-lysine9 N-trimethyltransferase EHMT [EC:2.1.1.355]
K11421 SETDB1; [histone H3]-N6,N6-dimethyl-lysine9 N-methyltransferase [EC:2.1.1.366]
K11430 EZH2; [histone H3]-lysine27 N-trimethyltransferase EZH2 [EC:2.1.1.356]
K11433 SETMAR; [histone H3]-lysine36 N-dimethyltransferase SETMAR [EC:2.1.1.357]
K11433 SETMAR; [histone H3]-lysine36 N-dimethyltransferase SETMAR [EC:2.1.1.357]
K11424 WHSC1; [histone H3]-lysine36 N-dimethyltransferase NSD2 [EC:2.1.1.357]
K11423 SETD2; [histone H3]-lysine36 N-trimethyltransferase [EC:2.1.1.359]
K11427 DOT1L; [histone H3]-lysine79 N-trimethyltransferase [EC:2.1.1.360]
K11428 SETD8; [histone H4]-lysine20 N-methyltransferase SETD8 [EC:2.1.1.361]
K11429 SUV420H; [histone H4]-N-methyl-L-lysine20 N-methyltransferase [EC:2.1.1.362]
K04462 MECOM; [histone H3]-lysine9 N-methyltransferase (ecotropic virus integration site 1 protein) [EC:2.1.1.367]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K13647 PLODN; procollagen-lysine,2-oxoglutarate 5-dioxygenase, invertebrate [EC:1.14.11.4]
K11703 GLT25D; collagen beta-1,O-galactosyltransferase [EC:2.4.1.50]
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00220 Arginine biosynthesis [PATH:ame00220]
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00330 Arginine and proline metabolism [PATH:ame00330]
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00340 Histidine metabolism [PATH:ame00340]
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00350 Tyrosine metabolism [PATH:ame00350]
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00360 Phenylalanine metabolism [PATH:ame00360]
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00380 Tryptophan metabolism [PATH:ame00380]
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410828 tryptophan 2,3-dioxygenase isoform X1
726754 kynurenine formamidase isoform X1
551858 kynurenine 3-monooxygenase isoform X5
412569 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial isoform X2
409155 dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial isoform X2
551039 dihydrolipoyl dehydrogenase, mitochondrial
102655391 dihydrolipoyl dehydrogenase, mitochondrial
410254 glutaryl-CoA dehydrogenase, mitochondrial
410325 trifunctional enzyme subunit alpha, mitochondrial
409150 probable enoyl-CoA hydratase, mitochondrial
726218 acetyl-CoA acetyltransferase, mitochondrial
551395 acetyl-CoA acetyltransferase, cytosolic
724811 kynurenine--oxoglutarate transaminase 3-like
724239 kynurenine/alpha-aminoadipate aminotransferase, mitochondrial
725529 kynurenine/alpha-aminoadipate aminotransferase, mitochondrial isoform X1
411200 tryptophan 5-hydroxylase 1
410638 aromatic-L-amino-acid decarboxylase
410639 alpha-methyldopa hypersensitive protein isoform X1
550687 aldehyde dehydrogenase, mitochondrial
408559 retinal dehydrogenase 1
411140 putative aldehyde dehydrogenase family 7 member A1 homolog
443552 Cat; catalase
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K00453 TDO2; tryptophan 2,3-dioxygenase [EC:1.13.11.11]
K01432 AFMID; arylformamidase [EC:3.5.1.9]
K00486 KMO; kynurenine 3-monooxygenase [EC:1.14.13.9]
K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
K00658 DLST; 2-oxoglutarate dehydrogenase E2 component (dihydrolipoamide succinyltransferase) [EC:2.3.1.61]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00252 GCDH; glutaryl-CoA dehydrogenase [EC:1.3.8.6]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00816 CCBL; kynurenine---oxoglutarate transaminase / cysteine-S-conjugate beta-lyase / glutamine---phenylpyruvate transaminase [EC:2.6.1.7 4.4.1.13 2.6.1.64]
K00825 AADAT; kynurenine/2-aminoadipate aminotransferase [EC:2.6.1.7 2.6.1.39]
K00825 AADAT; kynurenine/2-aminoadipate aminotransferase [EC:2.6.1.7 2.6.1.39]
K00502 TPH1_2; tryptophan 5-monooxygenase [EC:1.14.16.4]
K01593 DDC; aromatic-L-amino-acid/L-tryptophan decarboxylase [EC:4.1.1.28 4.1.1.105]
K01593 DDC; aromatic-L-amino-acid/L-tryptophan decarboxylase [EC:4.1.1.28 4.1.1.105]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K03781 katE; catalase [EC:1.11.1.6]
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00400 Phenylalanine, tyrosine and tryptophan biosynthesis [PATH:ame00400]
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09106 Metabolism of other amino acids
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00410 beta-Alanine metabolism [PATH:ame00410]
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411771 cysteine sulfinic acid decarboxylase
408509 glutamate decarboxylase 1
409063 cysteine sulfinic acid decarboxylase
408432 glutamate decarboxylase isoform X2
412393 cytosolic non-specific dipeptidase
408955 4-aminobutyrate aminotransferase, mitochondrial isoform X3
412177 4-aminobutyrate aminotransferase, mitochondrial isoform X1
726650 LOW QUALITY PROTEIN: uncharacterized protein LOC726650
725007 spermine oxidase
550687 aldehyde dehydrogenase, mitochondrial
408559 retinal dehydrogenase 1
411140 putative aldehyde dehydrogenase family 7 member A1 homolog
411822 aldehyde dehydrogenase family 3 member B1 isoform X1
410207 dihydropyrimidine dehydrogenase [NADP(+)]
102654653 dihydropyrimidinase isoform X1
409250 beta-ureidopropionase
551208 3-hydroxyisobutyrate dehydrogenase, mitochondrial isoform X1
412796 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X1
410325 trifunctional enzyme subunit alpha, mitochondrial
409150 probable enoyl-CoA hydratase, mitochondrial
724838 uncharacterized protein LOC724838
411697 short-chain specific acyl-CoA dehydrogenase, mitochondrial
412020 peroxisomal acyl-coenzyme A oxidase 3
552757 probable peroxisomal acyl-coenzyme A oxidase 1
552823 malonyl-CoA decarboxylase, mitochondrial isoform X1
409736 probable methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X2
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K18966 GADL1; sulfinoalanine decarboxylase / aspartate 1-decarboxylase [EC:4.1.1.29 4.1.1.11]
K18966 GADL1; sulfinoalanine decarboxylase / aspartate 1-decarboxylase [EC:4.1.1.29 4.1.1.11]
K18966 GADL1; sulfinoalanine decarboxylase / aspartate 1-decarboxylase [EC:4.1.1.29 4.1.1.11]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K08660 CNDP2; cytosolic nonspecific dipeptidase [EC:3.4.13.18]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K12259 SMOX; spermine oxidase [EC:1.5.3.16 1.5.3.-]
K12259 SMOX; spermine oxidase [EC:1.5.3.16 1.5.3.-]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00129 ALDH3; aldehyde dehydrogenase (NAD(P)+) [EC:1.2.1.5]
K00207 DPYD; dihydropyrimidine dehydrogenase (NADP+) [EC:1.3.1.2]
K01464 DPYS; dihydropyrimidinase [EC:3.5.2.2]
K01431 UPB1; beta-ureidopropionase [EC:3.5.1.6]
K23146 HPD1; 3-hydroxyisobutyrate/3-hydroxypropionate dehydrogenase [EC:1.1.1.31 1.1.1.59]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K14729 FOX2; multifunctional beta-oxidation protein [EC:4.2.1.- 1.1.1.-]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K01578 MLYCD; malonyl-CoA decarboxylase [EC:4.1.1.9]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
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00430 Taurine and hypotaurine metabolism [PATH:ame00430]
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00440 Phosphonate and phosphinate metabolism [PATH:ame00440]
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00450 Selenocompound metabolism [PATH:ame00450]
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00460 Cyanoamino acid metabolism
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00470 D-Amino acid metabolism [PATH:ame00470]
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00480 Glutathione metabolism [PATH:ame00480]
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09107 Glycan biosynthesis and metabolism
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09108 Metabolism of cofactors and vitamins
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09109 Metabolism of terpenoids and polyketides
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09110 Biosynthesis of other secondary metabolites
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09111 Xenobiotics biodegradation and metabolism
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09112 Not included in regular maps
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09120 Genetic Information Processing
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09130 Environmental Information Processing
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09140 Cellular Processes
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09150 Organismal Systems
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09160 Human Diseases
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09180 Brite Hierarchies
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09190 Not Included in Pathway or Brite
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