Mitochondrial Biogenesis - Homo sapiens (human)

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 Mitochondrial DNA transcription, translation, and replication factors
 
 Mitochondrial protein import machinery
 
 Mitochondrial quality control factors
   Regulator of mitochondrial biogenesis
   Mitochondrial respiratory chain complex assembly factors
   Mitochondrial dynamics
     Fission and Fusion factors
       55669 MFN1; mitofusin 1
       9927 MFN2; mitofusin 2
       4976 OPA1; OPA1 mitochondrial dynamin like GTPase
       80207 OPA3; outer mitochondrial membrane lipid metabolism regulator OPA3
       51499 TRIAP1; TP53 regulated inhibitor of apoptosis 1
       55486 PARL; presenilin associated rhomboid like
       578 BAK1; BCL2 antagonist/killer 1
       581 BAX; BCL2 associated X, apoptosis regulator
       10059 DNM1L; dynamin 1 like
       51024 FIS1; fission, mitochondrial 1
       6612 SUMO3; small ubiquitin like modifier 3
       6613 SUMO2; small ubiquitin like modifier 2
       7341 SUMO1; small ubiquitin like modifier 1
       387082 SUMO4; small ubiquitin like modifier 4
       51100 SH3GLB1; SH3 domain containing GRB2 like, endophilin B1
       23787 MTCH1; mitochondrial carrier 1
       23788 MTCH2; mitochondrial carrier 2
       56947 MFF; mitochondrial fission factor
       54332 GDAP1; ganglioside induced differentiation associated protein 1
       78997 GDAP1L1; ganglioside induced differentiation associated protein 1 like 1
       10493 VAT1; vesicle amine transport 1
       125170 MIEF2; mitochondrial elongation factor 2
       54471 MIEF1; mitochondrial elongation factor 1
       201164 PLD6; phospholipase D family member 6
       374986 MIGA1; mitoguardin 1
       84895 MIGA2; mitoguardin 2
K21356 MFN1; mitofusin 1 [EC:3.6.5.-] 
K06030 MFN2; mitofusin 2 [EC:3.6.5.-] 
K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] 
K23166 OPA3; optic atrophy 3 protein 
K17968 TRIAP1; TRIAP1/MDM35 family protein 
K09650 PARL; rhomboid-like protein [EC:3.4.21.105] 
K14021 BAK; Bcl-2 homologous antagonist/killer 
K02159 BAX; apoptosis regulator BAX 
K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] 
K17969 FIS1; mitochondrial fission 1 protein 
K12160 SUMO; small ubiquitin-related modifier 
K12160 SUMO; small ubiquitin-related modifier 
K12160 SUMO; small ubiquitin-related modifier 
K12160 SUMO; small ubiquitin-related modifier 
K11248 SH3GLB1; endophilin-B1 
K17885 MTCH; mitochondrial carrier 
K17885 MTCH; mitochondrial carrier 
K22076 MFF; mitochondrial fission factor 
K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 
K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 
K23167 VAT1; synaptic vesicle membrane protein VAT-1 
K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 
K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 
K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] 
K27289 MIGA; mitoguardin 
K27289 MIGA; mitoguardin 
     Actin cytoskeleton organization
     Mitochondrial movement
     Retention of mitochondria
     Morphogenesis factors
   Mitophagy factors

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Last updated: March 14, 2024