ICD-11 による疾患分類

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 01 Certain infectious or parasitic diseases
   Gastroenteritis or colitis of infectious origin
     Bacterial intestinal infections
       1A00  Cholera
         H00110  コレラ
       1A01  Intestinal infection due to other Vibrio
         H00307  腸炎ビブリオ感染症
         H00308  ビブリオ・バルニフィカス感染症
       1A02  Intestinal infections due to Shigella
         H00299  細菌性赤痢
       1A03  Intestinal infections due to Escherichia coli
         H00278  腸管病原性大腸菌感染症
         H00280  腸管毒素原性大腸菌感染症
         H01311  腸管組織侵襲性大腸菌感染症
         H00277  腸管出血性大腸菌感染症
         H01312  腸管凝集性大腸菌感染症
       1A04  Enterocolitis due to Clostridium difficile
         H00338  偽膜性大腸炎
       1A05  Intestinal infections due to Yersinia enterocolitica
         H00298  エルシニア感染症
       1A06  Gastroenteritis due to Campylobacter
         H00321  カンピロバクター感染症
       1A07  Typhoid fever
         H00111  腸チフス
       1A08  Paratyphoid Fever
         H00112  パラチフス
       1A09  Infections due to other Salmonella
         H00113  サルモネラ感染症
       1A0Y  Other specified bacterial intestinal infections
         H01454  結腸スピロヘータ症
       1A0Z  Bacterial intestinal infections, unspecified
     Bacterial foodborne intoxications
       1A10  Foodborne staphylococcal intoxication
         H01175  ブドウ球菌感染症
       1A11  Botulism
         H00339  ボツリヌス中毒症
       1A12  Foodborne Clostridium perfringens intoxication
         H00335  ウェルシュ菌食中毒
       1A13  Foodborne Bacillus cereus intoxication
         H00329  セレウス菌食中毒
       1A1Y  Other specified bacterial foodborne intoxications
         H00300  エンテロバクター感染症
       1A1Z  Bacterial foodborne intoxications, unspecified
     Viral intestinal infections
       1A20  Enteritis due to Adenovirus
       1A21  Gastroenteritis due to Astrovirus
       1A22  Gastroenteritis due to Rotavirus
         H00975  ロタウイルス腸炎
       1A23  Enteritis due to Norovirus
         H01323  ノーウォーク様ウイルスによる急性胃腸症
       1A24  Intestinal infections due to Cytomegalovirus
       1A2Y  Other specified viral intestinal infections
       1A2Z  Viral intestinal infections, unspecified
     Protozoal intestinal infections
       1A30  Infections due to Balantidium coli
         H01087  バランチジウム症
       1A31  Giardiasis
         H00362  ジアルジア症
       1A32  Cryptosporidiosis
         H00356  クリプトスポリジウム症
       1A33  Cystoisosporiasis
       1A34  Sarcocystosis
       1A35  Blastocystosis
       1A36  Amoebiasis
         H00360  アメーバ赤痢
       1A3Y  Other specified protozoal intestinal infections
       1A3Z  Protozoal intestinal infections, unspecified
       1A40  Gastroenteritis or colitis without specification of infectious agent
   Predominantly sexually transmitted infections
     Syphilis
       1A60  Congenital syphilis
         H00354  梅毒
       1A61  Early syphilis
         H00354  梅毒
       1A62  Late syphilis
         H00354  梅毒
       1A63  Latent syphilis, unspecified as early or late
       1A6Z  Syphilis, unspecified
     Gonococcal infection
       1A70  Gonococcal genitourinary infection
         H00315  淋菌感染症
       1A71  Gonococcal pelviperitonitis
         H00315  淋菌感染症
       1A72  Gonococcal infection of other sites
         H00315  淋菌感染症
       1A73  Disseminated gonococcal infection
       1A7Z  Gonococcal infection, unspecified
     Sexually transmissible infections due to chlamydia
       1A80  Chlamydial lymphogranuloma
         H00348  鼠径リンパ肉芽腫
       1A81  Non-ulcerative sexually transmitted chlamydial infection
         H00347  性器クラミジア感染症
       1A8Y  Other specified sexually transmissible infections due to chlamydia
       1A8Z  Sexually transmissible infections due to chlamydia, unspecified
       1A90  Chancroid
         H00305  軟性下疳
       1A91  Granuloma inguinale
         H01415  ドノヴァン症
       1A92  Trichomoniasis
         H00812  トリコモナス症
       1A93  Sexually transmissible infestations
       1A94  Anogenital herpes simplex infection
         H00365  単純ヘルペスウイルス感染症
       1A95  Anogenital warts
         H01418  尖圭コンジローム
       1A9Y  Other specified predominantly sexually transmitted infections
       1A9Z  Predominantly sexually transmitted infections, unspecified
   Mycobacterial diseases
     Tuberculosis
       1B10  Tuberculosis of the respiratory system
         H00342  結核
       1B11  Tuberculosis of the nervous system
         H00342  結核
       1B12  Tuberculosis of other systems and organs
         H00342  結核
       1B13  Miliary tuberculosis
       1B14  Latent tuberculosis
       1B1Y  Other specified tuberculosis
       1B1Z  Tuberculosis, unspecified
       1B20  Leprosy
         H00344  ハンセン病
         H01473  らい性結節性紅斑
       1B21  Infections due to non-tuberculous mycobacteria
         H01458  非結核性抗酸菌症
         H01462  Rapidly growing mycobacteria 感染症
         H02029  肺 MAC 症
         H01042  ブルーリ潰瘍
       1B2Y  Other specified mycobacterial diseases
       1B2Z  Mycobacterial diseases, unspecified
   Certain staphylococcal or streptococcal diseases
     Acute rheumatic fever
       1B40  Acute rheumatic fever without mention of heart involvement
       1B41  Acute rheumatic fever with heart involvement
       1B42  Rheumatic chorea
         H01924  シデナム舞踏病
       1B50  Scarlet fever
         H01515  猩紅熱
       1B51  Streptococcal pharyngitis
         H00333  レンサ球菌感染症
         H01424  A群溶血性レンサ球菌咽頭炎
       1B52  Toxic shock syndrome
       1B53  Meningitis due to Streptococcus
         H00333  レンサ球菌感染症
         H01406  Streptococcus suis 感染
       1B54  Meningitis due to Staphylococcus
       1B5Y  Other specified staphylococcal or streptococcal diseases
       1B5Z  Staphylococcal or streptococcal diseases, unspecified
   Pyogenic bacterial infections of the skin or subcutaneous tissues
     1B70  Bacterial cellulitis, erysipelas and lymphangitis
       H01517  丹毒
     1B71  Necrotising fasciitis
       H01455  壊死性筋膜炎
     1B72  Impetigo
     1B73  Ecthyma
     1B74  Superficial bacterial folliculitis
     1B75  Deep bacterial folliculitis or pyogenic abscess of the skin
     1B7Y  Other specified pyogenic bacterial infection of skin and subcutaneous tissue
   Certain zoonotic bacterial diseases
     1B90  Rat-bite fevers
       H01314  鼠咬症
     1B91  Leptospirosis
       H00355  レプトスピラ症
     1B92  Glanders
       H00316  鼻疽
     1B93  Plague
       H00297  ペスト
     1B94  Tularaemia
       H00312  野兎病
     1B95  Brucellosis
       H00325  ブルセラ症
     1B96  Erysipeloid
       H01315  類丹毒
     1B97  Anthrax
       H00328  炭疽
     1B98  Cat-scratch disease
       H00326  バルトネラ症
     1B99  Pasteurellosis
       H00306  パスツレラ症
     1B9A  Extraintestinal yersiniosis
       H00298  エルシニア感染症
     1B9Z  Unspecified zoonotic bacterial disease
   Other bacterial diseases
     1C10  Actinomycosis
       H01325  放線菌症
     1C11  Bartonellosis
       H00326  バルトネラ症
       H00327  ざんごう熱
     1C12  Whooping cough
       H00319  百日咳
     1C13  Tetanus
       H00337  破傷風
     1C14  Obstetrical tetanus
     1C15  Tetanus neonatorum
     1C16  Gas gangrene
       H00336  ガス壊疽
     1C17  Diphtheria
       H00343  ジフテリア
     1C18  Brazilian purpuric fever
       H01330  ブラジル紫斑熱
     1C19  Legionnaires' disease
       H00311  レジオネラ症
     1C1A  Listeriosis
       H00332  リステリア症
     1C1B  Nocardiosis
       H00345  ノカルジア症
     1C1C  Meningococcal disease
       H00314  髄膜炎菌感染症
     1C1D  Yaws
       H01318  フランベジア
     1C1E  Pinta
       H01530  ピンタ
     1C1F  Endemic non-venereal syphilis
       H01531  ベジェル
     1C1G  Lyme borreliosis
       H00353  ボレリア症
     1C1H  Necrotising ulcerative gingivitis
       H01440  急性壊死性潰瘍性歯肉炎
     1C1J  Relapsing fever
       H00427  回帰熱
     Other diseases due to chlamydiae
       1C20  Chlamydial conjunctivitis
       1C21  Chlamydial peritonitis
       1C22  Infections due to Chlamydia psittaci
         H00350  オウム病
       1C23  Trachoma
         H00349  トラコーマ
       1C2Y  Other specified diseases due to chlamydiae
       1C2Z  Other diseases due to chlamydiae, unspecified
     Rickettsioses
       1C30  Typhus fever
         H00322  発疹チフス
         H00324  ツツガムシ病
       1C31  Spotted fever
         H00323  紅斑熱
       1C32  Rickettsialpox
       1C33  Q fever
         H00310  Q熱
       1C3Y  Other specified rickettsioses
         H01140  腺熱リケッチア症
       1C3Z  Rickettsioses, unspecified
       1C40  Campylobacteriosis
       1C41  Bacterial infection of unspecified site
         H00302  シトロバクター感染症
         H00303  セラチア感染症
         H00388  非クラミジア性非淋菌性尿道炎
         H01441  緑膿菌感染症
       1C42  Melioidosis
         H00317  類鼻疽
       1C43  Actinomycetoma
         H01451  放線菌腫
       1C44  Non-pyogenic bacterial infections of the skin
       1C4Y  Other specified bacterial diseases
       1C4Z  Unspecified bacterial disease
   Human immunodeficiency virus disease
     1C60  Human immunodeficiency virus disease associated with tuberculosis
     1C61  Human immunodeficiency virus disease associated with malaria
     1C62  Human immunodeficiency virus disease without mention of tuberculosis or malaria
       H01563  HIV感染症
   Viral infections of the central nervous system
     1C80  Viral encephalitis not elsewhere classified
     1C81  Acute poliomyelitis
       H00376  急性灰白髄炎
     1C82  Rabies
       H00377  狂犬病
       H00378  リッサウイルス感染症
     1C83  Western equine encephalitis
       H01534  西部ウマ脳炎
     1C84  Eastern equine encephalitis
       H01535  東部ウマ脳炎
     1C85  Japanese encephalitis
       H01533  日本脳炎
     1C86  St Louis encephalitis
       H02166  セントルイス脳炎
     1C87  Rocio viral encephalitis
       H02171  ロシオウイルス脳炎
     1C88  Murray Valley encephalitis
       H01536  マレー渓谷脳炎
     1C89  Far Eastern tick-borne encephalitis
     1C8A  Central European tick-borne encephalitis
     1C8B  California encephalitis
     1C8C  Venezuelan equine encephalitis
       H01547  ベネズエラウマ脳炎
     1C8D  La Crosse encephalitis
       H01537  ラクロス脳炎
     1C8E  Viral meningitis not elsewhere classified
       H00393  エンテロウイルス感染症
     1C8F  Lymphocytic choriomeningitis
       H01324  リンパ球性脈絡髄膜炎
     1C8Y  Other specified viral infections of the central nervous system
     1C8Z  Viral infections of the central nervous system, unspecified
   Non-viral and unspecified infections of the central nervous system
     1D00  Infectious encephalitis not elsewhere classified
     1D01  Infectious meningitis not elsewhere classified
       H00304  インフルエンザ菌感染症
       H01313  大腸菌性髄膜炎
     1D02  Infectious myelitis not elsewhere classified
     1D03  Infectious abscess of the central nervous system
     1D04  Infectious granulomas of the central nervous system
     1D05  Infectious cysts of the central nervous system
     1D0Y  Other specified non-viral and unspecified infections of the central nervous system
     1D0Z  Non-viral and unspecified infections of the central nervous system, unspecified
   Dengue
     1D20  Dengue without warning signs
       H00381  デング熱
     1D21  Dengue with warning signs
       H00381  デング熱
     1D22  Severe dengue
       H00381  デング熱
     1D2Z  Dengue fever, unspecified
       H00381  デング熱
   Certain arthropod-borne viral fevers
     1D40  Chikungunya virus disease
       H01540  チクングニア熱
     1D41  Colorado tick fever
       H02165  コロラドダニ熱
     1D42  O'nyong-nyong fever
       H01545  オニオニオン熱
     1D43  Oropouche virus disease
       H02163  オロプーシェ熱
     1D44  Rift Valley fever
       H01549  リフトバレー熱
     1D45  Sandfly fever
       H02164  サシチョウバエ熱
     1D46  West Nile virus infection
       H01548  ウエストナイル熱
     1D47  Yellow fever
       H00384  黄熱
     1D48  Zika virus disease
       H01553  ジカ熱
     1D49  Crimean-Congo haemorrhagic fever
       H00284  クリミア・コンゴ出血熱
     1D4A  Omsk haemorrhagic fever
       H00416  オムスク出血熱
     1D4B  Kyasanur Forest disease
       H01322  キャサヌル森林病
     1D4C  Alkhurma haemorrhagic fever
       H01560  アルハムラ出血熱
     1D4D  Ross River disease
       H00397  ロスリバー熱
     1D4E  Severe fever with thrombocytopenia syndrome
       H01416  重症熱性血小板減少症候群
     1D4Y  Other specified arthropod-borne viral fevers
       H01546  マヤロ熱
       H01550  ブニヤムウェラ熱
     1D4Z  Arthropod-borne viral fever, virus unspecified
   Certain zoonotic viral diseases
     1D60  Filovirus disease
       H00283  エボラ出血熱
       H00405  マールブルグ病
     1D61  Arenavirus disease
       H01541  アルゼンチン出血熱
       H01542  ボリビア出血熱
       H00386  ラッサ熱
       H01543  ベネズエラ出血熱
       H01544  ブラジル出血熱
     1D62  Hantavirus disease
       H00389  腎症候性出血熱
       H00390  ハンタウイルス肺症候群
     1D63  Henipavirus encephalitis
       H00391  ヘニパウイルス感染症
       H01538  ヘンドラウイルス感染症
       H01539  ニパウイルス感染症
     1D64  Middle East respiratory syndrome
       H01419  中東呼吸器症候群
     1D65  Severe acute respiratory syndrome
       H00402  重症急性呼吸器症候群
     1D6Y  Other specified zoonotic viral diseases
     1D6Z  Zoonotic viral disease, virus unspecified
   Certain other viral diseases
     1D80  Mumps
       H00396  流行性耳下腺炎
     1D81  Infectious mononucleosis
       H00367  伝染性単核症
     1D82  Cytomegaloviral disease
       H00368  サイトメガロウイルス感染症
     1D83  Epidemic myalgia
     1D84  Viral conjunctivitis
       H01320  流行性角結膜炎
       H00393  エンテロウイルス感染症
       H01421  急性出血性結膜炎
     1D85  Viral carditis
     1D86  Viral haemorrhagic fever, not elsewhere classified
     Viral infection of unspecified site
       1D90  Adenovirus infection of unspecified site
       1D91  Enterovirus infection of unspecified site
         H00393  エンテロウイルス感染症
       1D92  Coronavirus infection, unspecified site
       1D93  Parvovirus infection of unspecified site
       1D9Y  Other viral infections of unspecified site
       1D9Z  Unspecified viral infection of unspecified site
       1E1Y  Other specified viral diseases
       1E1Z  Unspecified viral disease
   Influenza
     1E30  Influenza due to seasonal identified influenza virus
       H00398  インフルエンザ
     1E31  Influenza due to identified zoonotic or pandemic influenza virus
       H00399  鳥インフルエンザ
     1E32  Influenza, virus not identified
   Viral hepatitis
     1E50  Acute viral hepatitis
       H02162  ウイルス性肝炎
       H00411  A型肝炎
       H00412  B型肝炎
       H00413  C型肝炎
       H00414  D型肝炎
       H00415  E型肝炎
     1E51  Chronic viral hepatitis
       H02162  ウイルス性肝炎
       H00412  B型肝炎
       H00413  C型肝炎
       H00414  D型肝炎
       H00415  E型肝炎
     1E5Z  Viral hepatitis, unspecified
   Viral infections characterised by skin or mucous membrane lesions
     Infections due to poxvirus
       1E70  Smallpox
         H00372  天然痘
       1E71  Monkeypox
         H00373  サル痘
       1E72  Cowpox
       1E73  Vaccinia
       1E74  Buffalopox
       1E75  Orf
       1E76  Molluscum contagiosum
         H01052  伝染性軟属腫
       1E7Y  Other specified infections due to poxvirus
       1E7Z  Infections due to poxvirus, unspecified
     Human papillomavirus infection of skin or mucous membrane
     Varicella zoster virus infections
       1E90  Varicella
         H00366  水痘
       1E91  Zoster
         H00366  水痘
         H01624  帯状疱疹後神経痛
       1F00  Herpes simplex infections
         H00365  単純ヘルペスウイルス感染症
       1F01  Roseola infantum
         H00369  突発性発疹
       1F02  Rubella
         H00395  風疹
       1F03  Measles
         H00394  麻疹
       1F04  Erythema infectiosum
         H00404  伝染性紅斑
       1F05  Picornavirus infections presenting in the skin or mucous membranes
         H00393  エンテロウイルス感染症
         H01327  ヘルパンギーナ
         H01326  手足口病
       1F0Y  Other specified viral infections characterised by skin or mucous membrane lesions
       1F0Z  Viral infections characterised by skin or mucous membrane lesions, unspecified
   Mycoses
     1F20  Aspergillosis
       H01328  アスペルギルス症
     1F21  Basidiobolomycosis
     1F22  Blastomycosis
       H01501  ブラストミセス症
     1F23  Candidosis
       H00363  カンジダ症
     1F24  Chromoblastomycosis
       H01520  クロモミコーシス
     1F25  Coccidioidomycosis
       H01319  コクシジオイデス症
     1F26  Conidiobolomycosis
     1F27  Cryptococcosis
       H00364  クリプトコッカス症
     1F28  Dermatophytosis
       H01316  皮膚糸状菌症
     1F29  Eumycetoma
     1F2A  Histoplasmosis
       H01062  ヒストプラスマ症
     1F2B  Lobomycosis
       H01518  ロボミコーシス
     1F2C  Mucormycosis
       H01503  接合菌症
       H02032  エントモフトラ症
       H02033  ムコール症
     1F2D  Non-dermatophyte superficial dermatomycoses
       H01334  癜風
     1F2E  Paracoccidioidomycosis
       H01329  パラコクシジオイデス症
     1F2F  Phaeohyphomycosis
     1F2G  Pneumocystosis
     1F2H  Scedosporiosis
     1F2J  Sporotrichosis
       H01499  スポロトリコーシス
     1F2K  Talaromycosis
     1F2Z  Mycoses, unspecified
   Parasitic diseases
     Malaria
       1F40  Malaria due to Plasmodium falciparum
         H00361  マラリア
       1F41  Malaria due to Plasmodium vivax
         H00361  マラリア
       1F42  Malaria due to Plasmodium malariae
         H00361  マラリア
       1F43  Malaria due to Plasmodium ovale
         H00361  マラリア
       1F44  Other parasitologically confirmed malaria
       1F45  Malaria without parasitological confirmation
       1F4Z  Malaria, unspecified
     Nonintestinal protozoal diseases
       1F50  Acanthamoebiasis
       1F51  African trypanosomiasis
         H00357  アフリカ睡眠病
       1F52  Babesiosis
         H01060  バベシア症
       1F53  Chagas disease
         H00358  シャーガス病
       1F54  Leishmaniasis
         H00359  リーシュマニア症
       1F55  Naegleriasis
       1F56  Rhinosporidiosis
       1F57  Toxoplasmosis
         H00435  トキソプラズマ症
       1F58  Microsporidiosis
         H01336  Encephalitozoon 感染
       1F5Z  Unspecified protozoal disease
     Helminthiases
       Diseases due to nematodes
         1F60  Angiostrongyliasis
         1F61  Anisakiasis
           H01058  アニサキス症
         1F62  Ascariasis
           H01090  回虫症
         1F63  Capillariasis
         1F64  Dracunculiasis
           H01044  メジナ虫症
         1F65  Enterobiasis
           H01091  蟯虫症
         1F66  Filariasis
           H02028  フィラリア症、糸状虫症
           H01104  ロア糸状虫症
           H01061  マンソネラ症
           H01086  リンパ管フィラリア
         1F67  Gnathostomiasis
           H01057  顎口虫症
         1F68  Hookworm diseases
           H01092  鉤虫症
         1F69  Oesophagostomiasis
         1F6A  Onchocerciasis
           H01043  オンコセルカ症
         1F6B  Strongyloidiasis
           H01100  糞線虫症
         1F6C  Syngamosis
         1F6D  Toxocariasis
           H01056  トキソカラ症
         1F6E  Trichinosis
           H01099  旋毛虫症
         1F6F  Trichostrongyliasis
         1F6G  Trichuriasis
           H01046  鞭虫症
         1F6H  Uncinariosis
         1F6Y  Other specified diseases due to nematodes
         1F6Z  Diseases due to nematodes, unspecified
       Diseases due to cestodes
         1F70  Cysticercosis
           H01047  嚢虫症
         1F71  Diphyllobothriasis
           H01085  裂頭条虫症
         1F72  Dipylidiasis
         1F73  Echinococcosis
           H01153  エキノコックス症
         1F74  Hymenolepiasis
           H01138  膜様条虫症
         1F75  Sparganosis
           H01014  孤虫症
         1F76  Taeniasis
           H01047  嚢虫症
           H01152  Taenia saginata 感染
         1F7Y  Other specified diseases due to cestodes
         1F7Z  Diseases due to cestodes, unspecified
       Diseases due to trematodes
         1F80  Clonorchiasis
           H01610  肝吸虫症
         1F81  Dicrocoeliasis
         1F82  Fascioliasis
           H01048  肝蛭症
         1F83  Fasciolopsiasis
           H01107  肥大吸虫症
         1F84  Opisthorchiasis
           H01628  オピストルキス症
         1F85  Paragonimiasis
           H01093  肺吸虫症
         1F86  Schistosomiasis
           H01045  住血吸虫症
         1F8Y  Other specified diseases due to trematodes
           H01617  食物媒介吸虫類感染症
         1F8Z  Diseases due to trematodes, unspecified
         1F90  Other and unspecified infestation by parasitic worms
         1F91  Diphyllobothriasis and sparganosis
         1F9Z  Helminthiases, unspecified
           H01055  腎虫症
     Infestations by ectoparasites
       1G00  Pediculosis
         H01054  しらみ寄生症
       1G01  Myiasis
         H01178  ハエ幼虫症
       1G02  External hirudiniasis
       1G03  Phthiriasis
       1G04  Scabies
         H01519  疥癬
       1G05  Tungiasis
         H01179  スナノミ症
       1G06  Cimicosis
       1G07  Infestation by mites
       1G0Z  Infestation by unknown or unspecified ectoparasite
         H01098  舌虫症
       1G2Y  Other specified parasitic diseases
       1G2Z  Unspecified parasitic diseases
   Sepsis
   Sequelae of infectious diseases
     1G80  Sequelae of tuberculosis
     1G81  Sequelae of trachoma
     1G82  Sequelae of leprosy
     1G83  Sequelae of poliomyelitis
     1G84  Sequelae of viral encephalitis
     1G85  Sequelae of diphtheria
     1G8Y  Sequelae of other specified infectious diseases
     1H0Z  Infection, unspecified
 
 02 Neoplasms
   Neoplasms of brain or central nervous system
     2A00  Primary neoplasms of brain
       H00042  神経膠腫
       H01692  上衣下巨細胞性星細胞腫
       H01667  髄芽腫
       H01007  脈絡叢乳頭腫
     2A01  Primary neoplasms of meninges
       H01556  髄膜腫
     2A02  Primary neoplasm of spinal cord, cranial nerves or remaining parts of central nervous system
       H00043  神経芽腫
     2A0Z  Other and unspecified neoplasms of brain or central nervous system
   Neoplasms of haematopoietic or lymphoid tissues
     Myeloproliferative neoplasms
       2A20  Non mast cell myeloproliferative neoplasms
         H00004  慢性骨髄性白血病 (CML)
         H01605  骨髄線維症
         H01590  慢性好酸球性白血病
         H01599  好酸球増多症候群
         H00012  真性赤血球増加症
       2A21  Mastocytosis
         H01511  肥満細胞白血病
       2A22  Other and unspecified myeloproliferative neoplasms
     Myelodysplastic syndromes
       2A30  Refractory anaemia
       2A31  Refractory neutropenia
       2A32  Refractory thrombocytopenia
       2A33  Refractory anaemia with ring sideroblasts
       2A34  Refractory cytopenia with multi-lineage dysplasia
       2A35  Refractory anaemia with excess of blasts
       2A36  Myelodysplastic syndrome with isolated del(5q)
         H01481  骨髄異形成症候群
         H01484  5q- 症候群
       2A37  Myelodysplastic syndrome, unclassifiable
         H01481  骨髄異形成症候群
       2A38  Refractory cytopenia of childhood
       2A3Y  Other specified myelodysplastic syndromes
       2A3Z  Myelodysplastic syndromes, unspecified
         H01481  骨髄異形成症候群
     Myelodysplastic and myeloproliferative neoplasms
     Myeloid and lymphoid neoplasms with eosinophilia and abnormalities of PDGFRA, PDGFRB or FGFR1
       2A50  Myeloid neoplasm associated with PDGFRA rearrangement
       2A51  Myeloid neoplasm associated with PDGFRB rearrangement
       2A52  Myeloid or lymphoid neoplasms with FGFR1 abnormalities
       2A5Z  Myeloid and lymphoid neoplasms with eosinophilia and abnormalities of PDGFRA, PDGFRB or FGFR1, unspecified
       2A60  Acute myeloid leukaemias and related precursor neoplasms
         H00003  急性骨髄性白血病 (AML)
       2A61  Acute leukaemias of ambiguous lineage
     Precursor lymphoid neoplasms
       2A70  Precursor B-lymphoblastic neoplasms
         H00001  Bリンパ芽球性白血病/リンパ腫
       2A71  Precursor T-lymphoblastic neoplasms
         H00002  Tリンパ芽球性白血病/リンパ腫
       2A7Z  Precursor lymphoid neoplasms, unspecified
     Mature B-cell neoplasms
       2A80  Follicular lymphoma
         H01613  濾胞性リンパ腫
       2A81  Diffuse large B-cell lymphomas
       2A82  Mature B-cell neoplasm with leukaemic behaviour
         H00005  慢性リンパ性白血病 (CLL)
         H00006  毛様細胞性白血病
       2A83  Plasma cell neoplasms
         H00010  多発性骨髄腫
         H01461  クロウ・深瀬症候群
       2A84  Heavy chain diseases or malignant immunoproliferative diseases
       2A85  Other specified mature B-cell neoplasms or lymphoma
         H00011  リンパ形質細胞性リンパ腫
         H01464  マントル細胞リンパ腫
         H00008  バーキットリンパ腫
       2A86  B-cell lymphoma, mixed features
       2A8Z  Mature B-cell neoplasms, unspecified
     Mature T-cell or NK-cell neoplasms
       2A90  Mature T-cell lymphoma, specified types, nodal or systemic
         H01892  末梢性T細胞リンパ腫
         H00009  成人T細胞性白血病
         H01601  未分化大細胞リンパ腫
       Mature T-cell or NK-cell lymphoma, primary cutaneous specified types
         2B00  Subcutaneous panniculitis-like T-cell lymphoma
         2B01  Mycosis fungoides
           H01463  菌状息肉腫
         2B02  Sézary syndrome
         2B03  Primary cutaneous CD-30 positive T-cell lymphoproliferative disorders
         2B0Y  Other specified T cell lymphomas of the skin
         2B0Z  Primary cutaneous T-cell lymphoma of undetermined or unspecified type
         2B2Y  Other specified mature T-cell or NK-cell neoplasms
         2B2Z  Mature T-cell or NK-cell neoplasms, unspecified
         2B30  Hodgkin lymphoma
           H00007  ホジキンリンパ腫
         2B31  Histiocytic or dendritic cell neoplasms
           H01512  ランゲルハンス細胞組織球症
         2B32  Immunodeficiency-associated lymphoproliferative disorders
         2B33  Malignant haematopoietic neoplasms without further specification
         2B3Z  Neoplasms of haematopoietic or lymphoid tissues, unspecified
   Malignant neoplasms, except of lymphoid, haematopoietic, central nervous system or related tissues
     Malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphoid, haematopoietic, central nervous system or related tissues
       Malignant mesenchymal neoplasms
         2B50  Chondrosarcoma, primary site
           H00053  粘液様軟骨肉腫
         2B51  Osteosarcoma, primary site
           H00036  骨肉腫
           H01470  骨巨細胞腫
           H00881  リー・フラウメニ症候群
         2B52  Ewing sarcoma, primary site
           H00035  ユーイング肉腫
         2B53  Fibroblastic or myofibroblastic tumour, primary site
         2B54  Unclassified pleomorphic sarcoma, primary site
         2B55  Rhabdomyosarcoma, primary site
           H00037  胞巣状横紋筋肉腫
         2B56  Angiosarcoma, primary site
           H01666  血管肉腫
           H01557  肝血管肉腫
         2B57  Kaposi sarcoma, primary site
           H00041  カポジ肉腫
         2B58  Leiomyosarcoma, primary site
         2B59  Liposarcoma, primary site
           H00049  粘液様脂肪肉腫
         2B5A  Synovial sarcoma, primary site
           H00050  滑膜肉腫
         2B5B  Gastrointestinal stromal tumour, primary site
           H01591  消化管間質腫瘍
         2B5C  Endometrial stromal sarcoma, primary site
         2B5D  Malignant mixed epithelial mesenchymal tumour, primary site
         2B5E  Malignant nerve sheath tumour of peripheral nerves or autonomic nervous system, primary site
         2B5F  Sarcoma, not elsewhere classified, primary site
         2B5G  Myosarcoma of uterus, part not specified
         2B5H  Well differentiated lipomatous tumour, primary site
         2B5J  Malignant miscellaneous bone tumours of bone or articular cartilage of other or unspecified sites
         2B5K  Unspecified malignant soft tissue tumours or sarcomas of bone or articular cartilage of other or unspecified sites
           H00051  胞巣状軟部肉腫
           H00052  明細胞肉腫
           H01985  繊維形成性小円形細胞腫瘍
         2B5Y  Other specified malignant mesenchymal neoplasms
         2B5Z  Malignant mesenchymal neoplasm of unspecified type or site
       Malignant neoplasms of lip, oral cavity or pharynx
         2B60  Malignant neoplasms of lip
           H00016  口腔癌
         2B61  Malignant neoplasms of base of tongue
           H00016  口腔癌
         2B62  Malignant neoplasms of other or unspecified parts of tongue
           H00016  口腔癌
         2B63  Malignant neoplasms of gum
           H00016  口腔癌
         2B64  Malignant neoplasms of floor of mouth
           H00016  口腔癌
         2B65  Malignant neoplasms of palate
           H00016  口腔癌
         2B66  Malignant neoplasms of other or unspecified parts of mouth
           H00016  口腔癌
         2B67  Malignant neoplasms of parotid gland
         2B68  Malignant neoplasms of submandibular or sublingual glands
           H01508  唾液腺癌
         2B69  Malignant neoplasms of tonsil
           H01509  扁桃癌
         2B6A  Malignant neoplasms of oropharynx
           H01559  中咽頭癌
         2B6B  Malignant neoplasms of nasopharynx
           H00054  鼻咽頭癌
         2B6C  Malignant neoplasms of piriform sinus
         2B6D  Malignant neoplasms of hypopharynx
         2B6E  Malignant neoplasms of other or ill-defined sites in the lip, oral cavity or pharynx
         2B6Y  Other specified malignant neoplasms of lip, oral cavity or pharynx
         2B6Z  Malignant neoplasms of lip, oral cavity or pharynx, unspecified
       Malignant neoplasms of digestive organs
         2B70  Malignant neoplasms of oesophagus
           H00017  食道癌
         2B71  Malignant neoplasms of oesophagogastric junction
         2B72  Malignant neoplasms of stomach
           H00018  胃癌
         Malignant neoplasms of intestine
           2B80  Malignant neoplasms of small intestine
             H00034  カルチノイド
           2B81  Malignant neoplasms of appendix
           Malignant neoplasms of large intestine
             2B90  Malignant neoplasms of colon
               H00020  結腸直腸癌
             2B91  Malignant neoplasms of rectosigmoid junction
               H00020  結腸直腸癌
             2B92  Malignant neoplasms of rectum
               H00020  結腸直腸癌
             2B93  Malignant neoplasms of large intestine, site unspecified
             2B9Y  Other specified malignant neoplasms of large intestine
             2B9Z  Malignant neoplasms of large intestine, unspecified
             2C00  Malignant neoplasms of anus or anal canal
               H00044  肛門管癌
             2C0Y  Other specified malignant neoplasms of intestine
             2C0Z  Malignant neoplasms of intestine, unspecified
             2C10  Malignant neoplasm of pancreas
               H00019  膵癌
               H00045  膵神経内分泌腫瘍
             2C11  Malignant neoplasms of other or ill-defined digestive organs
             2C12  Malignant neoplasms of liver or intrahepatic bile ducts
               H00048  肝細胞癌
               H00046  胆管癌
             2C13  Malignant neoplasms of gallbladder
               H00047  胆嚢癌
             2C14  Malignant neoplasms of proximal biliary tract, cystic duct
             2C15  Malignant neoplasms of biliary tract, distal bile duct
             2C16  Malignant neoplasms of ampulla of Vater
             2C17  Malignant neoplasms of other or unspecified parts of biliary tract
             2C18  Malignant neoplasms of perihilar bile duct
             2C1Z  Malignant neoplasms of digestive organs, unspecified
       Malignant neoplasms of middle ear, respiratory or intrathoracic organs
         2C20  Malignant neoplasms of nasal cavity
           H00043  神経芽腫
         2C21  Malignant neoplasms of middle ear
         2C22  Malignant neoplasms of accessory sinuses
         2C23  Malignant neoplasms of larynx
           H00055  喉頭癌
         2C24  Malignant neoplasms of trachea
         2C25  Malignant neoplasms of bronchus or lung
           H00014  非小細胞肺癌
           H00013  小細胞肺癌
         2C26  Malignant neoplasms of the pleura
           H00015  悪性胸膜中皮腫
         2C27  Malignant neoplasms of thymus
         2C28  Malignant neoplasms of heart, mediastinum or non-mesothelioma of pleura
         2C29  Malignant neoplasms of other or ill-defined sites in the respiratory system or intrathoracic organs
         2C2Y  Other specified malignant neoplasms of middle ear, respiratory or intrathoracic organs
         2C2Z  Malignant neoplasms of middle ear, respiratory or intrathoracic organs, unspecified
       Malignant neoplasms of skin
         2C30  Melanoma of skin
           H00038  悪性黒色腫
         2C31  Squamous cell carcinoma of skin
           H00040  有棘細胞癌
         2C32  Basal cell carcinoma of skin
           H00039  基底細胞癌
         2C33  Adnexal carcinoma of skin
         2C34  Cutaneous neuroendocrine carcinoma
           H01555  メルケル細胞癌
         2C35  Cutaneous sarcoma
         2C36  Malignant neoplasm of eyelid NOS
         2C37  Malignant pilonidal cyst
         2C3Y  Other specified malignant neoplasms of skin
         2C3Z  Malignant neoplasm of skin of unknown or unspecified type
       Malignant neoplasms of peripheral nerves or autonomic nervous system
       Malignant neoplasms of retroperitoneum, peritoneum or omentum
         2C50  Malignant neoplasms of retroperitoneum
         2C51  Malignant neoplasms of peritoneum
           H01665  原発性腹膜癌
         2C52  Malignant neoplasms of omentum
         2C53  Overlapping malignant neoplasm of retroperitoneum, peritoneum or omentum
         2C5Y  Other specified malignant neoplasms of retroperitoneum, peritoneum or omentum
         2C5Z  Malignant neoplasms of retroperitoneum, peritoneum or omentum, unspecified
       Malignant neoplasms of breast
         2C60  Carcinoma of breast, specialised type
         2C61  Invasive carcinoma of breast
           H00031  乳癌
         2C62  Inflammatory carcinoma of breast
         2C63  Malignant phyllodes tumour of breast
         2C64  Solid papillary carcinoma of breast with evidence of invasion
         2C65  Hereditary breast and ovarian cancer syndrome
         2C6Y  Other specified malignant neoplasms of breast
         2C6Z  Malignant neoplasms of breast, unspecified
       Malignant neoplasms of female genital organs
         2C70  Malignant neoplasms of vulva
           H00029  外陰癌
         2C71  Malignant neoplasms of vagina
         2C72  Malignant neoplasms of uterine ligament, parametrium, or uterine adnexa
         2C73  Malignant neoplasms of ovary
           H00027  卵巣癌
         2C74  Malignant neoplasms of fallopian tube
           H01554  卵管癌
         2C75  Malignant neoplasms of placenta
           H00028  絨毛癌
         2C76  Malignant neoplasms of corpus uteri
           H00026  子宮内膜癌
         2C77  Malignant neoplasms of cervix uteri
           H00030  子宮頸癌
         2C78  Malignant neoplasms of uterus, part not specified
         2C7Y  Other specified malignant neoplasms of female genital organs
         2C7Z  Malignant neoplasms of female genital organs, unspecified
       Malignant neoplasms of male genital organs
         2C80  Malignant neoplasms of testis
           H00023  精巣癌
         2C81  Malignant neoplasms of penis
           H00025  陰茎癌
         2C82  Malignant neoplasms of prostate
           H00024  前立腺癌
         2C83  Malignant neoplasms of scrotum
         2C84  Malignant neoplasms of other specified male genital organs
         2C8Z  Malignant neoplasms of male genital organs, unspecified
       Malignant neoplasms of urinary tract
         2C90  Malignant neoplasms of kidney, except renal pelvis
           H00021  腎細胞癌
         2C91  Malignant neoplasms of renal pelvis
         2C92  Malignant neoplasms of ureter
         2C93  Malignant neoplasms of urethra or paraurethral gland
         2C94  Malignant neoplasms of bladder
           H00022  膀胱癌
         2C95  Malignant overlapping lesion of urinary organs
         2C9Y  Other specified malignant neoplasms of urinary tract
         2C9Z  Malignant neoplasms of urinary tract, unspecified
       Malignant neoplasms of eye or ocular adnexa
         2D00  Malignant neoplasm of conjunctiva
         2D01  Malignant neoplasm of cornea
         2D02  Malignant neoplasm of retina
           H01513  網膜芽細胞腫
         2D03  Malignant neoplasm of lacrimal apparatus
         2D04  Malignant neoplasm of orbit
         2D05  Malignant neoplasm of choroid
         2D06  Malignant neoplasm of ciliary body
         2D07  Malignant neoplasm of iris
         2D0Y  Other specified malignant neoplasms of eye and ocular adnexa
         2D0Z  Malignant neoplasms of eye or ocular adnexa, unspecified
       Malignant neoplasms of endocrine glands
         2D10  Malignant neoplasms of thyroid gland
           H00032  甲状腺癌
           H01592  甲状腺髄様癌
         2D11  Malignant neoplasms of adrenal gland
           H00033  副腎癌
         2D12  Malignant neoplasms of other endocrine glands or related structures
           H01510  悪性傍神経節腫
         2D1Y  Other specified malignant neoplasms of endocrine glands
         2D1Z  Malignant neoplasms of endocrine glands, unspecified
         2D3Y  Other specified malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphoid, haematopoietic, central nervous system or related tissues
         2D3Z  Malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphoid, haematopoietic, central nervous system or related tissues, unspecified
     Malignant neoplasms of ill-defined or unspecified primary sites
     Malignant neoplasm metastases
   In situ neoplasms, except of lymphoid, haematopoietic, central nervous system or related tissues
     2E60  Carcinoma in situ of oral cavity, oesophagus or stomach
     2E61  Carcinoma in situ of other or unspecified digestive organs
     2E62  Carcinoma in situ of middle ear or respiratory system
     2E63  Melanoma in situ neoplasms
     2E64  Carcinoma in situ of skin
     2E65  Carcinoma in situ of breast
     2E66  Carcinoma in situ of cervix uteri
     2E67  Carcinoma in situ of other or unspecified genital organs
     2E68  Carcinoma in situ of bladder
     2E69  Carcinoma in situ of other or unspecified urinary organs
     2E6A  Carcinoma in situ of the eye or ocular adnexa
     2E6B  Carcinoma in situ of thyroid and other endocrine glands
       H01558  副甲状腺癌
     2E6Y  Carcinoma in situ of other specified site
     2E6Z  Carcinoma in situ of unspecified site
   Benign neoplasms, except of lymphoid, haematopoietic, central nervous system or related tissues
     Benign mesenchymal neoplasms
       2E80  Benign lipomatous neoplasm
       2E81  Benign vascular neoplasms
         H01471  リンパ管腫
         H01735  リンパ管腫症
         H01482  乳児血管腫
         H01875  乳幼児肝血管腫
       2E82  Benign chondrogenic tumours
       2E83  Benign osteogenic tumours
       2E84  Benign fibrogenic or myofibrogenic tumour
       2E85  Benign fibrohistiocytic tumour
       2E86  Benign smooth muscle or skeletal muscle tumour
         H01640  子宮筋腫
       2E87  Benign gastrointestinal stromal tumour
       2E88  Benign endometrial stromal tumour
       2E89  Benign mesenchymal tumours of uncertain differentiation
       2E8A  Other mixed or unspecified benign mesenchymal tumours
       2E8Y  Benign neoplasm of mesothelial tissue, other specified organs
       2E8Z  Benign mesenchymal neoplasms, unspecified
         H00804  Multiple cutaneous and uterine leiomyomata
     Benign non-mesenchymal neoplasms
       2E90  Benign neoplasm of lip, oral cavity or pharynx
       2E91  Benign neoplasm of major salivary glands
       2E92  Benign neoplasm of digestive organs
         H01025  家族性大腸ポリポーシス
         H00539  PTEN過誤腫症候群
         H01023  若年性ポリポーシス症候群
         H01024  遺伝性混合ポリポーシス症候群
       Benign neoplasm of respiratory or intrathoracic organs
       Benign cutaneous neoplasms
         2F20  Benign cutaneous melanocytic neoplasms
         2F21  Benign keratinocytic acanthomas
         2F22  Benign neoplasms of epidermal appendages
           H00827  Brooke-Spiegler 症候群
           H00828  家族性円柱腫症
           H00829  多発性家族性毛包上皮腫
           H00947  毛母腫
         2F23  Benign dermal fibrous or fibrohistiocytic neoplasms
           H01910  乳児筋線維腫症
         2F24  Benign cutaneous neoplasms of neural or nerve sheath origin
         2F25  Cherry angioma
         2F26  Lobular capillary haemangioma
         2F2Y  Other specified benign cutaneous neoplasms
         2F2Z  Benign cutaneous neoplasm of unspecified type
         2F30  Benign neoplasm of breast
         2F31  Non-mesenchymal benign neoplasms of uterus
         2F32  Benign neoplasm of ovary
         2F33  Benign neoplasm of other or unspecified female genital organs
         2F34  Benign neoplasm of male genital organs
         2F35  Benign neoplasm of urinary organs
           H01691  腎血管筋脂肪腫
         2F36  Benign neoplasm of eye or ocular adnexa
           H01149  角膜輪状類皮
         2F37  Benign neoplasm of endocrine glands
           H01102  下垂体腺腫
         2F38  Benign neoplasm of other or unspecified sites
         2F3Y  Other specified benign non-mesenchymal neoplasms
         2F3Z  Benign non-mesenchymal neoplasms, unspecified
         2F5Y  Other specified benign neoplasms, except of lymphoid, haematopoietic, central nervous system or related tissues
         2F5Z  Benign neoplasms, except of lymphoid, haematopoietic, central nervous system or related tissues, unspecified
   Neoplasms of uncertain behaviour, except of lymphoid, haematopoietic, central nervous system or related tissues
     2F70  Neoplasms of uncertain behaviour of oral cavity or digestive organs
     2F71  Neoplasms of uncertain behaviour of middle ear, respiratory or intrathoracic organs
     2F72  Neoplasms of uncertain behaviour of skin
     2F73  Neoplasms of uncertain behaviour of retroperitoneum
     2F74  Neoplasms of uncertain behaviour of peritoneum
     2F75  Neoplasms of uncertain behaviour of breast
     2F76  Neoplasms of uncertain behaviour of female genital organs
     2F77  Neoplasms of uncertain behaviour of male genital organs
     2F78  Neoplasms of uncertain behaviour of urinary organs
     2F79  Neoplasms of uncertain behaviour of eye or ocular adnexa
     2F7A  Neoplasms of uncertain behaviour of endocrine glands
       H00247  多発性内分泌腫瘍症候群
     2F7B  Neoplasms of uncertain behaviour of bone or articular cartilage
     2F7C  Neoplasms of uncertain behaviour of connective or other soft tissue
     2F7Y  Neoplasms of uncertain behaviour of other specified site
     2F7Z  Neoplasms of uncertain behaviour of unspecified site
   Neoplasms of unknown behaviour, except of lymphoid, haematopoietic, central nervous system or related tissues
 
 03 Diseases of the blood or blood-forming organs
   Anaemias or other erythrocyte disorders
     Nutritional or metabolic anaemias
       3A00  Iron deficiency anaemia
         H01145  無トランスフェリン血症
         H01196  小球性低色素性貧血
         H01278  鉄剤不応性鉄欠乏性貧血
         H02206  無セルロプラスミン血症
       3A01  Megaloblastic anaemia due to vitamin B12 deficiency
         H01277  ビタミン B12 欠乏性貧血
         H01190  トランスコバラミン II 欠乏症
       3A02  Folate deficiency anaemia
         H01197  ジヒドロ葉酸還元酵素欠損症
         H01262  ホルムイミノトランスフェラーゼ欠損症
       3A03  Other nutritional or metabolic anaemias
         H00198  オロト酸尿症
     Haemolytic anaemias
       Congenital haemolytic anaemia
         3A10  Hereditary haemolytic anaemia
           H00668  グルタチオン代謝障害による貧血
           H01375  グルコース-6-リン酸脱水素酵素欠損症
           H00231  遺伝性楕円赤血球症
           H01125  熱変形赤血球症
           H02001  家族性偽高カリウム血症
           H00230  遺伝性球状赤血球症
           H00232  遺伝性有口赤血球症
           H00664  解糖系酵素障害による貧血
           H00674  ヌクレオチド代謝障害による貧血
           H00832  中核群神経有棘赤血球症
           H01214  Rh欠損症候群
           H01432  有棘赤血球を伴う舞踏病
           H01434  非典型溶血性尿毒症症候群
           H01720  東南アジア楕円赤血球症
           H01978  乾性遺伝性有口赤血球症
           H01979  水分過剰遺伝性有口赤血球症
           H02002  Cryohydrocytosis
         3A1Y  Other specified congenital haemolytic anaemia
       Acquired haemolytic anaemia
         3A20  Acquired haemolytic anaemia, immune
           H01585  自己免疫性溶血性貧血
         3A21  Acquired haemolytic anaemia, non-immune
           H01053  発作性夜間ヘモグロビン尿症
         3A2Z  Acquired haemolytic anaemia, unspecified
         3A4Z  Haemolytic anaemias, unspecified
         3A50  Thalassaemias
           H00228  サラセミア
         3A51  Sickle cell disorders or other haemoglobinopathies
           H00229  鎌状赤血球貧血
     Pure red cell aplasia
       3A60  Congenital pure red cell aplasia
         H00237  ダイアモンド・ブラックファン貧血
       3A61  Acquired pure red cell aplasia
         H01586  後天性赤芽球癆
       3A6Z  Pure red cell aplasia, unspecified
       3A70  Aplastic anaemia
         H01132  再生不良性貧血
         H00238  ファンコニー貧血
         H00439  シュバッハマン・ダイアモンド症候群
         H00507  先天性角化異常症
         H00788  Hoyeraal-Hreidarsson 症候群
       3A71  Anaemia due to chronic disease
         H01642  腎性貧血
       3A72  Sideroblastic anaemia
         H00982  遺伝性鉄芽球性貧血
         H00898  ミトコンドリアミオパチー及び鉄芽球性貧血
       3A73  Congenital dyserythropoietic anaemia
         H00917  先天性赤血球形成異常性貧血
     Polycythaemia
       3A80  Congenital polycythaemia
         H00236  先天性赤血球増加症
       3A81  Acquired polycythaemia
       3A8Z  Polycythaemia, unspecified
       3A90  Anaemia of acute disease
       3A91  Congenital methaemoglobinaemia
         H00235  メトヘモグロビン血症
       3A92  Hereditary methaemoglobinaemia
         H00235  メトヘモグロビン血症
       3A93  Acquired methaemoglobinaemia
       3A9Y  Other specified anaemias and erythrocyte disorders
       3A9Z  Anaemias or other erythrocyte disorders, unspecified
   Coagulation defects, purpura or other haemorrhagic or related conditions
     Coagulation defects
       Congenital or constitutional haemorrhagic condition
         3B10  Hereditary factor VIII deficiency
           H00219  血友病
         3B11  Hereditary factor IX deficiency
           H00219  血友病
         3B12  Von Willebrand disease
           H00219  血友病
           H02092  フォンウィレブランド病
         3B13  Haemophilia C
           H00938  先天性第XI因子欠乏症
         3B14  Other inherited coagulation factor deficiency with bleeding tendency
           H01254  プロトロンビン欠乏症
           H00222  無フィブリノゲン血症
           H02257  先天性第X因子欠乏症
           H00995  ビタミン K 欠乏による凝固因子欠乏
           H02256  先天性第VII因子欠乏症
           H00220  第V因子欠損症
           H00221  第Vおよび第VIII因子合併欠乏症
           H00945  先天性第XIII因子欠乏症
         3B15  Inherited coagulation factor deficiency without bleeding tendency
           H00941  先天性第XII因子欠乏症
           H01078  Fletcher因子欠乏症
         3B1Z  Congenital or constitutional haemorrhagic condition, unspecified
       Haemorrhagic diseases due to acquired coagulation factor defects
         3B20  Disseminated intravascular coagulation
           H01587  播種性血管内凝固症候群
         3B21  Haemorrhagic disorder due to circulating anticoagulants and coagulation factors
         3B22  Acquired haemophilia
         3B2Y  Other specified haemorrhagic diseases due to acquired coagulation factor defects
         3B4Z  Coagulation defects, unspecified
     Fibrinolytic defects
       3B50  Inherited fibrinolytic defects
         H00983  先天性アルファ2プラスミンインヒビター欠損症
         H01106  プラスミノーゲン活性化因子インヒビター1欠損症
         H01206  プラスミノーゲン欠損症
       3B51  Acquired fibrinolytic defects
       3B60  Non-thrombocytopenic purpura
       3B61  Thrombophilia
         H00223  遺伝性血栓形成傾向
         H01381  先天性アンチトロンビン欠損症
       3B62  Qualitative platelet defects
         H01235  血小板型出血性疾患
         H02097  灰色血小板症候群
         H00224  ベルナール・スーリエ症候群
         H00226  グランツマン血小板無力症
         H01523  ウィスコット・アルドリッチ症候群
         H01162  スコット症候群
         H02093  血小板型フォンウィレブランド病
         H02259  Stormorken 症候群
       3B63  Thrombocytosis
         H01612  本態性血小板血症
       3B64  Thrombocytopenia
         H00978  血小板減少症
         H00227  先天性無巨核球性血小板減少症
         H00233  MYH9 異常症
         H00578  エプスタイン症候群
         H00867  無巨核球性血小板減少を伴う橈尺骨癒合症
         H01740  巨大血小板性血小板減少症
         H01847  血小板減少-橈骨欠損症候群
         H02052  セバスチャン症候群
         H02053  フェクトナー症候群
         H01240  自己免疫性血小板減少性紫斑病
         H00225  血栓性血小板減少性紫斑病
       3B65  Thrombotic microangiopathy, not elsewhere classified
       3B6Y  Other specified coagulation defects, purpura or other haemorrhagic or related conditions
       3B6Z  Coagulation defects, purpura or other haemorrhagic or related conditions, unspecified
   Diseases of spleen
 
 04 Diseases of the immune system
   Primary immunodeficiencies
     4A00  Primary immunodeficiencies due to disorders of innate immunity
       H01725  原発性免疫不全症
       H00098  慢性肉芽腫症
       H02024  好中球二次顆粒欠損症
       H02025  ミエロペルオキシダーゼ欠損症
       H00102  古典的補体経路の構成要素の障害
       H00103  後期補体経路の障害
       H01006  遺伝性血管性浮腫
       H00105  マンノース結合レクチン経路の構成要素の障害
       H00106  補体制御タンパクの障害
       H01136  カルボキシペプチダーゼN 欠損症
       H00096  Toll様受容体シグナル伝達系の障害
       H00721  Pyogenic bacterial infections, recurrent, due to MYD88 deficiency
       H00090  NK細胞障害
       H00097  ケモカイン受容体障害
       H01117  慢性再発性多発性骨髄炎
     4A01  Primary immunodeficiencies due to disorders of adaptive immunity
       H01725  原発性免疫不全症
       H00085  無ガンマグロブリン血症
       H00086  高 IgM 症候群、常染色体劣性型
       H00088  分類不能型免疫不全症
       H00093  複合免疫不全症
       H00091  T-B+ 重症複合免疫不全症
       H00092  T-B- 重症複合免疫不全症
       H01128  細網異形成症
       H01244  T+B+ 重症複合免疫不全症
       H00984  露出リンパ球症候群 1 型
       H00985  露出リンパ球症候群 2 型
       H00087  他の体液性免疫不全症
       H00924  NHEJ1 症候群
       H01181  T-cell immunodeficiency congenital alopecia and nail dystrophy
       H02015  LIG4 症候群
       H02133  Vici 症候群
       H01971  IPEX 症候群
       H00108  自己免疫性リンパ増殖症候群
       H01969  X連鎖性リンパ球増殖症候群
       H01970  リンパ球増殖症候群 1型
       H00109  家族性血球貪食症候群
       H00064  毛細血管拡張性運動失調症
       H00094  DNA修復障害に伴う免疫不全症
       H00962  RIDDLE 症候群
       H01344  ナイミーヘン症候群
       H01346  ブルーム症候群
       H02014  毛細血管拡張性運動失調様症候群
       H00580  シムケ免疫性骨形成不全
       H01264  免疫不全を伴う肝静脈閉塞性疾患
       H01968  高 IgE 症候群
     4A0Y  Other specified primary immunodeficiencies
       H01245  外胚葉異形成症を伴わない免疫不全症
     4A0Z  Primary immunodeficiencies, unspecified
     4A20  Acquired immunodeficiencies
       H00406  後天性免疫不全症候群 (AIDS)
   Non-organ specific systemic autoimmune disorders
     4A40  Lupus erythematosus
       H00080  全身性エリテマトーデス
       H01500  ループス腎炎
     4A41  Idiopathic inflammatory myopathy
       H01604  皮膚筋炎/多発性筋炎
       H01229  Inclusion body myopathy 3
       H01505  封入体筋炎
       H02031  骨パジェット病および前頭側頭型痴呆をともなう封入体ミオパチー
     4A42  Systemic sclerosis
       H01492  全身性強皮症
     4A43  Overlap or undifferentiated non-organ specific systemic autoimmune disease
       H01761  IgG4 関連疾患
       H01502  シェーグレン症候群
       H01710  混合性結合組織病
       H01693  好酸球性筋膜炎
       H01133  Reynolds 症候群
       H01232  Syndromic multisystem autoimmune disease
     4A44  Vasculitis
       H01698  巨細胞性動脈炎
       H01382  結節性多発動脈炎
       H01718  川崎病
       H01625  バージャー病
       H01584  IgA 血管炎
       H01767  紫斑病性腎炎
       H01658  顕微鏡的多発血管炎
       H01655  多発血管炎性肉芽腫症
       H01468  好酸球性多発血管炎性肉芽腫症
       H01465  大型血管炎
     4A45  Antiphospholipid syndrome
       H01697  抗リン脂質抗体症候群
     4A4Y  Other specified non-organ specific systemic autoimmune disorders
     4A4Z  Non-organ specific systemic autoimmune disorders, unspecified
   Autoinflammatory disorders
     4A60  Monogenic autoinflammatory syndromes
       H00288  家族性地中海熱
       H00282  クリオピリン関連周期熱症候群
       H02159  家族性寒冷自己炎症症候群
       H00912  TNF受容体関連周期性症候群
       H00285  ブラウ症候群
       H00287  化膿性無菌性関節炎・壊疽性膿皮症・アクネ症候群
       H01743  自己炎症合併フォスフォリパーゼCγ2関連抗体欠損・免疫異常症
       H01744  HOIL-1 欠損症
     4A61  SAPHO syndrome
     4A62  Behçet disease
       H01476  ベーチェット病
     4A6Y  Other specified autoinflammatory disorders
       H01748  Autoinflammation with infantile enterocolitis
     4A6Z  Autoinflammatory disorders, unspecified
   Allergic or hypersensitivity conditions
     4A80  Allergic or hypersensitivity disorders involving the respiratory tract
     4A81  Allergic or hypersensitivity disorders involving the eye
     4A82  Allergic or hypersensitivity disorders involving skin or mucous membranes
     4A83  Allergic or hypersensitivity disorders involving the gastrointestinal tract
     4A84  Anaphylaxis
       H01359  アナフィラキシー
     4A85  Complex allergic or hypersensitivity conditions
     4A8Y  Allergic or hypersensitivity conditions of other specified type
     4A8Z  Allergic or hypersensitivity conditions of unspecified type
   Immune system disorders involving white cell lineages
     4B00  Disorders of neutrophil number
       H00100  好中球減少症
       H00939  Darsun 症候群
       H01218  P14 欠損症
     4B01  Disorders of neutrophil function
     4B02  Eosinopenia
     4B03  Eosinophilia
     4B04  Disorders with decreased monocyte counts
     4B05  Disorders with increased monocyte counts
     4B06  Acquired lymphopenia
     4B07  Acquired lymphocytosis
     4B0Y  Other specified immune system disorders involving white cell lineages
       H00234  ペルゲル・フエット核異常
       H02051  メイ・ヘグリン異常症
     4B0Z  Immune system disorders involving white cell lineages, unspecified
   Certain disorders involving the immune system
     4B20  Sarcoidosis
       H01309  若年性サルコイドーシス
     4B21  Polyclonal hypergammaglobulinaemia
     4B22  Cryoglobulinaemia
     4B23  Immune reconstitution inflammatory syndrome
     4B24  Graft-versus-host disease
       H00084  移植片対宿主病
     4B2Y  Other specified disorders involving the immune system
       H01479  キャッスルマン病
     4B40  Diseases of thymus
     4B4Y  Other specified diseases of the immune system
     4B4Z  Diseases of the immune system, unspecified
 
 05 Endocrine, nutritional or metabolic diseases
   Endocrine diseases
     Disorders of the thyroid gland or thyroid hormones system
       5A00  Hypothyroidism
         H01186  Abnormal thyroid hormone metabolism
         H00251  甲状腺内分泌不全症
         H00249  甲状腺ホルモン不応症候群
         H00250  先天性甲状腺機能低下症 (甲状腺腫を伴わない)
         H00650  Allan-Herndon-Dudley 症候群
         H01040  Bamforth-Lazarus 症候群
       5A01  Nontoxic goitre
       5A02  Thyrotoxicosis
         H01269  先天性甲状腺機能亢進症
         H01645  甲状腺機能亢進症
         H00082  グレーブス病
       5A03  Thyroiditis
         H01647  亜急性甲状腺炎
         H00081  橋本病
       5A04  Hypersecretion of calcitonin
       5A05  Generalised resistance to thyroid hormone
       5A06  Sick-euthyroid syndrome
       5A0Y  Other specified disorders of the thyroid gland or thyroid hormones system
       5A0Z  Disorders of the thyroid gland or thyroid hormones system, unspecified
     Diabetes mellitus
       5A10  Type 1 diabetes mellitus
         H00408  1型糖尿病
       5A11  Type 2 diabetes mellitus
         H00409  2型糖尿病
       5A12  Malnutrition-related diabetes mellitus
       5A13  Diabetes mellitus, other specified type
         H00410  若年発症成人型糖尿病 (MODY)
         H01228  タイプ A インスリン受容体異常症
         H00766  Wolcott-Rallison 症候群
       5A14  Diabetes mellitus, type unspecified
       Acute complications of diabetes mellitus
     Other disorders of glucose regulation or pancreatic internal secretion
       5A40  Intermediate hyperglycaemia
       5A41  Hypoglycaemia without associated diabetes
         H01909  Hypoinsulinemic hypoglycemia with hemihypertrophy
       5A42  Increased secretion of glucagon
       5A43  Abnormal secretion of gastrin
         H01522  ゾリンジャー-エリソン症候群
       5A44  Insulin-resistance syndromes
         H00419  先天性全身性リポジストロフィー
         H00420  家族性部分型リポジストロフィー
         H00719  妖精症
         H00942  Rabson–Mendenhall 症候群
         H01474  後天性全身性脂肪萎縮症
       5A45  Persistent hyperinsulinemic hypoglycaemia of infancy
         H01267  家族性高インスリン性低血糖症
       5A4Y  Other specified disorders of glucose regulation and pancreatic internal secretion
       5A4Z  Disorders of glucose regulation and pancreatic internal secretion, unspecified
     Disorders of the parathyroids or parathyroid hormone system
       5A50  Hypoparathyroidism
         H01862  副甲状腺機能低下症
         H00244  偽性副甲状腺機能低下症
       5A51  Hyperparathyroidism
         H00246  副甲状腺機能亢進症
         H01669  二次性副甲状腺機能亢進症
         H02026  家族性低カルシウム尿性高カルシウム血症
         H02030  新生児副甲状腺機能亢進症
       5A5Y  Other specified disorders of the parathyroids or parathyroid hormone system
       5A5Z  Disorders of the parathyroids or parathyroid hormone system, unspecified
     Disorders of the pituitary hormone system
       5A60  Hyperfunction of pituitary gland
         H01683  ADH 分泌異常症
         H01483  先端巨大症
         H01618  下垂体性巨人症
         H01864  下垂体性成長ホルモン分泌亢進症
         H01388  高プロラクチン血症
         H01682  抗利尿ホルモン不適合分泌症候群 (SIADH)
         H01294  抗利尿不適合性腎症候群
         H00937  思春期早発症
         H02018  中枢性思春期早発症
         H01701  下垂体性 TSH 分泌亢進症
       5A61  Hypofunction or certain specified disorders of pituitary gland
         H01683  ADH 分泌異常症
         H00254  成長ホルモン分泌不全症
         H00931  Growth hormone insensitivity with immunodeficiency
         H01253  卵胞刺激ホルモン単独欠損症
         H01274  IGF-I resistance
         H01700  下垂体前葉機能低下症
         H01907  酸不安定サブユニット欠損症
         H01973  妊性宦官型症候群
         H02035  成長ホルモン単独欠損症
         H02036  複合下垂体ホルモン欠損症
         H02037  ラロン症候群
         H02038  X連鎖性汎下垂体機能低下症
         H02039  Kowarski 症候群
         H02040  IGF1 欠損症
         H01011  ACTH単独欠損症
         H00255  低ゴナドトロピン性性腺機能低下症
         H01860  下垂体性ゴナドトロピン分泌異常症
         H01699  TSH 単独欠損症
         H02034  中枢性甲状腺機能低下および精巣腫大
         H00253  神経下垂体性尿崩症
         H00854  ウォルフラム症候群
         H00682  Woodhouse-Sakati 症候群
       5A6Z  Disorders of the pituitary hormone system, unspecified
     Disorders of the adrenal glands or adrenal hormone system
       5A70  Cushing syndrome
         H01431  クッシング症候群
         H00260  原発性色素性副腎皮質結節性異形成
         H01820  カーニー複合
         H02049  両側大結節性副腎皮質過形成
       5A71  Adrenogenital disorders
         H01702  グルココルチコイド抵抗症候群
         H00216  先天性副腎過形成症
         H01111  コルチゾンレダクターゼ欠損
       5A72  Hyperaldosteronism
         H00602  糖質コルチコイド反応性アルドステロン症
         H01603  原発性アルドステロン症
         H00259  AME 症候群
       5A73  Hypoaldosteronism
         H00258  アルドステロン合成酵素欠損症
       5A74  Adrenocortical insufficiency
         H01598  アジソン病
         H00177  新生児型副腎白質ジストロフィー
         H00256  家族性糖質コルチコイド欠損症
         H00257  AAA 症候群
       5A75  Adrenomedullary hyperfunction
       5A76  Certain specified disorders of adrenal gland
         H01163  先天性 CBG 欠損症
       5A7Z  Disorders of the adrenal glands or adrenal hormone system, unspecified
     Disorders of the gonadal hormone system
       5A80  Ovarian dysfunction
         H01739  多嚢胞性卵巣症候群
       5A81  Testicular dysfunction or testosterone-related disorders
         H02019  家族性男性思春期早発症
         H02027  男子性腺機能不全症
       5A8Z  Disorders of the gonadal hormone system, unspecified
     Certain disorders of puberty
       5A90  Disorder of puberty due to oestrogen resistance
         H02061  エストロゲン不応症候群
       5A91  Delayed puberty
       5A92  Peripheral precocious puberty
         H00794  アロマターゼ過剰症
         H00937  思春期早発症
       5A9Y  Other disorders of puberty
         H02020  アロマターゼ欠損症
       5A9Z  Disorders of puberty, unspecified
     Polyglandular dysfunction
       5B00  Autoimmune polyendocrinopathy
         H01972  多腺性自己免疫症候群 1型
       5B01  Polyglandular hyperfunction
       5B0Y  Other specified polyglandular dysfunction
       5B0Z  Polyglandular dysfunction, unspecified
     Endocrine disorders, not elsewhere classified
   Nutritional disorders
     Undernutrition
       5B50  Underweight in infants, children or adolescents
       5B51  Wasting in infants, children or adolescents
       5B52  Acute malnutrition in infants, children or adolescents
       5B53  Stunting in infants, children or adolescents
       5B54  Underweight in adults
       5B55  Vitamin A deficiency
         H01266  高カロチン血症およびビタミン A 欠乏症
       5B56  Vitamin C deficiency
         H01580  壊血病
       5B57  Vitamin D deficiency
         H01143  ビタミンD依存性くる病
       5B58  Vitamin E deficiency
         H00981  ビタミン E 欠乏による運動失調症
       5B59  Vitamin K deficiency
       5B5A  Vitamin B1 deficiency
         H01566  脚気
         H01565  ウェルニッケ脳症
       5B5B  Vitamin B2 deficiency
       5B5C  Vitamin B3 deficiency
         H01582  ペラグラ
       5B5D  Vitamin B6 deficiency
       5B5E  Folate deficiency
       5B5F  Vitamin B12 deficiency
       5B5G  Biotin deficiency
       5B5H  Pantothenic acid deficiency
       5B5J  Choline deficiency
       5B5K  Mineral deficiencies
         H01925  一過性乳児亜鉛欠乏症
       Sequelae of malnutrition and certain specified nutritional deficiencies
     Overweight, obesity or specific nutrient excesses
       Overweight or obesity
         5B80  Overweight or localised adiposity
         5B81  Obesity
           H02059  レプチン欠損症
           H02060  レプチン受容体欠損症
           H02105  プロホルモン転換酵素 1/3 欠損症
           H02106  遺伝性肥満
           H02235  病的肥満および精子形成不全
       Certain specified nutrient excesses
         5B90  Vitamin excesses
           H01266  高カロチン血症およびビタミン A 欠乏症
         5B91  Mineral excesses
         5B9Y  Other specified nutrient excesses
         5B9Z  Certain specified nutrient excesses, unspecified
         5C1Y  Other specified overweight, obesity or specific nutrient excesses
         5C1Z  Overweight, obesity or specific nutrient excesses, unspecified
         5C3Y  Other specified nutritional disorders
         5C3Z  Nutritional disorders, unspecified
   Metabolic disorders
     Inborn errors of metabolism
       5C50  Inborn errors of amino acid or other organic acid metabolism
         H00167  フェニルケトン尿症
         H00163  アルカプトン尿症
         H00165  チロシン血症
         H00171  ヒスチジン血症
         H01233  ウロカナーゼ欠損症
         H01583  ヒドロキシキヌレニン尿症
         H00188  高リジン血症
         H01242  サッカロピン尿症
         H01079  3-Phosphoglycerate dehydrogenase (3-PGDH) deficiency
         H01082  ホスホセリンアミノトランスフェラーゼ欠乏症
         H02116  ホスホセリンホスファターゼ欠損症
         H01003  ジメチルグリシンデヒドロゲナーゼ欠損
         H00191  非ケトーシス型高グリシン血症
         H00190  高プロリン血症
         H00187  オルニチントランスカルバミラーゼ欠損症
         H00189  高オルニチン血症
         H01398  尿素サイクル異常症 (原発性高アンモニア血症)
         H01400  二次性高アンモニア血症
         H01028  アルギニノコハク酸尿症
         H00164  カルバモイルリン酸合成酵素I欠損症
         H00186  高アルギニン血症
         H00185  シトルリン血症
         H01032  NAGS欠損症
         H01268  HHH症候群
         H00182  シスタチオニン尿症
         H00183  ホモシスチン尿症
         H00184  高メチオニン血症
         H01237  亜硫酸オキシダーゼ欠損症
         H01285  メチルコバラミン欠乏G
         H00172  メープルシロップ尿症
         H01076  アルファメチルアセト酢酸尿症
         H01279  イソブチリルCoA脱水素酵素欠損症
         H02136  分岐鎖ケト酸脱水素酵素キナーゼ欠損症
         H01349  メタクリル酸尿症
         H00173  イソ吉草酸血症
         H00174  メチルマロン酸尿症
         H00175  プロピオン酸血症
         H00180  ホロカルボキシラーゼ合成酵素欠損症
         H00181  3-メチルクロトニルグリシン尿症
         H00375  SBCAD 欠損症
         H00754  3-メチルグルタコン酸尿症
         H01182  ビオチニダーゼ欠損症
         H02221  メチルマロン酸尿症およびホモシスチン尿症
         H02222  メチルマロン酸血症およびホモシスチン血症 cblX 型
         H00074  カナバン病
         H00178  グルタル酸血症
         H00835  コハク酸セミアルデヒド脱水素酵素欠損症
         H01146  アミノアシラーゼ1欠損症
         H01225  D-2ヒドロキシグルタル酸尿症
         H01280  L-2-ヒドロキシグルタル酸尿症
         H01283  マロニル-CoA脱炭酸酵素欠損症
         H02109  マロン酸およびメチルマロン酸尿合併症
         H01119  プロリダーゼ欠損症
         H01234  トリメチルアミン尿症
         H00923  グルタミン合成の異常
         H01386  アスパラギン合成酵素欠損症
       5C51  Inborn errors of carbohydrate metabolism
         H01065  5炭糖尿症
         H01135  リボース5-リン酸イソメラーゼ欠損症
         H01189  トランスアルドラーゼ欠乏症
         H02013  グリセロールキナーゼ欠損症
         H00117  原発性高シュウ酸尿症
         H00069  糖原病
         H00150  ダノン病
         H01760  肝型糖原病
         H01762  筋型糖原病
         H01939  糖原病 I 型
         H01940  糖原病 II型
         H01941  糖原病 III 型
         H01942  糖原病 IV 型
         H01943  糖原病 V 型
         H01944  糖原病 VI 型
         H01945  糖原病 VII 型
         H01946  糖原病 XI 型
         H01947  ファンコニ・ビッケル症候群
         H01948  糖原病 IX 型
         H01949  糖原病 0b 型
         H01950  糖原病 0a 型
         H01951  糖原病 X 型
         H01952  糖原病 XII 型
         H01953  糖原病 XIII 型
         H01954  糖原病 XIV 型
         H01955  糖原病 XV 型
         H01956  心臓の糖原病
         H00070  ガラクトース血症
         H02008  ガラクトース-1-リン酸ウリジルトランスフェラーゼ欠損症
         H02009  ガラクトキナーゼ欠損症
         H02010  ガラクトースエピメラーゼ欠損症
         H00071  フルクトース血症
         H00114  フルクトース-1,6-ビスホスファターゼ欠損症
       5C52  Inborn errors of lipid metabolism
         H01589  全身性カルニチン欠乏症
         H01981  カルニチンパルミトイルトランスフェラーゼ I 欠損症
         H01982  カルニチンパルミトイルトランスフェラーゼ II 欠損症
         H01983  カルニチン-アシルカルニチントランスロカーゼ欠損症
         H00392  VLCAD 欠損症
         H00488  MCAD 欠損症
         H00489  LCHAD 欠損症
         H00525  ミトコンドリアの脂肪酸酸化異常症
         H00925  MHBD 欠損症
         H01352  ミトコンドリア三頭酵素欠損症
         H01364  HADH欠損症
         H01929  2,4-ジエノイル CoA レダクターゼ欠損症
         H01980  SCAD 欠損症
         H02085  アシル CoA デヒドロゲナーゼ 9 欠損症
         H00179  3-ヒドロキシ-3-メチルグルタリルCoAリアーゼ欠損症
         H01121  SCOT欠損症
         H01123  HMG-CoA合成酵素欠損症
         H00162  シェーグレン・ラルソン症候群
         H00161  スミス・レムリ・オピッツ症候群
         H00206  メバロン酸キナーゼ欠損症
         H00617  Desmosterolosis
         H01281  Lathosterolosis
         H00151  脳腱黄色腫症
         H00624  進行性家族性肝内胆汁うっ滞
         H00628  先天性胆汁酸代謝異常症
         H02099  2-メチルアシルCoAラセマーゼ欠損症
         H00152  シトステロール血症
         H00736  ドルフマン-シャナリン症候群
         H01297  ミオパシーを伴う中性脂質蓄積症
         H00654  バース症候群
       5C53  Inborn errors of energy metabolism
         H01427  ミトコンドリア病
         H01096  ピルビン酸キナーゼ異常症
         H00072  ピルビン酸脱水素酵素複合体欠損症
         H01996  ピルビン酸脱水素酵素ホスファターゼ欠損症
         H01997  ピルビン酸脱水素酵素 E1α 欠損症
         H01998  ピルビン酸脱水素酵素 E1β 欠損症
         H01999  ピルビン酸脱水素酵素 E2 欠損症
         H02000  ジヒドロリポアミド脱水素酵素欠損症
         H02003  ピルビン酸脱水素酵素 E3 結合タンパク欠損症
         H00073  ピルビン酸カルボキシラーゼ欠損症
         H02197  ミトコンドリアピルビン酸輸送体欠損症
         H01022  TCA回路の異常
         H02004  フマラーゼ欠損症
         H02006  α ケトグルタル酸脱水素酵素複合体欠損症
         H02113  小児小脳-網膜変性症
         H00469  ミトコンドリア DNA 枯渇症候群
         H01389  アルパーズ症候群
         H01390  ミトコンドリア神経性胃腸管系脳筋症
         H01384  ミトコンドリア劣性運動失調症候群
         H00999  コエンザイムQ10欠損症
         H00871  脳幹及び脊髄障害と乳酸上昇を伴う白質脳症
         H01367  小児肝不全
         H01354  リー症候群
         H01369  ATP合成酵素欠損症
         H00473  ミトコンドリア複合体 I 欠損症
         H00891  複合型酸化的リン酸化異常
         H00920  Exocrine pancreatic insufficiency, dyserythropoietic anemia, and calvarial hyperostosis
         H01201  イェンセン症候群
         H01368  チトクロムc酸化酵素欠損症
         H01894  多発性ミトコンドリア機能障害症候群
         H02005  ミトコンドリア複合体 II 欠損症
         H02007  GRACILE 症候群
         H02086  ミトコンドリア 複合体 III 欠損症
         H01305  脳のミエリン形成不全
         H01348  ミトコンドリアリン酸輸送体欠損症
         H00834  グアニジノ酢酸メチルトランスフェラーゼ欠損症
         H00849  クレアチン欠乏症候群
         H02181  特発性高 CK 血症
         H02196  X 連鎖性クレアチン欠乏症候群
         H01248  Erythrocyte lactate transporter defect
         H01900  ミトコンドリアおよびペルオキシソームの分裂異常による脳症
       5C54  Inborn errors of glycosylation or other specified protein modification
         H01486  多発先天奇形-筋緊張低下-けいれん症候群
         H01487  CHIME 症候群
         H00118  先天性グリコシル化異常症 I 型
         H00119  先天性グリコシル化異常症 II 型
         H01188  Tn 症候群
         H01193  家族性腫瘍状石灰化症
         H00996  アーミッシュ小児てんかん症候群
         H01127  PIGM 先天性グリコシル化異常症
         H01489  先天性GPI異常症
       5C55  Inborn errors of purine, pyrimidine or nucleotide metabolism
         H00192  キサンチン尿症
         H00194  レッシュ・ナイハン症候群
         H00195  アデニンホスホリボシルトランスフェラーゼ欠損症
         H00197  アデニロコハク酸リアーゼ欠損症
         H00964  チオプリンS−メチルトランスフェラーゼ欠損
         H00966  AICA-ribosiduria
         H02011  家族性若年性高尿酸血症性腎症
         H02237  AMP デアミナーゼ欠損症
         H00193  ジヒドロピリミジン脱水素酵素欠損症
         H00199  ジヒドロピリミジナーゼ欠損症
         H00200  βウレイドプロピオナーゼ欠損症
         H00290  アイカルディ-ゴーシェ症候群
         H00878  Cystic leukoencephalopathy without megalencephaly
       5C56  Lysosomal diseases
         H01425  リソソーム蓄積症 (ライソゾーム病)
         H00423  スフィンゴリピドーシス
         H00124  GM2 ガングリオシドーシス
         H00281  GM1 ガングリオシドーシス
         H00426  ガングリオシドーシス
         H02016  テイ・サックス病
         H02017  サンドホフ病
         H00125  ファブリー病
         H00127  異染性白質ジストロフィー
         H00272  マルチプルスルファターゼ欠損症
         H00126  ゴーシェ病
         H00136  ニーマン・ピック病 C 型
         H00137  ニーマン・ピック病 A/B 型
         H00138  ファーバー脂肪性肉芽腫症
         H00148  リソソーム酸性リパーゼ欠損症
         H00424  スフィンゴミエリン分解異常
         H01239  プロサポシン欠損症
         H00149  神経セロイドリポフスチン症
         H00422  糖タンパク分解反応異常症
         H00143  ムコリピドーシス II 型
         H00144  ムコリピドーシス IV 型
         H02130  ムコリピドーシス III 型
         H00139  α-マンノシドーシス
         H00140  β-マンノシドーシス
         H00141  フコース症
         H00142  シアリドーシス
         H00145  アスパルチルグルコサミン尿症
         H00146  α-N-アセチルガラクトサミニダーゼ欠損症
         H00276  ガラクトシアリドーシス
         H00421  ムコ多糖症
         H00128  ムコ多糖症 I 型
         H00129  ムコ多糖症 II 型
         H00123  ムコ多糖症 IV 型
         H00131  ムコ多糖症 VI 型
         H00130  ムコ多糖症 III 型
         H00132  ムコ多糖症 VII 型
         H00133  ムコ多糖症 IX 型
         H02205  ムコ多糖症プラス症候群
         H00147  シアル酸尿症
         H00273  濃化異骨症
         H00274  パピヨン・ルフェブル症候群
         H00425  リソソーム-システインプロテアーゼ異常疾患
         H02128  リソソーム輸送障害
       5C57  Peroxisomal diseases
         H00177  新生児型副腎白質ジストロフィー
         H00204  乳児レフスム病
         H00205  ペルオキシソーム形成異常症
         H00207  肢根型点状軟骨異形成症
         H01342  ツェルウエーガー症候群
         H02100  ペルオキシソーム脂肪酸アシルCoAレダクターゼ 1 欠損症
         H00075  レフスム病
         H00176  副腎白質ジストロフィー
         H00407  ペルオキシソームβ酸化系酵素欠損症
         H00874  ジストニアと運動神経障害を伴う白質脳症
         H02096  ペルオキシソームアシルCoAオキシダーゼ欠損症
         H02098  D-二頭酵素欠損症
         H02099  2-メチルアシルCoAラセマーゼ欠損症
         H00203  無カタラーゼ血症
       5C58  Inborn errors of porphyrin or heme metabolism
         H02025  ミエロペルオキシダーゼ欠損症
         H00208  高ビリルビン血症
         H02054  クリグラー・ナジャー症候群
         H02055  ジルベール症候群
         H02056  デュビン・ジョンソン症候群
         H00624  進行性家族性肝内胆汁うっ滞
         H02192  良性反復性肝内胆汁うっ滞
         H00950  ARC 症候群
         H01936  高ビリベルジン血症
         H02057  ローター症候群
         H01763  ポルフィリン症
         H00202  肝性ポルフィリン症
         H00201  骨髄性ポルフィリン症
       5C59  Inborn errors of neurotransmitter metabolism
         H01005  ドーパミンベータヒドロキシラーゼ欠損症
         H01161  芳香族アミノ酸脱炭酸酵素欠損症
         H00548  ブルンナー症候群
         H01257  GABA トランスアミナーゼ欠損症
       5C5A  Alpha-1-antitrypsin deficiency
         H01103  α1-アンチトリプシン欠乏症
       5C5Y  Other specified inborn errors of metabolism
         H01567  チアミンピロホスホキナーゼ欠損症
       5C5Z  Inborn errors of metabolism, unspecified
     Disorders of metabolite absorption or transport
       5C60  Disorders of amino acid absorption or transport
         H00692  ロウ症候群
         H00275  シスチン症
         H00901  シスチン尿症
         H00843  ハートナップ病
         H00899  リジン尿性蛋白不耐症
         H00905  イミノグリシン尿症
         H00911  Dicarboxylic aminoaciduria
         H01304  高グリシン尿症
       5C61  Disorders of carbohydrate absorption or transport
         H00115  スクラーゼ・イソマルターゼ欠損症
         H02090  トレハラーゼ欠乏症
         H00836  グルコーストランスポーター1欠損症
         H01126  腎性糖尿
         H00116  乳糖不耐症
         H01261  先天性グルコース・ガラクトース吸収不全症
       5C62  Disorders of lipid absorption or transport
       5C63  Disorders of vitamin or non-protein cofactor absorption or transport
         H01252  先天性葉酸吸収不全
         H01262  ホルムイミノトランスフェラーゼ欠損症
         H01295  脳葉酸輸送不全による神経変性
         H00214  低リン血症性くる病
         H02139  常染色体劣性低リン血症性くる病
         H02141  常染色体優性低リン血症性くる病
         H02142  X 連鎖劣性低リン血症性くる病
         H02143  X 連鎖優性低リン血症性くる病
         H01124  PNPO 欠損症
         H01183  ビタミン B1 反応性巨赤芽球性貧血症
         H01231  ビオチン依存性大脳基底核症
       5C64  Disorders of mineral absorption or transport
         H00210  ウィルソン病
         H00209  メンケス症候群
         H00833  脳の鉄沈着を伴う神経変性疾患
         H02207  Kufor-Rakeb 症候群
         H02208  パントテン酸キナーゼ関連神経変性症
         H02209  HARP 症候群
         H00211  ヘモクロマトーシス
         H00212  腸性肢端皮膚炎
         H00213  低ホスファターゼ症
         H01113  酸性ホスファターゼ欠損症
         H02138  高カルシウム尿症を伴う遺伝性低リン血症性くる病
         H00240  ギテルマン症候群
         H01210  低マグネシウム血症
         H00245  カルシウム感知受容体 (CASR) 異常症
         H01371  特発性乳児高カルシウム血症
         H01938  ジストニアを伴う高マンガン血症
       5C6Y  Other specified disorders of metabolite absorption or transport
       5C6Z  Disorders of metabolite absorption or transport, unspecified
     Disorders of fluid, electrolyte or acid-base balance
     Disorders of lipoprotein metabolism or certain specified lipidaemias
       5C80  Hyperlipoproteinaemia
         H01101  複合性リパーゼ欠損症
         H01635  脂質異常症
         H00155  家族性高コレステロール血症
         H01383  高リポ蛋白血症 IIa 型
         H01918  常染色体劣性遺伝性高コレステロール血症
         H00154  高リポ蛋白血症 I 型
         H00157  高リポ蛋白血症 V 型
         H01637  高トリグリセリド血症
         H01784  原発性高カイロミクロン血症
         H00153  家族性複合型高脂血症
         H00156  高リポ蛋白血症 III 型
         H01199  高アルファリポタンパク質血症
       5C81  Hypolipoproteinaemia
         H00159  タンジール病
         H00930  低アルファリポ蛋白血症
         H00160  無βリポタンパク血症
         H00927  カイロミクロン停滞病
         H01270  家族性低ベータリポタンパク血症
         H00158  レシチンコレステロールアシルトランスフェラーゼ欠損症
       5C8Y  Other specified disorders of lipoprotein metabolism or lipidaemias
       5C8Z  Unspecified disorders of lipoprotein metabolism or lipidaemias
       5C90  Metabolic or transporter liver disease
     Other metabolic disorders
       5D00  Amyloidosis
         H01185  脳アミロイド血管症
         H01217  Primary localized cutaneous amyloidosis
         H00845  家族性アミロイド症
       5D01  Tumour lysis syndrome
       5D0Y  Other specified metabolic disorders
       5D0Z  Unspecified metabolic disorders
       5D2Z  Metabolic disorders, unspecified
   Postprocedural endocrine or metabolic disorders
 
 06 Mental, behavioural or neurodevelopmental disorders
   Neurodevelopmental disorders
     6A00  Disorders of intellectual development
       H00480  X 連鎖精神遅滞
       H00658  X連鎖精神遅滞症候群
       H00768  常染色体劣性遺伝性精神遅滞
       H00773  常染色体優性精神遅滞
       H01306  FRA12A 精神遅滞
       H01911  常染色体劣性精神遅滞症候群
     6A01  Developmental speech or language disorders
       H00902  言語障害
     6A02  Autism spectrum disorder
       H02111  自閉症
       H01882  アスペルガー症候群
     6A03  Developmental learning disorder
     6A04  Developmental motor coordination disorder
     6A05  Attention deficit hyperactivity disorder
       H01895  注意欠陥多動障害 (ADHD)
     6A06  Stereotyped movement disorder
     6A0Y  Other specified neurodevelopmental disorders
     6A0Z  Neurodevelopmental disorders, unspecified
   Schizophrenia or other primary psychotic disorders
     6A20  Schizophrenia
       H01649  統合失調症
     6A21  Schizoaffective disorder
     6A22  Schizotypal disorder
     6A23  Acute and transient psychotic disorder
     6A24  Delusional disorder
     6A25  Symptomatic manifestations of primary psychotic disorders
     6A2Y  Other specified schizophrenia or other primary psychotic disorders
     6A2Z  Schizophrenia or other primary psychotic disorders, unspecified
   Catatonia
   Mood disorders
     Bipolar or related disorders
       6A60  Bipolar type I disorder
         H01653  双極性障害
       6A61  Bipolar type II disorder
         H01653  双極性障害
       6A62  Cyclothymic disorder
       6A6Y  Other specified bipolar or related disorders
       6A6Z  Bipolar or related disorders, unspecified
     Depressive disorders
       6A70  Single episode depressive disorder
         H01646  うつ病
       6A71  Recurrent depressive disorder
         H01646  うつ病
       6A72  Dysthymic disorder
       6A73  Mixed depressive and anxiety disorder
       6A7Y  Other specified depressive disorders
       6A7Z  Depressive disorders, unspecified
       6A80  Symptomatic and course presentations for mood episodes in mood disorders
       6A8Y  Other specified mood disorders
       6A8Z  Mood disorders, unspecified
   Anxiety or fear-related disorders
     6B00  Generalised anxiety disorder
       H01662  全般性不安障害
     6B01  Panic disorder
       H01664  パニック障害
     6B02  Agoraphobia
     6B03  Specific phobia
     6B04  Social anxiety disorder
       H01670  社会不安障害
     6B05  Separation anxiety disorder
     6B06  Selective mutism
     6B0Y  Other specified anxiety or fear-related disorders
     6B0Z  Anxiety or fear-related disorders, unspecified
   Obsessive-compulsive or related disorders
     6B20  Obsessive-compulsive disorder
       H01450  強迫性障害
     6B21  Body dysmorphic disorder
       H01447  身体醜形障害
     6B22  Olfactory reference disorder
     6B23  Hypochondriasis
     6B24  Hoarding disorder
       H01448  溜め込み障害
     6B25  Body-focused repetitive behaviour disorders
       H00864  抜毛癖
       H01449  皮膚引っ掻き症
     6B2Y  Other specified obsessive-compulsive or related disorders
     6B2Z  Obsessive-compulsive or related disorders, unspecified
       H01453  強迫性障害および関連障害群
   Disorders specifically associated with stress
   Dissociative disorders
   Feeding or eating disorders
     6B80  Anorexia Nervosa
     6B81  Bulimia Nervosa
     6B82  Binge eating disorder
     6B83  Avoidant-restrictive food intake disorder
     6B84  Pica
     6B85  Rumination-regurgitation disorder
     6B8Y  Other specified feeding or eating disorders
       H01703  中枢性摂食異常症 (摂食障害)
     6B8Z  Feeding or eating disorders, unspecified
   Elimination disorders
   Disorders of bodily distress or bodily experience
   Disorders due to substance use or addictive behaviours
     Disorders due to substance use
       6C40  Disorders due to use of alcohol
         H01611  アルコール依存症
         H01071  アルコール過敏症
       6C41  Disorders due to use of cannabis
       6C42  Disorders due to use of synthetic cannabinoids
       6C43  Disorders due to use of opioids
       6C44  Disorders due to use of sedatives, hypnotics or anxiolytics
       6C45  Disorders due to use of cocaine
       6C46  Disorders due to use of stimulants including amphetamines, methamphetamine or methcathinone
       6C47  Disorders due to use of synthetic cathinones
       6C48  Disorders due to use of caffeine
       6C49  Disorders due to use of hallucinogens
       6C4A  Disorders due to use of nicotine
       6C4B  Disorders due to use of volatile inhalants
       6C4C  Disorders due to use of MDMA or related drugs, including MDA
       6C4D  Disorders due to use of dissociative drugs including ketamine and phencyclidine [PCP]
       6C4E  Disorders due to use of other specified psychoactive substances, including medications
       6C4F  Disorders due to use of multiple specified psychoactive substances, including medications
       6C4G  Disorders due use of unknown or unspecified psychoactive substances
       6C4H  Disorders due to use of non-psychoactive substances
       6C4Y  Other specified disorders due to substance use
       6C4Z  Disorders due to substance use, unspecified
     Disorders due to addictive behaviours
   Impulse control disorders
   Disruptive behaviour or dissocial disorders
   Personality disorders and related traits
   Paraphilic disorders
   Factitious disorders
   Neurocognitive disorders
   Mental or behavioural disorders associated with pregnancy, childbirth and the puerperium
   Secondary mental or behavioural syndromes associated with disorders or diseases classified elsewhere
 
 07 Sleep-wake disorders
   Insomnia disorders
     7A00  Chronic insomnia
       H01609  不眠症
     7A01  Short-term insomnia
       H01609  不眠症
     7A0Z  Insomnia disorders, unspecified
   Hypersomnolence disorders
     7A20  Narcolepsy
       H01293  ナルコレプシー
     7A21  Idiopathic hypersomnia
     7A22  Kleine-Levin syndrome
     7A23  Hypersomnia due to a medical condition
     7A24  Hypersomnia due to a medication or substance
     7A25  Hypersomnolence associated with a mental disorder
     7A26  Insufficient sleep syndrome
     7A2Y  Other specified hypersomnolence disorders
     7A2Z  Hypersomnolence disorders, unspecified
   Sleep-related breathing disorders
     7A40  Central sleep apnoeas
     7A41  Obstructive sleep apnoea
     7A42  Sleep-related hypoventilation or hypoxemia disorders
       H01727  原発性肺胞低換気症候群
       H01729  期外収縮
       H01715  肥満低換気症候群
       H00916  先天性中枢性低換気症候群
     7A4Y  Other specified sleep-related breathing disorders
     7A4Z  Sleep-related breathing disorders, unspecified
   Circadian rhythm sleep-wake disorders
     7A60  Delayed sleep-wake phase disorder
       H00689  睡眠相後退症候群
     7A61  Advanced sleep-wake phase disorder
       H00688  家族性睡眠相前進症候群
     7A62  Irregular sleep-wake rhythm disorder
     7A63  Non-24 hour sleep-wake rhythm disorder
     7A64  Circadian rhythm sleep-wake disorder, shift work type
     7A65  Circadian rhythm sleep-wake disorder, jet lag type
     7A6Z  Circadian rhythm sleep-wake disorders, unspecified
   Sleep-related movement disorders
     7A80  Restless legs syndrome
       H01597  レストレスレッグス症候群
     7A81  Periodic limb movement disorder
     7A82  Sleep-related leg cramps
     7A83  Sleep-related bruxism
     7A84  Sleep-related rhythmic movement disorder
     7A85  Benign sleep myoclonus of infancy
     7A86  Propriospinal myoclonus at sleep onset
     7A87  Sleep-related movement disorder due to a medical conditoin
     7A88  Sleep-related movement disorder due to a medication or substance
     7A8Y  Other specified sleep-related movement disorders
     7A8Z  Sleep-related movement disorders, unspecified
   Parasomnia disorders
 
 08 Diseases of the nervous system
   Movement disorders
     8A00  Parkinsonism
       H01600  パーキンソン症候群
       H00057  パーキンソン病
       H00077  進行性核上性麻痺
       H00879  ペリー症候群
       H01574  家族性特発性基底核石灰化症
     8A01  Choreiform disorders
       H00860  良性遺伝性舞踏病
       H00059  ハンチントン病
       H01243  Huntington disease-like syndrome
       H00060  歯状核赤核淡蒼球ルイ体萎縮症 (DRPLA)
       H00655  McLeod 症候群
       H00832  中核群神経有棘赤血球症
       H01779  神経フェリチン症
     8A02  Dystonic disorders
       H00831  遺伝性ジストニア
       H01255  若年発症型ジストニー
       H01608  痙性斜頸
       H00989  Mohr-Tranebjaerg 症候群
     8A03  Ataxic disorders
       H01616  脊髄小脳変性症
       H00067  フリードライヒ運動失調症
       H00749  発作性運動失調症
       H00063  脊髄小脳失調症
       H01478  マチャドジョセフ病
       H01891  常染色体劣性遺伝性脊髄小脳失調症
       H00848  眼球運動失行を伴う失調症
       H01036  網膜色素変性症を伴う後索型失調症
       H01038  Cayman型小脳性運動失調症
       H01170  シャルルヴォア・サグエ型痙性失調症
       H01204  小脳失調・精神遅滞および平衡障害症候群 (CAMRQ)
       H01432  有棘赤血球を伴う舞踏病
       H02101  感覚性運動失調
       H02140  Boucher-Neuhauser 症候群
       H02144  Gordon Holmes 症候群
       H02273  精神遅滞を伴う非進行性小脳失調
     8A04  Disorders associated with tremor
       H01577  本態性振戦
     8A05  Tic disorders
       H00862  トゥーレット症候群
     8A06  Myoclonic disorders
     8A07  Certain specified movement disorder
       H01287  先天性鏡像運動症
       H01528  悪性症候群
     8A0Y  Other specified movement disorders
     8A0Z  Movement disorders, unspecified
   Disorders with neurocognitive impairment as a major feature
     8A20  Alzheimer disease
       H00056  アルツハイマー病
     8A21  Progressive focal atrophies
     8A22  Lewy body disease
       H00066  レビー小体型認知症
     8A23  Frontotemporal lobar degeneration
       H00078  前頭側頭葉変性症
     8A2Y  Other specified disorders with neurocognitive impairment as a major feature
       H00290  アイカルディ-ゴーシェ症候群
     8A2Z  Disorders with neurocognitive impairment as a major feature, unspecified
   Multiple sclerosis or other white matter disorders
     8A40  Multiple sclerosis
       H01490  多発性硬化症
     8A41  Isolated demyelinating syndromes of the central nervous system
     8A42  Acute disseminated encephalomyelitis
     8A43  Neuromyelitis optica
       H01491  視神経脊髄炎
     8A44  Leukodystrophies
       H00176  副腎白質ジストロフィー
       H00065  アレキサンダー病
       H00438  那須ハコラ病
       H00679  先天性大脳白質形成不全症
       H00869  VWM 型白質脳症
       H00875  皮質下嚢胞をもつ大頭型白質脳症
       H01230  成人発症型常染色体優性白質ジストロフィー
       H01807  神経軸索スフェロイド形成を伴う遺伝性びまん性白質脳症
       H02200  卵巣機能障害を伴う進行性白質脳症
       H00135  クラッベ病
     8A45  Secondary white matter disorders
       H01724  HTLV-1 関連脊髄症
       H01696  亜急性硬化性全脳炎
       H00370  進行性多巣性白質脳症
     8A46  Central demyelination of corpus callosum
     8A4Y  Other specified multiple sclerosis or other white matter disorders
     8A4Z  Multiple sclerosis or other white matter disorders, unspecified
   Epilepsy or seizures
     8A60  Epilepsy due to structural or metabolic conditions or diseases
       H01826  海馬硬化を伴う内側側頭葉てんかん
     8A61  Genetic or presumed genetic syndromes primarily expressed as epilepsy
       H00577  症候性全般てんかん
       H00808  特発性全般てんかん
       H01247  ピリドキシン依存性てんかん
       H01819  早期ミオクロニー脳症
       H02250  早期発症型ビタミン B6 依存性てんかん
       H00806  良性家族性新生児/乳児けいれん
       H01818  ドラベ症候群
       H01815  遊走性焦点発作を伴う乳児てんかん
       H01775  PCDH19 関連症候群
       H02212  家族性小児ミオクローヌスてんかん
       H02215  小児欠神てんかん
       H01823  ミオクロニー脱力発作を伴うてんかん
       H01822  ミオクロニー欠神てんかん
       H01258  全般てんかん及び発作性ジスキネジア
       H02217  若年性ミオクローヌスてんかん
       H02216  若年性欠神てんかん
       H02213  良性成人型家族性ミオクローヌスてんかん
       H00809  家族性側頭葉てんかん
       H00810  進行性ミオクローヌスてんかん
       H01212  ニューロセルピン封入体を持つ家族性脳症
       H01994  ラフォラ病
       H01995  Unverricht-Lundborg 病
       H00807  常染色体優性夜間前頭葉てんかん
       H00836  グルコーストランスポーター1欠損症
       H02214  多様な焦点を示す家族性焦点性てんかん
     8A62  Epileptic encephalopathies
       H01460  ウエスト症候群
       H01813  レノックス・ガストー症候群
       H01514  ランドウ・クレフナー症候群
       H00606  早期乳児てんかん性脳症
       H01808  片側痙攣・片麻痺・てんかん症候群
       H01812  ラスムッセン脳炎
       H01827  徐波睡眠期持続性棘徐波を示すてんかん性脳症
       H01829  難治頻回部分発作重積型急性脳炎
       H02150  乳児または幼児てんかん性脳症
     8A63  Seizure due to acute causes
       H00783  熱性けいれん
     8A64  Single seizure due to remote causes
     8A65  Single unprovoked seizure
     8A66  Status epilepticus
     8A67  Acute repetitive seizures
     8A68  Types of seizures
     8A6Y  Other specified epilepsy or seizures
     8A6Z  Epilepsy or seizures, unspecified
   Headache disorders
     8A80  Migraine
       H00775  片麻痺性偏頭痛
     8A81  Tension-type headache
     8A82  Trigeminal autonomic cephalalgias
       H01588  群発性頭痛
     8A83  Other primary headache disorder
     8A84  Secondary headache
     8A85  Painful cranial neuropathies or other facial pains
     8A8Y  Other specified headache disorders
     8A8Z  Headache disorders, unspecified
   Cerebrovascular diseases
     Intracranial haemorrhage
     Cerebral ischaemia
       8B10  Transient ischaemic attack
       8B11  Cerebral ischaemic stroke
       8B1Y  Other specified cerebral ischaemia
       8B1Z  Cerebral ischaemia, unspecified
       8B20  Stroke not known if ischaemic or haemorrhagic
       8B21  Cerebrovascular disease with no acute cerebral symptom
       8B22  Certain specified cerebrovascular diseases
         H01184  家族性認知症
         H00534  脳海綿状血管腫
         H01396  もやもや病
         H00536  皮質下梗塞および白質脳症を伴う常染色体優性脳動脈症
         H01757  禿頭と変形性脊椎症を伴う常染色体劣性白質脳症
         H00877  出血を伴う脳小血管病
       8B23  Cerebrovascular abnormalities
       8B24  Hypoxic-ischaemic encephalopathy
       8B25  Late effects of cerebrovascular disease
       8B26  Vascular syndromes of brain in cerebrovascular diseases
       8B2Z  Cerebrovascular diseases, unspecified
   Spinal cord disorders excluding trauma
     8B40  Cauda equina syndrome
     8B41  Myelitis
       H01863  アトピー性脊髄炎
     8B42  Myelopathy
     8B43  Non-compressive vascular myelopathies
     8B44  Degenerative myelopathic disorders
       H00266  遺伝性痙性対麻痺
       H01351  家族性痙性失調症
       H02114  Spastic paraplegia, optic atrophy, and neuropathy
       H02178  MASA 症候群
       H01172  若年発症型痙性対麻痺
     8B4Y  Other specified spinal cord disorders excluding trauma
     8B4Z  Spinal cord disorders excluding trauma, unspecified
   Motor neuron diseases or related disorders
     8B60  Motor neuron disease
       H00058  筋萎縮性側索硬化症 (ALS)
       H00970  若年性原発性側索硬化症
       H00841  小児進行性球麻痺
     8B61  Spinal muscular atrophy
       H00455  脊髄性筋萎縮症
       H00062  球脊髄性筋萎縮症 (SBMA)
       H00524  肩甲腓骨脊髄筋萎縮症
       H00856  遠位遺伝性運動ニューロパチー
       H02238  先天的易骨折性を伴う脊髄性筋萎縮症
     8B62  Post polio progressive muscular atrophy
     8B6Y  Other specified motor neuron diseases or related disorders
     8B6Z  Motor neuron diseases or related disorders, unspecified
   Disorders of nerve root, plexus or peripheral nerves
     Disorders of cranial nerves
     Nerve root or plexus disorders
     Polyneuropathy
       8C00  Idiopathic progressive neuropathy
       8C01  Inflammatory polyneuropathy
         H01436  ギランバレー症候群
         H01689  フィッシャー症候群
         H01842  ビッカースタッフ脳幹脳炎
         H01527  慢性炎症性脱髄性多発神経炎
       8C02  Toxic neuropathy
         H01578  スモン病
       8C03  Other secondary polyneuropathy
         H01459  糖尿病性神経障害
       8C0Y  Other specified polyneuropathy
       8C0Z  Polyneuropathy, unspecified
     Mononeuropathy
       8C10  Mononeuropathies of upper limb
         H00798  家族性手根管症候群
       8C11  Mononeuropathies of lower limb
       8C12  Certain specified mononeuropathies
       8C1Z  Mononeuropathy, unspecified
     Hereditary neuropathy
       8C20  Hereditary motor or sensory neuropathy
         H00264  シャルコー・マリー・トゥース病
         H01131  遺伝性神経痛性筋萎縮症
         H01155  ルシー・レヴィー症候群
         H01296  圧迫麻痺性遺伝性ニューロパチー (HNPP)
       8C21  Hereditary sensory or autonomic neuropathy
         H00265  遺伝性感覚性自律神経性ニューロパチー
         H01987  家族性自律神経失調症
         H01836  先天性無痛無汗症
         H00774  先天性無痛覚
         H00935  寒冷誘発性発汗症候群
       8C2Y  Other specified hereditary neuropathy
         H01259  巨大軸索性ニューロパチー
       8C2Z  Hereditary neuropathy, unspecified
       8C4Y  Other specified disorders of nerve root, plexus or peripheral nerves
       8C4Z  Disorders of nerve root, plexus or peripheral nerves, unspecified
   Diseases of neuromuscular junction or muscle
     Myasthenia gravis or certain specified neuromuscular junction disorders
       8C60  Myasthenia gravis
         H01594  重症筋無力症
       8C61  Congenital myasthenic syndromes
         H00770  先天性筋無力症候群
       8C62  Lambert-Eaton syndrome
         H01596  イートン・ランバート症候群
       8C6Y  Other specified myasthenia gravis and neuromuscular junction disorders
       8C6Z  Unspecified myasthenia gravis or neuromuscular junction disorders
     Primary disorders of muscles
       8C70  Muscular dystrophy
         H00562  ジストロフィン異常症
         H01964  ベッカー型筋ジストロフィー
         H01963  デュシェンヌ型筋ジストロフィー
         H00563  エメリー・ドレフュス型筋ジストロフィー
         H00591  顔面肩甲上腕型筋ジストロフィー
         H00565  サルコグリカン異常症
         H00593  肢帯型筋ジストロフィー
         H00567  肢帯型筋ジストロフィー 1C
         H00592  カルパイン異常症
         H01959  筋ジストロフィー・ジストログリカノパチー C 型
         H01962  先天性筋ジストロフィー 1D 型
         H01974  肢帯型筋ジストロフィー 2B
         H00656  肩甲腓骨型筋ジストロフィー
         H00120  筋ジストロフィー・ジストログリカノパチー A型
         H00590  先天性筋ジストロフィー
         H01284  マリネスコ・シェーグレン症候群
         H01340  ベスレムミオパチー
         H01341  6型コラーゲン関連筋疾患
         H01778  ウルリッヒ病
         H01957  福山型先天性筋ジストロフィー
         H01958  メロシン欠損型先天性筋ジストロフィー
         H01960  筋ジストロフィー・ジストログリカノパチー B 型
         H01961  先天性筋ジストロフィー 1C 型
         H00697  体位性筋収縮を伴うX連鎖ミオパチー
       8C71  Myotonic disorders
         H00568  筋緊張性ジストロフィー
         H01777  シュワルツ・ヤンペル症候群
         H00705  先天性ミオトニー
         H00744  カリウム惹起性ミオトニー
         H01804  アイザックス症候群
         H01780  非ジストロフィー性ミオトニー症候群
         H02179  Rippling muscle disease
       8C72  Congenital myopathies
         H01810  先天性ミオパチー
         H00698  ネマリンミオパチー
         H00702  キャップ病
         H00700  中心核ミオパチー
         H00699  セントラルコア病
         H00703  ミオシンストレージミオパチー
         H01291  スフェロイド小体ミオパチー
         H01310  マルチミニコア病
         H01338  筋硬化症
         H00701  先天性筋線維タイプ不均等症
         H00657  還元体筋障害
         H01781  自己貪食空胞性ミオパチー
         H02084  アメリカ先住民ミオパチー
         H02258  管状凝集体ミオパチー
       8C73  Mitochondrial myopathies
         H01363  NARP症候群
         H00068  レーベル遺伝性視神経症
         H01200  致死性乳児心臓脳筋症
         H01347  ミトコンドリア脳筋症・乳酸アシドーシス・脳卒中様発作症候群
         H01356  赤色ぼろ線維・ミオクローヌスてんかん症候群
         H01365  レーバー遺伝性視神経萎縮症 およびジストニア
         H02201  乳酸アシドーシスを伴うミトコンドリアミオパチー
       8C74  Periodic paralyses or disorders of muscle membrane excitability
         H00743  先天性パラミオトニー
         H00215  遺伝性周期性四肢麻痺
         H00746  低カリウム血性周期性四肢麻痺
         H00745  高カリウム血性周期性四肢麻痺
         H00747  低カリウム性甲状腺中毒性周期性四肢麻痺
         H00748  Andersen-Tawil 症候群
       8C75  Distal myopathies
         H00566  遠位型前脛骨筋ミオパチー
         H00594  遠位型ミオパチー
         H00596  埜中ミオパチー
         H01965  三好型ミオパチー
         H01975  Welander 遠位型ミオパチー
         H01976  脛骨筋ジストロフィー
         H01977  Laing 遠位型ミオパチー
         H02182  遠位型ミオパチー, Tateyama タイプ
       8C76  Myofibrillar myopathy
         H00595  筋原線維性ミオパチー
       8C77  Ocular myopathy
       8C78  Malignant hyperthermia or hyperpyrexia
       8C7Y  Other specified primary disorders of muscles
         H01129  ブロディーミオパチー
       8C7Z  Primary disorders of muscles, unspecified
     Secondary myopathies
   Cerebral palsy
     8D20  Spastic cerebral palsy
       H01097  痙攣性四肢脳性麻痺
     8D21  Dyskinetic cerebral palsy
     8D22  Ataxic cerebral palsy
     8D23  Worster-Drought syndrome
       H01837  先天性核上性球麻痺
     8D2Y  Other specified cerebral palsy
     8D2Z  Cerebral palsy, unspecified
   Nutritional or toxic disorders of the nervous system
   Disorders of cerebrospinal fluid pressure or flow
     8D60  Increased intracranial pressure
     8D61  Intracranial hypotension
     8D62  Cerebrospinal fluid rhinorrhoea
     8D63  Cerebrospinal fluid otorrhoea
     8D64  Hydrocephalus
       H01676  正常圧水頭症
     8D65  Cerebrospinal fluid fistula
     8D66  Syringomyelia or syringobulbia
       H01675  脊髄空洞症
     8D67  Intracranial arachnoid cyst
     8D68  Porencephalic cyst
     8D6Y  Other specified disorders of cerebrospinal fluid pressure or flow
     8D6Z  Disorders of cerebrospinal fluid pressure or flow, unspecified
   Disorders of autonomic nervous system
     8D80  Congenital malformations of the autonomic nervous system
     8D81  Inherited autonomic nervous system disorders
     8D82  Autoimmune disorders involving the autonomic nervous system
     8D83  Autonomic nervous system disorder due to infection
     8D84  Pure autonomic nervous system failure
     8D85  Autonomic nervous system disorder due to substances
     8D86  Autonomic nervous system hyperactivity
     8D87  Autonomic nervous system disorder due to certain specified neurodegenerative disorder
       H01614  多系統萎縮症
       H01177  乳児両側性線条体壊死
     8D88  Autonomic neuropathies
     8D89  Disorders of orthostatic tolerance
       H01031  起立耐性失調
     8D8A  Focal or segmental autonomic disorders
     8D8B  Disorders affecting autonomic synaptic neurotransmission
     8D8C  Autonomic dysreflexia
     8D8Y  Other specified disorders of autonomic nervous system
     8D8Z  Disorders of autonomic nervous system, unspecified
   Human prion diseases
     8E00  Sporadic Creutzfeldt-Jakob Disease
       H00061  プリオン病
     8E01  Acquired prion disease
       H00061  プリオン病
     8E02  Genetic prion diseases
       H00061  プリオン病
     8E03  Variably protease sensitive prionopathy
       H00061  プリオン病
     8E0Y  Other specified human prion diseases
       H00061  プリオン病
     8E0Z  Human prion diseases, unspecified
   Disorders of consciousness
   Other disorders of the nervous system
     8E40  Disorders of the meninges excluding infection
       H01668  腫瘍性髄膜炎
     8E41  Pachymeningitis
     8E42  Superficial siderosis of the nervous system
       H01846  脳表ヘモジデリン沈着症
     8E43  Pain disorders
       H01638  神経障害性疼痛
       H00772  発作性激痛症
       H01391  家族性エピソード性疼痛症候群
     8E44  Post anoxic brain damage
     8E45  Locked-in syndrome
     8E46  Reye syndrome
     8E47  Encephalopathy, not elsewhere classified
       H01841  痙攣重積型 (二相性) 急性脳症
       H02261  PEBAT
       H02262  PEBEL
     8E48  Encephalitis, not elsewhere classified
     8E49  Postviral fatigue syndrome
     8E4A  Paraneoplastic or autoimmune disorders of the nervous system
       H01452  レンサ球菌感染性小児自己免疫神経精神障害
     8E4Y  Other specified disorders of the nervous system
     8E4Z  Other disorders of the nervous system, unspecified
   Postprocedural disorders of the nervous system
 
 09 Diseases of the visual system
   Disorders of the ocular adnexa or orbit
     Disorders of eyelid or peri-ocular area
       9A00  Congenital malposition of eyelids
       9A01  Infectious disorders of eyelid
         H01644  眼瞼炎
       9A02  Inflammatory disorders of eyelid
         H01644  眼瞼炎
       9A03  Acquired malposition of eyelid
       9A04  Acquired disorders of eyelashes
       9A05  Movement disorders of eyelid
       9A06  Certain specified disorders of eyelid
       9A0Y  Other specified disorders of eyelid or peri-ocular area
       9A0Z  Disorders of eyelid or peri-ocular area, unspecified
     Disorders of lacrimal apparatus
     Disorders of orbit
   Disorders of the eyeball anterior segment
     Disorders of conjunctiva
       9A60  Conjunctivitis
         H01366  細菌性結膜炎
         H01367  小児肝不全
       9A61  Certain specified disorders of conjunctiva
       9A6Y  Other specified disorders of conjunctiva
       9A6Z  Disorders of conjunctiva, unspecified
     Disorders of the cornea
       9A70  Hereditary corneal dystrophies
         H00960  フックス角膜内皮変性症
         H00963  先天遺伝性角膜内皮変性症
         H00726  メースマン角膜上皮変性症
         H00951  Reis-Bucklers 角膜変性症
         H00952  Thiel–Behnke 角膜変性症
         H00953  膠様滴状角膜変性症
         H00954  斑状角膜変性症
         H00955  顆粒状角膜変性症
         H00956  格子状角膜変性症
         H00957  斑状角膜変性症
         H00958  先天性角膜実質変性症
         H00959  シュナイダー角膜変性症
         H01221  角膜上皮基底膜変性症
       9A71  Infectious keratitis
       9A72  Traumatic keratitis
       9A73  Exposure keratitis
       9A74  Neurotrophic keratitis
       9A75  Autoimmune keratitis
       9A76  Corneal ulcer
       9A77  Corneal scars or opacities
       9A78  Certain specified disorders of cornea
         H00789  円錐角膜
       9A79  Keratoconjunctivitis sicca
         H01641  ドライアイ
       9A7Y  Other specified disorders of the cornea
         H01273  常染色体優性遺伝性角膜炎
       9A7Z  Disorders of the cornea, unspecified
     Disorders of the anterior chamber
     Disorders of the anterior uvea
     Functional disorders of the pupil
     Disorders of lens
       9B10  Cataract
         H01202  白内障
         H02204  遺伝性高フェリチン血症・白内障症候群
       9B11  Certain specified disorders of lens
       9B1Z  Disorders of lens, unspecified
       9B3Y  Other specified disorders of the eyeball anterior segment
       9B3Z  Disorders of the eyeball anterior segment, unspecified
   Disorders of the eyeball posterior segment
     Disorders of sclera
     Disorders of the choroid
       9B60  Choroidal degeneration
       9B61  Choroidal dystrophy
         H00732  ソースビー眼底変性症
         H01116  全脈絡膜萎縮症
         H01768  中心性輪紋状脈絡膜ジストロフィー
         H01880  常染色体劣性遺伝性小頭症および網脈絡膜症
         H02107  クリスタリン網膜症
       9B62  Chorioretinal scars
       9B63  Choroidal haemorrhage or rupture
       9B64  Choroidal detachment
       9B65  Choroiditis
       9B66  Intermediate choroiditis
       9B6Y  Other specified disorders of the choroid
       9B6Z  Disorders of the choroid, unspecified
     Disorders of the retina
       9B70  Inherited retinal dystrophies
         H00481  錐体杆体ジストロフィおよび錐体ジストロフィー
         H00527  網膜色素変性
         H00814  卵黄状黄斑ジストロフィー
         H00819  シュタルガルト病
         H00825  家族性斑点網膜症
         H00837  レーバー先天性黒内障
         H00971  全色盲
         H00974  青錐体全色覚異常
         H01009  ニューファンドランド錐体杆体ジストロフィー
         H01130  遅発性網膜変性
         H01770  黄斑ジストロフィー
         H01890  模様黄斑ジストロフィー
         H02075  S 錐体増強症候群
         H02077  Snowflake 硝子体網膜変性
         H02078  常染色体優性硝子体網脈絡膜症
         H02108  基底膜ドルーゼン
         H02110  Doyne 蜂巣状網膜ジストロフィー
       9B71  Retinopathy
         H01457  糖尿病性網膜症
       9B72  Inflammatory diseases of the retina
       9B73  Retinal detachments or breaks
         H01766  若年網膜分離症
       9B74  Retinal vascular occlusions
       9B75  Macular Disorders
         H00821  加齢黄斑変性
         H01480  特発性黄斑円孔
         H01010  オカルト黄斑ジストロフィー
         H01651  黄斑浮腫
       9B76  Degenerative high myopia
       9B77  Eales disease
       9B78  Certain specified retinal disorders
         H01000  脳白質萎縮症を伴う網膜脈管障害
         H02251  コートプラス症候群
         H01798  常染色体優性新生血管炎症性硝子体網膜症
         H01180  Sveinsson 網脈絡膜萎縮
       9B7Y  Other specified disorders of the retina
         H00690  Forsius-Eriksson 症候群
         H01088  色素性傍静脈網脈絡膜萎縮
       9B7Z  Disorders of the retina, unspecified
     Disorders of the vitreous body
       9B80  Inherited vitreoretinal disorders
         H00805  硝子体網膜変性
         H02073  Wagner 症候群
       9B81  Posterior Vitreous Detachment
       9B82  Vitreous prolapse
       9B83  Vitreous haemorrhage
       9B84  Vitreous opacities, membranes or strands
       9B8Y  Other specified disorders of the vitreous body
       9B8Z  Disorders of the vitreous body, unspecified
       9C0Y  Other specified disorders of the eyeball posterior segment
       9C0Z  Disorders of the eyeball posterior segment, unspecified
   Disorders of the eyeball affecting both anterior and posterior segments
   Disorders of the visual pathways or centres
     9C40  Disorder of the optic nerve
       H01719  視神経症
       H01717  視神経炎
       H00068  レーベル遺伝性視神経症
       H01020  視神経萎縮症
       H01365  レーバー遺伝性視神経萎縮症 およびジストニア
       H01378  Bosch-Boonstra 視神経萎縮症候群
     9C41  Disorder of optic chiasm
     9C42  Disorder of post chiasmal visual pathways
     9C43  Disorder of visual cortex
     9C44  Disorder of higher visual centres
     9C4Y  Other specified disorders of the visual pathways or centres
     9C4Z  Disorders of the visual pathways or centres, unspecified
   Glaucoma or glaucoma suspect
     9C60  Glaucoma suspect
     9C61  Glaucoma
       H00612  原発開放隅角緑内障
       H01203  先天性緑内障
     9C6Y  Other specified glaucoma or glaucoma suspect
     9C6Z  Glaucoma or glaucoma suspect, unspecified
   Strabismus or ocular motility
     9C80  Non paralytic strabismus
     9C81  Ocular motor nerve palsies
     9C82  Disorders of extraocular muscles
       H01118  進行性外眼筋麻痺
       H01355  カーンズ・セイアー症候群
       H01395  常染色体劣性遺伝性進行性外眼筋麻痺
       H00704  眼球咽頭型筋ジストロフィー
       H00633  デュアン眼球後退症候群
       H00838  先天性外眼筋線維症
       H02151  先天性顔面神経麻痺
     9C83  Disorders of binocular movement
     9C84  Nystagmus
       H00776  先天性眼振
     9C85  Certain specified irregular eye movements
     9C8Y  Other specified strabismus or ocular motility
     9C8Z  Strabismus or ocular motility, unspecified
   Disorders of refraction or accommodation
     9D00  Disorders of refraction
       H02041  近視
     9D01  Disorders of accommodation
     9D0Y  Other specified disorders of refraction or accommodation
     9D0Z  Disorders of refraction or accommodation, unspecified
   Postprocedural disorders of eye or ocular adnexa
   Impairment of visual functions
     9D40  Impairment of visual acuity
     9D41  Impairment of visual field
     9D42  Patterns of visual field impairment
     9D43  Impairment of contrast vision
     9D44  Impairment of colour vision
       H00971  全色盲
       H00976  色覚異常
     9D45  Impairment of light sensitivity
       H00787  夜盲症
     9D46  Impairment of binocular functions
     Subjective visual experiences
       9D50  Visual discomfort
       9D51  Transient visual loss
       9D52  Hemifield losses
       9D53  Entoptic phenomena
       9D54  Visual illusions
       9D55  Nonorganic visual loss
       9D56  Visual release hallucinations
       9D5Y  Other specified subjective visual experiences
       9D5Z  Subjective visual experiences, unspecified
       9D7Y  Other specified impairment of visual functions
         H00973  遅視症
       9D7Z  Impairment of visual functions, unspecified
   Vision impairment
 
 10 Diseases of the ear or mastoid process
   Diseases of external ear
   Diseases of middle ear or mastoid
   Diseases of inner ear
     AB30  Acute vestibular syndrome
     AB31  Episodic vestibular syndrome
       H01495  メニエール病
       H01706  遅発性内リンパ水腫
     AB32  Chronic vestibular syndrome
     AB33  Otosclerosis
     AB34  Disorders of vestibular function
     AB35  Labyrinthine fistula
     AB36  Labyrinthine dysfunction
     AB37  Noise effects on inner ear
     AB3Y  Other specified diseases of inner ear
     AB3Z  Diseases of inner ear, unspecified
   Disorders with hearing impairment
     AB50  Congenital hearing impairment
       H00604  遺伝性難聴 (常染色体優性)
       H00605  遺伝性難聴 (常染色体劣性)
       H01209  遺伝性難聴 (X連鎖)
     AB51  Acquired hearing impairment
       H01704  突発性難聴
       H01705  若年発症型両側性感音難聴
     AB52  Deafness not otherwise specified
     AB53  Ototoxic hearing loss
     AB54  Presbycusis
     AB55  Sudden idiopathic hearing loss
     AB56  Hereditary hearing loss
     AB57  Auditory synaptopathy or neuropathy
     AB5Y  Other specified disorders with hearing impairment
     AB5Z  Disorders with hearing impairment, unspecified
   Disorders of ear, not elsewhere classified
   Postprocedural disorders of ear or mastoid process
 
 11 Diseases of the circulatory system
   Hypertensive diseases
     BA00  Essential hypertension
       H01633  高血圧症
     BA01  Hypertensive heart disease
     BA02  Hypertensive renal disease
     BA03  Hypertensive crisis
     BA04  Secondary hypertension
       H00242  リドル症候群
       H00603  妊娠誘発性高血圧症
   Hypotension
   Ischaemic heart diseases
     Acute ischaemic heart disease
       BA40  Angina pectoris
         H01632  狭心症
       BA41  Acute myocardial infarction
         H01730  心筋梗塞
       BA42  Subsequent myocardial infarction
       BA43  Coronary thrombosis not resulting in myocardial infarction
       BA4Z  Acute ischaemic heart disease, unspecified
     Chronic ischaemic heart disease
   Diseases of coronary artery
     BA80  Coronary atherosclerosis
       H01742  冠動脈疾患
     BA81  Coronary artery aneurysm
     BA82  Coronary artery dissection
     BA83  Coronary artery fistula, acquired
     BA84  Chronic total occlusion of coronary artery
     BA85  Coronary vasospastic disease
     BA86  Coronary microvascular disease
     BA8Y  Other specified diseases of coronary artery
     BA8Z  Diseases of coronary artery, unspecified
   Pulmonary heart disease or diseases of pulmonary circulation
     BB00  Pulmonary thromboembolism
     BB01  Pulmonary hypertension
       H01619  原発性肺高血圧症
       H01621  肺動脈性肺高血圧症
       H01866  肺静脈閉塞症/肺毛細血管腫症
       H01622  慢性血栓塞栓性肺高血圧症
     BB02  Certain specified diseases of pulmonary vessels
     BB03  Acquired pulmonary venous abnormality
     BB0Y  Other specified pulmonary heart disease or diseases of pulmonary circulation
     BB0Z  Pulmonary heart disease or diseases of pulmonary circulation, unspecified
   Pericarditis
   Acute or subacute endocarditis
   Heart valve diseases
     Mitral valve disease
       BB60  Mitral valve stenosis
       BB61  Mitral valve insufficiency
       BB62  Mitral valve prolapse
         H01868  僧帽弁逸脱症
       BB63  Mitral valve stenosis with insufficiency
       BB64  Mitral valvar abscess
       BB65  Mitral valve rupture
       BB6Y  Other specified mitral valve disease
       BB6Z  Mitral valve disease, unspecified
     Aortic valve disease
     Tricuspid valve disease
     Pulmonary valve disease
   Diseases of the myocardium or cardiac chambers
     BC40  Acquired atrial abnormality
     BC41  Acquired ventricular abnormality
     BC42  Myocarditis
       H00295  ウイルス性心筋炎
     BC43  Cardiomyopathy
       H00294  拡張型心筋症
       H00292  肥大型心筋症
       H01219  拘束性心筋症
       H00293  不整脈源性右室心筋症
       H00669  Naxos 病
       H02094  Carvajal 症候群
     BC44  Noncompaction cardiomyopathy
       H01216  左室緻密化障害
     BC45  Cardiomegaly
     BC46  Intracardiac thrombosis
     BC4Y  Other specified diseases of the myocardium or cardiac chambers
     BC4Z  Diseases of the myocardium or cardiac chambers, unspecified
   Cardiac arrhythmia
     BC60  Atrial premature depolarization
     BC61  Junctional premature depolarization
     BC62  Accessory pathway
     BC63  Conduction disorders
       H01263  進行性心臓伝導障害
       H02125  拡張型心筋症を伴う心臓伝導障害
     BC64  Sudden arrhythmic death syndrome
     BC65  Cardiac arrhythmia associated with genetic disorder
       H00720  QT 延長症候群
       H00748  Andersen-Tawil 症候群
       H02091  ジャーベル・ランゲ・ニールセン症候群
       H00728  ブルガダ症候群
       H00725  QT短縮症候群
       H00730  家族性特発性心室細動
       H01019  カテコールアミン誘発性多形性心室頻拍
       H02122  CAID 症候群
     Ventricular rhythm disturbance
       BC70  Ventricular premature depolarization
       BC71  Ventricular tachyarrhythmia
         H02269  家族性心室頻拍
       BC7Y  Other specified ventricular rhythm disturbance
       BC7Z  Ventricular rhythm disturbance, unspecified
     Supraventricular rhythm disturbance
       BC80  Supraventricular bradyarrhythmia
         H00729  洞不全症候群
       BC81  Supraventricular tachyarrhythmia
         H00731  心房細動
         H01154  早期興奮症候群
       BC8Y  Other specified supraventricular rhythm disturbance
       BC8Z  Supraventricular rhythm disturbance, unspecified
       BC90  Rhythm disturbance at level of atrioventricular junction
       BC91  Pacemaker or implantable cardioverter defibrillator battery at end of battery life
       BC9Y  Other specified cardiac arrhythmia
       BC9Z  Cardiac arrhythmia, unspecified
   Heart failure
     BD10  Congestive heart failure
     BD11  Left ventricular failure
     BD12  High output syndromes
     BD13  Right ventricular failure
     BD1Y  Other specified heart failure
       H01631  急性心不全
     BD1Z  Heart failure, unspecified
   Diseases of arteries or arterioles
     BD30  Acute arterial occlusion
     Chronic arterial occlusive disease
       BD40  Atherosclerotic chronic arterial occlusive disease
         H01626  閉塞性動脈硬化症
         H01629  慢性動脈閉塞症
       BD41  Non-atherosclerotic chronic arterial occlusive disease
         H01629  慢性動脈閉塞症
       BD42  Raynaud phenomenon
         H01620  レイノー症候群
         H01629  慢性動脈閉塞症
       BD4Y  Other specified chronic arterial occlusive disease
       BD4Z  Chronic arterial occlusive disease, unspecified
       BD50  Aortic aneurysm or dissection
         H00801  家族性胸部大動脈瘤及び解離
       BD51  Arterial aneurysm or dissection, excluding aorta
       BD52  Certain specified disorders of arteries or arterioles
         H01002  乳児全身性動脈石灰化 (GACI)
       BD53  Secondary disorders of arteries and arterioles
       BD54  Diabetic foot ulcer
       BD55  Asymptomatic stenosis of intracranial or extracranial artery
       BD56  Asymptomatic occlusion of intracranial or extracranial artery
       BD57  Cholesterol atheroembolism to skin
       BD5Y  Other specified diseases of arteries or arterioles
       BD5Z  Diseases of arteries or arterioles, unspecified
   Diseases of veins
     BD70  Superficial thrombophlebitis
     BD71  Deep vein thrombosis
       H01723  深部静脈血栓症
     BD72  Venous thromboembolism
     BD73  Acquired systemic vein abnormality
     BD74  Chronic peripheral venous insufficiency of lower extremities
     BD75  Venous varicosities of sites other than lower extremity
     BD7Y  Other specified diseases of veins
     BD7Z  Diseases of veins, unspecified
   Disorders of lymphatic vessels or lymph nodes
     BD90  Lymphadenitis
     BD91  Lymphangitis
     BD92  Lymphangiectasia
     BD93  Lymphoedema
       H00535  遺伝性リンパ水腫
       H01017  後鼻孔閉鎖症 および リンパ浮腫
       H02167  リンパ水腫・二重睫毛症候群
       H02168  乏毛症・リンパ水腫・毛細血管拡張症症候群
       H02169  Hennekam 症候群
     BD9Y  Other specified disorders of lymphatic vessels or lymph nodes
     BD9Z  Disorders of lymphatic vessels or lymph nodes, unspecified
   Postprocedural disorders of circulatory system
 
 12 Diseases of the respiratory system
   Upper respiratory tract disorders
     CA00  Acute nasopharyngitis
     CA01  Acute sinusitis
     CA02  Acute pharyngitis
     CA03  Acute tonsillitis
     CA04  Acute laryngopharyngitis
     CA05  Acute laryngitis or tracheitis
     CA06  Acute obstructive laryngitis or epiglottitis
     CA07  Acute upper respiratory infections of multiple and unspecified sites
     CA08  Vasomotor or allergic rhinitis
       H01360  アレルギー性鼻炎
     CA09  Chronic rhinitis, nasopharyngitis or pharyngitis
     CA0A  Chronic rhinosinusitis
       H01765  好酸球性副鼻腔炎
     CA0B  Silent sinus syndrome
     CA0C  Cyst or mucocele of nose or nasal sinus
     CA0D  Deviated nasal septum
     CA0E  Hypertrophy of nasal turbinates
     CA0F  Chronic diseases of tonsils or adenoids
     CA0G  Chronic laryngitis or laryngotracheitis
     CA0H  Diseases of vocal cords or larynx, not elsewhere classified
     CA0J  Nasal polyp
     CA0K  Abscess of upper respiratory tract
     CA0L  Dyskinesia trachea
     CA0M  Trachea ossification
     CA0N  Perichondritis of trachea
     CA0P  Trachea stricture
     CA0Q  Tracheomalacia
     CA0R  Rhinoscleroma
     CA0Y  Other specified upper respiratory tract disorders
     CA0Z  Upper respiratory tract disorders, unspecified
   Certain lower respiratory tract diseases
     CA20  Bronchitis
     CA21  Emphysema
     CA22  Chronic obstructive pulmonary disease
       H01714  慢性閉塞性肺疾患 (COPD)
       H01873  閉塞性細気管支炎
     CA23  Asthma
       H00079  喘息
       H01191  鼻茸を伴うアスピリン喘息
     CA24  Bronchiectasis
       H00892  気管支拡張症
     CA25  Cystic fibrosis
       H00218  嚢胞性線維症
     CA26  Chronic bronchiolitis
       H01873  閉塞性細気管支炎
       H01713  びまん性汎細気管支炎
     CA27  Tracheobronchitis
     CA2Y  Other specified lower respiratory tract disease
     CA2Z  Lower respiratory tract disease, unspecified
   Lung infections
     CA40  Pneumonia
       H00351  クラミジア肺炎
       H00304  インフルエンザ菌感染症
       H00301  クレブシェラ感染症
       H00341  マイコプラズマ肺炎
       H01441  緑膿菌感染症
       H00333  レンサ球菌感染症
       H00401  RSウイルス感染症
       H00400  パラインフルエンザ感染症
       H01063  ヒトメタニューモウイルス感染
       H01521  ニューモシスチス肺炎
     CA41  Acute bronchiolitis
       H00401  RSウイルス感染症
     CA42  Acute bronchitis
       H00341  マイコプラズマ肺炎
       H00401  RSウイルス感染症
       H00400  パラインフルエンザ感染症
       H00304  インフルエンザ菌感染症
     CA43  Abscess of lung or mediastinum
     CA44  Pyothorax
     CA45  Respiratory infections, not elsewhere classified
     CA4Y  Other specified lung infections
     CA4Z  Lung infections, unspecified
   Lung diseases due to external agents
     CA60  Pneumoconiosis
     Pneumonitis
       CA70  Hypersensitivity pneumonitis due to organic dust
         H00346  外因性アレルギー性肺胞炎
         H01411  Saccharomonospora viridis 感染
       CA71  Pneumonitis due to solids and liquids
       CA72  Mendelson syndrome
       CA7Y  Other specified pneumonitis
       CA7Z  Pneumonitis, unspecified
       CA80  Airway disease due to specific organic dust
       CA81  Respiratory conditions due to inhalation of chemicals, gases, fumes or vapours
       CA82  Respiratory conditions due to other external agents
       CA8Y  Other specified lung diseases due to external agents
       CA8Z  Lung diseases due to external agents, unspecified
   Respiratory diseases principally affecting the lung interstitium
     CB00  Acute respiratory distress syndrome
     CB01  Pulmonary oedema
     CB02  Pulmonary eosinophilia
     CB03  Idiopathic interstitial pneumonitis
       H01716  特発性間質性肺炎
       H01299  特発性肺線維症
     CB04  Primary interstitial lung diseases specific to infancy or childhood
       H00830  肺静脈の連結不良を伴う肺胞毛細管形成異常
       H00217  肺胞蛋白症
       H01122  先天性肺胞蛋白症
       H02124  間質性肺炎および肝疾患 (ILLD)
       H00913  Brain-lung-thyroid 症候群
     CB05  Interstitial lung diseases associated with systemic diseases
     CB06  Pulmonary alveolar microlithiasis
       H01298  肺胞微石症
     CB07  Lymphangioleiomyomatosis
       H00896  リンパ脈管筋腫症
     CB0Y  Other specified respiratory diseases principally affecting the lung interstitium
     CB0Z  Respiratory diseases principally affecting the lung interstitium, unspecified
   Pleural, diaphragm or mediastinal disorders
     CB20  Pleural plaque
     CB21  Pneumothorax
       H01110  気胸
     CB22  Diseases of mediastinum, not elsewhere classified
     CB23  Disorders of diaphragm
     CB24  Chylous effusion
     CB25  Fibrothorax
     CB26  Haemothorax
     CB27  Pleural effusion
     CB2Y  Other specified pleural, diaphragm or mediastinal disorders
     CB2Z  Pleural, diaphragm or mediastinal disorders, unspecified
     CB40  Certain diseases of the respiratory system
     CB41  Respiratory failure
   Postprocedural disorders of the respiratory system
 
 13 Diseases of the digestive system
   Diseases or disorders of orofacial complex
     DA00  Disorders of lips
     DA01  Disorders of oral mucosa
     DA02  Miscellaneous specified disorders of lips or oral mucosa
       H00724  白色海綿状母斑
     DA03  Diseases of tongue
     DA04  Diseases of salivary glands
     DA05  Cysts of oral or facial-neck region
     DA06  Certain specified diseases of jaws
     DA07  Disorders of tooth development or eruption
       H00680  原発性萌出不全
     DA08  Diseases of hard tissues of teeth
       H01331  う蝕
     DA09  Diseases of pulp or periapical tissues
     DA0A  Certain specified disorders of teeth or supporting structures
     DA0B  Gingival diseases
     DA0C  Periodontal disease
       H02050  前思春期性歯周炎
       H01317  歯周炎
     DA0D  Certain specified disorders of gingival or edentulous alveolar ridge
       H01250  遺伝性歯肉増殖症
     DA0E  Dentofacial anomalies
     DA0F  Sensory disturbances affecting orofacial complex
     DA0Y  Other specified diseases or disorders of orofacial complex
     DA0Z  Diseases or disorders of orofacial complex, unspecified
       H01407  Capnocytophaga ochracea 感染
       H01408  歯周疾患
   Diseases of oesophagus
     DA20  Acquired anatomical alterations of the oesophagus
     DA21  Motility disorders of oesophagus
     DA22  Gastro-oesophageal reflux disease
       H01602  胃食道逆流症
     DA23  Columnar metaplastic epithelium of the oesophagus
       H01901  バレット食道
     DA24  Oesophagitis
       H01361  好酸球性食道炎
     DA25  Oesophageal ulcer
     DA26  Vascular disorders of the oesophagus
     DA2Y  Other specified diseases of oesophagus
     DA2Z  Diseases of oesophagus, unspecified
   Diseases of the stomach or the duodenum
     Diseases of stomach
     Diseases of duodenum
     Ulcer of stomach or duodenum
       DA60  Gastric ulcer
         H01634  消化性潰瘍
       DA61  Peptic ulcer, site unspecified
         H01634  消化性潰瘍
       DA62  Anastomotic ulcer
         H01634  消化性潰瘍
       DA63  Duodenal ulcer
         H01634  消化性潰瘍
       DA7Y  Other specified diseases of the stomach or the duodenum
       DA7Z  Diseases of the stomach or the duodenum, unspecified
   Diseases of small intestine
     DA90  Nonstructural developmental anomalies of small intestine
       H01805  Tricho-hepato-enteric 症候群
       H01276  慢性特発性偽性腸閉塞症
     DA91  Obstruction of small intestine
     DA92  Other acquired anatomical alterations of small intestine
     DA93  Motility disorders of small intestine
     DA94  Noninfectious enteritis or ulcer of small intestine
       H01853  非特異性多発性小腸潰瘍症
     DA95  Coeliac disease
       H02123  セリアック病
     DA96  Intestinal malabsorption or protein-losing enteropathy
       H00352  ホイップル病
       H00988  エンテロキナーゼ欠損症
       H01016  原発性胆汁酸吸収不良
       H01935  家族性高胆汁性貧血
     DA97  Certain vascular disorders of small intestine
     DA98  Polyps of small intestine
     DA9Y  Other specified diseases of small intestine
     DA9Z  Diseases of small intestine, unspecified
   Diseases of appendix
   Diseases of large intestine
     DB30  Obstruction of large intestine
     DB31  Other acquired anatomical alterations of large intestine
     DB32  Motility disorders of large intestine
       H01871  腸管神経節細胞僅少症
     DB33  Certain noninfectious colitis or proctitis
     DB34  Certain vascular disorders of large intestine
     DB35  Polyp of large intestine
     DB36  Certain infections of the large intestine
     DB3Y  Other specified diseases of large intestine
     DB3Z  Diseases of large intestine, unspecified
   Diseases of anal canal
   Diseases of liver
     DB90  Infectious liver disease
     DB91  Acute or subacute hepatic failure
       H01712  劇症肝炎
     DB92  Non-alcoholic fatty liver disease
       H01333  非アルコール性脂肪肝疾患
     DB93  Hepatic fibrosis or cirrhosis
       H02194  North American Indian childhood cirrhosis
       H02225  家族性肝硬変
     DB94  Alcoholic liver disease
     DB95  Drug-induced or toxic liver disease
     DB96  Autoimmune liver disease
       H01685  自己免疫性肝炎
       H01467  原発性胆汁性肝硬変
       H01684  原発性硬化性胆管炎
       H00742  NISCH 症候群
     DB97  Certain specified inflammatory liver diseases
     DB98  Vascular disorders of the liver
       H01687  肝外門脈閉塞症
       H01433  バット・キアリ症候群
       H01686  特発性門脈圧亢進症
     DB99  Certain specified diseases of liver
       H00545  多嚢胞肝
       H01506  肝性脳症
     DB9Z  Diseases of liver, unspecified
   Diseases of gallbladder or biliary tract
     DC10  Acquired anatomical alterations of gallbladder or bile ducts
     DC11  Cholelithiasis
       H01213  胆のう疾患
       H01679  肝内結石症
     DC12  Cholecystitis
       H01213  胆のう疾患
     DC13  Cholangitis
     DC14  Certain specified biliary diseases
     DC1Y  Other specified diseases of gallbladder or biliary tract
     DC1Z  Diseases of gallbladder or biliary tract, unspecified
   Diseases of pancreas
     DC30  Cystic diseases of the pancreas
     DC31  Acute pancreatitis
       H01681  急性膵炎
     DC32  Chronic pancreatitis
       H01680  慢性膵炎
       H00933  遺伝性膵炎
       H00932  石灰沈着性膵炎
     DC33  Autoimmune pancreatitis
     DC34  Obstructive pancreatitis
     DC35  Certain specified diseases of pancreas
     DC3Y  Other specified diseases of pancreas
     DC3Z  Diseases of pancreas, unspecified
   Diseases of peritoneum
   Diverticular disease of intestine
   Ischaemic vascular disorders of intestine
   Hernias
   Inflammatory bowel diseases
     DD70  Crohn disease
       H00286  クローン病
       H01227  炎症性腸疾患 (IBD)
     DD71  Ulcerative colitis
       H01227  炎症性腸疾患 (IBD)
       H01466  潰瘍性大腸炎
     DD72  Indeterminate colitis
       H01227  炎症性腸疾患 (IBD)
     DD7Y  Other specified inflammatory bowel diseases
     DD7Z  Inflammatory bowel diseases, unspecified
   Functional gastrointestinal disorders
     DD90  Functional oesophageal or gastroduodenal disorders
     DD91  Irritable bowel syndrome or certain specified functional bowel disorders
       H01615  過敏大腸症
     DD92  Functional anorectal disorders
     DD93  Functional digestive disorders of infants, toddlers or children
     DD94  Functional gallbladder disorder
     DD95  Functional sphincter of Oddi disorder
     DD9Y  Other specified functional gastrointestinal disorders
     DD9Z  Functional gastrointestinal disorders, unspecified
   Postprocedural disorders of digestive system
 
 14 Diseases of the skin
   Certain skin disorders attributable to infection or infestation
     Certain skin disorders attributable to viral infection
       Viral exanthems
       Certain dermatoses with suspected viral aetiology
         EA10  Pityriasis rosea
           H01660  ジベルばら色粃糠疹
         EA11  Papular purpuric gloves and socks syndrome
         EA12  Infantile papular acrodermatitis
       Dermatoses from distant or systemic viral infection
     Certain skin disorders attributable to bacterial infection
   Inflammatory dermatoses
     Dermatitis and eczema
       EA80  Atopic eczema
         H01358  アトピー性皮膚炎
       EA81  Seborrhoeic dermatitis and related conditions
         H00795  乾癬を伴う脂漏様皮膚炎
         H01652  脂漏性皮膚炎
       EA82  Nummular dermatitis
       EA83  Lichen simplex or lichenification
       EA84  Asteatotic eczema
       EA85  Dermatitis or eczema of hands and feet
       EA86  Dermatitis and eczema of lower legs
       EA87  Dermatitis or eczema of anogenital region
       EA88  Miscellaneous specified eczematous dermatoses
       EA89  Generalised eczematous dermatitis of unspecified type
       EA8Y  Other specified eczematous dermatosis
       EA8Z  Dermatitis or eczema, unspecified
     Papulosquamous dermatoses
       EA90  Psoriasis
         H01656  乾癬
         H01663  膿疱性乾癬
       EA91  Lichen planus
         H01654  扁平苔癬
       EA92  Lichenoid dermatoses
       EA93  Pityriasis lichenoides
       EA94  Pityriasis rubra pilaris
         H01659  毛孔性紅色粃糠疹
       EA95  Small plaque parapsoriasis
     Urticaria, angioedema and other urticarial disorders
       EB00  Spontaneous urticaria
       EB01  Inducible urticaria and angioedema
         H01799  振動性蕁麻疹
       EB02  Cholinergic urticaria and related conditions
       EB03  Syndromes with urticarial reactions or angioedema
       EB04  Angioedema of unspecified type
       EB05  Urticaria of unspecified type
       EB0Y  Other specified urticarial disorders
     Inflammatory erythemas and other reactive inflammatory dermatoses
       EB10  Diffuse inflammatory erythemas
       EB11  Annular erythema
       EB12  Erythema multiforme
         H01695  多型紅斑
       EB13  Stevens-Johnson syndrome or toxic epidermal necrolysis
         H01694  スティーヴンス・ジョンソン症候群および中毒性表皮壊死症
       Neutrophilic dermatoses
     Immunobullous diseases of the skin
       EB40  Pemphigus
         H01648  天疱瘡
       EB41  Pemphigoid
         H01650  類天疱瘡
       EB42  Linear IgA bullous dermatosis
       EB43  Epidermolysis bullosa acquisita
       EB44  Dermatitis herpetiformis
         H01362  疱疹状皮膚炎
       EB4Y  Other specified immunobullous disorder
     Cutaneous lupus erythematosus
       EB50  Subacute cutaneous lupus erythematosus
         H01595  皮膚エリテマトーデス
       EB51  Chronic cutaneous lupus erythematosus
         H01595  皮膚エリテマトーデス
       EB5Z  Cutaneous lupus erythematosus of unspecified type
     Scarring or sclerosing inflammatory dermatoses
       EB60  Lichen sclerosus
         H01690  硬化性萎縮性苔癬
       EB61  Morphoea
         H01493  限局性強皮症
       EB7Y  Other specified inflammatory dermatoses
   Metabolic and nutritional disorders affecting the skin
     EB90  Dermatoses resulting from disturbed metabolic processes
       H01661  黄色腫
     EB9Y  Other specified metabolic and nutritional disorders affecting the skin
   Genetic and developmental disorders affecting the skin
     Genetic syndromes affecting the skin
       EC10  Genetic syndromes with poikiloderma
         H00793  好中球減少を伴う多形皮膚萎縮症
         H01906  腱性拘縮・ミオパチー・肺線維症を伴う遺伝性線維化多形皮膚萎縮症
       EC1Y  Other specified genetic syndromes affecting the skin
       EC20  Genetic disorders of keratinisation
         H01771  先天性魚鱗癬
         H00735  尋常性魚鱗癬
         H00134  X連鎖魚鱗癬
         H00733  道化師様魚鱗癬
         H00734  常染色体劣性遺伝性先天性魚鱗癬
         H00691  水疱型先天性魚鱗癬様紅皮症
         H00693  ジーメンス型水疱性魚鱗癬
         H00707  Curth-Macklin型豪猪皮状魚鱗癬
         H02265  環状表皮剥離性魚鱗癬
         H00710  変異性紅斑角皮症
         H00738  Ichthyosis with confetti
         H00790  KLICK 症候群
         H00737  Peeling skin 症候群
         H00715  ダリエ病
         H00716  難聴を伴う掌蹠角化症
         H00274  パピヨン・ルフェブル症候群
         H00695  メレダ病
         H00714  フォーヴィンケル症候群
         H00722  表皮剥離性掌蹠角化症
         H00723  非表皮剥離性掌蹠角化症
         H02264  長島型掌蹠角化症
         H02266  Bothnian 型掌蹠角化症
         H00717  線状掌蹠角化症
         H02263  非表皮剥離性焦点掌蹠角化症
         H00755  肬贅状肢端角化症
       EC21  Genetic defects of hair or hair growth
         H00667  縮毛症
         H00670  連珠毛
         H01796  櫛でとかせない頭髪症候群
         H00820  Bjornstad 症候群
         H00866  裂毛症
         H00893  Skin fragility-woolly hair 症候群
         H00780  丘疹を伴う無毛症
         H00784  限局性常染色体劣性遺伝性貧毛症
         H00786  先天性単純型乏毛症
         H00858  Marie-Unna 型先天性貧毛症
         H00782  貧毛症および反復性皮膚小水疱
       EC22  Genetic defects of nails or nail growth
         H00683  先天性無爪
         H01307  非症候性先天性爪疾患
       EC23  Genetic disorders of skin pigmentation
         H00884  家族性進行性色素増加症
         H00944  ダウリング‐デゴス病
         H02188  Watson 症候群
         H00166  ヘルマンスキー・プドラック症候群
         H00168  眼皮膚白皮症
         H02021  チェディアック・東症候群
         H00170  まだら症
         H00759  ワールデンブルグ症候群
         H00885  色素失調症
         H01187  Tietz syndrome
         H00880  遺伝性対側性色素異常症
     Genetically-determined epidermolysis bullosa
       EC30  Epidermolysis bullosa simplex
         H00584  単純型表皮水疱症
         H00585  ヘミデスモソーム型表皮水疱症
         H00644  外胚葉異形成・皮膚脆弱症候群
       EC31  Junctional epidermolysis bullosa
         H00586  接合部型表皮水疱症
       EC32  Dystrophic epidermolysis bullosa
         H00587  栄養障害型表皮水疱症
         H00763  新生児一過性表皮水疱症
       EC33  Syndromic epidermolysis bullosa
         H00588  キンドラー症候群
       EC3Z  Epidermolysis bullosa
         H00813  LOC 症候群
         H01737  表皮水疱症
     Genetic disorders affecting dermal collagen, elastin or other matrix proteins
       EC40  Pseudoxanthoma elasticum
         H00560  弾性線維性仮性黄色腫
       EC4Y  Other specified genetic disorders affecting dermal matrix proteins
     Specified developmental anomalies affecting the skin
   Sensory and psychological disorders affecting the skin
   Skin disorders involving specific cutaneous structures
     Disorders of the epidermis and epidermal appendages
       Disorders of epidermal keratinisation
         ED50  Ichthyoses
         ED51  Diffuse epidermal hyperkeratosis and acanthosis
         ED52  Porokeratoses
           H00791  播種性表在性光線性汗孔角化症
           H01933  汗孔角化症
         ED53  Skin peeling
         ED54  Xerosis cutis or asteatosis
         ED55  Palmoplantar keratodermas
           H01673  掌蹠角化症
         ED56  Keratosis pilaris
           H00750  Keratosis follicularis spinulosa decalvans
         ED5Y  Other specified disorders of epidermal keratinisation
       Disorders of skin colour
         ED60  Acquired hypermelanosis
         ED61  Acquired melanotic macules or lentigines
         ED62  Endogenous non-melanin pigmentation
         ED63  Acquired hypomelanotic disorders
           H01372  尋常性白斑
           H01504  フォークト・小柳・原田病
         ED64  Abnormal skin pigmentation
         ED6Y  Other specified disorders of skin pigmentation
       Disorders of hair
         ED70  Alopecia or hair loss
           H01158  全身性脱毛症
         ED71  Hypertrichosis
         ED72  Hirsutism and syndromes with hirsutism
         ED73  Acquired disorders of the hair shaft
         ED7Y  Other specified disorders of hair
       Disorders of the hair follicle
         Acne and related disorders
           ED80  Acne
             H01445  尋常性座瘡
           ED81  Acneform inflammatory disorders
           ED90  Rosacea and related disorders
           ED91  Disorders of the sebaceous gland
           ED92  Disorders involving the apocrine follicular unit
             H00681  化膿性汗腺炎
           ED9Y  Other specified disorders involving the hair follicle
             H00672  偽鬚毛嚢炎
       Disorders of eccrine sweat glands or sweating
         EE00  Hyperhidrosis
         EE01  Hypohidrosis
           H01848  特発性後天性全身性無汗症
         EE02  Miliaria
         EE0Y  Other specified disorders of eccrine sweat glands or sweating
       Disorders of the nail or perionychium
       Disorders of epidermal integrity
     Disorders of the dermis and subcutis
       Disorders of cutaneous connective tissue
         EE40  Atrophy or degeneration of dermal or subcutaneous connective tissue
         EE41  Abnormalities of dermal elastin
           H00557  皮膚弛緩症
         Poikiloderma
         Fibromatoses and keloids
           EE60  Keloid or hypertrophic scars
           EE61  Superficial fibromatoses
           EE6Y  Other specified fibromatous disorders of skin and soft tissue
             H00663  拘束性皮膚障害
             H01173  Stiff skin syndrome
           EE70  Perforating dermatoses
           EE7Y  Other specified disorders of cutaneous connective tissue
       Histiocytic-granulomatous disorders of the skin
       Benign dermal lymphocytic or lymphoplasmacytic infiltrations or proliferations
       Disorders of subcutaneous fat
         EF00  Panniculitis
         EF01  Lipoatrophy or lipodystrophy
           H01475  脂肪萎縮症
         EF02  Certain noninflammatory disorders of subcutaneous fat
         EF0Y  Other specified disorders of subcutaneous fat
     Disorders of cutaneous blood and lymphatic vessels
       Malformations involving cutaneous blood vessels
       Purpura or bruising
       Dermatoses attributable to hyperviscosity or microvascular occlusion
       Dermatoses resulting from vascular insufficiency
       Functional vascular disorders of the skin
         EG00  Vasodilatation of extremities
           H00771  原発性紅痛症
         EG01  Vasoconstriction of extremities
         EG02  Flushing disorders
         EG1Y  Other specified skin disorders involving specific cutaneous structures
         EG1Z  Skin disorders involving specific cutaneous structures, unspecified
   Skin disorders involving certain specific body regions
   Skin disorders associated with pregnancy, the neonatal period and infancy
   Adverse cutaneous reactions to medication
   Skin disorders provoked by external factors
     Dermatoses provoked by physical or environmental factors
       EH90  Pressure ulceration
       EH91  Miscellaneous specified dermatoses provoked by pressure
       EH92  Dermatoses provoked by friction or mechanical stress
       EH93  Dermatoses due to foreign bodies
       Dermatoses provoked or exacerbated by exposure to cold
       Dermatoses provoked by heat or electricity
       Dermatoses provoked by light or UV radiation
         Chronic effects of ultraviolet radiation on the skin
         Acute effects of ultraviolet radiation on normal skin
           EJ40  Sunburn
           EJ41  Burn from exposure to artificial source of ultraviolet radiation
           EJ4Z  Acute effects of ultraviolet radiation on normal skin, unspecified
           EJ6Y  Other specified dermatoses provoked by light or UV radiation
             H02131  紫外線高感受性症候群
       Dermatoses due to ionizing radiation
     Dermatitis due to exogenous factors
       EK00  Allergic contact dermatitis
         H01357  アレルギー性接触性皮膚炎
       EK01  Photo-allergic contact dermatitis
       EK02  Irritant contact dermatitis
       EK0Y  Dermatitis due to other specified exogenous factors
       EK0Z  Contact dermatitis, unspecified
     Allergy to substances in contact with the skin
     Dermatoses provoked by contact with irritant or noxious substance
   Benign proliferations, neoplasms and cysts of the skin
   Disorders of the skin of uncertain or unpredictable malignant potential
   Cutaneous markers of internal disorders
   Postprocedural disorders of the skin
 
 15 Diseases of the musculoskeletal system or connective tissue
   Arthropathies
     Osteoarthritis
     Infection related arthropathies
       FA10  Direct infections of joint
         H01442  敗血症性関節炎
       FA11  Reactive arthropathies
       FA12  Postinfectious arthropathies
       FA13  Infectious spondyloarthritis
       FA1Y  Other specified infection related arthropathies
       FA1Z  Infection related arthropathies, unspecified
     Inflammatory arthropathies
       FA20  Rheumatoid arthritis
         H00630  関節リウマチ
       FA21  Psoriatic arthritis
       FA22  Polymyalgia rheumatica
         H01606  リウマチ性多発筋痛症
       FA23  Adult-onset Still disease
         H01516  成人スチル病
       FA24  Juvenile idiopathic arthritis
         H01672  若年性特発性関節炎
       FA25  Gout
         H01532  痛風
       FA26  Certain specified crystal arthropathies
         H01236  家族性関節軟骨石灰化症
       FA27  Certain specified inflammatory arthropathies
       FA2Z  Inflammatory arthropathies, unspecified
     Certain specified joint disorders or deformities of limbs
   Conditions associated with the spine
     Structural disorders of spine
       FA70  Spinal deformities
       FA71  Torticollis
       FA72  Disorders of vertebra
         H01708  広汎性特発性骨増殖症
       FA7Y  Other specified structural disorders of spine
       FA7Z  Structural disorders of spine, unspecified
     Degenerative condition of spine
       FA80  Intervertebral disc degeneration
       FA81  Spondylolysis
       FA82  Spinal stenosis
         H01711  脊柱管狭窄
       FA83  Ossification of spinal ligaments
         H00431  後縦靭帯骨化症
         H01707  黄色靭帯骨化症
       FA84  Spondylolisthesis
       FA85  Spinal endplate defects
       FA8Y  Other specified degenerative condition of spine
       FA8Z  Degenerative condition of spine, unspecified
     Inflammation of spine
       FA90  Infection of vertebra
       FA91  Infection of intervertebral disc
       FA92  Inflammatory spondyloarthritis
         H01674  強直性脊椎炎
       FA9Y  Other specified inflammation of spine
       FA9Z  Inflammation of spine, unspecified
     Spondylopathies
   Soft tissue disorders
     Disorders of muscles
       FB30  Infectious myositis
       FB31  Calcification or ossification of muscle
         H00441  進行性骨性異形成症
         H00430  進行性骨化性線維異形成症
       FB32  Certain specified disorders of muscle
       FB33  Secondary disorders of muscle
       FB3Z  Disorders of muscles, unspecified
     Disorders of synovium or tendon
     Miscellaneous specified soft tissue disorders
   Osteopathies or chondropathies
     FB80  Certain specified disorders of bone density or structure
       H00501  多骨性線維性骨異形成症
       H01774  全身性皮質性骨増殖症
     FB81  Osteonecrosis
       H01709  特発性ステロイド性骨壊死症
     FB82  Chondropathies
       H00448  家族性離断性骨軟骨炎
       H01526  レッグ・カルベ・ペルテス病
       H01529  大腿骨頭壊死症
       H01758  再発性多発軟骨炎
     FB83  Low bone mass disorders
       H01593  骨粗鬆症
     FB84  Osteomyelitis or osteitis
     FB85  Paget disease of bone
       H00437  骨パジェット病
     FB86  Disorders associated with bone growth
       H00457  原発性肥厚性皮膚骨膜症
       H00472  Torg 症候群
       H00614  ヒアリン線維腫症候群
       H00623  Hajdu-Cheney症候群
       H01865  多中心性手根足根骨溶解症症候群
       H02042  家族性広汎性骨溶解症
       H02089  Winchester 症候群
     FB8Y  Other specified osteopathies or chondropathies
     FB8Z  Osteopathies or chondropathies, unspecified
     FC00  Certain specified acquired deformities of musculoskeletal system or connective tissue, not elsewhere classified
     FC01  Postprocedural disorders of the musculoskeletal system
     FC0Y  Other specified diseases of the musculoskeletal system or connective tissue
     FC0Z  Diseases of the musculoskeletal system or connective tissue, unspecified
 
 16 Diseases of the genitourinary system
   Diseases of the female genital system
     Inflammatory disorders of the female genital tract
     Noninflammatory disorders of female genital tract
       GA10  Endometriosis
         H01639  子宮内膜症
       GA11  Adenomyosis
       GA12  Dyspareunia
       GA13  Acquired abnormalities of vulva or perineum
       GA14  Acquired abnormalities of vagina
       GA15  Acquired abnormalities of cervix uteri
       GA16  Acquired abnormalities of uterus, except cervix
       GA17  Acquired abnormalities of fallopian tube
       GA18  Acquired abnormalities of ovary
       GA19  Acquired abnormalities of broad ligament
       GA1Y  Other specified noninflammatory disorders of female genital tract
       GA1Z  Noninflammatory disorders of female genital tract, unspecified
     Abnormal uterine or vaginal bleeding
       GA20  Menstrual cycle bleeding disorders
       GA21  Nonmenstrual bleeding disorders
       GA22  Excessive menstruation with irregular cycle
       GA23  Anovulatory bleeding
       GA2Y  Other specified abnormal uterine or vaginal bleeding
       GA2Z  Abnormal uterine or vaginal bleeding, unspecified
       GA30  Menopausal or certain specified perimenopausal disorders
         H00627  早期卵巣機能不全
       GA31  Female infertility
         H01897  卵母細胞の成熟異常
       GA32  Complications associated with medically assisted reproduction
         H01039  卵巣過刺激症候群
       GA33  Recurrent pregnancy loss
       GA34  Female pelvic pain associated with genital organs or menstrual cycle
     Dermatoses of female genitalia
   Diseases of the male genital system
     Dermatoses of male genitalia
     Diseases of prostate
       GA90  Hyperplasia of prostate
       GA91  Inflammatory and other diseases of prostate
       GB00  Hydrocele or spermatocele
       GB01  Torsion of testis, epididymis or appendices
       GB02  Orchitis or epididymitis
       GB03  Atrophy of testis
       GB04  Male infertility
         H00890  無精子症
         H01208  頭部円形精子症
         H01282  精子形成異常
       GB05  Redundant prepuce, phimosis or paraphimosis
       GB06  Certain specified disorders of penis
       GB07  Inflammatory disorders of male genital organs, not elsewhere classified
       GB08  Vascular disorders of male genital organs
       GB0Y  Other specified diseases of the male genital system
       GB0Z  Diseases of the male genital system, unspecified
   Disorders of breast
   Diseases of the urinary system
     Glomerular diseases
       GB40  Nephritic syndrome
         H01688  急速進行性糸球体腎炎
       GB41  Nephrotic syndrome
         H00576  ピアソン症候群
         H01657  ネフローゼ症候群
         H01722  ギャロウェイ・モワト症候群
       GB42  Persistent proteinuria or albuminuria
       GB4Y  Other specified glomerular diseases
         H00582  良性家族性血尿
       GB4Z  Glomerular diseases, unspecified
     Renal tubulo-interstitial diseases
       GB50  Acute tubulo-interstitial nephritis
       GB51  Acute pyelonephritis
       GB52  Acute tubular necrosis
       GB53  Acute renal papillary necrosis
       GB54  Tubulo-interstitial nephritis, not specified as acute or chronic
       GB55  Chronic tubulo-interstitial nephritis
       GB56  Obstructive or reflux nephropathy
         H01037  膀胱尿管逆流
       GB57  Nephrocalcinosis
       GB58  Pyonephrosis
       GB59  Renal or perinephric abscess
       GB5Y  Other specified renal tubulo-interstitial diseases
       GB5Z  Renal tubulo-interstitial diseases, unspecified
     Kidney failure
       GB60  Acute kidney failure
       GB61  Chronic kidney disease
         H01456  糖尿病性腎症
       GB6Z  Kidney failure, unspecified
     Urolithiasis
       GB70  Calculus of upper urinary tract
         H02145  シュウ酸カルシウム腎結石症
       GB71  Calculus of lower urinary tract
       GB7Z  Urolithiasis, unspecified
     Cystic or dysplastic kidney disease
       GB80  Nonfamilial nongenetic cystic kidney disease
       GB81  Autosomal dominant polycystic kidney disease
         H00542  多発性嚢胞腎
       GB82  Autosomal dominant tubulointerstitial disease
         H00541  常染色体優性遺伝性尿細管間質性腎疾患
         H02012  髄質性嚢胞腎
       GB83  Nephronophthisis
         H00537  ネフロン癆
         H00538  Senior-Loken 症候群
       GB8Y  Other specified cystic or dysplastic kidney disease
         H00542  多発性嚢胞腎
       GB8Z  Cystic or dysplastic kidney disease, unspecified
       GB90  Certain specified disorders of kidney or ureter
         H01198  腎ファンコニー症候群
         H00239  バーター症候群
         H00241  尿細管性アシドーシス III 型
         H00243  尿細管性アシドーシス IV 型
         H00428  尿細管性アシドーシス I 型 (遠位型)
         H00429  尿細管性アシドーシス II 型 (近位型)
         H00252  先天性腎性尿崩症
         H00694  デント病
         H00948  腎性低尿酸血症
         H02147  腎不全を伴う X 連鎖性劣性腎石灰化症
         H02148  高カルシウム尿症と腎石灰化症を伴う低分子蛋白尿
         H02149  X 連鎖性高カルシウム尿腎石灰化症
     Certain specified diseases of urinary system
       GC00  Cystitis
         H01551  間質性膀胱炎
       GC01  Other disorders of bladder
       GC02  Urethritis and urethral syndrome
         H00388  非クラミジア性非淋菌性尿道炎
       GC03  Urethral stricture
       GC04  Fistula of the genitourinary tract
       GC05  Prolapsed urethral mucosa
       GC06  Urethral diverticulum
       GC07  Urethral caruncle
       GC08  Urinary tract infection, site not specified
         H00279  尿路病原性大腸菌感染症
       GC0Y  Other diseases of urinary system
       GC0Z  Diseases of urinary system, unspecified
       GC2Z  Diseases of the urinary system, unspecified
   Other conditions of the genitourinary system
   Postprocedural disorders of genitourinary system
 
 17 Conditions related to sexual health
 
 18 Pregnancy, childbirth or the puerperium
   Abortive outcome of pregnancy
     JA00  Abortion
     JA01  Ectopic pregnancy
     JA02  Molar pregnancy
       H00289  反復性胞状奇胎
     JA03  Missed abortion
     JA04  Blighted ovum or nonhydatidiform mole
     JA05  Complications following abortion, ectopic or molar pregnancy
     JA0Z  Abortive outcome of pregnancy, unspecified
   Oedema, proteinuria, or hypertensive disorders in pregnancy, childbirth, or the puerperium
   Obstetric haemorrhage
   Certain specified maternal disorders predominantly related to pregnancy
     JA60  Excessive vomiting in pregnancy
     JA61  Venous complications in pregnancy
     JA62  Infections of genitourinary tract in pregnancy
     JA63  Diabetes mellitus in pregnancy
     JA64  Malnutrition in pregnancy
     JA65  Maternal care for other conditions predominantly related to pregnancy
       H02193  妊娠性肝内胆汁うっ滞
     JA66  Clinical findings on antenatal screening of mother
     JA67  Complications of anaesthesia during pregnancy
     JA6Z  Maternal disorders predominantly related to pregnancy, unspecified
   Maternal care related to the foetus, amniotic cavity or possible delivery problems
   Complications of labour or delivery
   Delivery
   Complications predominantly related to the puerperium
     JB40  Infections in the puerperium
     JB41  Venous complications in the puerperium
     JB42  Obstetric embolism
     JB43  Complications of anaesthesia during the puerperium
     JB44  Certain specified complications of the puerperium
     JB45  Infections of breast associated with childbirth
     JB46  Certain specified disorders of breast or lactation associated with childbirth
       H01607  乳汁漏出症
     JB4Z  Complications predominantly related to the puerperium, unspecified
   Certain obstetric conditions, not elsewhere classified
 
 19 Certain conditions originating in the perinatal period
   Foetus or newborn affected by maternal factors or by complications of pregnancy, labour or delivery
   Disorders of newborn related to length of gestation or foetal growth
   Birth injury
   Infections of the foetus or newborn
   Haemorrhagic or haematological disorders of foetus or newborn
     KA80  Foetal blood loss
     KA81  Umbilical haemorrhage of newborn
     KA82  Intracranial nontraumatic haemorrhage of foetus or newborn
     KA83  Certain specified neonatal haemorrhages
     KA84  Haemolytic disease of foetus or newborn
     KA85  Hydrops fetalis due to haemolytic disease
     KA86  Neonatal kernicterus
     KA87  Neonatal hyperbilirubinemia
       H02152  一過性家族性新生児高ビリルビン血症
     KA88  Disseminated intravascular coagulation of foetus or newborn
     KA89  Transient neonatal thrombocytopaenia
     KA8A  Polycythaemia neonatorum
     KA8B  Anaemia of prematurity
     KA8C  Congenital hypoplastic anaemia
     KA8D  Transient neonatal neutropenia
     KA8E  Alloimmune neonatal neutropenia
     KA8F  Neonatal vitamin K deficiency
     KA8Y  Other specified haemorrhagic or haematological disorders of foetus or newborn
     KA8Z  Haemorrhagic or haematological disorders of foetus or newborn, unspecified
   Neurological disorders specific to the perinatal or neonatal period
     KB00  Neonatal cerebral ischaemia
     KB01  Periventricular cysts of newborn
     KB02  Neonatal cerebral leukomalacia
     KB03  Neonatal encephalopathy
       H01211  重症新生児脳症
     KB04  Hypoxic ischaemic encephalopathy of newborn
     KB05  Neonatal hydrocephalus
     KB06  Neonatal seizures
     KB07  Compression of brain in neonate
     KB08  Disorders of muscle tone of newborn
     KB0Y  Other specified neurological disorders specific to the perinatal or neonatal period
     KB0Z  Neurological disorders specific to the perinatal or neonatal period, unspecified
   Respiratory disorders specific to the perinatal or neonatal period
   Cardiovascular disorders present in the perinatal or neonatal period
   Transitory endocrine or metabolic disorders specific to foetus or newborn
     KB60  Transitory disorders of carbohydrate metabolism specific to foetus or newborn
       H00513  新生児一過性糖尿病
       H00512  新生児永続型糖尿病
       H01377  Mitchell-Riley 症候群
     KB61  Transitory neonatal disorders of calcium or magnesium metabolism
     KB62  Transitory neonatal disorders of thyroid function
     KB63  Certain specified transitory neonatal electrolyte or metabolic disturbances
     KB64  Transitory neonatal hypoparathyroidism
     KB6Z  Transitory endocrine or metabolic disorders specific to foetus or newborn, unspecified
   Digestive system disorders of foetus or newborn
     KB80  Gastro-oesophageal reflux disease in newborn
     KB81  Oesophagitis in newborn
     KB82  Prenatal gastric perforation
     KB83  Postnatal gastric perforation
     KB84  Postnatal isolated ileal perforation
     KB85  Prenatal intrauterine intestinal perforation
     KB86  Postnatal intestinal perforation
     KB87  Intestinal obstruction of newborn
     KB88  Necrotising enterocolitis of newborn
     KB89  Neonatal malabsorption syndromes
       H01469  短腸症候群
       H01477  先天性短腸症候群
     KB8A  Neonatal haematemesis or melaena due to swallowed maternal blood
     KB8B  Neonatal peritonitis
     KB8C  Noninfectious neonatal diarrhoea
       H01174  先天性下痢症
     KB8Y  Other specified digestive system disorders of foetus or newborn
     KB8Z  Digestive system disorders of foetus or newborn, unspecified
   Genitourinary system disorders specific to the perinatal or neonatal period
   Disorders involving the integument of foetus or newborn
   Disturbances of temperature regulation of newborn
   Certain disorders originating in the perinatal period
 
 20 Developmental anomalies
   Structural developmental anomalies primarily affecting one body system
     Structural developmental anomalies of the nervous system
       LA00  Anencephaly or similar anomalies
         H02120  無脳症
       LA01  Cephalocele
       LA02  Spina bifida
         H00262  二分脊椎症
       LA03  Arnold-Chiari malformation type II
         H01561  キアリ奇形
       LA04  Congenital hydrocephalus
         H01677  先天性水頭症
       LA05  Cerebral structural developmental anomalies
         H00269  小頭症
         H01833  片側巨脳症
         H00267  全前脳胞症
         H00263  先端脳梁症候群
         H01835  神経細胞移動異常症
         H00271  多小脳回
         H01251  限局性皮質異形成 II 型
         H01881  他の脳奇形を伴う複合皮質異形成
         H00270  脳室周囲結節性異所性灰白質
         H00839  孔脳症
         H01160  裂脳症
         H01870  小水無脳症
       LA06  Cerebellar structural developmental anomalies
         H01678  ダンディ・ウォーカー症候群
       LA07  Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
         H01675  脊髄空洞症
         H01561  キアリ奇形
         H01893  側方髄膜瘤症候群
       LA0Y  Other specified structural developmental anomalies of the nervous system
       LA0Z  Structural developmental anomalies of the nervous system, unspecified
     Structural developmental anomalies of the eye, eyelid or lacrimal apparatus
       LA10  Structural developmental anomalies of ocular globes
         H01027  小眼球症
         H02172  真性小眼球
       LA11  Structural developmental anomalies of the anterior segment of eye
         H01114  眼組織欠損症
         H01029  先天性遺伝性扁平角膜
         H02104  巨大角膜
         H00620  Axenfeld–Rieger 症候群
         H01159  遺伝性前眼部形成異常
         H00635  無虹彩症
         H00961  後部多形性角膜変性症
         H01075  ピータース異常
       LA12  Structural developmental anomalies of lens or zonula
         H00676  先天性原発性無水晶体症
         H00662  水晶体転位
       LA13  Structural developmental anomalies of the posterior segment of eye
         H02112  硝子体血管系遺残
         H00589  滲出性硝子体網膜症
         H02203  視神経形成不全
         H02270  空洞視神経乳頭奇形
         H01256  中心窩低形成
         H02231  網膜や黄斑の変性を伴う視神経乳頭異常
       LA14  Structural developmental anomalies of eyelid, lacrimal apparatus or orbit
         H00677  涙腺および唾液腺の形成不全
       LA1Y  Other specified structural developmental anomalies of the eye, eyelid or lacrimal apparatus
       LA1Z  Structural developmental anomalies of the eye, eyelid or lacrimal apparatus, unspecified
     Structural developmental anomalies of the ear
       LA20  Structural anomaly of eustachian apparatus
       LA21  Minor anomalies of pinnae
       LA22  Structural developmental anomalies of ear causing hearing impairment
         H02115  先天性外耳道閉鎖症
       LA23  Otocephaly
         H02118  Otocephaly
       LA24  Accessory auricle
       LA2Y  Other specified structural developmental anomalies of the ear
       LA2Z  Structural developmental anomalies of the ear, unspecified
     Structural developmental anomalies of the face, mouth or teeth
       LA30  Structural developmental anomalies of teeth and periodontal tissues
         H00625  歯数不足症
         H00652  SMMCI 症候群
         H00615  エナメル質形成不全症
         H00618  長胴歯を伴うエナメル質形成不全・未成熟
         H01015  Jalili 症候群
         H00432  象牙質形成不全症
       LA31  Structural developmental anomalies of mouth or tongue
       Clefts of lip, alveolus or palate
         LA40  Cleft lip
           H00516  口唇口蓋裂
         LA41  Cleft lip and alveolus
           H00516  口唇口蓋裂
         LA42  Cleft palate
           H00516  口唇口蓋裂
           H00909  舌小体短縮症を伴う口蓋裂
         LA4Y  Other specified clefts of lip, alveolus or palate
         LA4Z  Clefts of lip, alveolus or palate, unspecified
         LA50  Congenital velopharyngeal incompetence
         LA51  Facial clefts
           H02202  斜顔面裂
         LA52  Facial asymmetry
         LA53  Macrocheilia
         LA54  Microcheilia
         LA55  Compression facies
         LA56  Pierre Robin syndrome
         LA5Y  Other specified structural developmental anomalies of the face, mouth or teeth
         LA5Z  Structural developmental anomalies of the face, mouth or teeth, unspecified
     Structural developmental anomalies of the neck
     Structural developmental anomalies of the respiratory system
       LA70  Structural developmental anomalies of the nose or cavum
         H01017  後鼻孔閉鎖症 および リンパ浮腫
       LA71  Structural developmental anomalies of larynx
       LA72  Laryngotracheooesophageal cleft
       LA73  Structural developmental anomalies of trachea
       LA74  Structural developmental anomalies of bronchi
       LA75  Structural developmental anomalies of lungs
         H00564  原発性繊毛ジスキネジア
       LA76  Structural developmental anomalies of pleura
       LA77  Congenital cyst of mediastinum
       LA7Y  Other specified structural developmental anomalies of the respiratory system
       LA7Z  Structural developmental anomalies of the respiratory system, unspecified
     Structural developmental anomalies of the circulatory system
       Structural developmental anomaly of heart and great vessels
         LA80  Anomalous position-orientation of heart
         LA81  Abnormal ventricular relationships
         LA82  Total mirror imagery
         LA83  Right isomerism
         LA84  Left isomerism
           H01764  多脾症候群
         LA85  Congenital anomaly of an atrioventricular or ventriculo-arterial connection
           H01786  修正大血管転位症
           H00550  完全大血管転位症
           H00918  両大血管右室起始症
           H01736  総動脈幹遺残症
         LA86  Congenital anomaly of the mediastinal vein
         LA87  Congenital anomaly of an atrioventricular valve or atrioventricular septum
           H02230  X連鎖心臓弁膜症
           H01783  エプスタイン病
           H00547  房室中隔欠損
         LA88  Congenital anomaly of a ventricle or the ventricular septum
           H00549  ファロー四徴症
           H01803  心室中隔欠損を伴う肺動脈閉鎖症
           H01926  心室中隔欠損症
         LA89  Functionally univentricular heart
           H01787  単心室症
           H01785  三尖弁閉鎖症
           H01272  左心低形成症候群
         LA8A  Congenital anomaly of a ventriculo-arterial valve or adjacent regions
           H01802  心室中隔欠損を伴わない肺動脈閉鎖症
           H00554  二尖大動脈弁
           H00553  大動脈弁上狭窄
         LA8B  Congenital anomaly of great arteries including arterial duct
           H01630  動脈管開存症
         LA8C  Congenital anomaly of coronary arteries
         LA8D  Structural developmental anomalies of the pericardium
         LA8E  Congenital anomaly of atrial septum
           H00546  心房中隔欠損
         LA8F  Congenital anomaly of right atrium
         LA8G  Congenital anomaly of left atrium
         LA8Y  Other specified structural developmental anomaly of heart and great vessels
           H00632  内臓錯位
           H02199  先天性心疾患(複合型)
         LA8Z  Structural developmental anomaly of heart and great vessels, unspecified
         LA90  Structural developmental anomalies of the peripheral vascular system
           H00533  オスラー病
           H00531  静脈奇形
           H01849  末梢性動静脈奇形
           H02043  毛細血管奇形および動静脈奇形 (CM-AVM)
         LA9Y  Other specified structural developmental anomalies of the circulatory system
         LA9Z  Structural developmental anomalies of the circulatory system, unspecified
     Structural developmental anomalies of the diaphragm, abdominal wall or umbilical cord
       LB00  Structural developmental anomalies of diaphragm
         H01241  先天性横隔膜ヘルニア
       LB01  Omphalocele
       LB02  Gastroschisis
       LB03  Structural developmental anomalies of umbilical cord
       LB0Y  Other specified structural developmental anomalies of the diaphragm, abdominal wall or umbilical cord
       LB0Z  Structural developmental anomalies of the diaphragm, abdominal wall or umbilical cord, unspecified
     Structural developmental anomalies of the digestive tract
       LB10  Structural developmental anomalies of salivary glands or ducts
       LB11  Congenital diverticulum of pharynx
       LB12  Structural developmental anomalies of oesophagus
       LB13  Structural developmental anomalies of stomach
       LB14  Structural developmental anomalies of duodenum
       LB15  Structural developmental anomalies of small intestine
       LB16  Structural developmental anomalies of large intestine
         H00910  ヒルシュスプルング病
         H01871  腸管神経節細胞僅少症
       LB17  Structural developmental anomalies of anal canal
         H01858  総排泄腔遺残
         H01856  総排泄腔外反症
       LB18  Congenital anomalies of intestinal fixation
       LB1Y  Other specified structural developmental anomalies of the digestive tract
       LB1Z  Structural developmental anomalies of the digestive tract, unspecified
     Structural developmental anomalies of the liver, biliary tract, pancreas or spleen
       LB20  Structural developmental anomalies of gallbladder, bile ducts or liver
         H01855  胆道閉鎖症
         H00551  アラジール症候群
       LB21  Structural developmental anomalies of pancreas
         H00861  膵臓非形成
       LB22  Structural developmental anomalies of spleen
         H01435  先天性無脾症
       LB2Y  Other specified structural developmental anomalies of the liver, biliary tract, pancreas or spleen
       LB2Z  Structural developmental anomalies of the liver, biliary tract, pancreas or spleen, unspecified
     Structural developmental anomalies of the urinary system
       LB30  Structural developmental anomalies of kidneys
         H01867  先天性腎尿路奇形
         H00822  腎欠損
         H01728  ポッター症候群
         H00575  腎尿細管形成不全
       LB31  Structural developmental anomalies of urinary tract
         H01867  先天性腎尿路奇形
       LB3Y  Other specified structural developmental anomalies of the urinary system
       LB3Z  Structural developmental anomalies of the urinary system, unspecified
     Structural developmental anomalies of the female genital system
       LB40  Structural developmental anomalies of vulva
       LB41  Structural developmental anomalies of clitoris
       LB42  Structural developmental anomalies of vagina
       LB43  Structural developmental anomalies of cervix uteri
       LB44  Structural developmental anomalies of uterus, except cervix
         H00600  ミュラー管無発生
       LB45  Structural developmental anomalies of ovaries, fallopian tubes or broad ligaments
         H00599  46,XX 性腺形成不全症
       LB4Y  Other specified structural developmental anomalies of the female genital system
       LB4Z  Structural developmental anomalies of the female genital system, unspecified
     Structural developmental anomalies of the male genital system
       LB50  Micropenis or penis agenesis
       LB51  Anorchia or microorchidia
       LB52  Cryptorchidism
         H02176  停留精巣
       LB53  Hypospadias
         H02175  尿道下裂
       LB54  Congenital chordee
       LB55  Epispadias
       LB56  Bifid scrotum
       LB57  Agenesis of vas deferens
         H01033  先天性両側精管欠損症
       LB58  Polyorchidism
       LB59  Hypoplasia of testis or scrotum
       LB5Y  Other specified structural developmental anomalies of the male genital system
       LB5Z  Structural developmental anomalies of the male genital system, unspecified
     Structural developmental anomalies of the breast
     Structural developmental anomalies of the skeleton
       LB70  Structural developmental anomalies of cranium
         H02160  頭蓋縫合早期癒合症
         H01207  三角頭蓋症
         H00475  拡張型頭頂孔/頭蓋裂
         H01105  頭蓋-レンズ-縫合異形成
       LB71  Structural developmental anomalies of facial bones
       LB72  Structural developmental anomalies of shoulder girdle
       LB73  Structural developmental anomalies of spine or bony thorax
         H01851  肋骨異常を伴う先天性側弯症
         H00852  Klippel-Feil 症候群
       LB74  Structural developmental anomalies of pelvic girdle
         H01817  Beukes 型股関節形成不全
       LB75  Brachydactyly
         H00482  短指 (趾) 症
       LB76  Triphalangeal thumb
       LB77  Hyperphalangy
       LB78  Polydactyly
         H01226  多合指症
         H01852  軸後性多指症
       LB79  Syndactyly
         H01095  合指症
         H00459  合多指 (趾) 症
         H01854  第 4-5 中手骨癒合症
       Congenital deformities of fingers or toes
         LB80  Congenital deformities of fingers
           H01246  非症候群性先天性ばち指
         LB81  Congenital deformities of toes
         LB8Z  Congenital deformities of fingers or toes, unspecified
         LB90  Joint formation defects
           H00484  多発性骨癒合症症候群
           H00851  近位指趾関節癒合症
         LB91  Congenital shoulder dislocation
         LB92  Congenital elbow dislocation
         LB93  Congenital knee dislocation
         LB94  Congenital patella dislocation
         LB95  Patella aplasia or hypoplasia
         LB96  Congenital bowing of long bones
         LB97  Limb overgrowth
         LB98  Congenital deformities of feet
           H00903  先天内反足
           H00929  先天性垂直距骨
         LB99  Reduction defects of upper limb
           H00471  裂手/裂足症
         LB9A  Reduction defects of lower limb
           H00471  裂手/裂足症
         LB9B  Reduction defects of upper or lower limbs
           H00629  無手足症
           H00636  無四肢症
         LB9Y  Other specified structural developmental anomalies of the skeleton
           H00873  Cousin 症候群
         LB9Z  Structural developmental anomalies of the skeleton, unspecified
           H00762  先天性関節脱臼を伴う脊椎骨端異形成
     Structural developmental anomalies of the skin
       Developmental hamartomata of the epidermis and epidermal appendages
       Developmental anomalies of skin pigmentation
       Hamartomata derived from dermal connective tissue
       Developmental defects of hair or nails
       Developmental anomalies of cutaneous vasculature
         LC50  Developmental capillary vascular malformations of the skin
         LC51  Developmental venous malformations involving the skin
           H02044  粘膜皮膚静脈奇形 (VMCM)
         LC52  Complex or combined developmental vascular malformations involving the skin
         LC5Y  Other specified developmental anomalies of cutaneous vasculature
         LC5Z  Cutaneous vascular malformation, unspecified
       Congenital anomalies of skin development
         LC60  Aplasia cutis congenita
           H01896  先天性皮膚欠損
         LC7Y  Other specified structural developmental anomalies of the skin
         LC7Z  Structural developmental anomalies of the skin, unspecified
     Structural developmental anomalies of the adrenal glands
       LC80  Congenital adrenal hypoplasia
         H01772  先天性副腎低形成症
       LC8Y  Other specified structural developmental anomalies of the adrenal glands
       LC8Z  Structural developmental anomalies of the adrenal glands, unspecified
       LD0Y  Other specified structural developmental anomalies primarily affecting one body system
       LD0Z  Structural developmental anomalies primarily affecting one body system, unspecified
   Multiple developmental anomalies or syndromes
     LD20  Syndromes with central nervous system anomalies as a major feature
       H00530  ジュベール症候群
       H00897  橋小脳低形成
       H01001  COACH 症候群
       H01811  有馬症候群
       H02272  CAPOS 症候群
       H00268  脳回欠損症
       H00792  ワールブルグ・ ミクロ症候群
       H02117  Neu-Laxova 症候群
       H00616  ボーエン-コンラディ症候群
       H00840  Band-like calcification with simplified gyration and polymicrogyria
       H00990  アーミッシュ型小頭症
       H00991  MOPD II
       H00993  Taybi-Linder 症候群
       H01872  小頭症-毛細血管異形成症候群
       H01876  Microcephaly with or without chorioretinopathy, lymphedema, or mental retardation
       H01921  MICPCH 症候群
       H02132  小頭症症候群
       H00544  中隔視神経形成異常症
       H00816  Agenesis of the corpus callosum with peripheral neuropathy (ACCPN)
       H01034  L1 症候群
       H01035  精神遅滞・眼欠損症・小顎症を伴う脳梁欠損症
       H01776  アイカルディ症候群
       H01789  You-Hoover-Fong 症候群
       H01919  Proud 症候群
       H01937  Multinucleated neurons, anhydramnios, renal dysplasia, cerebellar hypoplasia, and hydranencephaly
     LD21  Syndromes with eye anomalies as a major feature
       H01904  線状皮膚欠損を伴う小眼球症
       H02134  四肢異常を伴う眼球低形成
       H02170  小眼球症 (症候群性)
       H00673  Weill-Marchesani 症候群
       H00826  眼瞼裂狭小・眼瞼下垂・逆内眼角贅皮症候群
       H01012  眼-耳症候群
       H02045  Norrie 病
     LD22  Syndromes with dental anomalies as a major feature
     LD23  Syndromes with vascular anomalies as a major feature
       H00579  HANAC 症候群
       H01809  スタージ・ウェーバー症候群
       H02088  Primary intraosseous vascular malformation
     LD24  Syndromes with skeletal anomalies as a major feature
       H00520  II 型コラーゲン異常症
       H00505  FGFR3関連骨異形成症
       H01749  軟骨無形成症
       H02069  SADDAN
       H02068  軟骨低形成症
       H01750  タナトフォリック骨異形成症
       H00515  骨発生不全症 II 型
       H02063  捻曲性骨異形成症
       H00207  肢根型点状軟骨異形成症
       H00447  グリーンバーグ骨異形成症
       H00496  CHILD 症候群
       H01194  X連鎖性点状軟骨異形成症
       H00436  大理石骨病
       H00452  ブシュケ‐オレンドルフ症候群
       H00434  Camurati-Engelmann病
       H00444  頭部硬化症を伴う線状骨障害
       H00450  Worth 型 常染色体優性遺伝性骨硬化症
       H00486  硬結性骨化症
       H00490  貧血を伴う骨幹異形成
       H00491  頭蓋骨幹異形成症
       H00508  Blomstrand 症候群
       H00613  小児性皮質性骨増殖
       H00968  Raine 症候群
       H01832  Lenz-Majewski 症候群
       H00122  多発性外骨腫症
       H00493  ヘパラン硫酸プロテオグリカン異常
       H00497  ケルビム症
       H02127  Yunis-Varon 症候群
       H00443  骨空洞性骨異形成症
       H00498  顎骨骨幹異形成症
       H00521  鎖骨頭蓋異形成症
       H01018  Metachondromatosis
       H00445  軽症の軟骨形成異常に伴う変形性関節症
       H00474  蝸牛様骨盤異形成症
       H00483  天使形指節骨・骨端異形成症
       H00499  椎骨-手根骨-足根骨癒合症候群
       H00519  先天性脊椎骨端異形成
       H00757  Dyggve-Melchior-Clausen 病 及び Smith-McCort dysplasia
       H00758  Progressive pseudorheumatoid dysplasia
       H00760  遅発性脊椎骨端異形成
       H00761  パキスタン型脊椎骨端骨幹端異形成
       H00765  キンバリー型脊椎骨端異形成症
       H00767  Matrilin型脊椎骨端骨幹端異形成
       H00777  短肢・手型脊椎骨端骨幹端異形成
       H00863  脊椎分離-大骨端-骨幹端異形成
       H01494  脊椎骨端骨幹端異形成-関節弛緩
       H01575  Roifman 症候群
       H01576  Spondyloenchondrodysplasia with immune dysregulation (SPENCDI)
       H01967  Anauxetic dysplasia
       H02070  Kniest 異形成症
       H02071  Czech 異形成症
       H02079  耳・脊椎・巨大骨端異形成症
       H02080  Fibrochondrogenesis
       H02155  分節異常骨異形成症
       H02183  Parastremmatic dwarfism
       H02184  変容性骨異形成症
       H02186  脊椎骨端異形成 Maroteaux 型
       H02187  脊椎骨端骨幹端異形成
       H01821  錐体・杆体ジストロフィーを伴う脊椎骨幹端異形成
       H01825  Sedaghatian 型脊椎骨幹端異形成症
       H01830  Megarbane-Dagher-Melki 型脊椎骨幹端異形成症
       H02185  脊椎骨幹端異形成
       H00678  軟骨無発生症 IA 型
       H02065  軟骨無発生症 IB 型
       H02066  軟骨無発生症 II 型
       H00522  短体幹症
       H01828  成熟遅延骨異形成症
       H01844  透明脊椎異骨症
       H00495  Eiken dysplasia
       H00477  偽軟骨異形成症
       H00476  多発性骨端異形成症
       H00479  骨幹端異形成症
       H00518  貧毛を伴わない骨幹端形成異常
       H00675  先端大腿骨頭異形成
       H00900  Geleophysic dysplasia
       H02062  短指を伴う家族性指関節症
       H02228  先端短肢異形成症
       H02229  肢端骨異形成
       H00466  Grebe 型異形成症
       H00468  Demirhan型 遠位中間肢異形成症
       H00470  Maroteaux 型遠位中間肢異形成症
       H00485  ロビノウ症候群
       H00492  SHOX-関連低身長症
       H02154  肩骨異形成症
       H00511  短肋骨多指症候群
       H00751  窒息性胸郭ジストロフィー
       H02157  短肋骨胸郭異形成症
       H00462  Stuve-Wiedemann 症候群
       H00509  3M 症候群
       H00619  ケニー・キャフェイ症候群
       H00622  Hypoparathyroidism-retardation-dysmorphism 症候群
       H00992  Seckel 症候群
       H02223  骨頭蓋骨狭窄症
       H00494  Desbuquois 症候群
       H01498  多発性関節脱臼-低身長-頭蓋顔面形態異常-先天性心奇形
       H02048  ラーセン症候群
       H02064  骨発生不全症 I 型 および III 型
       H02067  ブーメラン異形成
       H00458  症候性頭蓋縫合早期癒合症
       H01756  ファイファー症候群
       H01754  クルーゾン症候群
       H01755  アペール症候群
       H01008  C 症候群
       H01753  アントレー・ビクスラー症候群
       H01888  カーペンター症候群
       H01988  Jackson-Weiss 症候群
       H01989  Beare-Stevenson 症候群
       H01990  Muenke 症候群
       H01991  ゼーツレ‐コッツェン症候群
       H01992  頭蓋前頭鼻骨症候群
       H01993  バラー・ゲロルト症候群
       H02047  Bohring-Opitz 症候群
       H02254  頭蓋縫合早期癒合症および歯の異常
       H00517  脊椎肋骨異骨症
       H01843  脳・肋骨・下顎症候群
       H00464  爪膝蓋骨症候群
       H00461  Ischiocoxopodopatellar 症候群
       H01889  Meier-Gorlin 症候群
       H00506  骨形成不全症
       H00451  骨粗鬆症・偽性神経膠腫症候群
       H00514  ブルック症候群
       H01496  椎体眼症候群
       H01571  Singleton-Merten 症候群
       H01572  Cole-Carpenter 症候群
       H02233  Alazami 症候群
     LD25  Syndromes with face or limb anomalies as a major feature
       H00454  Oral-facial-digital 症候群
       H00456  前頭・耳口蓋指症候群
       H01816  Frank-ter Haar 症候群
       H02227  前頭・骨幹端異形成症
       H01376  四肢顔面骨形成不全症
       H02158  Weyers 先端歯骨形成不全症
       H00528  前頭鼻異形成
       H00850  Frontorhiny
       H01884  Auriculocondylar 症候群
       H02210  遠位肢前頭鼻異形成症
       H02234  Hamamy 症候群
     LD26  Syndromes with limb anomalies as a major feature
       H00467  Du Pan症候群
       H00855  3節母指・多合指症候群
       H00859  Guttmacher 症候群
       H00870  短指‐合指症候群
       H02161  グレイグ尖頭多合指症候群
       H00778  Tarsal-carpal coalition 症候群
       H00986  多発性翼状片症候群
       H00935  寒冷誘発性発汗症候群
       H01392  関節拘縮・精神遅滞・てんかん
       H01886  Van den Ende-Gupta 症候群
       H00811  遠位関節拘縮症
       H00865  致死性先天性拘縮症候群
       H00872  Hecht-Beals 症候群
       H01931  Bartsocas-Papas 症候群
       H02268  Wieacker-Wolff 症候群
       H00532  パークスウェーバー症候群
       H01788  クリッペル・トレノネー・ウェーバー症候群
       H01497  軸前性短指症候群
       H00846  Fuhrmann 症候群
       H00847  Al-Awadi/Raas-Rothschild 症候群
     LD27  Syndromes with skin or mucosal anomalies as a major feature
       H00645  色素失調症
       H01874  クロンカイト・カナダ症候群
       H00651  発汗低下を伴う先天性外胚葉形成異常症
       H00648  外胚葉形成異常 Clouston 型
       H00095  外胚葉異形成症に伴う免疫不全症
       H00449  眼歯指異形成症
       H00487  毛髪・歯・骨症候群
       H00503  Ellis-van Creveld 症候群
       H00529  頭蓋外胚葉性異形成症
       H00540  OLEDAID
       H00571  ヨハンソン‐ブリザード症候群
       H00638  EEC 症候群
       H00639  EEM 症候群
       H00640  Limb-mammary 症候群
       H00641  ADULT 症候群
       H00642  LADD 症候群
       H00643  歯爪症候群
       H00646  歯・爪・皮膚形成異常
       H00647  外胚葉異形成‐合指症症候群
       H00649  外胚葉性形成異常 毛髪・爪型
       H00708  Naegeli-Franceschetti-Jadassohn 症候群
       H00752  Hay–Wells 症候群 及び Rapp–Hodgkin 症候群
       H00781  Schopf-Schulz-Passarge 症候群
       H00796  網状色素性皮膚症
       H00922  Schinzel-Giedion 症候群
       H00949  巣状皮膚低形成
       H00977  毛髪鼻指節骨症候群
       H01271  HDR症候群
       H01403  コフィン・シリス症候群
       H01905  長睫毛症
       H01966  軟骨毛髪低形成症
       H02058  Kohlschutter-Tonz 症候群
       H02081  マーシャル症候群
       H02083  巣状顔面皮膚異形成症
       H02218  DOORS 症候群
       H02219  DDOD 症候群
       H01428  色素性乾皮症
       H00671  ネザートン症候群
       H00712  KID/HID 症候群
       H00739  乏毛症を伴う魚鱗癬
       H00740  IFAP 症候群
       H00741  魚鱗癬未熟児症候群
       H00799  CEDNIK 症候群
       H01934  Barber-Say 症候群
       H00818  Birt-Hogg-Dube 症候群
       H01986  Legius 症候群
       H02189  神経線維腫性ヌーナン症候群
       H01741  中條-西村症候群
       H00665  下顎骨異形成
       H02236  Keppen-Lubinsky 症候群
       H00684  先天性爪甲硬厚症
       H00696  Haim-Munk 症候群
       H00785  若年性黄斑変性を伴う先天性貧毛症
       H00815  H 症候群
       H00883  類脂質蛋白症
     LD28  Syndromes with connective tissue involvement as a major feature
       H00660  先天性拘縮性クモ指症
       H00653  マルファン症候群
       H00800  Loeys-Dietz 症候群
       H00659  Shprintzen-Goldberg 症候群
       H00661  MASS 症候群
       H01385  Rienhoff 症候群
       H00802  エーラース・ダンロス症候群
       H01902  脆弱角膜症候群
       H02239  エーラース・ダンロス症候群 脊椎異形成型
       H02240  エーラース・ダンロス症候群 歯周型
       H02241  エーラース・ダンロス症候群 心臓弁型
       H02242  エーラース・ダンロス症候群 血管型
       H02243  エーラース・ダンロス症候群 多発関節弛緩型
       H02244  エーラース・ダンロス症候群 皮膚脆弱型
       H02245  エーラース・ダンロス症候群 後側彎型
       H02246  エーラース・ダンロス症候群 筋拘縮型
       H02247  エーラース・ダンロス症候群 ミオパチー型
       H00904  Urban-Rifkin-Davis 症候群
       H00906  MACS 症候群
       H01859  オクシピタル・ホーン症候群
       H00919  動脈蛇行症候群
       H02224  Grange 症候群
     LD29  Syndromes with obesity as a major feature
       H01915  Borjeson-Forssman-Lehmann 症候群
       H02195  MEHMO 症候群
       H02267  Wilson-Turner 症候群
     LD2A  Malformative disorders of sex development
       H00607  46,XY 性腺形成不全症
       H00608  46,XY性分化疾患 (テストステロン分泌異常)
       H02177  アンドロゲン不応症
       H00442  屈曲肢異形成
       H00598  46,XX 精巣性分化疾患
       H00609  ミュラー管遺残症候群
     LD2B  Syndromes with premature ageing appearance as a major feature
       H00076  コケイン症候群
       H00558  老人様皮膚萎縮骨形成異常症
       H00601  ハッチンソン・ギルフォード早老症候群
       H01733  ウェルナー症候群
       H01734  ロスムンド-トムソン症候群
       H01883  Nestor-Guillermo 早老症候群
     LD2C  Overgrowth syndromes
       H00713  ベックウィズ・ウイーデマン症候群
       H00718  ソトス症候群
       H00980  Nevo 症候群
       H01215  Simpson-Golabi-Behmel 症候群
       H01308  巨大頭蓋巨人症および顔異形症候群
       H01412  パールマン症候群
       H01751  ウィーバー症候群
       H01806  Tenorio 症候群
       H01834  Marshall-Smith 症候群
       H01885  Megalencephaly-polymicrogyria-polydactyly-hydrocephalus 症候群
       H01909  Hypoinsulinemic hypoglycemia with hemihypertrophy
       H01912  CLOVE 症候群
       H02119  プロテウス症候群
       H02153  巨頭症-毛細血管奇形症候群
     LD2D  Phakomatoses or hamartoneoplastic syndromes
       H00666  ポイツ・ジェーガーズ症候群
       H01437  神経線維腫症 I 型
       H01438  神経線維腫症 II 型
       H00915  結節性硬化症
       H00895  基底細胞母斑症候群
       H00559  フォンヒッペル・リンダウ症候群
       H01222  カウデン症候群
     LD2E  Syndromes with structural anomalies due to inborn errors of metabolism
     LD2F  Syndromes with multiple structural anomalies, without predominant body system involvement
       H00979  尾退行症候群 及び 人魚体
       H02129  Prune belly 症候群
       H01195  VATER/VACTERL連合
       H00261  メッケル症候群
       H01738  ヌーナン症候群
       H00610  トレチャーコリンズ症候群
       H01838  小頭症を伴う下顎顔面異形成症
       H02126  Mandibulofacial dysostosis with alopecia
       H02211  先端骨形成不全症
       H00433  ホルト・オラム症候群
       H00453  鰓弓耳腎症候群
       H00460  Hand-foot-genital 症候群
       H00463  Currarino 症候群
       H00500  Keutel 症候群
       H00502  Pallister-Hall 症候群
       H00504  ルビンシュタイン・テイビ症候群
       H00510  ファインゴールド症候群
       H00523  ヌーナン症候群類縁疾患
       H00555  Char 症候群
       H00556  チャージ症候群
       H00569  アースコグ症候群
       H00570  歌舞伎症候群
       H00572  ESCO2関連疾患
       H00573  Townes-Brocks 症候群
       H00574  コフィン・ローリー症候群
       H00583  Opitz-GBBB 症候群
       H00611  膝窩部贅皮症候群
       H00631  Cornelia de Lange 症候群
       H00634  オキヒロ症候群 及び IVIC 症候群
       H00637  Schinzel 症候群
       H00685  BNAR 症候群
       H00686  MOTA 症候群
       H00709  Birk-Barel 症候群
       H00711  ラッセル・シルバー症候群
       H00753  Urofacial 症候群
       H00756  Pitt-Hopkins 症候群
       H00797  Martsolf 症候群
       H00817  鰓・眼・顔面症候群
       H00868  Stapes ankylosis with broad thumb and toes
       H00886  Donnai-Barrow 症候群
       H00889  Lujan-Fryns 症候群
       H00894  FG 症候群
       H00907  Kleefstra 症候群
       H00908  モワットウィルソン症候群
       H00914  ワルシャワ破壊症候群
       H00926  Growth retardation, developmental delay, coarse facies, and early death
       H00934  尾方重複異常
       H00936  Goldberg-Shprintzen 巨大結腸症候群
       H00943  TARP 症候群
       H00965  RAPADILINO 症候群
       H00972  内分泌系-脳-骨異形成症候群
       H00987  Fetal akinesia deformation sequence
       H00997  CATSHL 症候群
       H01026  腎コロボーマ症候群
       H01030  前角細胞疾患を伴う致死性関節拘縮症
       H01156  STAR 症候群
       H01220  先天性白内障・顔貌異常およびニューロパチー
       H01265  Hydrolethalus 症候群
       H01289  マリブレー低身長症
       H01292  Nance-Horan 症候群
       H01370  SHORT 症候群
       H01413  アダムズ-オリバー症候群
       H01568  3C 症候群
       H01569  CHOPS 症候群
       H01573  Zimmermann-Laband 症候群
       H01745  CFC 症候群
       H01747  コステロ症候群
       H01793  ヤング・シンプソン症候群
       H01794  Genitopatellar 症候群
       H01795  眼瞼裂狭小・精神遅滞症候群
       H01797  Webb-Dattani 症候群
       H01814  Stromme 症候群
       H01839  Burn-McKeown 症候群
       H01840  メビウス症候群
       H01845  Catel-Manzke 症候群
       H01869  巨大膀胱短小結腸腸管蠕動不全症
       H01878  Al-Raqad 症候群
       H01879  ウィデマンスタイナー症候群
       H01887  3MC 症候群
       H01908  Carey‐Fineman‐Ziter 症候群
       H01917  CK 症候群
       H01923  小頭症・低身長・グルコース代謝異常
       H01927  Van der Woude 症候群
       H01930  Au-Kline 症候群
       H01932  無眼瞼・巨口症症候群
       H01984  レオパード症候群
       H02023  Baraitser-Winter 症候群
       H02046  OFC 症候群
       H02072  スティックラー症候群
       H02074  Knobloch 症候群
       H02082  Floating-Harbor 症候群
       H02087  先天性 NAD 欠乏症
       H02102  Myhre 症候群
       H02180  McKusick-Kaufman 症候群
       H02190  CBL 症候群
       H02191  成長期脱毛を伴うヌーナン様症候群
       H02198  膵欠損症および先天性心疾患
       H02232  CAGSSS 症候群
       H02248  MEND 症候群
       H02249  Primrose 症候群
       H02253  Beaulieu-Boycott-Innes 症候群
       H02255  FDLAB 症候群
       H02260  Chassaing-Lacombe 型軟骨異形成症
       H02271  小脳・顔・歯症候群
       H02274  小脳萎縮、視力障害および精神運動発達遅滞
       H01824  CODAS (脳・眼・歯・耳介・骨格) 症候群
       H01850  Hartsfield 症候群
       H01857  Filippi 症候群
     LD2G  Conjoined twins
     LD2H  Syndromic genetic deafness
       H00687  フレイザー症候群
       H00779  アッシャー症候群
       H00446  Craniofacial-deafness-hand 症候群
       H00581  アルポート症候群
       H00706  Bart-Pumphrey 症候群
       H00727  Athabascan 脳幹発育不全症候群
       H00803  SeSAME/EAST 症候群
       H00823  ABCD 症候群
       H00946  Arts 症候群
       H01286  小耳症・難聴および口蓋裂
       H01903  Brown-Vialetto-Van Laere 症候群
       H02095  Perrault 症候群
       H02135  錐体杆体ジストロフィーおよび難聴
       H02220  MEDNIK 症候群
       H02226  心脊椎手根骨顔症候群
     LD2Y  Other specified multiple developmental anomalies or syndromes
       H00417  アルストレム症候群
       H00418  バルデ・ビードル症候群
     LD2Z  Multiple developmental anomalies or syndromes, unspecified
       H00493  ヘパラン硫酸プロテオグリカン異常
   Chromosomal anomalies, excluding gene mutations
     LD40  Complete trisomies of the autosomes
       H01552  ダウン症候群
       H01562  パトー症候群
       H01564  エドワ−ズ症候群
     LD41  Duplications of the autosomes
       H01790  エマヌエル症候群
     LD42  Polyploidies
     LD43  Complete monosomies of the autosomes
     LD44  Deletions of the autosomes
       H01831  環状20番染色体症候群
       H01792  1p36 欠失症候群
       H00561  短指症-精神遅滞症候群
       H02146  Glass 症候群
       H01773  4p 欠失症候群
       H01223  常同性運動・てんかん および/または大脳奇形を伴う精神遅滞
       H00764  5p欠失症候群
       H01439  ウィリアムズ症候群
       H01800  Verheij 症候群
       H02103  Desanto-Shinawi 症候群
       H02156  Lamb-Shaffer 症候群
       H01861  15q24 微細欠失症候群
       H01877  15q13.3 微細欠失症候群
       H02121  Koolen-De Vries 症候群
       H01791  スミス・マギニス症候群
       H01004  口蓋心臓顔面症候群
       H01524  ディジョ−ジ症候群
       H01525  22q11.2 欠失症候群
       H01238  Phelan-McDermid 症候群
     LD45  Uniparental disomies
       H01801  第14番染色体父親性ダイソミー症候群
     LD46  Imprinting errors
     LD47  Balanced rearrangements or structural markers
     Sex chromosome anomalies
       LD50  Number anomalies of chromosome X
       LD51  Structural anomalies of chromosome X, excluding Turner syndrome
         H00552  Xp21欠失症候群
       LD52  Number anomalies of chromosome Y
       LD53  Structural anomalies of chromosome Y
       LD54  Male with sex chromosome mosaicism
       LD55  Fragile X chromosome
         H00465  脆弱X症候群
         H01731  脆弱X症候群関連疾患
       LD56  Chimaera 46, XX, 46, XY
       LD5Y  Other specified sex chromosome anomalies
       LD5Z  Sex chromosome anomalies, unspecified
       LD7Y  Other specified chromosomal anomalies, excluding gene mutations
         H01288  多彩異数性モザイク症候群
       LD7Z  Chromosomal anomalies, excluding gene mutations, unspecified
       LD90  Conditions with disorders of intellectual development as a relevant clinical feature
         H01732  アンジェルマン症候群
         H00478  プラダー・ウィリー症候群
         H00440  レット症候群
         H00597  シュナイダー ロビンソン症候群
         H00769  過剰驚愕症
         H00940  Cohen 症候群
         H01752  ATR-X 症候群
         H01769  ZTTK 症候群
         H01913  レンペニング症候群
         H01914  クリスチャンソン症候群
         H01916  Stocco dos Santos X連鎖性精神遅滞症候群
         H01920  Partington 症候群
         H01922  精神運動遅滞と特徴的顔貌を伴う小児筋緊張低下
         H02137  ローレンス・ムーン症候群
         H02252  PEHO 症候群
       LD9Y  Other specified developmental anomalies
       LD9Z  Developmental anomalies, unspecified
 
 21 Symptoms, signs or clinical findings, not elsewhere classified
   Symptoms, signs or clinical findings of blood, blood-forming organs, or the immune system
   Symptoms, signs or clinical findings of endocrine, nutritional or metabolic diseases
   Symptoms, signs or clinical findings of speech or voice
   Mental or behavioural symptoms, signs or clinical findings
   Symptoms, signs or clinical findings of the nervous system
     Symptoms or signs involving the nervous system
       MB40  Sensation disturbance
       MB41  Disturbances of smell and taste
       MB42  Phonophobia
       MB43  Dyssomnia
       MB44  Abnormalities of gait and mobility
       MB45  Lack of coordination
       MB46  Abnormal involuntary movements
       MB47  Abnormality of tonus and reflex
       MB48  Dizziness and giddiness
       MB49  Aura
       MB4A  Apraxia
       MB4B  Symbolic dysfunctions
         H01899  読字障害
       MB4C  Gerstmann syndrome
       Paralytic symptoms
         MB50  Tetraplegia
         MB51  Diplegia of upper extremities
         MB52  Diplegia of lower extremities
         MB53  Hemiplegia
           H00998  小児交互性片麻痺
         MB54  Monoplegia of upper extremity
         MB55  Monoplegia of lower extremity
         MB56  Paraplegia
         MB57  Functional level of injury of spinal cord
         MB5Y  Other specified paralytic symptoms
         MB5Z  Paralytic symptoms, unspecified
         MB60  Sleeptalking
         MB6Y  Other specified symptoms or signs involving the nervous system
     Clinical findings in the nervous system
   Symptoms, signs or clinical findings of the visual system
   Symptoms, signs or clinical findings of ear or mastoid process
   Symptoms, signs or clinical findings of the circulatory system
   Symptoms, signs or clinical findings of the respiratory system
   Symptoms, signs or clinical findings of the digestive system or abdomen
   Symptoms, signs or clinical findings involving the skin
   Symptoms, signs or clinical findings of the musculoskeletal system
   Symptoms, signs or clinical findings of the genitourinary system
     Symptoms, signs or clinical findings involving the female genital system
     Symptoms, signs or clinical findings involving the male genital system
     Symptoms, signs or clinical findings involving the urinary system
     Clinical findings in specimens from female genital organs
     Clinical findings in specimens from male genital organs
     Clinical findings in specimens from the urinary system
       MF80  Diffuse mesangial sclerosis
       MF81  Fibronectin glomerulopathy
         H01260  フィブロネクチン腎症
       MF82  Lipoprotein glomerulopathy
         H00887  Lipoprotein glomerulopathy
       MF83  Diabetic glomerular changes
       MF84  Pauci-immune proliferative glomerulonephritis
       MF85  Anti-glomerular basement membrane antibody mediated disease
         H01721  抗糸球体基底膜腎炎
       MF8Y  Other specified clinical findings in specimens from the urinary system
         H00626  巣状分節性糸球体硬化症
         H01581  IgA 腎症
         H01726  膜性増殖性糸球体腎炎
         H01767  紫斑病性腎炎
       MF8Z  Clinical findings in specimens from the urinary system, unspecified
     Clinical findings on examination of urine, without diagnosis
       MF90  Acetonuria
       MF91  Bilirubinuria
       MF92  Chyluria
       MF93  Glycosuria
       MF94  Haemoglobinuria
       MF95  Myoglobinuria
         H01290  発作性ミオグロビン尿症
       MF96  Proteinuria
       MF97  Pyuria
       MF98  Abnormal levels of serum electrolytes in the urine
       MF99  Elevated urine levels of drugs, medicaments and biological substances
       MF9A  Abnormal urine levels of substances chiefly nonmedicinal as to source
       MF9B  Abnormal findings on microbiological examination of urine
       MF9C  Abnormal findings on cytological and histological examination of urine
       MF9Y  Other specified clinical findings on examination of urine, without diagnosis
       MG00  Clinical findings on diagnostic imaging of breast
       MG01  Clinical findings on diagnostic imaging of urinary organs
       MG02  Results of kidney function studies
       MG0Y  Other specified symptoms, signs or clinical findings of the genitourinary system
   General symptoms, signs or clinical findings
     General symptoms
       MG20  Cachexia
       MG21  Chills
       MG22  Fatigue
       MG23  Fear of death or dying
       MG24  Fear of disease
       MG25  Feeling ill
       MG26  Fever of other or unknown origin
       MG27  Haemorrhage, not elsewhere classified
       MG28  Hypothermia, not associated with low environmental temperature
       MG29  Oedema
       MG2A  Old age
       Pain
         MG30  Chronic pain
           H01636  線維筋痛症
         MG31  Acute pain
         MG3Z  Pain, unspecified
         MG40  Shock
         MG41  Sleep disturbance, not elsewhere classified
         MG42  Somnolence, not elsewhere classified
         MG43  Symptoms and signs concerning food and fluid intake
         MG44  Symptoms peculiar to infancy
         MG45  Syncope and collapse
         MG46  Systemic inflammatory response syndrome of noninfectious origin
         MG47  Toxicosis not further specified
         MG48  Unknown and unspecified causes of morbidity
         MG4Y  Other specified general symptoms
     Finding of microorganism resistant to antimicrobial drugs
       MG50  Finding of gram negative bacteria resistant to antimicrobial drugs
         H00309  薬剤耐性アシネトバクター感染症
         H01422  カルバペネム耐性菌感染症
         H00313  多剤耐性緑膿菌感染症
       MG51  Finding of gram positive bacteria resistant to antimicrobial drugs
         H00330  メチシリン耐性ブドウ球菌感染症
         H00331  バンコマイシン耐性ブドウ球菌感染症
         H01423  ペニシリン耐性肺炎球菌感染症
         H00340  バンコマイシン耐性腸球菌感染症
         H01401  メチシリン耐性表皮ブドウ球菌感染症
       MG52  Finding of bacteria, neither gram negative nor positive, resistant to antimicrobial drugs
         H01472  多剤耐性結核
       MG53  Finding of virus resistant to antimicrobial drugs
       MG54  Finding of fungus resistant to antimicrobial drugs
       MG55  Finding of parasite resistant to antimicrobial drugs
       MG56  Finding of microorganism resistant to other multiple antimicrobial drugs
       MG5Y  Finding of other microorganism resistant to antimicrobial drugs
       MG5Z  Finding of microorganism resistant to antimicrobial drugs, unspecified
     Clinical findings in specimens from other specified organs, systems and tissues
     Abnormal results, not elsewhere classified
   Ill-defined and unknown causes of mortality
     MH10  Brain death
     MH11  Sudden infant death syndrome
       H02174  精巣形成不全を伴う乳児突然死症候群
     MH12  Other sudden death, cause unknown
     MH13  Unattended death
     MH14  Other ill-defined and unspecified causes of mortality
     MH15  Sudden unexplained death in epilepsy
     MH16  Multi organ failure
     MH2Y  Other specified symptoms, signs or clinical findings, not elsewhere classified
 
 22 Injury, poisoning or certain other consequences of external causes
   Injuries to the head
   Injuries to the neck
   Injuries to the thorax
   Injuries to the abdomen, lower back, lumbar spine or pelvis
   Injuries to the shoulder or upper arm
   Injuries to the elbow or forearm
   Injuries to the wrist or hand
   Injuries to the hip or thigh
   Injuries to the knee or lower leg
   Injuries to the ankle or foot
   Injuries involving multiple body regions
   Injuries to unspecified part of trunk, limb or body region
   Effects of foreign body entering through natural orifice
   Burns
   Frostbite
   Harmful effects of substances
   Injury or harm arising from surgical or medical care, not elsewhere classified
     NE80  Injury or harm arising following infusion, transfusion or therapeutic injection, not elsewhere classified
     NE81  Injury or harm arising from a procedure, not elsewhere classified
     NE82  Dysfunction or complication of pacemaker, pacemaker lead or implantable cardioverter defibrillator, not elsewhere classified
     NE83  Injury or harm arising from other device, implant or graft, not elsewhere classified
     NE84  Failure or rejection of transplanted organs or tissues
       H00083  同種移植片拒絶反応
     NE85  Complications peculiar to reattachment or amputation
     NE86  Malignant hyperthermia due to anaesthesia
     NE87  Failed or difficult intubation
     NE88  Drug toxicity associated with harm in surgical or medical care, not elsewhere classified
     NE8Y  Other specified injury or harm arising from surgical or medical care, not elsewhere classified