KEGG    Network variation - Sphingolipid degradation
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ENTRYnt06014
NameSphingolipid degradation
CategoryPathway view; Lipid/glycolipid metabolism
Pathwayhsa00600 Sphingolipid metabolism
DiseaseH00423 Sphingolipidosis
Display drug-target relation   disease type
N01710   
    GM1 gangliosidosis
    Tay-Sachs disease
    Sandhoff disease
N01713   
N01714    GM2 gangliosidosis, AB variant
N01711   
N01709   
N10015   
    Fabry disease
N10016   
    Fabry disease
 
N00640   
N10017   
    Gaucher disease
N10018   
N10017   
N00679    Gaucher disease
N00642   
N00643    Gaucher disease
 
N00644   
N01712   
    Krabbe disease
 
N00647   
    Metachromatic leukodystrophy
 
N00649   
N10029   
    Niemann-Pick disease
    Farber lipogranulomatosis

Disease nameDisease category
GM1 gangliosidosisH00281GM1 gangliosidosisInherited metabolic disorder, Lysosomal disease
Tay-Sachs diseaseH02016Tay-Sachs diseaseInherited metabolic disorder, Lysosomal disease
Sandhoff diseaseH02017Sandhoff diseaseInherited metabolic disorder, Lysosomal disease
GM2 gangliosidosis, AB variantH00124GM2 gangliosidosesInherited metabolic disorder, Lysosomal disease
Fabry diseaseH00125Fabry diseaseInherited metabolic disorder, Lysosomal disease
Gaucher diseaseH00126Gaucher diseaseInherited metabolic disorder, Lysosomal disease
Krabbe diseaseH00135Krabbe diseaseInherited metabolic disorder, Lysosomal disease
Metachromatic leukodystrophyH00127Metachromatic leukodystrophyInherited metabolic disorder, Lysosomal disease
Niemann-Pick diseaseH00137Niemann-Pick disease type A/BInherited metabolic disorder, Lysosomal disease
Farber lipogranulomatosisH00138Farber lipogranulomatosisInherited metabolic disorder, Lysosomal disease