CC: CCSD:48522
AU: Brady RO; Murray GJ; Barton NW
TI: Modifying exogenous glucocerebrosidase for effective replacement
therapy in Gaucher disease
CT: J Inherit Metab Dis (1994) 17: 510-519 [PMID:7967500]
SC: fig. 1
BS: (CN) human, (OT) placenta
PM: glucocerebrosidase
MT: N-linked glycoprotein
SB: Westra B
DA: 05-04-1996
FC: ee6b824e
SI: CBank:21874
----------------
structure:
b-D-Galp-(1-4)-b-D-GlcpNAc-(1-6)+
|
a-D-Manp-(1-6)+
| |
a-D-Neup5Ac-(2-3)-b-D-Galp-(1-4)-b-D-GlcpNAc-(1-2)+ b-D-Manp-(1-4)-b-D-GlcpNAc-(1-4)-D-GlcNAc
|
a-D-Neup5Ac-(2-3)-b-D-Galp-(1-4)-b-D-GlcpNAc-(1-2)-a-D-Manp-(1-3)+
================end of record