KEGG   ENZYME: 3.2.1.76Help
Entry
EC 3.2.1.76                 Enzyme                                 

Name
L-iduronidase;
alpha-L-iduronidase
Class
Hydrolases;
Glycosylases;
Glycosidases, i.e. enzymes that hydrolyse O- and S-glycosyl compounds
BRITE hierarchy
Sysname
glycosaminoglycan alpha-L-iduronohydrolase
Reaction(IUBMB)
Hydrolysis of unsulfated alpha-L-iduronosidic linkages in dermatan sulfate
Reaction(KEGG)
(other) R07813(G) R07822(G)
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Pathway
Glycosaminoglycan degradation
Metabolic pathways
Orthology
K01217  
L-iduronidase
Genes
HSA: 
3425(IDUA)
PTR: 
461056(IDUA)
PPS: 
100987172(IDUA)
GGO: 
101130097(IDUA)
PON: 
100458752(IDUA)
MMU: 
15932(Idua)
RNO: 
360904(Idua)
AML: 
FCA: 
101095896(IDUA)
BTA: 
511050(IDUA)
ECB: 
100146682(IDUA)
SHR: 
100921889(IDUA)
OAA: 
GGA: 
427294(IDUA)
MGP: 
TGU: 
ACS: 
100560915(idua)
XLA: 
446866(idua)
XTR: 
DRE: 
567720(idua)
TRU: 
OLA: 
BFO: 
CIN: 
SPU: 
DME: 
DPO: 
DAN: 
DER: 
DPE: 
DSE: 
DSI: 
DWI: 
DYA: 
DGR: 
DMO: 
DVI: 
AGA: 
AAG: 
CQU: 
TCA: 
PHU: 
ISC: 
NVE: 
MBR: 
RLE: 
 » show all
Taxonomy
Reference
1  [PMID:4993544]
  Authors
Matalon R, Cifonelli JA, Dorfman A.
  Title
L-iduronidase in cultured human fibroblasts and liver.
  Journal
Biochem. Biophys. Res. Commun. 42 (1971) 340-5.
  Organism
Homo sapiens [GN:hsa]
Reference
2  [PMID:30407]
  Authors
Rome LH, Garvin AJ, Neufeld EF.
  Title
Human kidney alpha-L-iduronidase: purification and characterization.
  Journal
Arch. Biochem. Biophys. 189 (1978) 344-53.
  Organism
Homo sapiens [GN:hsa]
Reference
3
  Authors
Srivastava, R.M., Hudson, N., Seymour, F.R. and Weissman, B.
  Title
Preparation of (aryl alpha-L-idopyranosid)uronic acids.
  Journal
Carbohydr. Res. 60 (1978) 315-326.
Other DBs
ExplorEnz - The Enzyme Database: 
IUBMB Enzyme Nomenclature: 
ExPASy - ENZYME nomenclature database: 
BRENDA, the Enzyme Database: 
CAS: 
9073-56-7

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