KEGG   Homo sapiens (human): 1962Help
Entry
1962              CDS       T01001                                 

Gene name
EHHADH, ECHD, L-PBE, LBFP, LBP, PBFE
Definition
enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase (EC:1.1.1.35 5.3.3.8 4.2.1.17)
Orthology
K07514  
enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
Organism
hsa  Homo sapiens (human)
Pathway
Fatty acid metabolism
Valine, leucine and isoleucine degradation
Lysine degradation
Tryptophan metabolism
beta-Alanine metabolism
Propanoate metabolism
Butanoate metabolism
Metabolic pathways
PPAR signaling pathway
Peroxisome
Module
Malonate semialdehyde pathway, propanoyl-CoA => Acetyl-CoA
Lysine degradation, lysine => saccharopine => acetoacetyl-CoA
beta-Oxidation
Class
Metabolism; Carbohydrate metabolism; Propanoate metabolism [PATH:hsa00640]
Metabolism; Carbohydrate metabolism; Butanoate metabolism [PATH:hsa00650]
Metabolism; Lipid metabolism; Fatty acid metabolism [PATH:hsa00071]
Metabolism; Amino acid metabolism; Valine, leucine and isoleucine degradation [PATH:hsa00280]
Metabolism; Amino acid metabolism; Lysine degradation [PATH:hsa00310]
Metabolism; Amino acid metabolism; Tryptophan metabolism [PATH:hsa00380]
Metabolism; Metabolism of other amino acids; beta-Alanine metabolism [PATH:hsa00410]
Cellular Processes; Transport and catabolism; Peroxisome [PATH:hsa04146]
Organismal Systems; Endocrine system; PPAR signaling pathway [PATH:hsa03320]
BRITE hierarchy
SSDB OrthologParalogGFIT
Motif Motif
Other DBs
NCBI-GI: 
NCBI-GeneID: 
OMIM: 
HGNC: 
HPRD: 
Ensembl: 
Vega: 
UniProt: 
Position
3q26.3-q28
AA seq 627 aa AA seqDB search
MAFGGGLELALGCHYRIAHAEAQVGLPEVTLGLLPGARGTQLLPRLTGVPAALDLITSGR
RILADEALKLGILDKVVNSDPVEEAIRFAQRVSDQPLESRRLCNKPIQSLPNMDSIFSEA
LLKMRRQHPGCLAQEACVRAVQAAVQYPYEVGIKKEEELFLYLLQSGQARALQYAFFAER
KANKWSTPSGASWKTASARPVSSVGVVGLGTMGRGIVISFARARIPVIAVDSDKNQLATA
NKMITSVLEKEASKMQQSGHPWSGPKPRLTSSVKELGGVDLVIEAVFEEMSLKKQVFAEL
SAVCKPEAFLCTNTSALDVDEIASSTDRPHLVIGTHFFSPAHVMKLLEVIPSQYSSPTTI
ATVMNLSKKIKKIGVVVGNCFGFVGNRMLNPYYNQAYFLLEEGSKPEEVDQVLEEFGFKM
GPFRVSDLAGLDVGWKSRKGQGLTGPTLLPGTPARKRGNRRYCPIPDVLCELGRFGQKTG
KGWYQYDKPLGRIHKPDPWLSKFLSRYRKTHHIEPRTISQDEILERCLYSLINEAFRILG
EGIAASPEHIDVVYLHGYGWPRHKGGPMFYASTVGLPTVLEKLQKYYRQNPDIPQLEPSD
YLKKLASQGNPPLKEWQSLAGSPSSKL
NT seq 1884 nt NT seq  +upstreamnt  +downstreamnt
atggctttcggagggggactagagctggccctgggctgtcactataggattgcccacgca
gaggctcaagttggcttaccagaagttacactgggacttctccctggtgcaagaggaacc
cagcttctccccagactcactggagttcctgctgcacttgacttaattacctcaggaaga
cgtattttagcagatgaagcactcaagctgggcattctagataaagttgtaaactcagac
ccggttgaagaagcaatcagatttgctcagagagtttcagatcaacctctagaatcccgt
agactctgcaacaagccaattcagagcttgcccaacatggacagcatttttagtgaggcc
ctcttgaagatgcggaggcagcaccctgggtgtcttgcacaggaggcttgtgtccgtgca
gtccaggctgctgtgcagtatccctatgaagtgggcatcaagaaggaggaggagctgttt
ctatatcttttgcaatcagggcaggctagagccctgcaatatgctttcttcgctgaaagg
aaagcaaataagtggtcaactccctccggagcatcgtggaaaacagcatcagcgcggcct
gtctcctcagttggtgttgttggcttgggaacaatgggccgaggcattgtcatttctttt
gcaagggccaggattcctgtgattgctgtagactcggacaaaaaccagctagcaactgca
aacaagatgataacctctgtcttggaaaaagaagcctccaaaatgcaacagagcggccac
ccttggtcaggaccaaaacccaggttaacttcatctgtgaaggagcttggtggtgtagat
ttagtcattgaagcagtatttgaggaaatgagcctgaagaagcaggtctttgctgaactc
tcagctgtgtgcaaaccagaagcatttttgtgcactaatacttcagccctggatgttgat
gagattgcttcttccactgatcgtcctcacttggtcattggcacccacttcttttcgcca
gctcatgtcatgaagttgttagaggttattcccagccaatactcttcccccactaccatt
gccactgttatgaacttatcaaaaaagattaaaaagattggagtcgttgtaggcaactgt
tttggatttgtggggaatcgaatgttgaatccttactacaatcaggcatatttcttgtta
gaagaaggcagcaaaccagaggaggtagatcaggtgctggaagagtttggttttaaaatg
ggaccttttagagtgtctgatcttgctgggttggatgtgggctggaaatctagaaagggg
caaggtcttactggacctacattgcttccaggaactcctgcccgaaaaaggggtaatagg
aggtactgcccaattcctgatgtgctctgtgaattaggacgatttggccagaagacaggt
aagggttggtatcaatatgacaagccattgggtaggattcacaaacctgatccctggctt
tccaaattcctatcacggtatagaaaaacccatcacattgaaccacgtaccattagccag
gatgagatccttgaacgctgcttatattcacttatcaatgaagcattccgtatcttggga
gaagggatagctgctagcccagagcacattgatgttgtctatttacatggatatggatgg
ccaaggcacaagggcgggcccatgttctatgcttccacagttgggttgcccacagttcta
gagaaattgcagaaatattacaggcagaaccctgatattccccaactggagccaagtgac
tatctaaaaaaactggcttctcagggaaaccctcccctgaaagaatggcaaagcttggca
ggctcccctagcagtaaattgtga

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