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Entry
map00280                    Pathway                                

Name
Valine, leucine and isoleucine degradation
Class
Metabolism; Amino acid metabolism
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Valine, leucine and isoleucine degradation
map00280

All organismsOrtholog table
Module
M00036  
Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:map00280]
Disease
H00172  
Maple syrup urine disease (MSUD)
H00173  
Isovaleric acidemia (IVA)
H00174  
Methylmalonic aciduria (MMA)
H00175  
Propionic acidemia
H00179  
3-Hydroxy-3-methylglutaryl-CoA lyase deficiency
H00181  
3-Methylcrotonylglycinuria
H00525  
Disorders of fatty-acid oxidation
H00754  
3-Methylglutaconic aciduria (MGCA)
H00925  
2-Methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiency
H01076  
Alpha-methylacetoacetic aciduria
H01121  
Succinyl CoA:3-oxoacid CoA transferase (SCOT) deficiency
H01123  
HMG-CoA synthase (HMGCS) deficiency
H01279  
Isobutyryl-CoA dehydrogenase (IBD) deficiency
H01349  
Methacrylic aciduria
H01364  
3-Hydroxyacyl-CoA dehydrogenase deficiency
H01400  
Secondary hyperammonemia
Other DBs
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