ORTHOLOGY: K03995
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Entry
K03995 KO
Symbol
C6
Name
complement component 6
Pathway
map04610
Complement and coagulation cascades
map04810
Regulation of actin cytoskeleton
map05020
Prion disease
map05171
Coronavirus disease - COVID-19
map05322
Systemic lupus erythematosus
Disease
H00103
Late complement pathway defects
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09140 Cellular Processes
09142 Cell motility
04810 Regulation of actin cytoskeleton
K03995 C6; complement component 6
09150 Organismal Systems
09151 Immune system
04610 Complement and coagulation cascades
K03995 C6; complement component 6
09160 Human Diseases
09172 Infectious disease: viral
05171 Coronavirus disease - COVID-19
K03995 C6; complement component 6
09163 Immune disease
05322 Systemic lupus erythematosus
K03995 C6; complement component 6
09164 Neurodegenerative disease
05020 Prion disease
K03995 C6; complement component 6
BRITE hierarchy
Genes
HSA:
729
(C6)
PTR:
449612
(C6)
PPS:
100978093
(C6)
GGO:
101148425
(C6)
PON:
100447541
(C6)
PPYG:
129037096
(C6)
NLE:
100598505
(C6)
HMH:
116456613
(C6)
SSYN:
129464479
(C6)
MCC:
696266
(C6)
MCF:
102116032
(C6)
MTHB:
126956469
MNI:
105487447
(C6)
CSAB:
103215186
(C6)
CATY:
105583474
(C6)
PANU:
101017836
(C6)
TGE:
112626163
(C6)
MLEU:
105529268
(C6)
RRO:
104676863
(C6)
RBB:
108544739
(C6)
TFN:
117065060
(C6)
PTEH:
111545574
(C6)
CANG:
105513531
(C6)
CJC:
100408852
(C6)
SBQ:
101028369
(C6)
CIMI:
108307691
(C6)
ANAN:
105722418
(C6)
CSYR:
103272410
(C6)
MMUR:
105878388
(C6)
LCAT:
123648659
(C6)
PCOQ:
105814561
(C6)
OGA:
100965204
(C6)
MMU:
12274
(C6)
MCAL:
110310600
(C6)
MPAH:
110329165
(C6)
RNO:
24237
(C6)
MCOC:
116083233
(C6)
ANU:
117724000
(C6)
ASYL:
127667127
(C6)
MUN:
110557743
(C6)
CGE:
100766699
(C6)
MAUA:
101829672
(C6)
PROB:
127220605
(C6)
PLEU:
114697334
(C6)
MORG:
121433003
(C6)
MFOT:
126499661
AAMP:
119810709
(C6)
NGI:
103741375
(C6)
HGL:
101719948
(C6)
CPOC:
100733974
(C6)
CCAN:
109680205
DORD:
105987300
(C6)
DSP:
122116949
(C6)
DMER:
138840754
(C6)
PLOP:
125367564
(C6)
NCAR:
124987052
MMMA:
107146395
(C6)
ITI:
101971417
(C6)
OCU:
100359210
OPI:
101522789
(C6)
TUP:
102477570
(C6)
GVR:
103597654
(C6)
CFA:
479348
(C6)
CLUD:
112652833
(C6)
VVP:
112933547
(C6)
VLG:
121487626
(C6)
NPO:
129509854
(C6)
AML:
100469180
(C6)
UMR:
103664673
(C6)
UAH:
113260935
(C6)
UAR:
123785513
(C6)
ELK:
111141090
LLV:
125100733
MPUF:
101692941
(C6)
MNP:
132027499
(C6)
MLK:
131831699
(C6)
NVS:
122902234
(C6)
ORO:
101368952
(C6)
EJU:
114204832
(C6)
ZCA:
113929082
(C6)
MLX:
118006357
118006570
NSU:
110586301
(C6)
LWW:
102749704
FCA:
101095155
(C6)
PYU:
121044119
(C6)
PCOO:
112861081
(C6)
PBG:
122494240
(C6)
PVIV:
125168604
(C6)
LRUF:
124507484
LGF:
123577259
(C6)
AJU:
106970902
PTG:
102968337
(C6)
PPAD:
109275850
(C6)
PUC:
125934622
PLEZ:
122201900
(C6)
HHV:
120239772
(C6)
BTA:
507749
(C6)
BOM:
102267472
(C6)
BIU:
109574981
(C6)
BBUB:
102408738
(C6)
BBIS:
104998522
(C6)
CHX:
102179521
(C6)
OAS:
101102674
(C6)
BTAX:
128066200
(C6)
CSUM:
138094374
(C6)
ODA:
120879422
(C6)
CCAD:
122454588
(C6)
MREE:
136146606
(C6)
OVR:
110143430
(C6)
MBEZ:
129553056
(C6)
SSC:
100037952
(C6)
CFR:
102511198
(C6)
CBAI:
105070840
(C6)
CDK:
105106962
(C6)
VPC:
102536433
(C6)
BACU:
103017983
(C6)
BMUS:
118892342
(C6)
LVE:
103073477
(C6)
OOR:
101286425
(C6)
LALB:
132518029
(C6)
GMF:
115866436
(C6)
DDP:
132423609
(C6)
DLE:
111187127
(C6)
PCAD:
102992965
(C6)
PSIU:
116751364
(C6)
PPHC:
136120555
(C6)
NASI:
112396577
(C6)
ECB:
100065952
(C6)
EPZ:
103562165
(C6)
EAI:
106847872
(C6)
MYB:
102250460
(C6)
MYD:
102760692
(C6)
MMYO:
118656910
(C6)
MLF:
102440901
(C6)
MDT:
132233729
(C6)
MYUM:
139008004
(C6)
PKL:
118703415
(C6)
EFUS:
103298827
(C6)
MNA:
107545944
(C6)
DRO:
112321121
(C6)
SHON:
118998807
(C6)
AJM:
119044248
(C6)
PDIC:
114506512
(C6)
PHAS:
123824601
(C6)
MMF:
118641548
(C6)
PPAM:
129079010
(C6)
HAI:
109374586
(C6)
RFQ:
117025221
(C6)
PALE:
102887523
(C6)
PGIG:
120586156
(C6)
PVP:
105299092
(C6)
RAY:
107512444
(C6)
MJV:
108403861
(C6)
TOD:
119260536
(C6)
SARA:
101551204
(C6)
SFUM:
130021328
(C6)
SETR:
125999858
(C6)
LAV:
100668994
(C6)
TMU:
101352489
ETF:
101654690
(C6)
DNM:
101412534
(C6)
MDO:
100018236
(C6)
GAS:
123237296
(C6)
SHR:
100928427
(C6)
AFZ:
127544428
PCW:
110215122
(C6)
TVP:
118850144
(C6)
PBRV:
138167241
(C6)
MLAO:
141503289
(C6)
OAA:
100075246
(C6)
TACU:
119925784
(C6)
GGA:
431585
(C6)
PCOC:
116236410
(C6)
MGP:
104914855
(C6)
CJO:
107305972
(C6)
TPAI:
128074466
(C6)
LMUT:
125686653
(C6)
NMEL:
110390182
(C6)
APLA:
101800292
(C6)
ACYG:
106036293
(C6)
CATA:
118257783
(C6)
AFUL:
116501076
(C6)
TGU:
100219414
(C6)
LSR:
110482287
(C6)
SCAN:
103821079
(C6)
PMOA:
120502444
(C6)
OTC:
121334112
(C6)
PRUF:
121356206
(C6)
ATRC:
139589252
(C6)
GFR:
102039194
(C6)
FAB:
101809016
(C6)
OMA:
130265207
(C6)
PHI:
102111095
(C6)
PMAJ:
107198376
(C6)
CCAE:
111941369
(C6)
CCW:
104686628
(C6)
CBRC:
103612935
(C6)
ACOE:
138103365
(C6)
ETL:
114063714
(C6)
ZAB:
102068154
(C6)
ZLE:
135459728
(C6)
ACHL:
103811012
(C6)
SVG:
106852737
(C6)
MMEA:
130572792
(C6)
HRT:
120765576
(C6)
SATI:
136374579
(C6)
CCIC:
134056727
(C6)
FPG:
101915168
(C6)
FCH:
102054544
(C6)
CCRI:
104158213
(C6)
NNT:
104406502
(C6)
SHAB:
115601372
(C6)
ACUN:
113489704
(C6)
TALA:
104357658
(C6)
ACHC:
115336744
(C6)
HALD:
104322074
(C6)
HLE:
104843073
(C6)
AGEN:
126035811
HHAR:
128136032
128137097
(C6)
GCL:
127027657
CSTI:
104553316
(C6)
LDI:
104349319
(C6)
MNB:
103781325
(C6)
DPUB:
104299686
(C6)
PPUS:
135193254
(C6)
AVIT:
104267655
(C6)
BRHI:
104493245
(C6)
EGZ:
104133866
(C6)
NNI:
104016186
(C6)
PCRI:
104024009
(C6)
PCAO:
104039401
(C6)
PADL:
103917435
(C6)
AFOR:
103895033
(C6)
FGA:
104076803
(C6)
GSTE:
104256665
(C6)
CBOY:
140650729
(C6)
CLV:
102088331
(C6)
CNIC:
136002341
(C6)
MUI:
104546544
(C6)
PGUU:
104457813
(C6)
PLET:
104618420
(C6)
EHS:
104511211
(C6)
CMAC:
104487010
(C6)
CUCA:
104059659
(C6)
TEO:
104370003
(C6)
BREG:
104640412
(C6)
OHA:
104337763
(C6)
ACAR:
104532549
(C6)
CPEA:
104398613
(C6)
CVF:
104294970
(C6)
RTD:
128902915
(C6)
CRID:
134508713
(C6)
AAM:
106499514
(C6)
AROW:
112962186
(C6)
NPD:
112945989
(C6)
TGT:
104564680
(C6)
DNE:
112983586
(C6)
SCAM:
104147805
(C6)
ASN:
102376310
102376566
AMJ:
102571057
102571296
CPOO:
109307865
109307866
GGN:
109297861
109297863
PSS:
102445298
(C6)
CMY:
102943577
(C6)
CCAY:
125637177
(C6)
DCC:
119855946
(C6)
CPIC:
101933919
(C6)
TST:
117879170
(C6)
CABI:
116837854
(C6)
MRV:
120408576
(C6)
ACS:
100566857
100567051
ASAO:
132766951
132766952
PVT:
110073919
(C6)
SUND:
121921100
121922431
(C6)
PBI:
103059215
103059458
112542663
PMUR:
107291123
107291130
(C6)
CTIG:
120302842
(C6)
120302843
TSR:
106540086
106540087
106546796
PGUT:
117679148
117679149
PCAE:
139311479
139313332
APRI:
131190742
131193270
(C6)
PTEX:
113446430
113446438
NSS:
113411399
113411400
VKO:
123031499
123031636
PMUA:
114606727
114606764
PRAF:
128423085
128423086
ZVI:
118077102
118077204
HCG:
128342462
(C6)
GJA:
107108807
107108813
STOW:
125436859
125437156
EMC:
129334250
129334252
XLA:
379126
(c6.2.L)
432346
(c6.1.L)
XTR:
100485342
(c6.1)
448630
(c6.2)
NPR:
108796897
RTEM:
120927857
(C6)
ACAT:
141132828
(C6)
BBUF:
120992149
(C6)
BGAR:
122925183
(C6)
DTC:
141075564
(C6)
PWL:
138283476
138283501
MUO:
115462961
(C6)
GSH:
117366434
(C6)
DRE:
393611
(c6.2)
798694
(c6.1)
SRX:
107706506
107708495
SANH:
107681131
SGH:
107589278
(c6)
CCAR:
109051643
(c6)
CAUA:
113038108
113039134
CGIB:
127985604
PTET:
122326959
(c6)
LROH:
127152155
(c6)
GRF:
141292038
(c6.2)
OMC:
131528354
(c6)
PPRM:
120490588
(c6)
MAMB:
125253096
(c6)
CIDE:
127503671
CERY:
137013345
(c6.2)
MASI:
127428662
TROS:
130570397
(c6)
TDW:
130407837
(c6)
MANU:
129423318
(c6.2)
PDAB:
135776792
(c6.2)
IPU:
108279068
IFU:
128622731
(c6)
PHYP:
113543129
(c6)
SMEO:
124398222
(c6)
TFD:
113638591
(c6)
TVC:
132860175
(c6)
CGAR:
128507745
(c6)
NGRA:
132894747
(c6)
TRN:
134330310
AMEX:
103037650
(c6)
CMAO:
118820517
(c6)
EEE:
113567938
(c6)
CHAR:
105890274
(c6)
SPIL:
134101513
(c6)
TRU:
101070280
(c6)
TFS:
130517365
(c6)
LCO:
104938603
(c6)
NCC:
104947463
(c6)
TBEN:
117478892
(c6)
CGOB:
115016532
(c6)
PGEO:
117456513
(c6.2)
GACU:
117542910
(c6)
EMAC:
134868965
(c6)
ELY:
117269593
(c6)
EFO:
125906358
(c6)
PLEP:
121959752
(c6)
SLUC:
116034816
(c6)
ECRA:
117958882
(c6)
ESP:
116704133
(c6)
PFLV:
114570943
(c6)
GAT:
120831901
(c6)
PPUG:
119226677
(c6)
AFB:
129102333
(c6)
CLUM:
117740631
(c6)
PSWI:
130205115
(c6)
CANA:
137783851
(c6.2)
CVE:
137888901
(c6.2)
MSAM:
119915106
SCHU:
122865542
(c6)
CUD:
121524913
(c6)
SPUL:
138605119
(c6.2)
LMIX:
132992205
(c6)
ALAT:
119029758
(c6)
ASTR:
137608098
(c6.2)
MZE:
101465400
(c6)
ONL:
100705566
(c6)
OAU:
116324888
(c6)
OLA:
101156343
(c6)
OML:
112139833
CSAI:
133455456
(c6)
XMA:
102233279
(c6)
XCO:
114149771
(c6)
XHE:
116724484
(c6)
PRET:
103474025
(c6)
PFOR:
103130712
(c6)
103130715
PLAI:
106939813
(c6)
106963533
PMEI:
106926770
(c6)
GAF:
122846991
(c6)
PPRL:
129352015
129353079
(c6)
CVG:
107097071
(c6)
CTUL:
119780572
(c6)
GMU:
124872356
(c6)
NFU:
107375025
(c6)
KMR:
108228854
(c6)
ALIM:
106530356
(c6)
NWH:
119424455
(c6)
AOCE:
111568618
(c6)
EJA:
138205170
(c6.2)
BFRE:
138625316
(c6.2)
MCEP:
124996918
(c6)
CSEM:
103389279
(c6)
POV:
109646969
(c6)
SSEN:
122758464
(c6)
SSOE:
131446265
(c6)
HHIP:
117772209
(c6)
HSP:
118126032
(c6)
PPLT:
128425169
(c6)
SMAU:
118284462
(c6)
LCF:
108901113
SDU:
111221120
(c6)
SLAL:
111669341
(c6)
XGL:
120806155
(c6)
HCQ:
109523967
(c6)
SSCV:
125979435
(c6.2)
SBIA:
133491040
(c6)
PEE:
133413341
(c6)
PTAO:
133465132
(c6)
BPEC:
110159912
(c6)
ENY:
140367021
MALB:
109973644
(c6)
BSPL:
114866553
(c6)
SJO:
128380016
(c6)
SSCO:
133995480
(c6)
GMH:
115541559
(c6)
SASA:
100380290
(c6)
STRU:
115204031
(c6)
OTW:
112230951
OMY:
100136644
(c6)
OGO:
124006991
ONE:
115101131
OKI:
109874016
(c6)
OKE:
118385344
(c6)
OMM:
135544502
(c6)
OCLA:
139388300
SALP:
111963984
(c6)
SNH:
120021224
CCLU:
121541634
ELS:
105015063
(c6)
OEP:
134033479
SFM:
108932022
(c6)
PKI:
111851443
(c6)
AANG:
118212294
(c6)
AROT:
135239986
(c6)
CCOG:
133141429
(c6)
LOC:
102692262
(c6)
PSPA:
121300557
(c6)
ARUT:
117403999
117963294
PSEX:
120532548
(c6)
LCM:
102356825
LERI:
129693745
HAKA:
140728903
BFO:
118408031
118410541
118415174
118422307
118431870
BBEL:
109476028
109487442
CIN:
100176718
100179109
100180005
100183313
100184927
100184973
100185682
100186935
113474037
SCLV:
120341657
120348019
» show all
Taxonomy
UniProt
Reference
PMID:
2808363
Authors
Haefliger JA, Tschopp J, Vial N, Jenne DE
Title
Complete primary structure and functional characterization of the sixth component of the human complement system. Identification of the C5b-binding domain in complement C6.
Journal
J Biol Chem 264:18041-51 (1989)
Sequence
[hsa:
729
]
All links
Gene (674)
MGENES (151)
RefGene (517)
OC (6)
All databases (674)
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