Entry
Symbol
COQ2
Name
4-hydroxybenzoate polyprenyltransferase [EC:
2.5.1.39 ]
Pathway
map00130 Ubiquinone and other terpenoid-quinone biosynthesis
map01110 Biosynthesis of secondary metabolites
Module
M00128 Ubiquinone biosynthesis, eukaryotes, 4-hydroxybenzoate + polyprenyl-PP => ubiquinol
Reaction
R05000 polyisopentenylpyrolinate:4-hydroxybenzoate nonaprenyltransferase
R05616 all-trans-hexaprenyl diphosphate:4-hydroxybenzoate hexaprenyltransferase
R07273 solanesyl-diphosphate:4-hydroxybenzoate nonaprenyltransferase
Disease
H00999 Coenzyme Q10 deficiency
H01614 Multiple system atrophy
Brite
KEGG Orthology (KO) [BR:ko00001 ]
09100 Metabolism
09108 Metabolism of cofactors and vitamins
00130 Ubiquinone and other terpenoid-quinone biosynthesis
K06125 COQ2; 4-hydroxybenzoate polyprenyltransferase
09180 Brite Hierarchies
09181 Protein families: metabolism
01006 Prenyltransferases
K06125 COQ2; 4-hydroxybenzoate polyprenyltransferase
Enzymes [BR:ko01000 ]
2. Transferases
2.5 Transferring alkyl or aryl groups, other than methyl groups
2.5.1 Transferring alkyl or aryl groups, other than methyl groups (only sub-subclass identified to date)
2.5.1.39 4-hydroxybenzoate polyprenyltransferase
K06125 COQ2; 4-hydroxybenzoate polyprenyltransferase
Prenyltransferases [BR:ko01006 ]
Compound prenylation
4HB prenyltransferase
K06125 COQ2; 4-hydroxybenzoate polyprenyltransferase
BRITE hierarchy
Other DBs
Genes
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Taxonomy UniProt
Reference
Authors
Forsgren M, Attersand A, Lake S, Grunler J, Swiezewska E, Dallner G, Climent I
Title
Isolation and functional expression of human COQ2, a gene encoding a polyprenyl transferase involved in the synthesis of CoQ.
Journal
Sequence
Reference
Authors
Okada K, Ohara K, Yazaki K, Nozaki K, Uchida N, Kawamukai M, Nojiri H, Yamane H
Title
The AtPPT1 gene encoding 4-hydroxybenzoate polyprenyl diphosphate transferase in ubiquinone biosynthesis is required for embryo development in Arabidopsis thaliana.
Journal
Sequence