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Mitochondrial Biogenesis - Apis mellifera (honey bee)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
C Mitochondrial respiratory chain complex III
C Cytochrome c oxidase
C F-type ATPase
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 725579 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 102654682 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 725496 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 726530 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 406098 IF-2mt; translation initiation factor 2 K02519 infB; translation initiation factor IF-2
D 408352 elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 408328 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 411351 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 408831 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 102654768 transcription termination factor 5, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 410339 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 102655778 translation factor GUF1 homolog, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 100578852 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 727419 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 552780 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 100576378 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 102655617 ribonuclease P protein subunit p20 isoform X2 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 100578399 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 551953 uncharacterized protein LOC551953 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 100577673 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 725274 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 726590 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 100576610 mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 100577377 uncharacterized protein LOC100577377 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 102656199 uncharacterized protein LOC102656199 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 102655127 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 552071 pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 113218580 protein PTCD3 homolog, mitochondrial-like isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 726077 putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 726341 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 552015 putative ATPase N2B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 551613 ATP-dependent RNA helicase SUV3 homolog, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 408355 endoribonuclease LACTB2 isoform X2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 406075 Ant; ADP/ATP translocase K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 107964398 ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 552801 mitoferrin-1 isoform X2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 100577644 uncharacterized protein LOC100577644 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 726385 GTPase Era, mitochondrial K03595 era; GTPase
D 552025 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 413909 tyrosine--tRNA ligase, cytoplasmic isoform X2 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 412282 leucine--tRNA ligase, cytoplasmic isoform X2 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 552532 probable leucine--tRNA ligase, mitochondrial isoform X2 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 725136 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 408392 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 552307 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 550903 arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 413878 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 102654365 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 113218895 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 551561 poly(A) RNA polymerase, mitochondrial isoform X1 K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 725486 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 102655141 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 413531 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 102655259 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 100577533 mitochondrial RNA pseudouridine synthase rpusd4 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 411554 RCC1-like G exchanging factor-like protein isoform X2 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 725822 RING finger protein PFF0165c K23496 NGRN; neugrin
D 551083 mitochondrial mRNA pseudouridine synthase Trub2 isoform X2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 100577803 uncharacterized protein LOC100577803 K18190 FASTKD2; FAST kinase domain-containing protein 2
D 724155 probable peptide chain release factor C12orf65, mitochondrial K23498 COXPD7; peptide chain release factor
D 724742 probable methyltransferase-like protein 15 homolog isoform X2 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 551296 UPF0160 protein MYG1, mitochondrial isoform X1 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 102654345 uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 411763 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 100576960 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 726041 DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 551715 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 725107 mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 100578653 twinkle protein, mitochondrial isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 410410 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 727210 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 551329 ATPase family AAA domain-containing protein 3A homolog K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 725244 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 410620 heat shock protein Hsp70Ab-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 409418 Hsc70-4; heat shock protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
B Outer membrane
C Transporter outer membrane (TOM) complex
D 408284 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 102655740 mitochondrial import receptor subunit TOM40 homolog 1-like K11518 TOM40; mitochondrial import receptor subunit TOM40
D 726081 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 409500 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 413845 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 727327 Tom7; translocase of outer membrane 7 K17771 TOM7; mitochondrial import receptor subunit TOM7
C TOB/SAM complex
D 413450 sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 551325 voltage-dependent anion-selective channel K15040 VDAC2; voltage-dependent anion channel protein 2
C ERMES complex
C Other outer membrane factor
D 551902 metaxin-1 K17776 MTX; metaxin
D 726364 metaxin-2 isoform X2 K17776 MTX; metaxin
D 724919 mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 100577026 mitochondrial amidoxime-reducing component 1 isoform X3 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 725240 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 726061 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 726131 mitochondrial import inner membrane translocase subunit Tim10B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 726498 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 725705 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 726337 mitochondrial intermembrane space import and assembly protein 40-B K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 724451 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 726902 MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10
D 408548 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 724706 trichohyalin isoform X2 K17785 IMMT; MICOS complex subunit MIC60
D 725253 MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 551742 MICOS complex subunit MIC25 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 552009 MICOS complex subunit MIC27 isoform X2 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 726902 MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10
D 408548 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 724706 trichohyalin isoform X2 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 100576422 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 552727 mitochondrial import inner membrane translocase subunit Tim23 isoform X1 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 413799 mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 113219103 probable mitochondrial import inner membrane translocase subunit Tim17 1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 726569 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 408569 mitochondrial import inner membrane translocase subunit TIM50-C K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 725974 calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 552081 calcium uptake protein 1 homolog, mitochondrial isoform X2 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 102654379 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
C Other inner membrane factors
D 551843 mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 102654681 mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 551426 uncharacterized protein LOC551426 K18157 TMEM126A; transmembrane protein 126A
D 411677 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 413186 mitochondrial pyruvate carrier 3 K22139 MPC2; mitochondrial pyruvate carrier 2
D 724499 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2
D 100578540 coiled-coil-helix-coiled-coil-helix domain-containing protein 2-like isoform X2 K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 412409 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 408605 Hsc70-5; heat shock protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 551769 grpE protein homolog, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 726653 mitochondrial import inner membrane translocase subunit TIM14 isoform X2 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 102655673 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 552175 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 100579052 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 410022 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 412784 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 409384 heat shock protein 60A K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 552531 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 411359 protein tumorous imaginal discs, mitochondrial isoform X2 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 102654261 uncharacterized protein C24H6.02c K17808 ZIM17; mitochondrial protein import protein ZIM17
D 551510 uncharacterized protein LOC551510 isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 410023 persulfide dioxygenase ETHE1, mitochondrial isoform X2 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 551574 polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 409401 cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 411351 elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 408831 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 100578927 transcriptional repressor protein YY1 isoform X2 K09201 YY; transcription factor YY
D 412357 GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 102654682 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 411828 DNA-binding protein P3A2 isoform X1 K11831 NRF1; nuclear respiratory factor 1
C Coactivators
D 727127 NK-tumor recognition protein isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 408676 CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 726280 histone acetyltransferase p300-like isoform X3 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 410039 cysteine desulfurase, mitochondrial isoform X2 K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 409130 uncharacterized protein LOC409130 K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 102655452 protein bcn92 K22069 LYRM4; LYR motif-containing protein 4
D 552635 frataxin homolog, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 413746 adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial
D 552105 adrenodoxin-like protein, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 100578109 NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 408605 Hsc70-5; heat shock protein cognate 5 K04043 dnaK; molecular chaperone DnaK
D 100577992 iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB
D 724587 nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 552835 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 552616 iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 724467 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 724700 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 412366 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 551959 uncharacterized protein LOC551959 K22066 BOLA1; BolA-like protein 1
D 727306 bolA-like protein 3 isoform X1 K22075 BOLA3; BolA-like protein 3
D 408539 sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 550915 sideroflexin-2 K23501 SFXN2; sideroflexin-2
C Other regulator of mitochondrial biogenesis
D 550695 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 412569 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial isoform X2 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 551738 F-box/LRR-repeat protein 4 isoform X2 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 551801 host cell factor 1 isoform X2 K14966 HCFC1; host cell factor 1
D 726358 huntingtin isoform X1 K04533 HD; huntingtin
D 409577 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 409459 lon protease homolog, mitochondrial isoform X2 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 411917 NAD-dependent protein deacetylase sirtuin-1 isoform X2 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 725516 protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 725210 protein UXT homolog K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 726255 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 100578218 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 102656215 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 102653955 protein NDUFAF4 homolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 100576544 arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 726383 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 551492 protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 726612 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 102654465 acyl-CoA dehydrogenase family member 9, mitochondrial-like K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 551442 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 552066 FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 411304 reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 551545 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 100577982 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 113218840 succinate dehydrogenase assembly factor 2, mitochondrial-like K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 552253 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 725675 tetratricopeptide repeat protein 19 homolog, mitochondrial-like K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 726662 complex III assembly factor LYRM7 isoform X2 K18170 LYRM7; complex III assembly factor LYRM7
D 726341 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 100576195 protein ccsmst1 isoform X2 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 107965597 uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
C Complex-IV assembly factors
D 552802 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 100576945 uncharacterized protein LOC100576945 K18173 COA1; cytochrome c oxidase assembly factor 1
D 725170 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 552586 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7
D 409103 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 409420 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 410617 cytochrome c oxidase assembly protein COX15 homolog isoform X3 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 726259 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 727026 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 725011 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18
D 102655540 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 102654007 uncharacterized protein LOC102654007 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 100577377 uncharacterized protein LOC100577377 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 102656199 uncharacterized protein LOC102656199 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 726644 Pet117; cytochrome c oxidase assembly factor-like K18188 PET117; protein PET117
D 408349 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 413781 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 726314 protein SCO2 homolog, mitochondrial K07152 SCO1; protein SCO1
D 100578853 uncharacterized protein LOC100578853 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 102654090 apoptogenic protein 1, mitochondrial K23506 APOPT1; apoptogenic protein 1
D 100578811 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 113219283 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 413714 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 725040 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 113218630 up-regulated during skeletal muscle growth protein 5-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 410263 transmembrane GTPase Marf isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 413438 dynamin-like 120 kDa protein, mitochondrial isoform X2 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 552659 optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 100578534 TP53-regulated inhibitor of apoptosis 1 isoform X2 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 412194 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 411472 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 551255 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 550834 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 409308 small ubiquitin-related modifier K12160 SUMO; small ubiquitin-related modifier
D 551100 endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1
D 726264 mitochondrial carrier homolog 2 isoform X2 K17885 MTCH; mitochondrial carrier
D 551864 transport and Golgi organization protein 11 K22076 MFF; mitochondrial fission factor
D 727254 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 410961 mitoguardin K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 406122 Arp1; actin related protein 1 K05692 ACTB_G1; actin beta/gamma 1
D 414027 N-alpha-acetyltransferase 20 isoform X1 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 413950 N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 408412 protein l(2)37Cc K17080 PHB1; prohibitin 1
D 551944 prohibitin-2 K17081 PHB2; prohibitin 2
C Retention of mitochondria
D 411472 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 726456 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
C Morphogenesis factors
D 727331 sorting nexin-25 K17887 SNX25; sorting nexin-25
D 725244 mitochondrial Rho GTPase isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 408548 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 724706 trichohyalin isoform X2 K17785 IMMT; MICOS complex subunit MIC60
D 724600 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 410856 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29
D 411723 E3 ubiquitin-protein ligase Nedd-4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 551622 protein misato K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 726497 autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 552315 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 552197 cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 410257 cysteine protease ATG4C isoform X3 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 551057 autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 408834 beclin-1-like protein isoform X2 K08334 BECN; beclin
D 726637 ubiquitin-like modifier-activating enzyme atg7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 725184 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 412115 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 726781 ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 113219359 autophagy protein 12-like isoform X1 K08336 ATG12; ubiquitin-like protein ATG12
D 412687 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 725024 autophagy-related protein 16 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 552201 WD repeat domain phosphoinositide-interacting protein 2 isoform X2 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 412975 E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 411585 E3 ubiquitin-protein ligase NRDP1 isoform X2 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 410511 protein CLEC16A homolog isoform X1 K19513 CLEC16A; protein CLEC16A
D 550929 serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 412194 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 408686 sequestosome-1 K14381 SQSTM1; sequestosome 1
D 100578919 tax1-binding protein 1 homolog isoform X1 K21347 TAX1BP1; Tax1-binding protein 1
D 727634 activating molecule in BECN1-regulated autophagy protein 1 isoform X2 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 551384 autophagy-related protein 13 homolog isoform X2 K08331 ATG13; autophagy-related protein 13
D 552571 serine/threonine-protein kinase unc-51 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 408358 RB1-inducible coiled-coil protein 1 isoform X3 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 411700 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG
D 408928 Hsp90; heat shock protein 90 K04079 HSP90A; molecular chaperone HtpG
D 724675 Cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 412866 E3 ubiquitin-protein ligase SMURF2 isoform X2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 412864 FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 409577 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 411870 microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 412224 tectonin beta-propeller repeat-containing protein isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 409941 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 552104 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 410570 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 113218716 protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024