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Mitochondrial Biogenesis - Boleophthalmus pectinirostris (great blue-spotted mudskipper)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D YP_004935131.1 NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D YP_004935132.1 NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D YP_004935138.1 NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D YP_004935140.1 NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D YP_004935139.1 NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D YP_004935141.1 NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D YP_004935142.1 NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D YP_004935143.1 cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D YP_004935133.1 cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D YP_004935134.1 cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D YP_004935137.1 cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D YP_004935135.1 ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D YP_004935136.1 ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 110174042 polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 110154265 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 110155388 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 110172981 tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 110166017 mtif2; LOW QUALITY PROTEIN: translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 110156142 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 110159119 elongation factor Ts, mitochondrial-like K02357 tsf; elongation factor Ts
D 110158709 elongation factor Ts, mitochondrial-like K02357 tsf; elongation factor Ts
D 110158237 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 110163584 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 110157490 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 110161151 mterf1; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 110161910 transcription termination factor 2, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 110165964 mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 110159216 transcription termination factor 4, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 110167471 mterf3; transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 110153806 translation factor GUF1, mitochondrial-like K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 110171651 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 110158819 pop4; ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 110163296 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 110174498 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 110163891 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 110175357 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 110168828 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 110163091 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 110173035 trmt10c; mitochondrial ribonuclease P protein 1 K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 110175804 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 110155606 kiaa0391; mitochondrial ribonuclease P protein 3 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 110159739 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 110159741 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 110172652 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 110167600 pentatricopeptide repeat-containing protein 1, mitochondrial-like K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 110157493 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 110156348 ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 110159555 dhx30; putative ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 110171176 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 110156334 lactation elevated protein 1-like K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 110156169 afg1l; lactation elevated protein 1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 110161796 atp23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 110175419 ATP-dependent RNA helicase SUPV3L1, mitochondrial-like K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 110175421 ATP-dependent RNA helicase SUPV3L1, mitochondrial-like K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 110155773 lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 110158852 ADP/ATP translocase 3-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 110158394 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 110165268 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 110157054 slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 110155968 mitoferrin-2-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 110169921 mitoferrin-1-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 110171843 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 110165123 eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 110167405 yars; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 110169422 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 110153970 lars; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 110171711 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 110170428 dars2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 110160908 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 110160940 glycine--tRNA ligase-like K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 110154269 rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 110156428 rars; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 110155568 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 110167616 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 110169857 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 110165527 mtpap; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 110173574 pde12; 2',5'-phosphodiesterase 12 isoform X1 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 110157190 mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 110165873 noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 110173072 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 110174788 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 110168711 RNA pseudouridylate synthase domain-containing protein 4-like K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 110161336 rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 110164862 ngrn; neugrin K23496 NGRN; neugrin
D 110168601 trub2; probable tRNA pseudouridine synthase 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 110168981 fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 110172506 cunh12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor
D 110155589 rmnd1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 110155409 G-rich sequence factor 1-like isoform X1 K24984 GRSF1; G-rich sequence factor 1
D 110172914 mettl15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 110171194 cunh12orf10; UPF0160 protein MYG1, mitochondrial isoform X1 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 110155660 cunh6orf203; uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 110165932 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 110166245 polg2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 110165266 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 110169241 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 110156977 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 110154341 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 110174822 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 110161739 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 110168699 atad3a; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 110168609 ubiquinol-cytochrome-c reductase complex assembly factor 2 isoform X1 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 110169153 dnaJ homolog subfamily A member 2-like K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 110175234 dnaja2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 110162521 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 110171385 mitochondrial Rho GTPase 1-A K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 110172568 mitochondrial Rho GTPase 1-A-like isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 110164814 heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110169090 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110169093 heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110167552 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110167569 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110167858 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110167859 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110167860 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110167861 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110167862 heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110171804 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110167641 heat shock 70 kDa protein 1 isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 110174386 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 110165358 aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 110174328 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 110158630 mitochondrial import receptor subunit TOM40B-like K11518 TOM40; mitochondrial import receptor subunit TOM40
D 110168926 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 110154719 tomm70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 110159689 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 110157097 tomm20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 110174919 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 110168611 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 110160731 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 110160321 sorting and assembly machinery component 50 homolog A-like K07277 SAM50; outer membrane protein insertion porin family
D 110167875 sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 110153977 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 110173602 vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 110164408 voltage-dependent anion-selective channel protein 2-like K15040 VDAC2; voltage-dependent anion channel protein 2
D 110172325 voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3
D 110171566 voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 110153134 mtx2; metaxin-2 K17776 MTX; metaxin
D 110157898 metaxin-1-like K17776 MTX; metaxin
D 110156741 mtx3; metaxin-3 K17776 MTX; metaxin
D 110165058 myo19; unconventional myosin-XIX K25838 MYO19; myosin XIX
D 110157527 mitochondrial amidoxime-reducing component 1-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 110159235 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 110175168 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 110158627 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 110162021 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 110158862 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 110160047 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 110171193 mitochondrial intermembrane space import and assembly protein 40-like isoform X1 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 110168397 mitochondrial intermembrane space import and assembly protein 40-B-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 110155778 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 110158032 minos1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 110168732 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 110155786 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
D 110174089 cunh19orf70; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 110174857 chchd3; MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 110169353 proline-rich extensin-like protein EPR1 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19
D 110158018 chchd6; MICOS complex subunit MIC25 K17564 CHCHD6; MICOS complex subunit MIC25
D 110175122 MICOS complex subunit MIC26-like K24625 APOO; MICOS complex subunit MIC26
D 110166932 MICOS complex subunit MIC26-like isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 110153804 uncharacterized protein LOC110153804 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 110158032 minos1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 110168732 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10
D 110155786 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 110165151 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 110164392 timm23; mitochondrial import inner membrane translocase subunit Tim23 isoform X1 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 110164817 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 110170231 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 110161015 timm21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 110156287 timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 110156991 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 110157263 micu1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 110169051 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 110165365 mcub; calcium uniporter regulatory subunit MCUb, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 110172596 essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial
D 110162272 smdt1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 110165625 mitochondrial calcium uniporter regulator 1-like K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 110171103 letm1; LETM1 and EF-hand domain-containing protein 1, mitochondrial isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 110167825 letm2; LETM1 domain-containing protein LETM2, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 110175500 immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 110155092 immp2l; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 110157656 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A
D 110175426 mpc1; mitochondrial pyruvate carrier 1 isoform X1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 110173114 mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 110167635 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 110160081 timm44; mitochondrial import inner membrane translocase subunit TIM44 isoform X1 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 110173496 mitochondrial import inner membrane translocase subunit TIM44-like K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 110164003 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 110164545 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 110160584 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
C Other matrix factors
D 110154475 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 110164440 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 110171875 mipep; LOW QUALITY PROTEIN: mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 110170534 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 110170595 hspe1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 110167443 dnaja3; dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 110168453 tamm41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 110157497 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 110168222 ethe1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 110160361 poldip2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 110165862 cyclic AMP-responsive element-binding protein 1-like K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 110170896 cyclic AMP-responsive element-binding protein 1-like K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 110163584 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 110157490 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 110171184 sp1; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 110155448 transcriptional repressor protein YY1-like K09201 YY; transcription factor YY
D 110168267 transcriptional repressor protein YY1-like isoform X1 K09201 YY; transcription factor YY
D 110170151 GA-binding protein subunit beta-2-like K09454 GABPB; GA-binding protein transcription factor, beta
D 110154265 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 110162502 nrf1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1
D 110166581 nfe2l2; nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
C Coactivators
D 110159306 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 110155788 peroxisome proliferator-activated receptor gamma coactivator 1-beta-like K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 110165179 peroxisome proliferator-activated receptor gamma coactivator-related protein 1-like isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 110157033 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 110174802 CREB-regulated transcription coactivator 1-like K15309 CRTC1; CREB-regulated transcription coactivator 1
D 110167998 crtc1; CREB-regulated transcription coactivator 1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 110159740 ep300; histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 110162399 LOW QUALITY PROTEIN: histone acetyltransferase p300-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 110169211 LOW QUALITY PROTEIN: CREB-binding protein-like K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 110166254 CREB-binding protein-like isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 110175547 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 110169897 iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 110163980 lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 110172504 fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 110173151 fdx1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 110172667 fdx1l; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 110155172 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 110164003 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 110155035 hscb; iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB
D 110158947 sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 110153272 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 110162056 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 110155633 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 110158804 iba57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 110169827 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 110164562 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 110168976 bola1; bolA-like protein 1 isoform X1 K22066 BOLA1; BolA-like protein 1
D 110175485 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 110157636 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 110164309 sideroflexin-1-like K23500 SFXN1_3; sideroflexin-1/3
D 110170863 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2
D 110162438 sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4
D 110157339 sideroflexin-5-like K23503 SFXN5; sideroflexin-5
D 110158988 sideroflexin-5-like K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 110159816 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 110165903 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 110166861 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 110172624 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 110169356 dhtkd1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 110171624 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 110170215 host cell factor 1-like K14966 HCFC1; host cell factor 1
D 110154468 host cell factor 1-like K14966 HCFC1; host cell factor 1
D 110161742 LOW QUALITY PROTEIN: host cell factor 2-like K27390 HCFC2; host cell factor 2
D 110161430 host cell factor 2-like K27390 HCFC2; host cell factor 2
D 110175726 htt; huntingtin K04533 HD; huntingtin
D 110165059 estrogen-related receptor gamma-like K08552 NR3B1; estrogen-related receptor alpha
D 110155531 esrrb; steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta
D 110153364 steroid hormone receptor ERR2-like K08553 NR3B2; estrogen-related receptor beta
D 110172944 esrrg; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma
D 110175171 estrogen-related receptor gamma-like isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 110169056 nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 110157325 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 110154939 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 110162805 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 110162160 sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 110153313 serac1; protein SERAC1 K23504 SERAC1; protein SERAC1
D 110158019 uxt; protein UXT K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 110171110 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 110167068 ndufaf2; mimitin, mitochondrial K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 110168725 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 110155549 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 110168501 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 110163864 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 110159672 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 110170790 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 110171125 acad9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 110153094 nubpl; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 110172209 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 110155621 rtn4ip1; reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 110175657 reticulon-4-interacting protein 1 homolog, mitochondrial-like K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 110153284 timmdc1; complex I assembly factor TIMMDC1, mitochondrial isoform X1 K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 110173063 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 110171371 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 110170955 ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 110157276 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 110171176 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 110168609 ubiquinol-cytochrome-c reductase complex assembly factor 2 isoform X1 K17682 MNF1; mitochondrial nucleoid factor 1
D 110172437 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 110159751 cunh16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 110157965 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 110160353 cunh12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 110165085 cunh7orf73; uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 110171796 cmc1; COX assembly mitochondrial protein homolog isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1
D 110175482 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 110168036 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 110172826 cytochrome c oxidase assembly factor 3 homolog, mitochondrial-like K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 110154197 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 110158645 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 110173186 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 110161879 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 110154860 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 110154254 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 110165454 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 110155834 cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 110157144 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 110156203 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 110160319 mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18
D 110173711 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 110166988 cytochrome c oxidase protein 20 homolog K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 110159739 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 110159741 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 110169684 pet100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 110173980 pet117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 110171965 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 110157414 surfeit locus protein 1 isoform X1 K14998 SURF1; surfeit locus 1 family protein
D 110157372 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 110161824 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 110171036 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 110156935 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 110153420 apopt1; apoptogenic protein 1, mitochondrial K23506 APOPT1; apoptogenic protein 1
D 110165085 cunh7orf73; uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1
D 110157965 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 110156131 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 110165663 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 110159674 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 110164250 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 110156527 cunh14orf2; 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 110153541 up-regulated during skeletal muscle growth protein 5-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 110175742 usmg5; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 110160071 mfn1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 110156031 mitofusin-2-like K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 110160112 opa1; dynamin-like 120 kDa protein, mitochondrial K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 110163671 opa3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein
D 110169687 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 110158822 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 110174766 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 110160566 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 110167787 bax; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 110174516 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 110164773 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 110164842 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 110169818 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 110169616 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 110172024 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 110153663 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 110166570 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 110171938 sumo2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 110172607 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 110165687 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 110165381 endophilin-B1-like K11248 SH3GLB1; endophilin-B1
D 110172893 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 110174321 mff; mitochondrial fission factor K22076 MFF; mitochondrial fission factor
D 110153387 mitochondrial fission factor homolog A-like K22076 MFF; mitochondrial fission factor
D 110160874 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 110154036 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 110161520 synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 110154199 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 110162356 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 110165571 mitochondrial dynamics protein MID51-like K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 110172588 pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 110157404 miga2; mitoguardin 2 K27289 MIGA; mitoguardin
D 110174921 miga1; mitoguardin 1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 110162397 actb; actin, cytoplasmic 1 isoform X1 K05692 ACTB_G1; actin beta/gamma 1
D 110153521 actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 110168536 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 110172332 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 110161576 phb; prohibitin K17080 PHB1; prohibitin 1
D 110162769 phb2; prohibitin-2 K17081 PHB2; prohibitin 2
D 110155262 ktn1; kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 110164842 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 110169818 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 110169616 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 110175253 myo5a; LOW QUALITY PROTEIN: unconventional myosin-Va K10357 MYO5; myosin V
D 110161435 myo5b; unconventional myosin-Vb K10357 MYO5; myosin V
D 110174026 LOW QUALITY PROTEIN: unconventional myosin-Va-like K10357 MYO5; myosin V
D 110169598 unconventional myosin-Va-like K10357 MYO5; myosin V
D 110169599 myo5c; unconventional myosin-Vc K10357 MYO5; myosin V
D 110158118 xiap; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 110163634 diablo homolog, mitochondrial-like K10522 DIABLO; diablo
D 110174032 diablo homolog, mitochondrial-like K10522 DIABLO; diablo
C Morphogenesis factors
D 110171385 mitochondrial Rho GTPase 1-A K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 110172568 mitochondrial Rho GTPase 1-A-like isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 110155786 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
D 110160577 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 110163087 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 110175206 nedd4; E3 ubiquitin-protein ligase NEDD4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 110171787 oxr1; oxidation resistance protein 1 K25437 OXR1; oxidation resistance protein 1
D 110168888 msto1; protein misato homolog 1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 110158829 atg2a; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 110155632 atg2b; autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2
D 110175605 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 110172623 atg4d; cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 110154699 atg4b; cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 110160085 atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 110171546 cysteine protease ATG4D-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 110161307 atg5; autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 110154282 becn1; beclin-1 K08334 BECN; beclin
D 110168467 atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 110159433 gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 110172754 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 110162996 gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 110153659 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 110158308 autophagy-related protein 9A-like K17907 ATG9; autophagy-related protein 9
D 110171350 atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 110163139 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 110167126 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 110169306 atg16l1; autophagy-related protein 16-1 K17890 ATG16L1; autophagy-related protein 16-1
D 110172305 autophagy-related protein 16-2-like K20868 ATG16L2; autophagy-related protein 16-2
D 110159536 wipi1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
D 110162433 wipi2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
D 110161022 WD repeat domain phosphoinositide-interacting protein 1-like K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 110168027 prkn; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 110164644 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 110155740 clec16a; LOW QUALITY PROTEIN: protein CLEC16A K19513 CLEC16A; protein CLEC16A
D 110159396 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 110158822 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 110174766 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 110153110 sqstm1; sequestosome-1 K14381 SQSTM1; sequestosome 1
D 110160382 LOW QUALITY PROTEIN: tax1-binding protein 1 homolog A-like K21347 TAX1BP1; Tax1-binding protein 1
D 110171619 tax1bp1; tax1-binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1
D 110154191 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
C Parkin-independent mechanism factors
D 110163259 atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 110169891 serine/threonine-protein kinase ULK1-like K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 110166347 serine/threonine-protein kinase ULK1-like K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 110171357 ulk2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 110157382 rb1cc1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 110168260 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 110168291 heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG
D 110164274 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 110157771 hsp90 co-chaperone Cdc37-like K09554 CDC37; cell division cycle protein 37
D 110167855 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 110166182 smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 110175789 E3 ubiquitin-protein ligase SMURF2-like K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 110162294 smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 110155210 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 110169883 BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 110170637 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1
D 110161078 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 110157325 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 110154939 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 110169302 map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 110174931 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 110158953 microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 110171170 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 110154256 nbr1; next to BRCA1 gene 1 protein K17987 NBR1; next to BRCA1 gene 1 protein
D 110160967 next to BRCA1 gene 1 protein-like isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 110171878 tectonin beta-propeller repeat-containing protein 1-like K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 110159580 tecpr1; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 110155059 zinc finger FYVE domain-containing protein 1-like K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 110155281 zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 110161983 zinc finger FYVE domain-containing protein 1-like isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 110154307 coasy; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 110168247 pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 110161334 protein C19orf12 homolog K23168 MPAN; protein MPAN
D 110162606 cunh19orf12; protein C19orf12 homolog K23168 MPAN; protein MPAN
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024