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Mitochondrial Biogenesis - Castor canadensis (American beaver)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 31082893 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 31082897 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 31082912 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 31082915 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 31082914 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 31082919 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 31082921 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 31082903 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 31082906 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 31082910 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 31082908 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 31082909 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 109692264 Polrmt; LOW QUALITY PROTEIN: DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 109688829 Tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 109688830 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
D 109700043 Tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 109674610 Tfb2m; dimethyladenosine transferase 2, mitochondrial isoform X1 K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 109681756 Mtif2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2
D 109694692 Mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 109686193 Tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 109682654 Tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 109682221 Gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 109696116 Gfm2; LOW QUALITY PROTEIN: ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 109697351 Mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 109696869 Mterf1; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 109702238 LOW QUALITY PROTEIN: transcription termination factor 2, mitochondrial-like K15031 MTERF; mitochondrial transcription termination factor family protein
D 109691930 Mterf3; transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 109698703 Mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 109694227 Guf1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 109703452 Pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 109693088 Pop4; ribonuclease P protein subunit p29 isoform X1 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 109696170 Pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 109699985 Rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 109698084 Pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 109694121 Rpp25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 109694680 Rpp25l; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 109691350 Rpp38; LOW QUALITY PROTEIN: ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 109698943 Rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
D 109698731 LOW QUALITY PROTEIN: ribonuclease P protein subunit p40-like K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 109693873 Trmt10c; mitochondrial ribonuclease P protein 1 K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 109702046 Hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 109697294 mitochondrial ribonuclease P protein 3-like K17655 MRPP3; mitochondrial ribonuclease P protein 3
D 109697254 mitochondrial ribonuclease P protein 3-like isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 109682628 Mss51; putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 109683329 transcription elongation factor, mitochondrial-like isoform X1 K17658 TEFM; transcription elongation factor, mitochondrial
D 109685056 pentatricopeptide repeat-containing protein 1, mitochondrial-like isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 109693386 Ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 109696131 Ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 109699219 Dhx30; putative ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 109681891 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 109703113 LOW QUALITY PROTEIN: ubiquinol-cytochrome-c reductase complex assembly factor 1-like K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 109686963 lactation elevated protein 1-like K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 109700753 lactation elevated protein 1-like K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 109686020 Atp23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 109685230 Supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 109688262 Lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 109675843 ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 109688777 Slc25a6; ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 109681419 Slc25a31; ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 109684937 Slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 109681507 Slc25a28; mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 109695386 Slc25a37; mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 109699609 Malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 109695649 Eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 109692981 Yars; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 109677883 LOW QUALITY PROTEIN: tyrosine--tRNA ligase, mitochondrial-like K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 109689201 Yars2; LOW QUALITY PROTEIN: tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 109686559 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 109686560 leucine--tRNA ligase, cytoplasmic-like K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 109694720 Dars2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 109681706 Gars; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 109681610 LOW QUALITY PROTEIN: arginine--tRNA ligase, cytoplasmic-like K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 109686474 Rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 109693600 Qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial isoform X1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 109680460 Gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 109696144 Gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 109695914 LOW QUALITY PROTEIN: poly(A) RNA polymerase, mitochondrial-like K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 109683130 Pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 109698395 Mtg1; mitochondrial ribosome-associated GTPase 1 isoform X1 K19828 MTG1; mitochondrial GTPase 1
D 109691662 Noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 109699128 Nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 109695244 Nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 109687018 Rpusd3; RNA pseudouridylate synthase domain-containing protein 3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 109698462 Rpusd4; RNA pseudouridylate synthase domain-containing protein 4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 109686972 Rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 109695074 Ngrn; neugrin K23496 NGRN; neugrin
D 109686797 Trub2; probable tRNA pseudouridine synthase 2 isoform X1 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 109688700 Fastkd2; LOW QUALITY PROTEIN: FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 109683527 CUNH12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor
D 109694209 Rmnd1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1
D 109687680 Grsf1; G-rich sequence factor 1 isoform X1 K24984 GRSF1; G-rich sequence factor 1
D 109698963 Mettl15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 109684047 CUNH12orf10; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 109687066 uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 109687557 Polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 109695646 Polg2; LOW QUALITY PROTEIN: DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 109689111 DNA-directed primase/polymerase protein-like K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
D 109689109 Primpol; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 109697705 Endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 109696451 Mgme1; LOW QUALITY PROTEIN: mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 109695730 Exog; nuclease EXOG, mitochondrial isoform X1 K15050 EXOG; nuclease EXOG, mitochondrial
D 109695267 Twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 109688306 Pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 109699051 Ssbp1; single-stranded DNA-binding protein, mitochondrial isoform X1 K03111 ssb; single-strand DNA-binding protein
D 109681086 LOW QUALITY PROTEIN: ATPase family AAA domain-containing protein 3-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 109686690 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 109696656 Dnaja2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 109681317 Tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 109683325 Rhot1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 109689570 LOW QUALITY PROTEIN: heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 109689571 heat shock 70 kDa protein 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 109689572 LOW QUALITY PROTEIN: heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 109697755 Hspa8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 109693503 LOW QUALITY PROTEIN: heat shock 70 kDa protein 6-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 109702663 Aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 109688621 Aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 109693210 Tomm40l; LOW QUALITY PROTEIN: mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 109692403 Tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 109676416 LOW QUALITY PROTEIN: mitochondrial import receptor subunit TOM70-like K17768 TOM70; mitochondrial import receptor subunit TOM70
D 109692631 Tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 109700070 Tomm20l; TOMM20-like protein 1 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 109692624 Tomm20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 109701043 Tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 109682163 Tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 109682756 Tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 109693121 Samm50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 109697584 Vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 109693642 Vdac2; LOW QUALITY PROTEIN: voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 109700211 voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 109696398 Vdac3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 109688024 Mtx1; metaxin-1 K17776 MTX; metaxin
D 109700588 Mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 109695045 Mtx2; metaxin-2 isoform X1 K17776 MTX; metaxin
D 109691231 Myo19; unconventional myosin-XIX K25838 MYO19; myosin XIX
D 109693407 Armcx2; armadillo repeat-containing X-linked protein 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2
D 109693410 Armcx3; armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3
D 109693409 Armcx6; protein ARMCX6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6
D 109687200 Marc1; mitochondrial amidoxime-reducing component 1 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 109700080 Timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 109679399 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 109688985 Timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 109696313 Timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 109699436 Timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 109692201 Timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 109691032 Timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 109694027 Chchd4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 109690199 Gfer; FAD-linked sulfhydryl oxidase ALR isoform X1 K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 109687476 Minos1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 109696133 Immt; LOW QUALITY PROTEIN: MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
D 109688201 CUNH19orf70; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 109685437 Chchd3; MICOS complex subunit MIC19 K17563 CHCHD3; MICOS complex subunit MIC19
D 109679148 Chchd6; MICOS complex subunit MIC25 K17564 CHCHD6; MICOS complex subunit MIC25
D 109685646 Apoo; MICOS complex subunit MIC26 isoform X1 K24625 APOO; MICOS complex subunit MIC26
D 109691339 Apool; LOW QUALITY PROTEIN: MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 109687476 Minos1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 109696133 Immt; LOW QUALITY PROTEIN: MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 109682610 Timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 109683988 Timm23b; putative mitochondrial import inner membrane translocase subunit Tim23B isoform X1 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 109692140 Timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 109684755 Timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 109698234 Timm21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 109681997 Timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 109688244 calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial
D 109702293 calcium uptake protein 1, mitochondrial-like K22827 MICU1; calcium uptake protein 1, mitochondrial
D 109685473 calcium uptake protein 1, mitochondrial-like K22827 MICU1; calcium uptake protein 1, mitochondrial
D 109689017 Micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 109694928 Mcub; calcium uniporter regulatory subunit MCUb, mitochondrial isoform X1 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 109689364 Smdt1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 109694530 Mcur1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 109695003 Letm1; LETM1 and EF-hand domain-containing protein 1, mitochondrial K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 109697161 Tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 109683069 Mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 109696040 Mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 109698450 Chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 109698440 Timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 109681366 Hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 109690573 Grpel2; LOW QUALITY PROTEIN: grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 109687263 Grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 109699655 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 109689668 Dnajc19; LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 109681692 Pam16; mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 109697435 Pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 109686864 Pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 109682365 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 109681926 Hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 109681928 Hspe1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 109694946 Tamm41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 109699035 Dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 109691867 Ethe1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 109698352 Poldip2; LOW QUALITY PROTEIN: polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 109691946 Creb1; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 109682221 Gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 109696116 Gfm2; LOW QUALITY PROTEIN: ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 109684073 Sp1; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 109694192 transcription factor YY2-like K09201 YY; transcription factor YY
D 109694359 Yy1; LOW QUALITY PROTEIN: transcriptional repressor protein YY1 K09201 YY; transcription factor YY
D 109681211 Gabpb2; GA-binding protein subunit beta-2 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 109699100 Gabpb1; GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 109688829 Tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 109688830 transcription factor A, mitochondrial-like K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 109684011 Nrf1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 109684347 Nfe2l2; nuclear factor erythroid 2-related factor 2 isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 109700384 metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 109700394 metallothionein-2 isoform X1 K14739 MT1_2; metallothionein 1/2
D 109700404 metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 109682416 metallothionein-4 K14741 MT4; metallothionein 4
D 109700374 Mt4; metallothionein-4 K14741 MT4; metallothionein 4
C Coactivators
D 109684858 Ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 109683169 Ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 109691308 Pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 109694650 Crtc1; LOW QUALITY PROTEIN: CREB-regulated transcription coactivator 1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 109681682 Crebbp; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 109690951 Ep300; histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 109682638 Nfs1; cysteine desulfurase, mitochondrial isoform X1 K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 109688617 Iscu; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 109674470 LYR motif-containing protein 4 isoform X1 K22069 LYRM4; LYR motif-containing protein 4
D 109696410 Fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 109700941 Fdx1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial
D 109693171 Fdx1l; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 109687573 Fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 109681366 Hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 109690243 Hscb; iron-sulfur cluster co-chaperone protein HscB, mitochondrial isoform X1 K04082 hscB; molecular chaperone HscB
D 109681361 Sil1; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 109693125 Isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 109686293 Isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 109698120 Iba57; putative transferase CAF17, mitochondrial isoform X1 K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 109695095 Nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 109677277 Bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 109688145 Bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 109691224 Sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 109701777 Sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 109691328 Sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2
D 109701122 Sfxn4; LOW QUALITY PROTEIN: sideroflexin-4 K23502 SFXN4; sideroflexin-4
D 109696450 Sfxn5; sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5
D 109696402 sideroflexin-5-like K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 109700002 Cpt1a; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 109697469 Cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform isoform X1 K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 109683908 Cpt1c; carnitine O-palmitoyltransferase 1, brain isoform K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
D 109682443 Dhtkd1; LOW QUALITY PROTEIN: probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 109695059 Fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 109701932 Hcfc1; host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1
D 109675858 Hcfc2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2
D 109687432 Htt; LOW QUALITY PROTEIN: huntingtin K04533 HD; huntingtin
D 109683286 Esrra; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 109702010 Esrrb; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta
D 109686056 estrogen-related receptor gamma-like K08554 NR3B3; estrogen-related receptor gamma
D 109702126 Esrrg; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma
D 109701289 Nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 109695664 Prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 109687258 Prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 109688221 Lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 109681555 Sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 109681904 Serac1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1
D 109696674 Uxt; protein UXT K26537 UXT; protein UXT
D 109685582 Perm1; PGC-1 and ERR-induced regulator in muscle protein 1 isoform X1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 109687954 Ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 109684239 Ndufaf2; mimitin, mitochondrial K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 109691971 Ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 109697516 Ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 109688318 Ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 109695604 Ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 109688637 Ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 109700466 Ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 109697159 Tmem126b; complex I assembly factor TMEM126B, mitochondrial isoform X1 K18165 TMEM126B; complex I assembly factor TMEM126B
D 109692584 Ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 109690107 Acad9; LOW QUALITY PROTEIN: acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 109698468 Foxred1; FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 109693601 Rtn4ip1; reticulon-4-interacting protein 1, mitochondrial isoform X1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 109694541 Timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 109689330 Sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 109686671 Sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial isoform X1 K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 109681369 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 109699490 tetratricopeptide repeat protein 19, mitochondrial-like isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 109692525 tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 109694338 Lyrm7; complex III assembly factor LYRM7 isoform X1 K18170 LYRM7; complex III assembly factor LYRM7
D 109681891 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 109703113 LOW QUALITY PROTEIN: ubiquinol-cytochrome-c reductase complex assembly factor 1-like K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 109686690 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 109697947 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 109690192 CUNH16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 109693714 Smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 109675774 CUNH12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 109698593 CUNH7orf73; uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 109700453 Cmc1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 109690787 Cmc2; COX assembly mitochondrial protein 2 homolog isoform X1 K18172 CMC2; COX assembly mitochondrial protein 2
D 109687314 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 109698324 cytochrome c oxidase assembly factor 4 homolog, mitochondrial isoform X1 K18177 COA4; cytochrome c oxidase assembly factor 4
D 109694388 cytochrome c oxidase assembly factor 5 isoform X1 K18178 COA5; cytochrome c oxidase assembly factor 5
D 109678049 LOW QUALITY PROTEIN: cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 109701128 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 109684973 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 109688430 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 109695416 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 109681509 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 109693492 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 109694538 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 109682065 mitochondrial inner membrane protein COX18 isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18
D 109690357 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 109700250 uncharacterized protein LOC109700250 isoform X1 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 109682628 Mss51; putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51
D 109690963 Pet100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 109699932 Pet117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 109685800 Oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 109696121 surfeit locus protein 1 isoform X1 K14998 SURF1; surfeit locus 1 family protein
D 109697086 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 109697514 protein SCO2 homolog, mitochondrial isoform X1 K23755 SCO2; protein SCO2
D 109703238 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 109700486 Lrpprc; leucine-rich PPR motif-containing protein, mitochondrial isoform X1 K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 109682450 apoptogenic protein 1, mitochondrial K23506 APOPT1; apoptogenic protein 1
D 109682451 apoptogenic protein 1, mitochondrial-like K23506 APOPT1; apoptogenic protein 1
D 109698593 CUNH7orf73; uncharacterized protein C7orf73 homolog K27319 STMP1; short transmembrane mitochondrial protein 1
D 109693714 Smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 109693851 Tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 109695460 Atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 109683614 Atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 109692109 Tmem70; transmembrane protein 70, mitochondrial isoform X1 K17966 TMEM70; transmembrane protein 70, mitochondrial
D 109701659 CUNH14orf2; 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 109697273 Usmg5; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 109689665 Mfn1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 109683965 Mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 109697831 Opa1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 109692388 Opa3; LOW QUALITY PROTEIN: optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein
D 109696145 Triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 109694101 Parl; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 109686692 Bak1; bcl-2 homologous antagonist/killer K14021 BAK; Bcl-2 homologous antagonist/killer
D 109682703 Bax; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 109689200 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 109689202 Dnm1l; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 109692812 Fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 109674475 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 109687593 Sumo2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 109694961 Sumo3; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 109683761 Sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 109686516 endophilin-B1 K11248 SH3GLB1; endophilin-B1
D 109686517 endophilin-B1-like K11248 SH3GLB1; endophilin-B1
D 109690899 Mtch1; mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier
D 109696181 Mtch2; mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier
D 109696755 Mff; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor
D 109692499 Gdap1l1; LOW QUALITY PROTEIN: ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 109694905 Gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 109687347 Vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 109693019 Mief1; LOW QUALITY PROTEIN: mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 109695108 Mief2; mitochondrial dynamics protein MID49 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 109698423 Pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 109693451 Miga2; mitoguardin 2 isoform X1 K27289 MIGA; mitoguardin
D 109692602 Miga1; mitoguardin 1 isoform X1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 109700700 actin, cytoplasmic 1 isoform X1 K05692 ACTB_G1; actin beta/gamma 1
D 109690954 Naa20; N-alpha-acetyltransferase 20 isoform X1 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 109684646 N-alpha-acetyltransferase 25, NatB auxiliary subunit-like K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
D 109684647 Naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 109691410 Phb; prohibitin K17080 PHB1; prohibitin 1
D 109682777 Phb2; prohibitin-2 K17081 PHB2; prohibitin 2
D 109698470 Ktn1; LOW QUALITY PROTEIN: kinectin K17975 KTN1; kinectin
C Retention of mitochondria
D 109689200 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 109689202 Dnm1l; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 109695551 Myo5a; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V
D 109695552 Myo5c; LOW QUALITY PROTEIN: unconventional myosin-Vc K10357 MYO5; myosin V
D 109698176 Myo5b; unconventional myosin-Vb K10357 MYO5; myosin V
D 109700263 Xiap; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 109684613 Diablo; diablo homolog, mitochondrial K10522 DIABLO; diablo
C Morphogenesis factors
D 109684935 LOW QUALITY PROTEIN: sorting nexin-25-like K17887 SNX25; sorting nexin-25
D 109683325 Rhot1; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 109696133 Immt; LOW QUALITY PROTEIN: MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
D 109696784 Mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 109688016 Dap3; 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29
D 109700662 E3 ubiquitin-protein ligase NEDD4-like K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 109690744 oxidation resistance protein 1-like isoform X1 K25437 OXR1; oxidation resistance protein 1
D 109688010 Msto1; protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 109687168 Atg2a; autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 109697559 Atg2b; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 109683338 Atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 109682471 Atg4b; cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 109686142 Atg4c; cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 109696110 Atg4d; cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 109685429 cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 109701355 Atg5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5
D 109687340 Becn1; beclin-1 isoform X1 K08334 BECN; beclin
D 109693432 Becn2; beclin-2 K08334 BECN; beclin
D 109694948 Atg7; ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 109674552 Gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 109684019 Gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 109689711 Gabarapl1; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 109691072 Atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 109694436 Atg9b; LOW QUALITY PROTEIN: autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 109695467 Atg10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 109691512 Atg12; ubiquitin-like protein ATG12 isoform X1 K08336 ATG12; ubiquitin-like protein ATG12
D 109698491 Atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 109695961 Atg16l1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 109686554 Atg16l2; autophagy-related protein 16-2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2
D 109687467 WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
D 109687468 WD repeat domain phosphoinositide-interacting protein 1-like K17908 WIPI1_2; autophagy-related protein 18
D 109694858 Wipi2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18
D 109681398 LOW QUALITY PROTEIN: WD repeat domain phosphoinositide-interacting protein 2-like K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 109688031 LOW QUALITY PROTEIN: E3 ubiquitin-protein ligase parkin-like K04556 PARK2; parkin [EC:2.3.2.31]
D 109686059 Rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 109686091 E3 ubiquitin-protein ligase NRDP1-like K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 109700719 protein CLEC16A K19513 CLEC16A; protein CLEC16A
D 109689686 Pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 109694101 Parl; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 109686732 Sqstm1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1
D 109696790 Tax1bp1; LOW QUALITY PROTEIN: tax1-binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1
D 109692964 Calcoco2; calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 109692005 Ambra1; activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 109696258 Atg13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13
D 109697545 Ulk1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 109687740 Ulk2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 109690087 Rb1cc1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 109682122 Hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 109696011 Hsp90aa1; heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 109693176 Cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 109684429 Smurf1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 109695587 Smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 109694062 Bnip3l; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 109699634 LOW QUALITY PROTEIN: FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 109695664 Prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 109687258 Prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 109696466 Map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 109685898 Map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 109687349 Nbr1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 109692910 Tecpr1; LOW QUALITY PROTEIN: tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 109687107 Zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 109687307 Coasy; bifunctional coenzyme A synthase isoform X1 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 109692765 Pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 109674620 protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN
D 109693089 CUNH19orf12; protein C19orf12 homolog K23168 MPAN; protein MPAN
D 109694747 LOW QUALITY PROTEIN: FUN14 domain-containing protein 2-like K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024