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  Mitochondrial Biogenesis - Lucilia cuprina (Australian sheep blowfly)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I C Mitochondrial respiratory chain complex III C Cytochrome c oxidase C F-type ATPase B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 111681407 DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 111680093 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 111683944 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 111690162 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 111683135 translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2 D 111690122 translation initiation factor IF-3, mitochondrial isoform X2 K02520 infC; translation initiation factor IF-3 D 111684956 elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 111677386 elongation factor Tu K02358 tuf; elongation factor Tu D 111675915 elongation factor Tu isoform X1 K02358 tuf; elongation factor Tu D 111685217 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 111690736 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 111679305 transcription termination factor 5, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 111677714 transcription termination factor, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 111685172 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 111679112 translation factor waclaw, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 111675972 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 111688765 ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 124420066 ribonuclease P protein subunit p29-like K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 111688785 ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 111686320 ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 111690801 ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 111679213 ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 111675345 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 111678909 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 111681252 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 111679909 uncharacterized protein LOC111679909 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 111682461 uncharacterized protein LOC111682461 K17658 TEFM; transcription elongation factor, mitochondrial D 111677217 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 111679856 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 111688941 putative ATPase N2B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 111675529 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 111675785 ATP-dependent RNA helicase SUV3 homolog, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 111684947 beta-lactamase-like protein 2 homolog isoform X1 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 111677160 ADP,ATP carrier protein K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 111677184 ADP,ATP carrier protein 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 111675489 mitoferrin K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 111686682 uncharacterized protein LOC111686682 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 111680380 GTPase Era, mitochondrial K03595 era; GTPase D 111686248 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 111689611 tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 111680411 probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 111682836 leucine--tRNA ligase, cytoplasmic isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 111682909 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 111683624 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 111682409 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 111681466 probable arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 111676449 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 111683391 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 111680014 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 111691042 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 111677870 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 111676081 mitochondrial GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 111677374 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 111681388 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 111685376 RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 111690250 uncharacterized protein LOC111690250 K23496 NGRN; neugrin D 111682513 mitochondrial mRNA pseudouridine synthase Trub2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 111678152 mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor D 111679109 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 111683241 C-1-tetrahydrofolate synthase, cytoplasmic K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 124418428 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 111674839 MYG1 protein isoform X1 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 111680981 mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 111686631 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 111680013 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 C Mitochondrial DNA maintenance factors D 111681962 endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 111681717 mitochondrial DNA helicase isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3] D 111684661 ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 111686001 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 111680257 ATPase family AAA domain-containing protein 3A homolog K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 111679532 dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 111684894 mitochondrial Rho GTPase isoform X2 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 111681612 heat shock protein 70 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111681632 heat shock protein 70 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111681634 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111687157 heat shock protein 68 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111679075 heat shock 70 kDa protein cognate 2 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111680172 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111677121 heat shock 70 kDa protein cognate 4 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 124419641 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 124419642 heat shock protein 68 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 124419643 heat shock protein 70 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 124419644 heat shock protein 70 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 124419829 heat shock protein 70 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 124419830 heat shock protein 70-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 111684520 AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 111676932 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 111690334 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 111684754 mitochondrial import receptor subunit TOM22 homolog isoform X1 K17769 TOM22; mitochondrial import receptor subunit TOM22 D 111688676 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 111680480 mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 111680481 mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 C TOB/SAM complex D 111687128 SAM50-like protein CG7639 K07277 SAM50; outer membrane protein insertion porin family C Porin D 111681702 voltage-dependent anion-selective channel K15040 VDAC2; voltage-dependent anion channel protein 2 C ERMES complex C Other outer membrane factor D 111680442 metaxin-1 homolog isoform X1 K17776 MTX; metaxin D 111682661 metaxin-2 isoform X1 K17776 MTX; metaxin D 111676180 mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 111684121 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 111679596 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 111680184 mitochondrial import inner membrane translocase subunit Tim10B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 111684471 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 111677723 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 111680942 mitochondrial intermembrane space import and assembly protein 40-B K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 111679460 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 111686254 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10 D 111686861 MICOS complex subunit Mic60 isoform X2 K17785 IMMT; MICOS complex subunit MIC60 D 111687208 MICOS complex subunit MIC13 homolog QIL1-like K24624 MICOS13; MICOS complex subunit MIC13 D 111681568 uncharacterized protein LOC111681568 K17563 CHCHD3; MICOS complex subunit MIC19 D 111690246 MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 111686254 MICOS complex subunit MIC10-like K17784 MICOS10; MICOS complex subunit MIC10 D 111686861 MICOS complex subunit Mic60 isoform X2 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 111689613 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 111675286 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 111688556 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 111681243 mitochondrial import inner membrane translocase subunit TIM50-C-like K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 111681413 calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial D 111685779 calcium uptake protein 1 homolog, mitochondrial isoform X3 K22827 MICU1; calcium uptake protein 1, mitochondrial D 111687796 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial C Other inner membrane factors D 111688259 mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 111680756 mitochondrial inner membrane protease subunit 1 isoform X1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 111678572 mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 111685491 uncharacterized protein LOC111685491 K18157 TMEM126A; transmembrane protein 126A D 111677175 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 111687678 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2 D 111687684 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2 D 124418430 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2 B Matrix C MMC/PAM proteins D 111678866 mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 111678546 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 111677396 grpE protein homolog, mitochondrial K03687 GRPE; molecular chaperone GrpE D 111678479 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 111676952 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 111678561 mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 111677338 mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 111680043 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 111681434 heat shock protein 60A K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 111677649 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 111680080 protein tumorous imaginal discs, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 111677320 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 111681247 uncharacterized protein LOC111681247 K17808 ZIM17; mitochondrial protein import protein ZIM17 D 111683739 uncharacterized protein LOC111683739 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 111683740 persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 111680439 polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 111685990 cyclic AMP response element-binding protein B isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 111685217 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 111690736 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 111675078 transcriptional regulator CRZ1 isoform X1 K09201 YY; transcription factor YY D 111682104 basic-leucine zipper transcription factor B isoform X2 K09454 GABPB; GA-binding protein transcription factor, beta D 111680093 transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 111677036 LOW QUALITY PROTEIN: DNA-binding protein Ewg K11831 NRF1; nuclear respiratory factor 1 C Coactivators D 111680919 histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 111681077 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 111680258 iron-sulfur cluster assembly scaffold protein IscU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 111675161 protein bcn92 K22069 LYRM4; LYR motif-containing protein 4 D 111682368 frataxin homolog, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 111686587 adrenodoxin-like protein 2, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 111675110 adrenodoxin-like protein 1, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 111684762 NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 111678546 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 111686370 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB D 111680268 nucleotide exchange factor Sil1 isoform X2 K14001 SIL1; nucleotide exchange factor SIL1 D 111688759 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 111686292 iron-sulfur cluster assembly 1 homolog, mitochondrial isoform X1 K22063 ISCA1; iron-sulfur cluster assembly 1 D 111690266 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 111675646 putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 111684204 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial-like K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 111676454 bolA-like protein DDB_G0274169 K22066 BOLA1; BolA-like protein 1 D 111678045 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 111675469 sideroflexin-1-3 K23500 SFXN1_3; sideroflexin-1/3 D 111689693 sideroflexin-2 K23501 SFXN2; sideroflexin-2 C Other regulator of mitochondrial biogenesis D 111680063 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 111681550 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 111680112 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 111676742 host cell factor-like K14966 HCFC1; host cell factor 1 D 111684600 host cell factor-like K14966 HCFC1; host cell factor 1 D 111675673 uncharacterized protein LOC111675673 isoform X1 K04533 HD; huntingtin D 111676734 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 111677879 lon protease homolog, mitochondrial isoform X1 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 111679526 NAD-dependent histone deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 111689400 uncharacterized protein LOC111689400 K23504 SERAC1; protein SERAC1 D 111679527 protein SERAC1 K23504 SERAC1; protein SERAC1 D 111687674 protein UXT K26537 UXT; protein UXT B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 111676105 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 111686432 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 111677012 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 111690539 protein NDUFAF4 homolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 111682382 arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 111682284 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 homolog K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 111690302 protein arginine methyltransferase NDUFAF7 homolog, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 111679591 uncharacterized protein LOC111679591 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 111690550 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 111679200 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 111676793 FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 111676097 RPII140-upstream gene protein K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 111677347 succinate dehydrogenase assembly factor 2-A, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 111685091 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 111687398 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 111678064 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 111679856 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 111685081 uncharacterized protein LOC111685081 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 111678944 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 111678945 protein brawnin K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 111685038 short transmembrane mitochondrial protein 1 isoform X1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 111688514 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 111689864 COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 111686913 uncharacterized protein LOC111686913 K18173 COA1; cytochrome c oxidase assembly factor 1 D 111683947 cytochrome c oxidase assembly factor 3, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 111680383 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 111677389 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 111681157 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 111677606 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7 D 111680678 protoheme IX farnesyltransferase, mitochondrial isoform X1 K02257 COX10; heme o synthase [EC:2.5.1.141] D 111682702 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 111677019 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 111681806 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 111677827 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 111683243 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18 D 111687336 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 111681629 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 111679909 uncharacterized protein LOC111679909 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 111684402 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 111678410 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 111677245 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 111685727 SURF1-like protein K14998 SURF1; surfeit locus 1 family protein D 111680549 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 111689574 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 111684698 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 111689015 COA8 family protein CG14806, mitochondrial K23506 APOPT1; apoptogenic protein 1 D 111685038 short transmembrane mitochondrial protein 1 isoform X1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 111678944 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 111675367 transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 111690660 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 111683927 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 111675116 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 111682851 uncharacterized protein LOC111682851 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 111679253 transmembrane GTPase Marf isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 111678528 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 111676090 putative OPA3-like protein CG13603 isoform X1 K23166 OPA3; optic atrophy 3 protein D 111686784 TP53-regulated inhibitor of apoptosis 1-like K17968 TRIAP1; TRIAP1/MDM35 family protein D 111678178 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 111679173 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 111680018 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 111687306 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 111688263 endophilin-B1 isoform X2 K11248 SH3GLB1; endophilin-B1 D 111682732 mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 111680377 transport and Golgi organization protein 11 isoform X1 K22076 MFF; mitochondrial fission factor D 111685353 ganglioside-induced differentiation-associated protein 1 isoform X2 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 111676024 mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 111674817 mitoguardin K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 111678903 actin-5C K05692 ACTB_G1; actin beta/gamma 1 D 111687954 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 111684095 phagocyte signaling-impaired protein K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 111686133 protein l(2)37Cc K17080 PHB1; prohibitin 1 D 111686145 prohibitin-2 K17081 PHB2; prohibitin 2 C Retention of mitochondria D 111679173 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 111675961 unconventional myosin-Va isoform X1 K10357 MYO5; myosin V C Morphogenesis factors D 111678614 sorting nexin-25 K17887 SNX25; sorting nexin-25 D 111684894 mitochondrial Rho GTPase isoform X2 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 111686861 MICOS complex subunit Mic60 isoform X2 K17785 IMMT; MICOS complex subunit MIC60 D 111685962 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 111680124 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 111676809 E3 ubiquitin-protein ligase Nedd-4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 111683281 protein misato K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 111680345 autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 111681918 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 111679667 cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 111680547 cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 111687638 autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 111687145 beclin-1-like protein K08334 BECN; beclin D 111684868 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 111685188 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 111679105 autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 111689686 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 111685366 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12 D 111679673 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 111683416 autophagy-related protein 16 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 111689616 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 111687393 WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 111685242 E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31] D 111687655 E3 ubiquitin-protein ligase NRDP1 isoform X2 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 111676757 protein CLEC16A homolog isoform X2 K19513 CLEC16A; protein CLEC16A D 111678178 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] C Parkin-independent mechanism factors D 111684618 autophagy-related protein 13 homolog K08331 ATG13; autophagy-related protein 13 D 111683141 serine/threonine-protein kinase unc-51 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 111676528 RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 111679400 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG D 111675609 hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 111682517 E3 ubiquitin-protein ligase Smurf1-like K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 111687310 FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 111676734 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 111690004 tectonin beta-propeller repeat-containing protein K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 111679262 zinc finger FYVE domain-containing protein 1-like isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 111682123 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 111675088 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 111680353 protein C19orf12 homolog K23168 MPAN; protein MPAN ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024