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Mitochondrial Biogenesis - Mus musculus (house mouse)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 17716 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 17717 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 17718 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 17719 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 17720 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 17721 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 17722 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 17711 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 17708 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 17709 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 17710 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 17706 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 17705 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 216151 Polrmt; polymerase (RNA) mitochondrial (DNA directed) K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 21780 Tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 224481 Tfb1m; transcription factor B1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 15278 Tfb2m; transcription factor B2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 76784 Mtif2; mitochondrial translational initiation factor 2 K02519 infB; translation initiation factor IF-2
D 76366 Mtif3; mitochondrial translational initiation factor 3 K02520 infC; translation initiation factor IF-3
D 66399 Tsfm; Ts translation elongation factor, mitochondrial K02357 tsf; elongation factor Ts
D 233870 Tufm; Tu translation elongation factor, mitochondrial K02358 tuf; elongation factor Tu
D 28030 Gfm1; G elongation factor, mitochondrial 1 K02355 fusA; elongation factor G
D 320806 Gfm2; G elongation factor, mitochondrial 2 K02355 fusA; elongation factor G
D 208595 Mterf1b; mitochondrial transcription termination factor 1b K15031 MTERF; mitochondrial transcription termination factor family protein
D 545725 Mterf1a; mitochondrial transcription termination factor 1a K15031 MTERF; mitochondrial transcription termination factor family protein
D 74238 Mterf2; mitochondrial transcription termination factor 2 K15031 MTERF; mitochondrial transcription termination factor family protein
D 66410 Mterf3; mitochondrial transcription termination factor 3 K15031 MTERF; mitochondrial transcription termination factor family protein
D 69821 Mterf4; mitochondrial transcription termination factor 4 K15031 MTERF; mitochondrial transcription termination factor family protein
D 231279 Guf1; GUF1 homolog, GTPase K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 67724 Pop1; processing of precursor 1, ribonuclease P/MRP family, (S. cerevisiae) K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 66161 Pop4; processing of precursor 4, ribonuclease P/MRP family, (S. cerevisiae) K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 117109 Pop5; processing of precursor 5, ribonuclease P/MRP family (S. cerevisiae) K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 54364 Rpp30; ribonuclease P/MRP 30 subunit K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 74097 Pop7; processing of precursor 7, ribonuclease P family, (S. cerevisiae) K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 102614 Rpp25; ribonuclease P/MRP 25 subunit K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 69961 Rpp25l; ribonuclease P/MRP 25 subunit-like K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 227522 Rpp38; ribonuclease P/MRP 38 subunit K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 208366 Rpp40; ribonuclease P 40 subunit K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 52575 Trmt10c; tRNA methyltransferase 10C, mitochondrial RNase P subunit K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 15108 Hsd17b10; hydroxysteroid (17-beta) dehydrogenase 10 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 66132 Prorp; protein only RNase P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 74843 Mss51; MSS51 mitochondrial translational activator K17656 MSS51; mitochondrial splicing suppressor protein 51
D 68550 Tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 71799 Ptcd1; pentatricopeptide repeat domain 1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 68927 Ptcd2; pentatricopeptide repeat domain 2 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 69956 Ptcd3; pentatricopeptide repeat domain 3 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 72831 Dhx30; DExH-box helicase 30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 56046 Uqcc1; ubiquinol-cytochrome c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 215951 Afg1l; AFG1 like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 68876 Atp23; ATP23 metallopeptidase and ATP synthase assembly factor homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 338359 Supv3l1; suppressor of var1, 3-like 1 (S. cerevisiae) K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 212442 Lactb2; lactamase, beta 2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 11739 Slc25a4; solute carrier family 25 (mitochondrial carrier, adenine nucleotide translocator), member 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 11740 Slc25a5; solute carrier family 25 (mitochondrial carrier, adenine nucleotide translocator), member 5 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 73333 Slc25a31; solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 31 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 67712 Slc25a37; solute carrier family 25, member 37 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 246696 Slc25a28; solute carrier family 25, member 28 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 100862085 Gm16867; predicted gene, 16867 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 75593 Malsu1; mitochondrial assembly of ribosomal large subunit 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 57837 Eral1; Era like 12S mitochondrial rRNA chaperone 1 K03595 era; GTPase
D 107271 Yars1; tyrosyl-tRNA synthetase 1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 70120 Yars2; tyrosyl-tRNA synthetase 2 (mitochondrial) K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 102436 Lars2; leucyl-tRNA synthetase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 107045 Lars1; leucyl-tRNA synthetase 1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 226539 Dars2; aspartyl-tRNA synthetase 2 (mitochondrial) K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 353172 Gars1; glycyl-tRNA synthetase 1 K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 104458 Rars1; arginyl-tRNA synthetase 1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 109093 Rars2; arginyl-tRNA synthetase 2, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 76563 Qrsl1; glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 229487 Gatb; glutamyl-tRNA amidotransferase subunit B K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 384281 Gatc; glutamyl-tRNA amidotransferase subunit C K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 67440 Mtpap; mitochondrial poly(A) polymerase K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 211948 Pde12; phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 212508 Mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 56412 Noa1; nitric oxide associated 1 K19832 NOA1; nitric oxide-associated protein 1
D 106338 Nsun3; NOL1/NOP2/Sun domain family member 3 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 72181 Nsun4; NOL1/NOP2/Sun domain family, member 4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 101122 Rpusd3; RNA pseudouridylate synthase domain containing 3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 71989 Rpusd4; RNA pseudouridylate synthase domain containing 4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 94254 Rcc1l; reculator of chromosome condensation 1 like K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 83485 Ngrn; neugrin, neurite outgrowth associated K23496 NGRN; neugrin
D 227682 Trub2; TruB pseudouridine (psi) synthase family member 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 75619 Fastkd2; FAST kinase domains 2 K18190 FASTKD2; FAST kinase domain-containing protein 2
D 72650 Mtrfr; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 66084 Rmnd1; required for meiotic nuclear division 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 231413 Grsf1; G-rich RNA sequence binding factor 1 K24984 GRSF1; G-rich sequence factor 1
D 76894 Mettl15; methyltransferase like 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 60315 Myg1; melanocyte proliferating gene 1 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 67851 Mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 18975 Polg; polymerase (DNA directed), gamma K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 50776 Polg2; polymerase (DNA directed), gamma 2, accessory subunit K02333 POLG2; DNA polymerase gamma 2
D 408022 Primpol; primase and polymerase (DNA-directed) K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 13804 Endog; endonuclease G K01173 ENDOG; endonuclease G, mitochondrial
D 74528 Mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 208194 Exog; exo/endonuclease G K15050 EXOG; nuclease EXOG, mitochondrial
D 226153 Twnk; twinkle mtDNA helicase K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 208084 Pif1; PIF1 5'-to-3' DNA helicase K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 381760 Ssbp1; single-stranded DNA binding protein 1 K03111 ssb; single-strand DNA-binding protein
D 108888 Atad3a; ATPase family, AAA domain containing 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 67267 Uqcc2; ubiquinol-cytochrome c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 56445 Dnaja2; DnaJ heat shock protein family (Hsp40) member A2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 67145 Tomm34; translocase of outer mitochondrial membrane 34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 59040 Rhot1; ras homolog family member T1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 15481 Hspa8; heat shock protein 8 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 15482 Hspa1l; heat shock protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 193740 Hspa1a; heat shock protein 1A K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 15511 Hspa1b; heat shock protein 1B K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 114230 Aipl1; aryl hydrocarbon receptor-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 11632 Aip; aryl-hydrocarbon receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 53333 Tomm40; translocase of outer mitochondrial membrane 40 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 641376 Tomm40l; translocase of outer mitochondrial membrane 40-like K11518 TOM40; mitochondrial import receptor subunit TOM40
D 28185 Tomm70a; translocase of outer mitochondrial membrane 70A K17768 TOM70; mitochondrial import receptor subunit TOM70
D 223696 Tomm22; translocase of outer mitochondrial membrane 22 K17769 TOM22; mitochondrial import receptor subunit TOM22
D 67952 Tomm20; translocase of outer mitochondrial membrane 20 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 75266 Tomm20l; translocase of outer mitochondrial membrane 20-like K17770 TOM20; mitochondrial import receptor subunit TOM20
D 66169 Tomm7; translocase of outer mitochondrial membrane 7 K17771 TOM7; mitochondrial import receptor subunit TOM7
D 66119 Tomm6; translocase of outer mitochondrial membrane 6 K17772 TOM6; mitochondrial import receptor subunit TOM6
D 68512 Tomm5; translocase of outer mitochondrial membrane 5 K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 68653 Samm50; SAMM50 sorting and assembly machinery component K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 22333 Vdac1; voltage-dependent anion channel 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 22334 Vdac2; voltage-dependent anion channel 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 22335 Vdac3; voltage-dependent anion channel 3 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 17827 Mtx1; metaxin 1 K17776 MTX; metaxin
D 382793 Mtx3; metaxin 3 K17776 MTX; metaxin
D 53375 Mtx2; metaxin 2 K17776 MTX; metaxin
D 66196 Myo19; myosin XIX K25838 MYO19; myosin XIX
D 78248 Armcx1; armadillo repeat containing, X-linked 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1
D 67416 Armcx2; armadillo repeat containing, X-linked 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2
D 71703 Armcx3; armadillo repeat containing, X-linked 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3
D 278097 Armcx6; armadillo repeat containing, X-linked 6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6
D 66112 Mtarc1; mitochondrial amidoxime reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 67247 Mtarc2; mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 30056 Timm9; translocase of inner mitochondrial membrane 9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 30059 Timm10; translocase of inner mitochondrial membrane 10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 14356 Timm10b; translocase of inner mitochondrial membrane 10B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 30058 Timm8a1; translocase of inner mitochondrial membrane 8A1 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 30057 Timm8b; translocase of inner mitochondrial membrane 8B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 223262 Timm8a2; translocase of inner mitochondrial membrane 8A2 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 30055 Timm13; translocase of inner mitochondrial membrane 13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 72170 Chchd4; coiled-coil-helix-coiled-coil-helix domain containing 4 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 11692 Gfer; growth factor, augmenter of liver regeneration K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 433771 Micos10; mitochondrial contact site and cristae organizing system subunit 10 K17784 MICOS10; MICOS complex subunit MIC10
D 76614 Immt; inner membrane protein, mitochondrial K17785 IMMT; MICOS complex subunit MIC60
D 224904 Micos13; mitochondrial contact site and cristae organizing system subunit 13 K24624 MICOS13; MICOS complex subunit MIC13
D 66075 Chchd3; coiled-coil-helix-coiled-coil-helix domain containing 3 K17563 CHCHD3; MICOS complex subunit MIC19
D 66098 Chchd6; coiled-coil-helix-coiled-coil-helix domain containing 6 K17564 CHCHD6; MICOS complex subunit MIC25
D 68316 Apoo; apolipoprotein O K24625 APOO; MICOS complex subunit MIC26
D 68117 Apool; apolipoprotein O-like K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 433771 Micos10; mitochondrial contact site and cristae organizing system subunit 10 K17784 MICOS10; MICOS complex subunit MIC10
D 76614 Immt; inner membrane protein, mitochondrial K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 56322 Timm22; translocase of inner mitochondrial membrane 22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 53600 Timm23; translocase of inner mitochondrial membrane 23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 21854 Timm17a; translocase of inner mitochondrial membrane 17a K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 21855 Timm17b; translocase of inner mitochondrial membrane 17b K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 67105 Timm21; translocase of inner mitochondrial membrane 21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 66525 Timm50; translocase of inner mitochondrial membrane 50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 215999 Mcu; mitochondrial calcium uniporter K20858 MCU; calcium uniporter protein, mitochondrial
D 216001 Micu1; mitochondrial calcium uptake 1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 68514 Micu2; mitochondrial calcium uptake 2 K22828 MICU2; calcium uptake protein 2, mitochondrial
D 66815 Mcub; mitochondrial calcium uniporter dominant negative beta subunit K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 69029 Smdt1; single-pass membrane protein with aspartate rich tail 1 K22830 SMDT1; essential MCU regulator, mitochondrial
D 76137 Mcur1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 56384 Letm1; leucine zipper-EF-hand containing transmembrane protein 1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 66541 Immp1l; IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 93757 Immp2l; IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 66271 Tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 667103 Gm13570; predicted gene 13570 K22138 MPC1; mitochondrial pyruvate carrier 1
D 245347 Gm4984; predicted pseudogene 4984 K22138 MPC1; mitochondrial pyruvate carrier 1
D 55951 Mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 70456 Mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2
D 103172 Chchd10; coiled-coil-helix-coiled-coil-helix domain containing 10 K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 21856 Timm44; translocase of inner mitochondrial membrane 44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 15526 Hspa9; heat shock protein 9 K04043 dnaK; molecular chaperone DnaK
D 17713 Grpel1; GrpE-like 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 17714 Grpel2; GrpE-like 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 67713 Dnajc19; DnaJ heat shock protein family (Hsp40) member C19 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 66449 Pam16; presequence translocase-asssociated motor 16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 66865 Pmpca; peptidase (mitochondrial processing) alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 73078 Pmpcb; peptidase (mitochondrial processing) beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 70478 Mipep; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 15510 Hspd1; heat shock protein 1 (chaperonin) K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 15528 Hspe1; heat shock protein 1 (chaperonin 10) K04078 groES; chaperonin GroES
D 623924 Gm6462; predicted gene 6462 K04078 groES; chaperonin GroES
D 83945 Dnaja3; DnaJ heat shock protein family (Hsp40) member A3 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 68971 Tamm41; TAM41 mitochondrial translocator assembly and maintenance homolog K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 52838 Dnlz; DNL-type zinc finger K17808 ZIM17; mitochondrial protein import protein ZIM17
D 66071 Ethe1; ethylmalonic encephalopathy 1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 67811 Poldip2; polymerase (DNA-directed), delta interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 12912 Creb1; cAMP responsive element binding protein 1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 28030 Gfm1; G elongation factor, mitochondrial 1 K02355 fusA; elongation factor G
D 320806 Gfm2; G elongation factor, mitochondrial 2 K02355 fusA; elongation factor G
D 20683 Sp1; trans-acting transcription factor 1 K04684 SP1; transcription factor Sp1
D 22632 Yy1; YY1 transcription factor K09201 YY; transcription factor YY
D 100073351 Yy2; Yy2 transcription factor K09201 YY; transcription factor YY
D 14391 Gabpb1; GA repeat binding protein, beta 1 K09454 GABPB; GA-binding protein transcription factor, beta
D 213054 Gabpb2; GA repeat binding protein, beta 2 K09454 GABPB; GA-binding protein transcription factor, beta
D 21780 Tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 18181 Nrf1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1
D 18024 Nfe2l2; nuclear factor, erythroid derived 2, like 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 17750 Mt2; metallothionein 2 K14739 MT1_2; metallothionein 1/2
D 17748 Mt1; metallothionein 1 K14739 MT1_2; metallothionein 1/2
D 17751 Mt3; metallothionein 3 K14740 MT3; metallothionein 3
D 17752 Mt4; metallothionein 4 K14741 MT4; metallothionein 4
C Coactivators
D 19017 Ppargc1a; peroxisome proliferative activated receptor, gamma, coactivator 1 alpha K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 170826 Ppargc1b; peroxisome proliferative activated receptor, gamma, coactivator 1 beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 226169 Pprc1; peroxisome proliferative activated receptor, gamma, coactivator-related 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 382056 Crtc1; CREB regulated transcription coactivator 1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 12914 Crebbp; CREB binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 328572 Ep300; E1A binding protein p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 18041 Nfs1; nitrogen fixation gene 1 (S. cerevisiae) K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 66383 Iscu; iron-sulfur cluster assembly enzyme K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 380840 Lyrm4; LYR motif containing 4 K22069 LYRM4; LYR motif-containing protein 4
D 14297 Fxn; frataxin K19054 FXN; frataxin [EC:1.16.3.1]
D 14148 Fdx1; ferredoxin 1 K22070 FDX1; ferredoxin-1, mitochondrial
D 68165 Fdx2; ferredoxin 2 K22071 FDX2; ferredoxin-2, mitochondrial
D 14149 Fdxr; ferredoxin reductase K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 15526 Hspa9; heat shock protein 9 K04043 dnaK; molecular chaperone DnaK
D 100900 Hscb; HscB iron-sulfur cluster co-chaperone K04082 hscB; molecular chaperone HscB
D 81500 Sil1; SIL1 nucleotide exchange factor K14001 SIL1; nucleotide exchange factor SIL1
D 73046 Glrx5; glutaredoxin 5 K07390 grxD; monothiol glutaredoxin
D 69046 Isca1; iron-sulfur cluster assembly 1 K22063 ISCA1; iron-sulfur cluster assembly 1
D 74316 Isca2; iron-sulfur cluster assembly 2 K22072 ISCA2; iron-sulfur cluster assembly 2
D 216792 Iba57; IBA57 homolog, iron-sulfur cluster assembly K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 56748 Nfu1; NFU1 iron-sulfur cluster scaffold K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 69168 Bola1; bolA family member 1 K22066 BOLA1; BolA-like protein 1
D 78653 Bola3; bolA family member 3 K22075 BOLA3; BolA-like protein 3
D 14057 Sfxn1; sideroflexin 1 K23500 SFXN1_3; sideroflexin-1/3
D 94280 Sfxn3; sideroflexin 3 K23500 SFXN1_3; sideroflexin-1/3
D 94279 Sfxn2; sideroflexin 2 K23501 SFXN2; sideroflexin-2
D 94281 Sfxn4; sideroflexin 4 K23502 SFXN4; sideroflexin-4
D 94282 Sfxn5; sideroflexin 5 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 12894 Cpt1a; carnitine palmitoyltransferase 1a, liver K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 12895 Cpt1b; carnitine palmitoyltransferase 1b, muscle K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 78070 Cpt1c; carnitine palmitoyltransferase 1c K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
D 209692 Dhtkd1; dehydrogenase E1 and transketolase domain containing 1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 269514 Fbxl4; F-box and leucine-rich repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 15161 Hcfc1; host cell factor C1 K14966 HCFC1; host cell factor 1
D 67933 Hcfc2; host cell factor C2 K27390 HCFC2; host cell factor 2
D 15194 Htt; huntingtin K04533 HD; huntingtin
D 26379 Esrra; estrogen related receptor, alpha K08552 NR3B1; estrogen-related receptor alpha
D 26380 Esrrb; estrogen related receptor, beta K08553 NR3B2; estrogen-related receptor beta
D 26381 Esrrg; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma
D 268903 Nrip1; nuclear receptor interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 105787 Prkaa1; protein kinase, AMP-activated, alpha 1 catalytic subunit K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108079 Prkaa2; protein kinase, AMP-activated, alpha 2 catalytic subunit K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 74142 Lonp1; lon peptidase 1, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 93759 Sirt1; sirtuin 1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 321007 Serac1; serine active site containing 1 K23504 SERAC1; protein SERAC1
D 22294 Uxt; ubiquitously expressed prefoldin like chaperone K26537 UXT; protein UXT
D 74183 Perm1; PPARGC1 and ESRR induced regulator, muscle 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 69702 Ndufaf1; NADH:ubiquinone oxidoreductase complex assembly factor 1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 75597 Ndufaf2; NADH:ubiquinone oxidoreductase complex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 66706 Ndufaf3; NADH:ubiquinone oxidoreductase complex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 68493 Ndufaf4; NADH:ubiquinone oxidoreductase complex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 69487 Ndufaf5; NADH:ubiquinone oxidoreductase complex assembly factor 5 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 76947 Ndufaf6; NADH:ubiquinone oxidoreductase complex assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 73694 Ndufaf7; NADH:ubiquinone oxidoreductase complex assembly factor 7 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 208501 Ndufaf8; NADH:ubiquinone oxidoreductase complex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 68472 Tmem126b; transmembrane protein 126B K18165 TMEM126B; complex I assembly factor TMEM126B
D 26940 Ecsit; ECSIT signalling integrator K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 229211 Acad9; acyl-Coenzyme A dehydrogenase family, member 9 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 76826 Nubpl; nucleotide binding protein-like K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 235169 Foxred1; FAD-dependent oxidoreductase domain containing 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 170728 Rtn4ip1; reticulon 4 interacting protein 1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 76916 Timmdc1; translocase of inner mitochondrial membrane domain containing 1 K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 68332 Sdhaf1; succinate dehydrogenase complex assembly factor 1 K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 66072 Sdhaf2; succinate dehydrogenase complex assembly factor 2 K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 66821 Bcs1l; BCS1 homolog, ubiquinol-cytochrome c reductase complex chaperone K08900 BCS1; mitochondrial chaperone BCS1
D 72795 Ttc19; tetratricopeptide repeat domain 19 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 75530 Lyrm7; LYR motif containing 7 K18170 LYRM7; complex III assembly factor LYRM7
D 56046 Uqcc1; ubiquinol-cytochrome c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 67267 Uqcc2; ubiquinol-cytochrome c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 107197 Uqcc3; ubiquinol-cytochrome c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 214489 Uqcc4; ubiquinol-cytochrome c reductase complex assembly factor 4 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 66487 Uqcc5; ubiquinol-cytochrome c reductase complex assembly factor 5 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 544717 Uqcc6; ubiquinol-cytochrome c reductase complex assembly factor 6 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 67705 Stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 67899 Cmc1; C-X9-C motif containing 1 K18171 CMC1; COX assembly mitochondrial protein 1
D 66531 Cmc2; C-X9-C motif containing 2 K18172 CMC2; COX assembly mitochondrial protein 2
D 52469 Coa3; cytochrome C oxidase assembly factor 3 K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 68185 Coa4; cytochrome c oxidase assembly factor 4 K18177 COA4; cytochrome c oxidase assembly factor 4
D 76178 Coa5; cytochrome C oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 67892 Coa6; cytochrome c oxidase assembly factor 6 K18179 COA6; cytochrome c oxidase assembly factor 6
D 69893 Coa7; cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 70383 Cox10; heme A:farnesyltransferase cytochrome c oxidase assembly factor 10 K02257 COX10; heme o synthase [EC:2.5.1.141]
D 69802 Cox11; cytochrome c oxidase assembly protein 11, copper chaperone K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 101055854 Gm29733; predicted gene, 29733 K18181 COX14; cytochrome c oxidase assembly factor 14
D 66379 Cox14; cytochrome c oxidase assembly protein 14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 226139 Cox15; cytochrome c oxidase assembly protein 15 K02259 COX15; heme a synthase [EC:1.17.99.9]
D 66272 Cox16; cytochrome c oxidase assembly protein 16 K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 12856 Cox17; cytochrome c oxidase assembly protein 17, copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 231430 Cox18; cytochrome c oxidase assembly protein 18 K17797 COX18; mitochondrial inner membrane protein COX18
D 68033 Cox19; cytochrome c oxidase assembly protein 19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 66359 Cox20; cytochrome c oxidase assembly protein 20 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 74843 Mss51; MSS51 mitochondrial translational activator K17656 MSS51; mitochondrial splicing suppressor protein 51
D 100503890 Pet100; PET100 homolog K18186 PET100; protein PET100, animal type
D 100048644 Pet117; PET117 homolog K18188 PET117; protein PET117
D 69089 Oxa1l; oxidase assembly 1-like K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 20930 Surf1; surfeit gene 1 K14998 SURF1; surfeit locus 1 family protein
D 52892 Sco1; SCO1 cytochrome c oxidase assembly protein K07152 SCO1; protein SCO1
D 100126824 Sco2; SCO2 cytochrome c oxidase assembly protein K23755 SCO2; protein SCO2
D 70207 Taco1; translational activator of mitochondrially encoded cytochrome c oxidase I K18189 TACO1; translational activator of cytochrome c oxidase 1
D 72416 Lrpprc; leucine-rich PPR-motif containing K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 68020 Coa8; cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1
D 67705 Stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 66487 Uqcc5; ubiquinol-cytochrome c reductase complex assembly factor 5 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 66836 Tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 230649 Atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 246782 Atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 70397 Tmem70; transmembrane protein 70 K17966 TMEM70; transmembrane protein 70, mitochondrial
D 115487466 Gm48175; predicted gene, 48175 K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 70257 Atp5mj; ATP synthase membrane subunit j K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 102635650 Gm32936; predicted gene, 32936 K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 66477 Atp5mk; ATP synthase membrane subunit k K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 102639577 Gm35857; predicted gene, 35857 K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 67414 Mfn1; mitofusin 1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 170731 Mfn2; mitofusin 2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 74143 Opa1; OPA1, mitochondrial dynamin like GTPase K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 403187 Opa3; optic atrophy 3 K23166 OPA3; optic atrophy 3 protein
D 102637572 Gm38499; predicted gene, 38499 K23166 OPA3; optic atrophy 3 protein
D 69076 Triap1; TP53 regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 381038 Parl; presenilin associated, rhomboid-like K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 12018 Bak1; BCL2-antagonist/killer 1 K14021 BAK; Bcl-2 homologous antagonist/killer
D 12028 Bax; BCL2-associated X protein K02159 BAX; apoptosis regulator BAX
D 74006 Dnm1l; dynamin 1-like K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 66437 Fis1; fission, mitochondrial 1 K17969 FIS1; mitochondrial fission 1 protein
D 170930 Sumo2; small ubiquitin-like modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 20610 Sumo3; small ubiquitin-like modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 22218 Sumo1; small ubiquitin-like modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 102640040 Gm11971; predicted gene 11971 K12160 SUMO; small ubiquitin-related modifier
D 54673 Sh3glb1; SH3-domain GRB2-like B1 (endophilin) K11248 SH3GLB1; endophilin-B1
D 56428 Mtch2; mitochondrial carrier 2 K17885 MTCH; mitochondrial carrier
D 56462 Mtch1; mitochondrial carrier 1 K17885 MTCH; mitochondrial carrier
D 75734 Mff; mitochondrial fission factor K22076 MFF; mitochondrial fission factor
D 14545 Gdap1; ganglioside-induced differentiation-associated-protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 228858 Gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 26949 Vat1; vesicle amine transport 1 K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 237781 Mief2; mitochondrial elongation factor 2 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 239555 Mief1; mitochondrial elongation factor 1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 194908 Pld6; phospholipase D family member 6 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 108958 Miga2; mitoguardin 2 K27289 MIGA; mitoguardin
D 215708 Miga1; mitoguardin 1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 11465 Actg1; actin, gamma, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 11461 Actb; actin, beta K05692 ACTB_G1; actin beta/gamma 1
D 67877 Naa20; N(alpha)-acetyltransferase 20, NatB catalytic subunit K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 231713 Naa25; N(alpha)-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 18673 Phb1; prohibitin 1 K17080 PHB1; prohibitin 1
D 237880 1700071K01Rik; RIKEN cDNA 1700071K01 gene K17080 PHB1; prohibitin 1
D 12034 Phb2; prohibitin 2 K17081 PHB2; prohibitin 2
D 16709 Ktn1; kinectin 1 K17975 KTN1; kinectin
C Retention of mitochondria
D 74006 Dnm1l; dynamin 1-like K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 17918 Myo5a; myosin VA K10357 MYO5; myosin V
D 17919 Myo5b; myosin VB K10357 MYO5; myosin V
D 208943 Myo5c; myosin VC K10357 MYO5; myosin V
D 11798 Xiap; X-linked inhibitor of apoptosis K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 66593 Diablo; diablo, IAP-binding mitochondrial protein K10522 DIABLO; diablo
C Morphogenesis factors
D 102141 Snx25; sorting nexin 25 K17887 SNX25; sorting nexin-25
D 59040 Rhot1; ras homolog family member T1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 76614 Immt; inner membrane protein, mitochondrial K17785 IMMT; MICOS complex subunit MIC60
D 67900 Mtfp1; mitochondrial fission process 1 K17981 MTFP1; mitochondrial fission process protein 1
D 65111 Dap3; death associated protein 3 K17408 DAP3; small subunit ribosomal protein S29
D 17999 Nedd4; neural precursor cell expressed, developmentally down-regulated 4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 170719 Oxr1; oxidation resistance 1 K25437 OXR1; oxidation resistance protein 1
D 229524 Msto1; misato 1, mitochondrial distribution and morphology regulator K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 329015 Atg2a; autophagy related 2A K17906 ATG2; autophagy-related protein 2
D 76559 Atg2b; autophagy related 2B K17906 ATG2; autophagy-related protein 2
D 67841 Atg3; autophagy related 3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 66615 Atg4b; autophagy related 4B, cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 235040 Atg4d; autophagy related 4D, cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 242557 Atg4c; autophagy related 4C, cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 666468 Atg4a; autophagy related 4A, cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 11793 Atg5; autophagy related 5 K08339 ATG5; autophagy-related protein 5
D 56208 Becn1; beclin 1, autophagy related K08334 BECN; beclin
D 74244 Atg7; autophagy related 7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 57436 Gabarapl1; GABA type A receptor associated protein like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 56486 Gabarap; gamma-aminobutyric acid receptor associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 93739 Gabarapl2; GABA type A receptor associated protein like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 213948 Atg9b; autophagy related 9B K17907 ATG9; autophagy-related protein 9
D 245860 Atg9a; autophagy related 9A K17907 ATG9; autophagy-related protein 9
D 66795 Atg10; autophagy related 10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 67526 Atg12; autophagy related 12 K08336 ATG12; ubiquitin-like protein ATG12
D 100504663 Atg14; autophagy related 14 K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 77040 Atg16l1; autophagy related 16 like 1 K17890 ATG16L1; autophagy-related protein 16-1
D 73683 Atg16l2; autophagy related 16 like 2 K20868 ATG16L2; autophagy-related protein 16-2
D 52639 Wipi1; WD repeat domain, phosphoinositide interacting 1 K17908 WIPI1_2; autophagy-related protein 18
D 74781 Wipi2; WD repeat domain, phosphoinositide interacting 2 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 50873 Prkn; parkin RBR E3 ubiquitin protein ligase K04556 PARK2; parkin [EC:2.3.2.31]
D 67588 Rnf41; ring finger protein 41 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 74374 Clec16a; C-type lectin domain family 16, member A K19513 CLEC16A; protein CLEC16A
D 68943 Pink1; PTEN induced putative kinase 1 K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 381038 Parl; presenilin associated, rhomboid-like K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 18412 Sqstm1; sequestosome 1 K14381 SQSTM1; sequestosome 1
D 52440 Tax1bp1; Tax1 (human T cell leukemia virus type I) binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1
D 76815 Calcoco2; calcium binding and coiled-coil domain 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 228361 Ambra1; autophagy/beclin 1 regulator 1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 51897 Atg13; autophagy related 13 K08331 ATG13; autophagy-related protein 13
D 22241 Ulk1; unc-51 like kinase 1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 29869 Ulk2; unc-51 like kinase 2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 12421 Rb1cc1; RB1-inducible coiled-coil 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 15519 Hsp90aa1; heat shock protein 90, alpha (cytosolic), class A member 1 K04079 HSP90A; molecular chaperone HtpG
D 15516 Hsp90ab1; heat shock protein 90 alpha (cytosolic), class B member 1 K04079 HSP90A; molecular chaperone HtpG
D 12539 Cdc37; cell division cycle 37 K09554 CDC37; cell division cycle protein 37
D 66313 Smurf2; SMAD specific E3 ubiquitin protein ligase 2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 75788 Smurf1; SMAD specific E3 ubiquitin protein ligase 1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 12177 Bnip3l; BCL2/adenovirus E1B interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 100043324 Bnip3l-ps; BCL2/adenovirus E1B interacting protein 3-like, pseudogene K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 72018 Fundc1; FUN14 domain containing 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 105787 Prkaa1; protein kinase, AMP-activated, alpha 1 catalytic subunit K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108079 Prkaa2; protein kinase, AMP-activated, alpha 2 catalytic subunit K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 66734 Map1lc3a; microtubule-associated protein 1 light chain 3 alpha K10435 MAP1LC; microtubule-associated protein 1 light chain
D 67443 Map1lc3b; microtubule-associated protein 1 light chain 3 beta K10435 MAP1LC; microtubule-associated protein 1 light chain
D 17966 Nbr1; NBR1, autophagy cargo receptor K17987 NBR1; next to BRCA1 gene 1 protein
D 70381 Tecpr1; tectonin beta-propeller repeat containing 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 217695 Zfyve1; zinc finger, FYVE domain containing 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 71743 Coasy; Coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 53357 Pla2g6; phospholipase A2, group VI K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 72244 1600014C10Rik; RIKEN cDNA 1600014C10 gene K23168 MPAN; protein MPAN
D 67391 Fundc2; FUN14 domain containing 2 K24308 FUNDC2; FUN14 domain-containing protein 2
D 73297 Fundc2b; FUN14 domain containing 2B K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024