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Mitochondrial Biogenesis - Rattus norvegicus (rat)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 26193 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 26194 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 26199 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 26201 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 26200 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 26202 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 26203 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 26192 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 26195 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 26198 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 26204 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 26196 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 26197 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 299604 Polrmt; DNA-directed RNA polymerase, mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 83474 Tfam; transcription factor A, mitochondrial precursor K11830 TFAM; transcription factor A, mitochondrial
D 308140 Tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 289307 Tfb2m; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 305606 Mtif2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 684274 Mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 679068 Tsfm; elongation factor Ts, mitochondrial precursor K02357 tsf; elongation factor Ts
D 293481 Tufm; elongation factor Tu, mitochondrial precursor K02358 tuf; elongation factor Tu
D 114017 Gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 294672 Gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 366856 Mterf2; transcription termination factor 2, mitochondrial precursor K15031 MTERF; mitochondrial transcription termination factor family protein
D 85261 Mterf1; transcription termination factor 1, mitochondrial precursor K15031 MTERF; mitochondrial transcription termination factor family protein
D 299514 Mterf3; transcription termination factor 3, mitochondrial precursor K15031 MTERF; mitochondrial transcription termination factor family protein
D 363289 Mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 305317 Guf1; translation factor GUF1, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 315045 Pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 292831 Pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 117241 Pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 685332 Rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 288564 Pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 298002 Rpp25l; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 315705 Rpp25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 291317 Rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 291071 Rpp40; ribonuclease P protein subunit p40 isoform 1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 304012 Trmt10c; tRNA methyltransferase 10 homolog C precursor K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 63864 Hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 299050 Prorp; mitochondrial ribonuclease P catalytic subunit precursor K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 289904 Mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 287554 Tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 304278 Ptcd1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 310025 Ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 500199 Ptcd3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 367172 Dhx30; ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 683512 Uqcc1; ubiquinol-cytochrome c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 502479 Afg1l; AFG1-like ATPase K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 299828 Atp23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 294385 Supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial precursor K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 297768 Lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 25176 Slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 85333 Slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 689108 Slc25a31; ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 498885 Slc25a6; solute carrier family 25 member 6 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 500871 Slc25a5l1; ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 306000 Slc25a37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 688811 Slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 297082 Malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 363646 Eral1; GTPase Era, mitochondrial isoform 2 K03595 era; GTPase
D 287924 Yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 313047 Yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 363172 Lars2; leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 291624 Lars1; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 304919 Dars2; aspartate--tRNA ligase, mitochondrial precursor K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 297113 Gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 287191 Rars1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 297969 Rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 309911 Qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 361974 Gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 360821 Gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 306231 Pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 100910751 Mtg1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1
D 289562 Noa1; nitric oxide-associated protein 1 isoform 2 K19832 NOA1; nitric oxide-associated protein 1
D 100360437 Nsun3; NOP2/Sun RNA methyltransferase 3 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 298426 Nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 362416 Rpusd3; mitochondrial mRNA pseudouridine synthase RPUSD3 isoform 2 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 315550 Rpusd4; pseudouridylate synthase RPUSD4, mitochondrial K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 360796 Rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 499191 Ngrn; neugrin precursor K23496 NGRN; neugrin
D 366012 Trub2; pseudouridylate synthase TRUB2, mitochondrial K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 301463 Fastkd2; FAST kinase domain-containing protein 2, mitochondrial isoform 1 K18190 FASTKD2; FAST kinase domain-containing protein 2
D 498179 Mtrfr; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 292268 Rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 305256 Grsf1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1
D 295985 Mettl15; 12S rRNA N4-methylcytidine (m4C) methyltransferase K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 300258 Myg1; MYG1 exonuclease precursor K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 683897 Mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 85472 Polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 303612 Polg2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 361147 Primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 362100 Endog; endonuclease G, mitochondrial precursor K01173 ENDOG; endonuclease G, mitochondrial
D 296200 Mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 301062 Exog; nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial
D 309441 Twnk; twinkle mtDNA helicase K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 367645 Pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 54304 Ssbp1; single-stranded DNA-binding protein, mitochondrial precursor K03111 ssb; single-strand DNA-binding protein
D 298682 Atad3a; ATPase family AAA domain-containing protein 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 361805 Uqcc2; ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 84026 Dnaja2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 311621 Tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 303351 Rhot1; mitochondrial Rho GTPase 1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 24468 Hspa8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 24472 Hspa1a; heat shock 70 kDa protein 1A K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 24963 Hspa1l; heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 680121 Haus8l2; heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 108348108 Hspa1b; heat shock 70 kDa protein 1B K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 282827 Aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
D 59110 Aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 308416 Tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 304971 Tomm40l; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 304017 Tomm70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 300075 Tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 266601 Tomm20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 689996 Tomm20l; TOMM20-like protein 1 isoform X1 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 685620 Tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 681123 Tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 680080 Tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 300111 Samm50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 83529 Vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 83531 Vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 83532 Vdac3; voltage-dependent anion-selective channel protein 3 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 295241 Mtx1; metaxin-1 isoform 2 K17776 MTX; metaxin
D 688905 Mtx3; metaxin-3 isoform X1 K17776 MTX; metaxin
D 288150 Mtx2; metaxin-2 K17776 MTX; metaxin
D 497974 Myo19; unconventional myosin-XIX K25838 MYO19; myosin XIX
D 501619 Armcx1; armadillo repeat-containing X-linked protein 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1
D 367903 Armcx2; armadillo repeat-containing X-linked protein 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2
D 367902 Armcx3; armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3
D 363496 Armcx6; protein ARMCX6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6
D 690745 Mtarc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 171451 Mtarc2; mitochondrial amidoxime reducing component 2 precursor K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 171139 Timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 64464 Timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 84384 Timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 84383 Timm8a1; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 64372 Timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 680794 Timm8a2; translocase of inner mitochondrial membrane 8A2 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 252928 Timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 312559 Chchd4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 120094797 mitochondrial intermembrane space import and assembly protein 40-like K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 27100 Gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 100361944 Micos10l1; MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 362641 Micos10; MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10
D 312444 Immt; MICOS complex subunit Mic60 K17785 IMMT; MICOS complex subunit MIC60
D 120102271 MICOS complex subunit MIC13-like K24624 MICOS13; MICOS complex subunit MIC13
D 296966 Chchd3; MICOS complex subunit MIC19 K17563 CHCHD3; MICOS complex subunit MIC19
D 297436 Chchd6; MICOS complex subunit Mic25 K17564 CHCHD6; MICOS complex subunit MIC25
D 363474 Apoo; MICOS complex subunit MIC26 K24625 APOO; MICOS complex subunit MIC26
D 317191 Apool; MICOS complex subunit MIC27 isoform 2 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 100361944 Micos10l1; MICOS complex subunit Mic10-like K17784 MICOS10; MICOS complex subunit MIC10
D 362641 Micos10; MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10
D 312444 Immt; MICOS complex subunit Mic60 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 79463 Timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 54312 Timm23; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 317374 Timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 54311 Timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 307210 Timm21; mitochondrial import inner membrane translocase subunit Tim21 precursor K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 687295 Timm50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 294560 Mcu; calcium uniporter protein, mitochondrial precursor K20858 MCU; calcium uniporter protein, mitochondrial
D 365567 Micu1; calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial
D 171433 Micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 295462 Mcub; calcium uniporter regulatory subunit MCUb, mitochondrial K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 315166 Smdt1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial
D 134483672 essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial
D 291034 Mcur1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 305457 Letm1; mitochondrial proton/calcium exchanger protein precursor K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 691145 Immp1l; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 100359529 Immp2l; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 293113 Tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 503429 Mpc1l; mitochondrial pyruvate carrier 1-like protein K22138 MPC1; mitochondrial pyruvate carrier 1
D 171087 Mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 100359982 Mpc2; mitochondrial pyruvate carrier 2 isoform 1 K22139 MPC2; mitochondrial pyruvate carrier 2
D 361824 Chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 29635 Timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 291671 Hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 79563 Grpel1; grpE protein homolog 1, mitochondrial precursor K03687 GRPE; molecular chaperone GrpE
D 688777 Grpel2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 502525 Dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 679907 Pam16; mitochondrial import inner membrane translocase subunit TIM16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 296588 Pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 64198 Pmpcb; mitochondrial-processing peptidase subunit beta precursor K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 81684 Mipep; mitochondrial intermediate peptidase precursor K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 63868 Hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 103694176 Hspd1l1; 60 kDa heat shock protein, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 25462 Hspe1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 360481 Dnaja3; dnaJ homolog subfamily A member 3, mitochondrial isoform 1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 362419 Tamm41; phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 296587 Dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 292710 Ethe1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 81646 Creb1; cyclic AMP-responsive element-binding protein 1 isoform A K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 114017 Gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 294672 Gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 24790 Sp1; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 24919 Yy1; transcriptional repressor protein YY1 K09201 YY; transcription factor YY
D 103690827 Yy2; transcription factor YY2 K09201 YY; transcription factor YY
D 499883 Gabpb1; GA-binding protein subunit beta-1 isoform 1 K09454 GABPB; GA-binding protein transcription factor, beta
D 295263 Gabpb2; GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta
D 364738 Gabpb1l; GA-binding protein subunit beta-1 K09454 GABPB; GA-binding protein transcription factor, beta
D 83474 Tfam; transcription factor A, mitochondrial precursor K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 312195 Nrf1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1
D 83619 Nfe2l2; nuclear factor erythroid 2-related factor 2 isoform 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 689415 Mt2A; metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 24567 Mt1; metallothionein-1 K14739 MT1_2; metallothionein 1/2
D 117038 Mt3; metallothionein-3 K14740 MT3; metallothionein 3
D 498911 Mt4; metallothionein-4 K14741 MT4; metallothionein 4
C Coactivators
D 83516 Ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 291567 Ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 294007 Pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 684527 Crtc1; CREB-regulated transcription coactivator 1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 54244 Crebbp; histone lysine acetyltransferase CREBBP K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 170915 Ep300; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 84594 Nfs1; cysteine desulfurase K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 288740 Iscu; iron-sulfur cluster assembly enzyme ISCU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 102550385 Lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 499335 Fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 29189 Fdx1; adrenodoxin, mitochondrial precursor K22070 FDX1; ferredoxin-1, mitochondrial
D 313786 Fdx2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 79122 Fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial precursor K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 291671 Hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 360826 Hscb; iron-sulfur cluster co-chaperone protein HscB precursor K04082 hscB; molecular chaperone HscB
D 291673 Sil1; nucleotide exchange factor SIL1 precursor K14001 SIL1; nucleotide exchange factor SIL1
D 362776 Glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 290985 Isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial precursor K22063 ISCA1; iron-sulfur cluster assembly 1
D 500694 Isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial precursor K22072 ISCA2; iron-sulfur cluster assembly 2
D 363611 Iba57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 297416 Nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial precursor K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 365875 Bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 297388 Bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 364678 Sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 65042 Sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 361778 Sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4
D 261737 Sfxn5; sideroflexin-5 K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 25757 Cpt1a; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 25756 Cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 308579 Cpt1c; palmitoyl thioesterase CPT1C K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
D 361272 Dhtkd1; 2-oxoadipate dehydrogenase complex component E1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 363519 Hcfc1; host cell factor 1 K14966 HCFC1; host cell factor 1
D 314704 Hcfc2; host cell factor 2 K27390 HCFC2; host cell factor 2
D 29424 Htt; huntingtin K04533 HD; huntingtin
D 293701 Esrra; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 299210 Esrrb; steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta
D 360896 Esrrg; estrogen-related receptor gamma isoform 2 K08554 NR3B3; estrogen-related receptor gamma
D 304157 Nrip1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 65248 Prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 78975 Prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 170916 Lonp1; lon protease homolog, mitochondrial precursor K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 309757 Sirt1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 499015 Serac1; protein SERAC1 K23504 SERAC1; protein SERAC1
D 299313 Uxt; protein UXT K26537 UXT; protein UXT
D 313776 Perm1; PGC-1 and ERR-induced regulator in muscle protein 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 296086 Ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 361894 Ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 56769 Ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 isoform a K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 362495 Ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 296190 Ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial precursor K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 297821 Ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 precursor K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 298748 Ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial precursor K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 690871 Ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 293114 Tmem126b; complex I assembly factor TMEM126B, mitochondrial K18165 TMEM126B; complex I assembly factor TMEM126B
D 300447 Ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial precursor K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 294973 Acad9; complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 299008 Nubpl; iron-sulfur protein NUBPL precursor K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 309912 Rtn4ip1; reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 303922 Timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 499125 Sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 361726 Sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial precursor K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 301514 Bcs1l; mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 691506 Ttc19; tetratricopeptide repeat protein 19, mitochondrial isoform 2 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 686506 Lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 683512 Uqcc1; ubiquinol-cytochrome c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 361805 Uqcc2; ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 690344 Uqcc3; uncharacterized protein LOC690344 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 120093241 ubiquinol-cytochrome-c reductase complex assembly factor 3-like K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 497874 Uqcc4; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 361111 Uqcc5; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 691921 Uqcc6; protein BRAWNIN precursor K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 689574 Stmp1; short transmembrane mitochondrial protein 1 isoform 1 precursor K27319 STMP1; short transmembrane mitochondrial protein 1
D 102547542 Stmp1l1; short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 100363376 Cmc2; COX assembly mitochondrial protein 2 homolog isoform 1 K18172 CMC2; COX assembly mitochondrial protein 2
D 498000 Coa3; coiled-coil domain-containing protein 56 K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 499214 Coa4; coiled-coil-helix-coiled-coil-helix domain-containing protein 8 K18177 COA4; cytochrome c oxidase assembly factor 4
D 503252 Coa5; uncharacterized protein LOC503252 K18178 COA5; cytochrome c oxidase assembly factor 5
D 102556031 Coa6; cytochrome c oxidase assembly factor 6 K18179 COA6; cytochrome c oxidase assembly factor 6
D 298377 Coa7; sel1 repeat-containing protein 1 K18180 COA7; cytochrome c oxidase assembly factor 7
D 691853 Cox10; cytochrome c oxidase assembly factor heme A:farnesyltransferase COX10 K02257 COX10; heme o synthase [EC:2.5.1.141]
D 103693419 Cox11; cytochrome c oxidase copper chaperone COX11 K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 681219 Cox14; cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14
D 309391 Cox15; COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 100302447 Cox16; COX16 cytochrome c oxidase assembly homolog K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 89786 Cox17; COX17 homolog, cytochrome c oxidase assembly protein K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 289522 Cox18; mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18
D 304330 Cox19; COX19 cytochrome c oxidase assembly homolog K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 289278 Cox20; cytochrome c oxidase assembly factor COX20 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 289904 Mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 688786 Pet100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 691393 Oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 64463 Surf1; surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 497930 Sco1; SCO cytochrome oxidase deficient homolog 1 K07152 SCO1; protein SCO1
D 360645 Taco1; translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 313867 Lrpprc; leucine-rich PPR motif-containing protein, mitochondrial precursor K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 299341 Coa8; cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1
D 689574 Stmp1; short transmembrane mitochondrial protein 1 isoform 1 precursor K27319 STMP1; short transmembrane mitochondrial protein 1
D 102547542 Stmp1l1; short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1
D 361111 Uqcc5; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 690285 Tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 313510 Atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 303190 Atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 500384 Tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 171069 Atp5mk; ATP synthase membrane subunit K, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 103693330 Atp5mkl1; ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 120094339 ATP synthase membrane subunit K, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 192647 Mfn1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 64476 Mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 171116 Opa1; dynamin-like 120 kDa protein, mitochondrial precursor K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 308409 Opa3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein
D 691278 Triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 287979 Parl; presenilin-associated rhomboid-like protein, mitochondrial precursor K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 116502 Bak1; bcl-2 homologous antagonist/killer K14021 BAK; Bcl-2 homologous antagonist/killer
D 24887 Bax; apoptosis regulator BAX K02159 BAX; apoptosis regulator BAX
D 367149 Bax-ps1; apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 681314 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 114114 Dnm1l; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 288584 Fis1; mitochondrial fission 1 protein isoform 1 K17969 FIS1; mitochondrial fission 1 protein
D 499417 Sumo3; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 690244 Sumo2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 301442 Sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 120102380 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier
D 108351070 Sumo2l1; small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 120095693 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier
D 292156 Sh3glb1; endophilin-B1 K11248 SH3GLB1; endophilin-B1
D 294313 Mtch1; mitochondrial carrier homolog 1 K17885 MTCH; mitochondrial carrier
D 295922 Mtch2; mitochondrial carrier homolog 2 isoform 1 K17885 MTCH; mitochondrial carrier
D 301563 Mff; mitochondrial fission factor isoform 2 K22076 MFF; mitochondrial fission factor
D 311616 Gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 312890 Gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 287721 Vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 315141 Mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 497916 Mief2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 362058 Miga1; mitoguardin 1 isoform X1 K27289 MIGA; mitoguardin
D 296623 Miga2; mitoguardin 2 isoform 2 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 100361457 Actg1l1; actin, gamma 1 propeptide-like K05692 ACTB_G1; actin beta/gamma 1
D 81822 Actb; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 287876 Actg1; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 120098222 POTE ankyrin domain family member F K05692 ACTB_G1; actin beta/gamma 1
D 362228 Naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 360811 Naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 25344 Phb1; prohibitin 1 K17080 PHB1; prohibitin 1
D 302688 Phb1l1; prohibitin 1-like K17080 PHB1; prohibitin 1
D 688815 Phb1l2; prohibitin 1-like K17080 PHB1; prohibitin 1
D 114766 Phb2; prohibitin-2 K17081 PHB2; prohibitin 2
D 361029 Ktn1; kinectin isoform X3 K17975 KTN1; kinectin
C Retention of mitochondria
D 114114 Dnm1l; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 25017 Myo5a; unconventional myosin-Va K10357 MYO5; myosin V
D 25132 Myo5b; unconventional myosin-Vb K10357 MYO5; myosin V
D 315820 Myo5c; unconventional myosin-Vc K10357 MYO5; myosin V
D 63879 Xiap; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 288753 Diablo; diablo IAP-binding mitochondrial protein K10522 DIABLO; diablo
D 100360940 Diablol1; diablo IAP-binding mitochondrial protein-like K10522 DIABLO; diablo
C Morphogenesis factors
D 306471 Snx25; sorting nexin-25 isoform X2 K17887 SNX25; sorting nexin-25
D 303351 Rhot1; mitochondrial Rho GTPase 1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 312444 Immt; MICOS complex subunit Mic60 K17785 IMMT; MICOS complex subunit MIC60
D 289745 Mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 295238 Dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 25489 Nedd4; E3 ubiquitin-protein ligase NEDD4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 117520 Oxr1; oxidation resistance protein 1 isoform 2 K25437 OXR1; oxidation resistance protein 1
D 295237 Msto1; protein misato homolog 1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 689688 Atg2a; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 171415 Atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 678769 Atg4a; cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 686505 Atg4d; cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 313391 Atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 365601 Atg5; autophagy protein 5 isoform 1 K08339 ATG5; autophagy-related protein 5
D 114558 Becn1; beclin-1 K08334 BECN; beclin
D 312647 Atg7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 58974 Gabarap; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 64670 Gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 689161 Gabarapl1; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 134484162 gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 120098596 Gabarapl4; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 363254 Atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 499973 Atg9b; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 688555 Atg10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 361321 Atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 305831 Atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 363278 Atg16l1; autophagy-related protein 16-1 K17890 ATG16L1; autophagy-related protein 16-1
D 308865 Atg16l2; protein Atg16l2 K20868 ATG16L2; autophagy-related protein 16-2
D 288498 Wipi2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
D 303630 Wipi1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 56816 Prkn; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 362814 Rnf41; E3 ubiquitin-protein ligase NRDP1 isoform 1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 287044 Clec16a; protein CLEC16A K19513 CLEC16A; protein CLEC16A
D 287979 Parl; presenilin-associated rhomboid-like protein, mitochondrial precursor K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 113894 Sqstm1; sequestosome-1 isoform 1 K14381 SQSTM1; sequestosome 1
D 246244 Tax1bp1; tax1-binding protein 1 homolog K21347 TAX1BP1; Tax1-binding protein 1
D 303479 Calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 59319 Ambra1; activating molecule in BECN1-regulated autophagy protein 1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 362164 Atg13; autophagy-related protein 13 K08331 ATG13; autophagy-related protein 13
D 360827 Ulk1; serine/threonine-protein kinase ULK1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 303206 Ulk2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 312927 Rb1cc1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 299331 Hsp90aa1; heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG
D 301252 Hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 114562 Cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 303614 Smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 690516 Smurf1; E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 140923 Bnip3l; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 363442 Fundc1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 65248 Prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 78975 Prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 362245 Map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 64862 Map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 303554 Nbr1; next to BRCA1 gene 1 protein K17987 NBR1; next to BRCA1 gene 1 protein
D 304285 Tecpr1; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 299188 Zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 287711 Coasy; bifunctional coenzyme A synthase precursor K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 360426 Pla2g6; 85/88 kDa calcium-independent phospholipase A2 isoform 1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 690000 C1h19orf12; protein C19orf12 homolog K23168 MPAN; protein MPAN
D 365778 Fundc2b; uncharacterized protein LOC365778 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024