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  Mitochondrial Biogenesis - Gallus gallus (chicken)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 39116926 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 39116929 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 39116938 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 39116916 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 39116939 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 39116942 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 39116944 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 39116918 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 39116934 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 39116936 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 39116913 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 39116937 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 39116912 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 420084 POLRMT; DNA-directed RNA polymerase, mitochondrial isoform X2 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 373888 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 428608 TFB1M; dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 421488 TFB2M; dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 421213 MTIF2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 418930 MTIF3; translation initiation factor IF-3, mitochondrial isoform 1 K02520 infC; translation initiation factor IF-3 D 107050777 TSFM; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 427205 GFM2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 425018 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 418067 MTERF2; transcription termination factor 2, mitochondrial isoform X3 K15031 MTERF; mitochondrial transcription termination factor family protein D 107051861 MTERF4; transcription termination factor 4, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 420237 MTERF3; transcription termination factor 3, mitochondrial precursor K15031 MTERF; mitochondrial transcription termination factor family protein D 422773 GUF1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 425567 POP1; LOW QUALITY PROTEIN: ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 768362 POP4; processing of precursor 4 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 416973 POP5; ribonuclease P/MRP protein subunit POP5 isoform X3 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 423795 RPP30; ribonuclease P protein subunit p30 isoform X2 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 427403 RPP25L; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 430848 RPP25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 420530 RPP38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 420876 RPP40; ribonuclease P protein subunit p40 isoform X2 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 418397 TRMT10C; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 425758 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 isoform X1 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 423325 MRPP3; mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 769454 MSS51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 427217 PTCD2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X2 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 422911 PTCD3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 420376 DHX30; ATP-dependent RNA helicase DHX30 precursor K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 419139 UQCC1; ubiquinol-cytochrome c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 421770 AFG1L; AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 417812 ATP23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 423697 SUPV3L1; ATP-dependent RNA helicase SUPV3L1, mitochondrial precursor K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 420178 LACTB2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 422546 SLC25A4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 374072 SLC25A6; ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 772225 SLC25A5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 419530 SLC25A37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 423832 SLC25A28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 420616 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 374084 ERAL1; GTPase Era, mitochondrial K03595 era; GTPase D 418131 YARS2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 419666 YARS; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 420702 LARS2; probable leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 416347 LARS; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 424408 DARS2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 428403 GARS; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 416168 RARS; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 421823 RARS2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 421781 QRSL1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial isoform X2 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 422480 GATB; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X2 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 416976 GATC; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial isoform X1 K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 420478 MTPAP; LOW QUALITY PROTEIN: poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 107054443 PDE12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 791224 MTG1; mitochondrial ribosome-associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 422622 NOA1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 418432 NSUN3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X2 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 424613 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 101748025 RPUSD3; mitochondrial mRNA pseudouridine synthase RPUSD3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 768808 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 417484 RCC1L; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 417218 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 isoform X2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 424096 FASTKD2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 416827 C15H12ORF65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor D 421636 RMND1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1 D 422646 GRSF1; G-rich sequence factor 1 isoform X1 K24984 GRSF1; G-rich sequence factor 1 D 421606 METTL15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 426187 C33H12orf10; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 421779 C3H6ORF203; uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 404292 POLG; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 417418 POLG2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 D 422549 PRIMPOL; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 417204 ENDOG; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 416719 MGME1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 420430 EXOG; nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial D 425626 TWNK; twinkle protein, mitochondrial precursor K17680 PEO1; twinkle protein [EC:5.6.2.3] D 429092 PIF1; ATP-dependent DNA helicase PIF1 isoform X1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 418122 SSBP1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 419412 ATAD3A; ATPase family AAA domain-containing protein 3A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 419909 C26H6ORF125; ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 415744 DNAJA2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 419188 TOMM34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 417410 RHOT1; mitochondrial Rho GTPase 1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 395853 HSPA8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 395123 AIP; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein D 769785 AIPL1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 426278 TOMM40L; mitochondrial import receptor subunit TOM40B isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 418387 TOMM70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 426309 TOMM20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 420610 TOMM7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 419924 TOMM6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 426803 TOMM5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 418234 SAMM50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family C Porin D 416320 VDAC1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 395498 VDAC2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 426793 VDAC3; voltage-dependent anion-selective channel protein 3 isoform X2 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 427176 MTX3; metaxin-3 K17776 MTX; metaxin D 424138 MTX2; metaxin-2 isoform X2 K17776 MTX; metaxin D 417649 MYO19; unconventional myosin-XIX isoform X1 K25838 MYO19; myosin XIX D 428563 MARC1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 100859762 TIMM9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 425202 TIMM10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 107052461 TIMM10B; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 422190 TIMM8A; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 100859352 TIMM13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 416037 CHCHD4; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 416547 GFER; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 419474 MINOS1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 422912 IMMT; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 D 100858091 C19orf70; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13 D 418435 CHCHD3; MICOS complex subunit MIC19 isoform X4 K17563 CHCHD3; MICOS complex subunit MIC19 D 416029 CHCHD6; MICOS complex subunit MIC25 isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 418599 APOO; MICOS complex subunit MIC26 isoform X1 K24625 APOO; MICOS complex subunit MIC26 D 422271 APOOL; MICOS complex subunit MIC27 precursor K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 419474 MINOS1; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 422912 IMMT; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 417594 TIMM22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 423616 TIMM23B; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 421147 TIMM17A; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 421016 TIMM21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 770413 TIMM50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 428942 MCU; calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial D 769141 MICU1; calcium uptake protein 1, mitochondrial isoform X2 K22827 MICU1; calcium uptake protein 1, mitochondrial D 418946 MICU2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 422698 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial isoform X2 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 770755 SMDT1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 420837 MCUR1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 422898 LETM1; mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 771365 IMMP1L; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 417780 IMMP2L; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 426392 TMEM126A; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 428592 MPC1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 768451 MPC2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 416933 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 420053 TIMM44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 416183 HSPA9; stress-70 protein, mitochondrial precursor K04043 dnaK; molecular chaperone DnaK D 422865 GRPEL1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 768554 GRPEL2; LOW QUALITY PROTEIN: grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 424966 DNAJC19; mitochondrial import inner membrane translocase subunit TIM14 isoform X2 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 416669 PAM16; mitochondrial import inner membrane translocase subunit TIM16 isoform X1 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 417134 PMPCA; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 417718 PMPCB; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 418942 MIPEP; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 424059 HSPD1; 60 kDa heat shock protein, mitochondrial precursor K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 395948 HSPE1; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 416671 DNAJA3; dnaJ homolog subfamily A member 3, mitochondrial isoform X2 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 427581 TAMM41; phosphatidate cytidylyltransferase, mitochondrial isoform X2 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 772152 DNLZ; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 417565 POLDIP2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 395099 CREB1; cyclic AMP-responsive element-binding protein 1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 427205 GFM2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 425018 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 395303 SP1; transcription factor Sp1 K04684 SP1; transcription factor Sp1 D 423455 YY1; transcriptional repressor protein YY1 K09201 YY; transcription factor YY D 415453 GABPB1; GA-binding protein subunit beta-1 isoform 2 K09454 GABPB; GA-binding protein transcription factor, beta D 100857414 GABPB2; GA-binding protein subunit beta-2 isoform X3 K09454 GABPB; GA-binding protein transcription factor, beta D 373888 TFAM; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 416677 NRF1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1 D 396014 NFE2L2; nuclear factor erythroid 2-related factor 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 396212 MT4L; metallothionein K14739 MT1_2; metallothionein 1/2 D 770592 MT3; metallothionein-3 K14739 MT1_2; metallothionein 1/2 C Coactivators D 422815 PPARGC1A; peroxisome proliferator-activated receptor gamma coactivator 1-alpha K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 416148 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 423848 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 771015 CRTC1; CREB-regulated transcription coactivator 1 isoform X2 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 416667 CREBBP; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 418000 EP300; histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 419133 NFS1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 416891 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 420874 LYRM4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4 D 427244 FXN; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1] D 373947 FDX1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 422172 FDX1L; adrenodoxin K22071 FDX2; ferredoxin-2, mitochondrial D 107050964 ferredoxin-2, mitochondrial isoform X2 K22071 FDX2; ferredoxin-2, mitochondrial D 769635 FDXR; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X8 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 416183 HSPA9; stress-70 protein, mitochondrial precursor K04043 dnaK; molecular chaperone DnaK D 768938 HSCB; iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB D 416185 SIL1; nucleotide exchange factor SIL1 isoform X2 K14001 SIL1; nucleotide exchange factor SIL1 D 423440 GLRX5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 427463 ISCA1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 423352 ISCA2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 420396 IBA57; putative transferase CAF17, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 419513 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 107049580 bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 107054980 BOLA3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 416221 SFXN1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 428972 SFXN3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 423866 SFXN2; sideroflexin-2 isoform X1 K23501 SFXN2; sideroflexin-2 D 771604 SFXN4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4 D 422954 SFXN5; sideroflexin-5 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 423118 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 426076 DHTKD1; LOW QUALITY PROTEIN: probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 421798 FBXL4; F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 418083 HCFC2; host cell factor 2 isoform X4 K27390 HCFC2; host cell factor 2 D 422878 HTT; huntingtin isoform X2 K04533 HD; huntingtin D 771938 ESRRB; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 421357 ESRRG; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma D 101749375 NRIP1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 427185 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 429110 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 768942 LONP1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 423646 SIRT1; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 421657 SERAC1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 112530998 UXT; protein UXT K26537 UXT; protein UXT D 428186 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 isoform X2 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 423214 NDUFAF1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 769549 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 precursor K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 107054424 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 isoform X3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 421802 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 isoform X1 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 416742 NDUFAF5; arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 420233 NDUFAF6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 421477 NDUFAF7; protein arginine methyltransferase NDUFAF7, mitochondrial isoform X2 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 422071 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 precursor K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 100857880 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 415974 ACAD9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 423312 NUBPL; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 419712 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 421782 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial isoform X2 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 418453 TIMMDC1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 107049539 SDHAF1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 426015 SDHAF2; succinate dehydrogenase assembly factor 2, mitochondrial isoform 1 K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 424212 BCS1L; mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 417597 TTC19; tetratricopeptide repeat protein 19, mitochondrial isoform X2 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 768932 LYRM7; complex III assembly factor LYRM7 isoform X3 K18170 LYRM7; complex III assembly factor LYRM7 D 419139 UQCC1; ubiquinol-cytochrome c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 419909 C26H6ORF125; ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 112533442 C14H16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 415896 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 772057 C1H12ORF73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 418128 STMP1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 420659 CMC1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 770023 CMC2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 772251 COA3; cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 101747545 COA4; cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 769722 COA5; cytochrome C oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 771652 COA6; cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 429105 COA7; sel1 repeat-containing protein 1 isoform 1 K18180 COA7; cytochrome c oxidase assembly factor 7 D 417329 COX10; protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 770638 COX11; cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 426880 COX14; cytochrome c oxidase assembly homolog 14 K18181 COX14; cytochrome c oxidase assembly factor 14 D 423830 COX15; cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 423257 COX16; COX16 cytochrome c oxidase assembly homolog K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 770190 COX17; COX17 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 422650 COX18; cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18 D 416452 COX19; cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 421493 COX20; protein FAM36A K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 769454 MSS51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 112531359 mitochondrial inner membrane protein OXA1L-like isoform X1 K03217 yidC; YidC/Oxa1 family membrane protein insertase D 417157 SURF1; surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 426060 SCO1; protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 429671 SCO2; protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 421403 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 423483 APOPT1; apoptogenic protein 1, mitochondrial isoform X1 K23506 APOPT1; apoptogenic protein 1 D 418128 STMP1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 415896 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 107049451 TMEM223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 424616 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 416511 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 420188 TMEM70; transmembrane protein 70, mitochondrial precursor K17966 TMEM70; transmembrane protein 70, mitochondrial D 772187 ATP5MPL; 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid D 423873 USMG5; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 424973 MFN1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 419484 MFN2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 424900 OPA1; dynamin-like 120 kDa protein, mitochondrial precursor K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 107057641 OPA3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein D 416977 TRIAP1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 424767 PARL; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 419912 BAK1; bcl-2 homologous antagonist/killer K14021 BAK; Bcl-2 homologous antagonist/killer D 418132 DNM1L; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 107051391 mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 770125 SUMO2; small ubiquitin-related modifier 2 precursor K12160 SUMO; small ubiquitin-related modifier D 770553 SUMO3; small ubiquitin-related modifier 3 precursor K12160 SUMO; small ubiquitin-related modifier D 373930 SUMO1; small ubiquitin-related modifier 1 precursor K12160 SUMO; small ubiquitin-related modifier D 424522 SH3GLB1; endophilin-B1 K11248 SH3GLB1; endophilin-B1 D 395597 MTCH2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 425491 MTCH1; mitochondrial carrier homolog 1 isoform X2 K17885 MTCH; mitochondrial carrier D 424796 MFF; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor D 771612 mitochondrial fission factor homolog B K22076 MFF; mitochondrial fission factor D 420191 GDAP1; ganglioside-induced differentiation-associated protein 1 isoform X2 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 420009 VAT1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 416516 MIEF2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 418012 MIEF1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 107054610 PLD6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 427765 MIGA2; mitoguardin 2 isoform X2 K27289 MIGA; mitoguardin D 771457 MIGA1; mitoguardin 1 isoform X1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 776816 actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 415296 ACTG1; actin, cytoplasmic type 5 K05692 ACTB_G1; actin beta/gamma 1 D 396526 ACTB; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 424333 NAA20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 416883 NAA25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 419980 PHB; prohibitin K17080 PHB1; prohibitin 1 D 771124 PHB2; prohibitin-2 K17081 PHB2; prohibitin 2 D 396335 KTN1; kinectin K17975 KTN1; kinectin C Retention of mitochondria D 418132 DNM1L; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 396237 MYO5A; unconventional myosin-Va K10357 MYO5; myosin V D 430027 MYO5C; unconventional myosin-Vc isoform X1 K10357 MYO5; myosin V D 430317 MYO5B; unconventional myosin-Va K10357 MYO5; myosin V D 395280 XIAP; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 416860 DIABLO; diablo homolog, mitochondrial isoform X2 K10522 DIABLO; diablo C Morphogenesis factors D 422544 SNX25; sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25 D 417410 RHOT1; mitochondrial Rho GTPase 1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 422912 IMMT; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60 D 417007 MTFP1; mitochondrial fission process protein 1 isoform X1 K17981 MTFP1; mitochondrial fission process protein 1 D 425065 DAP3; 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29 D 415406 NEDD4; E3 ubiquitin-protein ligase NEDD4 isoform X1 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 420270 OXR1; oxidation resistance protein 1 isoform X1 K25437 OXR1; oxidation resistance protein 1 D 425066 MSTO1; protein misato homolog 1 K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 423441 ATG2B; autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2 D 418369 ATG3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 404750 ATG4B; cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 424688 ATG4C; cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 772074 ATG4A; cysteine protease ATG4A isoform 2 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 421784 ATG5; autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 420018 BECN1; beclin-1 K08334 BECN; beclin D 415961 ATG7; ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 769118 GABARAPL1; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 770240 GABARAPL2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 425722 ATG9A; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 107055991 ATG9B; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9 D 427322 ATG10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 427390 ATG12; ubiquitin-like protein ATG12 isoform X2 K08336 ATG12; ubiquitin-like protein ATG12 D 428922 ATG14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 424746 ATG16L1; autophagy-related protein 16-1 isoform X7 K17890 ATG16L1; autophagy-related protein 16-1 D 416481 WIPI2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18 D 417437 WIPI1; WD repeat domain phosphoinositide-interacting protein 1 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 421690 vacuolar protein 8-like isoform X1 K08332 VAC8; vacuolar protein 8 C Parkin-dependent mechanism factors D 421577 PARK2; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31] D 426468 RNF41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 416632 CLEC16A; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 424767 PARL; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 770805 SQSTM1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1 D 395490 TAX1BP1; tax1-binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1 D 419993 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 423194 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 isoform X2 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 423192 ATG13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13 D 416800 ULK1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 417614 ULK2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 421116 RB1CC1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 396188 HSP90AB1; heat shock cognate protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 423463 HSP90AA1; heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG D 395430 CDC37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 427809 SMURF2; E3 ubiquitin-protein ligase SMURF2 isoform X2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 416487 SMURF1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 419522 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 418558 FUNDC1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 427185 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 429110 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 419142 MAP1LC3A; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 421504 MAP1LC3C; microtubule-associated proteins 1A/1B light chain 3C isoform X1 K10435 MAP1LC; microtubule-associated protein 1 light chain D 427559 MAP1LC3B2; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 420007 NBR1; next to BRCA1 gene 1 protein isoform X2 K17987 NBR1; next to BRCA1 gene 1 protein D 416436 TECPR1; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 423252 ZFYVE1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 418028 PLA2G6; 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 100858381 uncharacterized protein LOC100858381 K23168 MPAN; protein MPAN D 415756 uncharacterized protein LOC415756 K23168 MPAN; protein MPAN D 415757 C11H19orf12; uncharacterized protein LOC415757 isoform 1 K23168 MPAN; protein MPAN D 422200 FUNDC2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024