+D
#
Mitochondrial Biogenesis - Xenopus laevis (African clawed frog)
%
!
AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 2642086 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 2642087 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 2642085 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 2642077 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 2642076 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 2642078 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 2642079 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 2642080 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 2642088 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 2642081 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 2642084 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 2642082 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 2642083 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 394312 polrmt.L; polymerase (RNA) mitochondrial (DNA directed) L homeolog K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 394385 tfam.L; transcription factor A, mitochondrial L homeolog K11830 TFAM; transcription factor A, mitochondrial
D 108697175 tfam.S; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 379540 tfb1m.L; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 108717408 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
D 108716122 tfb2m.L; dimethyladenosine transferase 2, mitochondrial isoform X1 K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 108716409 mtif2.L; translation initiation factor IF-2, mitochondrial isoform X2 K02519 infB; translation initiation factor IF-2
D 100127256 mtif3.L; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 100036913 tsfm.L; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 108708995 tsfm.S; elongation factor Ts, mitochondrial-like K02357 tsf; elongation factor Ts
D 108704215 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 100101315 gfm1.L; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 108718111 elongation factor G isoform X1 K02355 fusA; elongation factor G
D 108717847 gfm2.L; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 108718831 mterf1.L; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 108710802 mterf2.L; transcription termination factor 2, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein
D 100158338 mterf3.S; uncharacterized protein LOC100158338 K15031 MTERF; mitochondrial transcription termination factor family protein
D 108717097 mterf4.L; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 100381110 guf1.L; translation factor Guf1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 108719350 pop1.L; ribonucleases P/MRP protein subunit POP1 isoform X1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 444526 pop4.L; POP4 homolog, ribonuclease P/MRP subunit L homeolog K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 100101322 pop5.L; POP5 homolog, ribonuclease P/MRP subunit L homeolog K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 494740 rpp30.L; ribonuclease P/MRP 30kDa subunit L homeolog K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 733359 pop7.L; uncharacterized protein LOC733359 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 447360 rpp25l.S; ribonuclease P/MRP 25kDa subunit-like S homeolog K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 108712477 rpp25.S; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 108711315 rpp25.L; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 447717 rpp38.S; ribonuclease P/MRP 38kDa subunit S homeolog K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 447458 rpp40.L; ribonuclease P/MRP 40kDa subunit L homeolog K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 100381127 trmt10c.L; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 108709677 trmt10c.S; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 446903 hsd17b10.L; hydroxysteroid (17-beta) dehydrogenase 10 L homeolog K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 108699982 hsd17b10.S; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 108699217 prorp.L; mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 108702067 mss51.L; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 108703255 mss51.S; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 108701223 tefm.L; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 495833 ptcd1.L; pentatricopeptide repeat domain 1 L homeolog K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 100036884 ptcd2.L; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 734981 ptcd3.L; pentatricopeptide repeat domain-containing protein 3, mitochondrial precursor K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 108718677 ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 100036956 dhx30.S; ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 398100 uqcc1.S; ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 108700815 uqcc1.L; ubiquinol-cytochrome-c reductase complex assembly factor 1-like K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 108716840 afg1l.L; AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 379946 atp23.L; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 108696207 ATP-dependent RNA helicase SUPV3L1, mitochondrial-like K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 108697443 supv3l1.S; ATP-dependent RNA helicase SUPV3L1, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 495268 lactb2.L; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 380187 slc25a5.L; adenine nucleotide translocator 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 432212 slc25a4.L; solute carrier family 25 (mitochondrial carrier, adenine nucleotide translocator), member 4 L homeolog K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 108700136 slc25a5.S; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 108705979 slc25a4.S; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 121394752 ADP/ATP translocase 2-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 108711591 slc25a37.L; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 108697466 mitoferrin-2-like K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 444758 slc25a28.S; mitoferrin-2A K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 447330 slc25a28.L; mitoferrin-2B K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 108712718 slc25a37.S; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 108718858 malsu1.L; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 100127247 eral1.L; GTPase Era, mitochondrial K03595 era; GTPase
D 380438 yars1.S; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 108708270 yars1.L; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 447217 lars1.L; leucyl-tRNA synthetase 1 L homeolog K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 443989 lars2.L; leucyl-tRNA synthetase 2 L homeolog K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 108714340 dars2.L; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 446482 gars1.L; glycyl-tRNA synthetase 1 L homeolog K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 734988 gars1.S; uncharacterized protein LOC734988 K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 443863 rars2.S; probable arginine--tRNA ligase, mitochondrial precursor K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 733251 rars1.S; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 380585 qrsl1.L; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 108699371 gatb.L; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 108716016 gatc.L; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial isoform X2 K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 108718472 mtpap.L; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 443670 pde12.S; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 108696349 mtg1.L; mitochondrial ribosome-associated GTPase 1 isoform X1 K19828 MTG1; mitochondrial GTPase 1
D 108712021 noa1.L; nitric oxide-associated protein 1 isoform X1 K19832 NOA1; nitric oxide-associated protein 1
D 108707430 nsun3.L; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 496225 nsun4.S; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 108714289 nsun4.L; 5-methylcytosine rRNA methyltransferase NSUN4-like isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 108715898 rpusd3.S; mitochondrial mRNA pseudouridine synthase RPUSD3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
D 108701711 rpusd4.L; mitochondrial RNA pseudouridine synthase rpusd4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 735132 rcc1l.L; uncharacterized protein LOC735132 K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 108705709 neugrin K23496 NGRN; neugrin
D 100036957 trub2.L; TruB pseudouridine (psi) synthase family member 2 L homeolog K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 108701469 fastkd2.L; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 108716624 mtrfr.L; probable peptide chain release factor C12orf65, mitochondrial K23498 COXPD7; peptide chain release factor
D 108710775 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 100158276 grsf1.S; G-rich RNA sequence binding factor 1 S homeolog K24984 GRSF1; G-rich sequence factor 1
D 108701302 grsf1.L; G-rich sequence factor 1 isoform X2 K24984 GRSF1; G-rich sequence factor 1
D 496075 myg1.S; uncharacterized protein LOC496075 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 108716848 mtres1.L; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 397851 polg.L; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 398112 polg2.L; DNA polymerase subunit gamma-2, mitochondrial precursor K02333 POLG2; DNA polymerase gamma 2
D 108702233 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 108698767 primpol.L; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 495982 endog.L; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 108716630 mgme1.L; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 108717772 mgme1.S; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 779295 exog.L; nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial
D 414487 twnk.L; uncharacterized protein LOC414487 K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 734585 pif1.L; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 100037159 ssbp1.S; single-stranded DNA-binding protein 1-B, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 397915 ssbp1.L; single-stranded DNA-binding protein 1-A, mitochondrial precursor K03111 ssb; single-strand DNA-binding protein
D 398759 atad3a.L; ATPase family AAA domain-containing protein 3-B K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 734380 atad3a.S; ATPase family AAA domain-containing protein 3-A K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 443971 uqcc2.S; ubiquinol-cytochrome c reductase complex assembly factor 2 S homeolog K17682 MNF1; mitochondrial nucleoid factor 1
D 379072 uqcc2.L; ubiquinol-cytochrome c reductase complex assembly factor 2 L homeolog K17682 MNF1; mitochondrial nucleoid factor 1
#
AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 380317 dnaja2.S; DnaJ subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 379373 dnaja2.L; DnaJ heat shock protein family (Hsp40) member A2 L homeolog K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 100158403 rhot1.L; ras homolog family member T1 L homeolog K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 108702234 rhot1.S; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 379319 hspa8.L; heat shock protein family A (Hsp70) member 8 L homeolog K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 379760 hspa1l.S; heat shock protein family A (Hsp70) member 1 like S homeolog K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 398343 hsp70.L; heat shock 70 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 108696811 hspa1a.L; heat shock cognate 71 kDa protein-like isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 100381020 hspa1a.S; heat shock protein family A (Hsp70) member 1A S homeolog K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 108696308 aip.L; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
D 108707685 aipl1.L; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 108709095 aipl1.S; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 380301 tomm40.L; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 108700389 tomm40l.S; mitochondrial import receptor subunit TOM40B isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 108699457 mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 379405 tomm40.S; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 398758 tomm70.S; to translocase of outer mitochondrial membrane 70 S homeolog K17768 TOM70; mitochondrial import receptor subunit TOM70
D 496012 tomm22.L; translocase of outer mitochondrial membrane 22 homolog L homeolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 108715774 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 108716729 tomm20.L; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 108704886 tomm20.S; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20
D 108718860 tomm7.L; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 108709455 tomm6.S; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 108713390 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 379807 samm50.L; sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family
D 398869 samm50.S; sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 380376 vdac1.S; voltage-dependent anion channel 1 S homeolog K05862 VDAC1; voltage-dependent anion channel protein 1
D 108710805 vdac1.L; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 734449 vdac2.S; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 443782 vdac3.L; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 407749 mtx1.S; metaxin 1 S homeolog K17776 MTX; metaxin
D 407751 mtx3.L; metaxin-3 K17776 MTX; metaxin
D 407750 mtx2.L; metaxin 2 L homeolog K17776 MTX; metaxin
D 108703005 metaxin-2 K17776 MTX; metaxin
D 734396 myo19.S; unconventional myosin-XIX K25838 MYO19; myosin XIX
D 108718925 mtarc1.L; mitochondrial amidoxime-reducing component 1-like K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 495382 mtarc1.S; mitochondrial amidoxime-reducing component 1 precursor K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
D 108716467 mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 734565 timm9.L; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 108700471 timm9.S; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 443956 timm10.L; mitochondrial import inner membrane translocase subunit Tim10-B K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 734492 timm10.S; mitochondrial import inner membrane translocase subunit Tim10-A K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 443743 timm10b.S; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 447075 timm8b.L; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 100036822 timm8b.S; translocase of inner mitochondrial membrane 8 homolog B S homeolog K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 108698275 timm8a.L; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 443601 timm13.L; mitochondrial import inner membrane translocase subunit Tim13-A K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
D 379114 timm13.S; mitochondrial import inner membrane translocase subunit Tim13-B K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 414630 chchd4.L; mitochondrial intermembrane space import and assembly protein 40-A K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 494790 chchd4.S; mitochondrial intermembrane space import and assembly protein 40-B K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 733269 gfer.L; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 100049137 micos10.L; uncharacterized protein LOC100049137 K17784 MICOS10; MICOS complex subunit MIC10
D 734595 micos10.S; mitochondrial contact site and cristae organizing system subunit 10 S homeolog K17784 MICOS10; MICOS complex subunit MIC10
D 100036792 immt.L; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 733343 immt.S; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 108700956 MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 108713429 MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 443931 chchd3.L; coiled-coil-helix-coiled-coil-helix domain containing 3 L homeolog K17563 CHCHD3; MICOS complex subunit MIC19
D 379142 chchd3.S; uncharacterized protein LOC379142 K17563 CHCHD3; MICOS complex subunit MIC19
D 495402 chchd6.L; MICOS complex subunit mic25-b K17564 CHCHD6; MICOS complex subunit MIC25
D 446271 chchd6.S; MICOS complex subunit mic25-a K17564 CHCHD6; MICOS complex subunit MIC25
D 414670 apoo.L; apolipoprotein O L homeolog K24625 APOO; MICOS complex subunit MIC26
D 494692 apool.L; apolipoprotein O-like L homeolog K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 100049137 micos10.L; uncharacterized protein LOC100049137 K17784 MICOS10; MICOS complex subunit MIC10
D 734595 micos10.S; mitochondrial contact site and cristae organizing system subunit 10 S homeolog K17784 MICOS10; MICOS complex subunit MIC10
D 100036792 immt.L; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 733343 immt.S; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 108709182 mitochondrial import inner membrane translocase subunit Tim22-like K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 432132 timm23.L; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 108703381 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 100037113 timm17a.L; uncharacterized protein LOC100037113 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 495285 timm17a.S; translocase of inner mitochondrial membrane 17A S homeolog K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 735201 timm17b.S; uncharacterized protein LOC735201 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 494838 timm21.L; mitochondrial import inner membrane translocase subunit Tim21 precursor K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 108695226 timm21.S; mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 431826 timm50.L; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
D 108700295 timm50.S; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 108697483 mcu.S; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 100037005 mcu.L; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 108697484 micu1.S; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 431854 micu1.L; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial
D 735133 micu2.S; mitochondrial calcium uptake 2 S homeolog K22828 MICU2; calcium uptake protein 2, mitochondrial
D 100036780 micu2.L; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 447698 mcub.L; mitochondrial calcium uniporter dominant negative beta subunit L homeolog K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 108706701 mcub.S; calcium uniporter regulatory subunit MCUb, mitochondrial isoform X2 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
D 108714476 smdt1.L; essential MCU regulator, mitochondrial-like K22830 SMDT1; essential MCU regulator, mitochondrial
D 495205 smdt1.S; essential MCU regulator, mitochondrial precursor K22830 SMDT1; essential MCU regulator, mitochondrial
D 100158282 mcur1.L; mitochondrial calcium uniporter regulator 1 L homeolog K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 108706514 letm1.S; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 108697680 letm1.L; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 108715214 immp1l.S; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 108713810 immp1l.L; mitochondrial inner membrane protease subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 495969 immp2l.L; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 379516 tmem126a.L; transmembrane protein 126A L homeolog K18157 TMEM126A; transmembrane protein 126A
D 780760 mpc1.L; mitochondrial pyruvate carrier 1 L homeolog K22138 MPC1; mitochondrial pyruvate carrier 1
D 496160 mpc1.S; mitochondrial pyruvate carrier 1 S homeolog K22138 MPC1; mitochondrial pyruvate carrier 1
D 379218 mpc2.S; mitochondrial pyruvate carrier 2 S homeolog K22139 MPC2; mitochondrial pyruvate carrier 2
D 100037110 chchd10.L; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 447516 timm44.S; translocase of inner mitochondrial membrane 44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 379314 hspa9.S; heat shock protein family A (Hsp70) member 9 S homeolog K04043 dnaK; molecular chaperone DnaK
D 379858 hspa9.L; heat shock protein family A (Hsp70) member 9 L homeolog K04043 dnaK; molecular chaperone DnaK
D 495350 grpel2.L; GrpE like 2, mitochondrial L homeolog K03687 GRPE; molecular chaperone GrpE
D 734538 grpel1.L; GrpE-like 1, mitochondrial L homeolog K03687 GRPE; molecular chaperone GrpE
D 108713253 grpel2.S; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 100049122 dnajc19.L; DnaJ heat shock protein family (Hsp40) member C19 L homeolog K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 414698 pam16.L; mitochondrial import inner membrane translocase subunit tim16-A K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
D 779194 pam16.S; mitochondrial import inner membrane translocase subunit tim16-B K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 734517 pmpca.S; peptidase (mitochondrial processing) alpha S homeolog K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 108698188 pmpca.L; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 432215 pmpcb.L; peptidase (mitochondrial processing) beta L homeolog K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 496289 pmpcb.S; uncharacterized protein LOC496289 K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 108709016 mipep.S; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 108708717 mipep.L; mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 379341 hspd1.L; heat shock protein family D (Hsp60) member 1 L homeolog K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 399217 hspd1.S; heat shock protein family D (Hsp60) member 1 S homeolog K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 414669 hspe1.L; heat shock protein family E (Hsp10) member 1 L homeolog K04078 groES; chaperonin GroES
D 108703085 hspe1.S; 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES
D 100037206 dnaja3.L; DnaJ heat shock protein family (Hsp40) member A3 L homeolog K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 108703192 dnaja3.S; dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 108704415 phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 779303 dnlz.S; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 379091 ethe1.L; ethylmalonic encephalopathy 1 L homeolog K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 108704965 ethe1.S; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 100037208 poldip2.S; uncharacterized protein LOC100037208 K17809 POLDIP2; polymerase delta-interacting protein 2
D 432266 poldip2.L; polymerase (DNA-directed), delta interacting protein 2 L homeolog K17809 POLDIP2; polymerase delta-interacting protein 2
#
AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 379764 creb1.S; cAMP responsive element binding protein 1 S homeolog K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 108701473 creb1.L; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 100101315 gfm1.L; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 108718111 elongation factor G isoform X1 K02355 fusA; elongation factor G
D 108717847 gfm2.L; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 431939 sp1.L; transcription factor Sp1 isoform X2 K04684 SP1; transcription factor Sp1
D 108709905 sp1.S; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 447228 yy1.S; YY1 transcription factor S homeolog K09201 YY; transcription factor YY
D 394372 yy1.L; YY1 transcription factor L homeolog K09201 YY; transcription factor YY
D 446342 gabpb2.S; GA binding protein transcription factor subunit beta 2 S homeolog K09454 GABPB; GA-binding protein transcription factor, beta
D 397965 gabpb1.S; GA binding protein transcription factor subunit beta 1 S homeolog K09454 GABPB; GA-binding protein transcription factor, beta
D 108711410 GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta
D 108705605 GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta
D 394385 tfam.L; transcription factor A, mitochondrial L homeolog K11830 TFAM; transcription factor A, mitochondrial
D 108697175 tfam.S; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 446711 nrf1.S; nuclear respiratory factor 1 S homeolog K11831 NRF1; nuclear respiratory factor 1
D 108711242 nrf1.L; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1
D 444736 nfe2l2.S; nuclear factor, erythroid 2 like 2 S homeolog K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 379209 nfe2l2.L; nuclear factor, erythroid 2 like 2 L homeolog K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 394349 mt4.L; metallothionein K14739 MT1_2; metallothionein 1/2
D 108714021 metallothionein-like K14739 MT1_2; metallothionein 1/2
D 108696601 metallothionein-like K14741 MT4; metallothionein 4
C Coactivators
D 100462892 ppargc1a.S; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 108698053 ppargc1a.L; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 108713242 ppargc1b.S; peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 108710955 ppargc1b.L; peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 108697434 peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 108696159 pprc1.L; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 734879 MGC132236; uncharacterized protein LOC734879 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 108713350 crtc1.L; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 108706909 crtc1.S; CREB-regulated transcription coactivator 1 isoform X2 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 495689 crebbp.L; CREB binding protein L homeolog K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 108714480 ep300.L; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 108715729 ep300.S; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 373795 crebbp.S; CREB-binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 108701071 nfs1.L; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 380393 iscu.L; iron-sulfur cluster assembly enzyme L homeolog K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 108695245 lyrm4.S; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 446871 lyrm4.L; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 108714196 fxn.L; frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1]
D 100037037 fdx1.L; ferredoxin 1 L homeolog K22070 FDX1; ferredoxin-1, mitochondrial
D 108709997 fdx1.S; adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial
D 108705502 fdx2.S; ferredoxin-2, mitochondrial-like isoform X1 K22071 FDX2; ferredoxin-2, mitochondrial
D 735053 fdx2.L; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial
D 496078 XB5934217.L; uncharacterized protein LOC496078 K22071 FDX2; ferredoxin-2, mitochondrial
D 495142 fdxr.L; ferredoxin reductase L homeolog precursor K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 108702801 fdxr.S; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 379314 hspa9.S; heat shock protein family A (Hsp70) member 9 S homeolog K04043 dnaK; molecular chaperone DnaK
D 379858 hspa9.L; heat shock protein family A (Hsp70) member 9 L homeolog K04043 dnaK; molecular chaperone DnaK
D 444532 hscb.L; HscB mitochondrial iron-sulfur cluster co-chaperone L homeolog K04082 hscB; molecular chaperone HscB
D 414657 sil1.L; nucleotide exchange factor SIL1 precursor K14001 SIL1; nucleotide exchange factor SIL1
D 734675 glrx5.L; glutaredoxin 5 L homeolog K07390 grxD; monothiol glutaredoxin
D 432034 glrx5.S; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 108714660 isca1.L; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1
D 108698671 isca2.L; iron-sulfur cluster assembly 2 homolog, mitochondrial isoform X1 K22072 ISCA2; iron-sulfur cluster assembly 2
D 108719803 iba57.S; putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 108711546 nfu1.L; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 779075 nfu1.S; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 108699364 bola1.L; bolA-like protein 1 isoform X1 K22066 BOLA1; BolA-like protein 1
D 108700349 bola1.S; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 108712778 bola3.S; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 379980 sfxn3.L; sideroflexin 3 L homeolog K23500 SFXN1_3; sideroflexin-1/3
D 779259 sfxn1.L; sideroflexin 1 L homeolog K23500 SFXN1_3; sideroflexin-1/3
D 379585 sfxn2.S; sideroflexin 2 S homeolog K23501 SFXN2; sideroflexin-2
D 443674 sfxn4.L; LOW QUALITY PROTEIN: sideroflexin-4 K23502 SFXN4; sideroflexin-4
D 100505449 sfxn5.L; sideroflexin 5 L homeolog K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 379393 cpt1al.L; carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 108713843 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 108715191 carnitine O-palmitoyltransferase 1, liver isoform isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 108697831 carnitine O-palmitoyltransferase 1, liver isoform-like isoform X1 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 495682 cpt1b.L; carnitine palmitoyltransferase 1B L homeolog K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
D 403360 dhtkd1.L; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 108697668 fbxl4.S; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 108696588 fbxl4.L; F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 494675 hcfc1.S; uncharacterized protein LOC494675 K14966 HCFC1; host cell factor 1
D 108704501 host cell factor 1-like isoform X2 K14966 HCFC1; host cell factor 1
D 108711028 host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2
D 108697843 htt.L; huntingtin isoform X8 K04533 HD; huntingtin
D 447206 esrra.L; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 108715152 esrra.S; steroid hormone receptor ERR1 isoform X1 K08552 NR3B1; estrogen-related receptor alpha
D 108698678 esrrb.L; steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta
D 108716458 esrrg.L; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 108698610 esrrgr.L; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 108717708 esrrg.S; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma
D 399072 nrip1.S; nuclear receptor interacting protein 1 S homeolog K17965 NRIP1; nuclear receptor-interacting protein 1
D 108707906 nrip1.L; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 495290 prkaa1.L; protein kinase, AMP-activated, alpha 1 catalytic subunit L homeolog K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 399172 prkaa2.S; protein kinase, AMP-activated, alpha 2 catalytic subunit S homeolog K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108715541 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108714249 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108712696 lonp1.L; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 100036963 sirt1.L; sirtuin 1 L homeolog K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 108697451 sirt1.S; NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 108716712 serac1.L; protein SERAC1 K23504 SERAC1; protein SERAC1
D 108699851 protein UXT-like K26537 UXT; protein UXT
D 108696527 uncharacterized protein LOC108696527 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 108699275 ndufaf1.L; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 495351 ndufaf2.L; NADH:ubiquinone oxidoreductase complex assembly factor 2 L homeolog K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 108714677 ndufaf3.L; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 734768 ndufaf4.L; NADH:ubiquinone oxidoreductase complex assembly factor 4 L homeolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 108716895 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 108705644 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 121393138 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 121393725 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like isoform X1 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 121393744 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 121393730 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 121393739 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 121393720 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 108716573 ndufaf5.L; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 108719748 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6-like K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 108719361 ndufaf6.L; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 443969 ndufaf7.S; protein arginine methyltransferase NDUFAF7, mitochondrial precursor K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 100037194 ecsit.S; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial precursor K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 446728 acad9.S; acyl-CoA dehydrogenase family member 9 S homeolog K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 108699236 nubpl.L; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 446896 foxred1.L; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 100036890 rtn4ip1.L; reticulon 4 interacting protein 1 L homeolog K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 494845 timmdc1.L; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 108707270 succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 108713460 sdhaf2.L; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
D 108715200 sdhaf2.S; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 380366 bcs1l.L; mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 108709194 ttc19.S; tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 494821 lyrm7.L; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 108707190 complex III assembly factor LYRM7-like isoform X1 K18170 LYRM7; complex III assembly factor LYRM7
D 398100 uqcc1.S; ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 108700815 uqcc1.L; ubiquinol-cytochrome-c reductase complex assembly factor 1-like K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 443971 uqcc2.S; ubiquinol-cytochrome c reductase complex assembly factor 2 S homeolog K17682 MNF1; mitochondrial nucleoid factor 1
D 379072 uqcc2.L; ubiquinol-cytochrome c reductase complex assembly factor 2 L homeolog K17682 MNF1; mitochondrial nucleoid factor 1
D 734185 uqcc3.L; ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 108701568 protein ccsmst1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 108704422 small integral membrane protein 4-like K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 108711022 c12orf73.L; protein brawnin K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 108706056 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 432002 cmc1.L; C-x(9)-C motif containing 1 L homeolog K18171 CMC1; COX assembly mitochondrial protein 1
D 100049117 cmc2.S; uncharacterized protein LOC100049117 K18172 CMC2; COX assembly mitochondrial protein 2
D 100101291 cmc2.L; uncharacterized protein LOC100101291 K18172 CMC2; COX assembly mitochondrial protein 2
D 108718983 coa1.L; cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1
D 444575 ccdc56.L; coiled-coil domain containing 56 L homeolog K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 108706187 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 100037054 coa5.L; cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 108709722 cytochrome c oxidase assembly factor 5-like K18178 COA5; cytochrome c oxidase assembly factor 5
D 100329134 coa6.L; uncharacterized protein LOC100329134 K18179 COA6; cytochrome c oxidase assembly factor 6
D 447115 coa7.L; cytochrome c oxidase assembly factor 7A K18180 COA7; cytochrome c oxidase assembly factor 7
D 734267 coa7.S; cytochrome c oxidase assembly factor 7B K18180 COA7; cytochrome c oxidase assembly factor 7
D 779326 cox10.L; cytochrome c oxidase assembly factor heme A:farnesyltransferase COX10 L homeolog K02257 COX10; heme o synthase [EC:2.5.1.141]
D 108702849 cox10.S; protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 108719441 cox11.L; cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 108709914 cox14.S; cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 108697465 cox15.S; cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 733273 cox16.L; cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 447142 cox17.S; COX17 homolog, cytochrome c oxidase assembly protein b K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 495379 cox17.L; COX17 cytochrome c oxidase assembly protein a K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 735188 cox18.L; cytochrome c oxidase assembly factor COX18r L homeolog K17797 COX18; mitochondrial inner membrane protein COX18
D 108703139 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 734404 cox20.L; uncharacterized protein LOC734404 K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 108702067 mss51.L; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 108703255 mss51.S; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 108711654 pet100.L; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 108716628 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117
D 108714882 oxa1l.L; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 108704939 mitochondrial inner membrane protein OXA1L-like isoform X1 K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 108698210 surf1.L; surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 108701199 sco1.L; protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 100137652 sco2.S; synthesis of cytochrome C oxidase 2 S homeolog K23755 SCO2; protein SCO2
D 108702561 taco1.S; translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 398720 lrpprc.L; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 108698794 coa8.L; cytochrome c oxidase assembly factor 8 isoform X1 K23506 APOPT1; apoptogenic protein 1
D 108706056 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 108704422 small integral membrane protein 4-like K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
C Complex-V assembly factors
D 108715584 atpaf1.S; ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 735134 atpaf2.S; ATP synthase mitochondrial F1 complex assembly factor 2 S homeolog K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 108701687 atpaf2.L; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 108695350 tmem70.S; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 108697413 atp5mk.S; ATP synthase membrane subunit K, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
D 108704950 atp5mk.L; ATP synthase membrane subunit K, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 443958 mfn1.L; mitofusin 1 L homeolog K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 495314 mfn1.S; mitofusin 1 S homeolog K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 431918 mfn2.L; mitofusin 2 L homeolog K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 108697551 mfn2.S; mitofusin-2 isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 108716991 opa1.L; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 108718082 opa1.S; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 108698513 opa3.L; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 494632 opa3.S; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 432296 triap1.S; TP53-regulated inhibitor of apoptosis 1-A K17968 TRIAP1; TRIAP1/MDM35 family protein
D 446769 triap1.L; TP53-regulated inhibitor of apoptosis 1-B K17968 TRIAP1; TRIAP1/MDM35 family protein
D 108708122 parl.L; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 734644 bak1.S; BCL2 antagonist/killer 1 S homeolog K14021 BAK; Bcl-2 homologous antagonist/killer
D 373637 bax.S; BCL2-associated X protein L homeolog K02159 BAX; apoptosis regulator BAX
D 108696744 bax.L; apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 379244 MGC53884; Dynamin-1-like protein-like K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 379875 dnm1l.L; dynamin 1-like L homeolog K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 735194 fis1.L; uncharacterized protein LOC735194 K17969 FIS1; mitochondrial fission 1 protein
D 733396 fis1.S; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 108705838 small ubiquitin-related modifier 3 isoform X1 K12160 SUMO; small ubiquitin-related modifier
D 379449 sumo3.L; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 379777 sumo2.L; small ubiquitin-related modifier 2-A K12160 SUMO; small ubiquitin-related modifier
D 444021 sumo2.S; small ubiquitin-related modifier 2-B K12160 SUMO; small ubiquitin-related modifier
D 399078 sumo1.L; small ubiquitin-related modifier 1-A K12160 SUMO; small ubiquitin-related modifier
D 779181 sumo1.S; small ubiquitin-related modifier 1-B K12160 SUMO; small ubiquitin-related modifier
D 443857 sh3glb1.S; SH3 domain GRB2 like, endophilin B1 S homeolog K11248 SH3GLB1; endophilin-B1
D 108714401 sh3glb1.L; endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1
D 379498 mtch2.L; mitochondrial carrier 2 L homeolog K17885 MTCH; mitochondrial carrier
D 108715225 mtch2.S; mitochondrial carrier homolog 2 isoform X2 K17885 MTCH; mitochondrial carrier
D 443869 mff.L; mitochondrial fission factor homolog B K22076 MFF; mitochondrial fission factor
D 446760 mff.S; mitochondrial fission factor homolog A isoform X1 K22076 MFF; mitochondrial fission factor
D 108700874 gdap1l1.L; ganglioside-induced differentiation-associated protein 1-like 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 108702576 gdap1l1.S; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 108719299 gdap1.L; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 100036826 vat1.S; uncharacterized protein LOC100036826 K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 444401 vat1.L; vesicle amine transport 1 L homeolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 108701679 mief2.L; mitochondrial dynamics protein MID49-like isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 108714529 mief1.L; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 443935 mief2.S; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 734397 mief1.S; uncharacterized protein LOC734397 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 100037063 pld6.S; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 443773 miga2.L; mitoguardin 2 K27289 MIGA; mitoguardin
D 431851 miga1.L; mitoguardin 1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 100337595 actg1.S; actin, cytoplasmic type 5 K05692 ACTB_G1; actin beta/gamma 1
D 734918 actg1.L; actin, cytoplasmic type 8 K05692 ACTB_G1; actin beta/gamma 1
D 108703086 actb.S; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 398459 actb.L; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 380338 naa20.S; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 733434 naa25.L; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
D 734215 naa25.S; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 379173 phb.L; prohibitin L homeolog K17080 PHB1; prohibitin 1
D 379509 phb.S; uncharacterized protein LOC379509 K17080 PHB1; prohibitin 1
D 444731 phb2.L; prohibitin 2 L homeolog K17081 PHB2; prohibitin 2
D 446470 phb2.S; prohibitin 2 S homeolog K17081 PHB2; prohibitin 2
D 108700468 kinectin isoform X1 K17975 KTN1; kinectin
D 108698890 kinectin isoform X1 K17975 KTN1; kinectin
C Retention of mitochondria
D 379244 MGC53884; Dynamin-1-like protein-like K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 379875 dnm1l.L; dynamin 1-like L homeolog K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 380409 myo5a.L; myosin VA L homeolog K10357 MYO5; myosin V
D 108711384 myo5c.L; unconventional myosin-Vc isoform X2 K10357 MYO5; myosin V
D 108718627 myo5b.L; unconventional myosin-Vb isoform X2 K10357 MYO5; myosin V
D 108712922 myo5a.S; unconventional myosin-Va isoform X4 K10357 MYO5; myosin V
D 108705475 myo5b.S; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 733235 xiap.L; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 100049147 diablo.L; diablo homolog, mitochondrial precursor K10522 DIABLO; diablo
D 108705716 diablo.S; diablo homolog, mitochondrial K10522 DIABLO; diablo
C Morphogenesis factors
D 100381058 snx25.L; sorting nexin-25 K17887 SNX25; sorting nexin-25
D 100158403 rhot1.L; ras homolog family member T1 L homeolog K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 108702234 rhot1.S; mitochondrial Rho GTPase 1 isoform X1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 100036792 immt.L; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 733343 immt.S; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60
D 100158358 mtfp1.L; mitochondrial fission process 1 L homeolog K17981 MTFP1; mitochondrial fission process protein 1
D 108699489 dap3.L; 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29
D 108712929 nedd4.S; E3 ubiquitin-protein ligase NEDD4 isoform X3 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 108711373 nedd4.L; E3 ubiquitin-protein ligase NEDD4 isoform X4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
D 100190768 oxr1.L; oxidation resistance protein 1 K25437 OXR1; oxidation resistance protein 1
D 734351 oxr1.S; oxidation resistance 1 S homeolog K25437 OXR1; oxidation resistance protein 1
D 108699490 msto1.L; protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 108713886 atg2a.L; autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2
D 108699808 atg2b.S; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2
D 108698738 atg2b.L; autophagy-related protein 2 homolog B K17906 ATG2; autophagy-related protein 2
D 443885 atg3.S; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 108707498 atg3.L; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 494717 atg4b.L; cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 495080 atg4c.S; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 447241 atg4d.L; LOW QUALITY PROTEIN: cysteine protease ATG4D K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 446253 atg4a.S; autophagy related 4A cysteine peptidase S homeolog K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 100137698 atg4d.S; uncharacterized protein LOC100137698 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 108698409 cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 108714230 atg4c.L; cysteine protease ATG4C-like isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 108718161 atg4b.S; cysteine protease ATG4B-like isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 443756 atg5.L; autophagy related 5 L homeolog K08339 ATG5; autophagy-related protein 5
D 444178 becn1.L; beclin-1 K08334 BECN; beclin
D 108701789 beclin-1-like K08334 BECN; beclin
D 108702722 beclin-1 isoform X1 K08334 BECN; beclin
D 108704011 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 414477 gabarap.L; uncharacterized protein LOC414477 K08341 GABARAP; GABA(A) receptor-associated protein
D 443979 gabarapl1.S; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 494762 gabarapl1.L; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein
D 734814 gabarapl2.L; GABA(A) receptor-associated protein like 2 L homeolog K08341 GABARAP; GABA(A) receptor-associated protein
D 108715442 gabarapl2.S; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 121402296 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein
D 108701286 atg9a.L; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 108704638 atg9b.L; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 108702922 atg9a.S; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 108717564 atg10.L; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 100126654 atg12.S; autophagy related 12 S homeolog K08336 ATG12; ubiquitin-like protein ATG12
D 108699170 atg14.L; beclin 1-associated autophagy-related key regulator isoform X1 K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 100049143 atg16l1.S; autophagy related 16 like 1 S homeolog K17890 ATG16L1; autophagy-related protein 16-1
D 495838 atg16l1.L; autophagy-related protein 16 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1
D 108708826 protein Atg16l2 K20868 ATG16L2; autophagy-related protein 16-2
D 380011 wipi2.L; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
D 446709 wipi1.L; WD repeat domain, phosphoinositide interacting 1 L homeolog K17908 WIPI1_2; autophagy-related protein 18
D 446901 wipi1.S; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
D 108717416 vacuolar protein 8 K08332 VAC8; vacuolar protein 8
C Parkin-dependent mechanism factors
D 495085 rnf41.L; uncharacterized protein LOC495085 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 734308 rnf41.S; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 108703106 clec16a.S; protein CLEC16A isoform X4 K19513 CLEC16A; protein CLEC16A
D 108701522 clec16a.L; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 108708122 parl.L; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 379610 sqstm1.L; sequestosome 1 L homeolog K14381 SQSTM1; sequestosome 1
D 100124683 tax1bp1.L; Tax1 binding protein 1 L homeolog K21347 TAX1BP1; Tax1-binding protein 1
D 414552 tax1bp1.S; Tax1 binding protein 1 S homeolog K21347 TAX1BP1; Tax1-binding protein 1
D 108702523 calcoco2.S; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 108700813 calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 108715245 ambra1.S; activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
D 121402910 activating molecule in BECN1-regulated autophagy protein 1-like isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 108713767 atg13.L; autophagy-related protein 13 isoform X2 K08331 ATG13; autophagy-related protein 13
D 108715246 atg13.S; autophagy-related protein 13 isoform X4 K08331 ATG13; autophagy-related protein 13
D 108716267 ulk1.L; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 108707144 ulk1.S; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 108709614 serine/threonine-protein kinase ULK2-like K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 108708293 ulk2.L; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 108695291 rb1cc1.S; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 733167 rb1cc1.L; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 446459 hsp90ab1.S; heat shock protein 90kDa alpha family class B member 1 S homeolog K04079 HSP90A; molecular chaperone HtpG
D 108716102 heat shock protein HSP 90-beta isoform X1 K04079 HSP90A; molecular chaperone HtpG
D 108698781 heat shock protein HSP 90-alpha isoform X1 K04079 HSP90A; molecular chaperone HtpG
D 379968 cdc37.S; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 398131 smurf1.L; E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 398372 smurf2.S; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 108701209 E3 ubiquitin-protein ligase SMURF2-like isoform X2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 108703087 smurf1.S; E3 ubiquitin-protein ligase SMURF1-like isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 779175 bnip3l.L; BCL2/adenovirus E1B 19kDa interacting protein 3-like L homeolog K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 108712712 bnip3l.S; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 734365 fundc1.S; FUN14 domain-containing protein 1A K17986 FUNDC1; FUN14 domain-containing protein 1
D 446354 MGC82241; FUN14 domain-containing protein 1B K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 495290 prkaa1.L; protein kinase, AMP-activated, alpha 1 catalytic subunit L homeolog K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 399172 prkaa2.S; protein kinase, AMP-activated, alpha 2 catalytic subunit S homeolog K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108715541 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 108714249 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 380234 map1lc3a.L; microtubule associated protein 1 light chain 3 alpha L homeolog K10435 MAP1LC; microtubule-associated protein 1 light chain
D 398857 map1lc3b.S; uncharacterized protein LOC398857 K10435 MAP1LC; microtubule-associated protein 1 light chain
D 733220 map1lc3b.L; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 779323 map1lc3c.L; microtubule associated protein 1 light chain 3 gamma L homeolog K10435 MAP1LC; microtubule-associated protein 1 light chain
D 379556 map1lc3a.S; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 108713898 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 108715162 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 379658 nbr1.L; neighbor of BRCA1 gene 1 L homeolog K17987 NBR1; next to BRCA1 gene 1 protein
D 108702726 nbr1.S; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein
D 108703147 tecpr1.S; LOW QUALITY PROTEIN: tectonin beta-propeller repeat-containing protein 1-like K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 108701895 tecpr1.L; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 444700 zfyve1.S; zinc finger FYVE-type containing 1 S homeolog K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 108700257 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 108698603 zfyve1l.L; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 108699185 zfyve1.L; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 444569 coasy.L; Coenzyme A synthase L homeolog precursor K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 446689 pla2g6.S; phospholipase A2 group VI S homeolog K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 108714545 pla2g6.L; 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 108715450 c19orf12.S; protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN
!
#
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024