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KO |
09100 Metabolism
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09101 Carbohydrate metabolism
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09102 Energy metabolism
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09103 Lipid metabolism
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00061 Fatty acid biosynthesis [PATH:chx00061]
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00062 Fatty acid elongation [PATH:chx00062]
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00071 Fatty acid degradation [PATH:chx00071]
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00073 Cutin, suberine and wax biosynthesis
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00100 Steroid biosynthesis [PATH:chx00100]
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00120 Primary bile acid biosynthesis [PATH:chx00120]
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00121 Secondary bile acid biosynthesis
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00140 Steroid hormone biosynthesis [PATH:chx00140]
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00561 Glycerolipid metabolism [PATH:chx00561]
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00564 Glycerophospholipid metabolism [PATH:chx00564]
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00565 Ether lipid metabolism [PATH:chx00565]
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00600 Sphingolipid metabolism [PATH:chx00600]
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102178736 SPTLC2; serine palmitoyltransferase 2
102173567 SPTLC1; serine palmitoyltransferase 1
102184072 SPTLC3; serine palmitoyltransferase 3
102183749 KDSR; 3-ketodihydrosphingosine reductase isoform X1
102189571 CERS1; ceramide synthase 1
102182556 CERS2; ceramide synthase 2
102174737 CERS4; ceramide synthase 4 isoform X1
102169911 CERS3; ceramide synthase 3
102176466 CERS6; ceramide synthase 6 isoform X2
102170747 CERS5; ceramide synthase 5 isoform X1
102170388 LOW QUALITY PROTEIN: ceramide synthase 5
102169733 ASAH1; acid ceramidase
102183481 neutral ceramidase
102179093 ACER1; alkaline ceramidase 1 isoform X1
102183323 ACER2; alkaline ceramidase 2 isoform X1
102177178 ACER3; alkaline ceramidase 3
102179052 DEGS2; sphingolipid delta(4)-desaturase/C4-monooxygenase DES2 isoform X1
102181802 DEGS1; sphingolipid delta(4)-desaturase DES1
102187660 SGMS2; phosphatidylcholine:ceramide cholinephosphotransferase 2
102184583 SGMS1; phosphatidylcholine:ceramide cholinephosphotransferase 1
102179963 SMPD1; LOW QUALITY PROTEIN: sphingomyelin phosphodiesterase
102186017 SMPD2; sphingomyelin phosphodiesterase 2
102169323 SMPD3; sphingomyelin phosphodiesterase 3
102169580 SMPD4; sphingomyelin phosphodiesterase 4 isoform X1
102186630 ENPP7; ectonucleotide pyrophosphatase/phosphodiesterase family member 7
102170015 ectonucleotide pyrophosphatase/phosphodiesterase family member 7-like
102180489 CERK; ceramide kinase
102171567 PLPP3; phospholipid phosphatase 3 isoform X1
102181946 PLPP2; phospholipid phosphatase 2 isoform X1
102183913 PLPP1; phospholipid phosphatase 1 isoform X1
102174749 SGPP1; sphingosine-1-phosphate phosphatase 1
102183470 SGPP2; sphingosine-1-phosphate phosphatase 2
102168201 SPHK1; sphingosine kinase 1 isoform X1
102184187 SPHK2; sphingosine kinase 2 isoform X1
100861080 SGPL1; sphingosine-1-phosphate lyase 1
102174936 UGCG; ceramide glucosyltransferase
102189810 GBA; glucosylceramidase
102179944 GBA2; non-lysosomal glucosylceramidase
102182084 B4GALT6; beta-1,4-galactosyltransferase 6 isoform X1
102172079 B4GALT5; beta-1,4-galactosyltransferase 5
102178493 GLB1; beta-galactosidase
102174638 UGT8; 2-hydroxyacylsphingosine 1-beta-galactosyltransferase
102188052 GALC; galactocerebrosidase isoform X1
102169694 GAL3ST1; galactosylceramide sulfotransferase isoform X1
102188131 ARSA; arylsulfatase A
102177389 NEU1; sialidase-1
108634534 NEU4; sialidase-4
102188734 NEU2; sialidase-2
102187969 NEU3; sialidase-3 isoform X1
102175656 GLA; alpha-galactosidase A
102173266 B4GALNT1; beta-1,4 N-acetylgalactosaminyltransferase 1 isoform X1
108634972 LOW QUALITY PROTEIN: beta-hexosaminidase subunit beta-like
102180045 HEXA; beta-hexosaminidase subunit alpha
102181720 HEXB; beta-hexosaminidase subunit beta
102181993 LOW QUALITY PROTEIN: beta-hexosaminidase subunit beta
102190510 GM2A; ganglioside GM2 activator
102175754 PSAPL1; proactivator polypeptide-like 1
102173365 PSAP; prosaposin isoform X1
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K00654 SPT; serine palmitoyltransferase [EC:2.3.1.50]
K00654 SPT; serine palmitoyltransferase [EC:2.3.1.50]
K00654 SPT; serine palmitoyltransferase [EC:2.3.1.50]
K04708 KDSR; 3-dehydrosphinganine reductase [EC:1.1.1.102]
K04710 CERS1; sphingoid base N-stearoyltransferase [EC:2.3.1.299]
K24621 CERS2_4; very-long-chain ceramide synthase [EC:2.3.1.297]
K24621 CERS2_4; very-long-chain ceramide synthase [EC:2.3.1.297]
K24622 CERS3; very-long-chain ceramide synthase / ultra-long-chain ceramide synthase [EC:2.3.1.297 2.3.1.298]
K23727 CERS5_6; sphingoid base N-palmitoyltransferase [EC:2.3.1.291]
K23727 CERS5_6; sphingoid base N-palmitoyltransferase [EC:2.3.1.291]
K23727 CERS5_6; sphingoid base N-palmitoyltransferase [EC:2.3.1.291]
K12348 ASAH1; acid ceramidase [EC:3.5.1.23]
K12349 ASAH2; neutral ceramidase [EC:3.5.1.23]
K01441 ACER1_2; alkaline ceramidase [EC:3.5.1.23]
K01441 ACER1_2; alkaline ceramidase [EC:3.5.1.23]
K04711 ACER3; dihydroceramidase [EC:3.5.1.-]
K04712 DEGS; sphingolipid 4-desaturase/C4-monooxygenase [EC:1.14.19.17 1.14.18.5]
K04712 DEGS; sphingolipid 4-desaturase/C4-monooxygenase [EC:1.14.19.17 1.14.18.5]
K04714 SGMS; shingomyelin synthase [EC:2.7.8.27]
K04714 SGMS; shingomyelin synthase [EC:2.7.8.27]
K12350 SMPD1; sphingomyelin phosphodiesterase [EC:3.1.4.12]
K12351 SMPD2; sphingomyelin phosphodiesterase 2 [EC:3.1.4.12]
K12352 SMPD3; sphingomyelin phosphodiesterase 3 [EC:3.1.4.12]
K12353 SMPD4; sphingomyelin phosphodiesterase 4 [EC:3.1.4.12]
K12354 ENPP7; ectonucleotide pyrophosphatase/phosphodiesterase family member 7 [EC:3.1.4.12]
K12354 ENPP7; ectonucleotide pyrophosphatase/phosphodiesterase family member 7 [EC:3.1.4.12]
K04715 CERK; ceramide kinase [EC:2.7.1.138]
K01080 PLPP1_2_3; phosphatidate phosphatase [EC:3.1.3.4]
K01080 PLPP1_2_3; phosphatidate phosphatase [EC:3.1.3.4]
K01080 PLPP1_2_3; phosphatidate phosphatase [EC:3.1.3.4]
K04716 SGPP1; sphingosine-1-phosphate phosphatase 1 [EC:3.1.3.-]
K04717 SGPP2; sphingosine-1-phosphate phosphotase 2 [EC:3.1.3.-]
K04718 SPHK; sphingosine kinase [EC:2.7.1.91]
K04718 SPHK; sphingosine kinase [EC:2.7.1.91]
K01634 SGPL1; sphinganine-1-phosphate aldolase [EC:4.1.2.27]
K00720 UGCG; ceramide glucosyltransferase [EC:2.4.1.80]
K01201 GBA; glucosylceramidase [EC:3.2.1.45]
K17108 GBA2; non-lysosomal glucosylceramidase [EC:3.2.1.45]
K07553 B4GALT6; beta-1,4-galactosyltransferase 6 [EC:2.4.1.274]
K09905 B4GALT5; beta-1,4-galactosyltransferase 5 [EC:2.4.1.274 2.4.1.-]
K12309 GLB1; beta-galactosidase [EC:3.2.1.23]
K04628 CGT; ceramide galactosyltransferase [EC:2.4.1.47]
K01202 GALC; galactosylceramidase [EC:3.2.1.46]
K01019 GAL3ST1; galactosylceramide sulfotransferase [EC:2.8.2.11]
K01134 ARSA; arylsulfatase A [EC:3.1.6.8]
K01186 NEU1; sialidase-1 [EC:3.2.1.18]
K12357 NEU2_3_4; sialidase-2/3/4 [EC:3.2.1.18]
K12357 NEU2_3_4; sialidase-2/3/4 [EC:3.2.1.18]
K12357 NEU2_3_4; sialidase-2/3/4 [EC:3.2.1.18]
K01189 GLA; alpha-galactosidase [EC:3.2.1.22]
K00725 B4GALNT1; (N-Acetylneuraminyl)-galactosylglucosylceramide N-acetylgalactosaminyltransferase [EC:2.4.1.92]
K12373 HEXA_B; hexosaminidase [EC:3.2.1.52]
K12373 HEXA_B; hexosaminidase [EC:3.2.1.52]
K12373 HEXA_B; hexosaminidase [EC:3.2.1.52]
K12373 HEXA_B; hexosaminidase [EC:3.2.1.52]
K12383 GM2A; ganglioside GM2 activator
K12382 PSAP; saposin
K12382 PSAP; saposin
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00590 Arachidonic acid metabolism [PATH:chx00590]
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00591 Linoleic acid metabolism [PATH:chx00591]
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00592 alpha-Linolenic acid metabolism [PATH:chx00592]
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01040 Biosynthesis of unsaturated fatty acids [PATH:chx01040]
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09104 Nucleotide metabolism
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09105 Amino acid metabolism
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09106 Metabolism of other amino acids
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09107 Glycan biosynthesis and metabolism
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00510 N-Glycan biosynthesis [PATH:chx00510]
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00513 Various types of N-glycan biosynthesis [PATH:chx00513]
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00512 Mucin type O-glycan biosynthesis [PATH:chx00512]
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00515 Mannose type O-glycan biosynthesis [PATH:chx00515]
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00514 Other types of O-glycan biosynthesis [PATH:chx00514]
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00532 Glycosaminoglycan biosynthesis - chondroitin sulfate / dermatan sulfate [PATH:chx00532]
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00534 Glycosaminoglycan biosynthesis - heparan sulfate / heparin [PATH:chx00534]
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00533 Glycosaminoglycan biosynthesis - keratan sulfate [PATH:chx00533]
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00531 Glycosaminoglycan degradation [PATH:chx00531]
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00563 Glycosylphosphatidylinositol (GPI)-anchor biosynthesis [PATH:chx00563]
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00601 Glycosphingolipid biosynthesis - lacto and neolacto series [PATH:chx00601]
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00603 Glycosphingolipid biosynthesis - globo and isoglobo series [PATH:chx00603]
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00604 Glycosphingolipid biosynthesis - ganglio series [PATH:chx00604]
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00511 Other glycan degradation [PATH:chx00511]
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102177389 NEU1; sialidase-1
108634534 NEU4; sialidase-4
102188734 NEU2; sialidase-2
102187969 NEU3; sialidase-3 isoform X1
102178493 GLB1; beta-galactosidase
108634972 LOW QUALITY PROTEIN: beta-hexosaminidase subunit beta-like
102180045 HEXA; beta-hexosaminidase subunit alpha
102181720 HEXB; beta-hexosaminidase subunit beta
102181993 LOW QUALITY PROTEIN: beta-hexosaminidase subunit beta
102175518 HEXDC; hexosaminidase D isoform X1
102190996 MAN2C1; alpha-mannosidase 2C1 isoform X1
102183410 MAN2B1; lysosomal alpha-mannosidase
102171400 epididymis-specific alpha-mannosidase-like
102189848 LOW QUALITY PROTEIN: epididymis-specific alpha-mannosidase
102173830 epididymis-specific alpha-mannosidase-like
102188844 epididymis-specific alpha-mannosidase-like
100750234 MANBA; beta-mannosidase precursor
102187164 ENGASE; cytosolic endo-beta-N-acetylglucosaminidase isoform X1
102179566 FUCA2; plasma alpha-L-fucosidase
102180711 FUCA1; tissue alpha-L-fucosidase
102190099 AGA; N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase
102189810 GBA; glucosylceramidase
102179944 GBA2; non-lysosomal glucosylceramidase
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K01186 NEU1; sialidase-1 [EC:3.2.1.18]
K12357 NEU2_3_4; sialidase-2/3/4 [EC:3.2.1.18]
K12357 NEU2_3_4; sialidase-2/3/4 [EC:3.2.1.18]
K12357 NEU2_3_4; sialidase-2/3/4 [EC:3.2.1.18]
K12309 GLB1; beta-galactosidase [EC:3.2.1.23]
K12373 HEXA_B; hexosaminidase [EC:3.2.1.52]
K12373 HEXA_B; hexosaminidase [EC:3.2.1.52]
K12373 HEXA_B; hexosaminidase [EC:3.2.1.52]
K12373 HEXA_B; hexosaminidase [EC:3.2.1.52]
K14459 HEX; hexosaminidase [EC:3.2.1.52]
K01191 MAN2C1; alpha-mannosidase [EC:3.2.1.24]
K12311 MAN2B1; lysosomal alpha-mannosidase [EC:3.2.1.24]
K12312 MAN2B2; epididymis-specific alpha-mannosidase [EC:3.2.1.24]
K12312 MAN2B2; epididymis-specific alpha-mannosidase [EC:3.2.1.24]
K12312 MAN2B2; epididymis-specific alpha-mannosidase [EC:3.2.1.24]
K12312 MAN2B2; epididymis-specific alpha-mannosidase [EC:3.2.1.24]
K01192 E3.2.1.25; beta-mannosidase [EC:3.2.1.25]
K01227 ENGASE; mannosyl-glycoprotein endo-beta-N-acetylglucosaminidase [EC:3.2.1.96]
K01206 FUCA; alpha-L-fucosidase [EC:3.2.1.51]
K01206 FUCA; alpha-L-fucosidase [EC:3.2.1.51]
K01444 AGA; N4-(beta-N-acetylglucosaminyl)-L-asparaginase [EC:3.5.1.26]
K01201 GBA; glucosylceramidase [EC:3.2.1.45]
K17108 GBA2; non-lysosomal glucosylceramidase [EC:3.2.1.45]
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00540 Lipopolysaccharide biosynthesis
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00542 O-Antigen repeat unit biosynthesis
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00541 O-Antigen nucleotide sugar biosynthesis
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00550 Peptidoglycan biosynthesis
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00552 Teichoic acid biosynthesis
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00571 Lipoarabinomannan (LAM) biosynthesis
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00572 Arabinogalactan biosynthesis - Mycobacterium
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00543 Exopolysaccharide biosynthesis
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09108 Metabolism of cofactors and vitamins
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09109 Metabolism of terpenoids and polyketides
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09110 Biosynthesis of other secondary metabolites
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09111 Xenobiotics biodegradation and metabolism
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09112 Not included in regular maps
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09120 Genetic Information Processing
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09130 Environmental Information Processing
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09140 Cellular Processes
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09150 Organismal Systems
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09160 Human Diseases
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09180 Brite Hierarchies
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09190 Not Included in Pathway or Brite
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