KEGG Orthology (KO) - Homo sapiens (human)

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     KO
 09100 Metabolism
 
 09120 Genetic Information Processing
 
 09130 Environmental Information Processing
 
 09140 Cellular Processes
 
 09150 Organismal Systems
 
 09160 Human Diseases
 
 09180 Brite Hierarchies
 
   09181 Protein families: metabolism
 
   09182 Protein families: genetic information processing
     03000 Transcription factors [BR:hsa03000]
     03021 Transcription machinery [BR:hsa03021]
     03019 Messenger RNA biogenesis [BR:hsa03019]
     03041 Spliceosome [BR:hsa03041]
     03011 Ribosome [BR:hsa03011]
     03009 Ribosome biogenesis [BR:hsa03009]
     03016 Transfer RNA biogenesis [BR:hsa03016]
     03012 Translation factors [BR:hsa03012]
       9086 EIF1AY; eukaryotic translation initiation factor 1A Y-linked
       1964 EIF1AX; eukaryotic translation initiation factor 1A X-linked
       124905557 eukaryotic translation initiation factor 1A, X-chromosomal
       10289 EIF1B; eukaryotic translation initiation factor 1B
       10209 EIF1; eukaryotic translation initiation factor 1
       1965 EIF2S1; eukaryotic translation initiation factor 2 subunit alpha
       8894 EIF2S2; eukaryotic translation initiation factor 2 subunit beta
       1968 EIF2S3; eukaryotic translation initiation factor 2 subunit gamma
       83939 EIF2A; eukaryotic translation initiation factor 2A
       1967 EIF2B1; eukaryotic translation initiation factor 2B subunit alpha
       8892 EIF2B2; eukaryotic translation initiation factor 2B subunit beta
       8891 EIF2B3; eukaryotic translation initiation factor 2B subunit gamma
       8890 EIF2B4; eukaryotic translation initiation factor 2B subunit delta
       8893 EIF2B5; eukaryotic translation initiation factor 2B subunit epsilon
       1939 EIF2D; eukaryotic translation initiation factor 2D
       1983 EIF5; eukaryotic translation initiation factor 5
       56648 EIF5A2; eukaryotic translation initiation factor 5A2
       1984 EIF5A; eukaryotic translation initiation factor 5A
       143244 EIF5AL1; eukaryotic translation initiation factor 5A like 1
       9669 EIF5B; eukaryotic translation initiation factor 5B
       3692 EIF6; eukaryotic translation initiation factor 6
       8661 EIF3A; eukaryotic translation initiation factor 3 subunit A
       8662 EIF3B; eukaryotic translation initiation factor 3 subunit B
       8663 EIF3C; eukaryotic translation initiation factor 3 subunit C
       728689 EIF3CL; eukaryotic translation initiation factor 3 subunit C like
       8664 EIF3D; eukaryotic translation initiation factor 3 subunit D
       3646 EIF3E; eukaryotic translation initiation factor 3 subunit E
       8665 EIF3F; eukaryotic translation initiation factor 3 subunit F
       8666 EIF3G; eukaryotic translation initiation factor 3 subunit G
       8667 EIF3H; eukaryotic translation initiation factor 3 subunit H
       8668 EIF3I; eukaryotic translation initiation factor 3 subunit I
       8669 EIF3J; eukaryotic translation initiation factor 3 subunit J
       27335 EIF3K; eukaryotic translation initiation factor 3 subunit K
       51386 EIF3L; eukaryotic translation initiation factor 3 subunit L
       10480 EIF3M; eukaryotic translation initiation factor 3 subunit M
       1973 EIF4A1; eukaryotic translation initiation factor 4A1
       1974 EIF4A2; eukaryotic translation initiation factor 4A2
       9775 EIF4A3; eukaryotic translation initiation factor 4A3
       1975 EIF4B; eukaryotic translation initiation factor 4B
       1977 EIF4E; eukaryotic translation initiation factor 4E
       9470 EIF4E2; eukaryotic translation initiation factor 4E family member 2
       253314 EIF4E1B; eukaryotic translation initiation factor 4E family member 1B
       8672 EIF4G3; eukaryotic translation initiation factor 4 gamma 3
       1981 EIF4G1; eukaryotic translation initiation factor 4 gamma 1
       1982 EIF4G2; eukaryotic translation initiation factor 4 gamma 2
       7458 EIF4H; eukaryotic translation initiation factor 4H
       4528 MTIF2; mitochondrial translational initiation factor 2
       219402 MTIF3; mitochondrial translational initiation factor 3
       23 ABCF1; ATP binding cassette subfamily F member 1
       55324 ABCF3; ATP binding cassette subfamily F member 3
       23277 CLUH; clustered mitochondria homolog
       54505 DHX29; DExH-box helicase 29
       3508 IGHMBP2; immunoglobulin mu DNA binding protein 2
       26608 TBL2; transducin beta like 2
       1915 EEF1A1; eukaryotic translation elongation factor 1 alpha 1
       1917 EEF1A2; eukaryotic translation elongation factor 1 alpha 2
       1933 EEF1B2; eukaryotic translation elongation factor 1 beta 2
       1937 EEF1G; eukaryotic translation elongation factor 1 gamma
       1936 EEF1D; eukaryotic translation elongation factor 1 delta
       1938 EEF2; eukaryotic translation elongation factor 2
       10102 TSFM; Ts translation elongation factor, mitochondrial
       7284 TUFM; Tu translation elongation factor, mitochondrial
       84340 GFM2; GTP dependent ribosome recycling factor mitochondrial 2
       85476 GFM1; G elongation factor mitochondrial 1
       60678 EEFSEC; eukaryotic elongation factor, selenocysteine-tRNA specific
       1801 DPH1; diphthamide biosynthesis 1
       1802 DPH2; diphthamide biosynthesis 2
       285381 DPH3; diphthamide biosynthesis 3
       120526 DNAJC24; DnaJ heat shock protein family (Hsp40) member C24
       51611 DPH5; diphthamide biosynthesis 5
       89978 DPH6; diphthamine biosynthesis 6
       92715 DPH7; diphthamide biosynthesis 7
       79048 SECISBP2; SECIS binding protein 2
       9728 SECISBP2L; SECIS binding protein 2 like
       221143 EEF1AKMT1; EEF1A lysine methyltransferase 1
       399818 EEF1AKMT2; EEF1A lysine methyltransferase 2
       25895 EEF1AKMT3; EEF1A lysine methyltransferase 3
       110599583 EEF1AKMT4-ECE2; EEF1AKMT4-ECE2 readthrough
       110599564 EEF1AKMT4; EEF1A lysine methyltransferase 4
       51603 METTL13; methyltransferase 13, eEF1A N-terminus and K55
       196483 EEF2KMT; eukaryotic elongation factor 2 lysine methyltransferase
       85002 FAM86B1; family with sequence similarity 86 member B1
       128966622 putative protein N-methyltransferase FAM86B2
       653333 FAM86B2; family with sequence similarity 86 member B2
       9567 GTPBP1; GTP binding protein 1
       2107 ETF1; eukaryotic translation termination factor 1
       23708 GSPT2; G1 to S phase transition 2
       2935 GSPT1; G1 to S phase transition 1
       7978 MTERF1; mitochondrial transcription termination factor 1
       80298 MTERF2; mitochondrial transcription termination factor 2
       130916 MTERF4; mitochondrial transcription termination factor 4
       51001 MTERF3; mitochondrial transcription termination factor 3
       3396 MRPL58; mitochondrial ribosomal protein L58
       54516 MTRF1L; mitochondrial translation release factor 1 like
       9617 MTRF1; mitochondrial translation release factor 1
       92399 MRRF; mitochondrial ribosome recycling factor
       51409 HEMK1; HemK methyltransferase family member 1
       29104 N6AMT1; N-6 adenine-specific DNA methyltransferase 1
       51504 TRMT112; tRNA methyltransferase activator subunit 11-2
       138428 PTRH1; peptidyl-tRNA hydrolase 1 homolog
       51651 PTRH2; peptidyl-tRNA hydrolase 2
K03236 EIF1A; translation initiation factor 1A
K03236 EIF1A; translation initiation factor 1A
K03236 EIF1A; translation initiation factor 1A
K03113 EIF1; translation initiation factor 1
K03113 EIF1; translation initiation factor 1
K03237 EIF2S1; translation initiation factor 2 subunit 1
K03238 EIF2S2; translation initiation factor 2 subunit 2
K03242 EIF2S3; translation initiation factor 2 subunit 3
K15026 EIF2A; translation initiation factor 2A
K03239 EIF2B1; translation initiation factor eIF-2B subunit alpha
K03754 EIF2B2; translation initiation factor eIF-2B subunit beta
K03241 EIF2B3; translation initiation factor eIF-2B subunit gamma
K03680 EIF2B4; translation initiation factor eIF-2B subunit delta
K03240 EIF2B5; translation initiation factor eIF-2B subunit epsilon
K15027 EIF2D; translation initiation factor 2D
K03262 EIF5; translation initiation factor 5
K03263 EIF5A; translation initiation factor 5A
K03263 EIF5A; translation initiation factor 5A
K03263 EIF5A; translation initiation factor 5A
K03243 EIF5B; translation initiation factor 5B
K03264 EIF6; translation initiation factor 6
K03254 EIF3A; translation initiation factor 3 subunit A
K03253 EIF3B; translation initiation factor 3 subunit B
K03252 EIF3C; translation initiation factor 3 subunit C
K03252 EIF3C; translation initiation factor 3 subunit C
K03251 EIF3D; translation initiation factor 3 subunit D
K03250 EIF3E; translation initiation factor 3 subunit E
K03249 EIF3F; translation initiation factor 3 subunit F
K03248 EIF3G; translation initiation factor 3 subunit G
K03247 EIF3H; translation initiation factor 3 subunit H
K03246 EIF3I; translation initiation factor 3 subunit I
K03245 EIF3J; translation initiation factor 3 subunit J
K15028 EIF3K; translation initiation factor 3 subunit K
K15029 EIF3L; translation initiation factor 3 subunit L
K15030 EIF3M; translation initiation factor 3 subunit M
K03257 EIF4A; translation initiation factor 4A
K03257 EIF4A; translation initiation factor 4A
K13025 EIF4A3; ATP-dependent RNA helicase [EC:5.6.2.7]
K03258 EIF4B; translation initiation factor 4B
K03259 EIF4E; translation initiation factor 4E
K03259 EIF4E; translation initiation factor 4E
K03259 EIF4E; translation initiation factor 4E
K03260 EIF4G; translation initiation factor 4G
K03260 EIF4G; translation initiation factor 4G
K03260 EIF4G; translation initiation factor 4G
K24086 EIF4H; translation initiation factor 4H
K02519 infB; translation initiation factor IF-2
K02520 infC; translation initiation factor IF-3
K06184 ABCF1; ATP-binding cassette, subfamily F, member 1
K06158 ABCF3; ATP-binding cassette, subfamily F, member 3
K03255 TIF31; protein TIF31
K18995 DHX29; ATP-dependent RNA helicase DHX29 [EC:5.6.2.6]
K19036 IGHMBP2; ATP-dependent RNA/DNA helicase IGHMBP2 [EC:5.6.2.5 5.6.2.3]
K23325 TBL2; transducin beta-like protein 2
K03231 EEF1A; elongation factor 1-alpha
K03231 EEF1A; elongation factor 1-alpha
K03232 EEF1B; elongation factor 1-beta
K03233 EEF1G; elongation factor 1-gamma
K15410 EEF1D; elongation factor 1-delta
K03234 EEF2; elongation factor 2
K02357 tsf; elongation factor Ts
K02358 tuf; elongation factor Tu
K02355 fusA; elongation factor G
K02355 fusA; elongation factor G
K03833 selB; selenocysteine-specific elongation factor
K07561 DPH1; 2-(3-amino-3-carboxypropyl)histidine synthase [EC:2.5.1.108]
K17866 DPH2; diphthamide biosynthesis protein 2
K15455 DPH3; diphthamide biosynthesis protein 3
K17867 DPH4; diphthamide biosynthesis protein 4
K00586 DPH5; diphthine methyl ester synthase [EC:2.1.1.314]
K06927 DPH6; diphthine-ammonia ligase [EC:6.3.1.14]
K17868 DPH7; diphthine methyl ester acylhydrolase [EC:3.1.1.97]
K19539 SECISBP2; selenocysteine insertion sequence-binding protein 2
K19539 SECISBP2; selenocysteine insertion sequence-binding protein 2
K22855 EEF1AKMT1; EEF1A lysine methyltransferase 1 [EC:2.1.1.-]
K22856 EEF1AKMT2; EEF1A lysine methyltransferase 2 [EC:2.1.1.-]
K21803 METTL21B; EEF1A lysine methyltransferase 3 [EC:2.1.1.-]
K01415 ECE; endothelin-converting enzyme [EC:3.4.24.71]
K22857 EEF1AKMT4; EEF1A lysine methyltransferase 4 [EC:2.1.1.-]
K25166 EEF1AKNMT; eEF1A lysine and N-terminal methyltransferase [EC:2.1.1.-]
K22696 EEF2KMT; protein-lysine N-methyltransferase EEF2KMT [EC:2.1.1.-]
K22696 EEF2KMT; protein-lysine N-methyltransferase EEF2KMT [EC:2.1.1.-]
K22696 EEF2KMT; protein-lysine N-methyltransferase EEF2KMT [EC:2.1.1.-]
K22696 EEF2KMT; protein-lysine N-methyltransferase EEF2KMT [EC:2.1.1.-]
K24887 GTPBP1; GTP-binding protein 1
K03265 ETF1; peptide chain release factor subunit 1
K03267 ERF3; peptide chain release factor subunit 3
K03267 ERF3; peptide chain release factor subunit 3
K15031 MTERF; mitochondrial transcription termination factor family protein
K15031 MTERF; mitochondrial transcription termination factor family protein
K15031 MTERF; mitochondrial transcription termination factor family protein
K15031 MTERF; mitochondrial transcription termination factor family protein
K15033 ICT1; peptidyl-tRNA hydrolase ICT1 [EC:3.1.1.29]
K02835 prfA; peptide chain release factor 1
K02835 prfA; peptide chain release factor 1
K02838 frr; ribosome recycling factor
K02493 hemK; release factor glutamine methyltransferase [EC:2.1.1.297]
K19589 N6AMT1; release factor glutamine methyltransferase [EC:2.1.1.297]
K15448 TRM112; multifunctional methyltransferase subunit TRM112
K01056 PTH1; peptidyl-tRNA hydrolase, PTH1 family [EC:3.1.1.29]
K04794 PTH2; peptidyl-tRNA hydrolase, PTH2 family [EC:3.1.1.29]
     03110 Chaperones and folding catalysts [BR:hsa03110]
     04131 Membrane trafficking [BR:hsa04131]
     04121 Ubiquitin system [BR:hsa04121]
     03051 Proteasome [BR:hsa03051]
     03032 DNA replication proteins [BR:hsa03032]
     03036 Chromosome and associated proteins [BR:hsa03036]
     03400 DNA repair and recombination proteins [BR:hsa03400]
     03029 Mitochondrial biogenesis [BR:hsa03029]
       4535 ND1; NADH dehydrogenase subunit 1
       4536 ND2; NADH dehydrogenase subunit 2
       4537 ND3; NADH dehydrogenase subunit 3
       4538 ND4; NADH dehydrogenase subunit 4
       4539 ND4L; NADH dehydrogenase subunit 4L
       4540 ND5; NADH dehydrogenase subunit 5
       4541 ND6; NADH dehydrogenase subunit 6
       4519 CYTB; cytochrome b
       4512 COX1; cytochrome c oxidase subunit I
       4513 COX2; cytochrome c oxidase subunit II
       4514 COX3; cytochrome c oxidase subunit III
       4509 ATP8; ATP synthase F0 subunit 8
       4508 ATP6; ATP synthase F0 subunit 6
       5442 POLRMT; RNA polymerase mitochondrial
       7019 TFAM; transcription factor A, mitochondrial
       51106 TFB1M; transcription factor B1, mitochondrial
       64216 TFB2M; transcription factor B2, mitochondrial
       4528 MTIF2; mitochondrial translational initiation factor 2
       219402 MTIF3; mitochondrial translational initiation factor 3
       10102 TSFM; Ts translation elongation factor, mitochondrial
       7284 TUFM; Tu translation elongation factor, mitochondrial
       84340 GFM2; GTP dependent ribosome recycling factor mitochondrial 2
       85476 GFM1; G elongation factor mitochondrial 1
       7978 MTERF1; mitochondrial transcription termination factor 1
       80298 MTERF2; mitochondrial transcription termination factor 2
       130916 MTERF4; mitochondrial transcription termination factor 4
       51001 MTERF3; mitochondrial transcription termination factor 3
       60558 GUF1; GTP binding elongation factor GUF1
       10940 POP1; POP1 homolog, ribonuclease P/MRP subunit
       10775 POP4; POP4 homolog, ribonuclease P/MRP subunit
       51367 POP5; POP5 homolog, ribonuclease P/MRP subunit
       10556 RPP30; ribonuclease P/MRP subunit p30
       10248 POP7; POP7 homolog, ribonuclease P/MRP subunit
       138716 RPP25L; ribonuclease P/MRP subunit p25 like
       54913 RPP25; ribonuclease P and MRP subunit p25
       10557 RPP38; ribonuclease P/MRP subunit p38
       10799 RPP40; ribonuclease P/MRP subunit p40
       54931 TRMT10C; tRNA methyltransferase 10C, mitochondrial RNase P subunit
       3028 HSD17B10; hydroxysteroid 17-beta dehydrogenase 10
       9692 PRORP; protein only RNase P catalytic subunit
       118490 MSS51; MSS51 mitochondrial translational activator
       79736 TEFM; transcription elongation factor, mitochondrial
       100526740 ATP5MF-PTCD1; ATP5MF-PTCD1 readthrough
       26024 PTCD1; pentatricopeptide repeat domain 1
       79810 PTCD2; pentatricopeptide repeat domain 2
       55037 PTCD3; pentatricopeptide repeat domain 3
       22907 DHX30; DExH-box helicase 30
       55245 UQCC1; ubiquinol-cytochrome c reductase complex assembly factor 1
       246269 AFG1L; AFG1 like ATPase
       91419 ATP23; ATP23 metallopeptidase and ATP synthase assembly factor homolog
       6832 SUPV3L1; Suv3 like RNA helicase
       51110 LACTB2; lactamase beta 2
       291 SLC25A4; solute carrier family 25 member 4
       292 SLC25A5; solute carrier family 25 member 5
       293 SLC25A6; solute carrier family 25 member 6
       83447 SLC25A31; solute carrier family 25 member 31
       51312 SLC25A37; solute carrier family 25 member 37
       81894 SLC25A28; solute carrier family 25 member 28
       115416 MALSU1; mitochondrial assembly of ribosomal large subunit 1
       26284 ERAL1; Era like 12S mitochondrial rRNA chaperone 1
       8565 YARS1; tyrosyl-tRNA synthetase 1
       51067 YARS2; tyrosyl-tRNA synthetase 2
       51520 LARS1; leucyl-tRNA synthetase 1
       23395 LARS2; leucyl-tRNA synthetase 2, mitochondrial
       55157 DARS2; aspartyl-tRNA synthetase 2, mitochondrial
       2617 GARS1; glycyl-tRNA synthetase 1
       57038 RARS2; arginyl-tRNA synthetase 2, mitochondrial
       5917 RARS1; arginyl-tRNA synthetase 1
       55278 QRSL1; glutaminyl-tRNA amidotransferase subunit QRSL1
       5188 GATB; glutamyl-tRNA amidotransferase subunit B
       283459 GATC; glutamyl-tRNA amidotransferase subunit C
       55149 MTPAP; mitochondrial poly(A) polymerase
       201626 PDE12; phosphodiesterase 12
       92170 MTG1; mitochondrial ribosome associated GTPase 1
       84273 NOA1; nitric oxide associated 1
       63899 NSUN3; NOP2/Sun RNA methyltransferase 3
       387338 NSUN4; NOP2/Sun RNA methyltransferase 4
       285367 RPUSD3; RNA pseudouridine synthase D3
       84881 RPUSD4; RNA pseudouridine synthase D4
       81554 RCC1L; RCC1 like
       51335 NGRN; neugrin, neurite outgrowth associated
       26995 TRUB2; TruB pseudouridine synthase family member 2
       22868 FASTKD2; FAST kinase domains 2
       91574 MTRFR; mitochondrial translation release factor in rescue
       55005 RMND1; required for meiotic nuclear division 1 homolog
       2926 GRSF1; G-rich RNA sequence binding factor 1
       196074 METTL15; methyltransferase 15, mitochondrial 12S rRNA N4-cytidine
       60314 MYG1; MYG1 exonuclease
       51250 MTRES1; mitochondrial transcription rescue factor 1
       5428 POLG; DNA polymerase gamma, catalytic subunit
       11232 POLG2; DNA polymerase gamma 2, accessory subunit
       201973 PRIMPOL; primase and DNA directed polymerase
       2021 ENDOG; endonuclease G
       92667 MGME1; mitochondrial genome maintenance exonuclease 1
       9941 EXOG; exo/endonuclease G
       56652 TWNK; twinkle mtDNA helicase
       80119 PIF1; PIF1 5'-to-3' DNA helicase
       6742 SSBP1; single stranded DNA binding protein 1
       83858 ATAD3B; ATPase family AAA domain containing 3B
       55210 ATAD3A; ATPase family AAA domain containing 3A
       84300 UQCC2; ubiquinol-cytochrome c reductase complex assembly factor 2
       10294 DNAJA2; DnaJ heat shock protein family (Hsp40) member A2
       10953 TOMM34; translocase of outer mitochondrial membrane 34
       55288 RHOT1; ras homolog family member T1
       3312 HSPA8; heat shock protein family A (Hsp70) member 8
       3303 HSPA1A; heat shock protein family A (Hsp70) member 1A
       3305 HSPA1L; heat shock protein family A (Hsp70) member 1 like
       3304 HSPA1B; heat shock protein family A (Hsp70) member 1B
       3310 HSPA6; heat shock protein family A (Hsp70) member 6
       23746 AIPL1; aryl hydrocarbon receptor interacting protein like 1
       9049 AIP; aryl hydrocarbon receptor interacting protein
       10452 TOMM40; translocase of outer mitochondrial membrane 40
       84134 TOMM40L; translocase of outer mitochondrial membrane 40 like
       9868 TOMM70; translocase of outer mitochondrial membrane 70
       56993 TOMM22; translocase of outer mitochondrial membrane 22
       387990 TOMM20L; translocase of outer mitochondrial membrane 20 like
       9804 TOMM20; translocase of outer mitochondrial membrane 20
       54543 TOMM7; translocase of outer mitochondrial membrane 7
       100188893 TOMM6; translocase of outer mitochondrial membrane 6
       401505 TOMM5; translocase of outer mitochondrial membrane 5
       25813 SAMM50; SAMM50 sorting and assembly machinery component
       7416 VDAC1; voltage dependent anion channel 1
       7417 VDAC2; voltage dependent anion channel 2
       7419 VDAC3; voltage dependent anion channel 3
       345778 MTX3; metaxin 3
       4580 MTX1; metaxin 1
       10651 MTX2; metaxin 2
       80179 MYO19; myosin XIX
       51309 ARMCX1; armadillo repeat containing X-linked 1
       9823 ARMCX2; armadillo repeat containing X-linked 2
       51566 ARMCX3; armadillo repeat containing X-linked 3
       54470 ARMCX6; armadillo repeat containing X-linked 6
       64757 MTARC1; mitochondrial amidoxime reducing component 1
       54996 MTARC2; mitochondrial amidoxime reducing component 2
       26520 TIMM9; translocase of inner mitochondrial membrane 9
       26519 TIMM10; translocase of inner mitochondrial membrane 10
       26515 TIMM10B; translocase of inner mitochondrial membrane 10B
       1678 TIMM8A; translocase of inner mitochondrial membrane 8A
       26521 TIMM8B; translocase of inner mitochondrial membrane 8 homolog B
       26517 TIMM13; translocase of inner mitochondrial membrane 13
       131474 CHCHD4; coiled-coil-helix-coiled-coil-helix domain containing 4
       2671 GFER; growth factor, augmenter of liver regeneration
       440574 MICOS10; mitochondrial contact site and cristae organizing system subunit 10
       10989 IMMT; inner membrane mitochondrial protein
       125988 MICOS13; mitochondrial contact site and cristae organizing system subunit 13
       54927 CHCHD3; coiled-coil-helix-coiled-coil-helix domain containing 3
       84303 CHCHD6; coiled-coil-helix-coiled-coil-helix domain containing 6
       79135 APOO; apolipoprotein O
       139322 APOOL; apolipoprotein O like
       29928 TIMM22; translocase of inner mitochondrial membrane 22
       100287932 TIMM23; translocase of inner mitochondrial membrane 23
       100652748 TIMM23B; translocase of inner mitochondrial membrane 23 homolog B
       10245 TIMM17B; translocase of inner mitochondrial membrane 17B
       10440 TIMM17A; translocase of inner mitochondrial membrane 17A
       29090 TIMM21; translocase of inner mitochondrial membrane 21
       92609 TIMM50; translocase of inner mitochondrial membrane 50
       90550 MCU; mitochondrial calcium uniporter
       10367 MICU1; mitochondrial calcium uptake 1
       221154 MICU2; mitochondrial calcium uptake 2
       55013 MCUB; mitochondrial calcium uniporter dominant negative subunit beta
       91689 SMDT1; single-pass membrane protein with aspartate rich tail 1
       63933 MCUR1; mitochondrial calcium uniporter regulator 1
       3954 LETM1; leucine zipper and EF-hand containing transmembrane protein 1
       196294 IMMP1L; inner mitochondrial membrane peptidase subunit 1
       83943 IMMP2L; inner mitochondrial membrane peptidase subunit 2
       84233 TMEM126A; transmembrane protein 126A
       347411 MPC1L; mitochondrial pyruvate carrier 1 like
       51660 MPC1; mitochondrial pyruvate carrier 1
       25874 MPC2; mitochondrial pyruvate carrier 2
       400916 CHCHD10; coiled-coil-helix-coiled-coil-helix domain containing 10
       10469 TIMM44; translocase of inner mitochondrial membrane 44
       3313 HSPA9; heat shock protein family A (Hsp70) member 9
       134266 GRPEL2; GrpE like 2, mitochondrial
       80273 GRPEL1; GrpE like 1, mitochondrial
       131118 DNAJC19; DnaJ heat shock protein family (Hsp40) member C19
       51025 PAM16; presequence translocase associated motor 16
       23203 PMPCA; peptidase, mitochondrial processing subunit alpha
       9512 PMPCB; peptidase, mitochondrial processing subunit beta
       4285 MIPEP; mitochondrial intermediate peptidase
       3329 HSPD1; heat shock protein family D (Hsp60) member 1
       3336 HSPE1; heat shock protein family E (Hsp10) member 1
       9093 DNAJA3; DnaJ heat shock protein family (Hsp40) member A3
       132001 TAMM41; TAM41 mitochondrial translocator assembly and maintenance homolog
       728489 DNLZ; DNL-type zinc finger
       23474 ETHE1; ETHE1 persulfide dioxygenase
       26073 POLDIP2; DNA polymerase delta interacting protein 2
       1385 CREB1; cAMP responsive element binding protein 1
       6667 SP1; Sp1 transcription factor
       7528 YY1; YY1 transcription factor
       404281 YY2; YY2 transcription factor
       2553 GABPB1; GA binding protein transcription factor subunit beta 1
       126626 GABPB2; GA binding protein transcription factor subunit beta 2
       4899 NRF1; nuclear respiratory factor 1
       4780 NFE2L2; NFE2 like bZIP transcription factor 2
       4490 MT1B; metallothionein 1B
       4493 MT1E; metallothionein 1E
       4494 MT1F; metallothionein 1F
       4495 MT1G; metallothionein 1G
       4496 MT1H; metallothionein 1H
       4499 MT1M; metallothionein 1M
       4501 MT1X; metallothionein 1X
       4502 MT2A; metallothionein 2A
       4489 MT1A; metallothionein 1A
       645745 MT1HL1; metallothionein 1H like 1
       4504 MT3; metallothionein 3
       84560 MT4; metallothionein 4
       10891 PPARGC1A; PPARG coactivator 1 alpha
       133522 PPARGC1B; PPARG coactivator 1 beta
       23082 PPRC1; PPARG related coactivator 1
       23373 CRTC1; CREB regulated transcription coactivator 1
       1387 CREBBP; CREB binding protein
       2033 EP300; E1A binding protein p300
       9054 NFS1; NFS1 cysteine desulfurase
       23479 ISCU; iron-sulfur cluster assembly enzyme
       57128 LYRM4; LYR motif containing 4
       2395 FXN; frataxin
       2230 FDX1; ferredoxin 1
       112812 FDX2; ferredoxin 2
       2232 FDXR; ferredoxin reductase
       150274 HSCB; HscB mitochondrial iron-sulfur cluster cochaperone
       64374 SIL1; SIL1 nucleotide exchange factor
       51218 GLRX5; glutaredoxin 5
       81689 ISCA1; iron-sulfur cluster assembly 1
       122961 ISCA2; iron-sulfur cluster assembly 2
       200205 IBA57; iron-sulfur cluster assembly factor IBA57
       27247 NFU1; NFU1 iron-sulfur cluster scaffold
       51027 BOLA1; bolA family member 1
       388962 BOLA3; bolA family member 3
       81855 SFXN3; sideroflexin 3
       94081 SFXN1; sideroflexin 1
       118980 SFXN2; sideroflexin 2
       119559 SFXN4; sideroflexin 4
       94097 SFXN5; sideroflexin 5
       1374 CPT1A; carnitine palmitoyltransferase 1A
       1375 CPT1B; carnitine palmitoyltransferase 1B
       126129 CPT1C; carnitine palmitoyltransferase 1C
       55526 DHTKD1; dehydrogenase E1 and transketolase domain containing 1
       26235 FBXL4; F-box and leucine rich repeat protein 4
       3054 HCFC1; host cell factor C1
       29915 HCFC2; host cell factor C2
       3064 HTT; huntingtin
       2101 ESRRA; estrogen related receptor alpha
       2103 ESRRB; estrogen related receptor beta
       2104 ESRRG; estrogen related receptor gamma
       8204 NRIP1; nuclear receptor interacting protein 1
       5562 PRKAA1; protein kinase AMP-activated catalytic subunit alpha 1
       5563 PRKAA2; protein kinase AMP-activated catalytic subunit alpha 2
       9361 LONP1; lon peptidase 1, mitochondrial
       23411 SIRT1; sirtuin 1
       84947 SERAC1; serine active site containing 1
       8409 UXT; ubiquitously expressed prefoldin like chaperone
       84808 PERM1; PPARGC1 and ESRR induced regulator, muscle 1
       51103 NDUFAF1; NADH:ubiquinone oxidoreductase complex assembly factor 1
       91942 NDUFAF2; NADH:ubiquinone oxidoreductase complex assembly factor 2
       25915 NDUFAF3; NADH:ubiquinone oxidoreductase complex assembly factor 3
       29078 NDUFAF4; NADH:ubiquinone oxidoreductase complex assembly factor 4
       79133 NDUFAF5; NADH:ubiquinone oxidoreductase complex assembly factor 5
       137682 NDUFAF6; NADH:ubiquinone oxidoreductase complex assembly factor 6
       55471 NDUFAF7; NADH:ubiquinone oxidoreductase complex assembly factor 7
       284184 NDUFAF8; NADH:ubiquinone oxidoreductase complex assembly factor 8
       55863 TMEM126B; transmembrane protein 126B
       51295 ECSIT; ECSIT signaling integrator
       28976 ACAD9; acyl-CoA dehydrogenase family member 9
       80224 NUBPL; NUBP iron-sulfur cluster assembly factor, mitochondrial
       55572 FOXRED1; FAD dependent oxidoreductase domain containing 1
       84816 RTN4IP1; reticulon 4 interacting protein 1
       51300 TIMMDC1; translocase of inner mitochondrial membrane domain containing 1
       644096 SDHAF1; succinate dehydrogenase complex assembly factor 1
       54949 SDHAF2; succinate dehydrogenase complex assembly factor 2
       617 BCS1L; BCS1 homolog, ubiquinol-cytochrome c reductase complex chaperone
       54902 TTC19; tetratricopeptide repeat domain 19
       90624 LYRM7; LYR motif containing 7
       790955 UQCC3; ubiquinol-cytochrome c reductase complex assembly factor 3
       283951 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
       440957 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
       728568 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
       647087 STMP1; short transmembrane mitochondrial protein 1
       152100 CMC1; C-X9-C motif containing 1
       56942 CMC2; C-X9-C motif containing 2
       55744 COA1; cytochrome c oxidase assembly factor 1
       28958 COA3; cytochrome c oxidase assembly factor 3
       51287 COA4; cytochrome c oxidase assembly factor 4 homolog
       493753 COA5; cytochrome c oxidase assembly factor 5
       388753 COA6; cytochrome c oxidase assembly factor 6
       65260 COA7; cytochrome c oxidase assembly factor 7
       1352 COX10; cytochrome c oxidase assembly factor heme A:farnesyltransferase COX10
       1353 COX11; cytochrome c oxidase copper chaperone COX11
       84987 COX14; cytochrome c oxidase assembly factor COX14
       1355 COX15; cytochrome c oxidase assembly homolog COX15
       51241 COX16; cytochrome c oxidase assembly factor COX16
       10063 COX17; cytochrome c oxidase copper chaperone COX17
       285521 COX18; cytochrome c oxidase assembly factor COX18
       90639 COX19; cytochrome c oxidase assembly factor COX19
       116228 COX20; cytochrome c oxidase assembly factor COX20
       100131801 PET100; PET100 cytochrome c oxidase chaperone
       100303755 PET117; PET117 cytochrome c oxidase chaperone
       5018 OXA1L; OXA1L mitochondrial inner membrane protein
       6834 SURF1; SURF1 cytochrome c oxidase assembly factor
       6341 SCO1; synthesis of cytochrome C oxidase 1
       9997 SCO2; synthesis of cytochrome C oxidase 2
       51204 TACO1; translational activator of cytochrome c oxidase I
       10128 LRPPRC; leucine rich pentatricopeptide repeat containing
       84334 COA8; cytochrome c oxidase assembly factor 8
       79064 TMEM223; transmembrane protein 223
       64756 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1
       91647 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2
       54968 TMEM70; transmembrane protein 70
       9556 ATP5MJ; ATP synthase membrane subunit j
       84833 ATP5MK; ATP synthase membrane subunit k
       55669 MFN1; mitofusin 1
       9927 MFN2; mitofusin 2
       4976 OPA1; OPA1 mitochondrial dynamin like GTPase
       80207 OPA3; outer mitochondrial membrane lipid metabolism regulator OPA3
       51499 TRIAP1; TP53 regulated inhibitor of apoptosis 1
       55486 PARL; presenilin associated rhomboid like
       578 BAK1; BCL2 antagonist/killer 1
       581 BAX; BCL2 associated X, apoptosis regulator
       10059 DNM1L; dynamin 1 like
       51024 FIS1; fission, mitochondrial 1
       6612 SUMO3; small ubiquitin like modifier 3
       6613 SUMO2; small ubiquitin like modifier 2
       7341 SUMO1; small ubiquitin like modifier 1
       387082 SUMO4; small ubiquitin like modifier 4
       51100 SH3GLB1; SH3 domain containing GRB2 like, endophilin B1
       23787 MTCH1; mitochondrial carrier 1
       23788 MTCH2; mitochondrial carrier 2
       56947 MFF; mitochondrial fission factor
       54332 GDAP1; ganglioside induced differentiation associated protein 1
       78997 GDAP1L1; ganglioside induced differentiation associated protein 1 like 1
       10493 VAT1; vesicle amine transport 1
       125170 MIEF2; mitochondrial elongation factor 2
       54471 MIEF1; mitochondrial elongation factor 1
       201164 PLD6; phospholipase D family member 6
       374986 MIGA1; mitoguardin 1
       84895 MIGA2; mitoguardin 2
       71 ACTG1; actin gamma 1
       60 ACTB; actin beta
       51126 NAA20; N-alpha-acetyltransferase 20, NatB catalytic subunit
       80018 NAA25; N-alpha-acetyltransferase 25, NatB auxiliary subunit
       5245 PHB1; prohibitin 1
       11331 PHB2; prohibitin 2
       3895 KTN1; kinectin 1
       4644 MYO5A; myosin VA
       4645 MYO5B; myosin VB
       55930 MYO5C; myosin VC
       331 XIAP; X-linked inhibitor of apoptosis
       56616 DIABLO; diablo IAP-binding mitochondrial protein
       83891 SNX25; sorting nexin 25
       51537 MTFP1; mitochondrial fission process 1
       7818 DAP3; death associated protein 3
       4734 NEDD4; NEDD4 E3 ubiquitin protein ligase
       55074 OXR1; oxidation resistance 1
       55154 MSTO1; misato mitochondrial distribution and morphology regulator 1
       23130 ATG2A; autophagy related 2A
       55102 ATG2B; autophagy related 2B
       64422 ATG3; autophagy related 3
       115201 ATG4A; autophagy related 4A cysteine peptidase
       23192 ATG4B; autophagy related 4B cysteine peptidase
       84938 ATG4C; autophagy related 4C cysteine peptidase
       84971 ATG4D; autophagy related 4D cysteine peptidase
       9474 ATG5; autophagy related 5
       8678 BECN1; beclin 1
       441925 BECN2; beclin 2
       10533 ATG7; autophagy related 7
       11337 GABARAP; GABA type A receptor-associated protein
       23710 GABARAPL1; GABA type A receptor associated protein like 1
       11345 GABARAPL2; GABA type A receptor associated protein like 2
       285973 ATG9B; autophagy related 9B
       79065 ATG9A; autophagy related 9A
       83734 ATG10; autophagy related 10
       9140 ATG12; autophagy related 12
       22863 ATG14; autophagy related 14
       55054 ATG16L1; autophagy related 16 like 1
       89849 ATG16L2; autophagy related 16 like 2
       26100 WIPI2; WD repeat domain, phosphoinositide interacting 2
       55062 WIPI1; WD repeat domain, phosphoinositide interacting 1
       5071 PRKN; parkin RBR E3 ubiquitin protein ligase
       10193 RNF41; ring finger protein 41
       23274 CLEC16A; C-type lectin domain containing 16A
       65018 PINK1; PTEN induced kinase 1
       8878 SQSTM1; sequestosome 1
       8887 TAX1BP1; Tax1 binding protein 1
       10241 CALCOCO2; calcium binding and coiled-coil domain 2
       55626 AMBRA1; autophagy and beclin 1 regulator 1
       9776 ATG13; autophagy related 13
       8408 ULK1; unc-51 like autophagy activating kinase 1
       9706 ULK2; unc-51 like autophagy activating kinase 2
       9821 RB1CC1; RB1 inducible coiled-coil 1
       3320 HSP90AA1; heat shock protein 90 alpha family class A member 1
       3326 HSP90AB1; heat shock protein 90 alpha family class B member 1
       11140 CDC37; cell division cycle 37, HSP90 cochaperone
       57154 SMURF1; SMAD specific E3 ubiquitin protein ligase 1
       64750 SMURF2; SMAD specific E3 ubiquitin protein ligase 2
       665 BNIP3L; BCL2 interacting protein 3 like
       139341 FUNDC1; FUN14 domain containing 1
       440738 MAP1LC3C; microtubule associated protein 1 light chain 3 gamma
       81631 MAP1LC3B; microtubule associated protein 1 light chain 3 beta
       84557 MAP1LC3A; microtubule associated protein 1 light chain 3 alpha
       643246 MAP1LC3B2; microtubule associated protein 1 light chain 3 beta 2
       4077 NBR1; NBR1 autophagy cargo receptor
       25851 TECPR1; tectonin beta-propeller repeat containing 1
       53349 ZFYVE1; zinc finger FYVE-type containing 1
       80347 COASY; Coenzyme A synthase
       8398 PLA2G6; phospholipase A2 group VI
       83636 C19orf12; chromosome 19 open reading frame 12
       65991 FUNDC2; FUN14 domain containing 2
K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
K02261 COX2; cytochrome c oxidase subunit 2
K02262 COX3; cytochrome c oxidase subunit 3
K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
K11830 TFAM; transcription factor A, mitochondrial
K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
K02519 infB; translation initiation factor IF-2
K02520 infC; translation initiation factor IF-3
K02357 tsf; elongation factor Ts
K02358 tuf; elongation factor Tu
K02355 fusA; elongation factor G
K02355 fusA; elongation factor G
K15031 MTERF; mitochondrial transcription termination factor family protein
K15031 MTERF; mitochondrial transcription termination factor family protein
K15031 MTERF; mitochondrial transcription termination factor family protein
K15031 MTERF; mitochondrial transcription termination factor family protein
K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
K17655 MRPP3; mitochondrial ribonuclease P protein 3
K17656 MSS51; mitochondrial splicing suppressor protein 51
K17658 TEFM; transcription elongation factor, mitochondrial
K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
K03595 era; GTPase
K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
K19828 MTG1; mitochondrial GTPase 1
K19832 NOA1; nitric oxide-associated protein 1
K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-]
K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
K23495 RCC1L; RCC1-like G exchanging factor-like protein
K23496 NGRN; neugrin
K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
K18190 FASTKD2; FAST kinase domain-containing protein 2
K23498 COXPD7; peptide chain release factor
K23499 RMND1; required for meiotic nuclear division protein 1
K24984 GRSF1; G-rich sequence factor 1
K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
K26186 MTRES1; mitochondrial transcription rescue factor 1
K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
K02333 POLG2; DNA polymerase gamma 2
K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
K01173 ENDOG; endonuclease G, mitochondrial
K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
K15050 EXOG; nuclease EXOG, mitochondrial
K17680 PEO1; twinkle protein [EC:5.6.2.3]
K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
K03111 ssb; single-strand DNA-binding protein
K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
K17682 MNF1; mitochondrial nucleoid factor 1
K09503 DNAJA2; DnaJ homolog subfamily A member 2
K17766 TOM34; mitochondrial import receptor subunit TOM34
K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
K17767 AIP; AH receptor-interacting protein
K17767 AIP; AH receptor-interacting protein
K11518 TOM40; mitochondrial import receptor subunit TOM40
K11518 TOM40; mitochondrial import receptor subunit TOM40
K17768 TOM70; mitochondrial import receptor subunit TOM70
K17769 TOM22; mitochondrial import receptor subunit TOM22
K17770 TOM20; mitochondrial import receptor subunit TOM20
K17770 TOM20; mitochondrial import receptor subunit TOM20
K17771 TOM7; mitochondrial import receptor subunit TOM7
K17772 TOM6; mitochondrial import receptor subunit TOM6
K17773 TOM5; mitochondrial import receptor subunit TOM5
K07277 SAM50; outer membrane protein insertion porin family
K05862 VDAC1; voltage-dependent anion channel protein 1
K15040 VDAC2; voltage-dependent anion channel protein 2
K15041 VDAC3; voltage-dependent anion channel protein 3
K17776 MTX; metaxin
K17776 MTX; metaxin
K17776 MTX; metaxin
K25838 MYO19; myosin XIX
K26187 ARMCX1; armadillo repeat-containing X-linked protein 1
K26188 ARMCX2; armadillo repeat-containing X-linked protein 2
K26189 ARMCX3; armadillo repeat-containing X-linked protein 3
K26190 ARMCX6; armadillo repeat-containing X-linked protein 6
K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
K17784 MICOS10; MICOS complex subunit MIC10
K17785 IMMT; MICOS complex subunit MIC60
K24624 MICOS13; MICOS complex subunit MIC13
K17563 CHCHD3; MICOS complex subunit MIC19
K17564 CHCHD6; MICOS complex subunit MIC25
K24625 APOO; MICOS complex subunit MIC26
K24626 APOOL; MICOS complex subunit MIC27
K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
K20858 MCU; calcium uniporter protein, mitochondrial
K22827 MICU1; calcium uptake protein 1, mitochondrial
K22828 MICU2; calcium uptake protein 2, mitochondrial
K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial
K22830 SMDT1; essential MCU regulator, mitochondrial
K22137 MCUR1; mitochondrial calcium uniporter regulator 1
K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
K18157 TMEM126A; transmembrane protein 126A
K22138 MPC1; mitochondrial pyruvate carrier 1
K22138 MPC1; mitochondrial pyruvate carrier 1
K22139 MPC2; mitochondrial pyruvate carrier 2
K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
K04043 dnaK; molecular chaperone DnaK
K03687 GRPE; molecular chaperone GrpE
K03687 GRPE; molecular chaperone GrpE
K09539 DNAJC19; DnaJ homolog subfamily C member 19
K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
K04078 groES; chaperonin GroES
K09504 DNAJA3; DnaJ homolog subfamily A member 3
K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
K17808 ZIM17; mitochondrial protein import protein ZIM17
K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
K17809 POLDIP2; polymerase delta-interacting protein 2
K05870 CREB1; cyclic AMP-responsive element-binding protein 1
K04684 SP1; transcription factor Sp1
K09201 YY; transcription factor YY
K09201 YY; transcription factor YY
K09454 GABPB; GA-binding protein transcription factor, beta
K09454 GABPB; GA-binding protein transcription factor, beta
K11831 NRF1; nuclear respiratory factor 1
K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
K14739 MT1_2; metallothionein 1/2
K14739 MT1_2; metallothionein 1/2
K14739 MT1_2; metallothionein 1/2
K14739 MT1_2; metallothionein 1/2
K14739 MT1_2; metallothionein 1/2
K14739 MT1_2; metallothionein 1/2
K14739 MT1_2; metallothionein 1/2
K14739 MT1_2; metallothionein 1/2
K14739 MT1_2; metallothionein 1/2
K14739 MT1_2; metallothionein 1/2
K14740 MT3; metallothionein 3
K14741 MT4; metallothionein 4
K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
K15309 CRTC1; CREB-regulated transcription coactivator 1
K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
K22069 LYRM4; LYR motif-containing protein 4
K19054 FXN; frataxin [EC:1.16.3.1]
K22070 FDX1; ferredoxin-1, mitochondrial
K22071 FDX2; ferredoxin-2, mitochondrial
K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
K04082 hscB; molecular chaperone HscB
K14001 SIL1; nucleotide exchange factor SIL1
K07390 grxD; monothiol glutaredoxin
K22063 ISCA1; iron-sulfur cluster assembly 1
K22072 ISCA2; iron-sulfur cluster assembly 2
K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
K22066 BOLA1; BolA-like protein 1
K22075 BOLA3; BolA-like protein 3
K23500 SFXN1_3; sideroflexin-1/3
K23500 SFXN1_3; sideroflexin-1/3
K23501 SFXN2; sideroflexin-2
K23502 SFXN4; sideroflexin-4
K23503 SFXN5; sideroflexin-5
K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21]
K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21]
K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
K10270 FBXL4; F-box and leucine-rich repeat protein 4
K14966 HCFC1; host cell factor 1
K27390 HCFC2; host cell factor 2
K04533 HD; huntingtin
K08552 NR3B1; estrogen-related receptor alpha
K08553 NR3B2; estrogen-related receptor beta
K08554 NR3B3; estrogen-related receptor gamma
K17965 NRIP1; nuclear receptor-interacting protein 1
K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
K23504 SERAC1; protein SERAC1
K26537 UXT; protein UXT
K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1
K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
K18165 TMEM126B; complex I assembly factor TMEM126B
K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
K03593 mrp; ATP-binding protein involved in chromosome partitioning
K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
K23505 TIMMDC1; complex I assembly factor TIMMDC1
K18167 SDHAF1; succinate dehydrogenase assembly factor 1
K18168 SDHAF2; succinate dehydrogenase assembly factor 2
K08900 BCS1; mitochondrial chaperone BCS1
K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
K18170 LYRM7; complex III assembly factor LYRM7
K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
K27319 STMP1; short transmembrane mitochondrial protein 1
K18171 CMC1; COX assembly mitochondrial protein 1
K18172 CMC2; COX assembly mitochondrial protein 2
K18173 COA1; cytochrome c oxidase assembly factor 1
K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
K18177 COA4; cytochrome c oxidase assembly factor 4
K18178 COA5; cytochrome c oxidase assembly factor 5
K18179 COA6; cytochrome c oxidase assembly factor 6
K18180 COA7; cytochrome c oxidase assembly factor 7
K02257 COX10; heme o synthase [EC:2.5.1.141]
K02258 COX11; cytochrome c oxidase assembly protein subunit 11
K18181 COX14; cytochrome c oxidase assembly factor 14
K02259 COX15; heme a synthase [EC:1.17.99.9]
K18182 COX16; cytochrome c oxidase assembly protein subunit 16
K02260 COX17; cytochrome c oxidase assembly protein subunit 17
K17797 COX18; mitochondrial inner membrane protein COX18
K18183 COX19; cytochrome c oxidase assembly protein subunit 19
K18184 COX20; cytochrome c oxidase assembly protein subunit 20
K18186 PET100; protein PET100, animal type
K18188 PET117; protein PET117
K03217 yidC; YidC/Oxa1 family membrane protein insertase
K14998 SURF1; surfeit locus 1 family protein
K07152 SCO1; protein SCO1
K23755 SCO2; protein SCO2
K18189 TACO1; translational activator of cytochrome c oxidase 1
K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
K23506 APOPT1; apoptogenic protein 1
K27342 TMEM223; transmembrane protein 223
K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
K17966 TMEM70; transmembrane protein 70, mitochondrial
K18193 MP68; 6.8 kDa mitochondrial proteolipid
K18194 USMG5; up-regulated during skeletal muscle growth protein 5
K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
K23166 OPA3; optic atrophy 3 protein
K17968 TRIAP1; TRIAP1/MDM35 family protein
K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
K14021 BAK; Bcl-2 homologous antagonist/killer
K02159 BAX; apoptosis regulator BAX
K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
K17969 FIS1; mitochondrial fission 1 protein
K12160 SUMO; small ubiquitin-related modifier
K12160 SUMO; small ubiquitin-related modifier
K12160 SUMO; small ubiquitin-related modifier
K12160 SUMO; small ubiquitin-related modifier
K11248 SH3GLB1; endophilin-B1
K17885 MTCH; mitochondrial carrier
K17885 MTCH; mitochondrial carrier
K22076 MFF; mitochondrial fission factor
K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
K23167 VAT1; synaptic vesicle membrane protein VAT-1
K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
K27289 MIGA; mitoguardin
K27289 MIGA; mitoguardin
K05692 ACTB_G1; actin beta/gamma 1
K05692 ACTB_G1; actin beta/gamma 1
K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
K17080 PHB1; prohibitin 1
K17081 PHB2; prohibitin 2
K17975 KTN1; kinectin
K10357 MYO5; myosin V
K10357 MYO5; myosin V
K10357 MYO5; myosin V
K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
K10522 DIABLO; diablo
K17887 SNX25; sorting nexin-25
K17981 MTFP1; mitochondrial fission process protein 1
K17408 DAP3; small subunit ribosomal protein S29
K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26]
K25437 OXR1; oxidation resistance protein 1
K27320 MSTO1; protein misato
K17906 ATG2; autophagy-related protein 2
K17906 ATG2; autophagy-related protein 2
K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
K08339 ATG5; autophagy-related protein 5
K08334 BECN; beclin
K08334 BECN; beclin
K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
K08341 GABARAP; GABA(A) receptor-associated protein
K08341 GABARAP; GABA(A) receptor-associated protein
K08341 GABARAP; GABA(A) receptor-associated protein
K17907 ATG9; autophagy-related protein 9
K17907 ATG9; autophagy-related protein 9
K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
K08336 ATG12; ubiquitin-like protein ATG12
K17889 ATG14L; beclin 1-associated autophagy-related key regulator
K17890 ATG16L1; autophagy-related protein 16-1
K20868 ATG16L2; autophagy-related protein 16-2
K17908 WIPI1_2; autophagy-related protein 18
K17908 WIPI1_2; autophagy-related protein 18
K04556 PARK2; parkin [EC:2.3.2.31]
K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
K19513 CLEC16A; protein CLEC16A
K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
K14381 SQSTM1; sequestosome 1
K21347 TAX1BP1; Tax1-binding protein 1
K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
K08331 ATG13; autophagy-related protein 13
K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
K17589 RB1CC1; RB1-inducible coiled-coil protein 1
K04079 HSP90A; molecular chaperone HtpG
K04079 HSP90A; molecular chaperone HtpG
K09554 CDC37; cell division cycle protein 37
K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
K17986 FUNDC1; FUN14 domain-containing protein 1
K10435 MAP1LC; microtubule-associated protein 1 light chain
K10435 MAP1LC; microtubule-associated protein 1 light chain
K10435 MAP1LC; microtubule-associated protein 1 light chain
K10435 MAP1LC; microtubule-associated protein 1 light chain
K17987 NBR1; next to BRCA1 gene 1 protein
K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
K23168 MPAN; protein MPAN
K24308 FUNDC2; FUN14 domain-containing protein 2
 
   09183 Protein families: signaling and cellular processes
 
   09185 Viral protein families
 
   09184 RNA family
 
 09190 Not Included in Pathway or Brite

[ KO | BRITE | KEGG2 | KEGG ]
Last updated: April 25, 2024