class name | count |
---|---|
Liliopsida | 15 |
rosids | 6 |
asterids | 2 |
class name | count |
---|---|
Hyacinthaceae | 9 |
Streptomycetaceae | 7 |
Fabaceae | 4 |
Araceae | 4 |
Euphorbiaceae | 2 |
Campanulaceae | 2 |
Stemonaceae | 2 |
br08003 Category | # of metabolite |
---|
br08003 Category | KEGG ID | KNApSAcK ID |
---|
accession | description | class description | KNApSAcK metabolite in interactions |
# of diseases
(OMIM / KEGG) |
---|---|---|---|---|
O43451 | Maltase-glucoamylase, intestinal | Hydrolase | C00002037 C00017836 C00018617 C00018724 C00036713 C00036798 C00036799 C00042067 C00042220 | 0 / 0 |
P06280 | Alpha-galactosidase A | Enzyme | C00002037 C00036713 C00036798 C00036799 C00038412 C00038589 C00042067 C00042220 C00045586 | 1 / 1 |
P04066 | Tissue alpha-L-fucosidase | Enzyme | C00002037 C00036713 C00036798 C00036799 C00038412 C00038589 C00042067 C00042220 C00045586 | 1 / 2 |
P04062 | Glucosylceramidase | Enzyme | C00002037 C00036713 C00036798 C00036799 C00042067 C00042220 | 6 / 4 |
P10253 | Lysosomal alpha-glucosidase | Hydrolase | C00002037 C00036713 C00036798 C00036799 C00042067 C00042220 | 1 / 1 |
Q8TET4 | Neutral alpha-glucosidase C | Enzyme | C00036713 C00036798 C00036799 C00042220 | 0 / 0 |
P35573 | Glycogen debranching enzyme | Enzyme | C00002037 C00042067 C00045536 | 1 / 1 |
Q9BTY2 | Plasma alpha-L-fucosidase | Enzyme | C00038412 C00038589 C00045586 | 0 / 0 |
Q14697 | Neutral alpha-glucosidase AB | Enzyme | C00002037 C00042067 | 0 / 0 |
Q9H227 | Cytosolic beta-glucosidase | Enzyme | C00002037 C00042067 | 0 / 0 |
OMIM | preferred title | UniProt |
---|---|---|
#301500 | Fabry disease |
P06280
|
#230000 | Fucosidosis |
P04066
|
#608013 | Gaucher disease, perinatal lethal |
P04062
|
#230800 | Gaucher disease, type i |
P04062
|
#230900 | Gaucher disease, type ii |
P04062
|
#231000 | Gaucher disease, type iii |
P04062
|
#231005 | Gaucher disease, type iiic |
P04062
|
#232300 | Glycogen storage disease ii |
P10253
|
#232400 | Glycogen storage disease iii |
P35573
|
#168600 | Parkinson disease, late-onset; pd |
P04062
|
KEGG | name | UniProt |
---|---|---|
H00066 | Lewy body dementia (LBD) |
P04062
(related)
|
H00126 | Gaucher disease |
P04062
(related)
|
H00426 | Defects in the degradation of ganglioside |
P04062
(related)
|
H00810 | Progressive myoclonic epilepsy (PME) |
P04062
(related)
|
H00141 | Fucosidosis |
P04066
(related)
|
H00422 | Glycoproteinoses |
P04066
(related)
|
H00125 | Fabry disease |
P06280
(related)
|
H00069 | Glycogen storage diseases (GSD) |
P10253
(related)
P35573 (related) |