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09100 Metabolism
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09101 Carbohydrate metabolism
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00010 Glycolysis / Gluconeogenesis [PATH:clv00010]
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00020 Citrate cycle (TCA cycle) [PATH:clv00020]
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00030 Pentose phosphate pathway [PATH:clv00030]
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00040 Pentose and glucuronate interconversions [PATH:clv00040]
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00051 Fructose and mannose metabolism [PATH:clv00051]
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00052 Galactose metabolism [PATH:clv00052]
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00053 Ascorbate and aldarate metabolism [PATH:clv00053]
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00500 Starch and sucrose metabolism [PATH:clv00500]
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00520 Amino sugar and nucleotide sugar metabolism [PATH:clv00520]
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00620 Pyruvate metabolism [PATH:clv00620]
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00630 Glyoxylate and dicarboxylate metabolism [PATH:clv00630]
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00640 Propanoate metabolism [PATH:clv00640]
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00650 Butanoate metabolism [PATH:clv00650]
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102096599 ACAT1; acetyl-CoA acetyltransferase, mitochondrial
102087586 ACAT2; acetyl-CoA acetyltransferase, cytosolic
102084813 HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial
102093055 HADHA; trifunctional enzyme subunit alpha, mitochondrial
102091542 EHHADH; peroxisomal bifunctional enzyme
102084289 ECHS1; LOW QUALITY PROTEIN: enoyl-CoA hydratase, mitochondrial
102088733 ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial
102088507 acyl-coenzyme A synthetase ACSM4, mitochondrial isoform X1
102088808 acyl-coenzyme A synthetase ACSM4, mitochondrial
102089184 ACSM3; acyl-coenzyme A synthetase ACSM3, mitochondrial isoform X1
102089678 L2HGDH; L-2-hydroxyglutarate dehydrogenase, mitochondrial
102096407 GAD1; glutamate decarboxylase 1
102086880 GAD2; glutamate decarboxylase 2
102086859 ABAT; 4-aminobutyrate aminotransferase, mitochondrial isoform X1
102091200 ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial
102084382 HMGCS1; hydroxymethylglutaryl-CoA synthase, cytoplasmic
102096047 LOW QUALITY PROTEIN: hydroxymethylglutaryl-CoA synthase, mitochondrial
102098502 HMGCL; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1
102092844 HMGCLL1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic isoform X1
102089756 OXCT1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial
102090816 AACS; acetoacetyl-CoA synthetase
102092067 D-beta-hydroxybutyrate dehydrogenase, mitochondrial
102092790 D-beta-hydroxybutyrate dehydrogenase, mitochondrial isoform X1
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K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K01896 ACSM; medium-chain acyl-CoA synthetase [EC:6.2.1.2]
K01896 ACSM; medium-chain acyl-CoA synthetase [EC:6.2.1.2]
K01896 ACSM; medium-chain acyl-CoA synthetase [EC:6.2.1.2]
K00109 L2HGDH; 2-hydroxyglutarate dehydrogenase [EC:1.1.99.2]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K01580 E4.1.1.15; glutamate decarboxylase [EC:4.1.1.15]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00139 ALDH5A1; succinate-semialdehyde dehydrogenase [EC:1.2.1.24]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01907 AACS; acetoacetyl-CoA synthetase [EC:6.2.1.16]
K00019 BDH1; 3-hydroxybutyrate dehydrogenase [EC:1.1.1.30]
K00019 BDH1; 3-hydroxybutyrate dehydrogenase [EC:1.1.1.30]
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00660 C5-Branched dibasic acid metabolism
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00562 Inositol phosphate metabolism [PATH:clv00562]
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09102 Energy metabolism
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09103 Lipid metabolism
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09104 Nucleotide metabolism
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09105 Amino acid metabolism
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00250 Alanine, aspartate and glutamate metabolism [PATH:clv00250]
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00260 Glycine, serine and threonine metabolism [PATH:clv00260]
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00270 Cysteine and methionine metabolism [PATH:clv00270]
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00280 Valine, leucine and isoleucine degradation [PATH:clv00280]
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102097105 BCAT1; branched-chain-amino-acid aminotransferase, cytosolic isoform X2
102086260 IL4I1; L-amino-acid oxidase
102097651 BCKDHB; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X4
102092936 DBT; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
102096110 DLD; dihydrolipoyl dehydrogenase, mitochondrial
102088733 ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial
102093964 ACADM; medium-chain specific acyl-CoA dehydrogenase, mitochondrial
102086614 IVD; isovaleryl-CoA dehydrogenase, mitochondrial isoform X1
102096980 ACADSB; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
102086923 ACAD8; isobutyryl-CoA dehydrogenase, mitochondrial
102093055 HADHA; trifunctional enzyme subunit alpha, mitochondrial
102091542 EHHADH; peroxisomal bifunctional enzyme
102084289 ECHS1; LOW QUALITY PROTEIN: enoyl-CoA hydratase, mitochondrial
102084813 HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial
102088336 ACAA1; 3-ketoacyl-CoA thiolase, peroxisomal
102090854 ACAA2; 3-ketoacyl-CoA thiolase, mitochondrial
102092691 HADHB; LOW QUALITY PROTEIN: trifunctional enzyme subunit beta, mitochondrial
102084098 propionyl-CoA carboxylase alpha chain, mitochondrial
102093066 PCCB; propionyl-CoA carboxylase beta chain, mitochondrial
102096437 MUT; methylmalonyl-CoA mutase, mitochondrial isoform X1
102093555 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
102088406 HIBADH; 3-hydroxyisobutyrate dehydrogenase, mitochondrial
102096481 ALDH6A1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
102085205 fatty aldehyde dehydrogenase
102085381 fatty aldehyde dehydrogenase
102097498 ALDH2; aldehyde dehydrogenase, mitochondrial
102091436 ALDH7A1; alpha-aminoadipic semialdehyde dehydrogenase
102087254 ALDH9A1; 4-trimethylaminobutyraldehyde dehydrogenase
102097486 AOX1; aldehyde oxidase isoform X1
102096424 ACSF3; acyl-CoA synthetase family member 3, mitochondrial isoform X1
102086859 ABAT; 4-aminobutyrate aminotransferase, mitochondrial isoform X1
102087277 AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1
102093392 MCCC1; methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
102084982 MCCC2; methylcrotonoyl-CoA carboxylase beta chain, mitochondrial
102092943 AUH; methylglutaconyl-CoA hydratase, mitochondrial isoform X1
102098502 HMGCL; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1
102092844 HMGCLL1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic isoform X1
102089756 OXCT1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial
102090816 AACS; acetoacetyl-CoA synthetase
102096599 ACAT1; acetyl-CoA acetyltransferase, mitochondrial
102087586 ACAT2; acetyl-CoA acetyltransferase, cytosolic
102084382 HMGCS1; hydroxymethylglutaryl-CoA synthase, cytoplasmic
102096047 LOW QUALITY PROTEIN: hydroxymethylglutaryl-CoA synthase, mitochondrial
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K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoyl dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00253 IVD; isovaleryl-CoA dehydrogenase [EC:1.3.8.4]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K11538 ACAD8; isobutyryl-CoA dehydrogenase [EC:1.3.99.-]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K01965 PCCA; propionyl-CoA carboxylase alpha chain [EC:6.4.1.3]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K00020 HIBADH; 3-hydroxyisobutyrate dehydrogenase [EC:1.1.1.31]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K18660 ACSF3; malonyl-CoA/methylmalonyl-CoA synthetase [EC:6.2.1.76 6.2.1.-]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00827 AGXT2; alanine-glyoxylate transaminase / (R)-3-amino-2-methylpropionate-pyruvate transaminase [EC:2.6.1.44 2.6.1.40]
K01968 MCCC1; 3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
K01969 MCCC2; 3-methylcrotonyl-CoA carboxylase beta subunit [EC:6.4.1.4]
K05607 AUH; methylglutaconyl-CoA hydratase [EC:4.2.1.18]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01640 HMGCL; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01907 AACS; acetoacetyl-CoA synthetase [EC:6.2.1.16]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01641 HMGCS; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
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00290 Valine, leucine and isoleucine biosynthesis [PATH:clv00290]
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00300 Lysine biosynthesis
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00310 Lysine degradation [PATH:clv00310]
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00220 Arginine biosynthesis [PATH:clv00220]
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00330 Arginine and proline metabolism [PATH:clv00330]
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00340 Histidine metabolism [PATH:clv00340]
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00350 Tyrosine metabolism [PATH:clv00350]
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00360 Phenylalanine metabolism [PATH:clv00360]
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00380 Tryptophan metabolism [PATH:clv00380]
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00400 Phenylalanine, tyrosine and tryptophan biosynthesis [PATH:clv00400]
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09106 Metabolism of other amino acids
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09107 Glycan biosynthesis and metabolism
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09108 Metabolism of cofactors and vitamins
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09109 Metabolism of terpenoids and polyketides
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09110 Biosynthesis of other secondary metabolites
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09111 Xenobiotics biodegradation and metabolism
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09112 Not included in regular maps
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09120 Genetic Information Processing
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09130 Environmental Information Processing
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09140 Cellular Processes
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09150 Organismal Systems
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09160 Human Diseases
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09180 Brite Hierarchies
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09190 Not Included in Pathway or Brite
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